Kai, shin ƙaramin yaronka yana yawan kamuwa da zazzabi a waɗannan kwanaki? Da zarar ka yi tunanin ka warke, shin yana sake tashi? Wani lokaci dalilin wannan bazai zama ƙwayar cuta ko ƙwayoyin cuta ba. A yau za mu yi magana game da wata cuta da ta ɗan yi rikitarwa, amma yana da matuƙar muhimmanci a sani. Ana kiran wannan da SAIDs, wanda ke nufin Cututtukan Kumburi na Tsari . A da, ana kiran wannan da `(Ciwon Zazzabi na Periodic)` ko `(Ciwon Zazzabi na Maimaita)`.
Menene SAIDs? Bari mu fahimce shi a taƙaice.
A taƙaice dai, SAIDs rukuni ne na cututtuka waɗanda ke faruwa sakamakon rashin aiki ko matsalar tsari a cikin tsarin garkuwar jikinmu . Shi ya sa yaro zai iya kamuwa da zazzabi akai-akai ko da ba tare da kamuwa da cuta ba (kamar ƙwayar cuta ko ƙwayoyin cuta).
Abu mafi mahimmanci shine kada a rikita waɗannan yanayi da ake kira SAIDs da `(Cututtukan Autoimmune)` (misali `(Rheumatoid Arthritis)` ko `(Lupus)` da ka ji labarinsu. A cikin cututtukan `(Autoimmune)`, saboda wani kuskure a cikin `(daidaitaccen tsarin garkuwar jiki)` na jikinmu, wannan tsarin yana kai hari ga ƙwayoyin halittarsa masu lafiya. Amma a cikin SAIDs, wani abu daban yana faruwa.
Kwayoyin cutar SAIDs sun fi na cututtukan da ke da alaƙa da garkuwar jiki yawa. Sau da yawa ana gado su kuma suna faruwa ne sakamakon maye gurbi a cikin kwayoyin halitta .
Yawanci, amma ba koyaushe ba, alamun SAID suna farawa ne lokacin da yaro yake ƙarami, ko dai a matsayin jariri ko kuma jariri . Yaronka na iya samun "lokacin" zazzabi da sauran alamu tare da wannan yanayin. A tsakanin waɗannan lokutan, yaronka ba zai iya samun alamun kwata-kwata ba. Kodayake babu maganin SAIDs, sau da yawa akwai magunguna don taimakawa wajen sarrafa alamun yaronka.
Wadanne manyan nau'ikan SAIDs ne?
Masu bincike sun gano nau'ikan SAIDs kimanin 60, kuma har yanzu ana gano sababbi. Ga wasu daga cikin nau'ikan SAIDs da aka fi sani:
- Zazzabin Bahar Rum na Iyali (FMF): Wannan shine mafi yawan cututtukan zazzaɓi da aka gada ta hanyar gado, wanda ke sake dawowa. Yana iya haifar da kumburi mai zafi a cikin ciki, ƙirji, da haɗin gwiwa a cikin yara.
- Zazzaɓin lokaci-lokaci, aphthous-stomatitis, pharyngitis, adenitis (PFAPA): Wannan yawanci yana farawa ne a cikin ƙananan yara kafin su kai shekara 4. Wani lokaci, yanayin na iya inganta shi da kansa bayan shekara 10.
- Ciwon da ke da alaƙa da masu karɓar ƙwayoyin cuta na Tumor necrosis factor (TRAPS): Wannan na iya faruwa a lokacin ƙuruciya, samartaka, ko ma a lokacin girma.
- Rashin ƙarancin Mevalonate kinase (MKD): A da ana kiransa da "Cutar Hyper-IgD", wannan yawanci yakan fara ne kafin yaron ya kai shekara ɗaya.
- Cututtukan kumburi masu alaƙa da NLRP3:A da ana kiran wannan da suna `(Cryopyrin-related periodic syndromes - CAPS)`. Akwai wasu nau'ikan guda uku a cikin wannan.
- Cutar Still da ta fara tasowa daga manya (AOSD): Kamar yadda sunan ya nuna, wannan nau'in ciwon yara ne da manya ke fama da shi, wato "Ciwon Jijiyoyi na Yara (JIA)".
- Cutar granulomatous mai alaƙa da NOD-2 (Blau syndrome): Wannan yawanci yana farawa ne kafin ya kai shekara 4. Yana shafar fatar yaron, idanu, da kuma haɗin gwiwa.
Mene ne alamun SAIDs?
Alamomin SAIDs yawanci suna farawa ne tun suna yara. Babban kuma mafi yawan alamun cutar ita ce zazzabin lokaci-lokaci . A lokacin zazzaɓi, mutane na iya zama cikin koshin lafiya kuma ba su da alamun cutar. Duk da haka, akwai wasu alamomin da suka shafi kowace irin SAID. Bari mu ga menene su:
- FMF: Wannan na iya haifar da kumburi da ciwo mai tsanani a cikin ciki, ƙirji, da kuma gidajen abinci na yaron . Haka kuma yana iya samun kuraje a ƙafafu ko idon sawu.
- PFAPA: Wannan na iya haifar da ciwon makogwaro, ciwon baki, da kumburin ƙwayoyin lymph a wuya . Misali, idan yaronka yana nuna alamun kamar yawan tonsils da gyambon baki, yana iya zama PFAPA.
- TARKO: Wannan na iya haifar da sanyi da ciwon tsoka a cikin gangar jiki/jijiyoyi da hannaye . Hakanan yana iya haifar da kuraje masu zafi waɗanda ke farawa a hannuwa da ƙafafu kuma suna bazuwa cikin jiki.
- MKD: Wannan na iya haifar da alamu kamar sanyi, ciwon kai, ciwon ciki, rashin ci, da kuma alamun mura .
- Cututtukan NLRP3: Wannan yanayin na iya haifar da kuraje a fata, ciwon kai, rashin lafiya, ciwon gaɓɓai, da kuma ruwan hoda na ido/ƙonewa .
- AOSD: Wannan yanayi ne da ke tattare da kuraje a fata, ciwon gaɓɓai, da ciwon tsoka . Wasu mutane kuma na iya fuskantar ciwon makogwaro, ciwon ciki, gajiya, da kuma rashin lafiya.
- Ciwon Blau: Wannan na iya haifar da raunuka a fata a hannun jaririnka, ƙafafuwansa, ko tsakiyarsa . Hakanan yana iya haifar da ciwon gaɓoɓi da ciwon ido .
Mene ne musabbabin SAIDs?
Yawancin SAIDs cututtuka ne na kwayoyin halitta . Wato, wani takamaiman maye gurbi (bambanci) a cikin wani takamaiman kwayar halitta yana haifar da kowace cuta. Ka yi tunanin cewa jikinmu yana da jerin umarni (kwayoyin halitta) waɗanda ke gaya mana yadda ake yin kowane aiki, don haka idan harafi ɗaya a cikin wannan littafin ba daidai ba ne, zai iya sa sauran aikin ya yi kuskure.
Ga manyan nau'ikan SAIDs da kwayoyin halittar da ke da alaƙa da su:
- FMF:Kwayar halittar 'MEFV' ita ce ke ba da umarni kan yadda ake yin furotin `(pyrin)`.
- PFAPA: Ba a tantance ainihin dalilin hakan ba tukuna .
- TARKO: Kwayar halittar `TNFRSF1A`. Wannan yana ba da umarni ga samar da furotin da ake kira `(mai karɓar ƙwayoyin cuta na tumor - TNFR)`.
- MDK: Kwayar halitta da ake kira 'MVK'. Wannan yana ba da umarni ga samar da furotin da ake kira `(mevalonic kinase)`.
- Cututtukan NLRP3: Kwayar halittar `NLRP3`. Wannan yana ba da umarni ga samar da furotin da ake kira `(cryopirin)`.
- AOSD: Ba a gano ainihin dalilin hakan ba tukuna .
- Ciwon Blau: Kwayar halittar `NOD2`. Wannan yana ba da umarni ga samar da furotin mai suna `(NOD2)`.
Yana da muhimmanci a fahimci cewa idan waɗannan abubuwan kwayoyin halitta ne suka haifar da su, ba laifin iyaye ba ne. Waɗannan matakai ne masu rikitarwa na halitta.
Matsalolin da SAIDs ke haifarwa
Yana da matuƙar muhimmanci a sami ingantaccen magani ga waɗannan yanayi. Domin idan kumburi ya ci gaba a jiki, zai iya haifar da wata cuta da ake kira `(Amyloidosis). `(Amyloidosis)` wani sinadari ne da ke taruwa a cikin kodan . Wannan na iya haifar da lalacewa ta dindindin ga kodan . Saboda haka, idan akwai alamu, yana da mahimmanci a nemi shawarar likita nan da nan.
Ta yaya ake gane SAIDs?
Gaskiya ne, gano cutar SAIDs na iya zama ɗan ƙalubale domin alamun na iya kama da na wasu cututtuka masu tsanani, kamar lupus ko lymphoma. Saboda haka, yana da mahimmanci a ga likita wanda ke da horo na musamman kan cututtukan kumburi (likitan rheumatologist) don gano da kuma kula da lafiyar ɗanku daidai.
Likitan rheumatologist na ɗanka zai yi amfani da abubuwa da dama don gano cutar SAIDs. Zai/za ta yi tambaya game da alamun ɗanka da kuma ko akwai wani a cikin iyalinka da ya taɓa samun waɗannan yanayi (tarihin iyali). Likitan zai iya zargin cewa ɗanka yana da Ciwon Zazzaɓi na Lokaci-lokaci idan:
- Idan kana yawan zazzabi
- Idan wani a cikin iyali yana da tarihin zazzabin lokaci-lokaci kamar wannan
- Idan kana cikin ƙungiyar mutanen da ke fama da irin wannan zazzaɓi
Wadanne gwaje-gwaje ake amfani da su?
Likitanka zai iya ba da shawarar gwaje-gwaje da dama don tabbatar da ganewar cutar. Waɗannan na iya haɗawa da:
- Gwaje-gwajen dakin gwaje-gwaje: Gwaje-gwaje kamar su `(C-reactive protein - CRP)` da `(Complete Blood Count - CBC)` na iya duba kumburi a jiki. Waɗannan gwaje-gwajen suna `(positive)` idan akwai zazzabi, kuma suna komawa ga dabi'un da suka dace idan zazzabin ya tafi.
- Gwajin fitsari:Ana iya yin gwajin furotin na fitsari don duba yawan furotin a cikin fitsari. A cikin MKD, gwajin fitsari don gano acid na halitta zai nuna yawan mevalonic acid.
- Gwajin Halittar Halitta: Wannan zai iya duba bambance-bambancen kwayoyin halitta. Duk da haka, wasu yara da ke dauke da SAIDs ba za a iya gano bambancin kwayoyin halitta ba. Saboda haka, ko da sakamakon gwajin ya kasance "mara kyau" ba, ba za a iya kawar da yiwuwar SAID ba.
Yaya ake kula da SAIDs?
Maganin SAIDs ya bambanta dangane da nau'in da tsananin cutar . Ko da yake ba za a iya warkar da waɗannan cututtukan gaba ɗaya ba, ana iya sarrafa alamun yaron sosai ta hanyar amfani da magunguna . Misali, idan yaronka yana samun waɗannan mura sau da yawa a shekara, magungunan rage radadi da magungunan hana kumburi marasa steroidal (NSAIDs) galibi suna iya magance alamun. Duk da haka, idan cutar ta fi tsanani, likita zai iya ba da shawarar wasu zaɓuɓɓukan magani.
Ga wasu irin waɗannan magunguna:
- FMF: Ana iya magance wannan da magani mai suna `(Colchicine)` don rage kumburi. Idan ba za ku iya shan `(Colchicine)` ba, za ku iya gwada nau'in magani mai suna `(Biologic)` mai suna `(Canakinumab)`.
- PFAPA: Ana iya rage yawan PFAPA ta hanyar ba wa steroids (sau da yawa prednisone). Wasu yara sun sami damar sarrafa alamun su ta hanyar amfani da cimetidine, wani magani da ake amfani da shi don magance ciwon ciki.
- TARKO: Maganin `(Canakinumab)` yana da tasiri sosai ga TARKO. Haka kuma, magungunan hana kumburi da likita ya rubuta kamar `(Glucocorticoids)` suma suna iya taimakawa wajen rage alamun.
- MKD: `(Canakinumab)` kyakkyawan zaɓi ne don maganin MKD. Amfani da `(NSAIDs)` ko `(Steroids)` a lokacin zazzabi na iya taimakawa.
- Cututtukan NLRP3: Sauran magungunan "Immunomodulators" kamar "Canakinumab" da "Rilonacept" da "Anakinra" an yi amfani da su cikin nasara don magance cututtukan NLRP3.
- AOSD: Ana amfani da nau'ikan magungunan rage kumburi daban-daban don AOSD. Waɗannan sun haɗa da `(Steroids)`, `(Magungunan rage kumburi masu canza cututtuka - DMARDs)`, da `(Biologics)`.
- Ciwon Blau: Dangane da alamun yaron, ana iya gwada magungunan rage garkuwar jiki, magungunan hana ciwon tumor necrosis factor (TNF), da/ko magungunan ido na waje.
Shin yanayin SAIDs yana inganta da kansa?
Wasu SAIDs na iya ɗaukar tsawon rai . Wasu kuma na iya ɗaukar shekaru kaɗan kuma su inganta da tsufa. Duk da cewa wasu yanayi na rayuwa ne, yawan zazzabi na iya raguwa akan lokaci kuma alamun na iya zama ƙasa da tsanani . Likitanka zai iya ba ka takamaiman bayani game da takamaiman yanayin ɗanka.
Kula da yaro mai fama da SAID na iya zama ƙalubale. Wataƙila kai ne ka SAID da kanka, amma za ka iya amfani da abubuwan da ka fuskanta don taimaka wa yaronka ya kula da shi da kuma taimaka masa ya jure wannan yanayin rayuwa.
Abu mafi mahimmanci shine a nemi magani daga kwararru waɗanda suka san sarkakiyar SAIDs. Za su iya taimakawa wajen magance alamun cutar da kuma taimaka masa ya sami mafi kyawun lokacin yarinta.
Muhimman abubuwan da ya kamata a tuna (Saƙon Kai Gida)
To, bari mu taƙaita wasu daga cikin abubuwan da ya kamata ku tuna daga abin da muka tattauna.
- Idan yaronka yana da zazzabi mai yawan gaske wanda ba a san dalilinsa ba , yi magana da likita game da shi. Zai iya zama alamar SAID.
- SAIDs matsala ce ta tsarin garkuwar jiki na asali , ba cuta ce da aka saba kamuwa da ita ba.
- Waɗannan sun bambanta da cututtukan "Autoimmune" .
- A mafi yawan lokuta, waɗannan abubuwan suna faruwa ne sakamakon abubuwan da suka shafi kwayoyin halitta .
- Yana da mahimmanci a ga likitan Rheumatologist don samun cikakken ganewar asali.
- Jiyya na iya sarrafa alamun cutar da kyau .
- Maganin da wuri yana da mahimmanci don hana lalacewar koda.
Idan kuna da wasu tambayoyi game da wannan, kada ku ji tsoron tambayar likitan iyali ko likitan yara. Za su iya taimaka muku sosai.
` SAIDs, zazzabin gado, yawan zazzabi, zazzabi ga yara, tsarin garkuwar jiki, cututtukan gado, likitan rheumatologist











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