Shin kun taɓa jin labarin wata cuta mai ban mamaki da ke shafar gefe ɗaya na kwakwalwa kuma tana ƙara muni akan lokaci? Wataƙila ƙaramin yaronku yana da saurin suma, rauni a gefe ɗaya na jiki, da wahalar magana? Abin fahimta ne a ji tsoro idan aka ji labarin irin wannan. A yau za mu yi magana game da wata cuta mai wuya amma mai mahimmanci. Ana kiranta da Rasmussen's Encephalitis.
Menene Rasmussen's Encephalitis?
A taƙaice dai, Rasmussen's Encephalitis wani kumburi ne mai ci gaba da daɗewa a ɗaya daga cikin ɓangarorin kwakwalwa guda biyu, wato a gefe ɗaya na kwakwalwa . A taƙaice dai, yanayi ne da ƙwayoyin kwakwalwa ke kumbura da ja. Wannan kuma ana kiransa Rasmussen syndrome.
Idan wani ɓangare na kwakwalwa ya yi kumburi ta wannan hanyar, yana fara haifar da suma akai-akai. A fannin likitanci, muna kuma kiran wannan farfadiya. Wannan ba kawai kumburi ba ne, yana fara lalata kwakwalwa kaɗan-kaɗan, kuma lalacewar tana da wahalar gyarawa. Bayan lokaci, aikin gefe ɗaya na jiki yana raguwa idan aka kwatanta da ɓangaren kwakwalwa da ya lalace. Ka yi tunanin, wannan ya shafi ɓangaren dama na kwakwalwa, sannan ɓangaren hagu na jiki na iya rasa ƙarfinsa, ya sami wahalar magana, kuma ya rasa ƙwaƙwalwar ajiya.
Likita mai suna Theodore Rasmussen ne ya fara gano wannan cuta a shekarar 1958. Don haka, ana kiranta da Rasmussen encephalitis don girmama shi.
Yaya wannan yanayin yake da wuya?
Wannan cuta ce da ba kasafai ake samunta ba . A cewar masu bincike, mutane biyu ne kawai cikin kowane mutum dubu ɗari goma ke iya kamuwa da wannan cutar. Wannan yana nufin ba kasafai ake samunta ba.
Wannan cuta ta fi shafar ƙananan yara tsakanin shekaru 2 zuwa 10. Duk da haka, wani lokacin matasa da manya na iya kamuwa da wannan yanayin.
Mene ne alamun cutar Rasmussen's Encephalitis?
Alamar farko ta wannan cuta sau da yawa ita ce ta suma. Wannan takura na iya zuwa ta hanyoyi daban-daban.
Alamomin farko
- Mummunan farfadiya ta tonic-clonic: A cikin wannan, tsokoki a ɓangarorin jiki biyu suna matsewa da ƙarfi, kuma ana iya rasa sani.
- Fargaba a hankali : A wannan yanayin, kana sane da abin da ke faruwa. Za ka iya jin ƙara a hannu ɗaya ko ƙafa ɗaya, ko kuma jin suma a wani yanki.
- Matsalar da ke damun hankali: Wannan wata irin suma ce da ke farawa daga gefe ɗaya na kwakwalwa, tana haifar da ɗan asarar sani, ko ma asarar sani gaba ɗaya.
Abu mafi mahimmanci shine, idan kai ko yaronka yana da irin wannan matsala,Kana buƙatar ganin likita da wuri-wuri. Wannan abu ne da dole ne ka yi.
Wani abu kuma shi ne cewa ɗan rauni a hannun yaro ko ƙafarsa na iya zama alamar farko ta wannan cutar.
Alamomin da ke bayyana akan lokaci
Farfadowar farko tana ƙaruwa a hankali. Kimanin rabin mutanen da ke fama da cutar Rasmussen encephalitis suna kamuwa da wata cuta da ake kira `(Epilepsia Partitalis Continua - EPC)`. Wannan yana nufin farfadowar tana ci gaba na ɗan lokaci ko mintuna kaɗan. Waɗannan farfadowar suna da matuƙar wahala a shawo kansu da magunguna na yau da kullun (ba za a iya magance su ba).
Alamomin da ke ƙasa suna fara bayyana cikin 'yan watanni, ko ma shekara ɗaya ko biyu, bayan kamuwa ta farko:
- Ragewar hankali a hankali : Wannan yana nufin cewa abubuwa kamar tunani, fahimta, da ƙwaƙwalwa na iya raguwa.
- Rashin motsi a hankali a gefe ɗaya na jiki (hemiparesis): Misali, hannun dama da ƙafar dama na iya yin rauni. Bayan lokaci, wannan na iya ci gaba zuwa gurguwa gaba ɗaya (hemiplegia).
- Aphasia : Wannan yana faruwa ne lokacin da cutar ta shafi ɓangaren kwakwalwa wanda ke da alhakin magana (yawanci gefen hagu).
- Rashin gani gaba ɗaya a gefe ɗaya (hemianopsia): Kamar rasa gani ne kawai a gefe ɗaya na ido.
Ga yawancin mutane, watanni 8 zuwa 12 na farko bayan fara cutar Rasmussen encephalitis su ne mafi muni . Bayan haka, cutar na iya zama kamar ta ragu ko ma ta tsaya. Duk da haka, lalacewar kwakwalwa ta dindindin ce kuma ba za a iya magance ta ba.
Menene dalilin hakan?
Gaskiya ne, masana kimiyya har yanzu ba su san ainihin abin da ke haifar da cutar Rasmussen encephalitis ba . Amma suna da manyan ka'idoji guda biyu:
1. Cututtukan garkuwar jiki : Wannan shine lokacin da garkuwar jikinmu, tsarin da ke kare mu daga cututtuka, ke kai hari ga ƙwayoyin halittarmu masu kyau. Don haka, ana tsammanin Rasmussen encephalitis wata cuta ce makamanciyar cutar garkuwar jiki da ke kai hari ga wani ɓangare na kwakwalwa kawai.
2. Kamuwa da cuta : Yana yiwuwa wata kwayar cuta da ba a san ko ta wanene ba ta shiga kwakwalwa ta haifar da wannan yanayin. Duk da haka, masu bincike sun binciki kwakwalwar mutanen da suka kamu da cutar, amma har yanzu ba su gano takamaiman kwayar cutar ba.
Ta yaya ake gane wannan cuta? (Ganewar asali)
Likitoci suna gano cutar Rasmussen encephalitis bisa ga alamun ɗanku da kuma sakamakon gwaje-gwaje na musamman da dama.
- Duban MRI (Magnetic Resonance Imaging - MRI): Wannan zai iya nuna ko ƙwayar kwakwalwa a gefe ɗaya na kwakwalwar yaron ta yi rauni ko ta yi rauni. Idan ɓangaren kwakwalwa ɗaya ya yi rauni a hankali tsawon watanni ko shekaru da yawa, to babbar alama ce ta cutar.
- Gwajin EEGElectroencephalography (EEG): Wannan kuma zai iya taimakawa wajen gano yanayin. Gwajin EEG yana yin rikodin ayyukan lantarki a cikin kwakwalwa. Wannan zai iya taimakawa wajen tantance yadda farfadiya ke faruwa da kuma ko kwakwalwa tana aiki yadda ya kamata.
Don haka, likitoci sun tabbatar da kamuwa da cutar Rasmussen encephalitis ta hanyar haɗa alamun cutar da sakamakon binciken, kamar atrophy na gefe ɗaya na kwakwalwa .
Menene maganin Rasmussen's Encephalitis?
Abin takaici, har yanzu babu maganin cutar Rasmussen encephalitis, don haka babban burin magani shine a shawo kan alamun cutar da kuma rage kumburi a kwakwalwa.
Ana iya yin waɗannan a matsayin magani:
Magungunan hana afkuwa
Waɗannan magunguna ba za su iya dakatar da farfaɗiyar da Rasmussen encephalitis ke haifarwa gaba ɗaya ba. Duk da haka, suna iya taimakawa wajen rage yawan farfaɗiyar da kuma tsananinta .
Maganin rigakafi
Maganin rigakafi, wanda ya ƙunshi ba da magunguna waɗanda ke canza aikin tsarin garkuwar jiki, zai iya taimakawa wajen shawo kan hare-haren da kuma rage lalacewar kwakwalwa daga tsarin garkuwar jiki tun farkon cutar.
Tiyatar kwakwalwa
Hanya mafi inganci don magance matsalar rashin daidaituwa a cikin cutar Rasmussen encephalitis ita ce tiyatar kwakwalwa . Wannan ana kiranta hemispherectomy. Wannan tiyatar ta ƙunshi raba ɓangaren kwakwalwar yaron da abin ya shafa, wato, raba ɓangaren kwakwalwa daga ɗayan gefen, ko cire shi gaba ɗaya.
A mafi yawan lokuta, yaran da aka yi musu wannan tiyatar sun riga sun rasa aiki sosai a ɓangaren kwakwalwa da abin ya shafa. Saboda haka, haɗarin ƙarin rasa aiki bayan tiyatar ba shi da yawa. Likitoci suna la'akari da tiyata ne kawai idan fa'idodin sun fi haɗarin .
Menene makomar wannan cuta? (Hasashen)
Hasashen kamuwa da cutar Rasmussen encephalitis na iya bambanta daga mutum zuwa mutum . Ga wasu mutane, cutar na iya daina yaɗuwa bayan tiyata kuma yawan kamuwa da ita na iya daidaita.
Duk da haka, mutane da yawa na iya fuskantar wani irin gurguwa, rashin hankali da tunawa, da kuma wahalar magana. Ba kasafai ake samun cutar ba, wadda ke iya yaɗuwa zuwa wasu sassan kwakwalwa.
Za a iya hana kamuwa da cutar Rasmussen's Encephalitis?
Domin kuwa cutar Rasmussen encephalitis cuta ce da ba kasafai ake samunta ba kuma har yanzu ba a san ainihin musabbabinta ba, babu abin da za mu iya yi don hana ta .
Domin kuwa yanayi ne mai wuya, yana da wuya masana kimiyya su yi nazarinsa. Amma labari mai daɗi shine akwai magunguna da za su iya taimakawa wajen shawo kan farfadiya da sauran alamu. Akwai ma gwaje-gwajen asibiti da ɗanka zai iya shiga ciki. Abu ne na al'ada a ji damuwa idan aka gano cutar kamar haka. Amma ku tuna, ƙungiyar likitocin yaronku tana nan don taimaka muku da ɗanku ta kowace hanya mai yiwuwa .
Bari mu tuna (Saƙon Kai Gida)
Ciwon kwakwalwa na Rasmussen (Rasmussen's Encephalitis) cuta ce mai matuƙar wuya, amma mai yuwuwa ta zama mai tsanani.
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* A wannan yanayin, kumburi yana faruwa a gefe ɗaya na kwakwalwa, wanda ke haifar da suma akai-akai, gurguwa a gefe ɗaya na jiki, da wahalar magana.
* Yara ƙanana ne suka fi shan wahala.
* Idan ka lura da alamun cutar, ka nemi likita nan take.
* Magani na iya sarrafa alamun cutar.
* Ba kai kaɗai ba ne a irin wannan lokaci, nemi taimako daga likitoci da waɗanda suka fi kusa da kai.
Ina fatan wannan bayanin zai amfane ku. Idan kuna da wasu tambayoyi, kada ku yi jinkirin yin magana da likita.
Rasmussen encephalitis, cututtukan kwakwalwa, farfadiya, fit, yara, kumburin kwakwalwa, cututtukan jijiyoyi











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