Ua noʻonoʻo paha ʻoe i nā puka liʻiliʻi i loko o kou puʻuwai? ʻAʻole paha mākou e noʻonoʻo i ke koʻikoʻi o kēia mau mea i ko mākou ola o kēlā me kēia lā. Akā, i kekahi manawa hele mai mākou i kēia ao me nā loli liʻiliʻi i loko o kēia mau puka liʻiliʻi, ʻo ia hoʻi, nā valves o ka puʻuwai. I kēia lā e kamaʻilio mākou e pili ana i kekahi ʻano maʻi puʻuwai kūikawā. Ua kapa ʻia kēia ʻo Bicuspid Aortic Valve Disease . Mai makaʻu, ʻo ka mea nui loa, ʻo ia ka makaʻala i kēia.
He aha kēia valve aortic bicuspid? I ka ʻōlelo maʻalahi...
E noʻonoʻo i kou puʻuwai e like me ka pamu wai. Hoʻopuka kēia pamu i ke koko maʻemaʻe a piha i ka oxygen ma kou kino holoʻokoʻa. Aia kahi puka koʻikoʻi loa kahi e kahe ai ke koko mai ka puʻuwai a i ke kīʻaha koko nui loa o ke kino, ʻo ia hoʻi ka aorta. Kāhea mākou i kēia puka ʻo ka valve aortic .
ʻO ka maʻamau, i loko o ke kanaka olakino, ʻekolu ʻāpana o ka valve aortic, a i ʻole nā ʻāpana, e like me ʻekolu lau ma ka puka. Hāmama a pani pono kēia mau ʻāpana ʻekolu e ʻae i ke koko e kahe i hoʻokahi wale nō ʻaoʻao - mai ka puʻuwai a i ka aorta. Pale kēia mau ʻāpana i ke koko mai ke kahe hou ʻana i loko o ka puʻuwai.
Eia nō naʻe, ʻo ke kanaka me ka `Bicuspid Aortic Valve` he ʻelua cusps i loko o ka `Aortic Valve`. ʻO ``Bi'' ke ʻano he ``ʻelua'' a ʻo ``cuspid'' ke ʻano he ``leaflet''. No laila, ua loaʻa ka inoa mai ka ʻoiaʻiʻo he ʻelua cusps. He ʻano ``congenital'' kēia, ʻo ia hoʻi, aia ia i ka wā hānau.
E noʻonoʻo, he aha ka mea e hana ʻia inā he ʻelua lau o ka puka ma kahi o ʻekolu? Malia paha ʻaʻole e wehe pono ka puka, a i ʻole ʻaʻole paha e pani pono. ʻO ia ka mea e hana ʻia i kēia kiwikā.
- Inā ʻaʻole e wehe pono ka valve: Lilo ia i mea paʻakikī no ke koko ke kahe i mua, ʻo ia hoʻi, i loko o ka aorta. Ua kapa ʻia kēia ʻo 'Aortic Stenosis' , ʻo ia hoʻi ka haiki ʻana o ka valve.
- Inā ʻaʻole pani pono ka valve: Hoʻi hou ke koko i loko o ka puʻuwai mai ka aorta. Ua kapa ʻia kēia he aortic regurgitation , ʻo ia hoʻi ke kahe hou ʻana o ke koko ma o ka valve.
Ua loaʻa paha iā ʻoe kēia 'Aortic Stenosis' a i ʻole 'Aortic Regurgitation' no nā makahiki, a ʻaʻole paha ʻoe i ʻike e pili ana i ia mea. ʻAʻole paha ʻoe e hōʻike i kekahi mau hōʻailona. No ka mea, ke hana nei kāu 'Aortic Valve' i kāna hana e like me ka hiki. Eia naʻe, ʻaʻole ia e like me ka pono o kahi valve me ʻekolu mau pepa liʻiliʻi.
I ka hala ʻana o ka manawa, hoʻoikaika kēia valve bicuspid i kou puʻuwai. Hiki i kēia ke alakaʻi i nā pilikia koʻikoʻi.Hiki ke hana. ʻOiai paha he mea paʻakikī ke ʻae i kēia ʻoiaʻiʻo, ʻo ke aʻo ʻana e pili ana i kēia kūlana e kōkua iā ʻoe e hoʻomaopopo maikaʻi iā ia.
Pehea ke koʻikoʻi o ka loaʻa ʻana o kahi valve aortic bicuspid?
ʻAʻole nā kānaka a pau me ka bicuspid aortic valve e loaʻa nā pilikia. Eia nō naʻe, ma kahi o hoʻokahi i loko o ʻekolu mau kānaka e loaʻa nā pilikia. I kekahi manawa hiki i kēia ke lilo i mea koʻikoʻi loa a hiki ke hoʻoweliweli i ke ola . ʻO ia ke kumu e hoʻomau ai ka poʻe i ʻike ʻia me ka maʻi bicuspid aortic valve i nā hoʻokolohua lapaʻau a me ka hahai ʻana.
Hoʻopilikia kēia maʻi ma waena o 1% a me 2% o ka heluna kanaka maʻamau. ʻOi aku ka pālua o ka maʻamau i nā kāne ma mua o nā wahine. ʻO ka poʻe me ka Turner syndrome kekahi i ka nui o ka pilikia o ka hoʻomohala ʻana i kēia ʻano maʻi puʻuwai , ʻoiai ka bicuspid regurgitation.
I ka manawa pinepine, ʻaʻole paha ʻoe e ʻike i nā hōʻailona a hiki i ka wā e holomua loa ai ka maʻi a i ʻole kahi pilikia olakino. Eia nō naʻe, hiki i nā hoʻokolohua kiʻi ke ʻike i nā loli liʻiliʻi ma mua o kou ʻike ʻana i nā hōʻailona. A hiki i nā holomua i ka mālama ʻana ke kōkua iā ʻoe e ola i kahi ola lōʻihi a olakino hoʻi .
He aha nā hōʻailona o kēia maʻi?
E like me ka mea i ʻōlelo ʻia ma mua, ʻaʻole paha ʻoe e loaʻa i kekahi mau hōʻailona. Hiki iā ʻoe ke ola no nā makahiki me ka ʻike ʻole he loli liʻiliʻi kēia i loko o kou puʻuwai. Akā i ka hala ʻana o ka manawa, e hoʻomaka nā hōʻailona e ʻike ʻia ma muli o ka 'Aortic Regurgitation' a i ʻole 'Aortic Stenosis'.
Nā keiki liʻiliʻi a me nā pēpē:
Inā he bicuspid aortic valve kāu pēpē, i kekahi mau hihia koʻikoʻi, hiki ke ʻike ʻia nā hōʻailona ma hope koke iho o ka hānau ʻana. Akā i ka hapanui o ka manawa, ʻaʻole ʻike ʻia kēia mau hōʻailona a hiki i ka wā ma hope.
- ʻIli keʻokeʻo a polū paha (Cyanosis)
- Ka hoʻokaʻulua ʻole e ʻai, nā pilikia o ka piʻi ʻana o ke kaumaha
Nā hōʻailona i nā mākua:
- Manaʻo luhi (ʻo kēia ka hōʻailona maʻamau)
- ʻEha a ʻeha paha ka umauma
- Pōʻino a i ʻole ka nawaliwali
- Nā palpitations o ka puʻuwai
- Ka paʻakikī o ka hanu ʻana , ʻoiai i ka wā o ka hana
ʻIke wale ka poʻe he nui he valve aortic bicuspid ko lākou ma hope o kahi hoʻāʻo lapaʻau. ʻO kēia no ka mea hiki ke maʻalahi ke ʻike ʻole ʻia nā hōʻailona. E ʻike paha kou ʻohana a i ʻole nā hoaaloha i ka ʻokoʻa i loko ou ma mua o kou ʻike ʻana.
E noʻonoʻo i ka nui o ka hana hiki iā ʻoe ke hana i kahi lā maʻamau. E hoʻohālikelike iā ia me ka nui o kāu hana i hoʻokahi makahiki i hala, a i ʻole ʻeono mahina i hala. Ke luhi koke nei ʻoe i kēia manawa? Pono ʻoe i ka manawa hou aku e hoʻomaha ai? Inā pēlā, ʻo ia hoʻi ke hana ikaika nei kou puʻuwai e hoʻopau i ka hana.
ʻO ia ke kumu he mea nui loa ka mālama ʻana i nā manawa i hoʻonohonoho ʻia e kāu kauka . E kamaʻilio me kāu kauka e pili ana i nā loli āu e ʻike ai i kou ola o kēlā me kēia lā.
He aha ke kumu o ka valve aortic bicuspid?
ʻAʻole i loaʻa i nā kānaka noiʻi ke kumu pololei o ka valve aortic bicuspid. Eia nō naʻe, ʻo ia ke ʻano puʻuwai hānau maʻamau . Hoʻomaka ia i ka wā mua o ka hāpai ʻana .
He mea kēia i loaʻa mai nā hanauna mai?
Me he mea lā he mea hiki, akā, ʻaʻole maopopo loa i nā kānaka noiʻi nā kikoʻī.
Hiki ke holo ka Bicuspid Aortic Valve i loko o nā ʻohana. Inā loaʻa i kahi hoahānau pili koko (makua, keiki, kaikunāne/kaikuahine) o ʻoe kēia maʻi puʻuwai, e kamaʻilio me kāu kauka. Hiki iā lākou ke paipai i kekahi mau hoʻokolohua e nānā i ke ʻano a me ka hana o kou puʻuwai .
Inā he valve aortic bicuspid kou a ke hoʻolālā nei e hāpai, e kamaʻilio me kāu kauka. ʻOiai ʻaʻole hiki ke pale ʻia kēia ʻano, hiki iā ʻoe ke nānā i kāu hāpai ʻana a hoʻāʻo e ʻike i nā pilikia i ka wā mua .
He aha nā pilikia o kēia maʻi?
Inā ʻaʻole mālama ʻia, hiki i ka Bicuspid Aortic Valve Disease ke alakaʻi i nā pilikia koʻikoʻi. ʻO kekahi o lākou:
- ʻO ka hāʻule ʻana o ka puʻuwai: I ke ʻano o ka stenosis aortic, ʻo ia ka wā e haiki ai ka valve, pono ka puʻuwai e hana ikaika loa e pamu i ke koko. ʻO ka ventricle hema, ʻo ia hoʻi ke keʻena pamu nui o ka puʻuwai, ʻo ia hoʻi ka ventricle hema, e mānoanoa a lilo i mea nui. ʻAʻole hiki iā ia ke pamu pono i ke koko. I ka hala ʻana o ka manawa, hiki i kēia ke alakaʻi i ka hāʻule ʻana o ka puʻuwai. Hiki ke hoʻolalelale ʻia kēia kaʻina hana inā he mau mea pilikia ʻē aʻe, e like me ka puhi paka a me ke cholesterol kiʻekiʻe.
- ʻO ka haki ʻana o ka Aortic Aneurysm a me ka dissection Aortic:Ma kahi o hoʻokahi o ʻekolu poʻe me ka valve aortic bicuspid e loaʻa paha kahi aorta dilated, a i ʻole hoʻonui ʻia, ma luna o ka valve. I ka wā e hoʻonui ai ka aorta, nalowale ka ikaika o kona mau paia a loli ke ʻano. I ka hopena, hiki i kēia ke alakaʻi i kahi aneurysm aortic, kahi puʻupuʻu e like me ka balloon i loko o ka paia o ka aorta. Inā lilo kēia aneurysm i mea nui loa, hiki iā ia ke haki a haehae paha i ka paia (aortic dissection) . He mau pilikia hoʻoweliweli ola kēia.
Pehea e ʻike ʻia ai ka valve aortic bicuspid?
I kekahi manawa, hiki i ke kauka ke ʻike i ke kūlana i ka wā o ka ultrasound prenatal cardiac i ka wā hāpai. I kekahi manawa, ʻike ʻia kahi valve aortic bicuspid i ka wā o nā hoʻokolohua i hana ʻia i ka wā e loaʻa ai i kahi pēpē nā hōʻailona ma muli o kekahi maʻi puʻuwai ʻē aʻe.
Eia nō naʻe, nui ka poʻe e hele i nā makahiki me ka ʻike ʻole he loaʻa iā lākou kēia maʻi. ʻO ka hōʻailona mua paha he murmur puʻuwai , he kani ʻē i loko o ka puʻuwai a kāu kauka e lohe ai me kahi stethoscope. A laila, hiki i kāu kauka ke hana i nā hoʻokolohua kiʻi e nānā i ke ʻano a me ka hana o ka puʻuwai.
He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia?
Hiki i kāu kauka ke nānā i kou puʻuwai a hana i kēia mau hoʻokolohua e ʻike ai inā he valve aortic bicuspid kou:
- Echocardiogram (Echocardiogram - echo) : ʻAe kēia iā ʻoe e ʻike i nā kiʻi ola o ka puʻuwai.
- Nā scan CT (Computed Tomography scans) : Lawe kēia i nā kiʻi ʻokiʻoki o ka puʻuwai.
- `Heart MRI` (Magnetic Resonance Imaging) : Hiki i kēia ke kiʻi i nā kiʻi kikoʻī o ka puʻuwai.
Hiki paha iā lākou ke kuhikuhi iā ʻoe no ka hoʻāʻo genetic .
Pehea e mālama ʻia ai ka Bicuspid Aortic Valve?
Hiki i nā lāʻau lapaʻau e like me nā beta-blockers a me nā diuretics ke kōkua i ka kaohi ʻana i nā hōʻailona. Akā, ʻaʻole lākou e ho'ōla loa i ke kūlana . Ma kahi o ʻehā o kēlā me kēia ʻelima mau kānaka me ka Bicuspid Aortic Valve Disease e pono ai ke ʻoki ʻana e mālama ai. E hoʻoponopono kāu kauka ʻoki i kāu valve aortic a i ʻole e hoʻokomo i kahi valve hou . Hiki iā lākou ke hoʻoponopono i nā pilikia ʻē aʻe, e like me ka aneurysm, i ka wā o ke ʻoki like.
E loiloi kāu kauka i kou kūlana, e hana i kekahi mau hoʻokolohua, a e kūkākūkā i kāu mau koho lapaʻau me ʻoe. ʻO ka lāʻau lapaʻau āu e loaʻa ai e pili ana i ke kūlana o kāu valve aortic a me ka aorta. E noʻonoʻo pū lākou i kou olakino puʻuwai holoʻokoʻa, ka makahiki, a me nā kūlana olakino ʻē aʻe.
ʻO ka mea nui loa, ʻo ia ke hana ʻoki kino koke, ma mua o ka hōʻino mau ʻana o ka puʻuwai. ʻOiai inā ʻaʻohe ou hōʻailona, makemake paha kāu kauka e mālama i ka pilikia i kēia manawa e pale aku i nā pilikia e hiki mai ana. He ʻokoʻa ka manawa maikaʻi loa no kēlā me kēia kanaka. E kūkākūkā kāu hui lapaʻau i kāu mau koho me ʻoe.
Ua hoʻomaikaʻi ka ʻenehana hou i nā hopena a ua hōʻemi i nā pilikia. Hiki i nā poʻe he nui ke hoʻohana i nā ʻano hana minimally invasive ma kahi o ke ʻoki puʻuwai hāmama kuʻuna.
ʻO ka ʻokoʻa ma waena o ke ʻoki ʻana i ka valve aortic kuʻuna a me ke ʻoki ʻana minimally invasive
- ʻO ke ʻoki ʻana i ka valve aortic kuʻuna (puʻuwai hāmama): Pili kēia i ka hana ʻana i kahi ʻoki ʻana he 6-8 ʻīniha ma waenakonu o ka umauma, ma ka sternum. Hoʻokaʻawale ke kauka lapaʻau i ka sternum i ʻelua e komo pololei i ka puʻuwai.
- ʻO ke ʻoki ʻana i ka valve aortic minimally invasive: Pili kēia i ka hana ʻana i kahi ʻoki liʻiliʻi, "J"-ʻano ma kahi o 2-4 ʻīniha ka lōʻihi. Hiki ke hana ʻia kēia ʻoki ma ka piko o ka iwi umauma a i ʻole ma waena o nā iwi ʻaoʻao. ʻAʻole pono ke kauka lapaʻau e wehe i ka umauma holoʻokoʻa. Hoʻemi kēia ʻano hana i ke kahe koko, ʻae i ka noho wikiwiki ʻana i ka haukapila, a hiki ke hoʻopōkole i ka manawa hoʻōla.
Ka Hoʻoponopono ʻana i ka Valve Aortic a i ʻole ke Hoʻololi ʻana i ka Valve Aortic?
- Hoʻoponopono Valve Aortic: He kaʻina hana kēia e hoʻoponopono ai i kāu valve me ka ʻole o ka hoʻololi ʻana. He koho maikaʻi kēia no ka poʻe me ka regurgitation aortic (ke kahe ʻana o ke koko mai ka valve). Eia naʻe, ʻaʻole hiki iā ia ke mālama i ka stenosis aortic (ka haiki ʻana o ka valve). Hiki i nā kauka ke hana pinepine i kēia kaʻina hana minimally invasive ma o kahi ʻoki "J". Hoʻololi hou ke kauka i nā pepa o kāu valve aortic e kōkua iā lākou e wehe a pani pono.
- Hoʻololi Valve Aortic: Pili kēia i ka wehe ʻana i kāu valve hiki ʻole ke hoʻoponopono hou ʻia a hoʻololi iā ia me kahi mea hou. Hiki i nā kauka lapaʻau ke hoʻololi i kāu valve ma o ke ʻoki kino hāmama kuʻuna a i ʻole ma o ke kaʻina hana minimally invasive i kapa ʻia ʻo Transcatheter Aortic Valve Replacement (TAVR) .
ʻO ka kiwikā hou e hoʻokomo ʻia ai iā ʻoe he 'kiwikā biological' a i ʻole he 'kiwikā mechanical' .
- `Kiwikā olaola`:Hoʻohana nā kauka lapaʻau i kēia ʻano kiwikā i 80% o ka manawa. Hana ʻia kēia kiwikā mai nā ʻiʻo puaʻa a bipi paha. He palekana a mau no ka manawa lōʻihi. Eia nō naʻe, ma hope o kahi 10 mau makahiki, pono paha ʻoe e hana hou i kahi ʻoki kino e pani ai i ka kiwikā.
- Kiwikā mīkini: He paʻa loa kēia kiwikā hana a hiki ke mau i kou ola a pau. Eia nō naʻe, i mea e hana pono ai, pono ʻoe e lawe i nā lāʻau hoʻokahe koko no ke koena o kou ola .
Makemake ka poʻe he nui i kahi valve biological no ka mea ʻaʻole pono lākou e lawe i nā lāʻau hoʻokahe koko. Akā pili ia i kou makahiki, nā kūlana olakino ʻē aʻe, a me nā makemake pilikino. E kamaʻilio kāu kauka me ʻoe e pili ana i kēia mau koho a kōkua iā ʻoe e hoʻoholo i ka mea maikaʻi loa iā ʻoe.
ʻO kekahi koho no ka hoʻololi ʻana i ka valve ʻo ia ke kaʻina hana Ross (i ʻike ʻia hoʻi ʻo ke kaʻina hana hoʻololi) . Pili kēia i ka lawe ʻana i kāu valve pulmonary a hoʻololi iā ia me kāu valve aortic. He koho maikaʻi paha kēia inā ʻoe ma lalo o 50 mau makahiki a makemake ʻoe e pale i ka lawe ʻana i nā lāʻau hoʻokahe koko no ka manawa lōʻihi.
Nā pilikia o ka mālama ʻana
Ma keʻano laulā, haʻahaʻa ka pilikia o nā pilikia mai ke ʻoki ʻana i ka valve. Eia nō naʻe, hiki i nā pilikia ke komo pū me:
- Nā maʻi
- Ke kahe ʻana o ke koko
- Nā ʻūpā koko
- Hahau
- Maʻi hohola
- Nā ʻano ʻē o ka puʻuwai `(Arrhythmia)` (no ka manawa pōkole)
- Ka emi ʻana o ka hana o nā puʻupaʻa (no kekahi manawa pōkole)
ʻEhia ka lōʻihi e ho'ōla ai mai kēia lāʻau lapaʻau?
Hiki i ke ʻoki hoʻololi valve aortic ke hala ma kahi o ʻelua a ʻekolu mahina e hoʻōla piha ai. Hiki i ke ʻoki hoʻoponopono valve aortic ke hala ma kahi o hoʻokahi a ʻelua mahina e hoʻōla piha ai.
Hiki ke pale ʻia ka valve aortic bicuspid?
ʻAʻohe ala e pale aku ai i ka valve aortic bicuspid. He mea hānau ia, ʻo ia hoʻi ua hānau ʻia ʻoe me ia. Eia nō naʻe, hiki iā ʻoe ke hana i nā hoʻololi i ke ʻano o ka nohona e hiki ai ke hōʻemi i kou pilikia o ka loaʻa ʻana o nā maʻi puʻuwai ʻē aʻe, e like me ka atherosclerosis a me ka maʻi artery coronary. Inā he valve aortic bicuspid kāu, e kamaʻilio me kāu kauka e pili ana i ka hoʻokele ʻana i kāu mau kumu pilikia maʻi puʻuwai. ʻO kēia mau mea:
- Ke koko kiʻekiʻe (Hypertension)
- ʻO ke kolesterol kiʻekiʻe `(Hyperlipidemia)`
- Maʻi diabetes
- Nā mea e pili ana i ke ʻano o ka nohona e like me nā huahana paka a me ka hoʻohana ʻana i ka waiʻona
Inā he bicuspid aortic valve koʻu, he aha kaʻu e manaʻo ai?
Ma kahi o 98% o ka poʻe i hana ʻia ke ʻoki valve e ola me ka ʻole o ka hopena i ko lākou ola. Inā he valve aortic bicuspid kou, hiki iā ʻoe ke ola e like me kekahi me ka ʻole o ke kūlana.Eia nō naʻe, pono ʻoe e nānā mau ʻia a me nā hoʻokolohua me kāu kauka. E nānā kāu kauka i kāu valve a e hōʻoia e loaʻa iā ʻoe ka lāʻau lapaʻau ke pono. He mea nui ka lāʻau lapaʻau e pale aku i nā pilikia.
Pehea wau e mālama ai iaʻu iho?
Me kahi valve aortic bicuspid, hiki iā ʻoe ke hana i nā mea he nui āu e makemake ai. Pono ʻoe e hana i kekahi mau hoʻololi i ke ʻano o ka nohona e kōkua ai i ka mālama ʻana i kou puʻuwai olakino a hoʻēmi i ke kaumaha ma kou puʻuwai. ʻO kēia mau mea:
- Ka ʻai ʻana i nā meaʻai olakino no ka puʻuwai.
- Hoʻemi nui i ka nui o ka sodium (paʻakai) āu e ʻai ai.
- Ke pale ʻana i ka hana kino nui.
Pono ʻoe i nā manawa maʻamau me kāu kauka e nānā i ke ʻano o ka hana ʻana o kou puʻuwai. Inā ua hana ʻia ke ʻoki kino, e loaʻa iā ʻoe nā hahai ʻana ma hope o ʻelua pule, ʻekolu mahina, a me ʻeono mahina. Ma hope o kēlā, e loaʻa iā ʻoe kahi manawa i kēlā me kēia makahiki. He mea nui kēia mau manawa e mālama iā ʻoe i ke olakino a e nānā i kāu mau valves e ʻike i nā pilikia ma mua o ko lākou lilo ʻana i mea koʻikoʻi.
Āhea wau e hopohopo ai e pili ana i ka valve aortic bicuspid?
Pono ʻoe e hopohopo e pili ana i kahi valve aortic bicuspid ke hoʻomaka ia e hoʻopilikia i ka hana o kou puʻuwai. Hiki i ka maʻi valve aortic bicuspid ke hana i ka stenosis aortic a me ka regurgitation. I ka hala ʻana o ka manawa, hiki i kēia mau pilikia ke hōʻeha mau loa i ka puʻuwai.
Āhea wau e ʻike ai i kaʻu kauka?
E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou pono e hele mai no nā manawa i hoʻonohonoho ʻia. Inā ua hana ʻia ke ʻoki kino iā ʻoe, e loaʻa ana kekahi mau hana hahai i loko o ka makahiki mua a laila hoʻokahi i kēlā me kēia makahiki ma hope o kēlā.
Inā loaʻa i kekahi o kou ʻohana nā pilikia valve puʻuwai, akā ʻaʻole ʻoe i ʻike ʻia, hiki i kāu kauka ke kuhikuhi iā ʻoe i kahi cardiologist . Hiki i kāu cardiologist ke hoʻāʻo iā ʻoe no ka maʻi puʻuwai a hāʻawi iā ʻoe i ka ʻōlelo aʻoaʻo.
Āhea wau e hele ai i ka Emergency Treatment Unit (ETU) ?
Inā loaʻa iā ʻoe nā hōʻailona o ka haki ʻana o ka aneurysm a i ʻole ka dissection , e kāhea koke i ka 911 (a i ʻole kāu helu ulia pōpilikia kūloko) :
- ʻEha koke, ʻoi, a ʻeha hou i ka umauma a i ʻole ke kua
- Manaʻo ka ʻili he pipili a he hou
- Pōʻino
- Pōʻino
- Nā palpitations o ka puʻuwai
- Ka luaʻi a me ka luaʻi
- Paʻakikī ka hanu ʻana
He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?
Inā ua ʻike ʻia ʻoe a i ʻole kāu keiki me kahi valve aortic bicuspid, e kamaʻilio me kāu kauka e pili ana i kou maʻi puʻuwai a inā pono ʻoe i ka lāʻau lapaʻau. ʻO kekahi mau nīnau e nīnau ai:
- He mea pono anei ke ʻoki kino?
- Hiki iā ʻoe ke paipai i nā hoʻololi nohona olakino no ka puʻuwai?
- Aia kekahi mau hōʻailona o ke kahe koko a i ʻole ka ʻūlū ʻana o ka aorta?
- Pehea lā ke ʻano o ke kaʻina hana ho'ōla?
- He aha nā hōʻailona a i ʻole nā pilikia e pono iaʻu e makaʻala ma ka home?
- He aha nā hana e hiki ke hoʻoweliweli?
- Pehea e hiki ai iaʻu ke hōʻemi i ka pilikia o kaʻu keiki i ka maʻi puʻuwai i ka wā e hiki mai ana?
- Loaʻa iā ʻoe nā kumuwaiwai e hiki ke kōkua iaʻu e wehewehe i kēia hōʻailona i kaʻu keiki?
Hiki ke hoʻoluhi nui ʻia ka hana ʻana me kahi valve aortic bicuspid a hiki ke hāpai i nā nīnau he nui. E hoʻomanaʻo, aia nā kauka a me nā kauka ʻoki ma aneʻi e kōkua iā ʻoe a i ʻole kāu keiki e noho olakino a ikaika. Inā ua ʻike ʻia ʻoe a i ʻole kāu keiki me kēia maʻi i kēia manawa, e hoʻokaʻawale i kekahi manawa e aʻo hou e pili ana i kēia maʻi. E kamaʻilio me kāu kauka a loaʻa ka ʻike e pono ai ʻoe e ʻoluʻolu e pili ana i ka mālama ʻana i ke ʻano. Eia kekahi, e hoʻomanaʻo he ʻenehana kā lākou e hopu a mālama i nā pilikia i ka wā mua.
ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai
He maʻi hānau ʻia ka valve aortic bicuspid i hiki ke mālama ʻia. Mai hopohopo, akā e makaʻala.
ʻO ka mea nui loa, ʻo ia ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono, e hoʻāʻo ʻia i ka manawa kūpono, a e ola i kahi nohona olakino. ʻAʻole ʻoe hoʻokahi, aia nā kauka e hiki ke kōkua iā ʻoe. Manaʻolana mākou ua kōkua kēia ʻike iā ʻoe e loaʻa kahi ʻike maikaʻi aʻe o kēia maʻi.
👩🏽⚕️ Nā nīnau hou aku (FAQs)
💬 He aha ke ʻano o ka valve aortic bicuspid?
ʻO ka valve nui i loko o ko kākou puʻuwai (Aortic valve) maʻamau he 3 mau leaflet. Eia nō naʻe, ʻo ka poʻe me kēia ʻano genetic ʻē aʻe i hānau ʻia me 2 mau leaflet wale nō. He maʻi genetic kēia e hoʻopilikia ana i nā poʻe he nui.
💬 He aha ka hopena o kēia ma ka puʻuwai?
Ke loaʻa wale nā lau liʻiliʻi ʻelua, ʻaʻole paha e pani pono ka valve, e kahe ana ke koko i hope (regurgitation), a i ʻole e paʻa paha ka valve a pale i ke kahe ʻana o ke koko i mua (stenosis). ʻO kēia ke kumu e hana ikaika ai ka puʻuwai.
💬 Pono anei kekahi kanaka me kēia maʻi i ke ʻoki kino?
ʻAʻole pono pinepine ke ʻoki kino i ka wā kamaliʻi. Eia nō naʻe, inā nāwaliwali ka valve i kou wā ʻelemakule, pono maoli ke ʻoki kino a me kahi valve hana hou (hoʻololi valve).
ʻO ka valve puʻuwai bicuspid, valve aortic, maʻi puʻuwai, nā kīnā puʻuwai hānau ʻia, ʻoki puʻuwai, stenosis aortic, regurgitation aortic











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