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He ʻokoʻa iki paha kou i loko o kou valve puʻuwai? E kamaʻilio kākou e pili ana i ka Bicuspid Aortic Valve!

He ʻokoʻa iki paha kou i loko o kou valve puʻuwai? E kamaʻilio kākou e pili ana i ka Bicuspid Aortic Valve!

Ua noʻonoʻo paha ʻoe i nā puka liʻiliʻi i loko o kou puʻuwai? ʻAʻole paha mākou e noʻonoʻo i ke koʻikoʻi o kēia mau mea i ko mākou ola o kēlā me kēia lā. Akā, i kekahi manawa hele mai mākou i kēia ao me nā loli liʻiliʻi i loko o kēia mau puka liʻiliʻi, ʻo ia hoʻi, nā valves o ka puʻuwai. I kēia lā e kamaʻilio mākou e pili ana i kekahi ʻano maʻi puʻuwai kūikawā. Ua kapa ʻia kēia ʻo Bicuspid Aortic Valve Disease . Mai makaʻu, ʻo ka mea nui loa, ʻo ia ka makaʻala i kēia.

He aha kēia valve aortic bicuspid? I ka ʻōlelo maʻalahi...

E noʻonoʻo i kou puʻuwai e like me ka pamu wai. Hoʻopuka kēia pamu i ke koko maʻemaʻe a piha i ka oxygen ma kou kino holoʻokoʻa. Aia kahi puka koʻikoʻi loa kahi e kahe ai ke koko mai ka puʻuwai a i ke kīʻaha koko nui loa o ke kino, ʻo ia hoʻi ka aorta. Kāhea mākou i kēia puka ʻo ka valve aortic .

ʻO ka maʻamau, i loko o ke kanaka olakino, ʻekolu ʻāpana o ka valve aortic, a i ʻole nā ​​ʻāpana, e like me ʻekolu lau ma ka puka. Hāmama a pani pono kēia mau ʻāpana ʻekolu e ʻae i ke koko e kahe i hoʻokahi wale nō ʻaoʻao - mai ka puʻuwai a i ka aorta. Pale kēia mau ʻāpana i ke koko mai ke kahe hou ʻana i loko o ka puʻuwai.

Eia nō naʻe, ʻo ke kanaka me ka `Bicuspid Aortic Valve` he ʻelua cusps i loko o ka `Aortic Valve`. ʻO ``Bi'' ke ʻano he ``ʻelua'' a ʻo ``cuspid'' ke ʻano he ``leaflet''. No laila, ua loaʻa ka inoa mai ka ʻoiaʻiʻo he ʻelua cusps. He ʻano ``congenital'' kēia, ʻo ia hoʻi, aia ia i ka wā hānau.

E noʻonoʻo, he aha ka mea e hana ʻia inā he ʻelua lau o ka puka ma kahi o ʻekolu? Malia paha ʻaʻole e wehe pono ka puka, a i ʻole ʻaʻole paha e pani pono. ʻO ia ka mea e hana ʻia i kēia kiwikā.

  • Inā ʻaʻole e wehe pono ka valve: Lilo ia i mea paʻakikī no ke koko ke kahe i mua, ʻo ia hoʻi, i loko o ka aorta. Ua kapa ʻia kēia ʻo 'Aortic Stenosis' , ʻo ia hoʻi ka haiki ʻana o ka valve.
  • Inā ʻaʻole pani pono ka valve: Hoʻi hou ke koko i loko o ka puʻuwai mai ka aorta. Ua kapa ʻia kēia he aortic regurgitation , ʻo ia hoʻi ke kahe hou ʻana o ke koko ma o ka valve.

Ua loaʻa paha iā ʻoe kēia 'Aortic Stenosis' a i ʻole 'Aortic Regurgitation' no nā makahiki, a ʻaʻole paha ʻoe i ʻike e pili ana i ia mea. ʻAʻole paha ʻoe e hōʻike i kekahi mau hōʻailona. No ka mea, ke hana nei kāu 'Aortic Valve' i kāna hana e like me ka hiki. Eia naʻe, ʻaʻole ia e like me ka pono o kahi valve me ʻekolu mau pepa liʻiliʻi.

I ka hala ʻana o ka manawa, hoʻoikaika kēia valve bicuspid i kou puʻuwai. Hiki i kēia ke alakaʻi i nā pilikia koʻikoʻi.Hiki ke hana. ʻOiai paha he mea paʻakikī ke ʻae i kēia ʻoiaʻiʻo, ʻo ke aʻo ʻana e pili ana i kēia kūlana e kōkua iā ʻoe e hoʻomaopopo maikaʻi iā ia.

Pehea ke koʻikoʻi o ka loaʻa ʻana o kahi valve aortic bicuspid?

ʻAʻole nā ​​kānaka a pau me ka bicuspid aortic valve e loaʻa nā pilikia. Eia nō naʻe, ma kahi o hoʻokahi i loko o ʻekolu mau kānaka e loaʻa nā pilikia. I kekahi manawa hiki i kēia ke lilo i mea koʻikoʻi loa a hiki ke hoʻoweliweli i ke ola . ʻO ia ke kumu e hoʻomau ai ka poʻe i ʻike ʻia me ka maʻi bicuspid aortic valve i nā hoʻokolohua lapaʻau a me ka hahai ʻana.

Hoʻopilikia kēia maʻi ma waena o 1% a me 2% o ka heluna kanaka maʻamau. ʻOi aku ka pālua o ka maʻamau i nā kāne ma mua o nā wahine. ʻO ka poʻe me ka Turner syndrome kekahi i ka nui o ka pilikia o ka hoʻomohala ʻana i kēia ʻano maʻi puʻuwai , ʻoiai ka bicuspid regurgitation.

I ka manawa pinepine, ʻaʻole paha ʻoe e ʻike i nā hōʻailona a hiki i ka wā e holomua loa ai ka maʻi a i ʻole kahi pilikia olakino. Eia nō naʻe, hiki i nā hoʻokolohua kiʻi ke ʻike i nā loli liʻiliʻi ma mua o kou ʻike ʻana i nā hōʻailona. A hiki i nā holomua i ka mālama ʻana ke kōkua iā ʻoe e ola i kahi ola lōʻihi a olakino hoʻi .

He aha nā hōʻailona o kēia maʻi?

E like me ka mea i ʻōlelo ʻia ma mua, ʻaʻole paha ʻoe e loaʻa i kekahi mau hōʻailona. Hiki iā ʻoe ke ola no nā makahiki me ka ʻike ʻole he loli liʻiliʻi kēia i loko o kou puʻuwai. Akā i ka hala ʻana o ka manawa, e hoʻomaka nā hōʻailona e ʻike ʻia ma muli o ka 'Aortic Regurgitation' a i ʻole 'Aortic Stenosis'.

Nā keiki liʻiliʻi a me nā pēpē:

Inā he bicuspid aortic valve kāu pēpē, i kekahi mau hihia koʻikoʻi, hiki ke ʻike ʻia nā hōʻailona ma hope koke iho o ka hānau ʻana. Akā i ka hapanui o ka manawa, ʻaʻole ʻike ʻia kēia mau hōʻailona a hiki i ka wā ma hope.

  • ʻIli keʻokeʻo a polū paha (Cyanosis)
  • Ka hoʻokaʻulua ʻole e ʻai, nā pilikia o ka piʻi ʻana o ke kaumaha

Nā hōʻailona i nā mākua:

  • Manaʻo luhi (ʻo kēia ka hōʻailona maʻamau)
  • ʻEha a ʻeha paha ka umauma
  • Pōʻino a i ʻole ka nawaliwali
  • Nā palpitations o ka puʻuwai
  • Ka paʻakikī o ka hanu ʻana , ʻoiai i ka wā o ka hana

ʻIke wale ka poʻe he nui he valve aortic bicuspid ko lākou ma hope o kahi hoʻāʻo lapaʻau. ʻO kēia no ka mea hiki ke maʻalahi ke ʻike ʻole ʻia nā hōʻailona. E ʻike paha kou ʻohana a i ʻole nā ​​hoaaloha i ka ʻokoʻa i loko ou ma mua o kou ʻike ʻana.

E noʻonoʻo i ka nui o ka hana hiki iā ʻoe ke hana i kahi lā maʻamau. E hoʻohālikelike iā ia me ka nui o kāu hana i hoʻokahi makahiki i hala, a i ʻole ʻeono mahina i hala. Ke luhi koke nei ʻoe i kēia manawa? Pono ʻoe i ka manawa hou aku e hoʻomaha ai? Inā pēlā, ʻo ia hoʻi ke hana ikaika nei kou puʻuwai e hoʻopau i ka hana.

ʻO ia ke kumu he mea nui loa ka mālama ʻana i nā manawa i hoʻonohonoho ʻia e kāu kauka . E kamaʻilio me kāu kauka e pili ana i nā loli āu e ʻike ai i kou ola o kēlā me kēia lā.

He aha ke kumu o ka valve aortic bicuspid?

ʻAʻole i loaʻa i nā kānaka noiʻi ke kumu pololei o ka valve aortic bicuspid. Eia nō naʻe, ʻo ia ke ʻano puʻuwai hānau maʻamau . Hoʻomaka ia i ka wā mua o ka hāpai ʻana .

He mea kēia i loaʻa mai nā hanauna mai?

Me he mea lā he mea hiki, akā, ʻaʻole maopopo loa i nā kānaka noiʻi nā kikoʻī.

Hiki ke holo ka Bicuspid Aortic Valve i loko o nā ʻohana. Inā loaʻa i kahi hoahānau pili koko (makua, keiki, kaikunāne/kaikuahine) o ʻoe kēia maʻi puʻuwai, e kamaʻilio me kāu kauka. Hiki iā lākou ke paipai i kekahi mau hoʻokolohua e nānā i ke ʻano a me ka hana o kou puʻuwai .

Inā he valve aortic bicuspid kou a ke hoʻolālā nei e hāpai, e kamaʻilio me kāu kauka. ʻOiai ʻaʻole hiki ke pale ʻia kēia ʻano, hiki iā ʻoe ke nānā i kāu hāpai ʻana a hoʻāʻo e ʻike i nā pilikia i ka wā mua .

He aha nā pilikia o kēia maʻi?

Inā ʻaʻole mālama ʻia, hiki i ka Bicuspid Aortic Valve Disease ke alakaʻi i nā pilikia koʻikoʻi. ʻO kekahi o lākou:

  • ʻO ka hāʻule ʻana o ka puʻuwai: I ke ʻano o ka stenosis aortic, ʻo ia ka wā e haiki ai ka valve, pono ka puʻuwai e hana ikaika loa e pamu i ke koko. ʻO ka ventricle hema, ʻo ia hoʻi ke keʻena pamu nui o ka puʻuwai, ʻo ia hoʻi ka ventricle hema, e mānoanoa a lilo i mea nui. ʻAʻole hiki iā ia ke pamu pono i ke koko. I ka hala ʻana o ka manawa, hiki i kēia ke alakaʻi i ka hāʻule ʻana o ka puʻuwai. Hiki ke hoʻolalelale ʻia kēia kaʻina hana inā he mau mea pilikia ʻē aʻe, e like me ka puhi paka a me ke cholesterol kiʻekiʻe.
  • ʻO ka haki ʻana o ka Aortic Aneurysm a me ka dissection Aortic:Ma kahi o hoʻokahi o ʻekolu poʻe me ka valve aortic bicuspid e loaʻa paha kahi aorta dilated, a i ʻole hoʻonui ʻia, ma luna o ka valve. I ka wā e hoʻonui ai ka aorta, nalowale ka ikaika o kona mau paia a loli ke ʻano. I ka hopena, hiki i kēia ke alakaʻi i kahi aneurysm aortic, kahi puʻupuʻu e like me ka balloon i loko o ka paia o ka aorta. Inā lilo kēia aneurysm i mea nui loa, hiki iā ia ke haki a haehae paha i ka paia (aortic dissection) . He mau pilikia hoʻoweliweli ola kēia.

Pehea e ʻike ʻia ai ka valve aortic bicuspid?

I kekahi manawa, hiki i ke kauka ke ʻike i ke kūlana i ka wā o ka ultrasound prenatal cardiac i ka wā hāpai. I kekahi manawa, ʻike ʻia kahi valve aortic bicuspid i ka wā o nā hoʻokolohua i hana ʻia i ka wā e loaʻa ai i kahi pēpē nā hōʻailona ma muli o kekahi maʻi puʻuwai ʻē aʻe.

Eia nō naʻe, nui ka poʻe e hele i nā makahiki me ka ʻike ʻole he loaʻa iā lākou kēia maʻi. ʻO ka hōʻailona mua paha he murmur puʻuwai , he kani ʻē i loko o ka puʻuwai a kāu kauka e lohe ai me kahi stethoscope. A laila, hiki i kāu kauka ke hana i nā hoʻokolohua kiʻi e nānā i ke ʻano a me ka hana o ka puʻuwai.

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia?

Hiki i kāu kauka ke nānā i kou puʻuwai a hana i kēia mau hoʻokolohua e ʻike ai inā he valve aortic bicuspid kou:

  • Echocardiogram (Echocardiogram - echo) : ʻAe kēia iā ʻoe e ʻike i nā kiʻi ola o ka puʻuwai.
  • Nā scan CT (Computed Tomography scans) : Lawe kēia i nā kiʻi ʻokiʻoki o ka puʻuwai.
  • `Heart MRI` (Magnetic Resonance Imaging) : Hiki i kēia ke kiʻi i nā kiʻi kikoʻī o ka puʻuwai.

Hiki paha iā lākou ke kuhikuhi iā ʻoe no ka hoʻāʻo genetic .

Pehea e mālama ʻia ai ka Bicuspid Aortic Valve?

Hiki i nā lāʻau lapaʻau e like me nā beta-blockers a me nā diuretics ke kōkua i ka kaohi ʻana i nā hōʻailona. Akā, ʻaʻole lākou e ho'ōla loa i ke kūlana . Ma kahi o ʻehā o kēlā me kēia ʻelima mau kānaka me ka Bicuspid Aortic Valve Disease e pono ai ke ʻoki ʻana e mālama ai. E hoʻoponopono kāu kauka ʻoki i kāu valve aortic a i ʻole e hoʻokomo i kahi valve hou . Hiki iā lākou ke hoʻoponopono i nā pilikia ʻē aʻe, e like me ka aneurysm, i ka wā o ke ʻoki like.

E loiloi kāu kauka i kou kūlana, e hana i kekahi mau hoʻokolohua, a e kūkākūkā i kāu mau koho lapaʻau me ʻoe. ʻO ka lāʻau lapaʻau āu e loaʻa ai e pili ana i ke kūlana o kāu valve aortic a me ka aorta. E noʻonoʻo pū lākou i kou olakino puʻuwai holoʻokoʻa, ka makahiki, a me nā kūlana olakino ʻē aʻe.

ʻO ka mea nui loa, ʻo ia ke hana ʻoki kino koke, ma mua o ka hōʻino mau ʻana o ka puʻuwai. ʻOiai inā ʻaʻohe ou hōʻailona, ​​makemake paha kāu kauka e mālama i ka pilikia i kēia manawa e pale aku i nā pilikia e hiki mai ana. He ʻokoʻa ka manawa maikaʻi loa no kēlā me kēia kanaka. E kūkākūkā kāu hui lapaʻau i kāu mau koho me ʻoe.

Ua hoʻomaikaʻi ka ʻenehana hou i nā hopena a ua hōʻemi i nā pilikia. Hiki i nā poʻe he nui ke hoʻohana i nā ʻano hana minimally invasive ma kahi o ke ʻoki puʻuwai hāmama kuʻuna.

ʻO ka ʻokoʻa ma waena o ke ʻoki ʻana i ka valve aortic kuʻuna a me ke ʻoki ʻana minimally invasive

  • ʻO ke ʻoki ʻana i ka valve aortic kuʻuna (puʻuwai hāmama): Pili kēia i ka hana ʻana i kahi ʻoki ʻana he 6-8 ʻīniha ma waenakonu o ka umauma, ma ka sternum. Hoʻokaʻawale ke kauka lapaʻau i ka sternum i ʻelua e komo pololei i ka puʻuwai.
  • ʻO ke ʻoki ʻana i ka valve aortic minimally invasive: Pili kēia i ka hana ʻana i kahi ʻoki liʻiliʻi, "J"-ʻano ma kahi o 2-4 ʻīniha ka lōʻihi. Hiki ke hana ʻia kēia ʻoki ma ka piko o ka iwi umauma a i ʻole ma waena o nā iwi ʻaoʻao. ʻAʻole pono ke kauka lapaʻau e wehe i ka umauma holoʻokoʻa. Hoʻemi kēia ʻano hana i ke kahe koko, ʻae i ka noho wikiwiki ʻana i ka haukapila, a hiki ke hoʻopōkole i ka manawa hoʻōla.

Ka Hoʻoponopono ʻana i ka Valve Aortic a i ʻole ke Hoʻololi ʻana i ka Valve Aortic?

  • Hoʻoponopono Valve Aortic: He kaʻina hana kēia e hoʻoponopono ai i kāu valve me ka ʻole o ka hoʻololi ʻana. He koho maikaʻi kēia no ka poʻe me ka regurgitation aortic (ke kahe ʻana o ke koko mai ka valve). Eia naʻe, ʻaʻole hiki iā ia ke mālama i ka stenosis aortic (ka haiki ʻana o ka valve). Hiki i nā kauka ke hana pinepine i kēia kaʻina hana minimally invasive ma o kahi ʻoki "J". Hoʻololi hou ke kauka i nā pepa o kāu valve aortic e kōkua iā lākou e wehe a pani pono.
  • Hoʻololi Valve Aortic: Pili kēia i ka wehe ʻana i kāu valve hiki ʻole ke hoʻoponopono hou ʻia a hoʻololi iā ia me kahi mea hou. Hiki i nā kauka lapaʻau ke hoʻololi i kāu valve ma o ke ʻoki kino hāmama kuʻuna a i ʻole ma o ke kaʻina hana minimally invasive i kapa ʻia ʻo Transcatheter Aortic Valve Replacement (TAVR) .

ʻO ka kiwikā hou e hoʻokomo ʻia ai iā ʻoe he 'kiwikā biological' a i ʻole he 'kiwikā mechanical' .

  • `Kiwikā olaola`:Hoʻohana nā kauka lapaʻau i kēia ʻano kiwikā i 80% o ka manawa. Hana ʻia kēia kiwikā mai nā ʻiʻo puaʻa a bipi paha. He palekana a mau no ka manawa lōʻihi. Eia nō naʻe, ma hope o kahi 10 mau makahiki, pono paha ʻoe e hana hou i kahi ʻoki kino e pani ai i ka kiwikā.
  • Kiwikā mīkini: He paʻa loa kēia kiwikā hana a hiki ke mau i kou ola a pau. Eia nō naʻe, i mea e hana pono ai, pono ʻoe e lawe i nā lāʻau hoʻokahe koko no ke koena o kou ola .

Makemake ka poʻe he nui i kahi valve biological no ka mea ʻaʻole pono lākou e lawe i nā lāʻau hoʻokahe koko. Akā pili ia i kou makahiki, nā kūlana olakino ʻē aʻe, a me nā makemake pilikino. E kamaʻilio kāu kauka me ʻoe e pili ana i kēia mau koho a kōkua iā ʻoe e hoʻoholo i ka mea maikaʻi loa iā ʻoe.

ʻO kekahi koho no ka hoʻololi ʻana i ka valve ʻo ia ke kaʻina hana Ross (i ʻike ʻia hoʻi ʻo ke kaʻina hana hoʻololi) . Pili kēia i ka lawe ʻana i kāu valve pulmonary a hoʻololi iā ia me kāu valve aortic. He koho maikaʻi paha kēia inā ʻoe ma lalo o 50 mau makahiki a makemake ʻoe e pale i ka lawe ʻana i nā lāʻau hoʻokahe koko no ka manawa lōʻihi.

Nā pilikia o ka mālama ʻana

Ma keʻano laulā, haʻahaʻa ka pilikia o nā pilikia mai ke ʻoki ʻana i ka valve. Eia nō naʻe, hiki i nā pilikia ke komo pū me:

  • Nā maʻi
  • Ke kahe ʻana o ke koko
  • Nā ʻūpā koko
  • Hahau
  • Maʻi hohola
  • Nā ʻano ʻē o ka puʻuwai `(Arrhythmia)` (no ka manawa pōkole)
  • Ka emi ʻana o ka hana o nā puʻupaʻa (no kekahi manawa pōkole)

ʻEhia ka lōʻihi e ho'ōla ai mai kēia lāʻau lapaʻau?

Hiki i ke ʻoki hoʻololi valve aortic ke hala ma kahi o ʻelua a ʻekolu mahina e hoʻōla piha ai. Hiki i ke ʻoki hoʻoponopono valve aortic ke hala ma kahi o hoʻokahi a ʻelua mahina e hoʻōla piha ai.

Hiki ke pale ʻia ka valve aortic bicuspid?

ʻAʻohe ala e pale aku ai i ka valve aortic bicuspid. He mea hānau ia, ʻo ia hoʻi ua hānau ʻia ʻoe me ia. Eia nō naʻe, hiki iā ʻoe ke hana i nā hoʻololi i ke ʻano o ka nohona e hiki ai ke hōʻemi i kou pilikia o ka loaʻa ʻana o nā maʻi puʻuwai ʻē aʻe, e like me ka atherosclerosis a me ka maʻi artery coronary. Inā he valve aortic bicuspid kāu, e kamaʻilio me kāu kauka e pili ana i ka hoʻokele ʻana i kāu mau kumu pilikia maʻi puʻuwai. ʻO kēia mau mea:

  • Ke koko kiʻekiʻe (Hypertension)
  • ʻO ke kolesterol kiʻekiʻe `(Hyperlipidemia)`
  • Maʻi diabetes
  • Nā mea e pili ana i ke ʻano o ka nohona e like me nā huahana paka a me ka hoʻohana ʻana i ka waiʻona

Inā he bicuspid aortic valve koʻu, he aha kaʻu e manaʻo ai?

Ma kahi o 98% o ka poʻe i hana ʻia ke ʻoki valve e ola me ka ʻole o ka hopena i ko lākou ola. Inā he valve aortic bicuspid kou, hiki iā ʻoe ke ola e like me kekahi me ka ʻole o ke kūlana.Eia nō naʻe, pono ʻoe e nānā mau ʻia a me nā hoʻokolohua me kāu kauka. E nānā kāu kauka i kāu valve a e hōʻoia e loaʻa iā ʻoe ka lāʻau lapaʻau ke pono. He mea nui ka lāʻau lapaʻau e pale aku i nā pilikia.

Pehea wau e mālama ai iaʻu iho?

Me kahi valve aortic bicuspid, hiki iā ʻoe ke hana i nā mea he nui āu e makemake ai. Pono ʻoe e hana i kekahi mau hoʻololi i ke ʻano o ka nohona e kōkua ai i ka mālama ʻana i kou puʻuwai olakino a hoʻēmi i ke kaumaha ma kou puʻuwai. ʻO kēia mau mea:

  • Ka ʻai ʻana i nā meaʻai olakino no ka puʻuwai.
  • Hoʻemi nui i ka nui o ka sodium (paʻakai) āu e ʻai ai.
  • Ke pale ʻana i ka hana kino nui.

Pono ʻoe i nā manawa maʻamau me kāu kauka e nānā i ke ʻano o ka hana ʻana o kou puʻuwai. Inā ua hana ʻia ke ʻoki kino, e loaʻa iā ʻoe nā hahai ʻana ma hope o ʻelua pule, ʻekolu mahina, a me ʻeono mahina. Ma hope o kēlā, e loaʻa iā ʻoe kahi manawa i kēlā me kēia makahiki. He mea nui kēia mau manawa e mālama iā ʻoe i ke olakino a e nānā i kāu mau valves e ʻike i nā pilikia ma mua o ko lākou lilo ʻana i mea koʻikoʻi.

Āhea wau e hopohopo ai e pili ana i ka valve aortic bicuspid?

Pono ʻoe e hopohopo e pili ana i kahi valve aortic bicuspid ke hoʻomaka ia e hoʻopilikia i ka hana o kou puʻuwai. Hiki i ka maʻi valve aortic bicuspid ke hana i ka stenosis aortic a me ka regurgitation. I ka hala ʻana o ka manawa, hiki i kēia mau pilikia ke hōʻeha mau loa i ka puʻuwai.

Āhea wau e ʻike ai i kaʻu kauka?

E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou pono e hele mai no nā manawa i hoʻonohonoho ʻia. Inā ua hana ʻia ke ʻoki kino iā ʻoe, e loaʻa ana kekahi mau hana hahai i loko o ka makahiki mua a laila hoʻokahi i kēlā me kēia makahiki ma hope o kēlā.

Inā loaʻa i kekahi o kou ʻohana nā pilikia valve puʻuwai, akā ʻaʻole ʻoe i ʻike ʻia, hiki i kāu kauka ke kuhikuhi iā ʻoe i kahi cardiologist . Hiki i kāu cardiologist ke hoʻāʻo iā ʻoe no ka maʻi puʻuwai a hāʻawi iā ʻoe i ka ʻōlelo aʻoaʻo.

Āhea wau e hele ai i ka Emergency Treatment Unit (ETU) ?

Inā loaʻa iā ʻoe nā hōʻailona o ka haki ʻana o ka aneurysm a i ʻole ka dissection , e kāhea koke i ka 911 (a i ʻole kāu helu ulia pōpilikia kūloko) :

  • ʻEha koke, ʻoi, a ʻeha hou i ka umauma a i ʻole ke kua
  • Manaʻo ka ʻili he pipili a he hou
  • Pōʻino
  • Pōʻino
  • Nā palpitations o ka puʻuwai
  • Ka luaʻi a me ka luaʻi
  • Paʻakikī ka hanu ʻana

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

Inā ua ʻike ʻia ʻoe a i ʻole kāu keiki me kahi valve aortic bicuspid, e kamaʻilio me kāu kauka e pili ana i kou maʻi puʻuwai a inā pono ʻoe i ka lāʻau lapaʻau. ʻO kekahi mau nīnau e nīnau ai:

  • He mea pono anei ke ʻoki kino?
  • Hiki iā ʻoe ke paipai i nā hoʻololi nohona olakino no ka puʻuwai?
  • Aia kekahi mau hōʻailona o ke kahe koko a i ʻole ka ʻūlū ʻana o ka aorta?
  • Pehea lā ke ʻano o ke kaʻina hana ho'ōla?
  • He aha nā hōʻailona a i ʻole nā ​​​​pilikia e pono iaʻu e makaʻala ma ka home?
  • He aha nā hana e hiki ke hoʻoweliweli?
  • Pehea e hiki ai iaʻu ke hōʻemi i ka pilikia o kaʻu keiki i ka maʻi puʻuwai i ka wā e hiki mai ana?
  • Loaʻa iā ʻoe nā kumuwaiwai e hiki ke kōkua iaʻu e wehewehe i kēia hōʻailona i kaʻu keiki?

Hiki ke hoʻoluhi nui ʻia ka hana ʻana me kahi valve aortic bicuspid a hiki ke hāpai i nā nīnau he nui. E hoʻomanaʻo, aia nā kauka a me nā kauka ʻoki ma aneʻi e kōkua iā ʻoe a i ʻole kāu keiki e noho olakino a ikaika. Inā ua ʻike ʻia ʻoe a i ʻole kāu keiki me kēia maʻi i kēia manawa, e hoʻokaʻawale i kekahi manawa e aʻo hou e pili ana i kēia maʻi. E kamaʻilio me kāu kauka a loaʻa ka ʻike e pono ai ʻoe e ʻoluʻolu e pili ana i ka mālama ʻana i ke ʻano. Eia kekahi, e hoʻomanaʻo he ʻenehana kā lākou e hopu a mālama i nā pilikia i ka wā mua.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai

He maʻi hānau ʻia ka valve aortic bicuspid i hiki ke mālama ʻia. Mai hopohopo, akā e makaʻala.

ʻO ka mea nui loa, ʻo ia ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono, e hoʻāʻo ʻia i ka manawa kūpono, a e ola i kahi nohona olakino. ʻAʻole ʻoe hoʻokahi, aia nā kauka e hiki ke kōkua iā ʻoe. Manaʻolana mākou ua kōkua kēia ʻike iā ʻoe e loaʻa kahi ʻike maikaʻi aʻe o kēia maʻi.

👩🏽‍⚕️ Nā nīnau hou aku (FAQs)

💬 He aha ke ʻano o ka valve aortic bicuspid?

ʻO ka valve nui i loko o ko kākou puʻuwai (Aortic valve) maʻamau he 3 mau leaflet. Eia nō naʻe, ʻo ka poʻe me kēia ʻano genetic ʻē aʻe i hānau ʻia me 2 mau leaflet wale nō. He maʻi genetic kēia e hoʻopilikia ana i nā poʻe he nui.

💬 He aha ka hopena o kēia ma ka puʻuwai?

Ke loaʻa wale nā ​​​​​​lau liʻiliʻi ʻelua, ʻaʻole paha e pani pono ka valve, e kahe ana ke koko i hope (regurgitation), a i ʻole e paʻa paha ka valve a pale i ke kahe ʻana o ke koko i mua (stenosis). ʻO kēia ke kumu e hana ikaika ai ka puʻuwai.

💬 Pono anei kekahi kanaka me kēia maʻi i ke ʻoki kino?

ʻAʻole pono pinepine ke ʻoki kino i ka wā kamaliʻi. Eia nō naʻe, inā nāwaliwali ka valve i kou wā ʻelemakule, pono maoli ke ʻoki kino a me kahi valve hana hou (hoʻololi valve).


ʻO ka valve puʻuwai bicuspid, valve aortic, maʻi puʻuwai, nā kīnā puʻuwai hānau ʻia, ʻoki puʻuwai, stenosis aortic, regurgitation aortic

Frequently Asked Questions (FAQ)

He mea kēia i loaʻa mai nā hanauna mai?

Me he mea lā he mea hiki, akā, ʻaʻole maopopo loa i nā kānaka noiʻi nā kikoʻī.

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia?

Hiki i kāu kauka ke nānā i kou puʻuwai a hana i kēia mau hoʻokolohua e ʻike ai inā he valve aortic bicuspid kou:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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He ʻokoʻa iki paha kou i loko o kou valve puʻuwai? E kamaʻilio kākou e pili ana i ka Bicuspid Aortic Valve!
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He ʻokoʻa iki paha kou i loko o kou valve puʻuwai? E kamaʻilio kākou e pili ana i ka Bicuspid Aortic Valve!

Ua noʻonoʻo paha ʻoe i nā puka liʻiliʻi i loko o kou puʻuwai? ʻAʻole paha mākou e noʻonoʻo i ke koʻikoʻi o kēia mau mea i ko mākou ola o kēlā me kēia lā. Akā, i kekahi manawa hele mai mākou i kēia ao me nā loli liʻiliʻi i loko o kēia mau puka liʻiliʻi, ʻo ia hoʻi, nā valves o ka puʻuwai. I kēia lā e kamaʻilio mākou e pili ana i kekahi ʻano maʻi puʻuwai kūikawā. Ua kapa ʻia kēia ʻo Bicuspid Aortic Valve Disease . Mai makaʻu, ʻo ka mea nui loa, ʻo ia ka makaʻala i kēia.

He aha kēia valve aortic bicuspid? I ka ʻōlelo maʻalahi...

E noʻonoʻo i kou puʻuwai e like me ka pamu wai. Hoʻopuka kēia pamu i ke koko maʻemaʻe a piha i ka oxygen ma kou kino holoʻokoʻa. Aia kahi puka koʻikoʻi loa kahi e kahe ai ke koko mai ka puʻuwai a i ke kīʻaha koko nui loa o ke kino, ʻo ia hoʻi ka aorta. Kāhea mākou i kēia puka ʻo ka valve aortic .

ʻO ka maʻamau, i loko o ke kanaka olakino, ʻekolu ʻāpana o ka valve aortic, a i ʻole nā ​​ʻāpana, e like me ʻekolu lau ma ka puka. Hāmama a pani pono kēia mau ʻāpana ʻekolu e ʻae i ke koko e kahe i hoʻokahi wale nō ʻaoʻao - mai ka puʻuwai a i ka aorta. Pale kēia mau ʻāpana i ke koko mai ke kahe hou ʻana i loko o ka puʻuwai.

Eia nō naʻe, ʻo ke kanaka me ka `Bicuspid Aortic Valve` he ʻelua cusps i loko o ka `Aortic Valve`. ʻO ``Bi'' ke ʻano he ``ʻelua'' a ʻo ``cuspid'' ke ʻano he ``leaflet''. No laila, ua loaʻa ka inoa mai ka ʻoiaʻiʻo he ʻelua cusps. He ʻano ``congenital'' kēia, ʻo ia hoʻi, aia ia i ka wā hānau.

E noʻonoʻo, he aha ka mea e hana ʻia inā he ʻelua lau o ka puka ma kahi o ʻekolu? Malia paha ʻaʻole e wehe pono ka puka, a i ʻole ʻaʻole paha e pani pono. ʻO ia ka mea e hana ʻia i kēia kiwikā.

  • Inā ʻaʻole e wehe pono ka valve: Lilo ia i mea paʻakikī no ke koko ke kahe i mua, ʻo ia hoʻi, i loko o ka aorta. Ua kapa ʻia kēia ʻo 'Aortic Stenosis' , ʻo ia hoʻi ka haiki ʻana o ka valve.
  • Inā ʻaʻole pani pono ka valve: Hoʻi hou ke koko i loko o ka puʻuwai mai ka aorta. Ua kapa ʻia kēia he aortic regurgitation , ʻo ia hoʻi ke kahe hou ʻana o ke koko ma o ka valve.

Ua loaʻa paha iā ʻoe kēia 'Aortic Stenosis' a i ʻole 'Aortic Regurgitation' no nā makahiki, a ʻaʻole paha ʻoe i ʻike e pili ana i ia mea. ʻAʻole paha ʻoe e hōʻike i kekahi mau hōʻailona. No ka mea, ke hana nei kāu 'Aortic Valve' i kāna hana e like me ka hiki. Eia naʻe, ʻaʻole ia e like me ka pono o kahi valve me ʻekolu mau pepa liʻiliʻi.

I ka hala ʻana o ka manawa, hoʻoikaika kēia valve bicuspid i kou puʻuwai. Hiki i kēia ke alakaʻi i nā pilikia koʻikoʻi.Hiki ke hana. ʻOiai paha he mea paʻakikī ke ʻae i kēia ʻoiaʻiʻo, ʻo ke aʻo ʻana e pili ana i kēia kūlana e kōkua iā ʻoe e hoʻomaopopo maikaʻi iā ia.

Pehea ke koʻikoʻi o ka loaʻa ʻana o kahi valve aortic bicuspid?

ʻAʻole nā ​​kānaka a pau me ka bicuspid aortic valve e loaʻa nā pilikia. Eia nō naʻe, ma kahi o hoʻokahi i loko o ʻekolu mau kānaka e loaʻa nā pilikia. I kekahi manawa hiki i kēia ke lilo i mea koʻikoʻi loa a hiki ke hoʻoweliweli i ke ola . ʻO ia ke kumu e hoʻomau ai ka poʻe i ʻike ʻia me ka maʻi bicuspid aortic valve i nā hoʻokolohua lapaʻau a me ka hahai ʻana.

Hoʻopilikia kēia maʻi ma waena o 1% a me 2% o ka heluna kanaka maʻamau. ʻOi aku ka pālua o ka maʻamau i nā kāne ma mua o nā wahine. ʻO ka poʻe me ka Turner syndrome kekahi i ka nui o ka pilikia o ka hoʻomohala ʻana i kēia ʻano maʻi puʻuwai , ʻoiai ka bicuspid regurgitation.

I ka manawa pinepine, ʻaʻole paha ʻoe e ʻike i nā hōʻailona a hiki i ka wā e holomua loa ai ka maʻi a i ʻole kahi pilikia olakino. Eia nō naʻe, hiki i nā hoʻokolohua kiʻi ke ʻike i nā loli liʻiliʻi ma mua o kou ʻike ʻana i nā hōʻailona. A hiki i nā holomua i ka mālama ʻana ke kōkua iā ʻoe e ola i kahi ola lōʻihi a olakino hoʻi .

He aha nā hōʻailona o kēia maʻi?

E like me ka mea i ʻōlelo ʻia ma mua, ʻaʻole paha ʻoe e loaʻa i kekahi mau hōʻailona. Hiki iā ʻoe ke ola no nā makahiki me ka ʻike ʻole he loli liʻiliʻi kēia i loko o kou puʻuwai. Akā i ka hala ʻana o ka manawa, e hoʻomaka nā hōʻailona e ʻike ʻia ma muli o ka 'Aortic Regurgitation' a i ʻole 'Aortic Stenosis'.

Nā keiki liʻiliʻi a me nā pēpē:

Inā he bicuspid aortic valve kāu pēpē, i kekahi mau hihia koʻikoʻi, hiki ke ʻike ʻia nā hōʻailona ma hope koke iho o ka hānau ʻana. Akā i ka hapanui o ka manawa, ʻaʻole ʻike ʻia kēia mau hōʻailona a hiki i ka wā ma hope.

  • ʻIli keʻokeʻo a polū paha (Cyanosis)
  • Ka hoʻokaʻulua ʻole e ʻai, nā pilikia o ka piʻi ʻana o ke kaumaha

Nā hōʻailona i nā mākua:

  • Manaʻo luhi (ʻo kēia ka hōʻailona maʻamau)
  • ʻEha a ʻeha paha ka umauma
  • Pōʻino a i ʻole ka nawaliwali
  • Nā palpitations o ka puʻuwai
  • Ka paʻakikī o ka hanu ʻana , ʻoiai i ka wā o ka hana

ʻIke wale ka poʻe he nui he valve aortic bicuspid ko lākou ma hope o kahi hoʻāʻo lapaʻau. ʻO kēia no ka mea hiki ke maʻalahi ke ʻike ʻole ʻia nā hōʻailona. E ʻike paha kou ʻohana a i ʻole nā ​​hoaaloha i ka ʻokoʻa i loko ou ma mua o kou ʻike ʻana.

E noʻonoʻo i ka nui o ka hana hiki iā ʻoe ke hana i kahi lā maʻamau. E hoʻohālikelike iā ia me ka nui o kāu hana i hoʻokahi makahiki i hala, a i ʻole ʻeono mahina i hala. Ke luhi koke nei ʻoe i kēia manawa? Pono ʻoe i ka manawa hou aku e hoʻomaha ai? Inā pēlā, ʻo ia hoʻi ke hana ikaika nei kou puʻuwai e hoʻopau i ka hana.

ʻO ia ke kumu he mea nui loa ka mālama ʻana i nā manawa i hoʻonohonoho ʻia e kāu kauka . E kamaʻilio me kāu kauka e pili ana i nā loli āu e ʻike ai i kou ola o kēlā me kēia lā.

He aha ke kumu o ka valve aortic bicuspid?

ʻAʻole i loaʻa i nā kānaka noiʻi ke kumu pololei o ka valve aortic bicuspid. Eia nō naʻe, ʻo ia ke ʻano puʻuwai hānau maʻamau . Hoʻomaka ia i ka wā mua o ka hāpai ʻana .

He mea kēia i loaʻa mai nā hanauna mai?

Me he mea lā he mea hiki, akā, ʻaʻole maopopo loa i nā kānaka noiʻi nā kikoʻī.

Hiki ke holo ka Bicuspid Aortic Valve i loko o nā ʻohana. Inā loaʻa i kahi hoahānau pili koko (makua, keiki, kaikunāne/kaikuahine) o ʻoe kēia maʻi puʻuwai, e kamaʻilio me kāu kauka. Hiki iā lākou ke paipai i kekahi mau hoʻokolohua e nānā i ke ʻano a me ka hana o kou puʻuwai .

Inā he valve aortic bicuspid kou a ke hoʻolālā nei e hāpai, e kamaʻilio me kāu kauka. ʻOiai ʻaʻole hiki ke pale ʻia kēia ʻano, hiki iā ʻoe ke nānā i kāu hāpai ʻana a hoʻāʻo e ʻike i nā pilikia i ka wā mua .

He aha nā pilikia o kēia maʻi?

Inā ʻaʻole mālama ʻia, hiki i ka Bicuspid Aortic Valve Disease ke alakaʻi i nā pilikia koʻikoʻi. ʻO kekahi o lākou:

  • ʻO ka hāʻule ʻana o ka puʻuwai: I ke ʻano o ka stenosis aortic, ʻo ia ka wā e haiki ai ka valve, pono ka puʻuwai e hana ikaika loa e pamu i ke koko. ʻO ka ventricle hema, ʻo ia hoʻi ke keʻena pamu nui o ka puʻuwai, ʻo ia hoʻi ka ventricle hema, e mānoanoa a lilo i mea nui. ʻAʻole hiki iā ia ke pamu pono i ke koko. I ka hala ʻana o ka manawa, hiki i kēia ke alakaʻi i ka hāʻule ʻana o ka puʻuwai. Hiki ke hoʻolalelale ʻia kēia kaʻina hana inā he mau mea pilikia ʻē aʻe, e like me ka puhi paka a me ke cholesterol kiʻekiʻe.
  • ʻO ka haki ʻana o ka Aortic Aneurysm a me ka dissection Aortic:Ma kahi o hoʻokahi o ʻekolu poʻe me ka valve aortic bicuspid e loaʻa paha kahi aorta dilated, a i ʻole hoʻonui ʻia, ma luna o ka valve. I ka wā e hoʻonui ai ka aorta, nalowale ka ikaika o kona mau paia a loli ke ʻano. I ka hopena, hiki i kēia ke alakaʻi i kahi aneurysm aortic, kahi puʻupuʻu e like me ka balloon i loko o ka paia o ka aorta. Inā lilo kēia aneurysm i mea nui loa, hiki iā ia ke haki a haehae paha i ka paia (aortic dissection) . He mau pilikia hoʻoweliweli ola kēia.

Pehea e ʻike ʻia ai ka valve aortic bicuspid?

I kekahi manawa, hiki i ke kauka ke ʻike i ke kūlana i ka wā o ka ultrasound prenatal cardiac i ka wā hāpai. I kekahi manawa, ʻike ʻia kahi valve aortic bicuspid i ka wā o nā hoʻokolohua i hana ʻia i ka wā e loaʻa ai i kahi pēpē nā hōʻailona ma muli o kekahi maʻi puʻuwai ʻē aʻe.

Eia nō naʻe, nui ka poʻe e hele i nā makahiki me ka ʻike ʻole he loaʻa iā lākou kēia maʻi. ʻO ka hōʻailona mua paha he murmur puʻuwai , he kani ʻē i loko o ka puʻuwai a kāu kauka e lohe ai me kahi stethoscope. A laila, hiki i kāu kauka ke hana i nā hoʻokolohua kiʻi e nānā i ke ʻano a me ka hana o ka puʻuwai.

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia?

Hiki i kāu kauka ke nānā i kou puʻuwai a hana i kēia mau hoʻokolohua e ʻike ai inā he valve aortic bicuspid kou:

  • Echocardiogram (Echocardiogram - echo) : ʻAe kēia iā ʻoe e ʻike i nā kiʻi ola o ka puʻuwai.
  • Nā scan CT (Computed Tomography scans) : Lawe kēia i nā kiʻi ʻokiʻoki o ka puʻuwai.
  • `Heart MRI` (Magnetic Resonance Imaging) : Hiki i kēia ke kiʻi i nā kiʻi kikoʻī o ka puʻuwai.

Hiki paha iā lākou ke kuhikuhi iā ʻoe no ka hoʻāʻo genetic .

Pehea e mālama ʻia ai ka Bicuspid Aortic Valve?

Hiki i nā lāʻau lapaʻau e like me nā beta-blockers a me nā diuretics ke kōkua i ka kaohi ʻana i nā hōʻailona. Akā, ʻaʻole lākou e ho'ōla loa i ke kūlana . Ma kahi o ʻehā o kēlā me kēia ʻelima mau kānaka me ka Bicuspid Aortic Valve Disease e pono ai ke ʻoki ʻana e mālama ai. E hoʻoponopono kāu kauka ʻoki i kāu valve aortic a i ʻole e hoʻokomo i kahi valve hou . Hiki iā lākou ke hoʻoponopono i nā pilikia ʻē aʻe, e like me ka aneurysm, i ka wā o ke ʻoki like.

E loiloi kāu kauka i kou kūlana, e hana i kekahi mau hoʻokolohua, a e kūkākūkā i kāu mau koho lapaʻau me ʻoe. ʻO ka lāʻau lapaʻau āu e loaʻa ai e pili ana i ke kūlana o kāu valve aortic a me ka aorta. E noʻonoʻo pū lākou i kou olakino puʻuwai holoʻokoʻa, ka makahiki, a me nā kūlana olakino ʻē aʻe.

ʻO ka mea nui loa, ʻo ia ke hana ʻoki kino koke, ma mua o ka hōʻino mau ʻana o ka puʻuwai. ʻOiai inā ʻaʻohe ou hōʻailona, ​​makemake paha kāu kauka e mālama i ka pilikia i kēia manawa e pale aku i nā pilikia e hiki mai ana. He ʻokoʻa ka manawa maikaʻi loa no kēlā me kēia kanaka. E kūkākūkā kāu hui lapaʻau i kāu mau koho me ʻoe.

Ua hoʻomaikaʻi ka ʻenehana hou i nā hopena a ua hōʻemi i nā pilikia. Hiki i nā poʻe he nui ke hoʻohana i nā ʻano hana minimally invasive ma kahi o ke ʻoki puʻuwai hāmama kuʻuna.

ʻO ka ʻokoʻa ma waena o ke ʻoki ʻana i ka valve aortic kuʻuna a me ke ʻoki ʻana minimally invasive

  • ʻO ke ʻoki ʻana i ka valve aortic kuʻuna (puʻuwai hāmama): Pili kēia i ka hana ʻana i kahi ʻoki ʻana he 6-8 ʻīniha ma waenakonu o ka umauma, ma ka sternum. Hoʻokaʻawale ke kauka lapaʻau i ka sternum i ʻelua e komo pololei i ka puʻuwai.
  • ʻO ke ʻoki ʻana i ka valve aortic minimally invasive: Pili kēia i ka hana ʻana i kahi ʻoki liʻiliʻi, "J"-ʻano ma kahi o 2-4 ʻīniha ka lōʻihi. Hiki ke hana ʻia kēia ʻoki ma ka piko o ka iwi umauma a i ʻole ma waena o nā iwi ʻaoʻao. ʻAʻole pono ke kauka lapaʻau e wehe i ka umauma holoʻokoʻa. Hoʻemi kēia ʻano hana i ke kahe koko, ʻae i ka noho wikiwiki ʻana i ka haukapila, a hiki ke hoʻopōkole i ka manawa hoʻōla.

Ka Hoʻoponopono ʻana i ka Valve Aortic a i ʻole ke Hoʻololi ʻana i ka Valve Aortic?

  • Hoʻoponopono Valve Aortic: He kaʻina hana kēia e hoʻoponopono ai i kāu valve me ka ʻole o ka hoʻololi ʻana. He koho maikaʻi kēia no ka poʻe me ka regurgitation aortic (ke kahe ʻana o ke koko mai ka valve). Eia naʻe, ʻaʻole hiki iā ia ke mālama i ka stenosis aortic (ka haiki ʻana o ka valve). Hiki i nā kauka ke hana pinepine i kēia kaʻina hana minimally invasive ma o kahi ʻoki "J". Hoʻololi hou ke kauka i nā pepa o kāu valve aortic e kōkua iā lākou e wehe a pani pono.
  • Hoʻololi Valve Aortic: Pili kēia i ka wehe ʻana i kāu valve hiki ʻole ke hoʻoponopono hou ʻia a hoʻololi iā ia me kahi mea hou. Hiki i nā kauka lapaʻau ke hoʻololi i kāu valve ma o ke ʻoki kino hāmama kuʻuna a i ʻole ma o ke kaʻina hana minimally invasive i kapa ʻia ʻo Transcatheter Aortic Valve Replacement (TAVR) .

ʻO ka kiwikā hou e hoʻokomo ʻia ai iā ʻoe he 'kiwikā biological' a i ʻole he 'kiwikā mechanical' .

  • `Kiwikā olaola`:Hoʻohana nā kauka lapaʻau i kēia ʻano kiwikā i 80% o ka manawa. Hana ʻia kēia kiwikā mai nā ʻiʻo puaʻa a bipi paha. He palekana a mau no ka manawa lōʻihi. Eia nō naʻe, ma hope o kahi 10 mau makahiki, pono paha ʻoe e hana hou i kahi ʻoki kino e pani ai i ka kiwikā.
  • Kiwikā mīkini: He paʻa loa kēia kiwikā hana a hiki ke mau i kou ola a pau. Eia nō naʻe, i mea e hana pono ai, pono ʻoe e lawe i nā lāʻau hoʻokahe koko no ke koena o kou ola .

Makemake ka poʻe he nui i kahi valve biological no ka mea ʻaʻole pono lākou e lawe i nā lāʻau hoʻokahe koko. Akā pili ia i kou makahiki, nā kūlana olakino ʻē aʻe, a me nā makemake pilikino. E kamaʻilio kāu kauka me ʻoe e pili ana i kēia mau koho a kōkua iā ʻoe e hoʻoholo i ka mea maikaʻi loa iā ʻoe.

ʻO kekahi koho no ka hoʻololi ʻana i ka valve ʻo ia ke kaʻina hana Ross (i ʻike ʻia hoʻi ʻo ke kaʻina hana hoʻololi) . Pili kēia i ka lawe ʻana i kāu valve pulmonary a hoʻololi iā ia me kāu valve aortic. He koho maikaʻi paha kēia inā ʻoe ma lalo o 50 mau makahiki a makemake ʻoe e pale i ka lawe ʻana i nā lāʻau hoʻokahe koko no ka manawa lōʻihi.

Nā pilikia o ka mālama ʻana

Ma keʻano laulā, haʻahaʻa ka pilikia o nā pilikia mai ke ʻoki ʻana i ka valve. Eia nō naʻe, hiki i nā pilikia ke komo pū me:

  • Nā maʻi
  • Ke kahe ʻana o ke koko
  • Nā ʻūpā koko
  • Hahau
  • Maʻi hohola
  • Nā ʻano ʻē o ka puʻuwai `(Arrhythmia)` (no ka manawa pōkole)
  • Ka emi ʻana o ka hana o nā puʻupaʻa (no kekahi manawa pōkole)

ʻEhia ka lōʻihi e ho'ōla ai mai kēia lāʻau lapaʻau?

Hiki i ke ʻoki hoʻololi valve aortic ke hala ma kahi o ʻelua a ʻekolu mahina e hoʻōla piha ai. Hiki i ke ʻoki hoʻoponopono valve aortic ke hala ma kahi o hoʻokahi a ʻelua mahina e hoʻōla piha ai.

Hiki ke pale ʻia ka valve aortic bicuspid?

ʻAʻohe ala e pale aku ai i ka valve aortic bicuspid. He mea hānau ia, ʻo ia hoʻi ua hānau ʻia ʻoe me ia. Eia nō naʻe, hiki iā ʻoe ke hana i nā hoʻololi i ke ʻano o ka nohona e hiki ai ke hōʻemi i kou pilikia o ka loaʻa ʻana o nā maʻi puʻuwai ʻē aʻe, e like me ka atherosclerosis a me ka maʻi artery coronary. Inā he valve aortic bicuspid kāu, e kamaʻilio me kāu kauka e pili ana i ka hoʻokele ʻana i kāu mau kumu pilikia maʻi puʻuwai. ʻO kēia mau mea:

  • Ke koko kiʻekiʻe (Hypertension)
  • ʻO ke kolesterol kiʻekiʻe `(Hyperlipidemia)`
  • Maʻi diabetes
  • Nā mea e pili ana i ke ʻano o ka nohona e like me nā huahana paka a me ka hoʻohana ʻana i ka waiʻona

Inā he bicuspid aortic valve koʻu, he aha kaʻu e manaʻo ai?

Ma kahi o 98% o ka poʻe i hana ʻia ke ʻoki valve e ola me ka ʻole o ka hopena i ko lākou ola. Inā he valve aortic bicuspid kou, hiki iā ʻoe ke ola e like me kekahi me ka ʻole o ke kūlana.Eia nō naʻe, pono ʻoe e nānā mau ʻia a me nā hoʻokolohua me kāu kauka. E nānā kāu kauka i kāu valve a e hōʻoia e loaʻa iā ʻoe ka lāʻau lapaʻau ke pono. He mea nui ka lāʻau lapaʻau e pale aku i nā pilikia.

Pehea wau e mālama ai iaʻu iho?

Me kahi valve aortic bicuspid, hiki iā ʻoe ke hana i nā mea he nui āu e makemake ai. Pono ʻoe e hana i kekahi mau hoʻololi i ke ʻano o ka nohona e kōkua ai i ka mālama ʻana i kou puʻuwai olakino a hoʻēmi i ke kaumaha ma kou puʻuwai. ʻO kēia mau mea:

  • Ka ʻai ʻana i nā meaʻai olakino no ka puʻuwai.
  • Hoʻemi nui i ka nui o ka sodium (paʻakai) āu e ʻai ai.
  • Ke pale ʻana i ka hana kino nui.

Pono ʻoe i nā manawa maʻamau me kāu kauka e nānā i ke ʻano o ka hana ʻana o kou puʻuwai. Inā ua hana ʻia ke ʻoki kino, e loaʻa iā ʻoe nā hahai ʻana ma hope o ʻelua pule, ʻekolu mahina, a me ʻeono mahina. Ma hope o kēlā, e loaʻa iā ʻoe kahi manawa i kēlā me kēia makahiki. He mea nui kēia mau manawa e mālama iā ʻoe i ke olakino a e nānā i kāu mau valves e ʻike i nā pilikia ma mua o ko lākou lilo ʻana i mea koʻikoʻi.

Āhea wau e hopohopo ai e pili ana i ka valve aortic bicuspid?

Pono ʻoe e hopohopo e pili ana i kahi valve aortic bicuspid ke hoʻomaka ia e hoʻopilikia i ka hana o kou puʻuwai. Hiki i ka maʻi valve aortic bicuspid ke hana i ka stenosis aortic a me ka regurgitation. I ka hala ʻana o ka manawa, hiki i kēia mau pilikia ke hōʻeha mau loa i ka puʻuwai.

Āhea wau e ʻike ai i kaʻu kauka?

E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou pono e hele mai no nā manawa i hoʻonohonoho ʻia. Inā ua hana ʻia ke ʻoki kino iā ʻoe, e loaʻa ana kekahi mau hana hahai i loko o ka makahiki mua a laila hoʻokahi i kēlā me kēia makahiki ma hope o kēlā.

Inā loaʻa i kekahi o kou ʻohana nā pilikia valve puʻuwai, akā ʻaʻole ʻoe i ʻike ʻia, hiki i kāu kauka ke kuhikuhi iā ʻoe i kahi cardiologist . Hiki i kāu cardiologist ke hoʻāʻo iā ʻoe no ka maʻi puʻuwai a hāʻawi iā ʻoe i ka ʻōlelo aʻoaʻo.

Āhea wau e hele ai i ka Emergency Treatment Unit (ETU) ?

Inā loaʻa iā ʻoe nā hōʻailona o ka haki ʻana o ka aneurysm a i ʻole ka dissection , e kāhea koke i ka 911 (a i ʻole kāu helu ulia pōpilikia kūloko) :

  • ʻEha koke, ʻoi, a ʻeha hou i ka umauma a i ʻole ke kua
  • Manaʻo ka ʻili he pipili a he hou
  • Pōʻino
  • Pōʻino
  • Nā palpitations o ka puʻuwai
  • Ka luaʻi a me ka luaʻi
  • Paʻakikī ka hanu ʻana

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

Inā ua ʻike ʻia ʻoe a i ʻole kāu keiki me kahi valve aortic bicuspid, e kamaʻilio me kāu kauka e pili ana i kou maʻi puʻuwai a inā pono ʻoe i ka lāʻau lapaʻau. ʻO kekahi mau nīnau e nīnau ai:

  • He mea pono anei ke ʻoki kino?
  • Hiki iā ʻoe ke paipai i nā hoʻololi nohona olakino no ka puʻuwai?
  • Aia kekahi mau hōʻailona o ke kahe koko a i ʻole ka ʻūlū ʻana o ka aorta?
  • Pehea lā ke ʻano o ke kaʻina hana ho'ōla?
  • He aha nā hōʻailona a i ʻole nā ​​​​pilikia e pono iaʻu e makaʻala ma ka home?
  • He aha nā hana e hiki ke hoʻoweliweli?
  • Pehea e hiki ai iaʻu ke hōʻemi i ka pilikia o kaʻu keiki i ka maʻi puʻuwai i ka wā e hiki mai ana?
  • Loaʻa iā ʻoe nā kumuwaiwai e hiki ke kōkua iaʻu e wehewehe i kēia hōʻailona i kaʻu keiki?

Hiki ke hoʻoluhi nui ʻia ka hana ʻana me kahi valve aortic bicuspid a hiki ke hāpai i nā nīnau he nui. E hoʻomanaʻo, aia nā kauka a me nā kauka ʻoki ma aneʻi e kōkua iā ʻoe a i ʻole kāu keiki e noho olakino a ikaika. Inā ua ʻike ʻia ʻoe a i ʻole kāu keiki me kēia maʻi i kēia manawa, e hoʻokaʻawale i kekahi manawa e aʻo hou e pili ana i kēia maʻi. E kamaʻilio me kāu kauka a loaʻa ka ʻike e pono ai ʻoe e ʻoluʻolu e pili ana i ka mālama ʻana i ke ʻano. Eia kekahi, e hoʻomanaʻo he ʻenehana kā lākou e hopu a mālama i nā pilikia i ka wā mua.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai

He maʻi hānau ʻia ka valve aortic bicuspid i hiki ke mālama ʻia. Mai hopohopo, akā e makaʻala.

ʻO ka mea nui loa, ʻo ia ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono, e hoʻāʻo ʻia i ka manawa kūpono, a e ola i kahi nohona olakino. ʻAʻole ʻoe hoʻokahi, aia nā kauka e hiki ke kōkua iā ʻoe. Manaʻolana mākou ua kōkua kēia ʻike iā ʻoe e loaʻa kahi ʻike maikaʻi aʻe o kēia maʻi.

👩🏽‍⚕️ Nā nīnau hou aku (FAQs)

💬 He aha ke ʻano o ka valve aortic bicuspid?

ʻO ka valve nui i loko o ko kākou puʻuwai (Aortic valve) maʻamau he 3 mau leaflet. Eia nō naʻe, ʻo ka poʻe me kēia ʻano genetic ʻē aʻe i hānau ʻia me 2 mau leaflet wale nō. He maʻi genetic kēia e hoʻopilikia ana i nā poʻe he nui.

💬 He aha ka hopena o kēia ma ka puʻuwai?

Ke loaʻa wale nā ​​​​​​lau liʻiliʻi ʻelua, ʻaʻole paha e pani pono ka valve, e kahe ana ke koko i hope (regurgitation), a i ʻole e paʻa paha ka valve a pale i ke kahe ʻana o ke koko i mua (stenosis). ʻO kēia ke kumu e hana ikaika ai ka puʻuwai.

💬 Pono anei kekahi kanaka me kēia maʻi i ke ʻoki kino?

ʻAʻole pono pinepine ke ʻoki kino i ka wā kamaliʻi. Eia nō naʻe, inā nāwaliwali ka valve i kou wā ʻelemakule, pono maoli ke ʻoki kino a me kahi valve hana hou (hoʻololi valve).


ʻO ka valve puʻuwai bicuspid, valve aortic, maʻi puʻuwai, nā kīnā puʻuwai hānau ʻia, ʻoki puʻuwai, stenosis aortic, regurgitation aortic

Frequently Asked Questions (FAQ)

He mea kēia i loaʻa mai nā hanauna mai?

Me he mea lā he mea hiki, akā, ʻaʻole maopopo loa i nā kānaka noiʻi nā kikoʻī.

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia?

Hiki i kāu kauka ke nānā i kou puʻuwai a hana i kēia mau hoʻokolohua e ʻike ai inā he valve aortic bicuspid kou:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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