Loaʻa iā ʻoe a i ʻole kekahi āu i ʻike ai he aTTP (acquired thrombotic thrombocytopenic purpura), kahi maʻi koko koʻikoʻi a laha ʻole? Inā pēlā, ua lohe paha ʻoe i kahi lāʻau i kapa ʻia ʻo Caplacizumab. ʻOiai he lāʻau lapaʻau kūikawā ia me kahi inoa paʻakikī, e kamaʻilio maʻalahi kākou e pili ana iā ia, ma ke ʻano hiki iā ʻoe ke hoʻomaopopo, a ma ke ʻano aloha, ʻeā?
He aha ke ʻano lāʻau lapaʻau ʻo Caplacizumab?
I ka ʻōlelo maʻalahi, he pilikia koʻikoʻi ka aTTP me ko kākou koko ʻana a me ke kahe ʻana o ke koko. ʻO ka mea e hana ʻia ana, ʻo ia ka hana ʻana o nā ʻōpū koko liʻiliʻi i loko o nā kīʻaha koko ma ke kino holoʻokoʻa, a emi koke ka nui o kā kākou mau platelets. ʻO nā platelets kahi ʻano cell e kōkua ana i ka hoʻōki ʻana i ke kahe ʻana o ke koko. Ke hoʻohana ʻia lākou e hana i nā ʻōpū koko pono ʻole ma kēia ʻano, lilo lākou i lawa ʻole e hoʻōki i ke kahe ʻana o ke koko ma kahi e pono maoli ai.
ʻO kēia kahi e hele mai ai kahi lāʻau i kapa ʻia ʻo Caplacizumab e hoʻopakele iā mākou. Hana ia ma ka hoʻōki ʻana i kēlā mau ʻōpū koko mai ka pipili ʻana a me ka hana ʻana i nā ʻōpū koko pono ʻole. He ʻano protein kikoʻī ia (monoclonal antibody) . ʻO ke ʻano kēia ua hoʻolālā ʻia e hana wale ma kahi pahuhopu kikoʻī loa.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau
Ma mua o kou hoʻomaka ʻana e lawe i kēia lāʻau lapaʻau, he mea nui loa ia e hāʻawi i kāu kauka i kahi moʻolelo piha o kou olakino. Mai hūnā i kekahi mea. E hōʻoia e haʻi iā lākou, ʻoiai hoʻi:
- Inā he maʻi kahe koko kou.
- Inā pono ʻoe e hana i kekahi ʻoki kino koke.
- Inā he maʻi kou akepaʻa.
- Inā he mau maʻi ʻaleka kou iā Caplacizumab, nā lāʻau lapaʻau ʻē aʻe, nā meaʻai, a i ʻole nā mea hoʻoluʻu.
- Inā ʻoe e hāpai ana, e hoʻāʻo ana e hāpai, a e hānai waiū ana paha.
He mea nui no kou palekana e kūkākūkā i kēia mau mea a pau me kāu kauka me ka hūnā ʻole i kekahi mea.
Pehea e hoʻohana ai i ka lāʻau lapaʻau?
He lāʻau lapaʻau kēia i hāʻawi ʻia ma ke ʻano he inikini. Hiki ke inikini ʻia i loko o kahi aʻa koko a i ʻole ma lalo o ka ʻili. Hāʻawi pinepine ʻia ia ma kahi haukapila a i ʻole ke keʻena lapaʻau. Akā i kekahi manawa pono paha ʻoe e hoʻohana i kēia inikini ma ka home.
Inā pēlā, e hāʻawi ke kauka a i ʻole ke kahu maʻi iā ʻoe i ke aʻo piha āu e pono ai. No laila, mai makaʻu. E wehewehe pono lākou i nā mea āpau, me ke ʻano o ka hoʻomākaukau ʻana i ka lāʻau lapaʻau a me ke ʻano o ka hoʻokomo ʻana. E hoʻohana i ka nui kikoʻī, i ka manawa kikoʻī, e like me ka ʻōlelo a ke kauka iā ʻoe.
He mea nui loa:Mai hoʻolei i nā nila a me nā syringe i hoʻohana ʻia i loko o ka ʻōpala. Akā, e waiho iā lākou i loko o kahi pahu ʻoi kūikawā. Inā ʻaʻohe āu, e noi i kāu kauka e kiʻi i hoʻokahi.
He aha inā e hala iaʻu kahi mahele lāʻau lapaʻau?
Inā ʻoe e poina i kahi lāʻau lapaʻau, e lawe koke iā ia i kou hoʻomanaʻo ʻana. Eia nō naʻe, inā ʻoi aku ma mua o 12 mau hola i hala, e kāpae i ka lāʻau lapaʻau i poina a lawe i kāu lāʻau lapaʻau aʻe i ka manawa maʻamau. Mai lawe i ʻelua mau lāʻau lapaʻau i ka manawa hoʻokahi.
He aha kāu e hana ai inā lawe nui ʻoe i ka lāʻau lapaʻau?
Inā manaʻo ʻoe ua lawe nui ʻoe i ka lāʻau lapaʻau, e hele koke i ka Emergency Unit (ETU) o ka haukapila. A i ʻole e kelepona i ke National Poisons Information Centre ma ka Colombo National Hospital .
Nā mea e makaʻala ai i ka wā e lawe ai i ka lāʻau lapaʻau
Pono ʻoe e noʻonoʻo hou aʻe e pili ana i kou palekana i ka wā e lawe ana i kēia lāʻau.
- Ka pilikia o ke kahe koko: ʻOiai ʻo ka hana nui o kēia lāʻau lapaʻau ka hoʻōki ʻana i ke kāpili ʻana o ke koko, ʻoi aku ka kiʻekiʻe o ka pilikia o ke kahe ʻana o ke koko. ʻO ke ʻano kēia, hiki i kahi ʻeha liʻiliʻi ke kahe koko ma mua o ka maʻamau. Hiki paha iā ʻoe ke loaʻa nā palapū ma kou kino. No laila, e makaʻala i nā hana e hiki ai ke hōʻeha, e like me ka hoʻohana ʻana i nā mea ʻoi.
- ʻOki niho a me ka mālama ʻana i nā niho: Inā e hana ʻia ana kekahi ʻoki niho a i ʻole kekahi lāʻau lapaʻau ʻē aʻe, e hōʻoia e haʻi aku i ke kauka e lawe ana ʻoe i kēia lāʻau. Pono hoʻi ʻoe e hoʻomaopopo i kāu kauka niho ma mua o ka hana ʻana i kekahi ʻoki niho.
- Nā lāʻau lapaʻau ʻē aʻe: E haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei, ʻaʻole wale nā mea i kuhikuhi ʻia e ke kauka, akā, ʻo nā lāʻau lapaʻau ma waho o ke kauka, nā huaora, nā lāʻau lapaʻau lāʻau, a me nā mea hoʻohui. Hiki i nā lāʻau hoʻokahe koko (e.g., warfarin, enoxaparin, apixaban, rivaroxaban) ke launa pū me kēia lāʻau lapaʻau.
- Nā hoʻokolohua lapaʻau: E hele i nā keʻena lapaʻau i nā lā i hoʻonohonoho ʻia e like me ke kuhikuhi a ke kauka a nānā i kou kūlana.
He aha nā hopena ʻaoʻao e hiki mai ana?
E like me nā lāʻau lapaʻau āpau, hiki iā Caplacizumab ke hana i kekahi mau hopena ʻaoʻao. He koʻikoʻi kekahi o kēia mau mea, aʻo kekahi he mea maʻamau. ʻO ka mea nui, ʻo ia ka makaʻala i kēia mau hōʻailona a hana koke inā pono.
| ʻAno o ka hopena ʻaoʻao | Nā hōʻailona āu e ʻike ai |
|---|---|
| E hoʻomaopopo koke i kāu kauka! | |
| Nā hopena alerika | ʻŌhūhū ʻili, maneʻo, pehu o ka maka, lehelehe, alelo a i ʻole ka puʻu, paʻakikī ke hanu. |
| Nā hōʻailona o ke kahe koko nui | ʻO ka ʻōpala ʻeleʻele a ʻālohilohi paha, ka luaʻi ʻana i ke koko e like me ke kofe, ka mimi ʻulaʻula a ʻeleʻele paha, nā ʻeha a i ʻole nā kiko ʻulaʻula/poni ma ka ʻili, a me ke kahe ʻana o ka ihu a i ʻole ke kahe ʻana o ke koko me ka hiki ʻole ke hoʻōki. |
| Inā hoʻomau kēia mau mea a lilo paha i mea hoʻopilikia, e haʻi i kāu kauka. | |
| Nā hopena ʻaoʻao ʻē aʻe | ʻEha poʻo, ʻeha ʻiʻo, ʻeha kua, luhi. |
Pehea e mālama ai i ka lāʻau lapaʻau?
No ka mālama ʻana i ka maikaʻi o ka lāʻau lapaʻau, he mea nui e mālama pono.
- E mālama ʻia mai nā keiki liʻiliʻi a me nā holoholona.
- Hiki ke mālama ʻia i loko o ka pahu hau a i ʻole ma ka mahana o ka lumi (ma lalo o 30°C). Mai waiho i loko o ka pahu hau.
- E mālama i ka lāʻau lapaʻau i loko o ka pahu kumu i hoʻouna ʻia mai ai, mai ka mālamalama aku.
- Inā mālama ʻoe iā ia ma ka mahana o ka lumi, hiki ke mālama ʻia a hiki i 2 mahina. Akā, mai hoʻihoʻi i kekahi lāʻau lapaʻau i mālama ʻia ma ia ʻano i loko o ka pahu hau. Inā he koena ma hope o 2 mahina, e hoʻolei aku.
- Mai hoʻohana i ka lāʻau lapaʻau i pau ka lā.
Leka Lawe-Home
- He lāʻau pale kūikawā ʻo Caplacizumab i hāʻawi ʻia no kahi maʻi koko koʻikoʻi i kapa ʻia ʻo aTTP.
- E makaʻala loa i nā ʻeha, no ka mea, he nui ka pilikia o ke kahe ʻana o ke koko i ka wā e lawe ai i kēia lāʻau.
- E hōʻoia e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei.
- Inā ʻike ʻoe i nā hōʻailona o ke kahe koko nui (nā ʻōpala ʻeleʻele, ka luaʻi ʻana i ke koko) a i ʻole nā hōʻailona o kahi maʻi ʻaleka (ka pehu ʻana o ka maka), e ʻimi koke i ke kōkua lapaʻau.
- Nou wale nō kēia lāʻau lapaʻau. Mai kaʻana like me nā poʻe ʻē aʻe.
- E hahai mau i nā ʻōlelo a kāu kauka me ka pololei.











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