He puʻupuʻu liʻiliʻi i loko o ke poʻo? E aʻo kākou e pili ana i ka craniopharyngioma ma nā ʻōlelo maʻalahi!

Ua lohe paha ʻoe i kahi puʻupuʻu ʻē e ulu ana i loko o ke poʻo, a i ʻole ma ka lolo, kokoke i kahi gland liʻiliʻi akā koʻikoʻi loa - ʻo ka pituitary gland ? Ua kapa ʻia kēia he craniopharyngioma. He mea laha ʻole ia, ʻo ia hoʻi, ʻaʻole ia he maʻi e hoʻopilikia i nā mea āpau. Akā hiki i kēia puʻupuʻu liʻiliʻi ke loaʻa ka hopena nui i kou ʻike a me kāu ʻōnaehana endocrine . No laila e kamaʻilio kākou e pili ana i kēia me nā kikoʻī hou aku i kēia lā, ʻae?

He aha ka craniopharyngioma?

I ka ʻōlelo maʻalahi, he puʻupuʻu kakaikahi loa ka craniopharyngioma, ʻaʻole maʻi kanesa (benign). Hoʻomohala ia ma kahi kokoke i kou kelepa pituitary. Ulu mālie ka puʻupuʻu. Eia naʻe, hiki iā ia ke hoʻopilikia i kou mau aʻalolo cranial , ʻoiai nā aʻalolo e pili ana i kou ʻike. Hiki iā ia ke hoʻopilikia i kāu ʻōnaehana endocrine, ka mea e kaohi ana i nā hormones i loko o kou kino.

ʻO nā lāʻau lapaʻau nui no kēia, ʻo ia ke ʻoki kino a me ka radiation therapy . I kekahi manawa, hoʻohana ʻia ka chemotherapy no kahi ʻano kikoʻī o ka puʻupuʻu, ka papillary subtype.

ʻO ka nūhou maikaʻi, ʻoi aku ma mua o 90% o ka poʻe me kēia puʻupuʻu e ola ana i ʻelima mau makahiki ma hope o ka ʻike ʻia ʻana. Eia nō naʻe, ua manaʻo ʻia kēia puʻupuʻu he maʻi mau loa . No ka mea, ʻaʻole hoʻōla mau ka lāʻau lapaʻau i nā maʻi ʻē aʻe i hoʻokumu ʻia e kēia puʻupuʻu, a ʻoi aku ka nui o ka hiki ke hoʻi hou mai kēia ʻano puʻupuʻu.

ʻO wai ka mea e loaʻa ana i ka craniopharyngioma?

I kēlā me kēia makahiki, ma kahi o ʻelua kānaka no kēlā me kēia miliona e loaʻa i kekahi o nā ʻano ʻelua o ka craniopharyngioma: adamantinomatous a me papillary . ʻO lākou ka mea maʻamau i nā hui makahiki ʻelua:

• Nā keiki ma waena o 5 a me 14 mau makahiki
• Nā mākua ma waena o 50 a me 74 mau makahiki

ʻOiai hiki ke ulu ke ʻano adamantinomatous i nā kānaka o kēlā me kēia makahiki, ʻike pinepine ʻia ke ʻano papillary i nā pākeke.

Pehea ke koʻikoʻi o kēia craniopharyngioma?

ʻO ka ʻoiaʻiʻo, he maʻi koʻikoʻi ka craniopharyngioma. Hiki ke koi ʻia ka mālama ola no ke ola holoʻokoʻa. Ma kahi o ka hapalua o nā puʻupuʻu i wehe loa ʻia me ke ʻoki ʻana e hoʻi hou mai ma hope o kekahi manawa. Hiki i kekahi o nā kūlana olakino i hoʻokumu ʻia e kēia mau puʻupuʻu ke hoʻomau ʻia ma hope o ka wehe ʻia ʻana o ka puʻupuʻu.

He aha ka ʻokoʻa ma waena o ka Craniopharyngioma a me ka Pituitary Adenoma?

Hiki i kēia mau mea ʻelua ke hoʻopilikia i ka hana o ka hormone.ʻO ka adenoma pituitary kahi ʻano puʻupuʻu e ulu ana i loko o kou kelepa pituitary. Eia nō naʻe, ulu ka craniopharyngioma ma kahi kokoke i ka kelepa. ʻOiai he benign nā ʻano puʻupuʻu ʻelua, ʻoi aku ka ikaika o ka craniopharyngioma ma mua o ka adenoma pituitary.

He aha nā hōʻailona o Craniopharyngioma?

Pili nā hōʻailona o ke craniopharyngioma i nā kūlana e kū mai ana ke hoʻopilikia kekahi mea i kāu a i ʻole kāu keiki pituitary gland, hypothalamus gland, optic nerves , a me ka lolo.

• No nā keiki: Hiki i kēia ke hoʻopilikia i ka ulu ʻana a me ka ulu ʻana o nā keiki. ʻOi aku ka maopopo o kēia i nā keiki ma mua o nā pākeke me ka craniopharyngioma.
• No nā keiki a me nā pākeke: Hiki ke hoʻopilikia ʻia ka ʻike. ʻOi aku hoʻi, hiki ke emi ka ʻike peripheral .

Eia nō naʻe, no ka mea hiki ke like kēia mau hōʻailona me nā maʻi ʻē aʻe, hiki ke paʻakikī i nā kauka ke hoʻoholo koke ua hoʻokumu ʻia kēia mau hōʻailona e kēia puʻupuʻu.

Nā kūlana i hoʻokumu ʻia e ke kaomi ma ka pituitary gland

ʻO kāu a i ʻole ke kelepa pituitary o kāu keiki ke kaohi i nā hana hormonal he nui o ke kino. Ke kaomi kahi craniopharyngioma ma kēia kelepa, hiki ke loaʻa nā kūlana penei:

• Ka hemahema o ka Hormone Ulu (GH): Hiki i kēia ke kumu i ka ulu ʻole o nā keiki. I nā pākeke, hiki i ka hemahema o ka GH ke alakaʻi i ka nāwaliwali, ka osteoporosis ( ka lahilahi o nā iwi), ka emi ʻana o ka ikaika o nā ʻiʻo, ka piʻi ʻana o ka cholesterol LDL, a me nā maʻi puʻuwai.
• Ka hemahema o ka Gonadotropin: Hiki i ka poʻe me kēia maʻi ke lohi ka wā ʻōpiopio. Hiki i nā wahine ke oki i ka menstruation, kahi maʻi i kapa ʻia ʻo amenorrhea .
• Ka hemahema o ka hormone adrenocorticotropic (ACTH): Hiki i kēia ke hoʻonāwaliwali a me ka luhi. Hiki iā ia ke hoʻemi i ke kaumaha, ka nalowale o ka makemake, ka nāwaliwali o nā ʻiʻo, ka nausea a me ka luaʻi ʻana, a me ke koko haʻahaʻa ( hypotension ).
• Ka hemahema o ka Thyroid Stimulating Hormone (TSH): Hiki i ka poʻe me ka TSH haʻahaʻa ke ʻike i nā hōʻailona e like me ka luhi, nā wā kūpono ʻole, a me ka poina ʻana.
• ʻO ka maʻi diabetes insipidus waena (CDI): Hōʻike ʻia kēia ʻano e ka makewai nui ( polydipsia ) a me ka mimi pinepine ( polyuria).) hiki mai. Hiki i ka poʻe me CDI ke ʻike i nā kūlana e like me ka maloʻo ʻana o ka wai , ka puʻuwai puʻuwai kūpono ʻole, ke kuni, ka ʻili maloʻo a me nā membrane mucous, ka huikau, a me nā hopu ʻana.

Nā kūlana i hoʻokumu ʻia e ke kaomi ma ka hypothalamus

ʻO ka hypothalamus o kāu a i ʻole kāu keiki e kāohi i nā kaʻina hana o ke kino e like me ke ʻano, ka pōloli a me ka make wai, nā ʻano hiamoe, a me ka hana moekolohe. Ke kaomi kahi puʻupuʻu craniopharyngioma i ka hypothalamus, hiki ke loaʻa nā kūlana penei:

• ʻO ka momona hypothalamic: Pili kēia i ka momona e kū mai ana me ka palena o ka calorie, hoʻoikaika kino, a me ka kaohi ʻana i ka ʻai.
• ʻO ka maʻi Froehlich: Makemake ka poʻe me kēia maʻi i ka pōloli ʻaʻohe mea nui ka nui o kā lākou ʻai ʻana, e alakaʻi ana i ka momona. Hiki i nā keiki me ka maʻi Froehlich ke ulu mālie aʻe ma mua o nā keiki ʻē aʻe. Hiki i kekahi mau keiki ke loaʻa ka ʻike maka maikaʻi ʻole a me ke kīnā noʻonoʻo.
• ʻO ka maʻi hiamoe-ala ʻole 24 hola: He maʻi hiamoe kēia e hiki ʻole ai i nā kānaka ke hahai i kahi papa hana hiamoe maʻamau. Hiki i kekahi poʻe ke loaʻa i ka nele nui o ka hiamoe .

Pehea ka hopena o kēia puʻupuʻu i kāu ʻike a i ʻole kāu keiki?

Hoʻomohala pinepine nā ʻōʻō Craniopharyngioma kokoke loa i nā aʻalolo optic o kāu a i ʻole kāu keiki. Ke hoʻopaʻa ʻia kēia mau aʻalolo, hiki iā lākou ke hana i ka ʻike maka pōwehiwehi a i ʻole nā ​​pilikia me ka ʻike peripheral.

He aha ke kumu o ka craniopharyngioma?

ʻAʻole ʻike nā kānaka noiʻi i ke kumu kikoʻī, akā manaʻoʻiʻo lākou e ulu ana kēia mau puʻupuʻu mai nā pūnaewele e kōkua ana i ke kūkulu ʻana i ka pituitary gland o kāu a i ʻole kāu keiki. No kekahi kumu, lilo kēia mau pūnaewele i mea ʻē, hoʻonui, a ulu.

Pehea e ʻike ai nā kauka i ka Craniopharyngioma?

Inā e nānā ʻia ʻoe no kēia ʻano puʻupuʻu, e nīnau paha kāu kauka e pili ana i kou mōʻaukala olakino a me ka ulu ʻana o ke kino. Inā e nānā ʻia ana kāu keiki, e nīnau paha lākou e pili ana i kona ulu kino, ka ulu ʻana o ka noʻonoʻo, ka ʻike, a inā paha e makewai nui ʻo ia a pono paha e mimi pinepine.

He aha ke ʻano o nā hoʻokolohua e hana ʻia?

Hiki i nā kauka ke hana i nā hoʻokolohua e like me kēia:

• Nā hoʻāʻo koko: Ke ana kēia i kekahi mau pae hormone.
• Urinalysis: Nānā i nā pilikia o ka puʻupaʻa.
• CT scan (Computed Tomography - CT scan): Hoʻohana ʻia kahi moʻo o nā kukuna X a me kahi kamepiula e hana i nā kiʻi ʻekolu-dimensional (3D) o nā ʻiʻo palupalu a me nā iwi.
• MRI Scan (Magnetic Resonance Imaging - MRI):He hoʻāʻo ʻeha ʻole kēia e hoʻohana ana i kahi magnet nui, nā nalu lekiō, a me ke kamepiula e hana i nā kiʻi maopopo loa o nā ʻōpū a me nā ʻano o ke kino.
• Biopsy: Hana nā kauka i kahi biopsy (lawe i kahi hāpana kiko) a nānā i nā pūnaewele, wai, ʻiʻo, a i ʻole nā ​​​​​​mea ulu ma lalo o kahi microscope.

Hiki ke mālama ʻia ke Craniopharyngioma?

Hoʻōla pinepine ʻia ka Craniopharyngioma me ke ʻoki lolo . Hiki ke hana ʻia kēia me ka hoʻohana ʻana i kahi kāmela liʻiliʻi (scope) i hoʻokomo ʻia ma o ka ihu, a i ʻole ma ka hana ʻana i kahi lua liʻiliʻi ma ke poʻo ( craniotomy ). ʻO ka pahuhopu o ke ʻoki ʻana, ʻo ia ka wehe ʻana i ka nui o ka puʻupuʻu e like me ka hiki me ka hoʻēmi ʻana i ka hōʻino ʻana i ka pituitary gland, hypothalamus, a i ʻole nā ​​​​aʻalolo optic. Eia nō naʻe, pono paha kekahi poʻe e lawe i nā lāʻau lapaʻau hormone ma hope o ke ʻoki ʻana. Eia kekahi, hiki ke ʻōlelo ʻia ka radiation therapy ma hope o ke ʻoki ʻana inā ʻaʻole hiki ke wehe pono ʻia ka puʻupuʻu.

He aha nā hopena ʻaoʻao maʻamau o ke ʻoki kino?

He paʻakikī loa ke ʻoki ʻana i ka craniopharyngioma. ʻO ka mea mua, no ka mea, ulu kēia mau puʻupuʻu kokoke i nā aʻalolo palupalu loa a me ke kelepa pituitary, aia kahi pilikia kiʻekiʻe o ka hōʻino ʻana iā lākou. ʻO ka lua, ʻo ka wehe ʻana i kahi craniopharyngioma ua like ia me ka wehe ʻana i kahi sticker mai kahi envelopp me ka ʻole o ka hōʻino ʻana i ka envelopp. ʻO kēia no ka mea ua pili pono kēia mau puʻupuʻu i ka kelepa pituitary a me nā aʻalolo e pili ana i ka ʻike. Manaʻo kekahi mau kauka hiki i ke ʻoki ʻana e wehe i kēia mau puʻupuʻu ke hana i ka pōʻino e like me ka puʻupuʻu ponoʻī. No laila, he mea nui e hoʻomaopopo mua i ke kumu o ke ʻoki ʻana a me nā hopena ʻaoʻao e manaʻo ʻia.

Hiki ke pale ʻia ke Craniopharyngioma?

ʻO ka mea pōʻino, ʻaʻole hiki ke pale ʻia kēia mau puʻupuʻu. Hoʻokumu ʻia lākou ma muli o nā loli i loko o nā pūnaewele e kū mai ana i ka wā o ka ulu ʻana o ke kino o kāu a i ʻole ke kino o kāu keiki.

ʻEhia ka lōʻihi e hiki ai iā ʻoe ke ola me Craniopharyngioma?

He nui ka poʻe e ola ana no nā makahiki ma hope o ka mālama ʻana. Akā hiki i kēia mau puʻupuʻu ke hoʻi hou mai. Ma keʻano holoʻokoʻa, ma kahi o 17% o nā puʻupuʻu i wehe loa ʻia me ke ʻoki ʻana e hoʻi hou mai. Piʻi kēia helu i 25% a 63% no nā puʻupuʻu i wehe hapa wale ʻia. ʻO ka hapa nui o nā craniopharyngiomas e hoʻi mai ana e hoʻi mai i loko o ʻekolu mau makahiki o ke ʻoki ʻana.

Manaʻo kekahi mau kauka he maʻi mau ka craniopharyngioma e pono ai ka mālama lōʻihi a me ka nānā ʻana. Aia kekahi mau kumu no kēia:

• Pono paha ʻoe a i kāu keiki paha i kahi ʻoki ʻē aʻe e wehe ai i kahi puʻupuʻu e hoʻi hou mai ana.
• Inā pili ʻoe a i ʻole ka pituitary gland a i ʻole hypothalamus o kāu keiki i kahi puʻupuʻu a i ʻole ke ʻoki ʻana, pono paha ka lāʻau hoʻololi hormone .
• He nui nā keiki me ka momona hypothalamic i hoʻokumu ʻia e ka puʻupuʻu e pilikia nui ana i nā pilikia olakino ʻē aʻe. Inā loaʻa i kāu keiki ka momona hypothalamic, pono ʻoe i ke kākoʻo a me ke alakaʻi e kōkua i kāu keiki e koho i nā meaʻai maikaʻi a hoʻoikaika kino mau.

Āhea wau/kaʻu keiki e ʻike ai i ke kauka?

Pono paha ʻoe a i ʻole kāu keiki e noho me kahi craniopharyngioma no nā makahiki he nui. Hiki i kēia mau puʻupuʻu ke ulu hou, a ʻaʻole paha e hoʻopau loa ka lāʻau lapaʻau i nā hōʻailona āpau. E noʻonoʻo i kēia mau mea i ka wā e hoʻolālā ai i kāu/kāu keiki:

• Pono ʻoe e ʻike i kāu kauka i kēlā me kēia makahiki e nānā i ke olakino holoʻokoʻa o kāu a i ʻole kāu keiki.
• E kauoha paha kāu kauka a i ʻole ke kauka o kāu keiki i nā scan makahiki, ʻo ia hoʻi nā scan MRI , e nānā no ka hoʻi hou ʻana o nā ʻōpū.
• Pono paha ʻoe a i kāu keiki paha i ke kōkua i ka mālama ʻana i nā kūlana e like me ka hemahema o ka hormone a i ʻole nā ​​​​pilikia ʻike i hoʻoponopono ʻole ʻia e ke ʻoki ʻana.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka o kaʻu keiki?

ʻOiai he puʻupuʻu kakaikahi ka craniopharyngioma, ʻaʻole ia he maʻi kanesa, hiki iā ia ke hana i kekahi mau kūlana olakino paʻakikī e pono ai ka mālama lōʻihi. Inā loaʻa iā ʻoe a i ʻole kāu keiki kēia puʻupuʻu, e hopohopo paha ʻoe e pili ana i ka mālama ʻana i kēia kūlana no ke ola holoʻokoʻa. Eia kekahi mau nīnau e hiki ke kōkua iā ʻoe e kamaʻilio me kāu kauka a i ʻole ke kauka o kāu keiki:

• ʻAʻole au i lohe i kēia hua. Hiki iā ʻoe ke wehewehe mai i ke ʻano o ia mea?
• Hiki i kēia puʻupuʻu ke hoʻoulu iaʻu/kaʻu keiki i nā pilikia olakino koʻikoʻi ʻē aʻe?
• No ke aha i loaʻa ai kēia puʻupuʻu iaʻu/kaʻu keiki?
• He aha nā koho lapaʻau e loaʻa ana?
• He aha nā kūlana o ka holomua ʻana o ka lāʻau lapaʻau?
• E hoʻopau anei ka lāʻau lapaʻau i nā hōʻailona o kaʻu/kaʻu keiki?
• He aha nā hopena ʻaoʻao pōkole a me ka hopena lōʻihi o ka lāʻau lapaʻau?
• He aha ka mea e hana ai inā ulu hou ka puʻupuʻu?

ʻOiai inā loaʻa iā ʻoe ke ʻoki ʻana e wehe i kahi craniopharyngioma, hiki i kēia mau puʻupuʻu kakaʻikahi, ʻaʻole cancerous ke loaʻa nā hopena lōʻihi iā ʻoe a i kāu keiki paha. Eia kekahi, pono paha ʻoe a i ʻole kāu keiki i ka mālama olakino mau no nā kūlana i hoʻokumu ʻia e ka puʻupuʻu. Ma kekahi ʻano, he maʻi mau ka craniopharyngioma e pono ai ʻoe a i ʻole kāu keiki e mālama no ke koena o kou ola. ʻOiai ʻaʻole hiki i nā kauka ke ho'ōla piha iā ia, hiki iā lākou ke hana i kā lākou mea maikaʻi loa e kōkua iā ʻoe a me kāu keiki e kū i nā pilikia o ka noho ʻana me kēia puʻupuʻu kakaʻikahi.

ʻO ka mea hope loa, leka lawe i ka home:

He maʻi koʻikoʻi a laha ʻole ka Craniopharyngioma, akā hiki ke mālama ʻia me ka mālama lapaʻau kūpono a me ka hoʻolālā lōʻihi.

• E ʻimi i ka ʻōlelo aʻoaʻo lapaʻau maʻamau: He mea nui loa ia e noho pū me kāu hui lapaʻau a hele i nā hoʻokolohua a me nā manawa i hoʻonohonoho ʻia.
• E noho me ka manaʻolana: ʻOiai he huakaʻi paʻakikī kēia, ʻaʻole ʻoe hoʻokahi. Me ke kākoʻo o nā kauka, ka ʻohana, a me nā hoaaloha, e loaʻa iā ʻoe ka ikaika e lanakila ai i kēia.
• E hoʻomaopopo: ʻO ka hoʻomaopopo maikaʻi ʻana e pili ana i kēia maʻi, kāna mau lāʻau lapaʻau, a me nā pilikia e hiki mai ana e kōkua iā ʻoe e hana i nā hoʻoholo naʻauao.

E hoʻomanaʻo, ʻo ka ʻike mua ʻana a me ka mālama pono ʻana nā ala maikaʻi loa e ola pono ai me kēia maʻi. Inā loaʻa iā ʻoe a i ʻole kāu keiki kekahi o kēia mau hōʻailona, ​​mai kānalua e ʻike i ke kauka.

ʻO Craniopharyngioma, nā puʻupuʻu lolo, ke kelepa pituitary, nā hormones, ka ʻike, ke olakino o ke keiki, nā puʻupuʻu ʻaʻole maʻi kanesa