E aʻo kākou e pili ana i ka lāʻau pale Fosdenopterin (he lāʻau lapaʻau no ka Molybdenum Cofactor Deficiency)

He mea hauʻoli no ka ʻohana ka lawe ʻana mai i kahi pēpē hānau hou i ka home. Akā i kekahi manawa, hiki i kekahi mau pēpē ke hānau ʻia me nā maʻi genetic kakaʻikahi loa. He mea maʻamau iā mākou ke makaʻu a hopohopo nui i ka lohe ʻana i kēia mau mea. Akā i kēia lā, no ka mea ua holomua nui ka ʻepekema lapaʻau, aia nā hopena no nā maʻi he nui i loaʻa ʻole ka lāʻau lapaʻau ma mua. I kēia lā, e kamaʻilio mākou e pili ana i kahi lāʻau lapaʻau kūikawā i hāʻawi ʻia no ia ʻano maʻi kakaʻikahi. ʻO ia ka lāʻau pale Fosdenopterin.

He aha kēia Fosdenopterin? He aha kāna hana?

I ka ʻōlelo maʻalahi, ʻo Fosdenopterin (inoa inoa: Nulibry) kahi lāʻau lapaʻau i hoʻohana ʻia e mālama i kahi maʻi genetic kakaʻikahi loa i kapa ʻia ʻo Molybdenum cofactor deficiency (MoCD) . ʻAe, e nānā kākou i ke ʻano o MoCD. E noʻonoʻo i ko kākou kino e like me kahi hale hana nui. I mea e hana pono ai kēia hale hana i nā mea āpau, pono ia i nā limahana liʻiliʻi like ʻole i kapa ʻia ʻo enzymes. No ka hana pono ʻana o kēia enzyme, pono ia i kahi ʻāpana liʻiliʻi ʻē aʻe e kōkua iā ia. Kāhea mākou iā ia he cofactor. ʻO Molybdenum cofactor kekahi o ia mau mea kōkua koʻikoʻi. ʻO ke kanaka me MoCD he kīnā genetic i loko o ko lākou kino e pale ai iā ia mai ka hana ʻana i kēia Molybdenum cofactor. A laila, ma muli o kēia mea kōkua, ʻaʻole hana kekahi mau enzymes. ʻO ka hopena, hoʻomaka nā toxins e hōʻiliʻili i loko o ke kino. ʻO kēia mau toxins, ʻoiai nā mea e hōʻeha nui ai i ka lolo, ʻo ia ka mea e hana ʻia ma MoCD. ʻO kēia kahi e komo mai ai kahi lāʻau lapaʻau i kapa ʻia ʻo Fosdenopterin. ʻO ka mea a kēia lāʻau lapaʻau e hana ai, ʻo ia ka hāʻawi ʻana i ka Molybdenum cofactor ʻaʻole hiki i ke kino ke hana mai waho. Ua like ia me ka lawe ʻana mai i kahi limahana nalowale mai ka hale hana. A laila hoʻomaka hou kēlā mau enzyme hana ʻole e hana, ua pau ka hōʻiliʻili ʻana o nā mea ʻawahia, a ua emi ka pōʻino o ka lolo.

Nā mea āu e haʻi aku ai i kāu kauka ma mua o ka lawe ʻana i ka lāʻau lapaʻau

Ma mua o ka hāʻawi ʻana i kēia lāʻau lapaʻau iā ʻoe a i kāu pēpē paha, he mea nui loa ia e kūkākūkā i kekahi mau ʻike me kāu kauka. No ka mea, ʻo ka holomua a me ka palekana o ka lāʻau lapaʻau e pili ana i kēlā ʻike. Eia kekahi mau mea e pono e haʻi pono ʻia:

• Nā Allergies : E haʻi mai iā mākou inā he mau allergies kou iā Fosdenopterin a i ʻole kekahi lāʻau lapaʻau ʻē aʻe, meaʻai, nā kala, a i ʻole nā ​​mea mālama.
• Hāpai keiki : Inā hāpai ʻoe, e hoʻāʻo ana e hāpai, a manaʻo paha ua hāpai ʻoe, pono ʻoe e haʻi i kāu kauka.
• Inā he makuahine hānai waiū ʻoe: Inā he makuahine hānai waiū ʻoe, e hoʻomaopopo pū i ke kauka e pili ana i kēia.

Inā ʻoe e haʻi pololei mai i kēia ʻike me ka hūnā ʻole ʻana, e kōkua nui ia i ka hui lapaʻau e hāʻawi iā ʻoe i ka lāʻau kūpono a palekana loa.

Pehea ʻoe e hoʻohana ai i kēia lāʻau lapaʻau?

He inikini ʻo Fosdenopterin i hoʻokomo ʻia i loko o kahi aa. Hāʻawi pinepine ʻia e kahi hui lapaʻau ma kahi haukapila a i ʻole ke keʻena lapaʻau. Eia nō naʻe, i kekahi mau hihia, hiki ke hāʻawi ʻia ma waho o ka haukapila, ma ka home. Inā hana ʻia kēia, ʻaʻohe ou hopohopo. E hoʻomaʻamaʻa pono ke hui lapaʻau iā ʻoe i ke ʻano o ka hoʻomākaukau ʻana a me ka hāʻawi ʻana i kēia lāʻau lapaʻau me ka pololei.

• E hahai pono i nā kuhikuhi: He mea nui loa ka lawe ʻana i ka lāʻau lapaʻau e like me ka ʻōlelo a kāu kauka iā ʻoe, i ka manawa kūpono, i kēlā me kēia lā. E hoʻomau i ka lawe ʻana a hiki i ka wā e ʻōlelo ai kāu hui lapaʻau iā ʻoe e hoʻōki.
• Nā nila a me nā syringe i hoʻohana ʻia: He mea nui loa kēia. Mai hoʻolei i nā nila a me nā syringe i hoʻohana ʻia i loko o ka ʻōpala. Aia kahi pahu kūikawā no lākou (pahu ʻoi). Inā ʻaʻohe āu, hiki iā ʻoe ke noi i kāu kauka a i ʻole ka hui lapaʻau no hoʻokahi. E pale kēia iā ʻoe, kou ʻohana, a me ke kaiapuni.
• Nā Kuhikuhi no ka Hoʻohana ʻana: E heluhelu pono i nā KUHIKUHI NO KA HOʻOHANA ʻana e hele mai me kēia lāʻau lapaʻau. Inā he mau nīnau kāu e pili ana i nā mea i loko, e nīnau i kāu hui lapaʻau no ka wehewehe ʻana.

He aha kāu e hana ai inā e poina ʻoe i kahi lāʻau?

ʻOkoʻa iki kēia ma muli o kahi i loaʻa ai ka lāʻau lapaʻau.

• Inā ʻoe e lawe ana i kāu lāʻau lapaʻau ma ka haukapila a i ʻole ke keʻena lapaʻau: Inā ʻaʻole hiki iā ʻoe ke hele i kāu manawa i hoʻonohonoho ʻia, e kāhea koke i kāu hui lapaʻau. He mea nui loa ia ʻaʻole e haʻalele i kāu manawa i hoʻonohonoho ʻia.
• Inā ʻoe e lawe ana i kāu lāʻau lapaʻau ma ka home: Inā poina iā ʻoe kahi lāʻau, e lawe koke iā ia i kou hoʻomanaʻo ʻana. Akā i ka wā e lawe ai ʻoe i kāu lāʻau aʻe, e kali ma ka liʻiliʻi he 6 mau hola ma mua o kou lawe ʻana i ka lāʻau i poina. Mai lawe i ka lāʻau pālua a i ʻole kahi lāʻau keu. Inā kānalua ʻoe, e kamaʻilio me kāu hui mālama ola no ka ʻōlelo aʻo.

He aha ka mea e hana ai inā ʻoe e lawe i ka overdose?

Inā manaʻo ʻoe ua lawe nui ʻoe i ka lāʻau lapaʻau, e kāhea koke aku i ke Kikowaena ʻIke ʻAihue Lahui ma ka Halemai Lahui ma Colombo, a i ʻole e hele i ka ʻOihana Pilikia (ETU) o ka haukapila kokoke loa.

Nā mea e makaʻala ai i ka wā e hoʻohana ai i ka lāʻau lapaʻau

• Nā lāʻau lapaʻau ʻē aʻe: ʻAʻole i manaʻo ʻia kēia lāʻau lapaʻau e launa pū me nā lāʻau lapaʻau ʻē aʻe. Eia nō naʻe, ʻoi aku ka palekana o ka haʻi ʻana i kāu kauka e pili ana i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei (me nā huaora , nā lāʻau lapaʻau lāʻau, a me nā mea hoʻohui). Eia kekahi, e haʻi i kāu kauka inā ʻoe e puhipaka a inu waiʻona paha .
• E pale iā ʻoe iho mai ka lā: He mea nui loa kēia. Hiki i kou ʻili ke lilo i mea maʻalahi loa i ka lā i ka wā e lawe ana i kēia lāʻau lapaʻau. No laila, e pale i ka hele ʻana i waho i ka lā i ka hiki. Inā pono ʻoe e hele i waho, e ʻaʻahu i nā lole e uhi pono i kou ʻili a hoʻohana i kahi sunscreen maikaʻi. Mai hoʻohana i nā kukui lā a i ʻole nā ​​​​moena tanning.
• Nā nānā maʻamau: E hōʻoia e hele i nā manawa a kāu kauka. Pono ʻoe e nānā mau i ke ʻano o kāu lāʻau lapaʻau. Inā ʻaʻole e hoʻomaikaʻi ana kāu mau hōʻailona a i ʻole e ʻoi aku ka ʻino, e hoʻomaopopo i kāu hui lapaʻau.

He aha nā hopena ʻaoʻao e hiki ke loaʻa mai kēia lāʻau lapaʻau?

E like me nā lāʻau lapaʻau āpau, hiki iā Fosdenopterin ke hana i kekahi mau hopena ʻaoʻao. Eia naʻe, ʻaʻole loaʻa i nā kānaka a pau. He koʻikoʻi kekahi o kēia mau mea, a he mea maʻamau kekahi. ʻO ka mea nui loa, ʻo ia ka makaʻala iā lākou. ʻAʻole i loko o kēia papa inoa nā hopena ʻaoʻao āpau. Inā loaʻa iā ʻoe kekahi mau hōʻailona ʻē, e kamaʻilio me kāu kauka no ka ʻōlelo aʻoaʻo lapaʻau.

Pehea e mālama ai i ka lāʻau lapaʻau?

He mea nui loa ka mālama pono ʻana i kēia lāʻau lapaʻau. Inā mālama pono ʻole ʻia, e nalowale paha ka pono o ka lāʻau lapaʻau.

• E mālama ʻia mai ka hiki ʻana aku o nā keiki: E mālama ʻia mai ka hiki ʻana aku o nā keiki a me nā holoholona.
• Nā ʻōmole i wehe ʻole ʻia: Pono e mālama ʻia kēia mau mea i loko o ka pahu hau ma kahi mahana ma waena o -25 a me -10 degere Celsius . E mālama i loko o ka pahu kumu a hiki i ka hoʻohana ʻana. E pale pū mai ka mālamalama. E wehe mai ka pahu ma kahi o 30 mau minuke ma mua o ka hoʻohana ʻana.
• Ma hope o ke kāwili ʻana: Ma hope o ke kāwili ʻana i ka lāʻau lapaʻau, hiki ke mālama ʻia ma ka mahana o ka lumi a i ʻole i loko o ka friji ma kahi mahana ma waena o 2 a me 8 degere Celsius . Eia nō naʻe, pono e hoʻohana ʻia i loko o 4 mau hola o ke kāwili ʻana .
• Lāʻau lapaʻau i pau ka lāʻau: E hoʻolei aku i ka lāʻau lapaʻau i pau ka lāʻau.

E noi i kāu hui lapaʻau no ka ʻōlelo aʻoaʻo no ka hoʻolei palekana ʻana i nā lāʻau lapaʻau i hoʻohana ʻole ʻia a pau ka lāʻau. ʻO Fosdenopterin, Nulibry, Ka hemahema o ka cofactor Molybdenum, MoCD, nā maʻi genetic, nā maʻi kamaliʻi, ka lāʻau pale, nā hopena ʻaoʻao, ka lāʻau lapaʻau, Sri Lanka