Ua lohe paha ʻoe i ka mānoanoa o ke koko? He mea hou paha kēia iā ʻoe. ʻAʻole ke koko i loko o ko kākou kino he wai e like me ka wai, akā he mea ia e mānoanoa iki ana. Akā pehea inā e lilo kēia mānoanoa i mea kiʻekiʻe loa ma mua o ka mea e pono ai? ʻO ia ka manawa e loaʻa ai iā kākou ke kūlana a kākou e kamaʻilio ai i kapa ʻia ʻo "Hyperviscosity Syndrome". ʻO ia ka manawa e lilo ai kou koko i mānoanoa loa a ʻaʻole hiki ke kahe pono ma o kou mau kīʻaha koko.
He aha ka Hyperviscosity Syndrome? E hoʻomaopopo maʻalahi kākou.
I ka ʻōlelo maʻalahi, ʻo `(Hyperviscosity Syndrome)` ʻo ia hoʻi ke lilo kou koko i mānoanoa loa . E noʻonoʻo e like me ka meli. ʻOi aku ka mānoanoa o ka meli ma mua o ka wai, a ʻo ia ka mea e hana ʻia ma ʻaneʻi. Loaʻa i ko kākou koko nā mea e like me nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā protein koko. Inā piʻi aʻe kekahi a ʻoi aku paha o kēia mau mea i ka nui a inā paha e lilo nā hunaola koko ʻulaʻula i ʻano ʻē, hiki i ke koko ke mānoanoa loa. Ua like ia me ka hoʻohui ʻana i kahi palaoa hou aʻe i kahi paila a mānoanoa ia.
Ke mānoanoa ke koko ma kēia ʻano, ʻaʻole ia e neʻe maʻalahi ma o nā kīʻaha koko palupalu ma loko o ko kākou kino. ʻO ia ka manawa e hoʻomaka ai nā pilikia e kū mai.
Hiki paha i kēia kūlana ke lilo i mea weliweli?
ʻAe, he maʻi koʻikoʻi ka Hyperviscosity Syndrome. ʻIke anei ʻoe i ke ʻano o ia mea? Inā ʻaʻole holo pono ke koko, ʻaʻole loaʻa i ko kākou mau kino koʻikoʻi (e like me ka lolo, ka puʻuwai, a me nā puʻupaʻa) ka oxygen a me nā meaʻai e pono ai lākou. Hiki i kēia ke alakaʻi i nā poloka i loko o nā kīʻaha koko a me ka hana ʻole o nā kino.
Inā loaʻa i kahi keiki ʻōpio kēia maʻi, hiki iā ia ke hoʻopilikia pololei i ko lākou ulu ʻana a me ka ulu ʻana . No ka mea, i ka wā e ulu wikiwiki ana ko lākou lolo a me ke kino, he pilikia nui ka kahe koko. No laila, he mea nui loa ka makaʻala i kēia.
ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o ka Hyperviscosity Syndrome?
ʻOiai hiki ke ulu kēia ʻano i loko o kekahi, ʻoi aku ka nui o ka pilikia o kekahi poʻe. ʻO ka poʻe me kahi ʻano laha ʻole i kapa ʻia ʻo Waldenstrom macroglobulinemia e pilikia nui ana i ka loaʻa ʻana o ka Hyperviscosity Syndrome. ʻO kēia ka manawa e lilo ai kahi ʻano protein kūikawā i kapa ʻia ʻo macroglobulin i loko o ko mākou koko i kiʻekiʻe loa. Wahi a nā helu helu, ʻoi aku ma mua o 30% o ka poʻe me Waldenstrom macroglobulinemia e loaʻa i ka Hyperviscosity Syndrome i kekahi manawa o ko lākou ola.
He aha nā hōʻailona o ka Hyperviscosity Syndrome? E makaʻala kākou!
Hiki ke ʻokoʻa nā hōʻailona o kēia maʻi mai kēlā kanaka a kēia kanaka, akā hiki iā mākou ke hoʻokaʻawale iā lākou i nā ʻano maʻamau a me nā ʻano kakaʻikahi.
Nā hōʻailona maʻamau:
- ʻEha poʻo: Pinepine, i kekahi manawa ʻeha poʻo nui.
- Nā hopu ʻana: Hiki i kekahi poʻe ke loaʻa i nā kūlana e like me ka hopu ʻana.
- ʻIli ʻulaʻula: I kekahi manawa ʻulaʻula paha nā wahi e like me ka maka a me nā lima.
Nā hōʻailona maʻamau ʻole, akā koʻikoʻi:
- ʻEha umauma: Hiki ke loaʻa ka ʻeha umauma, e like me ka maʻi puʻuwai.
- Paʻakikī ke hele wāwae: He paʻakikī paha ke hele wāwae, me he mea lā ua nalowale kou kaulike.
- Nā pilikia lohe: Manaʻo paha ʻoe e nalowale ana kou lohe, a lohe paha ʻoe i nā leo like ʻole i loko o kou mau pepeiao.
- Ke kahe koko ʻana ma ke ʻano kūpono ʻole: No ka laʻana, ke kahe ʻana o nā ʻāʻī a me ke kahe pinepine ʻana o ka ihu.
- Paʻakikī ka hanu ʻana (Dyspnea): Manaʻo paha ʻoe e like me ʻoe e pilikia ana i ka hanu ʻana ʻoiai ke piʻi ʻana i nā alapiʻi a i ʻole e hana ana i nā hana māmā.
- Vertigo: Hiki paha iā ʻoe ke poniuniu, me he mea lā e wili ana kou poʻo, a ʻaʻole hiki ke kū.
- Nā loli o ka ʻike: Hiki ke ʻike ʻia ka ʻike pōwehiwehi a me ka ʻike pālua.
Inā hoʻomau ʻoe i kekahi a ʻoi aku paha o kēia mau hōʻailona, ʻoi aku ka maikaʻi o ka ʻimi ʻana i ke kōkua lapaʻau. Mai hopohopo, akā, mai hoʻowahāwahā iā lākou.
He aha ke kumu o ka Hyperviscosity Syndrome i nā pēpē ʻōpio?
Aia kekahi mau kumu kikoʻī e hiki ai ke loaʻa kēia ʻano maʻi i kahi pēpē hānau hou:
- Nā maʻi hoʻoilina: No ka laʻana, nā kūlana e like me ka "Down syndrome".
- ʻO ka maʻi diabetes gestational: Inā loaʻa ka maʻi diabetes i ka makuahine i ka wā hāpai, hiki iā ia ke hoʻopilikia i ka pēpē.
- Nā maʻi hoʻoilina: Inā ua loaʻa i kekahi o ka ʻohana kēia mau kūlana.
- Ka paʻa ʻana o ke kaula umbilical i ka hopena: Hiki i kēia ke kumu i kekahi mau hihia.
- ʻO ka maʻi hoʻoili ʻana o ka māhoe-a-māhoe: Hiki ke hana kēia i ka wā e loaʻa ai i nā māhoe like nā pilina koko ʻē aʻe i ka placenta ma waena o lākou.
He aha nā kumu o kēia maʻi i nā pākeke?
I nā mākua, e like me ka mea i ʻōlelo ʻia ma mua, ʻo `(Waldenstrom macroglobulinemia)` ke kumu nui. Ma waho aʻe o kēlā, aia paha kekahi mau kumu ʻē aʻe:
- Nā ʻano maʻi ʻaʻai koko: No ka laʻana, `(Acute myeloid leukemia - AML)` a me nā ʻano `(Leukemia)` ʻē aʻe.
- ʻO ka hypoxia mau loa: Hiki ke hana ʻia kēia e nā mea e like me kekahi mau maʻi hanu.
- Nā maʻi pili pili: No ka laʻana, nā maʻi e like me ka '(Rheumatoid arthritis)' a me ka '(Lupus)'.
- Cryoglobulinemia: ʻO kahi kūlana e hana ʻia ai nā protein ʻano ʻē i loko o ke koko.
- ʻO ka thrombocythemia koʻikoʻi: He piʻi nui o ka helu o nā platelets koko.
- ʻO ka myeloma maha: He maʻi ʻaʻai o ka iwi iwi.
- (Nā maʻi Paraneoplastic):He hōʻiliʻili o nā hōʻailona i hoʻokumu ʻia e ka maʻi ʻaʻai ma nā wahi ʻē aʻe o ke kino.
- (Polycythemia vera): Ka hoʻonui nui ʻia ʻana o ka helu o nā hunaola koko ʻulaʻula.
- (Sjögren's syndrome): He kūlana e hoʻopilikia ai i nā kelepa e hana ai i ka makū i loko o ke kino.
- ʻO ka maʻi Myelodysplastic: He pilikia me ka hana ʻana o nā pūnaewele i loko o ka iwi iwi.
Me he mea lā he mea huikau iki kēia mau inoa iā ʻoe. ʻO ka mea nui e hoʻomanaʻo ai, ʻaʻole kēia mau kūlana āpau ke kumu o ka Hyperviscosity Syndrome, akā ʻo kahi kūlana ma lalo e like me kēia e hiki ai ke hoʻomānoanoa i ke koko.
Pehea e ʻike ai i ka Hyperviscosity Syndrome? (Diagnosis)
Hoʻomaopopo pinepine nā kauka i kēia kūlana ma ka hana ʻana i kekahi mau hoʻokolohua koko , ʻo kekahi o ia mau mea:
- Hoʻāʻo kinoea koko arterial: Nānā i nā pae o ka oxygen a me ke kalapona ʻokikene i loko o ke koko.
- Hoʻāʻo Bilirubin: Nānā i ka pae o ka bilirubin, kahi mea melemele i hana ʻia i ka wā e haki ai nā hunaola koko ʻulaʻula.
- Hoʻāʻo kō koko: E nānā i ka pae kō koko (glucose).
- Helu koko piha (CBC): Ana i nā pae o nā ʻāpana āpau i loko o ke koko, me nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā protein.
- Hoʻāʻo Creatinine: Nānā i ka hana maikaʻi o nā puʻupaʻa.
- Hoʻāʻo hana o ke akepaʻa: Nānā i nā protein o ke akepaʻa.
- Nā hoʻāʻo mānoanoa o ke koko a i ʻole nā hoʻāʻo mānoanoa o ke koko holoʻokoʻa: Nā hoʻāʻo e ana pololei i ka mānoanoa o ke koko.
- Nā hoʻāʻo protein: E ana i ka nui o nā protein like ʻole i loko o ke koko.
Ma muli o nā hopena o kēia mau hoʻokolohua hiki i ke kauka ke haʻi pololei inā he Hyperviscosity Syndrome kou a i ʻole.
He aha nā lāʻau lapaʻau no kēia? (Nā ʻano lapaʻau)
ʻOkoʻa paha ka lāʻau no ka "Hyperviscosity Syndrome" ma muli o ke kumu kumu . No ka mea hiki ke ʻoi aku ka maikaʻi o ka dehydration i kēia kūlana, hiki i ke kauka ke ʻōlelo aku i ka intravenous (IV) hydration .
I kekahi mau hihia koʻikoʻi, hiki i nā kauka ke hoʻohana i nā lāʻau lapaʻau e like me:
- Nā hoʻoili koko hapa: Pili kēia i ka wehe ʻana i kahi koko liʻiliʻi a hoʻololi iā ia me kahi wai saline. Hiki i kēia ke kōkua i ka hoʻēmi ʻana i ka mānoanoa o ke koko.
- Plasmapheresis: Pili kēia i ka wehe ʻana i kahi liʻiliʻi o ka plasma, ka ʻāpana wai o ke koko, a me ka hoʻololi ʻana me kahi pani plasma. Kōkua kēia i ka wehe ʻana i nā protein ʻino mai ke koko a hoʻemi i kona mānoanoa.
Hoʻoholo ʻia kēia mau lāʻau lapaʻau e kāu kauka, ma muli o kou kūlana a me ke kumu.
Aia kekahi mau ala e pale aku ai i ka Hyperviscosity Syndrome?
ʻO ka ʻoiaʻiʻo, ʻaʻohe ala e pale loa ai i ka `(Hyperviscosity Syndrome)`. Eia nō naʻe, inā hāpai ʻoe, aia kekahi mau mea hiki iā ʻoe ke hana e hōʻemi i ka pilikia o kāu pēpē e loaʻa ana i kēia maʻi :
- E kiʻi i ka hoʻāʻo genetic: E kōkua kēia iā ʻoe e hoʻomaopopo i nā manawa kūpono e loaʻa ai kahi keiki me kahi maʻi genetic.
- E ʻai i ka meaʻai momona a hoʻoikaika kino mau : Hiki i kēia ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i ka maʻi diabetes gestational.
- E hele i nā keʻena lapaʻau a hana i nā hoʻokolohua e like me ka hoʻonohonoho ʻana: He mea nui loa e hahai i ka ʻōlelo aʻo lapaʻau i kou wā hāpai.
He aha ka mea e hana ʻia i kahi kanaka me ka Hyperviscosity Syndrome? (Hahai ʻana)
ʻO ka Hyperviscosity Syndrome kahi kūlana e pono ai ka mālama koke ʻana . Inā ʻaʻole mālama ʻia, hiki iā ia ke alakaʻi i nā pilikia e hoʻoweliweli i ke ola a me ka hāʻule ʻana o nā ʻōkana.
ʻO ka nūhou maikaʻi, ʻo nā pēpē a me nā pākeke e loaʻa ana ka lāʻau lapaʻau i ka manawa kūpono e hoʻōla loa mai kēia ʻano . Eia nō naʻe, inā ua hoʻokumu ʻia ka hyperviscosity syndrome e kahi maʻi maʻi maʻi, pono paha ʻoe e hoʻomau i ka lāʻau lapaʻau e pale aku ai i ka hoʻi hou ʻana.
He aha ke ʻano o ka Hyperviscosity Syndrome?
Hiki ke ʻokoʻa kēia mai kēlā kanaka a kēia kanaka. Ke mānoanoa ke koko, ua emi ke kahe ʻana o ke koko i ka lolo, a hiki ke hana i ka ʻeha poʻo, ka poniuniu, a i ʻole ka māʻule ʻana . Hiki i kekahi poʻe ke paʻakikī i ka hanu ʻana a i ʻole ka ʻike pohihihi .
He aha nā kumu ʻē aʻe e hoʻopilikia ai i ke kahe ʻana o ke koko?
Aia kekahi mau kumu e hiki ai i kou koko ke mānoanoa. Hiki i kou koko ke mānoanoa inā ʻano ʻē ke ʻano o kou mau hunaola koko ʻulaʻula . Hiki nō hoʻi ke mānoanoa inā kiʻekiʻe loa nā pae o kekahi o kāu mau ʻāpana koko, e like me nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a i ʻole nā protein i loko o kou koko .
ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)
ʻAe, i kēia manawa ua ʻoi aku kou maopopo i ka mea a mākou i kamaʻilio ai, ʻo "Hyperviscosity Syndrome." E hoʻomanaʻo, ʻo kēia ka manawa e mānoanoa ai ke koko a ʻaʻole hiki ke kahe pono ma ke kino holoʻokoʻa.
Hiki i kēia ke hana i nā poʻe me kekahi mau maʻi koko, a me nā pēpē hānau hou me kekahi mau maʻi genetic a i ʻole nā maʻi hoʻoilina.
ʻOiai he maʻi koʻikoʻi kēia, inā ʻike ʻia a mālama ʻia i ka wā mua, hoʻōla loa ka hapa nui o ka poʻe. No laila, inā he hopohopo a hōʻailona paha kāu a i ʻole kāu keiki, e ʻike koke i ke kauka no ka ʻōlelo aʻo. Mai hopohopo, ʻo ka mea nui ka hoʻomaopopo ʻia.
Inā he mau nīnau hou aku kāu, mai kānalua e nīnau i kāu kauka:
- He aha ke kumu kūpono loa o kēia `(Hyperviscosity Syndrome)`?
- He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia?
- Pehea e mālama ʻia ai?
- Pono anei au e hoʻomau i ka lāʻau lapaʻau?
- Inā loaʻa iaʻu kekahi keiki ʻē aʻe, hiki paha iā ia ke loaʻa i kēia maʻi pū kekahi?
E nīnau i nā nīnau e like me kēia a hoʻoponopono i nā pilikia a pau i loko o kou manaʻo.
ʻO ka maʻi hyperviscosity, ke koko ʻana, nā maʻi koko, nā hōʻailona, ka lāʻau lapaʻau, ke olakino o ke keiki, ke olakino o ka pākeke











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