He nui loa anei ka cornea o kāu keiki? Hiki paha ma muli o Megalocornea!

Ua nānā pono anei ʻoe i nā maka o kāu keiki liʻiliʻi? I kekahi manawa hiki iā mākou ke ʻike he nui iki ka cornea, ka ʻāpana poepoe a moakaka kahi e komo ai ka mālamalama i ka maka. A i ʻole ua huikau iki paha ʻoe i ka wā i haʻi aku ai ke kauka iā ʻoe i ka huaʻōlelo "Megalocornea". He aha maoli ka "Megalocornea"? Mai hopohopo, e kamaʻilio mākou e pili ana i ia mea ma ke ʻano maʻalahi e hiki ai iā ʻoe ke hoʻomaopopo.

He aha maoli ka `(Megalocornea)`?

I ka ʻōlelo maʻalahi, ʻo `(Megalocornea)` ka wā e ʻoi aku ka nui o ka membrane moakaka ma ke alo o ka maka, ka ʻāpana a mākou e kapa nei he cornea , ma mua o ka maʻamau. E noʻonoʻo, inā like ko kākou maka me ke kāmela, ua like kēia cornea me ke aniani pale ma ke alo o ke aniani o kēlā kāmela. Komo ke kukui i loko o ka maka ma o kēia. I ke ʻano o `(Megalocornea)`, ʻoi aku ke anawaena o kēia cornea (ʻo ia hoʻi, ka mamao mai kekahi ʻaoʻao a i kekahi ʻaoʻao) ma mua o 13 millimeters. ʻO ka maʻamau, ʻoi aku ka liʻiliʻi o kēia nui i kahi keiki liʻiliʻi.

ʻO kekahi mea e hana ʻia me kēia, ʻo ia ka hohonu o ka hakahaka piha i ka wai ma waena o ka cornea a me ka ʻāpana kala o ka maka (a mākou e kapa nei ʻo ka iris), i kapa ʻia ʻo ke keʻena mua , ma mua o ka maʻamau.

ʻO ka mea nui, ʻo ka `(Megalocornea)` he maʻi `(congenital)` . ʻO ia hoʻi, ua hānau ʻia ke pēpē me kēia mau hiʻohiʻona. ʻO ka hapa nui o ka manawa, ʻike nā kauka iā ia i ka wā ʻōpiopio. ʻAʻole pilikia nui ka ʻike maka o ka hapa nui o ka poʻe ma muli o kēia, a ʻaʻole ia he maʻi `(progressive)` e ʻoi aku ka ʻino i ka hala ʻana o ka manawa. ʻO ia hoʻi, ua like ia me ia. ʻO ke kū'ē kēia i kahi maʻi i kapa ʻia ʻo `(Microcornea)`. I loko o `(Microcornea)`, ua liʻiliʻi loa ka cornea.

Akā i kekahi manawa hiki ke pili kēia ʻano `(Megalocornea)` me nā maʻi ʻē aʻe. No ka laʻana, ʻike ʻia me nā maʻi pili e like me `(Marfan syndrome)`. Inā hana ʻia kēia, hiki i kāu keiki ke pilikia i ka loaʻa ʻana o nā maʻi maka ʻē aʻe e like me ka cataracts. ʻO ia ke kumu he mea nui loa ka ʻike ʻana i ke ʻano `(Megalocornea)` i ka wā mua. A laila hiki i nā kauka ke nānā pono i nā maka a me ka ʻike o ke keiki.

Hoʻohana nā kauka i kekahi mau inoa ʻē aʻe no ke kūlana:

• ʻO ka megalophthalmos mua
• ʻO ka megalophthalmia mua hānau
• ʻO ka megalocornea hānau kaʻawale
• Makakonea

Pehea ka hopena o ka Megalocornea i nā maka?

ʻO ka hapa pinepine, hoʻopilikia ke kūlana "Megalocornea" i nā maka ʻelua. ʻO ka hapa nui ma nā ʻano ʻelua:

1. ʻOi aku ka nui o ke anawaena o ka cornea (i ana ʻia mai kēlā ʻaoʻao a i kēia ʻaoʻao) ma mua o ka maʻamau (ʻoi aku ma mua o 13 millimeters).

2. ʻO ka ʻaoʻao mua o ka maka, kahi e kahe ai kahi wai maopopo a wai (ke keʻena mua) e lilo i hohonu ma mua o ka maʻamau.

ʻO kēia mau loli ke kumu e ʻike ʻia ai nā maka i ʻoi aku ka nui mai waho mai.

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia kūlana?

ʻIke pinepine ʻia ka Megalocornea i nā keikikāne . ʻO kēia no ka mea ʻoi aku ma mua o 90% o nā hihia o ka megalocornea i hoʻokumu ʻia e kahi mutation genetic ma ka chromosome X. Hoʻopilikia kēia mau kūlana i hoʻopili ʻia me X i nā keikikāne ma mua o nā kaikamahine.

He maʻi laha ʻole kēia. ʻAʻole hiki i nā kānaka noiʻi ke ʻōlelo pololei i ka nui o ka poʻe i hānau ʻia me ia, akā manaʻoʻiʻo lākou ʻaʻole paha i ʻike pono ʻia.

He aha nā ʻano nui o ka `(Megalocornea)`?

ʻElua ʻano nui o ka `(Megalocornea)`:

1. Megalocornea i hoʻokaʻawale ʻia a maʻalahi paha : Hoʻopilikia wale kēia i ka cornea a ʻaʻole pili pū me kekahi maʻi ʻē aʻe.

2. Anterior megalophthalmos : Pili kēia ʻano me kahi maʻi kumu, no laila hiki ke hoʻopilikia i nā ʻāpana ʻē aʻe o nā maka o ke keiki a i ʻole nā ​​​​ʻāpana ʻē aʻe o ke kino.

He aha ke kumu o ka Megalocornea?

Hoʻokumu ʻia ʻo Megalocornea e kahi mutation genetic i loko o ka gene CHRDL1, ka mea e kōkua ai i ka kaohi ʻana i ka ulu ʻana o ka maka. Manaʻo nā kānaka noiʻi ʻo kēia mutation ke kumu o ka ulu ʻana o ke kīʻaha optic , ʻo ia kekahi ʻāpana o ka maka, ma mua o ka maʻamau. ʻO kēia ke kumu nui o ka nui ʻana o ka cornea.

He aha nā hōʻailona o ke ʻano `(Megalocornea)`?

ʻO ka nūhou maikaʻi, ʻo ka hapa nui o ka poʻe i hānau ʻia me Megalocornea ʻaʻole lākou e ʻike i kekahi mau hōʻailona . Hiki iā lākou ke ola i kahi ola maʻamau.

Akā, hiki i kekahi mau keiki ke loaʻa nā hōʻailona e like me kēia:

• Hoʻololi mālie ka ʻike maka a i ʻole ka ʻike pōwehiwehi ma muli o ka astigmatism. (ʻO ka Astigmatism kahi kūlana i ʻole poepoe pono ka cornea, e hoʻoulu ai i ka mālamalama ʻaʻole e kau ma kahi hoʻokahi i loko o ka maka.)
• ʻIke i ke kukui ʻālohilohi (photophobia) - ʻO ke ʻano kēia e lilo nā maka i polū ke hōʻike ʻia i ka lā a i ʻole nā ​​kukui ʻālohilohi.
• ʻIke pōkole (myopia).

Eia nō naʻe, inā pili ka maʻi "Megalocornea" me nā maʻi ʻē aʻe, hiki i ke keiki ke ʻike i nā hōʻailona koʻikoʻi e like me:

• Nā katarata.
• ʻO Coloboma (kahi ʻāpana o ka maka e ulu pono ʻole ana).
• ʻO ka lens i wehe ʻia (ectopia lentis) a i ʻole phacondonesis.
• ʻO Glaucoma (hōʻino ʻia ka ʻike ma muli o ka hoʻonui ʻia o ke kaomi o ka maka).
• ʻOi aku ka nui o ke apo a puni ke aniani o ka maka (ciliary body band) ma mua o ka maʻamau.
• ʻIke haʻahaʻa.
• Ka hemo ʻana o ka retina.

Mea nui: Inā loaʻa i kāu keiki kekahi o kēia mau hōʻailona, ​​e ʻike koke i ke kauka maka. ʻOi aku ka maʻalahi o ka mālama ʻana i ka ʻike mua ʻana.

Pehea e ʻike ai i ka `(Megalocornea)`?

ʻO ka maʻamau, ʻike nā kauka i ka megalocornea i ka wā kamaliʻi . Hōʻoia nā kauka maka i kēia me ka hoʻokolokolo maka a, inā pono, ka hoʻāʻo ʻana i ka genetic.

He mea nui loa ka ʻike pololei ʻana i kēia, no ka mea hiki ke hoʻokaʻawale ʻia mai nā maʻi koʻikoʻi ʻē aʻe, e like me ka glaucoma, a he mea nui nō hoʻi no ke alakaʻi ʻana i ka mālama pono ʻana.

Hiki i kāu kauka ke hana i nā hoʻokolohua ʻē aʻe, e like me:

• Nā hoʻāʻo Glaucoma.
• Gonioscopy (ka nānā ʻana i ke kihi o ke keʻena mua o ka maka).
• ʻO ka tomography coherence optical (OCT) (ke kiʻi ʻana i nā kiʻi o nā papa o ka maka).
• Tonometry (ana o ke kaomi o nā maka).
• Hoʻokolokolo ʻana o ka ultrasound.
• Ke helu nei i ka helu vitreous e ana i ke kahe wai i loko o ka maka.

Aia kekahi lāʻau lapaʻau no ka `(Megalocornea)`?

ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau no Megalocornea. Akā, mai hopohopo! Hiki i ka lāʻau lapaʻau ke kōkua i ka pale ʻana i ka ʻike o kāu keiki, ka mālama ʻana i nā kūlana ʻē aʻe, a me ka pale ʻana i nā pilikia. ʻO ka ʻike mua ʻana ke ala maikaʻi loa e loaʻa ai i kāu keiki ka lāʻau kūpono e pono ai lākou.

Hiki i kāu kauka ke kuhikuhi iā ʻoe i kahi kauka maka o nā keiki. Inā loaʻa i kāu keiki nā maʻi ʻē aʻe, pono paha ʻoe e ʻike i nā loea ʻē aʻe.

He aha nā lāʻau lapaʻau no ka `(Megalocornea)`?

I ka hapanui o nā hihia, ʻaʻole pono ka megalocornea i kekahi lāʻau lapaʻau kūikawā , ʻoiai inā maʻamau ka ʻike o kāu keiki a maʻamau ke kaomi intraocular. Hiki i ke kauka o kāu keiki ke paipai i kahi ala "kali makaʻala". ʻO ke ʻano kēia o ka nānā mau ʻana i ke olakino o nā maka o kāu keiki a me ka nānā ʻana i nā loli.

Eia nō naʻe, inā loaʻa i kāu keiki nā hōʻailona a i ʻole nā ​​​​maʻi ʻē aʻe, pono paha lākou i ka lāʻau lapaʻau e mālama iā lākou. ʻO nā lāʻau lapaʻau ʻoki ʻole:

• Nā lāʻau lapaʻau, no ka laʻana, nā kulu maka.
• Nā mea kōkua ʻike maka (nā maka aniani a i ʻole nā ​​​​aniani hoʻopili i hoʻolālā kūikawā ʻia).

I kekahi mau hihia, pono paha ke ʻoki kino:

• ʻO ke ʻoki ʻana i ka cataract a i ʻole ke ʻoki ʻana e mālama ai i ka glaucoma.
• ʻO ke keratectomy Photorefractive (PRK) kahi ʻoki maka e mālama ai i ka nearsightedness a i ʻole ka astigmatism.

He aha kaʻu e manaʻo ai inā loaʻa i kaʻu keiki ʻo `(Megalocornea)`?

ʻO ka hapa nui o nā keiki me ka megalocornea e ulu a mālama i ka ʻike maikaʻi . Hiki i kekahi poʻe ke hoʻokele i kā lākou mau hōʻailona me nā mea kōkua ʻike a i ʻole nā ​​​​​​aniani hoʻoponopono.

Eia nō naʻe, ʻo ka wā e hiki mai ana o nā keiki me kēia maʻi e pili ana i ke ʻano a me ke koʻikoʻi o ke ʻano. Inā manaʻo ʻoe e ʻoi aku ka ʻino o kāu mau hōʻailona , ​​e kamaʻilio me kāu kauka e pili ana i nā koho maikaʻi loa e pale aku i nā maka a me ke olakino o kāu keiki.

Hiki iaʻu ke hōʻemi i ka pilikia o ka loaʻa ʻana o ka Megalocornea i kaʻu keiki?

ʻOiaʻiʻo, ʻaʻohe mea hiki iā ʻoe ke hana e pale aku ai iā Megalocornea. He maʻi hoʻoilina kēia. Eia nō naʻe, hiki iā ʻoe ke hana i nā hana e pale ai i nā maka o kāu keiki.

Hiki iā ʻoe ke pale i ka hōʻino ʻana o ka corneal ma ke kau ʻana i nā maka pale ke hana ʻoe a kāu keiki paha i kēia mau mea:

• I ka hoʻomaʻemaʻe ʻana me ka bleach a i ʻole nā ​​​​kemika ʻē aʻe.
• I ka wā o ka hana waho e like me ke ʻoki ʻana i ka lau nahele.
• I ka wā o ka hana hoʻoponopono e pili ana i ka hoʻohana ʻana i nā lako uila, ka hāmare, a i ʻole ke kau ʻana i ka pena.
• Ma nā haʻuki e like me ka baseball a i ʻole ka hockey.

Inā ʻaʻahu kāu keiki i nā aniani hoʻopili, e hahai pono i nā ʻōlelo kuhikuhi no ka hoʻomaʻemaʻe ʻana a me ka hoʻomaʻemaʻe ʻana iā lākou e pale aku i nā maʻi maka a i ʻole nā ​​​​maʻi corneal. Mai poina i kāu mau manawa kauka maka , a e hahai i nā alakaʻi lapaʻau e pale aku i nā pilikia a mālama i ka ʻike o kāu keiki.

I ka manawa hea ʻoe e ʻimi ai i ke kōkua lapaʻau no ke kūlana `(Megalocornea)`?

He mea nui ka ʻike mua ʻana i ka megalocornea no ka mālama pono ʻana. Inā ʻike kāu keiki i ka ʻeha o nā maka, ka ʻeha, a i ʻole nā ​​loli i ka ʻike, e kelepona koke aku i kāu kauka.

Hiki i kāu kauka ke hāʻawi i nā koho lapaʻau kūpono e hāʻawi i kāu keiki i ka hōʻoluʻolu a mālama i ka ʻike.

He mea nui ka mālama ʻana i ka maʻi maka maʻamau no ka mālama ʻana i nā maʻi kumu a pale i nā pilikia e like me ka cataracts a i ʻole glaucoma.

He maʻi laha ʻole ka Megalocornea e hoʻonui ai i ka cornea o ka maka. Akā ʻo ka nūhou maikaʻi, ʻaʻole ʻike ka hapa nui o ka poʻe i nā hōʻailona. Hiki i kekahi ke pale i ko lākou ʻike me nā aniani hoʻoponopono a pale i nā pilikia. Me nā hoʻokolohua maka maʻamau, hiki i kāu keiki ke ʻike maopopo i ke ao nei a hauʻoli i ke ola piha!

Nā mea e pono ai ʻoe e ʻike (Leka Lawe-Home)

ʻAe, i kēia manawa ua maopopo iā ʻoe ka mea a mākou i kamaʻilio ai (Megalocornea). Eia kekahi mau mea nui e hoʻomanaʻo ai:

• He ʻano hānau ka Megalocornea kahi i ʻoi aku ai ka nui o ka cornea o ka maka ma mua o ka maʻamau.
• Hoʻopilikia pinepine kēia i nā keikikāne.
• ʻAʻole pilikia nui ka ʻike o ka hapa nui o nā keiki ma muli o kēia, a ʻaʻole ia e lilo i mea ʻino i ka hala ʻana o ka manawa.
• Eia nō naʻe, i kekahi manawa hiki ke pili pū me nā kūlana olakino ʻē aʻe. No laila, he mea nui loa ka ʻike mua ʻana i ka maʻi a me ka hoʻokolokolo mau ʻana i nā maka e like me ke aʻo ʻana a ke kauka.
• Pono wale nō ka lāʻau lapaʻau inā he mau hōʻailona a i ʻole nā ​​​​pilikia ʻē aʻe.
• Mai hopohopo, ma lalo o ka mākaʻikaʻi lapaʻau kūpono, hiki i ke keiki ke ola i ke ola maʻamau me ka ʻike maikaʻi.

Inā he mau nīnau kāu e pili ana i kēia, mai kānalua e nīnau i kāu kauka ʻohana a i ʻole he kauka maka.

ʻO Megalocornea, Hoʻonui ʻia o ka Cornea, Nā maʻi maka o nā keiki, Nā maʻi maka hānau, ʻO ka membrane mua o ka maka, Nā hoʻāʻo maka, gene CHRDL1