Ke pehu koke nei kou mau lehelehe, nā papālina, a i ʻole nā wahi ʻē aʻe o kou helehelena? Manaʻo paha ʻoe i kekahi manawa he mau puʻupuʻu liʻiliʻi? ʻOiai he mea ʻē paha kēia, he maʻi olakino paha ia. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi i kapa ʻia ʻo 'Orofacial Granulomatosis' e hōʻike ana i nā hōʻailona like, he mea kakaikahi iki akā he mea nui e ʻike.
He aha ka 'Orofacial Granulomatosis'?
I ka ʻōlelo maʻalahi, ʻo ka 'Orofacial Granulomatosis' kahi maʻi ʻili e hoʻoulu ai i ka pehu a me nā puʻupuʻu ma ko mākou helehelena, i loko o ka waha, ʻoi aku hoʻi ma nā lehelehe a me nā papālina. He mea kākaʻikahi kēia. I kekahi manawa hiki ke ʻike ʻia kēia mau puʻupuʻu me ka maka ʻōlohelohe a hiki ke hoʻopā ʻia me ka lima.
I kēia manawa, inā ua kaupalena ʻia kēia kūlana 'Orofacial Granulomatosis' i nā lehelehe, aia kekahi mau inoa kūikawā no ia. ʻO lākou:
- ʻO ka maʻi ʻōpū (Cheilitis granulomatosa)
- ʻO ka cheilitis granulomatous
- ʻO ka cheilitis Miescher
ʻOiai paha he ʻano paʻakikī kēia mau inoa, ua like ke ʻano o lākou a pau - ʻo ia hoʻi, ke ʻano pehu a me ka puʻupuʻu o nā lehelehe i ʻōlelo ʻia ma luna.
ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o kēia maʻi?
ʻAe, e nānā kākou i ka mea i ʻoi aku ka nui o ka loaʻa ʻana o ka 'Orofacial Granulomatosis'. ʻAʻole kēia he maʻi maʻamau. Hoʻopilikia ia ma lalo o 1% o ka heluna kanaka. ʻOiai hiki ke hoʻopilikia i kekahi o kēlā me kēia makahiki, ʻoi aku ka maʻamau i nā poʻe ʻōpio ma waena o 20 a me 40 mau makahiki .
ʻO kekahi mea ʻē aʻe, hiki i kēia ʻano ke hana hoʻokahi i kekahi manawa (idiopathic), ʻo ia hoʻi hiki ke hana me ka ʻole o kekahi maʻi ʻē aʻe. Eia nō naʻe, hiki nō hoʻi ke hana pū me nā ʻano olakino ʻē aʻe. Eia kekahi laʻana:
- ʻO ka maʻi o Crohn : Ua lohe paha ʻoe i kēia, kahi maʻi mumū mau loa o nā ʻōpū.
- ʻO Sarcoidosis : He ʻano kēia e kū mai ai nā puʻupuʻu liʻiliʻi o nā cell (granulomas) ma nā ʻāpana like ʻole o ke kino, ʻoi aku hoʻi i nā māmā a me nā lymph nodes.
- Nā maʻi lele like ʻole : No ka laʻana, hiki ke pili kēia me nā maʻi e like me ka maʻi puʻupuʻu.
ʻO kekahi mea hoihoi ʻē aʻe, ʻo kēia ʻano i kapa ʻia ʻo 'Orofacial Granulomatosis' e pili pinepine ʻia me kahi ʻano neurological i kapa ʻia ʻo 'Melkersson-Rosenthal syndrome' . ʻEkolu mau hōʻailona nui o kēia maʻi:
- Ka pehu ʻana o ka maka a i ʻole nā lehelehe.
- Hiki i ke alelo ke ʻano nalu a i ʻole nā ʻauwaha hohonu (nā kualono a i ʻole nā ʻauwaha).
- Ka nalowale pinepine ʻana o ka hana o ka maka, ʻo ia hoʻi ka hiki ʻole ke kāohi i nā ʻano helehelena ('facial paralysis').
He aha ke kumu o ka 'Orofacial Granulomatosis'?
He aha ke kumu maoli o ka 'Orofacial Granulomatosis'?ʻAʻole maopopo loa i nā kānaka ʻepekema ke kumu o ia mea, akā ke hoʻomau nei lākou i ka noiʻi ʻana. Manaʻo lākou i kēia manawa aia kekahi mau kumu hiki ke loaʻa:
- Nā maʻi ʻaleka a i ʻole nā mea ʻoluʻolu i kekahi mau meaʻai : No ka laʻana, nā mea e like me ke kinamona, kokoleka, a me kekahi mau mea mālama.
- Nā maʻi bacteria a fungal paha .
- Nā loli i ka hana o ka ʻōnaehana pale kino (nā pane pale kino) o ka poʻe me kekahi mau ʻano maʻi genetic .
Manaʻo nā kānaka ʻepekema ua loaʻa kēia pehu ʻana ma muli o nā puʻupuʻu liʻiliʻi o nā keena i kapa ʻia ʻo 'granulomas' (ʻo ia hoʻi nā puʻupuʻu liʻiliʻi i hana ʻia e nā keena o ka ʻōnaehana pale) e ālai ana i kā mākou ʻōnaehana lymphatic . E noʻonoʻo penei: ʻo ka ʻōnaehana lymphatic kahi ʻōnaehana hoʻokahe wai e wehe ana i nā huahana ʻōpala mai ko mākou kino. No laila, ke pau ka hana pono ʻana o kēia ʻōnaehana ma muli o kēia mau 'granulomas', hōʻiliʻili ka wai lymph a hoʻoulu i ka pehu. Ua kapa ʻia kēia ʻo 'lymphedema' .
He aha nā hōʻailona o kēia maʻi?
ʻO ka hōʻailona mua a maʻamau o ka Orofacial Granulomatosis he pehu palupalu a ʻeha ʻole o kekahi a i ʻole nā lehelehe ʻelua. ʻOi aku ka pehu o ka lehelehe lalo ma mua o ka lehelehe luna. Hele mai kēia pehu a hele. I kekahi manawa hiki ke mau no nā pule a i ʻole nā mahina. I ka hala ʻana o ka manawa, hiki i kēia pehu ke lilo i ʻōpala, paʻakikī, ʻeha, a mau loa paha.
Ma waho aʻe o kēia hōʻailona nui, hiki ke ʻike ʻia kekahi mau hōʻailona ʻē aʻe:
- Nā lehelehe māwae .
- Ka kulu ʻana o ka wai , i kekahi manawa me ka hiki ʻole ke kaohi.
- ʻIli maloʻo, ʻulaʻula, a ʻili a puni kou waha .
- E like me ka mea i ʻōlelo ʻia ma mua, aia nā ʻauwai a i ʻole nā kihi ma kou alelo .
- Nā ʻeha waha a i ʻole nā puʻupuʻu liʻiliʻi a i ʻole nā hōʻailona ʻili i loko o ka waha .
- Ka paʻakikī i ka ʻōlelo ʻana a i ʻole ka ʻai ʻana .
- Hiki paha iā ʻoe ke ʻike i ka pehu ʻana a i ʻole nā puʻupuʻu i loko o kou waha, nā papālina, nā ʻāʻī, ke alelo, ka ʻauwae, nā maka, ka lae, a i ʻole kou poʻo . E noʻonoʻo i ke ʻano o ka ʻoluʻolu ʻole o kēia.
He maʻi laha anei ka `Orofacial Granulomatosis`?
ʻO kahi nīnau a ka poʻe he nui, inā he maʻi lele ia. Hiki i ka Orofacial Granulomatosis ke laha mai kekahi ʻāpana o ka maka a i kekahi. ʻO ia hoʻi, hiki ke hoʻomaka ma nā lehelehe a neʻe i nā papālina. Eia naʻe, ʻaʻole ia he maʻi lele . No laila, ʻaʻohe mea e hopohopo ai.
Pehea e ʻike ai i kēia maʻi?
ʻĀ, pehea lā e ʻike ʻia ai kēia maʻi ʻo 'Orofacial Granulomatosis'?
No ka ʻike ʻana i kēia, e nānā ke kauka ʻili i ka wahi i pehu ai.Lawe ʻia kahi ʻāpana ʻili liʻiliʻi a nānā ʻia (he `biopsy`). Ua like kēia me kahi hana liʻiliʻi. A laila nānā kekahi kauka pathologist i kēia ʻāpana ʻili ma lalo o kahi microscope e ʻike inā he `noncaseating granulomas` (ka inoa lapaʻau no kēia mau puʻupuʻu o nā cell). Inā loaʻa lākou, ua hōʻoia ʻia ka maʻi.
Ma waho aʻe o kēia hoʻāʻo nui, hiki i ke kauka ke hana i kekahi mau hoʻokolohua hou aʻe e nānā i nā kūlana olakino ʻē aʻe, e like me kā mākou i kūkākūkā ai ma mua e hiki ke pili kēia me nā maʻi ʻē aʻe.
- Nā hoʻāʻo koko e nānā i nā maʻi e like me ka maʻi puʻupuʻu.
- Nā kiʻi X-ray o ka umauma e nānā ai no ka sarcoidosis.
- ʻO Colonoscopy (kahi hoʻāʻo i hana ʻia me kahi kāmela i loko o ka kolona) a me nā hoʻāʻo koko e nānā ai i ka maʻi o Crohn.
- Hana ʻia nā hoʻāʻo ʻāpana e nānā i nā maʻi allergies a i ʻole nā mea ʻike. Pili kēia i ka hoʻopili ʻana i kekahi mau mea i ka ʻili e ʻike ai inā he maʻi ʻoe iā lākou.
Pehea e mālama ʻia ai ka `Orofacial Granulomatosis`?
I kēia manawa, e nānā kākou pehea e mālama ai i kēia `Orofacial Granulomatosis`. ʻAʻole hoʻomaka koke ka poʻe a pau i ka lāʻau lapaʻau. Hoʻoholo ke kauka e hoʻomaka i ka lāʻau lapaʻau ma nā hihia aʻe:
- Inā ʻoe e hopohopo nui a kaumaha paha no kou helehelena .
- Inā he ʻeha .
- Inā pilikia ʻoe i ka hoʻohana pono ʻana i kou maka a i kou waha paha, ʻo ia hoʻi, ka ʻōlelo ʻana, ka ʻai ʻana, a i ʻole ka inu ʻana .
ʻO ka lāʻau lapaʻau maʻamau no kēia ʻano maʻi, ʻo ia ka hoʻohana ʻana i kahi ʻano lāʻau i kapa ʻia ʻo 'Corticosteroids' . Ua lohe paha ʻoe i kēia inoa. He ʻano steroid kēia. ʻO ke ʻano o ka steroid i hāʻawi ʻia a me ke ʻano o ka hāʻawi ʻana e ʻokoʻa ma muli o ke koʻikoʻi o ke ʻano:
- Nā steroid topical : Hiki ke hele mai kēia mau mea ma ke ʻano he poni, kirīmi, a i ʻole nā mea holoi waha.
- Hāʻawi pololei ʻia nā inikini Cortisone i kahi o ka pehu ʻana .
- Nā steroid ʻōnaehana : ʻO ka hapa pinepine, ʻo ke ʻano steroid i hāʻawi ʻia ua kapa ʻia ʻo "Prednisone."
Ma waho aʻe o kēia mau lāʻau steroid, hiki i ke kauka ke ʻōlelo i kēia mau mea:
- Inā he mau maʻi, e hakakā iā lākou me nā 'Antibiotics' .
- Inā ʻike ʻia kahi maʻi allergie, e noi ʻia ʻoe e hana i nā hoʻololi i kāu meaʻai e like me ia .
- Nā Immunosuppressants : Hiki ke hāʻawi ʻia kēia mau mea ma ke ʻano he lāʻau lapaʻau waha a i ʻole he lāʻau lapaʻau topical.
- Inā ke hoʻopilikia nei ka pehu mau loa i nā hana koʻikoʻi e like me ke kamaʻilio ʻana, ka ʻai ʻana, a me ka inu ʻana, hiki ke hana ʻia ke ʻoki ʻana e hōʻemi i ka pehu .
Aia kekahi lāʻau lapaʻau mau loa no kēia?
ʻO kahi nīnau a ka poʻe he nui e nīnau ai, inā paha he lāʻau lapaʻau mau loa no kēia. ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau mau loa no ka Orofacial Granulomatosis i kēia manawa. ʻO ka mea nui o ka lāʻau lapaʻau, ʻo ia ke kāohi ʻana i nā hōʻailona a me ka hoʻēmi ʻana i ka ʻehaʻeha i loaʻa i ka mea maʻi, e hāʻawi ana i kahi hōʻoluʻolu.
Hiki ke pale ʻia ka Orofacial Granulomatosis?
ʻOiai ʻaʻole ʻike ʻia ke kumu kikoʻī o ka Orofacial Granulomatosis, ʻaʻohe ala i hōʻoia ʻia e pale aku ai .
He aha ka manaʻolana no ka poʻe me kēia maʻi?
He mea paʻakikī iki ka mālama ʻana i kēia maʻi, ʻo ia hoʻi ʻo 'Orofacial Granulomatosis'. Hiki ke hala i nā mahina, a i ʻole nā makahiki, no ka hōʻike ʻana o nā lāʻau lapaʻau o kēia manawa i nā hopena. ʻO ke ʻano kēia, lohi loa nā hopena. I kekahi manawa, ʻaʻole paha e kōkua iki nā lāʻau lapaʻau.
He mea kākaʻikahi loa, ʻo ia hoʻi, he mea kākaʻikahi loa, hiki i kēia kūlana ke hoʻōla koke iā ia iho ('remission spontaneous') me ka ʻole o kekahi lāʻau lapaʻau. Akā, he mea kākaʻikahi loa ia.
Pehea ʻoe e hoʻoponopono pono ai i kēia kūlana?
ʻO ka noho ʻana me kēia maʻi, ʻo ia hoʻi ʻo 'Orofacial Granulomatosis', hiki ke paʻakikī loa . Hiki iā ia ke hoʻopilikia i kou helehelena, ka hana a kou waha, a hiki nō hoʻi ke loaʻa nā hopena noʻonoʻo he nui. Akā aia kekahi mau ala e kōkua iā ʻoe e hoʻoponopono i kēia maʻi:
- Nā hālāwai kūkākūkā : Hiki i kēia ke kōkua nui i ke kamaʻilio ʻana e pili ana i kou mau manaʻo a me kou mau naʻau a me ke aʻo ʻana pehea e hoʻokele ai iā lākou.
- Nā hui kākoʻo : He manawa kūpono kēia e launa pū me nā poʻe ʻē aʻe e hele ana i nā kūlana like a kaʻana like i nā ʻike. E kōkua kēia iā ʻoe e manaʻo ʻaʻole ʻoe hoʻokahi.
- Nā hoʻomaʻamaʻa noʻonoʻo maikaʻi : Nā mea e like me ka noʻonoʻo ʻana a me ka nānā ʻana i kou mau ʻano maikaʻi loa, nā hoʻokō āu i hana ai.
- Ke komo ʻana i nā hana pilikanaka : He mea nui e hoʻolilo i ka manawa me nā hoaaloha a me ka ʻohana e kākoʻo a hoʻomaopopo i ʻole ʻoe e manaʻo mehameha.
Āhea ʻoe e ʻimi ai i ke aʻo lapaʻau?
Inā loaʻa koke iā ʻoe ka nāwaliwali a i ʻole ka lolo ma kekahi ʻāpana o kou maka, pono ʻoe e ʻimi koke i ke kōkua lapaʻau . Eia kekahi, inā ʻike ʻoe i nā kualono a i ʻole nā ʻauwaha ma kou alelo, e like me ka mea i ʻōlelo ʻia ma mua, pono ʻoe e hoʻomaopopo i kāu kauka e pili ana i ia mea . ʻO kēia mau hōʻailona paha he mau hōʻailona o ka maʻi Melkersson-Rosenthal a mākou i kūkākūkā ai a i ʻole kekahi maʻi koʻikoʻi ʻē aʻe.
He maʻi ʻili laha ʻole ka Orofacial Granulomatosis e hiki ai ke hoʻoulu i ka pehu ʻana o kou mau lehelehe, waha, a me nā ʻāpana ʻē aʻe o kou maka. No laila, inā he pehu kou ma kou maka, ʻoi aku ka maikaʻi o ke ʻike ʻana i ke kauka no ka ʻike kūpono a me ka mālama ʻana. ʻAʻohe lāʻau lapaʻau no ka Orofacial Granulomatosis, akā hiki i nā lāʻau lapaʻau e like me corticosteroids ke kōkua i ka hōʻemi ʻana i nā hōʻailona.
He aha nā mea nui a kākou e lawe ai mai kēia moʻolelo mai?
ʻAe, ua kamaʻilio nui mākou e pili ana i ka 'Orofacial Granulomatosis'. Eia kekahi mau mea maʻalahi e hoʻomanaʻo ai:
- He maʻi laha ʻole ka Orofacial Granulomatosis e hoʻoulu ai i ka pehu a me nā puʻupuʻu ma ka maka, ʻoiai hoʻi nā lehelehe a me nā papālina.
- ʻAʻole i loaʻa ke kumu kikoʻī o kēia , akā ua manaʻo ʻia he mau kumu kōkua nā maʻi allergies, nā maʻi, nā genetics, a me nā pilikia o ka ʻōnaehana pale.
- ʻO ka hōʻailona nui ka pehu ʻana o nā lehelehe. Eia nō naʻe, hiki ke loaʻa nā ʻeha waha, nā loli i ke alelo, a me ka paʻakikī i ka ʻai ʻana a me ka ʻōlelo ʻana.
- ʻAʻole kēia he mea laha .
- ʻO ke ʻano nui o ka hōʻoia ʻana he biopsy ʻili.
- Hoʻohana pinepine ʻia nā Corticosteroids ma ke ʻano he lāʻau lapaʻau. I kekahi manawa pono paha ke ʻoki ʻana.
- ʻOiai ʻaʻohe lāʻau lapaʻau mau loa i kēia manawa, hiki ke kaohi ʻia nā hōʻailona .
- Inā ʻike ʻoe i ka nalowale koke ʻana o ke ʻano o ka helehelena a i ʻole kahi loli ʻē i kou alelo, e ʻike koke i ke kauka .
Mai poina, inā loaʻa iā ʻoe kēia mau hōʻailona, mai hilahila a makaʻu paha iā lākou. E ʻimi koke i ke kōkua lapaʻau. ʻO ka mea nui loa, ʻo ia ka ʻike pololei ʻana i ka maʻi a me ka ʻimi ʻana i ka lāʻau kūpono. Eia kekahi, he mea nui loa ka noho ikaika ʻana i ka noʻonoʻo i ka wā e hana ai i kahi kūlana e like me kēia.
ʻO ka pehu ʻana o ka maka, ka pehu ʻana o ka lehelehe, ka granulomatosis orofacial, nā dermatoses, nā nodules, ka maʻi Melkersson-Rosenthal, nā corticosteroids











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