Ua manaʻo paha ʻoe he puʻupuʻu liʻiliʻi kou e ulu ana ma kou kino, ʻoi aku hoʻi ma kahi kokoke i kahi hono? Hiki ke ʻeha iki ke kaomi ʻoe iā ia. He mea maʻamau ke makaʻu iki ke ʻike ʻoe i kahi mea e like me kēia. Akā, ʻaʻole nā puʻupuʻu a pau he maʻi kanesa. I kēia lā, e kamaʻilio mākou e pili ana i kekahi puʻupuʻu, ʻaʻole ia he maʻi kanesa, akā pono kekahi hopohopo. He ʻano ia i kapa ʻia ʻo `(Tenosynovial Giant Cell Tumor)`.
He aha ke ʻano o kēia puʻupuʻu? `(Tenosynovial Giant Cell Tumor)` maʻalahi
I ka ʻōlelo maʻalahi, ʻo ka Tenosynovial Giant Cell Tumor he puʻupuʻu ʻaʻole kanesa e ulu ana i loko o nā ʻiʻo palupalu a puni kou mau hono. Ua kapa pinepine ʻia kēia mau mea he mau puʻupuʻu benign. ʻO ke ʻano kēia, ʻaʻole lākou he kanesa a ʻaʻole hoʻi e hoʻoulu i ka maʻi kanesa.
No kēia ʻano puʻupuʻu laha ʻole i kapa ʻia ʻo "Giant Cell Tumor." ʻAʻole laha pinepine kēia mau puʻupuʻu mai kekahi wahi a i kekahi wahi o ke kino. Eia nō naʻe, hiki iā lākou ke ulu a ulu koke ma kahi i hana ʻia ai lākou.
Ma muli o kahi o ka puʻupuʻu, hiki iā ia ke hoʻolilo i mea paʻakikī ke hoʻoneʻe i ke ami ma ia wahi a hōʻeha. I kekahi manawa hiki i kēia mau puʻupuʻu ke ulu a kaomi ma luna o nā iwi, a hiki ke haki ka iwi.
ʻO ka hapa pinepine, pono ke ʻoki kino e wehe i kēia "Tenosynovial Giant Cell Tumor." Pono paha kekahi poʻe i ka radiation therapy.
Pehea ka hopena o kēia i ke kino?
ʻEkolu ʻano o ka "Tenosynovial Giant Cell Tumor", ma muli o ke ʻano o ko lākou hana ʻana ma nā ʻiʻo like ʻole o ke kino:
1. Nā cysts e hana ʻia ana i loko o ka uhi o kou mau hono: Hana ʻia kēia mau mea i loko o ka membrane lahilahi e uhi ana i loko o kou mau hono (synovium). E like me nā hono o loko e like me kou mau kuli a me nā kuʻekuʻe lima.
2. Nā Cysts ʻUhi Tendon: ʻO nā tendons nā ʻano like me ke kāʻei e hoʻopili ai i ko mākou mau ʻiʻo i ko mākou mau iwi. Hiki i kēia mau cysts ke hana i loko o ka ʻupena pale a puni kēia mau tendons, i kapa ʻia ʻo Tendon Sheath.
3. Nā cysts Bursal: He mau ʻeke liʻiliʻi piha i ka wai nā Bursae e kokoke ana i nā hono, kahi e hui ai nā ʻiʻo, nā tendon, a me nā iwi. Hāʻawi lākou i ka palupalu a me ka pale no nā hono. Hiki nō hoʻi ke ulu aʻe ka Bursae.
ʻOiai hiki i kēia mau "Tenosynovial Giant Cell Tumors" ke ulu aʻe ma nā wahi āpau o ke kino, ʻike pinepine ʻia lākou ma:
- Manamana lima a i ʻole nā manamana nui
- Nā kuʻekuʻe wāwae a i ʻole nā wāwae
- Nā kuli
- Nā pulima lima
- Nā kuʻekuʻe lima
Ua ʻōlelo ʻia hoʻi ʻoiai inā e ho'ōla ʻia kahi puʻupuʻu e like me kēia, ʻoi aku ka nui o ka loaʻa ʻana o kekahi poʻe i ka rheumatoid arthritis a i ʻole ka osteoarthritis ma kēlā hui ma hope aku.
ʻO wai ka mea e loaʻa pinepine ai kēia mau mea? Pehea ka maʻamau?
Hiki i kekahi ke loaʻa i kēia "Tenosynovial Giant Cell Tumor". Eia nō naʻe, ʻoi aku ka maʻamau i kekahi mau hui:
- ʻOi aku ka maʻamau i waena o nā wahine ma mua o nā kāne.
- 30 a 50 mau makahikiHe mea maʻamau ia i waena o nā mākua.
Akā, mai hopohopo, he maʻi laha ʻole kēia `(Tenosynovial Giant Cell Tumors)`. Ma ka honua holoʻokoʻa, ʻaʻole i hiki i 50 mau kānaka no kēlā me kēia miliona e loaʻa i kēia mau maʻi i kēlā me kēia makahiki. No laila, ʻaʻole kēia he maʻi e hoʻopilikia i nā mea āpau.
He aha nā hōʻailona?
ʻO nā hōʻailona maʻamau o kēia tumor:
- He puʻu a ʻōpū paha e puka mai ana mai kahi hono.
- Hoʻonui ka ʻeha ke hoʻoneʻe ʻoe i kēlā ʻāpana.
- He pehu.
Eia kekahi, hiki i ka hono kokoke i ka puʻupuʻu ke loaʻa nā hōʻailona penei:
- He manaʻo o ka paʻa, ka laka ʻana, a i ʻole ke kani "kaomi ʻana" i ka wā e hoʻoneʻe ai i ke hono.
- Ke mehana nei ka ʻili a puni ke ami.
- ʻOʻoleʻa i ke ami.
- Ua nāwaliwali a make ke ʻano o ke ami.
He aha nā hōʻailona āu e loaʻa ai a pehea ka koʻikoʻi o lākou e pili ana i kekahi mau mea:
- He aha ke ʻano o ka ʻiʻo i hana ʻia ai ka puʻupuʻu.
- Aia ma hea ia i loko o ke kino?
- Pehea ka nui o ka puʻupuʻu.
He nui ka poʻe e ʻike wale he Tenosynovial Giant Cell Tumor ko lākou ma hope o nā makahiki o nā hōʻailona. No laila, ʻoi aku ka maikaʻi o ka haʻi ʻana i ke kauka inā ʻike ʻoe i kekahi mau loli hou a i ʻole nā puʻupuʻu i loko o kou kino.
No ke aha e like ai kēia ʻano o nā puʻupuʻu?
ʻAʻole i loaʻa i nā loea kahi kumu kikoʻī no ka ulu ʻana o kēia mau "Tenosynovial Giant Cell Tumors." Eia nō naʻe, ua ʻike kekahi mau noiʻi aia kekahi mau loli i nā chromosomes o ka poʻe e ulu ana i kēia mau tumors.
ʻO nā chromosome nā ʻāpana o ko kākou mau cell e loaʻa ana kā kākou ʻike genetic (DNA). Inā hōʻino ʻia kēia mau chromosome, hiki iā lākou ke hana i nā loli like ʻole i ke kino. Ma ke ʻano kūikawā, ua manaʻo ʻia i kēia manawa ua ulu kēia mau puʻupuʻu ma muli o ke kaʻina hana i kapa ʻia ʻo "Translocation", kahi e haki ai nā ʻāpana o nā chromosome a hui hou ma nā ʻano hou.
Pehea ʻoe e ʻike ai i kēia?
E ʻike ke kauka i kēia "Tenosynovial Giant Cell Tumor" ma ka nānā ʻana iā ʻoe, ka hana ʻana i kahi "Hoʻokolohua Kino", a me ka hana ʻana i kekahi mau "Hoʻāʻo Kiʻi".
Ma muli o kahi o ka puʻupuʻu, hiki paha iā ʻoe ke ʻike iā ia ma lalo o kou ʻili. E nānā pono ke kauka i ka puʻupuʻu a me ka ʻāina a puni. Eia kekahi, e hana lākou i hoʻokahi a ʻoi aku paha o nā hoʻokolohua e hiki mai ana e kiʻi i nā kiʻi o ka puʻupuʻu:
- Nā kukuna X
- ʻO ke kiʻi MRI (Magnetic Resonance Imaging)
- ʻO ke kiʻi ʻana o ka ultrasound
Hiki i ke kauka ke lawe i kahi hāpana liʻiliʻi o ka puʻupuʻu a i ʻole nā ʻiʻo a puni a hoʻouna iā ia i kahi keʻena hoʻokolohua no ka hoʻāʻo ʻana. Ua kapa ʻia kēia he "biopsy." Hiki i kēia ke kōkua i ka hoʻoholo pololei ʻana i ke ʻano o ka puʻupuʻu.
Pehea e mālama ʻia ai?
Hoʻopau pinepine ʻia nā ʻōpū cell nui Tenosynovial ma ke ʻoki kino. E wehe kāu kauka ʻoki i ka ʻōpū ma o ke ʻoki kino hāmama a i ʻole ma o ke kaʻina hana i kapa ʻia ʻo arthroscopy. I kekahi manawa hiki ke wehe ʻia ka ʻōpū me ka ʻiʻo i hoʻopilikia ʻia a puni.
ʻO Arthroscopy kahi hana e hoʻokomo ʻia ai kahi ʻōmole lōʻihi a lahilahi me kahi kāmela a me ke kukui (i kapa ʻia he arthroscope) ma o kekahi mau ʻoki liʻiliʻi ma ka ʻili kokoke i ke hono. ʻOiai e nānā ana i loko o ke hono, hoʻohana ʻia nā mea hana liʻiliʻi e wehe i ka puʻupuʻu a me nā ʻiʻo ʻē aʻe i hōʻino ʻia. ʻAʻole pili kēia hana i kahi ʻoki nui, no laila hiki ke wikiwiki ka ho'ōla ʻana.
E wehewehe aku kāu kauka lapaʻau iā ʻoe i ke ʻano o ke ʻoki kino āu e hana ai a me nā mea e manaʻo ai ma hope. E hilinaʻi ka manawa hoʻōla i:
- Ma muli ia o kahi o ke kino i loaʻa ai ka puʻupuʻu.
- Aia nō ia i kona nui.
- Ma muli o ka nui o nā ʻiʻo i pono e wehe ʻia i ka wā o ke ʻoki ʻana.
Hiki ke mālama ʻia kekahi mau ʻōhū Tenosynovial Giant Cell me kekahi mau ʻano chemotherapy, kahi lāʻau lapaʻau no ka maʻi kanesa. ʻOiai ʻo ka chemotherapy ka mea maʻamau e hoʻohana ʻia e pepehi i nā hunaola kanesa, hiki i kekahi mau ʻano chemotherapy ke kuhikuhi a pepehi i kēia mau ʻōhū benign.
ʻO kekahi o nā mea nui e pili ana i kēia mau `(Tenosynovial Giant Cell Tumors)` ʻo ia ka loaʻa ʻana o ka `(Recurrence Rate)` kiʻekiʻe. ʻO ke ʻano kēia, inā paha e wehe pono ʻia lākou me ke ʻoki kino a i ʻole e luku ʻia me `(Chemotherapy),` aia kahi manawa kūpono e ulu hou mai ai kēlā ʻano puʻupuʻu.
He mea kākaʻikahi loa, inā ua hōʻino nui ka puʻupuʻu i ke hono, pono paha e wehe i ka ʻāpana o ke hono, e like me ka lima a i ʻole ka wāwae, nona ke hono. Eia naʻe, he mea kākaʻikahi loa kēia e hana.
Hiki ke pale ʻia kēia mai ka hana ʻana?
ʻO ka mea pōʻino, ʻaʻohe ala e pale aku ai i ka ulu ʻana o kēia `(Tenosynovial Giant Cell Tumor)` i loko o kou kino. No ka mea, ʻaʻole ʻike ʻia ke kumu pololei o kēia mau hoʻokumu ʻana, ʻaʻole hiki ke wānana i ka wā, i loko o wai, a i ʻole ke kumu e ulu ai lākou.
He aha ka mea e hana ai inā loaʻa iā ʻoe kahi puʻupuʻu e like me kēia?
Ma hope o ka wehe ʻia ʻana o kahi Tenosynovial Giant Cell Tumor, hiki iā ʻoe ke manaʻo e hoʻōla piha. Ma hope o ka wehe ʻia ʻana o ka puʻupuʻu, pono ʻoe e hoʻomau i ka launa pū me kāu kauka a hele i nā manawa hoʻopaʻa maʻamau. E nānā kāu kauka i kou hoʻōla ʻana a nānā i nā puʻupuʻu hou. Inā ulu kahi puʻupuʻu hou, hiki ke ʻike ʻia a mālama ʻia i ka wā hikiwawe loa.
ʻOiai ʻaʻole kēia he maʻi kanesa a ʻaʻole hoʻi e hoʻoulu i ka maʻi kanesa, aia kahi manawa kūpono e loaʻa hou aku ai iā ʻoe nā Tenosynovial Giant Cell Tumors. ʻOi aku ma mua o ka hapalua o ka poʻe i loaʻa i kēia maʻi e loaʻa hou i kēia mau maʻi. Malia paha ma kahi like i ʻike mua ʻia ai lākou, a i ʻole ma nā ʻiʻo ʻē aʻe o ke kino. Hiki i ke kauka ke kapa i kēia he recurrence.
ʻAʻole hiki iaʻu ke hele i ka hana/kula a hiki i koʻu ho'ōla ʻana?
Ma hope o ka wehe ʻana i kahi Tenosynovial Giant Cell Tumor, ʻaʻole paha ʻoe e hiki ke hele i ka hana a i ke kula a hiki i kona ho'ōla ʻia ʻana. No ka laʻana, inā pono ʻoe e kū ma ka hana, inā aia ka puʻupuʻu ma kou kuʻekuʻe wāwae, a inā paha ʻoe e hoʻolilo i ka manawa nui e paʻi ana ma ke kamepiula, inā he ʻoki ʻana kou ma ka manamana lima, pono paha ʻoe e hoʻomaha iki mai ka hana a i ʻole nā papa e hāʻawi i kou kino i ka manawa e ho'ōla ai. ʻO ka lōʻihi o ka manawa e lawe ai iā ʻoe e pili ana i kahi i hana ʻia ai ke ʻoki ʻana a me ka nui o ka puʻupuʻu. E haʻi aku kāu kauka ʻoki i kēia iā ʻoe.
Mai poina e nīnau i kāu kauka a kauka ʻoki paha ma mua o kou hoʻi ʻana i nā hana maʻamau a i ʻole ka hoʻoikaika kino ma hope o ke ʻoki ʻana.
Āhea wau e ʻike ai i ke kauka?
Inā ʻike ʻoe i kahi puʻupuʻu hou a i ʻole ka ulu ʻana ma kekahi wahi o kou kino, ʻoi aku hoʻi ma kahi kokoke i kahi hono, a ʻoi aku hoʻi inā he ʻeha, e ʻike pono i ke kauka. ʻOiai inā ʻaʻole ia he "Tenosynovial Giant Cell Tumor", ʻo ka wikiwiki o kou ʻike ʻana i ke kauka e pili ana i kekahi puʻupuʻu, ʻo ka wikiwiki o ka ʻike ʻia a me ka mālama ʻia ʻana.
Inā ʻaʻole hiki koke iā ʻoe ke hoʻoneʻe i kahi hono, he pilikia ia. Inā hana ʻia kēlā, e hele koke i ka haukapila.
Nā nīnau koʻikoʻi e nīnau aku i kāu kauka
Ke ʻike ʻoe he loaʻa iā ʻoe kēia maʻi, aia kekahi mau nīnau koʻikoʻi e nīnau aku i kāu kauka:
- He aha ke ʻano o ka Tenosynovial Giant Cell Tumor i loaʻa iaʻu?
- He aha nā hoʻokolohua e pono ai iaʻu e hana?
- Pono maoli anei au i ke ʻoki kino?
- He aha nā kūlana o ka ulu hou ʻana o kēia puʻupuʻu?
He ʻokoʻa anei kēia mau puʻupuʻu mai nā `(Ganglion Cysts)`?
ʻO nā "Tenosynovial Giant Cell Tumors" a me nā "Ganglion Cysts" he mau ʻano puʻupuʻu e hana ʻia ana i loko o nā hono.
ʻO ka ʻokoʻa nui ma waena o nā mea ʻelua kahi i hoʻokumu ʻia ai. Hoʻokumu ʻia nā Tenosynovial Giant Cell Tumors i loko a i ʻole a puni ke hono. ʻO nā Ganglion Cysts he mau cysts piha i ka wai e hana ʻia ma lalo o kou ʻili.
ʻAʻole loa e lilo kēia mau ʻano puʻupuʻu ʻelua i mea ʻino, ʻo ia hoʻi, ʻaʻole lākou he maʻi kanesa.
Inā ʻike ʻoe i nā puʻupuʻu hou a i ʻole nā puʻupuʻu ma kou ʻili, ʻoiai inā he ʻeha a paʻakikī paha ka hoʻoneʻe ʻana i kahi hui, e ʻike i ke kauka.
ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai
ʻOiaʻiʻo, ke lohe ʻoe i ka huaʻōlelo "tumor" makaʻu ʻoe. Akā , ʻaʻole loa he maʻi kanesa nā "tenosynovial giant cell tumors", a ʻaʻole lākou e hoʻoulu i ka maʻi kanesa. I ka hapanui o nā hihia, pono ke ʻoki ʻana e wehe i kēia mau tumors. Inā ua ulu kekahi "tenosynovial giant cell tumor", aia kahi manawa e ulu hou aku ai i ka wā e hiki mai ana.
No laila, e kamaʻilio me kāu kauka e pili ana i nā mea e makaʻala ai. Inā ʻike ʻoe i kahi puʻupuʻu hou a i ʻole ka ulu ʻana, e ʻike koke i ke kauka. ʻO ka mea nui loa, ʻo ia ka palekana, e kiʻi i ka ʻike kūpono, a e loaʻa ka lāʻau kūpono.
Nā pilikia o nā pūnaewele nui tenosynovial , nā puʻupuʻu hono, nā puʻupuʻu iwi, nā puʻupuʻu ʻiʻo palupalu, ʻeha hono, ʻoki kino, nā puʻupuʻu ʻaʻole maʻi kanesa











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