I ka wā e pili ana i ka maʻi diabetes , ʻaʻohe mea ma ko kākou ʻāina i ʻike ʻole. Manaʻo ka poʻe he ʻelua wale nō ʻano o ka maʻi diabetes , ʻo ia hoʻi ke ʻano 1 a me ke ʻano 2. Akā, ua ʻike anei ʻoe aia kekahi ʻano maʻi diabetes kūikawā ʻē aʻe ma waho aʻe o kēia? ʻO ia ka mea a mākou e kapa nei ma ke ʻano lapaʻau ʻo MODY, a i ʻole 'Maturity-Onset Diabetes of the Young'. He mea kakaikahi kēia, a ua hoʻoilina pololei ʻia. He mea nui loa ka ʻike pololei ʻana i kēia, no ka mea, hiki ke ʻokoʻa ka lāʻau no kēia mai nā ʻano maʻi diabetes ʻē aʻe.
No ke aha e ulu ai ʻo MODY? He aha ke kumu?
I ka ʻōlelo maʻalahi, ua hoʻokumu ʻia ʻo MODY e kahi loli, a i ʻole mutation, i loko o hoʻokahi gene i loko o ko kākou kino. ʻO kēia ka ʻokoʻa nui ma waena o MODY a me ka maʻi diabetes Type 1 a me Type 2. ʻO nā ʻano maʻi diabetes ʻē aʻe i hoʻokumu ʻia e ka hui pū ʻana o nā kumu, e like me nā genes he nui, ka momona , a me ke ʻano nohona maikaʻi ʻole. Akā ua hoʻokumu ʻia ʻo MODY e hoʻokahi gene.
E noʻonoʻo, ma muli o kēia loli hoʻoilina, ʻaʻole lawa ka hana ʻana o kāu pancreas i kahi hormone i kapa ʻia ʻo insulin . E like me kou ʻike, he hormone koʻikoʻi ka insulin e kōkua i ke kino e omo i ke kō i loko o ka meaʻai a mākou e ʻai ai ma ke ʻano he ikehu, a hoʻomalu pū ia i nā pae kō koko. No laila, ke lawa ʻole ka insulin, piʻi aʻe nā pae kō koko.
ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o kēia maʻi?
He maʻi hoʻoilina ʻo MODY. ʻO ia hoʻi, inā loaʻa i kekahi o kou ʻohana ka MODY, ʻoi aku ka nui o kou loaʻa ʻana iā ia. No ka laʻana, inā loaʻa i kou makuahine a i ʻole kou makuakāne ka MODY, he 50% kou manawa e loaʻa ai. He pilina hoʻoilina ikaika loa kēia. I kekahi mau ʻohana, hiki ke ʻike ʻia ka maʻi i nā hanauna ʻekolu: nā kūpuna, nā makuahine, nā makuakāne, a me nā keiki.
ʻIke pinepine ʻia kēia maʻi i nā poʻe ʻōpio ma lalo o 35 mau makahiki. Eia nō naʻe, hiki ke loaʻa i kēlā me kēia makahiki.
ʻO ka mea nui, ʻaʻole like me ka maʻi diabetes Type 2, ʻaʻole pinepine ka poʻe i loaʻa iā MODY i ka momona, a ʻaʻohe o lākou koko kiʻekiʻe. Hiki iā lākou ke kaumaha olakino.
Pehea ʻoe e ʻike ai inā loaʻa iā ʻoe ʻo MODY? He aha nā hōʻailona?
Aia nā hōʻailona o MODY i ke ʻano o ka gene i loaʻa iā ʻoe ke kīnā. I kekahi manawa ʻaʻole paha ʻoe e loaʻa i kekahi mau hōʻailona. Akā ma ke ʻano laulā, ulu mālie ka maʻi. Ua loaʻa paha iā ʻoe nā pae kō koko kiʻekiʻe no nā makahiki, a hiki ke ʻike ʻia kēia mau hōʻailona ma hope:
- ʻO ka makewai pinepine a me ka pōloli
- Pono e mimi pinepine ma mua o ka maʻamau
- ʻIke pōwehiwehi
- Loaʻa pinepine ʻana o nā maʻi ʻili a i ʻole nā maʻi hū
- ʻO ka pohō kaumaha me ke kumu ʻole
- Luhi pinepine
He aha nā pilikia e hiki mai ana inā ʻaʻole mālama ʻia?
E like me nā ʻano maʻi diabetes ʻē aʻe, ua ʻike ʻia ʻo MODY e ke kiʻekiʻe o ke kō koko. Inā ʻaʻole mālama ʻia, hiki i ke kiʻekiʻe o ke kō koko i loko o kahi manawa lōʻihi ke alakaʻi i nā pilikia koʻikoʻi. He mea maʻamau nō hoʻi kēia i ka MODY.
- Ka pōʻino o ke aʻalolo
- Maʻi puʻuwai
- Ka hōʻino ʻana o ka maka (hiki ke alakaʻi i ka makapō )
- Nā pilikia wāwae
- Nā maʻi ʻili pinepine
Pehea e ʻike ʻia ai ʻo MODY?
No ka mea, he ʻoluʻolu loa nā hōʻailona o MODY, ʻaʻole paha ʻoe a i ʻole kāu kauka e manaʻo he MODY ia i ka wā mua. Ke hōʻike kahi hoʻāʻo koko maʻamau ua kiʻekiʻe kou pae kō koko, e haʻi aku kāu kauka iā ʻoe he maʻi diabetes kou. ʻO ka hana aʻe, ʻo ia ka ʻike pono i ke ʻano o ka maʻi diabetes āu.
E nānā pono kāu kauka i ka mōʻaukala ʻohana o ka maʻi diabetes a hiki paha ke kauoha i nā hoʻāʻo koko kūikawā e hoʻoponopono i ka maʻi diabetes type 1 a i ʻole type 2.
Ma muli o kēia mau hopena, hiki i kāu kauka ke kuhikuhi i ka hoʻāʻo genetic e hōʻoia inā loaʻa iā ʻoe ʻo MODY. Pili kēia i ka lawe ʻana i ka DNA mai kahi laʻana lawai a i ʻole ke koko a hoʻāʻo iā ia i loko o kahi lab e ʻike ai inā he mau loli i loko o nā genes e hoʻokumu ai iā MODY.
Pehea e mālama ʻia ai ʻo MODY?
ʻO ka lāʻau lapaʻau no MODY e pili ana i ka gene āu i loaʻa ai ke kīnā. ʻO ia ke kumu he mea nui ka loaʻa ʻana o kahi hōʻailona pololei. Hōʻike ka papa ma lalo nei i kekahi o nā ʻano nui o MODY a me kā lākou mau lāʻau lapaʻau.
| ʻAno MODY | Lapaʻau |
|---|---|
| MODY 1 a me MODY 4 | Hoʻohana pinepine ʻia nā Sulfonylureas ma ke ʻano he lāʻau lapaʻau maʻi diabetes. Hoʻoulu kēia mau lāʻau lapaʻau i ka pancreas e hana i ka insulin hou aʻe. Pono paha kekahi poʻe i nā inikini insulin. |
| MODY 2 | He maʻi palupalu loa kēia. Hiki ke hoʻomalu ʻia me ka ʻai a me ka hoʻoikaika kino . I ka hapanui o nā hihia, ʻaʻole pono ka lāʻau lapaʻau. |
| MODY 3 | I nā pae mua, hiki ke kaohi ʻia ma o ka ʻai. I ka hala ʻana o ka manawa, pono paha nā papa sulfonylureas a ma hope nā inikini insulin. |
| MODY 5 | Pono kēia i nā inikini insulin . He ʻano kakaikahi kēia. Hiki iā ia ke hoʻopilikia i nā ʻōpū ʻē aʻe, e like me nā puʻupaʻa. No laila, pono e mālama ʻia nā pilikia e like me nā cysts puʻupaʻa a i ʻole ka hāʻule ʻana o ka puʻupaʻa. |
| MODY 6 | ʻIke pinepine ʻia kēia ʻano ma kahi o 40 mau makahiki. Hāʻawi ʻia ka insulin ma ke ʻano he lāʻau lapaʻau. |
E like me kāu e ʻike ai, ʻokoʻa ke ʻano o ka lāʻau lapaʻau ma muli o ke ʻano o MODY. No laila, inā he maʻi diabetes kou a i ʻole kekahi lālā o ka ʻohana, ʻoiai inā ua ulu ia i ka wā ʻōpiopio a me ka ʻole o ka momona, he mea nui loa ia e kamaʻilio me kāu kauka e pili ana i ia mea.
Leka Lawe-Home
- He ʻano maʻi diabetes ʻokoʻa ʻo MODY mai ke ʻano 1 a me ke ʻano 2 a ua hoʻokumu ʻia e nā kumu genetic.
- Hoʻoili ʻia kēia mai kēlā hanauna a i kēia hanauna a loaʻa pinepine i nā poʻe ʻōpio a wīwī.
- Ma muli o ke ʻano o ka mālama ʻana, ʻokoʻa nā ʻano lapaʻau ma muli o ke ʻano o MODY, he mea nui loa ka loaʻa ʻana o kahi hōʻailona pololei.
- Inā holo ka maʻi diabetes i loko o kekahi mau hanauna o kou ʻohana, e kamaʻilio pono me kāu kauka e pili ana i ia mea.
- Ma waho o ke ʻano o ka maʻi diabetes, he mea nui e hahai pono i nā ʻōlelo aʻoaʻo a ke kauka e pale aku i nā pilikia.











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