Koj tus me nyuam puas nkees tas li? Nws puas zoo li ua pa nyuaj? Nws daim tawv nqaij puas qee zaum zoo li xiav? Txawm hais tias cov no feem ntau yog qhov ib txwm muaj, qee zaum lawv yuav yog vim muaj teeb meem plawv txij thaum yug los. Hnub no peb yuav tham txog ib qho mob plawv uas tsis tshua muaj tab sis tseem ceeb. Nws hu ua Ebstein's Anomaly.
Ebstein's Anomaly yog dab tsi tiag?
Hais yooj yim xwb, qhov no yog ib qho mob plawv uas muaj txij thaum yug los. Uas yog, ib qho teeb meem hauv lub plawv uas tshwm sim thaum tus menyuam tseem nyob hauv plab. Peb lub plawv muaj plaub chav, ob chav sab saud thiab ob chav sab hauv qab. Nruab nrab ntawm cov chav no muaj cov qhov dej uas ua haujlwm zoo li lub qhov rooj. Cov no tswj cov ntshav ntws mus rau ib qho kev taw qhia xwb.
Ebstein's Anomaly feem ntau cuam tshuam rau lub tricuspid valve, uas nyob nruab nrab ntawm lub plawv sab saud (lub plawv sab xis) thiab lub plawv sab qis (lub plawv sab xis) ntawm sab xis ntawm lub plawv. Ob yam tseem ceeb tshwm sim hauv qhov mob no:
1. Lub valve nyob rau hauv qhov chaw tsis raug: Lub tricuspid valve no nyob rau hauv qhov chaw qis dua li nws yuav tsum tau ua, mus rau hauv lub chamber sab xis qis.
2. Cov nplooj ntawv valve tsis tau tsim kom zoo: Cov nplooj ntawv valve tsis zoo li qub. Qee zaum lawv yuav lo rau ntawm phab ntsa plawv.
Xav txog seb yuav muaj li cas thaum lub qhov rooj tsis kaw zoo. Ib yam li ntawd, vim tias lub qhov rooj no tsis kaw zoo, cov ntshav uas yuav tsum tau nqus los ntawm chav hauv qab yuav ntws rov qab mus rau hauv chav sab saud.
Qhov no ua rau chav sab saud ntawm sab xis ntawm lub plawv loj dua. Tsis tas li ntawd, chav sab hauv qab, uas muaj lub qhov cua uas nyob qis dua, muaj chaw tsawg dua los ua haujlwm kom zoo. Raws li lub sijhawm dhau mus, sab xis ntawm lub plawv no tuaj yeem qaug zog thiab ua rau lub plawv tsis ua haujlwm.
Tus mob no tsis cuam tshuam rau txhua tus menyuam tib yam. Tej zaum yuav muaj cov tsos mob me me xwb, thaum lwm tus yuav muaj cov tsos mob hnyav heev.
Feem ntau, cov menyuam yaus uas muaj tus kab mob Ebstein's Anomaly muaj lwm yam mob plawv. Qhov feem ntau yog lub qhov hauv phab ntsa ntawm ob chav sab saud ntawm lub plawv. Qhov no hu ua '(Atrial Septal Defect - ASD )'.
Cov tsos mob ntawm tus mob no yog dab tsi?
Cov tsos mob ntawm tus kab mob no muaj ntau yam heev. Tej zaum, yog tias tus kab mob hnyav heev, cov tsos mob yuav tshwm sim hauv ob peb hnub tom qab yug los. Txawm li cas los xij, yog tias tus kab mob tsis hnyav heev, tej zaum yuav tsis muaj tsos mob li txog thaum nws tseem hluas.
| Lub cib fim | Cov tsos mob feem ntau |
|---|---|
| Cov menyuam yug tshiab (mob hnyav heev) |
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| Cov menyuam yaus laus dua thiab cov tub ntxhais hluas |
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Vim li cas qhov no thiaj tshwm sim? Yog vim li cas?
Qhov tseeb, feem ntau nws nyuaj rau nrhiav qhov ua rau qhov no. Tab sis cov kws kho mob ntseeg tias kev hloov pauv caj ces yuav ua lub luag haujlwm. Kuj tseem muaj kev ntseeg tias kev raug tshuaj xws li lithium lossis benzodiazepines thaum cev xeeb tub kuj tseem yuav ua rau muaj kev pheej hmoo me me. Tab sis cov no tseem nyob rau theem tshawb fawb.
Tus kws kho mob nrhiav tau qhov no li cas? (Kev kuaj mob)
Yog koj tus menyuam muaj cov tsos mob no, tus kws kho mob yuav xub kuaj tus menyuam kom zoo zoo. Tom qab ntawd, lawv yuav xaj ntau qhov kev kuaj kom paub tseeb tias lub plawv ua haujlwm li cas.
- Echocardiogram: Qhov no yog qhov kev kuaj mob tseem ceeb tshaj plaws. Zoo ib yam li kev ntsuas ultrasound ntawm tus menyuam hauv plab, nws thaij duab kom ntxaws ntawm lub plawv. Nws tuaj yeem qhia qhov chaw uas cov valve nyob, lawv cov duab, seb cov ntshav puas ntws rov qab, ntau npaum li cas, thiab cov chav plawv loj npaum li cas.
- Electrocardiogram (EKG): Qhov no ntsuas qhov ua haujlwm hluav taws xob ntawm lub plawv. Qhov no pab nrhiav pom lub plawv dhia tsis xwm yeem (arrhythmias).
- Kev Siv MRI Rau Lub Plawv: Qhov no tuaj yeem tsim cov duab peb sab ntawm lub plawv thiab cov qhov (valves) kom meej dua thiab meej dua. Qhov no tseem ceeb heev rau cov xwm txheej xws li ua ntej phais.
- Kev Ntsuas Kev Nyuaj Siab Thaum Ua Si: Rau cov menyuam loj dua, kev kuaj EKG yuav ua thaum lawv taug kev saum lub treadmill. Qhov no yuav pab kom pom tias lub plawv teb li cas thaum lawv siv zog.
- Holter Monitor: Qhov no yog ib lub cuab yeej me me uas hnav rau ntawm lub cev rau 24 txog 48 teev. Nws sau cov suab paj nruag thoob plaws hnub thiab siv los ntes cov suab paj nruag tsis tu ncua uas tshwm sim thaum nruab hnub.
Cov kev kho mob rau qhov no yog dab tsi?
Kev kho mob nyob ntawm seb tus kab mob hnyav npaum li cas thiab tus menyuam cov tsos mob.
Kev kho mob nrog tshuaj
Yog tias cov tsos mob tsis hnyav heev, tus kws kho mob yuav txiav txim siab saib xyuas tus menyuam tus mob. Yog tias muaj cov cim qhia tias lub plawv tsis ua haujlwm zoo, lawv yuav muab tshuaj los pab lub plawv ua haujlwm zoo dua lossis tshem tawm cov kua dej ntau dhau ntawm lub cev. Yog tias lub plawv dhia tsis xwm yeem, kuj muaj tshuaj los tswj nws.
Kev phais mob
Yog tias cov tsos mob hnyav heev lossis lub plawv maj mam qaug zog, tej zaum yuav tsim nyog phais.
- Kho Lub Qhov Ncauj: Qhov kev xaiv ua ntej ntawm cov kws phais yog sim kho thiab kho lub qhov ncauj ntawm tus menyuam. Siv cov nqaij ntawm tus menyuam, cov qhov ncauj ntawm lub qhov ncauj raug kho kom lawv ua haujlwm tau zoo.
- Hloov Lub Qhov (Valve): Yog tias lub qhov (valve) puas tsuaj heev kho tsis tau, yuav muab ib lub qhov (valve) cuav tso rau hauv nws qhov chaw. Cov no tuaj yeem ua los ntawm hlau (Lub qhov (valve)) lossis ua los ntawm cov nqaij tsiaj (Lub qhov (valve). Yog tias muab lub qhov (valve) hlau tso rau hauv, koj yuav tsum noj cov tshuaj ua kom cov ntshav nyias mus tas koj lub neej.
- Lwm cov txheej txheem: Thaum lub sijhawm phais, lub qhov hauv lub plawv (ASD) tuaj yeem kaw thiab qhov ntawm lub plawv uas ua rau lub plawv dhia tsis xwm yeem (catheter ablation) tuaj yeem kho tau.
Qee zaum mob hnyav heev, yog tias tsis muaj lwm txoj kev kho mob zoo, tej zaum yuav tsum tau hloov plawv. Txawm li cas los xij, qhov no tsis tshua muaj.
Cov yam tshwj xeeb twg yuav tsum tau ceev faj txog?
Ib tug me nyuam uas muaj tus mob no yuav tsum tau mus ntsib kws kho mob plawv tas mus li . Txawm tias tom qab phais lawm los, nws tseem ceeb heev uas yuav tsum mus ntsib kws kho mob kom kuaj xyuas raws sijhawm teem tseg.
Yog tias koj tus menyuam muaj tus mob no, saib xyuas cov tsos mob hauv qab no:
- Yog tias daim tawv nqaij tig xiav ntau zaus.
- Yog tias tus me nyuam txoj kev ua ub ua no, kev khiav, thiab kev ua si txo qis.
- Yog tias muaj kev o ntawm lub cev.
- Yog koj xav tias koj lub plawv dhia ceev dua.
Yog koj pom muaj kev hloov pauv zoo li no, qhia rau koj tus kws kho mob tam sim ntawd .
Tsis tas li ntawd xwb, qee zaum, xws li ua ntej cov hniav tawm, tus kws kho mob yuav qhia cov menyuam yaus kom noj tshuaj tua kab mob kom tiv thaiv kab mob plawv. Ib txwm ua raws li tus kws kho mob cov lus qhia kom meej.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Ebstein's Anomaly yog ib qho mob tsis tshua muaj uas cuam tshuam rau lub plawv tricuspid valve.
- Tus mob no tsis cuam tshuam rau txhua tus tib yam. Ib txhia yuav nyob tsis muaj tsos mob, thaum lwm tus yuav raug kev txom nyem hnyav heev.
- Ua pa nyuaj, nkees yooj yim, thiab tig xiav yog cov tsos mob tseem ceeb.
- Kev kho mob nyob ntawm seb tus kab mob hnyav npaum li cas. Cov tshuaj thiab phais kom kho lossis hloov lub valve yog cov kev kho mob tseem ceeb.
- Ib tug me nyuam uas muaj tus mob no yuav tsum tau kev saib xyuas los ntawm kws kho mob tshwj xeeb mus tas li. Kev mus kuaj mob thiab mus ntsib kws kho mob tsis tu ncua yuav pab tau tus me nyuam kom muaj lub neej noj qab nyob zoo.
- Yog koj muaj lus nug lossis kev tsis ntseeg txog koj tus menyuam, tsis txhob ntshai tham nrog koj tus kws kho mob txog qhov ntawd.











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus