Xav txog saib hauv daim iav thiab pom ib txoj kab ncaj nraim hauv nruab nrab ntawm koj lub ntsej muag, ib sab liab heev thiab hws, thiab sab tod ib txwm, tej zaum me ntsis dawb... Qhov ntawd puas tsis txaus ntshai thiab xav tsis thoob me ntsis? Los yog ua li cas yog tias koj pom ib sab ntawm koj tus menyuam mos lub cev hloov liab thiab sab tod ib txwm? Qhov no yog qhov peb hu ua Harlequin Sign hauv tshuaj. Vim tias lub npe txawv me ntsis, cia peb kawm ntxiv txog nws thiab seb qhov no puas yog ib yam dab tsi uas yuav tsum ntshai.
Lub cim Harlequin no yog dab tsi tiag?
Hais yooj yim xwb, lub cim Harlequin yog thaum ib sab ntawm koj lub cev lossis lub ntsej muag hloov xim tawv nqaij (liab lossis tsaus), thaum lwm sab tseem zoo li qub, qee zaum txawm dawb. Ob sab no zoo li raug sib cais los ntawm ib txoj kab ncaj nraim, txoj cai hauv nruab nrab ntawm lub cev.
Nrog rau qhov sib txawv ntawm cov xim tawv nqaij no, lwm yam ntxwv tuaj yeem pom ntawm ob sab.
- Liab: Thaj chaw no tej zaum yuav yog hyperhidrosis (tawm hws ntau dhau). Daim tawv nqaij ntawm thaj chaw ntawd kuj tseem yuav sov me ntsis thaum kov.
- Sab dawb/Sab ib txwm: Sab no tsis hws. Daim tawv nqaij kuj yuav txias thaum kov.
Txawm hais tias qhov cim Harlequin no qee zaum tuaj yeem yog ib qho tsos mob ntawm tus mob xws li 'Harlequin syndrome', feem ntau nws tsis muaj teeb meem dab tsi thiab tsuas yog ploj mus xwb.
Cov laj thawj tseem ceeb rau qhov no yog dab tsi?
Nws tsis yog ib txwm muaj peev xwm nrhiav tau qhov ua rau qhov no. Qhov laj thawj tseem ceeb rau qhov no yog teeb meem kev sib txuas lus hauv peb lub cev lub paj hlwb autonomic. Xav txog qhov no ua peb lub cev "auto-pilot" system. Lub cev no tswj cov yam uas peb tsis paub tias peb muaj, xws li peb txoj kev ua pa, lub plawv dhia, thiab kev tawm hws.
Yog li ntawd, yog tias muaj kev thaiv lossis qhov tsis zoo hauv txoj hlab ntsha uas xa cov lus los ntawm lub hlwb (hypothalamus) los ntawm cov hlab ntsha qaum mus rau lub ntsej muag thiab lub cev sab saud, cov lus yuav tsis raug xa mus rau ib sab ntawm lub cev kom raug. Qhov no yog vim li cas cov hlab ntsha ntawm ib sab nthuav dav thiab tig liab, thaum sab tod tsis tau txais cov lus thiab tseem zoo li qub.
Qhov no puas tshwm sim rau cov menyuam mos tshiab thiab?
Yog, qhov no yog ib yam dab tsi uas pom tau hauv cov menyuam mos tshiab. Raws li kev soj ntsuam, kwv yees li 10% ntawm cov menyuam mos noj qab haus huv yuav muaj lub cim Harlequin no. Yog li, tsis txhob txhawj yog tias koj tus menyuam muaj qhov no.
Qhov no feem ntau tshwm sim ntawm ob thiab tsib hnub tom qab tus menyuam yug los, tab sis qee zaum nws tuaj yeem tshwm sim lig txog peb lub lis piam.
Qhov tseem ceeb tshaj plaws yog lub cim Harlequin no uas cov menyuam mos muaj.Nws tsis muaj teeb meem dab tsi li. Qhov kev hloov xim no ploj mus li ntawm 30 vib nas this xwb. Qee zaum nws yuav kav ntev txog li 20 feeb. Nws yuav rov tshwm sim dua thaum muab tus me nyuam tso rau ntawm nws ib sab.
Tseem ceeb heev: Tus mob no hu ua Harlequin Sign tsis yog yuav tsum tsis meej pem nrog 'Harlequin ichthyosis', uas yog ib qho mob txaus ntshai heev, ua rau tuag taus thiab tsis tshua muaj neeg mob. 'Harlequin ichthyosis' yog ib qho mob uas tag nrho tus menyuam lub cev raug npog nrog cov nplai tuab, zoo li phaj, nrog rau cov kab nrib pleb tob hauv nruab nrab. Nws yog ib yam dab tsi txawv kiag li.
Lwm yam kab mob cuam tshuam
Lub Cim Harlequin qee zaum tuaj yeem tshwm sim ua ib qho tsos mob ntawm lwm yam mob.
Harlequin Syndrome
Qhov no yog ib qho mob uas cuam tshuam rau peb lub paj hlwb sympathetic. Lub paj hlwb no tswj peb qhov kev teb "sib ntaus lossis khiav", uas yog cov kev hloov pauv uas tshwm sim hauv lub cev thaum peb zoo siab, ntshai, lossis ua si nawv. Thaum twg lub cev no raug qhib rau ib tus neeg uas muaj Harlequin Syndrome (piv txwv li, thaum ua si nawv), ib sab ntawm lub ntsej muag thiab lub cev yuav liab thiab hws, thaum sab tod yuav tsis.
Horner Syndrome
Qhov no kuj yog ib qho mob tsis tshua muaj ntawm lub paj hlwb. Nws cuam tshuam rau lub qhov muag thiab cov nqaij nyob ib puag ncig ntawm ib sab ntawm lub ntsej muag. Nws kuj hu ua 'oculosympathetic palsy'. Nws yog tshwm sim los ntawm kev thaiv hauv txoj hlab ntsha ntawm lub hlwb mus rau lub qhov muag thiab lub ntsej muag. Ntawm no thiab, sab uas raug mob ntawm lub ntsej muag yuav liab.
| Xwm txheej | Leej twg raug kev cuam tshuam? | Cov yam ntxwv tseem ceeb | Tiag tiag? |
|---|---|---|---|
| Lub Cim Harlequin (rau cov menyuam mos) | Cov menyuam mos noj qab nyob zoo (kwv yees li 10%) | Liab ib ntus rau ib sab ntawm lub cev. | Tsis yog. Nws tsis muaj teeb meem dab tsi li thiab nws yuav ploj mus nws tus kheej. |
| Harlequin Syndrome | Rau txhua tus neeg txawm hnub nyoog li cas los xij | Liab thiab tawm hws ntawm ib sab thaum ua si lossis zoo siab. | Nyob ntawm seb qhov ua rau muaj teeb meem yog dab tsi. Feem ntau tsis ua teeb meem dab tsi. |
| Horner Syndrome | Rau txhua tus neeg txawm hnub nyoog li cas los xij | Qis muag ntawm ib sab ntawm lub ntsej muag, qhov muag dub me me, tawm hws tsawg dua, thiab ntsej muag liab. | Qhov ua rau mob (piv txwv li, mob qog) tej zaum yuav loj heev. Kev kuaj mob yog qhov tseem ceeb. |
Yuav kho li cas?
Kev kho mob nyob ntawm seb qhov ua rau muaj tus kab mob Harlequin yog dab tsi.
- Rau cov menyuam mos: Tsis tas yuav kho mob. Nws yuav ploj mus nws tus kheej hauv ob peb feeb xwb.
- Rau Harlequin Syndrome: Kev kho mob tsis tas yuav tsum tau kho txhua lub sijhawm. Qee zaum qhov mob no tuaj yeem zoo dua ntawm nws tus kheej. Txawm li cas los xij, yog tias koj tus kws kho mob xav tias kev kho mob yog qhov tsim nyog, lawv yuav sau ntawv kho mob raws li qhov ua rau. Cov no suav nrog:
- Ib hom tshuaj tiv thaiv kab mob hu ua 'Stellate ganglion block' siv los tswj kev hloov pauv ntawm daim tawv nqaij.
- Kev txhaj tshuaj botulinum toxin los tswj kev tawm hws.
- Yog tias muaj ib qho qog nqaij hlav hauv qab, nws tuaj yeem raug tshem tawm los ntawm kev phais lossis los ntawm kev kho mob hluav taws xob.
- Kev sab laj rau kev ntxhov siab ntawm lub hlwb uas tshwm sim los ntawm qhov tsos mob no.
- Rau Horner Syndrome: Yog tias tsis muaj mob, tej zaum yuav tsis tas yuav kho mob. Hauv qhov no, tus kws kho mob yuav kho qhov ua rau mob.
Thaum twg koj yuav tsum mus ntsib kws kho mob?
Yog tias koj lossis ib tug neeg hauv koj tsev neeg pom lub cim Harlequin, uas yog xim liab, hws, thiab kub rau ib sab ntawm lub cev, qhov zoo tshaj plaws ua yog mus ntsib kws kho mob thiab mus kuaj mob.
Koj tus kws kho mob yuav kuaj koj, nug txog koj cov tsos mob, thiab yog tias tsim nyog, yuav kuaj qee yam kom paub tseeb tias tsis muaj lwm yam mob. Txawm hais tias tsis tshua muaj, nws yog ib qho tseem ceeb uas yuav tsum paub tseeb tias tsis muaj qog nqaij hlav lossis lwm yam mob, vim qhov no yuav yog qhov ua rau muaj mob.
Yog tias cov tsos mob no tam sim ntawd nrog rau lwm cov tsos mob hnyav (piv txwv li mob taub hau hnyav, pom kev hloov pauv, tsis nco qab), nws yog ib qho tseem ceeb heev uas yuav tsum mus rau Chav Kho Mob Thaum Muaj Xwm Ceev (ETU) ntawm lub tsev kho mob ze tshaj plaws tam sim ntawd .
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Lub Cim Harlequin yog ib qho mob uas ib sab ntawm lub cev lossis lub ntsej muag liab thiab lwm sab dawb. Qhov no feem ntau tsis ua rau muaj kev phom sij.
- Qhov no feem ntau tshwm sim rau cov menyuam mos tshiab. Nws ploj mus nws tus kheej, hauv ob peb feeb xwb, yam tsis tau kho, thiab tsis muaj dab tsi yuav tsum txhawj txog. Nco ntsoov tias qhov no tsis yog tus kab mob 'Harlequin ichthyosis' txaus ntshai.
- Yog qhov no tshwm sim rau cov neeg laus, nws yuav yog ib qho tsos mob ntawm tus kab mob ntawm lub paj hlwb xws li 'Harlequin syndrome' lossis 'Horner syndrome'.
- Yog tias koj lossis koj tus menyuam muaj cov tsos mob no, nws yog ib qho zoo uas tsis txhob ntshai, tab sis mus ntsib koj tus kws kho mob kom paub meej tias muaj qhov ua rau muaj tseeb thiab xyuas kom meej tias tsis muaj lwm yam mob hnyav.
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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus