Tej zaum koj twb tau hnov txog "anemia" lossis "anemia" lawm, puas yog? Hais yooj yim xwb, nws yog thaum peb lub cev tsis tsim cov qe ntshav liab txaus lossis cov qe ntshav liab uas peb muaj tsis ua haujlwm zoo. Cov qe ntshav liab yog cov nqa oxygen tseem ceeb thoob plaws peb lub cev. Yog li thaum lawv tsawg, peb tuaj yeem xav tias nkees thiab qaug zog txhua lub sijhawm. Cov qe ntshav liab no tau tsim tawm hauv cov pob txha, ib daim ntaub mos mos, spongy hauv peb cov pob txha. Diamond-Blackfan Anemia (DBA) yog ib hom qe ntshav dawb tshwj xeeb uas tshwm sim thaum cov pob txha tsis tuaj yeem tsim cov qe ntshav liab txaus.
Dab tsi ua rau muaj mob Diamond-Blackfan Anemia (DBA)?
Kab mob Diamond-Blackfan Anemia, qee zaum hu ua "acquired pure red cell aplasia", feem ntau cov kws kho mob kuaj pom ua ntej tus menyuam muaj ib xyoos. Qhov ua rau qhov no yog kev hloov pauv, lossis kev hloov pauv, hauv cov noob caj noob ces uas yog cov khoom tsim ntawm peb lub cev.
Nco ntsoov tias, qee zaum qhov teeb meem caj ces no tuaj yeem tau txais los ntawm leej niam lossis leej txiv. Tab sis qhov ntawd tsis yog txhua lub sijhawm. Qee tus menyuam cov noob caj ces kuj tuaj yeem hloov pauv yam tsis muaj laj thawj. Feem ntau ntawm cov menyuam yaus uas muaj DBA muaj qhov mob no vim yog kev hloov pauv caj ces tshiab. Yog li ntawd, ua niam txiv, tsis tas yuav txhawj txog qhov no yam tsis tsim nyog. Txawm hais tias yuav luag ib nrab ntawm cov neeg mob DBA tau pom ib qho laj thawj tshwj xeeb rau qhov mob no, rau qee tus neeg, tseem tsis tau pom ib qho laj thawj tshwj xeeb rau qhov mob no.
Cov tsos mob ntawm DBA yog dab tsi?
Cov menyuam yaus uas muaj DBA kuj tseem yuav muaj ntau yam tsos mob ntawm lwm hom ntshav tsis txaus.
- qaug zog tas li
- Daim tawv nqaij daj ntseg
- Xav tias tsis muaj zog
Ntxiv rau cov yam ntxwv no, qee tus menyuam uas yug los nrog DBA yuav muaj cov yam ntxwv sab nraud ntawm lawv lub ntsej muag thiab lub cev. Cia peb saib seb lawv yog dab tsi.
| Lub cev ib feem | Cov yam ntxwv pom tseeb |
|---|---|
| Lub taub hau | Muaj lub taub hau me dua li qub. |
| Lub ntsej muag | Nrug deb ntawm ob lub qhov muag thiab lub qhov ntswg tiaj tus. |
| Pob ntseg | Ob lub pob ntseg me me uas teem qis dua li qub. |
| Lub puab tsaig | Muaj lub puab tsaig me me hauv qab. |
| Caj dab | Ib lub caj dab luv luv, muaj cov ntaub nplaum. |
| Xub pwg | Cov hniav xub pwg me me. |
| Tes | Cov ntiv tes xoo uas zoo li txawv txawv. |
| Qhov ncauj | Muaj ib daim di ncauj tawg los yog ib lub qhov ncauj tawg. |
Ntxiv rau, DBA tuaj yeem ua rau muaj teeb meem raum , mob plawv tsis zoo , thiab teeb meem qhov muag xws li cataracts thiab glaucoma . Cov tub hluas kuj tuaj yeem muaj qhov tsis zoo yug los hu ua hypospadias, uas yog thaum qhov qhib rau cov zis tsis nyob ntawm qhov kawg ntawm tus qau.
Yuav ua li cas thiaj paub qhov mob no kom meej?
Koj tus kws kho mob tuaj yeem ua ntau yam kev kuaj mob kom paub tseeb tias koj tus menyuam puas muaj DBA. Cov menyuam yaus uas muaj DBA muaj cov qe ntshav liab tsawg, tab sis cov qe ntshav dawb thiab cov qe ntshav dawb zoo li qub.
Qhov tseem ceeb tshaj plaws yog tsis txhob ntshai thaum koj pom cov tsos mob no, tab sis mus ntsib kws kho mob sai li sai tau. Nws yuav ua qhov kev kuaj mob tsim nyog thiab muab cov ntaub ntawv tseeb tshaj plaws rau koj.
Nov yog qee qhov kev kuaj mob tseem ceeb uas tus kws kho mob ua.
| Kev Ntsuas | Nws nrhiav dab tsi? |
|---|---|
| Kev suav ntshav tag nrho (CBC) | Muaj ntau yam ntsuas hauv cov ntshav, xws li tus naj npawb ntawm cov qe ntshav liab, cov qe ntshav dawb, cov platelets, cov protein hemoglobin uas nqa oxygen, thiab qhov ntim ntawm cov qe ntshav liab (hematocrit) . |
| Kev suav ntawm cov reticulocyte | Qhov no ntsuas tus naj npawb ntawm cov qe ntshav liab uas tseem tsis tau loj hlob lossis tshiab tsim. Qhov no tuaj yeem qhia tau seb cov pob txha puas tsim cov qe ntshav liab zoo. |
| Kev kuaj xyuas qib eADA | Kwv yees li 80% ntawm cov neeg uas muaj DBA muaj cov enzyme hu ua erythrocyte adenosine deaminase (eADA) ntau ntxiv. Qhov no yog qhov kev kuaj no nrhiav. |
| Cov theem hemoglobin ntawm tus menyuam hauv plab | Nov yog hom hemoglobin uas cov menyuam mos muaj nyob hauv plab. Nws yuav tsum txo qis tom qab yug los. Txawm li cas los xij, cov menyuam uas muaj DBA tseem yuav muaj cov ntshav ntau thaum lawv loj hlob tuaj. |
| Kev rho cov pob txha tawm thiab kev kuaj mob | Siv koob txhaj tshuaj rho me me ntawm cov hlwb pob txha thiab kuaj. Cov menyuam yaus uas muaj DBA muaj cov hlwb liab noj qab haus huv tsawg heev hauv lawv cov hlwb pob txha. |
| Kev kuaj noob caj noob ces | Qhov kev kuaj no rau cov noob caj noob ces uas muaj feem cuam tshuam nrog DBA lossis lwm yam kab mob ntshav tsis txaus uas tau txais los ntawm niam txiv. |
Muaj lwm yam teeb meem dab tsi tshwm sim vim yog DBA?
Cov neeg uas muaj DBA muaj feem yuav mob qee yam kab mob thiab tej yam mob me ntsis. Cov no suav nrog mob qog ntshav thiab pob txha (mob qog ntshav myeloid leukemia), mob qog ntshav pob txha (osteosarcoma), thiab lwm yam kab mob uas pob txha tsis tuaj yeem tsim cov qe ntshav zoo (myelodysplastic syndrome). Tab sis tsis txhob txhawj txog qhov no. Cov kws kho mob yeej ib txwm saib xyuas qhov no, yog li koj tuaj yeem ua cov kev kho mob tsim nyog thaum lub sijhawm zoo.
Cov kev kho mob rau qhov no yog dab tsi?
Qhov no yog qhov tseem ceeb tshaj plaws thiab nplij siab tshaj plaws. Cov menyuam yaus uas kuaj pom tias muaj DBA tuaj yeem ua neej ntev thiab muaj kev vam meej nrog kev kho mob. Ib txhia menyuam yaus mus rau hauv kev zam txim tag nrho, txhais tau tias cov tsos mob ploj mus rau ib lub sijhawm.
Ob txoj kev kho mob tseem ceeb uas siv yog cov tshuaj corticosteroid thiab kev hloov ntshav.
- Cov tshuaj Corticosteroid: Cov tshuaj xws li '(Prednisone)' ua rau cov pob txha ua haujlwm thiab pab nws tsim cov qe ntshav liab ntau dua.
- Kev ntxiv ntshav: Qhov no yog ib qho kev xaiv zoo yog tias cov tshuaj steroid tsis zoo, lossis yog tias qhov ntshav tsis txaus heev. Qhov no suav nrog kev muab cov ntshav lossis cov qe ntshav liab los ntawm tus neeg pub dawb uas noj qab nyob zoo rau tus menyuam.
- Kev hloov hlwb pob txha/cov hlwb qia: Qhov no yog tib txoj kev kho mob rau DBA. Txawm li cas los xij, nws muaj kev pheej hmoo me ntsis. Tsis tas li ntawd, kev nrhiav tus neeg pub dawb uas phim qee zaum yuav nyuaj.
Nws yog ib qho tseem ceeb uas yuav tsum tham txog txhua txoj kev kho mob no, lawv qhov zoo thiab qhov tsis zoo, kom meej meej nrog koj tus kws kho mob, thiab xaiv qhov zoo tshaj plaws rau koj tus menyuam.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Kab mob Diamond-Blackfan Anemia (DBA) yog ib yam mob caj ces tsis tshua muaj rau cov menyuam yaus uas cov pob txha tsis muaj peev xwm tsim cov qe ntshav liab txaus.
- Nrog rau cov tsos mob xws li qaug zog thiab ntsej muag dawb paug ntau zaus, tus kab mob no kuj tseem tuaj yeem ua rau muaj qee yam tshwj xeeb sab nraud ntawm lub ntsej muag thiab lub cev.
- Tus kws kho mob tuaj yeem kuaj mob no tau zoo los ntawm kev kuaj ntshav thiab kuaj pob txha.
- Kev kho mob xws li cov tshuaj steroid thiab kev hloov ntshav tuaj yeem pab cov menyuam yaus kom muaj sia nyob ntev thiab noj qab nyob zoo. Kev hloov pob txha yog tib txoj kev kho mob uas kho tau.
- Yog tias koj muaj kev xav tias koj tus menyuam muaj cov tsos mob no, tsis txhob ntshai thiab mus ntsib kws kho mob menyuam yaus tam sim ntawd. Kev kuaj mob sai thiab kev kho mob yog qhov tseem ceeb heev.
💬 Comments (0)
Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus