Koj puas tau pom ib qho chaw liab-xim av ntawm koj tus menyuam lossis koj lub cev? Tej zaum koj tsuas yog maj mam kov qhov chaw ntawd nrog koj tus ntiv tes, thiab tam sim ntawd qhov chaw ntawd hloov mus ua liab, pib khaus, thiab muaj ib lub pob me me tshwm rau saum. Yog tias qhov kev paub no koj paub, nws yog ib qho tseem ceeb heev uas yuav tsum paub txog qhov mob uas peb tab tom tham txog hnub no.
Hais yooj yim xwb, Urticaria Pigmentosa yog dab tsi?
Urticaria Pigmentosa yog ib hom pob khaus uas tshwm sim rau ntawm daim tawv nqaij. Feem ntau pom muaj rau cov menyuam yaus thiab cov hluas. Qhov tseeb, nws yog ib hom mob hu ua 'mastocytosis'.
Tam sim no tej zaum koj yuav xav paub tias 'mastocytosis' yog dab tsi. Nws yooj yim heev. 'Mast cells' yog ib hom cell tshwj xeeb hauv peb lub cev tiv thaiv kab mob. Lawv zoo li lub cev tiv thaiv kev ruaj ntseg. Thaum qee qhov laj thawj cov mast cell no sib sau ua ke ntau dhau hauv ib cheeb tsam ntawm daim tawv nqaij, peb hu nws tias Urticaria Pigmentosa. Txawm li cas los xij, cov mast cell no tuaj yeem sib sau ua ke tsis yog hauv daim tawv nqaij xwb, tab sis qee zaum hauv lwm yam kabmob xws li pob txha thiab txoj hnyuv. Tom qab ntawd nws hloov mus ua ib qho mob hu ua 'systemic mastocytosis'. Tab sis tsis txhob txhawj, feem ntau, Urticaria Pigmentosa hauv menyuam yaus tsuas yog txwv rau daim tawv nqaij xwb.
Hauv tus kab mob no, thaum muaj ib qho xim av tshwm sim rau ntawm daim tawv nqaij, nws yuav liab, o, khaus, thiab nce siab zoo li nws raug lub tsheb tsoo. Hauv kev kho mob, cov tsos mob no hu ua "Darier's sign."
Vim li cas ho muaj tej yam zoo li no tshwm sim?
Qhov laj thawj tseem ceeb rau qhov no yog cov "mast cells" uas peb tau tham txog ua ntej. Cov no yog ib hom qe ntshav dawb uas tsim tawm hauv peb cov pob txha. Cov qe no pom muaj thoob plaws hauv peb lub cev, tshwj xeeb tshaj yog qhov chaw uas peb kov lub ntiaj teb sab nraud, xws li daim tawv nqaij, lub ntsws, thiab txoj hnyuv. Thaum ib yam dab tsi zoo li kab mob nkag mus rau hauv lub cev, cov qe mast no tso tawm cov tshuaj hu ua "histamine" los pab tiv thaiv lub cev.
Urticaria Pigmentosa yog tshwm sim los ntawm kev hloov pauv caj ces uas ua rau cov hlwb mast no sib sau ua ke ntau dhau hauv daim tawv nqaij. Kev hloov pauv caj ces no feem ntau tshwm sim thaum tus menyuam tseem nyob hauv plab. Txawm li cas los xij, nws tsis yog ib yam dab tsi uas tau txais los ntawm niam txiv mus rau cov menyuam . Qhov ua rau muaj kev hloov pauv no tseem tsis tau pom.
Yog tias cov neeg laus muaj tus mob no, nws yuav hnyav dua me ntsis. Nws hu ua 'indolent systemic mastocytosis'. Hauv qhov no, cov mast cells sib sau ua ke rau hauv cov chaw xws li cov pob txha pob txha ntxiv rau ntawm daim tawv nqaij. Tsis tshua muaj, tus mob no tuaj yeem hloov mus ua mob qog noj ntshav hu ua 'mast cell leukemia'. Tab sis dua, cov no yog cov khoom tsis tshua muaj . 99% ntawm Urticaria Pigmentosa uas tshwm sim rau cov menyuam yaus tsis hnyav heev.
Cov tsos mob ntawm tus kab mob no yog dab tsi?
Cov tsos mob tseem ceeb thiab pom tseeb tshaj plaws yog 'Darier's sign' uas peb tau tham txog. Ntawd yog, cov xim av yuav liab thiab khaus thaum txhuam. Tsis tas li ntawd, qee tus neeg kuj tseem yuav muaj cov tsos mob hauv qab no.
| Cov tsos mob | Ib qho lus piav qhia yooj yim |
|---|---|
| Lub plawv dhia ceev | Lub plawv dhia nce ntxiv zoo li koj ntshai. |
| Mob plab (mob plab) | Nws tuaj yeem tshwm sim los ntawm kev ua haujlwm ntawm mast cell hauv lub cev zom zaub mov. |
| Flushing | Liab ntawm lub ntsej muag thiab lub cev sab saud tam sim ntawd. |
| Ua pa nyuaj (Ua pa nrov nrov) | Lub suab 'cheese-cheese' thaum ua pa, zoo ib yam li cov neeg mob hawb pob. |
| Tsaus muag | Tsis nco qab vim yog ntshav siab poob qis tam sim ntawd. |
| Mob taub hau | Mob taub hau. |
Ntau tshaj 75% ntawm cov neeg mob Urticaria Pigmentosa yog cov menyuam yaus hnub nyoog qis dua 10 xyoo. Feem ntau cov menyuam yaus, qhov mob no tsuas yog tshwm sim rau ntawm daim tawv nqaij xwb thiab zoo dua thaum muaj hnub nyoog.
Tus kws kho mob kuaj mob li cas?
Feem ntau, koj tus kws kho mob tuaj yeem kuaj mob no tau yooj yim los ntawm kev saib cov pob ntawm koj daim tawv nqaij thiab kuaj xyuas seb puas muaj tsos mob Darier. Tsis tas yuav kuaj lwm yam.
Txawm li cas los xij, yog tias muaj kev tsis ntseeg tias qhov mob no tsis yog tsuas yog rau ntawm daim tawv nqaij xwb tab sis kuj tau cuam tshuam rau lwm qhov ntawm lub cev, tus kws kho mob yuav pom zoo kom ua cov kev kuaj mob hauv qab no.
- Kev kuaj ntshav (' suav cov ntshav '): Kawm txog ntau hom thiab ntau npaum li cas ntawm cov qe ntshav hauv cov ntshav.
- Kev kuaj tryptase hauv cov ntshav: Xyuas seb puas muaj ib qho enzyme hauv cov ntshav uas cov mast cell tso tawm.
- Kev ntsuas qhov ntom ntawm pob txha: Saib seb koj cov pob txha muaj zog npaum li cas.
- Kev kuaj pob txha: Xyuas seb pob txha puas tsim cov qe ntshav dawb zoo.
Cov kev kho mob thiab yuav ua li cas tswj tus kab mob
Qhov xov xwm zoo yog tias rau feem ntau cov menyuam yaus, Urticaria Pigmentosa yuav ploj mus thaum lawv loj hlob tuaj . Tsis muaj kev kho mob tshwj xeeb los tiv thaiv cov pob tshiab kom tsis txhob tshwm sim. Cov pob uas twb muaj lawm yuav siv sijhawm ntau xyoo kom ploj mus.
Yog tias qhov mob tsuas yog nyob rau ntawm daim tawv nqaij xwb, feem ntau tsis tas yuav kho mob loj. Koj tus kws kho mob yuav pom zoo kom ua raws li cov hauv qab no los pab tswj koj cov tsos mob:
- Cov tshuaj antihistamines hauv qhov ncauj: Tswj kev khaus thiab o.
- Cov tshuaj pleev Corticosteroid: Siv rau thaj chaw khaus.
- Cromolyn sodium: Ib yam tshuaj uas siv los kho cov tsos mob xws li ntuav thiab raws plab.
- EpiPen: Ib lub cuab yeej uas muab rau cov neeg uas muaj kev tsis haum tshuaj hnyav (anaphylactic reaction) siv thaum muaj xwm txheej ceev. Tsis yog txhua tus neeg xav tau qhov no.
Tej yam uas yuav tsum zam tshwj xeeb
Qhov tseem ceeb tshaj plaws hauv tus kab mob no yog kom nyob deb ntawm cov yam uas ua rau cov tsos mob hnyav dua, uas yog, cov khoom ua rau cov pob khaus thiab liab.
| Cov tshuaj uas yuav tsum tsis txhob noj | Lwm yam uas yuav tsum zam |
|---|---|
| Tshuaj aspirin | Kev tawm dag zog (tshwj xeeb tshaj yog ua kom lub cev muaj zog) |
| Cawv | Siv phuam so kom huv si los so daim tawv nqaij |
| Cov tshuaj tua mob xws li morphine thiab codeine ('Opiates') | Da dej hauv dej kub |
| Thiamine (Vitamin B1) | Dej haus kub |
| Quinine ('Quinine' - tshuaj kho mob malaria) | Kev raug tshav ntuj ntau dhau |
| Dextromethorphan (tshuaj kho hnoos) | Kev raug cua txias heev |
| Qee cov tshuaj loog thiab cov xim X-ray | Cov khoom noj ntsim, kub |
Tseem Ceeb: Yog tias koj lossis koj tus menyuam yuav tsum tau noj tshuaj rau lwm yam mob, nco ntsoov qhia rau koj tus kws kho mob txog Urticaria Pigmentosa.
Puas muaj teeb meem tshwm sim tau?
Tsis tshua muaj mob li no, tus mob no yuav loj hlob mus ua "systemic mastocytosis". Cov neeg zoo li no muaj feem yuav ua xua hnyav heev hu ua "anaphylactic shock", uas yuav ua rau tuag taus. Yog tias koj muaj cov tsos mob xws li ua pa nyuaj thiab tsis nco qab , koj yuav tsum mus rau chav kho mob ceev (ETU) ntawm tsev kho mob tam sim ntawd .
Lwm yam teeb meem ntawm kev mob mastocytosis muaj xws li:
- Osteoporosis: Kev ua rau cov pob txha tsis muaj zog.
- Cytopenia: Kev tsim cov qe ntshav tsawg dua hauv lub cev.
- Teeb meem siab.
- Mob qog noj ntshav (tsawg heev).
Dua li no, cov no yog cov teeb meem tsis tshua muaj. Lawv tsis tshua muaj rau cov menyuam yaus uas muaj Urticaria Pigmentosa.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Urticaria Pigmentosa yog ib yam mob ntawm daim tawv nqaij uas feem ntau cuam tshuam rau cov menyuam yaus. Nws tsis kis tau lossis tsis tau txais los ntawm niam txiv.
- Cov tsos mob tseem ceeb yog thaum ib qho xim av raug txhuam, nws yuav liab, o, thiab khaus ('Darier's sign').
- Tsis txhob ntshai tsis tsim nyog, vim tias qhov mob no yuav zoo dua rau feem ntau cov menyuam thaum lawv loj hlob tuaj.
- Txoj kev tswj hwm zoo tshaj plaws yog nyob deb ntawm cov khoom noj, tshuaj, thiab cov dej num uas ua rau cov tsos mob hnyav dua.
- Yog tias koj lossis koj tus menyuam muaj cov tsos mob no, nco ntsoov mus ntsib kws kho mob kom paub tseeb tias koj muaj mob dab tsi thiab tau txais cov lus qhia tsim nyog.
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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus