Yu dɔn ɛva si, ɔ ɛkspiriɛns, wan say na yu fes we de tɔn rɛd ɛn swet wantɛm wantɛm, ɛn di ɔda say nɔmal ɔltogɛda? Fɔ sɔm pipul dɛn, dis kin bi sɔntin we strenj, sɔntɛm i kin ivin mek dɛn nɔ fil fayn. Dis na wetin wi kin kɔl Harlequin Syndrome pan mɛrɛsin. Pan ɔl we di nem kin tan lɛk big tin, i nɔto natin fɔ fred, bɔt i impɔtant fɔ no bɔt am.
Wetin na dis rili (Harlequin Syndrome)?
Fɔ tɔk am simpul wan, Harlequin Syndrome na wan say nɔmɔ na yu fes, yu nɛk, ɛn sɔntɛnde yu ɔp chɛst kin rɛd ɛn swet . I sɔprayz fɔ no se nɔ pan dɛn tin ya nɔ kin apin na di ɔda say na yu bɔdi, we kin kɔntinyu fɔ bi nɔmal.
Dis kכndyushכn kin apin bikoz fכ chenj na di fכnshכn na wi bכdi in simpatik nεv sεstem . Naw yu kin de wɔnda wetin na dis sɔri-at nervɔs sistɛm. Wi bɔdi gɛt wan rili wɔndaful kɔntrol sistɛm, we dɛn kɔl di autonomic nervous system . dis na di tin we de kכntro bכku tin dεm we de apin "כtomatik" we wi nכ de tink bכt dεm, lεk wi at rεt, bכdi prεshכn, brith, εn digεshכn.
pat pan dis כtonom nεv sεstem na di simpatik nεv sεstem. I tan lɛk di ‘alert’ sistɛm we wi bɔdi gɛt . Dis sistɛm kin aktiv we wi de rɔn, we wi de fred, ɔ we wi fil strɔng filin lɛk big gladi ɔr sɔri. Dɛn kɔl dis di ‘fayt-ɔ-flay’ rispɔns . Dis sympathetic nervous system na di wan we de signal wi bɔdi fɔ swet fɔ kɔntrol wi bɔdi tɛmpracha, jɔs lɛk we wi de ɛksesaiz fɔ kol. (Harlequin Syndrome) Di simptom dεm de sho we dis simpatik nεv sεstem de wok.
(Harlequin Syndrome) ɛn (Harlequin Sign) na tu difrɛn tin?
Yɛs, smɔl difrɛns de. (Harlequin Syndrome) de tɔk bɔt di nyurolɔjik kɔndishɔn we a bin dɔn tɔk bɔt. (Harlequin Sign) de tɔk bɔt di men sayn fɔ di sik. dat min se di skin kכla na wan say na di bכdi de chenj (rεd כ dak) εn di skin na di כda say de stil bεlε כ nכmal. Dis (Harlequin Sign) nɔr kin si am nɔmɔ pan (Harlequin Syndrome) bɔt yu kin si am bak as sayn fɔ sɔm ɔda wɛl bɔdi kɔndishɔn.
Dis na tin we rili kɔmɔn? Yu tink se i de mek pɔsin in layf de pan denja?
Harlequin Syndrome na rili wan sik we nɔ kin apin so ɔltɛm . Na wan wan pipul dɛn nɔmɔ dɛn dɔn ripɔt am ɔlsay na di wɔl. So i nɔ go sɔprayz if yu nɔ yɛri bɔt am bifo.
Di impɔtant tin na dat dis sik nɔ de mek pɔsin in layf de pan denja . Ɛn i nɔ go afɛkt di tɛm we yu go liv yu layf. So no rizin nɔ de fɔ mek wi fred we wi nɔ nid fɔ fred.
Wetin na di sayn dɛm fɔ dis?
Insay Harlequin Syndrome, de sayn dɛm wae yu kin gɛt na ɛni say na yu bɔdi kin difrɛn.
Di sayn dɛm wae yu kin si na di say we di sik afɛkt:
- Skin de tɔn rɛd ɔ dak pas yu nɔmal skin kɔlɔ.
- Swet bɔku bɔku wan.
- Di skin we de na da say de kin wam we yu tɔch am.
Di sayn dɛm wae dɛn kin si na di sayd wae nɔr afɛkt:
- Pale skin.
- Nɔto fɔ swet atɔl.
- Di skin we de na da say de kin kol we yu tɔch am.
dis we ya, dεn tin ya de luk lεk se dεn sheb di sayd dεm na di bכdi to tu. Imajin wan vertikal layn we dɛn drɔ frɔm di midul pan yu fɔɛd, dɔŋ yu nos, ɛn dɔŋ to yu chɛst.
Apat frɔm dɛn men sayn ya, yu kin si sɔm ɔda sayn dɛm wae nɔr kin pasmak bak:
- Na sɔm say dɛn, di skin kin dray ɛn i kin kɔmɔt lɛk skel.
- Ed de at.
- Nɔs we de rɔn .
- Kray wata we de kɔmɔt na di yay.
- di aylid dכp wan sayd εn/כ chenj dεm na di pupil dεm (dεn kכl am bak Hכna Sindrom , we kin kכnεkt wit wan sεparat kכndyushכn).
Ustɛm dɛn sayn ya kin apia?
Yu kin gɛt dɛn sayn ya fɔ Harlequin Syndrome, mɔ pan dɛn tin ya:
- We yu de du ɛksɛsayz: We yu de rɔn, jomp, ple, ɔ wok na di jim.
- Di tɛm we yu gɛt strɔng filin ɔr yu maynd strɛs: we yu rili gladi, sɔri, de fred, ɔr de ɔnda prɛshɔn bifo sɔmtin lɛk ɛgzam ɔr intavyu.
- Na hot klaymat: we yu de go na do na di san, we yu de na hot rum.
- We yu de it it we gɛt spays: We yu de it it we dɛn mek wit bɔku chili.
Imajin se yu de ple kriket wit yu padi dɛn ɛn yu de swet bɔku bɔku wan, ɛn na di rayt say nɔmɔ yu fes rɛd ɛn swet, bɔt di lɛft say fayn, jɔs lɛk aw yu kin du ɔltɛm. Na dat kin apin insay dis ɛkspiriɛns.
Wetin na de tin wae kin mek pɔrsin gɛt Harlequin Syndrome?
Bɔrku tɛm, e kin tranga fɔ fɛn wan patikyula kɔz fɔ Harlequin Syndrome. Dat min se, di tin we mek i apin nɔ klia. Bɔt risach dɔn sho se i kin bi bikɔs di kɔmyunikeshɔn bitwin di sɛl dɛn we de na di rayt ɛn lɛft say na wi ɔtonomik nɛvɔ sistɛm nɔ de wok fayn .
Sɔntɛnde, disrɔpshɔn kin de na dis kɔmyunikeshɔn we. dis kכmyunikeshn mεsej de kכmכt fr כm di haypothalamus na wi bren to di tכraks spεnal kכd na di כp chεst. na de di simpatik nεv dεm de gi di fes εn di כp pat na di bכdi. Dis rod de kɔntrol di swet ɛn di blɔd vesel dɛn.
Bɔku rizin dɛn de we mek dis intarapshɔn kin apin:
- na tכmכro we de fכm along di nεv path.
- Wund ɔ damej we infɛkshɔn ɔ inflamɛns dɔn mek.
- Aksidɛnt we kin apin bikɔs dɛn du ɔpreshɔn pan di ɔpa chɛst, lɛk we dɛn du ɔpreshɔn pan di spɛnal.
Udat dɛn kin gɛt dis sik mɔ? (Di tin dɛn we kin mek pɔsin gɛt prɔblɛm)
Dis sik we dɛn kɔl Harlequin Syndrome kin afɛkt ɛnibɔdi we ol ɛni ej, ivin bebi, pikin, ɛn big pipul . Bɔt yu kin gɛt dis sik if yu:
- If yu dɔn gɛt ɛndoskopik thoracic sympathectomy (na ɔpreshɔn we dɛn kin yuz fɔ trit we yu swet pasmak).
- If yu dɔn gɛt anestezi.
- If yu dɔn gɛt aksidɛnt we afɛkt yu sympathetic nervous system.
- If ɔda ɔndalayn mɛdikal kɔndishɔn de lɛk Horner Syndrome .
Us prɔblɛm dɛn dis kin mek?
Pan ɔl we dis nɔ kin apin so ɔltɛm, sɔm prɔblɛm dɛn kin apin bikɔs ɔf di Harlequin Syndrome. Dɛn tin ya na:
- I nɔ kin izi fɔ kɔntrol di bɔdi in tɛmpracha.
- Chenj fɔ ɔltɛm na di fes kɔlɔ (na wan say).
- Pwɛl hat, wɔri, ɔr nɔr de fil bad bɔt insɛf wae kin kam wae pɔrsin de tink bɔt aw pɔrsin de luk. Bikɔs, we ɔda pipul dɛn si dis na sosayti, i kin shem smɔl fɔ sɔm pipul dɛn.
Aw fɔ no di kɔrɛkt tin bɔt (Harlequin Syndrome)? (Diagnosis) .
Dɔktɔ go no if yu gɛt Harlequin Syndrome bay we i go chɛk yu sayn dɛm. Di fɔs tin we yu fɔ du na fɔ chɛk yu bɔdi . Dɔn, dɛn kin du difrɛn tɛst dɛn fɔ no ɔda tin dɛn we kin mek pɔsin gɛt di sem kayn sik ɛn fɔ no if sɔntin de we kin mek pɔsin gɛt di sem kayn sik.
Bɔku tɛst dɛn de we dɛn kin yuz fɔ no if pɔsin gɛt Harlequin Syndrome:
- Stress test: Insay dis tɛst, dɔktɔ go mek yu du ɛksɛsayz ɛn wach yu fɔ si if yu bɔdi de mek yu gɛt di sik. Di simptom dɛm fɔ Harlequin Syndrome kin bi mɔr we yu de du ɛksɛsayz.
- Imej tɛst: Dɛn tɛst ya kin mek yu dɔktɔ si insay yu bɔdi. Dis na tɛst dɛn we nɔ de mek pɔsin fil pen. Sɔm ɛgzampul dɛn na fɔ tek ɛkstrem rayt na in chɛst, CT skan (Computed Tomography), ɛn MRI (Magnetic Resonance Imaging) .
Wetin na di tritmɛnt dɛm fɔ dis?
Di gud nyus na dat Harlequin Syndrome nɔr kin nid tritmɛnt ɔltɛm . Sɔmtɛm de sik kin bɛtɛ fɔ insɛf. If dɔktɔ tɛl yu fɔ gi yu tritmɛnt, i go dipen pan wetin de mek yu gɛt di sik. Di tritmɛnt dɛn we yu kin gɛt na:
- Tɛrapi ɔr advays kin ɛp fɔ ridyus de sɔshal diskɔmfɔt ɛn maynd strɛs wae dis sik kin kam wit.
- Na vaysin we dɛn kin gi fɔ kɔntrol di fes we de rɛd ɔ we di skin kin chenj`(stɛlɛt ganglion blɔk)` .
- Kɔntrol di swet ɛn ɔda sayn dɛm wit botulinum toxin injection.
- If di tin we mek am na tumbu ɔ lɛsin, dɛn go nid fɔ du ɔpreshɔn ɔ redyushɔn tɛrapi fɔ pul am.
Wetin yu kin ɛkspɛkt if yu gɛt Harlequin Syndrome?
Bɔrku tɛm, Harlequin Syndrome nɔr kin kɔz ɛni big bad tin to yu bɔdi. Yu sik kin go fɔ dɛnsɛf as tɛm de go. Ɔ, yu kin jɔs gɛt di sayn dɛn we yu de du ɛksɛsayz ɔ it sɔntin we gɛt spays. Nɔto ɔlman nid tritmɛnt. Yu dɔktɔ go tɛl yu mɔ bɔt yu sik ɛn wetin fɔ ɛkspɛkt tumara bambay.
Aw lɔng dɛn sik ya kin te?
Bɔku tɛm di sayn dɛn kin las fɔ sɔm minit to sɔm awa nɔmɔ . Dis min se afta yu dɔn stɔp di aktiviti we mek yu gɛt di sik, di skin go kam bak to nɔmal insay shɔt tɛm. Fɔ ɛgzampul, if yu gɛt sɔm sayn dɛn we yu de du ɛksɛsayz, wans yu dɔn stɔp fɔ du ɛksɛsayz, kol, ɛn rɛst, di skin go kam bak to nɔmal.
Yu tink se dɛn kin ebul fɔ avɔyd di Harlequin Syndrome?
As fa as dɛn dɔn diskɔba te naw, no we nɔ de fɔ mek dɛn nɔ gɛt Harlequin Syndrome.
Ustɛm yu fɔ go to dɔktɔ?
If yu gɛt sɔm sayn dɛn we gɛt Harlequin Syndrome, lɛk we yu de swet na wan say nɔmɔ na yu bɔdi ɛn yu skin kɔlɔ de chenj, i impɔtant fɔ go to dɔktɔ . Bɔrku tɛm, Harlequin Syndrome nɔr kin wɔri bɔt. Bɔt nɔ kin apin so ɔltɛm, i kin bi sayn fɔ wan ɔndalayn mɛrɛsin, lɛk tumbu, so i impɔtant fɔ go to dɔktɔ fɔ no di rayt tin we mek i gɛt am.
Us kwɛstyɔn dɛn yu fɔ aks di dɔktɔ?
We yu go si dɔktɔ, i go fayn fɔ aks dɛn kwɛstyɔn ya:
- Wetin de mek a gɛt dis sik?
- A nid tritmɛnt ɔ ɔpreshɔn?
- Ɛni bad tin de we di tritmɛnt kin du?
- If a fil se a de shem ɔ a nɔ de fil fayn bikɔs ɔf di sik dɛn we a gɛt, us tritmɛnt dɛn de?
(Harlequin Syndrome) ɛn (Harlequin Ichthyosis) na di sem tin?
Nɔ, dɛn tin ya na tu tin dɛn we rili difrɛn. Dis na sɔntin we kin kɔnfyus bɔku pipul dɛn, so i fayn fɔ mek wi no klia wan.
Harlequin Syndrome na wan sik wae de mek yu swet ɛn yu skin kin chenj in kɔlɔ na wan say na di bɔdi. I nɔ de mek pɔsin in layf de pan denja, ɛn i nɔto tin we pɔsin kin gɛt we i kam pan in jɛnɛtiks (bɔt sɔm tɛm dɛn kin apin we pɔsin bɔn am).
Na di ɔda say, Harlequin Ichthyosis na wan sik we de kɔmɔt na di bɔdi we kin mek pɔsin in layf de pan denja.. di pikin we gεt dis kכndyushכn de bכn wit rili tik, rכf skin. di pikin dεm we gεt Harlequin Ichthyosis gεt pat dεm na dεn skin we shep lεk dayamכnd we dip fכs dεm de separet. Sɔntɛnde, dɔktɔ dɛn kin kɔl dis sik "Harlequin Baby Syndrome." Pan ɔl we i kin tan lɛk "Harlequin Syndrome," dis na tu rili difrɛn kɔndishɔn.
Mɛsej we dɛn kin kɛr go na os
Harlequin Syndrome (na wan sik wae kin mek yu swet fɔ sɔm tɛm ɛn yu skin kin chenj in kɔlɔ na wan say na yu bɔdi) kin afɛkt wan say na yu bɔdi nɔmɔ. Na nɔmal tin fɔ mek yu nɔ fil fayn we yu skin luk difrɛn pas aw i kin luk. Bɔt mɛmba se dis nɔto tin we de mek pɔsin denja.
Di tin we impɔtant pas ɔl na fɔ go to dɔktɔ if yu gɛt dɛn sik ya ɛn no di rayt tin we mek yu gɛt dis sik . Sɔntɛnde, di tin we kin mek i apin nɔ kin klia. Ivin if yu se yu nɔ nid tritmɛnt, if yu de gɛt ɛni saykilɔjik diskɔmfɔt bikɔs ɔf dis chenj pan aw yu de luk, yu kin tɔk to mɛntɛl hεlth kɔlnɔ bɔt am ɛn tɔk bɔt aw fɔ bil yusɛf ɛn gɛt fayn fayn pikchɔ bɔt yusɛf. Nɔto yu wan de, ɛn nɔ ɛva shem fɔ gɛt ɛp.
` Harlequin Syndrome, nervous system, swet, flush, autonomic nervous system, Horner Syndrome, sik dɛm we nɔ kin bɔku











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