Prɔblɛm de wit di ilɛktrik sistɛm na yu at? Lɛ wi tɔk bɔt Lɔng QT Sindrom (LQTS).

Yu dɔn ɛva yɛri bɔt di ilɛktrik we de na di at? Wi at de wok lɛk smɔl mashin. I gɛt ilɛktrik sistem, we de kɔntrol di at bit. Sɔntɛnde, smɔl chenj dɛn kin apin na dis ilɛktrik sistɛm. wan pan dεn chenj dεm ya dεn kכl am Long QT Syndrome, כ `(Long QT Syndrome - LQTS)`. Nɔ wɔri, lɛ wi tɔk bɔt dis simpul wan.

Wetin na Lɔng QT Sindrom? Fɔ tɔk am simpul wan...

Imajin se afta yu at bit wan tɛm, i de tek smɔl "rɛst" bifo i bit bak, lɛk we batri de chaj bak. di tεm we i tek fכ "rεst" כ richaj de lכng sכmtεm pas nכmal, we wi kכl lכng QT sεndrכm.

If yu dɔn gɛt ECG, we na tɛst we de luk di ilɛktrik aktiviti na di at, wan pat de we dɛn kɔl di QT intaval. dis sho aw lכng i tek fכ di lכw chεmba dεm na yu at, we dεn kכl di vεntrikl dεm, fכ kכntrakt εn afta dat i rilaks, כ "richaj" lεk aw a bin se.

di ilektrikal aktiviti na wi at de εp bay sכm sכm ilektrikal chaj patikyula dεm we dεn kכl `ayכn`. Ayɔn dɛn lɛk sɔdiɔm, kalsiɔm, potashɔm, ɛn klorayd kin ɛp fɔ mek dis apin. dis ayכn dεm de muv insay εn kכmכt na di at sεl dεm tru spεshal path dεm we dεn kכl `ayכn chεnal dεm`. naw, insay dis `(Long QT Syndrome)`, i kin bi se prכblεm de wit dεn ayכn chεnal dεm ya, כ dεn nכ de. afta dat di at de delay fכ "richaj". we di QT intaval de lכng, di risk de fכ wan denja fast at ritm dizכrd we dεn kכl `Torsades de Pointes`, we kin mek yu layf de pan denja.

Sɔm kayn Lɔng QT Sindrom de?

Yɛs, tu men kayn dɛn de. Wan na inherited , we min se i de pas tru jin. Di ɔda wan na acquired , we min se na ɔda tin dɛn lɛk sɔm mɛrɛsin dɛn kin mek i gɛt am.

Di kayn dɛn we dɛn bɔn wit:

dis dεm na di mεntal kכz fכ di jεnεtik difεkt dεm na di `ayכn chεnal dεm` we a bin mεnshכn.

• Ayɔn chanɛl abnɔmaliti: Dis na di kayn we we dɛn kin gɛt mɔ. difrεn tכp dεm de lεk `LQT1, LQT2, LQT3, LQT4, LQT5`. Dɛn kin klas dɛn tin ya akɔdin to di kayn ayɔn chanɛl we de insay. Di risk fɔ gɛt at sik tumara bambay kin difrɛn difrɛn wan bay di kayn sik.
• Jervell ɛn Lange-Nielsen Syndrome: Insay dis sik, dɛn mama ɛn papa ɔl tu kin gɛt di abnɔmal jin, bɔt dɛn nɔ kin gɛt ɛni sayn. Dis na tin we nɔ kin apin so ɔltɛm. Bikɔs i nɔ go izi fɔ mek di mama ɛn papa ɔl tu go kɛr di jin, ɛni pikin gɛt 25% chans fɔ gɛt am. Pipul wae gɛt dis sik kin bɔn dɛf.
• Romano-Ward Sindrom: Di sik we dɛn kɔl Romano-Ward Sindrom:insay dis kes, wan mama εn papa kin gεt di ``Lכng QT Syndrome'' εn di כda wan nכ kin gεt am. εvri pikin gεt 50% chans fכ gεt dis abnכmal jin. If na so i bi, fɔ yɛri na nɔmal tin.
• Timothy Syndrome: Dis na wan kayn sik bak we nɔ kin apin so ɔltɛm. I nɔ kin afɛkt di at nɔmɔ, bɔt i kin afɛkt ɔda pat dɛn na di bɔdi bak.

Aw dis sik kin kɔmɔn?

Long QT Syndrome na rili wan sik we nɔ kin apin so ɔltɛm . Fɔ ɛgzampul, na Amɛrika, dɛn se na lɛk wan pan ɛvri 2,000 pipul dɛn gɛt dis sik.

Wetin na di sayn dɛm wae de sho se yu gɛt Long QT Syndrome?

Dis na di sayn dɛm wae dɛn kin si bɔrku tɛm:

• Sinkɔp: I nɔ kin no natin wantɛm wantɛm.
• Sɔm kayn sik: Sɔm pipul dɛn kin gɛt sik wae de mɛk dɛn sik.
• Cardiac arrest: Dis kin rili denja.
• Day wantɛm wantɛm:

Dɛn simptom ya kin apin we di denja at ritm disɔda we dɛn kɔl `Torsades de Pointes` we a bin dɔn tɔk bɔt kin apin. Dis tεm, di at nɔ kin ebul fɔ pɔmp blɔd fayn fayn wan. If di bren nɔ gɛt bɛtɛ blɔd, tin dɛn lɛk fɔ fɔdɔm ɛn fɔ gɛt sik kin apin. If dis sik kɔntinyu, pɔsin kin day wantɛm wantɛm. Bɔt if di at rit kam bak lɛk aw i bin de, di sayn dɛn kin stɔp.

Di sayn dɛm kin apin mɔs we:

• We yu de du ɛksɛsayz (ɔ sɔm minit afta yu dɔn du ɛksɛsayz).
• During strong emotional stimulation , mɔ we yu fred ɔ sɔprayz wantɛm wantɛm.
• We yu de slip ɔ we yu wek wantɛm wantɛm .

Impɔtant, te to 50% pan di pipul dɛm wae gɛt Long QT Syndrome nɔr kin ɛva gɛt dis sik . Ɛn, fɔ lɛk wan pan ɛvri tɛn pipul dɛn, di at we de stɔp na di fɔs sayn fɔ di sik. Dis kin kil pɔsin if dɛn nɔ trit am kwik.

Bɔrku tɛm di sayn dɛm kin bigin wae pɔrsin dɔn big . If yu gɛt sɔm sayn dɛn, dɛn kin kam bak. De sik kin kam bifo yu rich 30. Bɔt sɔm pipul dɛn kin gɛt dis sik wae dɛn dɔn pas 50 ia ɛn pas dat.

Wetin kin mek pɔsin gɛt Long QT Syndrome?

As a bin dɔn tɔk bifo tɛm, dis kin kɔmɔt frɔm yu mama ɛn papa (we yu bɔn am) ɔ yu kin gɛt am bikɔs ɔf sɔm mɛrɛsin dɛn . insay Long QT Syndrome, wan abnכmaliti de na di jin kכd fכ yu ayכn chεnal dεm. dis abnכmal ayכn chεnal dεm de mek di rεkכvεshכn fεz fכ yu at rεt delay. Dis kin mek yu gɛt arrhythmia we go mek yu layf de pan denja.

Sɔm mɛrɛsin kin mek ``Lɔng QT Sindrom'' pan pipul dɛm we gɛt sɔm kayn prɛdispɔzishɔn to dɛn ayɔn chanɛl dɛm. Dɛn nɔ kin ivin no am, bɔt na we dɛn tek dɛn mɛrɛsin dɛn de na in ``Lɔng QT'' kin apin.

Drug dεm wae kin mek yu gεt akwyayz lכng QT sεndrכm:

• Sɔm `Antiarrhythmics` (mɛrɛsin fɔ at ritm dizayd) .
• Sɔm mɛrɛsin dɛn we de mek pɔsin in at pwɛl
• Sɔm diuretics (mɛrɛsin dɛn we de mek yu pis mɔ) .
• Sɔm antibayɔtik dɛn
• Serotonin risεptor inhibito dεm כ antagonist dεm
• Histamin rεsεptכr antagonist dεm

Ɔda tin dɛn we kin mek pɔsin gɛt di sik we dɛn kɔl acquired long QT syndrome:

• Sɔm kayn pɔyzin dɛn
• Anorexia nervosa (mɛntal sik we gɛt fɔ du wit anorexia) .
• Sɔm `bradyarrhythmias` (di at rit we nɔrmal fɔ slo) .
• Di smɔl smɔl kalsiɔm, magnɛsiɔm, ɔ potashɔm na di bɔdi
• Injury to yu nervɔs sistɛm

Udat de pan big risk fɔ gɛt dis sik?

Dɛn pipul ya de pan ay risk fɔ gɛt ``Long QT Syndrome``:

• Fɔ pikin dɛn we dɛf frɔm we dɛn bɔn dɛn.
• Pikin ɛn yɔŋ pipul dɛm wae gɛt famili histri wae dɛn nɔr ɛksplen bɔt dɛn kin day kwik kwik wan ɔr kin fɔdɔm (syncope).
• Fɔ blɔd fambul dɛm we gɛt ``Long QT Syndrome``.
• Fɔ di wan dɛn we gɛt `Cardiomyopathy` (at mɔsul sik) ɔ we dɛn bɔn wit at sik.
• Fɔ di wan dɛn we gɛt smɔl lɛvɛl pan sɔm ilɛktrɔlayt dɛn na di bɔdi bikɔs ɔf ɔda mɛrɛsin.
• Fɔ di wan dɛn we de tek mɛrɛsin we de afɛkt di ayɔn chanɛl dɛn na di at.

Yu tink se dɛn fɔ tɛst mi bak fɔ Long QT Syndrome?

Long QT Syndrome na wan jεnεtik kכndyushכn we kin pas dכn frכm jεnereshכn to jεnereshכn. If wan pan yu fɔs digri fambul dɛm (mama ɛn papa, brɔda ɛn sista, pikin dɛm) gɛt Long QT Syndrome, i fayn fɔ mek dɛn du yu jenɛtik skrinin .

Ɔl di fɔs digri fambul dɛn (brɔda ɛn sista, mama ɛn papa, ɛn pikin dɛn) fɔ gɛt ECG. I impɔtant bak fɔ ɛnibɔdi we gɛt famili histri fɔ sik ɔ fɔdɔm fɔ gɛt dis tɛst.

Di fɔs tin we yu fɔ du na fɔ mek yu dɔktɔ no se yu famili gɛt dis sik. I go mɔs bi se i go du di tɛst dɛn we i nid fɔ chɛk yu at. If dɛn tɛst dɛn de kɔnfyus se yu gɛt dis sik, yu fɔ go to dɔktɔ we de mɛn yu at ɛn we sabi bɔt Long QT Syndrome.

Wetin na di kɔmplikɛshɔn dɛm wae de kam wit Long QT Syndrome?

``Long QT Syndrome`` kin mek di layf-threatning aritmia ``Torsades de Pointes`` we a bin menshon. Dis kin ivin mek pɔsin day wantɛm wantɛm.

Aw dɛn kin no se pɔsin gɛt Long QT Syndrome?

Dɔktɔ dɛn kin no di Long QT Syndrome wit wan simpul ECG tɛst. Fɔ no di kɔndishɔn, dɛn kin mɛzhɔ di QT intaval na di ECG. If yu QT intaval lɔng pas 450 milisekɔnd, yu kin gɛt Lɔng QT Sindrom.

Yu dɔktɔ go aks yu bɔt dɛn tin ya:

• Yu tink se famili histri de fɔ ``Lɔng QT Sindrom''?
• Yu tink se famili histri de we dɔn mek dɛn nɔ ebul fɔ du natin, dɛn kin gɛt sik, ɔ dɛn at kin stɔp?
• Yu dɔn ɛva gɛt fɔdɔm, sik, ɔ yu at nɔ de stɔp, mɔ we yu de du ɛksɛsayz?

Us tɛst dɛn kin yuz fɔ no if pɔsin gɛt Long QT Syndrome?

Apat frɔm di ECG, dɛn kin du dɛn tɛst ya bak:

• Blɔd tɛst dɛn.
• Test fɔ di jenɛtiks.
• Ɛksesaiz strɛs tɛst.
• Ambulatory monitor: Dis de mכnitor yu hat fכ sכm dez.

Aw dɛn kin trit Long QT Syndrome?

Mɛrɛsin, divays, ɔ ɔpreshɔn de we kin ɛp fɔ kɔntrol di sayn dɛm ɛn fɔ mek pɔsin nɔ day wantɛm wantɛm fɔ Long QT Syndrome. Pan ɔl we dɛn tritmɛnt ya nɔ kin ebul fɔ mɛn di sik kpatakpata, dɛn kin protɛkt yu frɔm di at ritm we nɔr fayn.

Di mɛrɛsin dɛn we dɛn kin yuz

Bɔrku pipul dɛm wae gɛt Long QT Syndrome (ivin di wan dɛm wae nɔr gɛt sɔm kayn sik) kin tek wan beta-blocker, lɛk nadolol. Ɔda mɛrɛsin kin mek yu QT intaval shɔt ɔr kin mek yu ilɛktrɔlayt lɛvɛl bɛtɛ. Yu dɔktɔ go tɛl yu us mɛrɛsin dɛn go fayn fɔ yu.

Divays dɛn we dɛn kin yuz

Sɔm sik pipul dɛm wae gɛt ``Long QT Syndrome'' kin nid divays dɛm lɛk dɛn wan ya bak:

• Implantable Cardioverter Defibrillator (ICD): Dɛn kin put implantable cardioverter defibrillator (ICD) pan pipul dɛn we gɛt histri bɔt aw dɛn at dɔn stɔp ɔ we stil gɛt di sik pan ɔl we dɛn dɔn trit dɛn wit beta-blocker. Dis divays kin no if pɔsin gɛt aritmia we kin mek pɔsin in layf de pan denja ɛn i kin mek di at shɔk insɛf fɔ mek i nɔ day wantɛm wantɛm.
• Pacemaker: Dis divays de ɛp pipul dɛm wae gɛt abnɔmal slow hat rit.

Ɔpreshɔn

Sɔm pipul dɛm wae gɛt Long QT Syndrome kin nid fɔ du Left Cardiac Sympathetic Denervation (LCSD) ɔr sympathectomy. Dis na wan we we nɔ kin tek bɔku tin we dɛn kin pul sɔm nɛv dɛn na yu simpatik nɛv sistɛm.

Wetin na di kɔmplikeshɔn/sayd ifɛkt dɛm wae de kam wit tritmɛnt?

Di sayd ɛfɛkt ɔ prɔblɛm dɛn we kin apin kin dipen pan di kayn tritmɛnt we yu kin gɛt.

• Beta-blɔk: .
• Lɔw blɔd prɛshɔn.
• Diziz we pɔsin kin gɛt.
• Ed de at .
• Taya.
• ICD (Implantabl Kadiɔvata Difibrilatɔ): .
• Divays mistek dɛn.
• Di lɔng we dɔn fɔdɔm.
• Blɔd we de kɔmɔt.
• Infεkshכn dεm.
• Pesmɛka we de mek pɔsin peshɛnt: .
• Di lɔng we dɔn fɔdɔm.
• Blɔd we de kɔmɔt.
• Infεkshכn dεm.
• Divays mistek dɛn.
• LCSD (Lɛft Kadyak Simpatik Nɛv Dikɔmpreshɔn Ɔpreshɔn):
• Di sik we dɛn kɔl Horner syndrome.
• Di lɔng we dɔn fɔdɔm.
• Fes we de flash ɔ we de swet.

Yu tink se dɛn kin ebul fɔ protɛkt di Long QT Syndrome?

Yu nɔ go ebul fɔ stɔp am if yu gɛt am frɔm yu mama ɛn papa. Bɔt fɔ di wan dɛn we nɔ gɛt am, yu kin avɔyd di kɔndishɔn dɛn we de mek pɔsin gɛt akwyayz (lɔng QT sindrom) leta. Fɔ ɛgzampul, tek tɛm wit sɔm mɛrɛsin dɛn.

Wetin kin apin if a gɛt Long QT Syndrome?

Wit di rayt tritmɛnt , di mɔtaliti rεt fɔ pipul dɛm wae gɛt ``Lɔng QT Sindrom`` na lɛk 1%. If dɛn nɔ gɛt tritmɛnt, di tin kin rili bad. Na lɛk 21% pan di pipul dɛm wae gɛt dis sik wae nɔr de gɛt tritmɛnt kin day insay wan ia frɔm wae dɛn bigin fɔ gɛt dis sik.

Bɔt mɛmba se, pipul dɛm wae gɛt ``Long QT Syndrome'' kin liv ful layf . Dɛn kin gɛt bɛlɛ ɛn bɔn pikin dɛn.

Aw lɔŋ di Long QT Syndrome kin las?

Inherited Long QT Syndrome na wan sik wae de kam wae yu de liv yu layf. Bɔt di sayn dɛm ɛn di risk fɔ gɛt prɔblɛm kin go dɔŋ as tɛm de go.

Aw a kin kia fɔ misɛf?

Long QT Syndrome kin afɛkt bɔrku tin na yu ɛvride layf. Yu fɔ go to yu dɔktɔ bifo yu du sɔm tin dɛn.

Nɔys ɛn strɛs

Sɔm pipul dɛm wae gɛt Long QT Syndrome kin afɛkt wae dɛn kin gɛt lawd nɔys wantɛm wantɛm ɔr kin gɛt strɛs pan aw dɛn de fil. Pan ɔl we yu nɔ ebul fɔ kɔntrol ɔl di nɔys ɛn strɛs we de arawnd yu, yu kin tray fɔ stɔp dɛn.

• Tɛl yu padi ɛn fambul dɛn se i nɔ sef fɔ wek yu wantɛm wantɛm.
• Bifo yu yuz ala lawd wan we de ɔf wan tɛm, yuz alam we gɛt fayn sawnd.
• Tɔn di vɔlyum fɔ lawd tin dɛn we go mek yu sɔprayz.

Ɛksasayz

Sɔm kayn Long QT Syndrome kin gɛt prɔblɛm wit ɛksesaiz. Yu dɔktɔ go tɛl yu us aktiviti dɛn we fayn fɔ yu, i go dipen pan di kayn abnɔmal jin we yu gɛt. Bikɔs ɛksesaiz kin mek yu nɔ gɛt ritmi, yu fɔ tɔk to yu dɔktɔ bifo yu disayd fɔ ple kɔmpitishɔn spɔt. If yu disayd fɔ ple spɔt, yu go nid fɔ tek sɔm tin dɛn fɔ mek yu nɔ gɛt prɔblɛm.

Swim kin bi denja fɔ sɔm pipul dɛm wae gɛt ``Long QT Syndrome''. If yu fɔdɔm we yu de swim, yu kin drawn.

Mɛrɛsin dɛn we dɛn kin yuz

Bɔku mɛrɛsin kin mek di QT intaval lɔng. Dɛn mɛrɛsin ya kin afɛkt pipul dɛm wae gɛt ``Long QT Syndrome`` pas di wan dɛm wae nɔr gɛt am. If yu gɛt ``Long QT Syndrome``, yu fɔ du dɛn tin ya:

• Tɛl ɔl yu dɔktɔ dɛm se yu gɛt ``Long QT Syndrome''.
• Tɔk to yu dɔktɔ bifo yu tek ɛni mɛrɛsin we dɛn gi yu fɔ ɔda mɛrɛsin.
• Nɔ tek mɛrɛsin dɛn we yu kin bay na kɔt (OTC) (eksept klin aspirin ɔ paracetamol) we yu nɔ tɔk to yu dɔktɔ.

If yu gɛt ``Long QT Syndrome'', dɛn kayn mɛrɛsin ya kin afɛkt yu:

• Antihistamines (mɛrɛsin fɔ alɛji) .
• Antidipreshɔn (mɛrɛsin fɔ pwɛl hat) .
• Mɛrɛsin fɔ mental wɛlbɔdi prɔblɛm
• Mɛrɛsin fɔ gɛt at sik
• `Antibayɔtiks`
• Antifungals dɛn we dɛn kin yuz
• `Antivayrɔs dɛn`
• Mɛrɛsin fɔ sik dɛn we de na intestinal
• Di tin dɛn we de mek pɔsin nɔ gɛt kɔnvuls
• Diuretics (mɛrɛsin dɛn we de mek pɔsin de pis mɔ ɛn mɔ) .
• Mɛrɛsin fɔ mek pɔsin gɛt ay blɔd prɛshɔn
• Mɛrɛsin fɔ mɛn maygren
• Drug dɛn we de mek di kɔlɔstrel nɔ bɔku

Ustɛm a fɔ go to mi dɔktɔ?

Yu fɔ go to dɔktɔ we yu bigin fɔ gɛt di sik ɛn at le wan tɛm insay di ia afta dat. Wan ilɛktrofisiɔlɔjis na di bɛst tin fɔ du.

If yu pikin gɛt ``Long QT Syndrome'', yu fɔ go to yu dɔktɔ pas wan tɛm insay di ia fɔ mek shɔ se dɛn de gɛt di kɔrɛkt doz fɔ mɛrɛsin fɔ dɛn wet naw.

If yu gɛt divays we dɛn put insay yu bɔdi, yu fɔ go to yu dɔktɔ wan tɛm insay di ia fɔ mek shɔ se i de wok fayn.

Ustɛm a fɔ go na di Imejɛnsi Dipatmɛnt (ETU) ?

Pɔsin we in at nɔ de wok fayn nid fɔ go to dɔktɔ wantɛm wantɛm . Sɔmbɔdi we de nia yu fɔ bigin CPR (cardiac resuscitation) ɛn kɔl 911 (ɔ yu lokal imejensi nɔmba).

Us kwɛstyɔn dɛn a fɔ aks mi dɔktɔ?

Sɔm kwɛstyɔn dɛn we yu kin aks yu dɔktɔ:

• Us kayn ``Long QT Syndrome'' a gɛt?
• Us patikyula tritmɛnt yu kin kɔmɛnt fɔ mi?
• Aw ɔltɛm a nid fɔ si yu?
• Us mɛrɛsin ɛn aktiviti dɛm a fɔ avɔyd wit mi patikyula kayn ``Long QT Syndrome''?

Fɔ dɔn, wan Mɛsej we dɛn kin kɛr go na os

Na nɔmal tin fɔ fil wɔri we yu kam fɔ no se yu gɛt at sik. Bɔt if yu aks yu dɔktɔ kwɛstyɔn dɛn ɛn if nid de, tɔk to pɔsin we de gi yu advays, dat go ɛp yu fɔ fil fayn. I impɔtant fɔ fala yu dɔktɔ in instrɔkshɔn, tek yu mɛrɛsin dɛn di rayt tɛm, ɛn kip yu apɔntinmɛnt dɛn.

I kin fayn bak fɔ mek yu fambul ɛn padi dɛn no se yu gɛt Long QT Syndrome. If yu gɛt sɔm kayn sik wae dɛn de wit yu, dɛn kin kɔl fɔ ɛp kwik kwik wan. Ivin bɛtɛ, if dɛn no aw fɔ du CPR, i kin sev yu layf. Nɔ wɔri, wit di rayt manejmɛnt, yusɛf kin liv wɛlbɔdi layf.

` Lכng QT Sindrom, LQTS, hat sik, QT intaval, hat rεt, aritmia, jεnεtik sik dεm