Sɔntɛnde, yu kin fil smɔl fɔ blo? Ɔ yu kin fil taya pasmak ivin we yu de waka fɔ shɔt tɛm? Yu dɔn ɛva notis se yu finga dɛn ɛn yu lip dɛn kin tɔn blu wit sɔm tayt ɔ pen na yu chɛst? Nɔ dismis dɛn tin ya as jɔs nɔmal tin dɛn. Bikɔs sɔm tɛm, biɛn dɛn sik ya, sɔm kayn wɛl bɔdi prɔblɛm kin de we nid sɔm atɛnshɔn. Wan pan dɛn kayn tin ya na Pulmonary Arterial Hypertension (PAH) . Pan ɔl we di nem kin tan lɛk se i de mek pɔsin fred smɔl, lɛ wi tɔk bɔt am simpul wan ɛn di we we yu go ɔndastand.
Wetin na di Pulmonary Arterial Hypertension (PAH)? Fɔ tɔk am simpul wan...
Fɔ tɔk am simpul wan, Pulmonary Arterial Hypertension (PAH) na wan sik we di smɔl smɔl blɔd vesel dɛn na yu lɔng (pulmonary arteries) kin smɔl. Tink bɔt am lɛk wata paip we dɔn blok, ɛn i nɔ kin izi fɔ mek di wata pas insay. We dɛn blɔd vesel ya kin smɔl, di blɔd nɔ kin ebul fɔ pas fayn fayn wan na yu lɔng. Dis kin mek di prɛshɔn we de insay dɛn blɔd vesel dɛn ya ɔ blɔd prɛshɔn tumɔs . Na dɛn blɔd vesel ya kin kɛr blɔd we nɔ gɛt ɔksijɛn kɔmɔt na yu at to yu lɔng, usay dɛn kin klin am.
So wetin kin apin we dis kin apin? Di rayt say na yu at gɛt fɔ wok tranga wan pas aw i kin wok fɔ pɔmp blɔd to di lɔng dɛn. I tan lɛk we yu es ebi ebi wet ɛn klaym mawnten. We di at gɛt fɔ kɛr dis ɛkstra lod as tɛm de go, i kin bigin fɔ wik smɔl smɔl. If dɛn nɔ trit yu fayn, dis sik, PAH, kin mek yu gɛt sɔm prɔblɛm dɛn nɔto jɔs fɔ yu at ɛn yu lɔng, bɔt fɔ yu ɔl bɔdi.
Mɛmba se PAH na jɔs wan patikyula we fɔ wan big kategori we dɛn kɔl Pulmonary Hypertension . Pulmonary Hypertension na we di prɛshɔn de go ɔp na di blɔd vesel dɛm na di lכng bikɔs ɔf ɛni kɔz.
Aw PAH de afɛkt yu bɔdi?
Pulmonary Arterial Hypertension (PAH) kin mɔs put prɛshɔn na di rayt say na yu at. Dis na bikɔs dis pat pan di at de pɔmp blɔd we nɔ gɛt ɔksijɛn to di lɔng dɛn. As tɛm de go, dis ay prɛshɔn kin mek yu rayt-sayd at pwɛl .
Nɔto dat nɔmɔ, PAH de mek di blɔd flɔ bitwin di at ɛn di lɔng dɛn slo bak. Dis min se smɔl blɔd de go na di lɔng fɔ gɛt fresh ɔksijɛn. Dis dɔn mek smɔl ɔksijɛn de go na di ɔda ɔgan ɛn tisu dɛn na yu bɔdi. Infakt, ɔl pat na wi bɔdi nid ɔksijɛn fɔ mek i go liv. If i nɔ gɛt inof, prɔblɛm kin kam.
Aw siriɔs dis sik dɛn kɔl PAH?
Pulmonary Arterial Hypertension (PAH) na wan sik we rili siriɔs, sɔntɛnde i kin mek pɔsin in layf de pan denja . Bɔt if dɛn no am kwik ɛn trit am kwik, yu kin liv lɔng, bɛtɛ layf. Na dat mek i impɔtant fɔ pe atɛnshɔn to di sayn dɛm.
Udat dɛn PAH kin afɛkt mɔ?
PAH kin afɛkt big pipul dɛn we gɛt ɛni ej. Bɔt i kin bɔku pan uman dɛn , we dɛn kin no se dɛn gɛt di sik bitwin 30 ɛn 60. Dɛn dɔn si bak se man dɛn we dɔn pas 65 ia we gɛt PAH kin gɛt mɔ risk fɔ gɛt dis sik.
Dis sik kin afɛkt yɔŋ pikin dɛn bak. we i kin apin to pikin dεm we dεn bכn, wi kin kכl am Pεrsisεnt Pulmonary Hypertension in di Neonate (PPHN) .
Aw kɔmɔn tin fɔ PAH?
We yu kɔmpia am wit ɔda kayn pulmonary hypertension, lɛk pulmonary hypertension we kin kam wit at sik ɔ lɔng sik, PAH nɔto wan sik we kin rili kɔmɔn . Ivin na kɔntri lɛk Amɛrika, na 500 to 1,000 nyu pipul dɛn nɔmɔ kin gɛt PAH ɛvri ia. Insay Wɛstinian kɔntri dɛn, di wan dɛn we kin gɛt dis sik kin bi lɛk 25 pan ɛvri milyɔn.
Wetin na di sayn dɛm fɔ Pulmonary Arterial Hypertension (PAH)?
Yu nɔ go gɛt ɛni simptom na di fɔs stej fɔ PAH. Bɔrku pipul dɛn kin jɔs bigin fɔ gɛt sɔm sayn dɛm wae de sik de go bifo. Sɔm pan dɛn sayn ya na:
- Blu di kɔlɔ we di finga dɛn ɔ di lip dɛn kin chenj: I tan lɛk se di blɔd nɔ gɛt ɔksijɛn.
- Chɛst pen ɔ tayt: I tan lɛk se pɔsin de swɛt yu chɛst.
- Diziz ɔr fɔdɔm: Dis kin apin we di blɔd nɔ de flɔ na di bren.
- Taya: Fɔ fil taya pasmak , nɔto jɔs taya.
- Rɛsin ɔ paund at bit.
- Fɔ blo shɔt: Dis kin bɔku as tɛm de go. Ivin we yu du smɔl smɔl wok dɛn, dat kin mek yu nɔ blo fayn.
- Swel (Edima): Swel kin bigin fɔs na di leg ɛn anklɛ, dɔn i kin go na di bɛlɛ ɛn nɛk.
If dɛn nɔ trit dɛn, dɛn PAH simptom ya go wɔs as tɛm de go. Yu kin si se yu nɔ ebul fɔ du ivin di men tin dɛn we yu kin du ɛvride we yu nɔ nid fɔ blo ɔ rɛst.
Wetin na di tin dɛm wae kin mek pɔrsin gɛt Pulmonary Arterial Hypertension (PAH)?
Di men tin we kin mek yu gɛt PAH na we di layn we de na di blɔd vesel dɛn na yu lɔng dɛn kin pwɛl. Bɔt, nɔto ɔltɛm i kin klia wetin kin mek dis damej.
Kes dɛm we dɛn nɔ kin fɛn ɛni kɔz (Idiopathic PAH) .
Sɔntɛnde, dɛn nɔ kin ebul fɔ fɛn ɛni patikyula rizin . Wi dɔktɔ dɛn kin kɔl am “idiopathic” pulmonary arterial hypertension . I tan lɛk se na mistɛri.
Di tin dɛn we dɛn no bɔt di tin dɛn we kin mek i apin
Bɔt ɔda tɛm dɛn, klia tin dɛn de we kin mek i apin. Sɔm pan di tin dɛn we dɛn no se kin mek pɔsin gɛt PAH na:
- Sɔm sik dɛn we pɔsin kin gɛt:
- Hat sik we dɛn bɔn wit
- Di sik dɛn we kin mek pɔsin stɔrɔj glycogen
- HIV infɛkshɔn
- Liva sik
- Ɔtoimyun sik dɛm lɛk lupus
- Pɔtal haypatɛnshɔn (di prɛshɔn we de go ɔp na di blɔd vesel dɛn we de go na di liva) .
- di pulmonary capillary hemangiomatosis (di kapilari dεm we de na di lכng dεm de gro we nכ nכmal) .
- Pulmonary veno-occlusive disease (we di vein dεm na di lכng dεm de blok) .
- Schistosomiasis (na infεkshכn we wan parasayt de kכz) .
- Skleroderma (we di skin ɛn di kɔnɛktiv tisu tik) .
- Di chenj dɛn we de apin na di jɛnɛtiks:
- Bɔku tɛm, dis kin bi bikɔs ɔf wan muteshon na yu BMPR2 jin . Dis jin de kɔntrol di nɔmba fɔ di sɛl dɛn we de na sɔm tisu dɛn na wi bɔdi. So, we dɛn chenj dis jin, di sɛl dɛn we de na di smɔl smɔl blɔd vesel dɛn na yu lɔng kin gro tumɔs. We dɛn sɛl dɛn ya ful-ɔp, di say dɛn we de opin na di blɔd vesel dɛn kin smɔl.
- PAH kin rɔn insay famili. Wi kɔl am heritable PAH . bכt 80% pan di pipul dεm we gεt dis kכndyushכn gεt mכtεshכn na di BMPR2 jin.
- Sɔm pipul dɛn kin gɛt dis jin we dɛn dɔn chenj, bɔt dɛn nɔ kin ɛva gɛt PAH.
- Sɔm pipul dɛn kin gɛt PAH pan ɔl we nɔbɔdi nɔ gɛt am na dɛn famili, bikɔs ɔf wan jɛnɛtik muteshon. Dɛn kɔl dis sporadik PAH .
- Sɔm mɛrɛsin ɛn mɛrɛsin dɛn:
- Sɔm diet pills , lɛk di ol drɔg “fen-phen,” dɔn ban naw, bɔt dɛn kin stil mek PAH sɔm ia afta dɛn dɔn yuz am.
- Drug dɛn fɔ ɛnjɔy yusɛf , fɔ ɛgzampul kɔkɛyn ɛn mɛtamfɛtamin.
Aw dɛn kin no se pɔsin gɛt di sik we dɛn kɔl Pulmonary Arterial Hypertension (PAH)?
I kin tranga fɔ no PAH bikɔs di sayn dɛm fɔ PAH tan lɛk bɔku ɔda sik dɛm. Yu dɔktɔ go du yu bɔdi ɛgzam ɛn tɔk to yu bɔt yu sik ɛn mɛdikal histri. Dɛn go du bɔku tɛst (inklud imej tɛst ɛn blɔd tɛst) fɔ no if yu gɛt pulmonary hypertension ɛn, if na so, us kayn i bi.
Yu dɔktɔ kin sɛn yu bak to dɔktɔ we de mɛn yu pulmonɔn ɔ dɔktɔ we de mɛn yu at . Dɛn spɛshal pipul ya go du spɛshal tɛst fɔ chɛk aw yu at ɛn yu lɔng dɛn de wok. Dɛn go no if yu gɛt PAH ɔ ɔda kayn pulmonary hypertension. Dɛn go asɛs bak aw yu sik bad.
Spɛshal tritmɛnt dɛn de fɔ PAH we nɔ de fɔ ɔda kayn pulmonary hypertension. So, yu mɛdikal tim nid fɔ no bɔku tin bɔt wetin de apin na yu lɔng ɛn at. Dis infɔmeshɔn go ɛp dɛn fɔ mek di bɛst tritmɛnt plan fɔ yu.
Us tɛst dɛn kin yuz fɔ no if pɔsin gɛt PAH?
Yu mɛdikal tim go yuz kɔmbayn tɛst fɔ pul ɔda sik dɛn ɛn fɔ no se yu gɛt PAH.
If yu dɔktɔ sɔspɛkt se yu kin gɛt PAH afta yu fyzikal ɛgzam, di fɔs tɛst we dɛn go ɔda na transthoracic echocardiogram . Dis tεst de evaluate di כvala strכkchכ εn di wok we yu at de du.
Ɔda tɛst dɛn kin bi:
- Blɔd tɛst: Chɛk di ɔgan dɛn we de wok, di ɔmon lɛvɛl, ɛn no di sik dɛn we de ɔnda di sik. εspεshali tεst dεm lεk di komplit mεtabolik panεl εn komplit bכdi kכnt .
- Chɛst CT skan: Fɔ chɛk ɛn pul ɔda tin dɛn lɛk kidni sik. (Sɔntɛm di kidni sik we de na di ɔrijinal atikul fɔ bi lכng sik. CT chεst skan de luk di lכng εn chεst כgan dεm. Lε wi se wi de luk di kכndishכn fכ di lכng.
- Chɛst ɛkstrem rayt: Fɔ si if yu at ɔ yu pulmonari at dɛn big pas aw i fɔ bi.
- At MRI: Asɛs di kɔndishɔn na yu at in rayt ventricle (dis na di chɛmba na di at we de pɔmp blɔd to di lכng).
- Polysomnogram (PSG): I de chɛk fɔ si if pɔsin nɔ ebul fɔ slip, we kin mek PAH wɔs. PSG na wan kayn slip tɛst we dɛn kin du wan nɛt.
- Pulmonary function tests: Si aw yu lכng dεm de wok fayn fayn wan.
- Pulmonary ventilation/perfusion (VQ) scan: I de chɛk fɔ si if blɔd dɔn klot na di lɔng dɛn. dis tεst kin pul wan kכndyushכn we dεn k כl krכnik tromboεmbolik pulmonari haypatεnshכn .
- rayt hat kateshכn: I de mכsu di prεshכn na di bכdi vεsul dεm na yu lכng (pulmonary artery prεshכn). Dis tɛst impɔtant fɔ difinitiv wan fɔ no PAH.
- Siks minit waka tɛst: Si ɔmɔs ɛksesaiz yu kin bia ɛn ɔmɔs ɔksijɛn de go na yu blɔd we yu de muv.
Tɔk to yu dɔktɔ bɔt us tɛst yu nid fɔ du ɛn aw fɔ rɛdi fɔ dɛn.
Wetin na di krayteria fɔ no if pɔsin gɛt Pulmonary Arterial Hypertension?
Dɔktɔ dɛn kin no if yu gɛt pulmonari haypatɛyshɔn bay we dɛn de mɛzhɔ di prɛshɔn we de na di blɔd vesel dɛn na yu lɔng. di krayteria fכ no di sik na dat di pulmonary arterial prεshכn na yu lכng dεm pas 20 milimita mεkkyuri (20 mmHg) we yu de rεst . Dɛn kin mɛzhɔ dis valyu bay we dɛn de yuz rayt at kateshɔn .
Wetin na di tritmɛnt fɔ Pulmonary Arterial Hypertension (PAH)?
Di men gol dɛm fɔ tritmɛnt fɔ PAH na fɔ kɔntrol aw di sik de go bifo ɛn fɔ gi yu bɛtɛ kwaliti layf. No wan saiz-fit-ɔl tritmɛnt nɔ de fɔ PAH. Yu dɔktɔ go wok wit yu fɔ no di bɛst tritmɛnt fɔ yu patikyula nid dɛn.
Yu PAH tritmɛnt plan kin inklud:
- Balloon atrial septostomy (BAS): Dɛn kin du dis fɔ pikin dɛn we gɛt at prɔblɛm we dɛn bɔn wit, bɔt sɔm tɛm dɛn kin yuz am fɔ big pipul dɛn we gɛt PAH. Septostomy de ɛp fɔ ridyus di prɛshɔn na di rayt say na di at, we de mek mɔ ɔksijɛn go ɔlsay na di blɔd. Dɛn kin du am bak as brij fɔ transplant lɔng.
- Calcium channel blockers: Dɛn mɛrɛsin ya kin ɛp fɔ mek di blɔd prɛshɔn na di blɔd vesel dɛn na yu lɔng ɛn ɔlsay na yu bɔdi go dɔŋ.
- Diuretics: Dɛn kin kɔl dɛn bak "wata pills," dɛn drɔgs ya kin ɛp fɔ pul di wata we pasmak na di bɔdi ɛn ridyus di swel.
- Ɔksijɛn tɛrapi: Dɛn kin nid dis tritmɛnt if yu nɔ gɛt bɛtɛ ɔksijɛn na yu blɔd. Ɛkstra ɔksijɛn kin ɛp we yu de rɛst, slip, ɔ du ɛksɛsayz.
- Pulmonary vasodilators: Dɛn drɔgs ya de ɛp di blɔd vesel dɛm na yu lכng (pulmonary arteries) fɔ rilaks ɛn opin big wan. Dis kin mek yu at nɔr de strɛs ɛn ɛp fɔ mek yu nɔr gɛt di sik.
Fɔ sɔm pipul dɛm wae gɛt siriɔs PAH , fɔ transplant dɛn lɔng kin bi di las tin fɔ du. Dis ɔpreshɔn kin gi yu wan ɔ tu nyu lɔng dɛn. If yu transplant yu at-lɔng, dat kin gi yu nyu at bak.
Wetin na di mɛrɛsin dɛn we dɛn kin gi fɔ PAH?
Di mɛrɛsin dɛn fɔ trit PAH kin kam difrɛn we dɛn:
- Mεdikeshכn dεm we dεn kin tek fכ it: Dεn mεdikeshכn ya kin εp fכ rilaks di blכd vesel dεm na di lכng εn mek dεn nכ sכmtεm. Dɛn mɛrɛsin ya kin ɛp yu bak fɔ du tin wit yu bɔdi.
- Mɛrɛsin dɛn we yu kin blo: Trit di prɔblɛm dɛn we yu kin gɛt we yu de blo.
- Pɔtabl infushɔn pɔmp: Dis kin ɛp fɔ opin di blɔd vesel dɛn ɛn mek di blɔd flɔ mɔ. Dis kin ɛp fɔ mek yu gɛt bɛtɛ sik.
- Intravenous (IV) mεdikeshכn: Opin di blɔd vesel dεm εn rεliv di simptom dεm lεk chεst pen εn difεlεbl fכ brith.
Na sɔm mɛrɛsin dɛn we di US Food and Drug Administration (FDA) dɔn gri fɔ di wan dɛn we gɛt PAH:
- Ambrisentan (we dɛn kin yuz mɔt) .
- Bosentan (we dɛn kin yuz mɔt) .
- Epoprostenol (IV) we dɛn kɔl .
- Iloprost (we yu de blo) .
- Macitentan (we dɛn kin tɔk to pɔsin) .
- Riociguat (we dɛn kin yuz mɔt) .
- Selexipag (we dɛn kin yuz mɔt) .
- Sildenafil (we dɛn kin yuz mɔt) .
- Tadalafil (we dɛn kin yuz mɔt) .
- Treprostinil (we yu de tek yu mɔt, we yu inhal, pɔmp, IV) .
Sayd ɛfɛkt dɛn we PAH mɛrɛsin dɛn kin gɛt
Sɔm kɔmɔn sayd ɛfɛkt dɛm fɔ di mɛrɛsin dɛm we dɛn kin yuz fɔ trit PAH na:
- Fɔ fil se yu ed de tɔn ɔ yu de fil fɔdɔm.
- Fɔ fil se yu fes, yu nɛk, ɔ yu an wam (flɔsh).
- Di simptom dɛm we de na di bɛlɛ lɛk fɔ blo, fɔ nɔs, fɔ vɔmit, ɛn fɔ gɛt dayarɛa.
- Ɛd we de at (ed we de at).
- Lɔw blɔd prɛshɔn (Hypotension) .
- swel na di leg ɛn ankles (Pedal edema) .
- Rash na di skin.
- Fɔ fil se di ɔpa respiratɔri trakt kɔnjɛshɔn.
Sɔm mɛrɛsin dɛn kin gɛt ɔda bad bad tin dɛn. Tɔk to yu dɔktɔ bɔt aw fɔ kɔntrol ɛni sayd ɛfɛkt. Sɔntɛnde, yu dɔktɔ kin nid fɔ chenj di doz fɔ yu mɛrɛsin.
Yu tink se dɛn kin mɛn Pulmonary Arterial Hypertension (PAH) ɔltogɛda?
Pan ɔl we di mɛrɛsin dɛn we dɛn de yuz naw kin kɔntrol aw PAH de go bifo, dɛn nɔ kin ebul fɔ rivɛns di damej we dɔn ɔlrɛdi apin . Bɔt di wan dɛn we de stɔdi bɔt dis de chɛk nyu mɛrɛsin dɛn we dɛn tink se kin rivɛns PAH. Dɛn kayn drɔgs ya kin mek di ɛndoteyl sɛl dɛn we de layn di blɔd vesel dɛn na yu lɔng dɛn dɔn pwɛl.
Tɔk to yu dɔktɔ fɔ lan mɔ bɔt di laytst risach ɛn klinik trial fɔ PAH tritmɛnt.
Us tin dɛn kin mek pɔsin gɛt di chans fɔ gɛt Pulmonary Arterial Hypertension (PAH)?
Bɔku tin dɛn we kin mek di risk fɔ gɛt PAH bɔku na:
- Kɔnɛktif tisu sik .
- Daun sindrom .
- Famili histri fɔ pulmonari haypatɛyshɔn.
- HIV infɛkshɔn.
- Yuz drɔgs fɔ lɔs yu wet lɛk “fen-phen” (dexfenfluramine ɛn phentermine).
- Yuz drɔgs we nɔ rayt (drɔg dɛn we de na strit).
If pɔsin na yu famili gɛt PAH, aks yu dɔktɔ bɔt aw fɔ tɛst yu jɛnɛtiks. If dɛn no se yu gɛt PAH, i fayn fɔ aks yu famili fɔ tink bɔt fɔ tɛst yu jɛnɛtiks bak.
Aw fɔ mek yu nɔ gɛt Pulmonary Arterial Hypertension (PAH)?
wi nכ kin kכntro sכm risk fכ PAH (lεk jεnεtik mכtεshכn). Bɔt fɔ de fa frɔm di mɛrɛsin dɛn we nɔ rayt , dat kin mek yu nɔ gɛt PAH nɔmɔ, bɔt bɔku ɔda wɛlbɔdi prɔblɛm dɛn. Dɔn bak, tɔk to yu dɔktɔ bifo yu tek ɛni mɛrɛsin fɔ mek yu nɔ gɛt bɔku bɔku bɔdi.
Dipen pan di tin dɛm wae de mek yu gɛt dis sik, yu dɔktɔ kin se yu fɔ chɛk fɔ no if yu gɛt PAH.
Wetin na di fyuchu fɔ pipul dɛm wae gɛt Pulmonary Arterial Hypertension (PAH)?
Wit di advans pan tritmɛnt, pipul dɛm wae gɛt PAH de liv lɔng pas aw dɛn bin de liv bifo. Aw yu go liv yu layf kin dipen pan bɔku tin, lɛk aw yu sik kin tranga ɛn aw dɛn kin no aw yu sik kwik kwik wan. Tɔk to yu dɔktɔ bɔt yu patikyula sik.
Di tin we impɔtant pas ɔl na fɔ kɔntinyu fɔ gɛt yu tritmɛnt ɛn fala yu dɔktɔ in instrɔkshɔn dɛn gud gud wan. Sɔm tin dɛn de we yu kin du fɔ mek yu gɛt mɔ chans fɔ liv:
- Mek wan imejensi kit. Sɔm sapɔt ɛn infɔmeshɔn dɛn de we yu fɔ gɛt wit yu ɔltɛm. Aks yu dɔktɔ wetin fɔ put insay yu kit, ɛn nɔ ɛva kɔmɔt na os we yu nɔ gɛt am.
- Gɛt sizin vaysin dɛn lɛk aw yu dɔktɔ tɛl yu. I rili impɔtant fɔ protɛkt yusɛf frɔm flu ɛn nyumonia.
- Kip ɔl di apɔntinmɛnt dɛn fɔ fala yu. I impɔtant fɔ chɛk-ap ɔltɛm fɔ chɛk aw yu lɔng ɛn at de wok ɛn fɔ no aw yu tritmɛnt de go bifo.
- Tek yu mɛrɛsin dɛn jɔs lɛk aw yu dɔktɔ tɛl yu fɔ tek, di sem tɛm ɛvride. Nɔ chenj di we aw yu de tek yu mɛrɛsin dɛn if yu dɔktɔ nɔ advays yu.
Us chenj dɛn we a nid fɔ chenj mi layf?
Fɔ fala yu dɔktɔ in advays bɔt ɛni chenj na yu layf we yu want fɔ mek. Jɛnɛral wan, na sɔm advays dɛn ya we impɔtant:
- Nɔ yuz ɔt tub, sawna, ɛn travul go na ay ay ples.
- Tink bɔt aw fɔ kɔntrol bɔn pikin. Bεlε kin denja fכ pipul dεm we gεt PAH. Tɔk to yu dɔktɔ if yu de plan fɔ gɛt bɛlɛ ɔ if yu kin gɛt bɛlɛ.
- Ɛksesaiz ɛn kɔntinyu fɔ du tin dɛn as yu ebul. Tɔk to yu dɔktɔ bɔt us ɛksesaiz dɛn we nɔ bad fɔ yu ɛn ɔmɔs aktiviti yu fɔ du ɛvride. Aks yu dɔktɔ bifo yu bigin fɔ du nyu ɛksɛsayz program.
- Fɔ fala di it we go ɛp yu at. Dis inklud it dɛn we nɔ gɛt bɔku sɛtyuret fat, trans fat, ɛn sɔdiɔm.
- Stɔp fɔ smok ɛn yuz tin dɛn we dɛn kin yuz fɔ smok. Dɔn bak, nɔ smok sɛkɔn-han smok.
- Sik sɔpɔt, nɔ tray fɔ go tru yu PAH joyn yu wan. Aks yu dɔktɔ bɔt sɔpɔt grup ɛn risɔs.
Ustɛm a fɔ kɔl mi dɔktɔ?
Kɔl yu dɔktɔ if yu gɛt ɛni wan pan dɛn kwɛstyɔn ya:
- If di at rit pas 120 bit pan minit (fast hat rit).
- If infεkshכn we de na di rεspiretכri כ kכf de bכku.
- If bɔku tɛm yu kin fil lɛk se yu ed de tɔn ɔ yu kin fɔdɔm.
- If yu gɛt pen na yu chɛst ɔ yu nɔ de fil fayn we yu de du tin dɛn we yu de du.
- If yu taya pasmak ɔ yu nɔ ebul fɔ du nɔmal wok dɛn.
- Nɔs ɔ nɔ want fɔ it.
- Nɔ rɛst ɔ kɔnfyushɔn.
- If yu shɔt briz de wɔs, mɔ if yu fil se yu nɔ de blo fayn we yu wek.
- If yu anklɛ, yu leg, ɔ yu bɛlɛ we de swel go wɔs.
- I nɔ izi fɔ blo we yu de du nɔmal tin ɔ we yu de rɛst.
- We yu de gɛt bɔku bɔku wet (2 paund fɔ wan de ɔ 5 paund fɔ wan wik).
Ustɛm a fɔ go na di Imejɛnsi Tritmɛnt Yunit (ETU) ?
If yu gɛt ɛni wan pan dɛn tin ya, go na di imejensi rum ɔ kɔl yu lokal imejensi nɔmba:
- If di at rit (120-150 bit pan minit) nɔ go dɔŋ.
- Faint, mek yu nɔr no natin.
- Kɔmplikɛshɔn dɛn we de kɔmɔt frɔm yu IV ɔ infushɔn pɔmp (lɛk infɛkshɔn, kateshɔn we de kɔmɔt, sɔlvushɔn lik, blɔd, IV pɔmp nɔ de wok fayn).
- If di shɔt briz nɔ go ivin afta yu dɔn rɛst.
- Chest pen we kin kam wantɛm wantɛm ɛn we kin rili bad.
- Wan ed we kin at wantɛm wantɛm ɛn we kin at bad bad wan.
- Di an ɔ leg dɛn kin wik ɔ paralayz wantɛm wantɛm.
Fɔ dɔn, wan mɛsej we wi fɔ mɛmba
Pulmonary Arterial Hypertension (PAH) na wan sik we de chenj in layf. If yu ɔr pɔrsin wae yu lɛk dɔn gɛt dis sik, tek tɛm lan bɔt de sik ɛn wetin yu kin ɛkspɛkt. Aks yu dɔktɔ bɔt di tin dɛm wae de ɛksplen aw PAH de woke ɛn aw tritmɛnt kin ɛp.
Wan pan di tin dɛn we yu go ebul fɔ gɛt na di sɔpɔt we ɔda pipul dɛn de gi yu na yu layf. Nɔ tray fɔ mɛn dis kɔndishɔn yu wan. If yu fambul ɛn padi dɛm nɔr de, aks yu dɔktɔ bɔt sɔpɔt grup ɛn kɔmyuniti risɔs.
If dɛn dɔn no se yu pɔsin we yu lɛk gɛt dis sik, du ɔl wetin yu ebul fɔ mek dɛn fil se dɛn de sɔpɔt am ɛn ɛp dɛn fɔ kɔnɛkt wit ɔda pipul dɛn. We wi sik kin mek wi fil se wi nɔ de nia wi kɔmpin dɛn pan sɔm we dɛn, bɔt i kin mek wi kam nia wi kɔmpin bak. Yuz dis tɛm fɔ bil kɔmyuniti we go ɛp yu ɔ pɔsin we yu lɛk fɔ go bifo.
` Pulmonary Arterial Hypertension, PAH, pulmonary hypertension, shɔt brith, at sik, lכng sik, simptom dεm











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