Sɔntɛnde, yu pikin kin fil bad fɔ blo? Ɔ i kin taya kwik kwik wan ivin afta we i dɔn ple fɔ sɔm tɛm? Sɔm yɔŋ pikin dɛn kin gɛt at sik dɛn we dɛn bɔn wit. Tide wi go tɔk bɔt wan pan dɛn kayn sik ya, we nɔ kin bɔku, bɔt we rili impɔtant fɔ no bɔt. Wi kin kɔl dis `(Pulmonary Artery Stenosis)`. Fɔ tɔk am simpul wan, na we di men at we de kɛr blɔd go na di lɔng dɛn we de blok.
Wetin na di Pulmonary Artery Stenosis?
fכ put am simpul, wan big bכdi de we de kכri bכdi frכm di rayt say na wi at (we wi kכl ``rayt vεntrikl``) to di lכng dεm. dis dεn kכl am di ``pulmonary artery``. We i rich na di lɔng dɛn, dis blɔd kin gɛt ɔksijɛn, dɔn da blɔd de we gɛt ɔksijɛn kin go ɔlsay na di bɔdi.
naw, insay dis kכndishכn we dεn kכl `(Pulmonary Artery Stenosis)`, di bכdi we de kכri bכdi to di lכng dεm de blok כ sכmtεm na wan say כ na wan pan in branch dεm. I tan lɛk se wata paip de blok na di midul. Wetin kin apin da tɛm de? I kin at fɔ mek blɔd go na di lɔng dɛn. If di blɔd nɔ de flɔ fayn, di bɔdi nɔ go gɛt di ɔksijɛn we i nid. Bikɔs ɔf dis, di pikin in at ɛn di wan ol bɔdi nɔ kin ebul fɔ wok fayn.
dis blכk kin apin na di men pulmonari atεri (`(mεn pulmonari atεri)`), כ na in lεft כ rayt branch dεm (`(lεft כ rayt branch dεm)`). we dis blכk de apin, di rayt say na di at (`(rayt vεntrikl)`) fכ wok tranga wan fכ pכmp bכdi pas di blכk. I tan lɛk se yu fɔ yuz bɔku pawa fɔ push wata tru paip we dɔn blok. As tɛm de go, dis kɔntinyu fɔ tray kin pwɛl di at mɔsul.
Us prɔblɛm dɛn kin kam wit dis sik?
If dɛn nɔ trit dis fayn, as tɛm de go di rayt say na di at kin nɔ ebul fɔ wok fayn. dat min se, posisibul de fכ divεlכp wan kכndyushכn we dεn kכl ``Right-sided heart failure''. So, i rili impɔtant fɔ tek kia ɔf dis.
Udat dɛn dis kayn tin kin afɛkt mɔ?
dis kכndyushכn we dεn kכl `(Pulmonary Artery Stenosis)` na rili kwik rεs . Dat min se i nɔ kin apin to ɔlman. sכm pikin dεm kin gεt am wit כda at sik dεm (`(congenital heart disease)` - dat na hat sik dεm we de de we dεn bכn dεm). Sɔntɛnde, na in wangren kin bi wae nɔr gɛt ɛni ɔda at prɔblɛm. Dɔn bak, dis sik kin apin afta sɔm ɔpreshɔn dɛn na yu at.
Wetin na di sayn dɛm fɔ dis? Si if yu pikin gɛt dɛn tin ya bak.
Dɛn sayn ya de dipen pan aw di tiub smɔl. Sɔmtɛm, if di stenosis rili smɔl (`mild stenosis`), i nɔ kin gɛt ɛni sayn at ɔl . Bɔt as di stenɔsis de wɔs, yu pikin kin sho tin dɛn lɛk:
- Fɔ fil lɛk se i at fɔ blo (`(Shortness of breath)`).
- Fɔ fil taya ɔltɛm (`(Fatigue)`).
- I kin tan lɛk se yu de blo fast fast , ɔ sɔntɛm yu de blo lawd wan.Yu tink se i tan lɛk dis? (`(I de blo ebi ɔ kwik)`).
- Yu at rit de fil lɛk se i de bit tumɔs ? (Rapid at rit).
- Ɛni swɛlin de na yu leg, yu anklɛ, yu fes, yu yaylid, ɔ yu bɛlɛ? (`(Swɛlin)`).
- Sɔntɛnde yu kin fil lɛk se yu de tɔn ɔ yu kin pas ? (`(Diziz ɔ pas aut)`).
- Yu lip, finga, ɛn fut finga dɛn kin tɔn blu ? Dis na wetin wi kin kɔl ``Cyanosis'' pan mɛrɛsin.
- Yu kin taya kwik we yu de ple wit ɔda pikin dɛn? Yu nɔ ebul fɔ rɔn ɛn jomp lɛk ɔda pikin dɛn? (`(Rɛdyus ɛksɛsayz tolɛreshɔn)`).
Mɛmba se, fɔ jɔs gɛt wan ɔ tu pan dɛn sayn ya nɔ min se yu gɛt di sik. Bɔt if yu pikin gɛt ɛni wan pan dɛn tin ya, i go fayn fɔ mek yu go to dɔktɔ.
Wetin mek dis pulmonary artery kin blok? Wetin na di tin dɛn we kin mek i apin?
sכm pikin dεn kin bכn wit dis kכndyushכn (Pulmonary Artery Stenosis), εn kin gεt prכblεm bak wit di valv dεm, di wכl dεm, כ כda pat dεm na di at. Ɔda pipul dɛn kin bɔn wit dis sik bɔt nɔr gɛt ɔda at prɔblɛm. Apat frɔm dat, dis sik kin apin afta dɛn dɔn ɔpreshɔn di at ɔ bikɔs ɔf ɔda tin dɛn we nɔ kin apin so ɔltɛm.
Di tin dɛn we kin mek pɔsin bɔn pikin
Ɔl togɛda, lɛk 40% pan di pipul dɛn kin bɔn wit dis sik (Pulmonary Artery Stenosis), bɔt dɛn nɔ gɛt ɔda at prɔblɛm.
כltu, bitwin 2% εn 3% pan di pipul dεm we gεt כda hat dεm we dεn bכn wit kin gεt dis kכndyushכn bak (Pulmonary Artery Stenosis). Na sɔm pan de prɔblɛm dɛn we kin apin to pɔsin in at:
- (Tetralogy of Fallot): Insay dis, di pikin kin gɛt 4 prɔblɛm dɛn wit in at, we kin mek di blɔd nɔ flɔ.
- (Pulmonary atresia): insay dis, di valv (pulmonary valve) bitwin di rayt vεntrikl na di at εn di pulmonary artery (pulmonary artery) nכ de fכm. So, blɔd nɔ de flɔ to di lɔng dɛn.
- (Truncus arteriosus): Na wan big blɔd vesel instead ɔf di tu we dɛn kin yuz. Dis kin mek blɔd we gɛt ɔksijɛn miks wit blɔd we nɔ gɛt ɔksijɛn.
- Aortic valve stenosis: Na prɔblɛm wit di valv we de na di men at we de kɛr blɔd frɔm di at to di bɔdi, we de ridyus di blɔd we de flɔ to di bɔdi.
- di atrial septal difεkt: na ol na di wכl bitwin di tu כp chεmba dεm na di at (di atria). Dis kin mek di blɔd we gɛt ɔksijɛn ɛn we nɔ gɛt ɔksijɛn miks.
- vεntrikul septal dεfekt: Na ol na di wכl we de sεparayt di tu lכw chεmba dεm (vεntrikul dεm) na di at. Dis kin mek tumɔs blɔd lik insay di lɔng dɛn.
- (Transposition of the great vessels): Di tu men blɔd vesel dɛm we de kɛr blɔd frɔm di at kin tɔn bak. Dis kin ambɔg di nɔmal blɔd flɔ ɛn i kin mek di ɔksijɛn nɔ rich di bɔdi in sɛl dɛn.
- (Patent daktus atεriɔs): .dis na kכnεkshכn bitwin di pikin in pulmonari at εn di men at we de kכri bכdi to di bכdi (di aorta). dis fכ klos afta dεn bכn am, bכt if i nכ de, tumכs bכdi go fכ fכlכ di lכng.
Ɔda rizin dɛn
Apat frɔm dis, sɔm ɔda rizin dɛn kin de:
- Rubella syndrome: If yu gɛt rubella we yu gɛt bɛlɛ, yu pikin kin gɛt at ɛn ɔda wɛlbɔdi prɔblɛm dɛn.
- (Williams syndrome): Dis kin mek difrɛn tin dɛn we nɔ fayn na di pikin in at ɛn ɔda pat dɛn.
- (Alagille syndrome): Dis kin mek yu gɛt prɔblɛm wit yu liva ɛn yu gɛt at sik.
- Takayasu’s arteritis: Dis na inflamɛns we de pwɛl big blɔd vesel dɛn.
- Sɔm prɔblɛm wit di we aw dɛn de push di pikin in pulmonari at fɔ go na do.
Di tin dɛn we kin mek pɔsin du ɔpreshɔn
Sɔm pipul dɛn kin gɛt dis sik afta dɛn dɔn du dɛn ɔpreshɔn. Fɔ ɛgzampul:
- Wan transplant we dɛn kin put na di lɔng.
- Ɔpreshɔn fɔ kɔrɛkt wan at prɔblɛm we dɛn bɔn wit pikin, ɔ fɔ mek blɔd flɔ fayn fayn wan na di at.
- Wan ɔpreshɔn we dɛn kɔl ``Pulmonary artery banding''. insay dis, dεn kin mek di at sכmtεm sכmtεm fכ ridyus di bכdi we de go na di lכng dεm.
Aw fɔ no bɔt dis sik?
we dכkta de egzamin yu pikin, dεn kin yεri wan abnכmal at sawnd (a ``murmur''). If na so, dɛn go ɔda fɔ mek dɛn du sɔm ɔda tɛst dɛn. Sɔm pan dɛn tin ya na:
- ilektrokardiogram - ECG כ EKG: dis de rεkכd di ilektrikal chenj dεm we de apin we di at de bit. I kin no di at bit we nɔ de bit ɔltɛm (ari at) ɛn strɛs pan di at mɔsul.
- X-ray na di chɛst: Dis kin sho di sayz ɛn shep fɔ di at, di lɔng dɛn, ɛn di at dɛn we de na di pulmonari.
- Echocardiogram: Dis tan lɛk pikchɔ we de muv di at. I de yuz sawnd wev fɔ luk di at mɔsul ɛn di valv dɛn.
- Cardiac magnetic resonance imaging (MRI): Dis na tri-dimensional (3D) imaging teknik we kin si aw blɔd de flɔ tru yu pikin in at ɛn blɔd vesel dɛn.
- (CT scan): Dis na `(X-ray)` tɛst bak. kכmpyuta de yuz wan siriכs `(X-ray)` pikchכ dεm fכ di pikin in at fכ mek kכros-sekshכnal vεyushכn dεm. wan spεshal day (`(IV contrast)`) dεn injεkt insay di at fכ luk di strכkchכ εn di bכdi fכ fכlכ di at.
- di kadyak kateshכn: insay dis prכsidכm, dεn kin put wan tin tכb (kateshכn) insay wan vein כ atεri εn gayd am insay di at. Dis kin mek di dɔktɔ ebul fɔ wach di ɔksijɛn lɛvɛl, di prɛshɔn we de chenj, ɛn tek ɛkstrem rayt na di at.
- Pulmonary angiography: Dɛn kin tek ɛkstrem rayt fɔ di pulmonary arteries ɛn veins na di at bay we dɛn yuz day.
- (Perfusion scan): Insay dis, dɛn kin injɛkt smɔl redioaktiv tin. Dɔn, dɛn kin yuz spɛshal mashin fɔ chɛk aw blɔd de flɔ fayn fayn wan na ɛni lɔng.
If yu dɔktɔ si se yu pikin gɛt Pulmonary Artery Stenosis, dɛn go rifer yu to wan dɔktɔ we de mɛn yu at. Dis kayn dɔktɔ gɛt di skil ɛn trenin fɔ no di kɔrɛkt we aw yu pikin gɛt at prɔblɛm, fɔ du ɛni tɛst we nid fɔ du, fɔ gi yu mɛrɛsin, fɔ du ɔpreshɔn pan yu at, ɛn fɔ chɛk yu pikin fɔ fala am . Dɛn kin du mɔ tɛst dɛn bak if nid de.
We yu de tɔk bɔt dis sik, yu dɔktɔ kin kɔl am Tayp I, II, III, ɔ IV. dis na klasification bays pan us pat dεm na di atεri dεn blכk εn aw bכku.
Wetin na di tritmɛnt dɛm fɔ dis? (Tritmɛnt)
Di bɛst tritmɛnt de dipen pan di sik dɛn we yu pikin gɛt ɛn ɔda tin dɛn. If wan ɔ mɔ branch dɛn na di pulmonari at de smɔl to smɔl, i nɔ go nid fɔ gɛt tritmɛnt . Bɔt if di smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl .
Di tritmɛnt dɛm fɔ `(Pulmonary Artery Stenosis)` na:
Balɔn dilayshɔn / Angioplasti
Insay dis, di dɔktɔ kin du:
- wan kateta we lεk balכn (balכn dilayshכn kateta) de insay di dakt we dεn blכk.
- Dɔn, dɛn kin tek tɛm, dɛn kin blo di balyɔn frɔm lɔw prɛshɔn to ay prɛshɔn.
- Dɔn da dakt de we dɔn blok kin big.
- Dɔn dɛn kin pul di briz na di balyɔn ɛn pul am.
Balɔn dilayshɔn ɛn stent ples (dɛn kin du dis mɔs) .
Insay dis, di dɔktɔ kin du:
- wan stent we dεn kin εkspεnd wit balכn (stεnt na sכm mεsh tyub) fכ opin di at we dεn blכk.
- Dɛn kin put dis stent oba wan balyɔn angioplasti kateta ɛn kɔba am wit wan swɛt.
- Dɛn de muf di stent to di rayt ples.
- Dɛn kin pul di kɔva we de na di stent-balɔn.
- Dɔn dɛn kin blo di balyɔn to di rayt prɛshɔn, ɛn dis kin mek di stent big ɛn mek i kɔntinyu fɔ stɔp de.
Wan spɛshal balyɔn we dɛn kɔl ``Di Kɔtin BalɔnTM``
Dis balyɔn jɔs tan lɛk balɔn we dɛn kin yuz ɔltɛm. Bɔt i gɛt sɔm smɔl smɔl bled dɛn along in lɔng. We di dɔktɔ inflayt di balyɔn, dɛn bled ya kin wok ɛn kɔt di say we dɔn blok. Dis kin mek i izi fɔ mek di tiub big, ɛn dis kin mek di tiub big.
Bɔrku pipul dɛm wae nɔr gɛt ɔda kayn hat sik wae dɛn bɔn kin gɛt gud rizɔlt wit dis prɔsidyu. Bɔt lɛk 21% pan pipul dɛn kin gɛt dɛn at we dɛn kin blok bak afta sɔm mɔnt.
Ɔpreshɔn
Di dɔktɔ dɛn we de du ɔpreshɔn kin yuz difrɛn we dɛn fɔ trit di pulmonary artery stenosis. Di tin we yu kin pik kin dipen pan di kayn we aw di blɔd de blo, di blɔd vesel dɛn we de rawnd am, ɛn ɔda tin dɛn we de apin.
Ɛni kɔmplikeshɔn de pan di tritmɛnt?
Balכn dilayshכn de ridyus di blכk na bכku pipul dεm. כltu, as tεm de go, di at kin blok bak bay 15% to 20%, εn dεn fכ ripit di prosidכs. Naw, pipul dɛn we de stɔdi bɔt difrɛn kayn balyɔn dɛn we go mek dɛn gɛt bɛtɛ tin fɔ du ɛn we go las fɔ lɔng tɛm.
Di prɔblɛm dɛn we kin apin we dɛn de dilayt di balɔn:
- Pulmonari atεri anεrizm.
- Pulmonary artery dissection (Pulmonary artery dissection) we de mek pɔsin nɔ ebul fɔ du am.
- Pulmonary artery rupture (`(Pulmonary artery rupture)`).
- Pulmonari εdima (`(Pulmonari εdima)`).
- Na smɔl tɛm nɔmɔ, pipul dɛn kin day.
Di prɔblɛm dɛn we kin apin we pɔsin yuz stent:
- Blɔd we de klɔt.
- di at ritm irεgulεriti dεm (`(Ventricular arrhythmias)`).
- Di stent kin misplace ɔ dislodged.
- fכ fכ mek di at big bak (dis kin apin sכmtεm sכmtεm).
Wetin na di bɛnifit dɛn we pɔsin kin gɛt we i de trit pɔsin?
Dɔktɔ dɛn kin lɛk fɔ put stent fɔ Pulmonary Artery Stenosis fɔ dɛn rizin ya:
- Dɛn kin wok lɛk 96% wantɛm wantɛm .
- I kin tek lɔng tɛm fɔ mek di at opin.
- Di say we smɔl kin big lɛk tu tɛm pas dat .
- I nɔ dia ɛn i kin wok pas fɔ jɔs put balyɔn insay ɔ du ɔpreshɔn.
- Mɔ sakrifays pas balyɔn angioplasty.
Dɔktɔ dɛn kin pik balyɔn angioplasty instead fɔ stent pan dɛn kayn tin ya:
- If di pikin in kɔndishɔn rili siriɔs .
- if di intanal strכkchכ fכ di pikin in bכdi kכmpleks (`(kכmpleks anatomi)`).
- If di pikin rili smɔl .
Wetin kin apin afta di ɔpreshɔn?
If yu pikin gɛt stent, i go nid fɔ tek antibayɔtik ɛn sɔntɛm tin fɔ mek blɔd tan fɔ sɔm tɛm. Dɛn kin gi dɛn mɛrɛsin ya fɔ mek i nɔ gɛt di sik ɛn fɔ stɔp di blɔd we de klɔt.
Aw kwik di pikin go fil fayn afta dɛn dɔn trit am?
di prכsεs fכ mek yu pikin in pulmonari atεri big de wok wantεm wantεm. Dis min se i kin izi fɔ yu pikin fɔ mek blɔd go insay in lɔng ɛn gɛt ɔksijɛn.
If mi pikin gɛt dis sik, aw tumara bambay go tan lɛk? (Prɔgnosis) .
Wit di advans tritmɛnt dɛm tide, bɔrku pipul dɛm wae gɛt dis sik kin liv te dɛn big. Bɔt pipul dɛm wae gɛt sik lɛk ``Williams syndrome'' ɛn ``Alagille syndrome'' nɔr kin ansa fayn fayn wan to tritmɛnt.
Ustɛm yu fɔ kɛr yu pikin go to dɔktɔ?
Yu go nid fɔ kɛr yu pikin go fɔ chɛk am ɔltɛm fɔ si aw dɛn de du. Yu go nid bak fɔ gɛt ɛkokardiogram ɔltɛm fɔ si if dɛn nid fɔ mek di at big bak tumara bambay.
Wetin a fɔ aks di dɔktɔ?
Yu kin aks di dɔktɔ kwɛstyɔn dɛn lɛk dɛn wan ya:
- Wetin mek mi pikin gɛt `(Pulmonary Artery Stenosis)`?
- Wetin na di bɛst tritmɛnt fɔ mi pikin?
- Wetin na di chans fɔ mek mi pikin nid fɔ gɛt tritmɛnt fɔ dis bak?
If yu pikin nid tritmɛnt fɔ Pulmonary Artery Stenosis, di dɔktɔ go tink bɔt di bɛst tritmɛnt fɔ yu pikin in kɔndishɔn. Nɔ shek fɔ aks kwɛstyɔn bɔt ɛnitin we yu nɔ ɔndastand bɔt aw yu pikin de du am.
Mɛsej we dɛn kin kɛr go na os
We i kam pan dis sik we dɛn kɔl `(Pulmonary Artery Stenosis)`, di tin we impɔtant pas ɔl na fɔ no di sik dɛn kwik kwik wan ɛn go to dɔktɔ . I impɔtant fɔ aks fɔ advays frɔm `(congenital heart specialist)`, mɔ if pikin dɛn gɛt dis sik.
Nɔ wɔri, tritmɛnt dɛn de fɔ dis . Dɛn kin kɔntrol dis sik wit tin dɛn lɛk we dɛn de mek di balyɔn, fɔ put stent, ɛn if nid de, ɔpreshɔn. Ivin afta dɛn dɔn trit di pikin, i rili impɔtant fɔ mek di pikin in wɛlbɔdi go de chɛk am ɔltɛm ɛn fala wetin di dɔktɔ tɛl am fɔ du . Tɔk to di dɔktɔ bɔt ɛni kwɛstyɔn ɔ tin we de mɔna yu.
` Pulmonary Artery Stenosis, Pediatric At Disease, Kɔnjɛnital At Difɛkt, Difikulti fɔ Brith, At Ɔpreshɔn, Stɛnt











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