We di dɔktɔ tɛl yu se yu smɔl pikin gɛt at sik we dɛn kɔl "Shone's Complex," yu kin fil shɔk, fred, ɛn kɔnfyus . I rili kɔmɔn. Sɔntɛm yu nɔ ɛva yɛri bɔt dis nem bifo. "Wetin na dis sik? Wetin go apin to mi pikin?" Yu go gɛt bɔku kwɛstyɔn dɛn na yu maynd. Nɔ wɔri. Lɛ wi tɔk bɔt dis simpul wan ɛn klia wan. Wetin na Shone in Kɔmpleks? Lɛ wi ɔndastand gud gud wan wetin i de du to di pikin.
Fɔ tɔk am simpul wan, wetin na dis Shone in Kɔmpleks?
Shone’s Complex na wan sik we dɛn kin bɔn wit at sik . wetin kin apin pan dis na dat, wan tin we de ambɔg de na mכr dan wan ples na di bכdi fכ fכlכ we de go na di lεft say na wi pikin in at. Imajin, di lɛft say na wi at na di wan we de tek di blɔd we gɛt ɔksijɛn ɛn klin na di lɔng ɛn pɔmp am go na di wan ol bɔdi. Jɔs lɛk wata motoka. Naw wetin kin apin if blok ɔ lɛsin de na dis blɔd we de flɔ? I kin at fɔ mek di at tek blɔd, ɛn i kin at fɔ pɔmp blɔd na di bɔdi. Na dat kin apin na Shone in Kɔmpleks.
Dɛn kɔl dis sik Shone’s Complex, afta di dɔktɔ we bin fɔs tɔk bɔt am. Pan ɔl we i bin no 4 at prɔblɛm dɛn we gɛt fɔ du wit am, dɔktɔ dɛn dɔn kam fɔ no naw se bɔku ɔda prɔblɛm dɛn de we gɛt fɔ du wit am.
Us at pwɛl hat kin gɛt fɔ du wit Shone’s Complex?
Fɔ mek dɛn no se pikin gɛt Shone’s Complex, i fɔ gɛt at le tu pan di et at prɔblɛm dɛn we wi go tɔk bɔt dɔŋ ya. Lɛ wi si wetin dɛn bi. Sɔm pan di wɔd dɛn kin tan lɛk se dɛn kɔmplikt smɔl, bɔt a go ɛksplen dɛn simpul wan.
| At Difɛkt | Fɔ tɔk am simpul wan, wetin kin apin wit dis? |
|---|---|
| Triad we gɛt at | wan ekstra mεmbran de fכm insay di כp lεft chεmba na di at (lεft atrium). dis de sheb di chεmba to tu pat, we de mek bכdi nכ fכ fכlכ insay di lכw chεmba (lεft vεntrikl). |
| Supravalvular mitral ring we de na di bɔdi | wan ring fכ fayv tisu de divεlכp jכs oba di mitral valv na di at. Dis kin mek di opin we di valv de opin tru, smɔl, ɛn dis kin mek di blɔd nɔ flɔ. |
| Parachute mitral valv | nכmal wan, tu mכsul dεm de (papillary muscles) we de εp di mitral valv fכ opin εn klos. Insay dis dɛfɛkt, na wan nɔmɔ de. I tan lɛk se dɛn gɛda ɔl di strɛch dɛn na parachute na wan ples. Dis kin mek di valv smɔl ɔ blɔd kin lik bak. |
| Hypoplastic lεft vεntrikl | "Hypoplastic" min se dεn nכ de divεlכp fayn fayn wan. na ya, di lεft vεntrikl, we na di men pכmp chεmba na di at, nכ de divεlכp fayn fayn wan. I smɔl. So i nɔ kin ebul fɔ pɔmp blɔd fayn fayn wan. |
| Subaortic stenosis we de mek pɔsin gɛt sik | εkstra tisu de bכlכp כnda di aorta valv, we de pכmp bכdi insay di aorta, we de mek di εria sכmtεm sכmtεm. Dis we aw di at kin smɔl kin mek i nɔ izi fɔ mek di at pɔmp blɔd. |
| Bikuspid aorta valv | nכmal wan, di aorta valv gεt tri flap dεm. Bɔt bebi dɛn we gɛt dis prɔblɛm kin gɛt tu nɔmɔ. Dis kin mek di valv smɔl ɔ lik blɔd. |
| Smɔl aorta valv anul | di strכng ring (anulus) we de rawnd di bכs pat pan di aorta valv de sכm sכm pas nכmal, so di bכdi we kin pas tru di valv go insay di aorta de rεdכks. |
| Kכarktεshכn na di aorta | We di aorta, we na di men blɔd vesel we de kɛr blɔd go na di bɔdi, we smɔl, dat kin mek di at wok tranga wan fɔ pɔmp blɔd tru di say we smɔl. |
Di impɔtant tin na dat if tu ɔ mɔ pan dɛn et tin ya we nɔ fayn, na wetin dɔktɔ dɛn kin kɔl Shone’s Complex. Bɔku tɛm, wan tin kin de we kin ambɔg yu we yu de go insay ɛn wan tin kin ambɔg yu we yu de kɔmɔt.
Wetin na di sayn dɛm if mi pikin gɛt dis sik?
Sɔm pikin dɛn we gɛt dis sik, if i tranga, dɛn kin bigin fɔ sho di sik lɛk aw dɛn bɔn dɛn . dis na biכs di pikin in at nכ ebul fכ pכmp inof bכdi na di bכdi. Bɔt sɔntɛnde, di sayn dɛn kin apin we i smɔl ɔ ivin we i yɔŋ.
Luk fɔ dɛn sayn ya na yu pikin:
- I nɔ izi fɔ gɛt wet: Nɔ fɔ gɛt wet fayn.
- Fɔ fil taya we yu de drink milk: Afta yu dɔn drink sɔm milk, yu kin bigin fɔ swet ɛn i nɔ kin izi fɔ yu fɔ blo.
- di urine we de kכmכt dכn: I de pas lεs urine pas aw i nכmal.
- Wik puls: Di puls kin rili wik, mɔ na di an ɛn fut.
- Difrɛns pan blɔd prɛshɔn bitwin an ɛn leg: Blɔd prɛshɔn na di an kin ay pas di leg.
- Akyumyuleshכn כf laktik asid na di bכdi.
If yu pikin gɛt wan ɔ mɔ pan dɛn sik ya, i rili impɔtant fɔ tɔk to yu dɔktɔ kwik kwik wan.
Wetin mek dis bin apin to mi pikin? Wetin na di rizin we mek dis de apin?
Naw yu kin de wɔnda, "Wetin mek dis apin to mi pikin? Na mi fɔlt?" Fɔ tru, dɔktɔ dɛn nɔ dɔn fɛn ɛni patikyula rizin yet fɔ dis. Bɔku tɛm, i kin apin wan wan tɛm. Wi stil nɔ gɛt inof infɔmeshɔn fɔ tɔk fɔ tru if na jenɛtik ɔ envayrɔmɛnt factor.
Pan ɔl we sɔm risach dɛn dɔn sho se i kin kɔmɔt frɔm dɛn mama ɛn papa, di we aw dɛn kin pas am insay famili dɛn rili kɔmpleks. So wi nid fɔ du mɔ risach fɔ ɔndastand dis gud gud wan.
So duya mɛmba se, dis nɔto yu fɔlt. Wi nɔ gɛt ɛni kɔntrol pan dɛn tin ya.
Wetin na de prɔblɛm wae kin kam wit dis sik?
Shone’s Complex kin mek sɔm kɔmplikɛshɔn, na dat mek fɔ trit kwik kwik wan ɛn fɔ wach am fɔ lɔng tɛm impɔtant.
- Pulmonary hypertension: Na abnɔmal inkris na di blɔd prɛshɔn na di blɔd vesel dɛm we de kɛr blɔd go na di lɔng.
- At ritm dεm we nכ nכmal: At ritm dεm we nכ de rεgulεr.
- At nɔ de wok fayn: Na tin we de mek di at nɔ ebul fɔ pamp inof blɔd to di bɔdi.
Aw dɔktɔ dɛn kin fɛn dis?
Dɔktɔ dɛn kin yuz bɔku tɛst fɔ no if pɔsin gɛt dis sik.
- Fetal echocardiogram: dis na spεshal skan we dεn kin du we di pikin stil de na di bεlε. I kin no if pɔsin gɛt at prɔblɛm bifo dɛn bɔn di pikin.
- Transthoracic echocardiogram (TTE): Na ɔltra saund skan fɔ di at we dɛn kin du afta dɛn bɔn di pikin. Dɛn kin yuz dis tɛst mɔ fɔ no di sik we dɛn kɔl Shone’s Complex.
- Cardiac CT scan or MRI: Dɛn nɔ kin du dɛn tin ya fɔ ɔlman, bɔt sɔm tɛm dɛn de, dɛn tɛst ya kin ɛp fɔ gi mɔ dip infɔmeshɔn bɔt aw di at tan.
Bɔrku tɛm, dɛn kin no dis sik bifo ɔ afta dɛn bɔn am. Bɔt sɔntɛnde, dɛn kin no di sik fɔs we dɛn smɔl ɔ we dɛn yɔŋ, we di sayn dɛn nɔ kin rili bad ɛn nɔ kin so bad. Insay dɛn kayn tin ya, dɔktɔ kin rifer fɔ mek dɛn du ɔda tɛst bikɔs ɔf wan abnɔmal sawnd (at grɔmbul) we dɛn kin yɛri we dɛn de lisin to di at.
Wetin na di tritmɛnt dɛm fɔ dis?
Di wangren we fɔ trit Shone’s Complex na fɔ ɔpreshɔn . Naw, no mɛrɛsin nɔr de we go mɛn dis sik. Bɔt di dɔktɔ kin gi am mɛrɛsin fɔ kɔntrol di pikin in sik ɛn sɔpɔt di at fɔ wok te dɛn du di ɔpreshɔn.
No patikyula ɔpreshɔn nɔ de fɔ dis. Bifo dat, di dɔktɔ dɛn go disayd us ɔpreshɔn fɔ du bay we dɛn fala us at prɔblɛm yu pikin gɛt ɛn aw in at de wok fayn.
Yu pikin kin nid fɔ du wan ɔ mɔ pan dɛn ɔpreshɔn ya:
- di rimobul fכ di ekstra tisu ring we de rawnd di mitral valv.
- Mitral valv ripair.
- Mitral valv riplesmεnt (dis nכ kin kכmכn sכmtεm).
- fכ pul di εksyכs tisu dεm we de dכn di aorta valv.
- di opin we di aorta valv de opin.
- Ripair wan pat we dɔn smɔl na di aorta.
Di we aw dɛn kin du ɔpreshɔn
Sɔntɛnde dɔktɔ dɛn kin du dis bay we dɛn de du am stej . Dat min se, dɛn nɔ de du di ɔpreshɔn wan tɛm. Dɛn kin du am insay tu pat, ɛn sɔm tɛm dɛn kin sheb am. Fɔ ɛgzampul, di fɔs ɔpreshɔn kin pul di blɔk we de na di we aw blɔd de kɔmɔt na di at. Dɔn, di sɛkɔn ɔpreshɔn de pul di blɔk we de na di we aw blɔd de flɔ insay di at. Yu dɔktɔ go ɛksplen to yu ustɛm ɔmɔs ɔpreshɔn yu pikin go nid ɛn ustɛm i go fayn fɔ du am.
Wetin na di pikin in layf tumara bambay ɛn di prɔgnosis?
Di pikin in layf ɛn wɛlbɔdi tumara bambay dipen pan sɔm tin dɛn:
- Aw di sik kin tranga: Aw di at pwɛl hat kin tranga.
- Spid fɔ tritmɛnt: Aw dɛn kin bigin fɔ trit am kwik kwik wan.
- Kɔmplikeshɔn: If ɔda kɔmplikeshɔn go apin ɔ nɔ go apin.
- Prɔblɛm dɛn we kin kam bak: Yu tink se di at prɔblɛm dɛn we dɛn bin dɔn trit bifo tɛm go kam bak as tɛm de go?
fכ egzampl, tin dεm lεk we di aorta kכrekt kin kam bak as tεm de go. So, as yu pikin de ol, i go nid fɔ du mɔ ɔpreshɔn. Yu dɔktɔ go gi yu mɔ infɔmeshɔn bɔt dis dipen pan aw yu pikin in kɔndishɔn.
Bɔku stɔdi dɛn dɔn sho se di nɔmba fɔ pipul dɛn we kin liv fɔ lɔng tɛm afta dɛn dɔn du di ɔpreshɔn pas 75%, we kin rich 20 ia . Dat min se tri pan ɔl 4 pikin dɛn kin liv fayn ɛn gɛt wɛlbɔdi afta dɛn dɔn trit dɛn.
Yu kin gɛt wan tawzin kwɛstyɔn dɛn na yu maynd afta yu dɔn yɛri bɔt aw yu pikin gɛt di sik. Dat na rili nɔmal tin. Rayt di kwɛstyɔn dɛn we kin kam na yu maynd insay wan notbuk. We yu go si di dɔktɔ, aks dɛn ɔl. Yu pikin in mɛdikal tim go ɛksplen ɔl dis to yu ɛn gayd yu fɔ no wetin fɔ du nɛks.
Mɛsej we dɛn kin kɛr go na os
- Shone’s Complex na wan sik wae nɔr kin bɔrku wae kin kam wit hat sik wae kin mek blɔd nɔr de go na di lɛft say na di at.
- Fɔ mek dɛn no se pikin gɛt dis sik, i fɔ gɛt at le 2 pan 8 patikyula at prɔblɛm dɛn.
- Di wangren tritmɛnt fɔ dis na ɔpreshɔn. Bɔku tɛm, ɔpreshɔn kin wok fayn.
- Afta dɛn dɔn du di ɔpreshɔn, di pikin go nid fɔ fala am fɔ ɔl in layf wit dɔktɔ we de mɛn di at. Nɔ mis ɛni wan pan dɛn apɔntinmɛnt dɛn ya.
- Di tin we impɔtant pas ɔl na dat dis tin we apin nɔto yu fɔlt ɔ yu patna in fɔlt. Nɔ wɔri bɔt am.

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