Sɔntɛnde na wi layf, strenj tin dɛn kin apin, nɔto so? Yu dɔn ɛva yɛri bɔt wan sik we pɔsin in bɔdi, in swet, in briz, ɔ in urine kin smɛl lɛk fish we dɔn rɔtin? I tan lɛk se i strenj, nɔto so? Bɔt, dis kayn kɔndishɔn rili de. Dis na di kɔndishɔn we wi go tɔk bɔt tide, Trimethylaminuria, ɔ `(TMAU)` fɔ shɔt. Sɔm pipul dɛn kin kɔl am bak ``Fish Odor Syndrome``.
Wetin na trimethylaminuria (TMAU)?
Fɔ tɔk am simpul wan, trimethylaminuria (TMAU) na wan sik we de mek pɔsin in bɔdi de wok fayn . Naw yu kin de wɔnda wetin na mɛtabolik disɔda. Insay wi bɔdi, kemikal prɔses, ɔ mɛtabolik prɔses , kin apin fɔ chenj di it we wi de it to ɛnaji ɛn fɔ mek di tin dɛn we wi bɔdi nid. di εnzym dεm na wi bכdi de εp dεn prכsεs dεm ya fכ apin fayn fayn wan. so, insay dis kכndishכn we dεn kכl trimethylaminuria, bikoz fכ chenj na di aktiviti fכ wan sכm εnzym, sכm pan di kεmikכl dεm we dεn prodyuz na di bכdi nכ kin brok dכn fayn fayn wan. Na dat mek da fish smel we nɔ fayn de kɔmɔt frɔm swet, briz, saliva, ɛn urine.
Yu kin dɔn yɛri dɔktɔ dɛn kin kɔl dis sik `(TMAU)` ɔ `(Fish Odor Syndrome)`. No kɔmplit mɛrɛsin nɔ de fɔ dis yet . Bɔt, nɔ wɔri. Yu kin ridyus dɛn sik ya bɔku bɔku wan bay we yu chenj wetin yu de it ɛn drink, yuz sɔm sop ɛn loshan dɛn, ɛn kɔntrol yu strɛs .
Wetin na di men kayn `(TMAU)`?
Tu men kayn trimethylaminuria de:
1. Praymari Trimethylaminuria : Dis na di kayn we we pɔsin kin bɔn wit . dis min se dis kכndyushכn de kכz fכ sכm chenj dεm (`(Jεnεtik mכtεshכn)`) insay di jin dεm (`(Jεn)`) we dεn gεt frכm di mama εn di papa.
2. Sεkɔndari Trimethylaminuria : Dis kin apin leta na layf . Dis fishy smel kin bi bikɔs ɔf sɔm mɛrɛsin ɔr it supamakit.
Aw dis sik kin kɔmɔn?
Infakt, TMAU na wan sik we nɔ kin apin so ɔltɛm . Wan stɔdi sho se na wan pan ɔl 200,000 to wan milyɔn pipul dɛn nɔmɔ i kin afɛkt ɔlsay na di wɔl. Bɔt dɛn kin tɔk bak se uman dɛn kin gɛt am smɔl pas man dɛn.
Bɔt sɔm pipul dɛn we de du risach biliv se sɔntɛm pipul dɛn we gɛt `(TMAU)` go bɔku na di sosayti pas aw dɛn statystik ya sho. Na bikɔs bɔku pipul dɛn kin tink se dis na prɔblɛm we de wit dɛn yon klin layf . So, dɛn nɔ kin tɛl ɛnibɔdi bɔt am ɔ go to dɔktɔ bikɔs dɛn shem. So, dɛn nɔ kin gɛt diagnosis (`(Diagnosis)`).
Wetin na di sayn dɛm fɔ trimethylaminuria?
Di men ɛn klia sayn na we yu bɔdi de smɛl lɛk fish, yu de blo, ɛn yu de swet . Sɔntɛnde, dis smel kin so nɔ fayn dat i kin mek pɔsin nɔ fil fayn. Fɔ sɔm pipul dɛm, i kin kam bak wit bad briz (`(Halitosis)`) ɛn wan strɔng smel frɔm di urine.
Sɔmtɛm, pɔrsin wae gɛt `(TMAU)` kin fil dis smɛl pasmak wae dɛn de swet ɔr wae dɛn strɛs. Bɔt fɔ sɔm pipul dɛn, dis smel kin so strɔng dat ilɛksɛf dɛn go insay rum usay dɛn de, tinap nia di kɔwnta na stɔ, ɔ sidɔm na di sem say na bɔs ɔ tren, ɔda pipul dɛn kin stil smɛl am. Imajin aw i at fɔ du dat.
Wetin na di tin dɛm we de mek `(TMAU)`?
trimethylaminuria de apin we di fכnshכn fכ wan εnzym we dεn kכl `(FMO3)` na wi bכdi de pwεl. `(FMO3)` tinap fכ Flavin- we gεt monooxygenase 3. di men wok we dis εnzym de du na fכ kכntro di kεmikכl we dεn kכl `( Trimethylamine )` we de prodyuz na wi bכdi. Dis trimethylamine na in de mek da fishy smel de. Dis trimethylamine kin kɔmɔt we sɔm it dɛn we wi kin it, fɔ ɛgzampul, fish, bins, ɛn eg, kin digest.
wetin kin apin na dis: we trimethylamine de bכlכp na wi bכdi, di εnzym `(FMO3)` de kam εn brok am dכn, tכn am to kεmikכl we nכ de smεl. Dɔn, pan ɔl we i de pas frɔm wi dijestiv sistɛm ɛn go insay wi blɔd, i nɔ de smɛl.
bכt, wetin kin apin if dat `(FMO3)` εnzym nכ de wok fayn? Dat trimethylamine we de smɛl kin bɔku na wi bɔdi. We i bɔku, i kin dɔn kɔmɔt insay swet, briz, saliva, ɛn urine, ɛn da fish smel de kin kɔmɔt. Yu ɔndastand?
Pipul dεm we gεt praymar trimethylaminuria (`(Primary TMAU)`) de divεlכp dis kכndyushכn biכs dεn de inhεrit abnכmal kכpi dεm fכ di jin dεm we de mek di `(FMO3)` εnzym (`(Abnormal FMO3 genes)`) frכm dεn mama εn papa.
insay sεkכnd trimethylaminuria (`(Sεkכndari TMAU)`), yu `(FMO3)` εnzym nכ de ebul fכ brok dכn trimethylamine fכ sכm כda rizin. Dis kin bi bikɔs ɔf:
- If yu gɛt mɛrɛsin, lɛk we yu liva nɔ wok ɔ we yu gɛt vayral ɛpatitis , i kin ambɔg di ɛnzaym in wok ɛn mek i nɔ brok di trimethylamine.
- if yu gut maykrobayom nɔ de balans, we min se i nɔ balans bitwin di gud ɛn bad baktri dɛm na yu gut, tumɔs trimethylamine kin bil. Dɔn di ɛnzaym (FMO3) nɔ kin ebul fɔ pul ɔl da smel de.
- If yu tek supamakit we gɛt kɔlin ɔ kanitin , dɛn tin ya kin ɛp fɔ mek trimethylamine.
Wetin na de prɔblɛm wae kin kam wit dis sik?
Aw wan sik wae dɛn kɔl trimethylaminuria kin afɛkt yu kwaliti fɔ liv(`(Kwaliti fɔ layf)`) kin rili damej. Risach dɔn sho se pipul dɛm wae gɛt dis sik kin avɔyd fɔ gɛt padi biznɛs, woke, ɛn fɔ de wit ɔda pipul dɛm bikɔs dɛn kin fred se ɔda pipul dɛn go notis di smel we nɔ fayn. Bikɔs ɔf dis, pipul dɛm wae gɛt dis sik kin gɛt difrɛn kayn maynd wɛl bɔdi prɔblɛm. Fɔ ɛgzampul:
- Anxiety (`(Wan wɔri)`) .
- Pwɛl at
- Wɔri ɛn fred we nɔ gɛt sɛns (`(Paranoia)`)
Pan ɔl we i nɔ kin apin so ɔltɛm, dɛn dɔn ripɔt se sɔm pipul dɛn we gɛt TMAU kin tink bɔt fɔ kil dɛnsɛf (`(Suicidal behavior)`). Dis de sho aw siriɔs di saykilɔjik impak we dis kɔndishɔn kin gɛt kin bi.
Aw dɛn kin no se pɔsin gɛt trimethylaminuria?
Dɔktɔ dɛn kin no se yu gɛt TMAU bay we dɛn de mɛzhɔ di kayn trimethylamine we de na yu urine. Dis kin bi tru wan urine test . pan tap dat, yu dכkta kin rεkomεnd fכ du jεnεtik tεst fכ no if yu gεt di praymar (i.e., congenital) כ sεkכnd (i.e., acquired) fכm.
Wetin na di tritmɛnt fɔ trimethylaminuria?
Yu dɔktɔ kin tɛl yu difrɛn tin dɛn fɔ ɛp fɔ ridyus di sayn dɛm fɔ TMAU.
- Di it: I fayn fɔ pul sɔm it dɛn we de mek di bɔdi gɛt di kemikal we de mek di sik (TMAU) bɔku.
- Speshal sop ɛn loshan: I fayn fɔ yuz spɛshal sop ɛn loshan we de ɛp fɔ ridyus di fish smel we de kɔmɔt na di skin.
- Mɛrɛsin: Sɔntɛnde, dɛn kin gi yu mɛrɛsin bak.
- Mental hεlth sɔpɔt: Dɛn kin advays yu bak fɔ go to saykilɔjik kɔyl fɔ ɛp yu fɔ bia wit de strɛs wae dis sik kin kam wit.
Us kayn it dɛn fɔ pul kɔmɔt?
If yu gɛt trimethylaminuria, dɔktɔ dɛn kin tɛl yu fɔ stɔp ɔ avɔyd dɛn it ya ɔl:
- Fish ɛn ɔda sifud dɛn (espɛshali fish dɛn we de na sɔl wata) .
- Eg (especially eg yolk) .
- Liva ɛn ɔda animal dɛn insay pat
- Ligim lɛk soya bin, chikip, ɛn lentil
- Krɔs vɛjitebul dɛn lɛk kabij, brɔkoli, kɔliflawa, ɛn Brussels sprouts
- Pinat
- Milk ɛn dairy prodakt (fɔ sɔm) .
- Fɔd ɛn nyutrishɔn sɔpɔtmɛnt dɛn we gɛt bɔku bɔku kɔlin ɛn L-kanitin
Impɔtant: Nɔto ɔlman nid fɔ pul ɔl dɛn it ya. I bɛtɛ fɔ tɔk to dɔktɔ ɔ pɔsin we sabi bɔt it fɔ no us it dɛn we fayn fɔ yu.
Wetin na di mɛrɛsin dɛm we dɛn kin gi fɔ `(TMAU)`?
Yu dɔktɔ kin gi yu mɛrɛsin lɛk dis fɔ ridyus di sayn dɛm fɔ TMAU:
- Antibayɔtik ɛn probayotik : Dɛn mɛrɛsin ya kin ɛp fɔ ridyus di bɔdi we de na yu intestinal, ɛn dis kin mek di trimethylamine nɔ bɔku.
- Activated charcoal : Dis tan lɛk spɔnj. I de absɔb trimethylamine na di bɔdi ɛn ɛp fɔ mek i kɔmɔt na di stɔl.
- Antidipreshan ɛn anti-anxiety mɛrɛsin : Dɛn kin gi dɛn mɛrɛsin ya fɔ trit mɛntɛl hεlth prɔblɛm wae sɔm pipul dɛm wae gɛt TMAU kin gɛt.
Yu dɔktɔ kin rifer yu bak to mental wɛlbɔdi sɔpɔt . Fɔ tɔk to pɔsin we de stɔdi bɔt pɔsin in maynd ɔ pɔsin we de gi advays, impɔtant mɔ if yu de sɔfa wit prɔblɛm dɛn we yu de tink bɔt yusɛf ɛn aw yu de si yu bɔdi. Saykotɛrapi kin ɛp yu fɔ lan aw fɔ bia wit yu sik ɛn kɔntrol strɛs.
Wetin pɔsin we gɛt trimethylaminuria kin ɛkspɛkt?
Trimethylaminuria na wan sik we nɔ de mɛn . Dis min se i nɔ go ebul fɔ wɛl ɔl ɔ i nɔ go bɛtɛ fɔ insɛf. Bɔt lɛk aw wi bin dɔn tɔk, tritmɛnt ɛn tin dɛn de we yu kin du fɔ ridyus di sayn dɛm fɔ TMAU ɛn ridyus di impak we di sik gɛt pan yu layf.
Aw a kin kia fɔ misɛf?
Fɔ kia fɔ yusɛf rili impɔtant we yu de liv wit TMAU. Na sɔm tin dɛn we yu fɔ tink bɔt:
- Pɔsin in yon hajɛns : If yu yuz sop ɛn loshan we gɛt smɔl `(pH)` valyu, i kin ɛp fɔ ridyus yu bɔdi smel. Aks yu dɔktɔ wetin `(pH)` valyu we rayt fɔ yu ɛn us prɔdak dɛn bɛtɛ.
- Tek tɛm wetin yu de it : Bɔku it kin mek trimethylaminuria wɔs. Tɔk to pɔsin we sabi bɔt it fɔ plan yu it ɛn it we yu go pik so dat yu go gɛt di tin dɛn we yu nid.
- Manej strɛs : We yu strɛs bɔku, dat kin mek di sayn dɛm fɔ TMAU bɔku. So, aks yu dɔktɔ bɔt aw fɔ ɛp fɔ ridyus yu strɛs. (e.g., meditashɔn, yoga, ɛksesaiz fɔ blo)
- Fɛn sɔpɔt : Trimethylaminuria na wan sik wae nɔr kin bɔrku, so yu kin fil lɛk yu wan ɛn yu kin fil lɛk yu nɔr de nia ɔda pipul dɛm. So, e kin bi big ɛp fɔ kɔnɛkt wit sɔpɔt grup dɛm usay dɛn kin fɛn ɔda pipul dɛm wae gɛt di sem sik .
Ustɛm a fɔ go to mi dɔktɔ?
If yu sik nɔr de bɛtɛ ivin afta yu dɔn chenj yu it ɛn aw fɔ mɛn yu strɛs, mek shɔ se yu go to yu dɔktɔ. I kin tɔk bɔt ɔda tritmɛnt dɛn we yu go tink bɔt.
Us kwɛstyɔn dɛn a fɔ aks mi dɔktɔ?
Bikɔs trimethylaminuria na wan sik we nɔ kin apin so, yu nɔ go no bɔku tin bɔt am. Na sɔm kwɛstyɔn dɛn we yu kin aks yu dɔktɔ:
- Wetin mek a bin gɛt dis kayn tin?
- Wetin na di bɛst tritmɛnt dɛn we yu kin advays fɔ mi?
- Yu kin rɛkɔmɛnd wan sɔpɔt grup ɔ program usay a go ebul fɔ gɛt ɛp?
Pipul wae gɛt trimethylaminuria kin smɛl dɛnsɛf?
Dis na prɔblɛm bak fɔ bɔku pipul dɛn. Yes, wi kin smɛl wi yon swet ɛn bɔdi ɔda, ɛn pipul dɛn we gɛt `(TMAU)` kin smɛl dɛn yon smel. Bɔt sɔntɛnde, we dɛn dɔn yus to dɛn yon smel, dɛn nɔ kin notis am tranga wan lɛk ɔda pipul dɛn. Dɔn bak, nɔto ɔlman kin se dɛn nɔ de smɛl am; sɔm pipul dɛn nɔ kin ivin notis se dɛn bɔdi gɛt wan ɔda smel we nɔ kɔmɔn.
Fɔ dɔn, di mɛsej we impɔtant pas ɔl
Trimethylaminuria na wan sik wae kin rili mek pɔrsin nɔr kin ebul fɔ du natin, nɔr to na in bɔdi nɔmɔ, bɔt na in maynd bak . Ivin if i nɔr de mek yu bɔdi fil pen, i kin mek yu fil pen ɛn gɛt skata na yu maynd. Sɔm pipul dɛm wae gɛt dis sik kin de fa frɔm di sosayti ɛn tray fɔ de fa frɔm ɔda pipul dɛm, ɛn dɛn kin fred se dɛn go de mɔna ɔda pipul dɛm. Ivin afta dɛn dɔn chenj dɛn it ɛn fala ɔda advays, sɔm pipul dɛn we gɛt `(TMAU)` kin fil se dɛn stil nid fɔ kip dɛn layf fa frɔm ɔda pipul dɛn. Dis kayn soshal ayzolayshɔn kin mek yu gɛt tin dɛm lɛk pwɛl hat ɛn wɔri.
Mɛmba se nɔto yu wangren de . If yu de sɔfa wit dis sik, duya nɔ shem ɔ fred fɔ aks yu dɔktɔ fɔ ɛp yu. Dɛn kin ɔndastand wetin yu de go tru ɛn dɛn kin tɛl yu bɔt program ɛn savis dɛn we go ɛp yu. Yu maynd wɛlbɔdi impɔtant jɔs lɛk aw yu bɔdi impɔtant. So mek shɔ se yu tink bɔt am bak.
` trimethylaminuria, fish odor sindrom, fish odor sindrom, bodi odor, mεtabolik sik dεm, FMO3 εnzym, trimethylamine











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