Yu dɔn ɛva fil sɔntin lɛk lump we de gro ɛn big sɔmsay na yu bɔdi? Sɔntɛnde, fɔ no rizin, yu kin gɛt swel ɔ swɛla na yu an ɔ yu leg. Pan ɔl we bɔku tɛm wi nɔ kin pe atɛnshɔn tumɔs to dɛn tin ya, sɔntɛm sɔntin we siriɔs ayd biɛn dɛn. Tide, wi go tɔk bɔt wan spɛshal kayn kansa we bɔku pipul dɛn nɔ kin yɛri bɔt bɔku tɛm, bɔt i rili impɔtant fɔ mek wi ɔl no bɔt. Nɔ fred, lɛ wi ɔndastand dis simpul wan.
Wetin na ``Undifferentiated Pleomorphic Sarkoma - UPS''?
Fɔ tɔk am simpul wan, ``Undifferentiated Pleomorphic Sarcoma'' ɔ ``UPS'' as wi kin kɔl am fɔ shɔt, na wan kayn kansa we dɛn kɔl sɔft tisu sarkoma . Dis na we kansa sɛl dɛn kin fɔm na di sɔft tisu dɛn na wi bɔdi, lɛk di mɔsul dɛn, di fat tisu dɛn, ɛn di blɔd vesel dɛn.
כltu, dis `(UPS)` de stat na di sכft tisu dεm na yu an כ yu leg dεm . sכmtεm i kin apin bak na di dip pat na di bak pat na di bכdi, we dεn kכl di `retroperitoneum` . na sכm tεm, dis `(UPS)` de afekt di bon dεm. Di tin we sɔri na dat, dis kin bi wan kayn kansa we kin rili bad . So i kin izi fɔ mek i go na ɔda pat dɛn na di bɔdi, mɔ di lɔng dɛn ɔ di limf no dɛn .
trade, dεn bin de kכl dis `(UPS)` `malignant fibrous histiocytoma` . di rizin fכ dis na biכs di risach dεm bin tink se dis kεnsar de kכmכt fr כm spεshal imyun sεl dεm we dεn kכl `histiocytes` . כltu, leta risεch fכnshכn se i mכst lεk fכ bigin insay sεl dεm we dεn kכl `mεsenchymal sεl`, we de mek di kכnektiv tisu na wi bכdi.
Naw lɛ wi luk wetin di tu wɔd dɛn we de insay dis nem min.
"Undifferentiated" min se dεn kεnsar sεl dεm ya de tek wan rili chaotic, disorganized appearance . Lɛk tɔys dɛn we skata rawnd we nɔ gɛt ɛni ɔda. Dɛn dɔn so difrɛn ɛn nɔ machɔ so i nɔ pɔsibul fɔ no ustɛm dɛn bigin fɔ gɛt wɛlbɔdi sɛl dɛn ɔ us wok dɛn bin want fɔ du.
di wכd "pleomorphic" min se dεn sεl dεm ya difrεn in shep, saiz, כ di nyuklios, we na di kכntrol sεntr fכ di sεl . Tink bɔt am lɛk fɔnicha we dɛn nɔ mek wit di sem mol, ɛni wan pan dɛn gɛt difrɛn shep ɛn saiz. Sɔm sɛl dɛn smɔl, sɔm big. Sɔm dɛn rawnd, sɔm dɛn lɔng. Ivin di nyuklios we gɛt di kromozom dɛn we de insay di sɛl dɛn, difrɛn na ɛni sɛl. Dis na di rizin we mek dɛn kansa sɛl ya de gro rili irɛgyula ɛn kwik kwik wan we dɛn nɔ gɛt ɛni kɔntrol.
UPS na rili wan kayn kansa we nɔ kin bɔku . Fɔ ɛgzampul, na Amɛrika, dis sik nɔ kin pas 5,000 pipul dɛn insay wan ia. Bɔt pan di kayn sɔft tisu sarkoma, .Apat frɔm di liposarcoma (wan kansa we de divɛlɔp na di fat tisu) ɛn leiomyosarcoma (wan kansa we de divɛlɔp na di smol mɔsul), (UPS) na di tɔd kayn sɔft tisu sarkoma .
Wetin na di simptom dɛm fɔ `(UPS)`?
Di sayn dɛm fɔ `Undifferentiated Pleomorphic Sarcoma (UPS)` kin difrɛn frɔm wan pɔsin to ɔda pɔsin. Sɔm pipul dɛn nɔ kin gɛt ɛni sayn. Bɔt sɔm sayn dɛn de we kin apin:
- Lump ɔ mas we de gro smɔl smɔl: Dis na di men sayn. I kin fil lɛk wan lump ɛnisay na di bɔdi, mɔ na an, leg, ɔ bɛlɛ.
- Lump we nɔ gɛt pen we kin muv ɔ nɔ kin muf we yu tɔch am: Bɔku tɛm, dɛn lumps ya nɔ kin mek yu fil pen we yu bigin. So, sɔm pipul dɛn nɔ kin pe atɛnshɔn to dɛn bɛtɛ.
- Numbness ɔ bɔn senseshɔn bikɔs di tumor de prɛs pan wan nerve: Sɔntɛnde, as dis tumor de gro, i kin pres pan wan nerve we de nia am. Dis kin mek yu an ɔ fut nɔ gɛt bɛtɛ trɛnk, yu kin fil lɛk yu de swɛt, ɔ yu kin bɔn.
- Swel na yu an ɔ yu leg: If yu an ɔ yu leg swel fɔ no rizin, dɛn fɔ tink bɔt dat bak.
Impɔtant tin na dat, UPS nɔ kin sho klia sayn ɔltɛm. Bɔku tɛm dɛn nɔ kin gɛt pen , ɛn nɔ chenj nɔ kin chenj na di skin oba di lump (lɛk we di kɔlɔ chenj ɔ we i gɛt sɔri). Dɔn bak, dɛn nɔ kin si di kɔmɔn sayn dɛm lɛk fiva, we yu de lɔs yu wet, ɛn we yu nɔ de fil fayn.
Wetin na di tin dɛm we de mek `(UPS)`?
Di masta sabi pipul dɛn stil nɔ no bɛtɛ bɛtɛ wan wetin kin mek pɔsin gɛt UPS. wetin dεn no na dat, i de kכz fכ chenj (mכtεshכn) na di DNA (di mכlikul we gεt wi jεnεtik infכmeshכn) fכ hεlty sεl dεm. Bɔt wetin kin mek dɛn chenj dɛn de na DNA nɔ klia yet.
Risk Factors We De Inkrisayz di Risk fɔ Divɛlɔp UPS
Risk factor na sɔmtin wae de mek pɔrsin gɛt mɔr sik. Bɔku risk factor dɛm de we dɛn dɔn no fɔ `(UPS)`. Bɔt mɛmba se nɔto ɔlman we gɛt dɛn risk factor ya go gɛt `(UPS)`, ɛn dɛn nɔ go se pipul dɛn we nɔ gɛt ɛni wan pan dɛn risk factor ya nɔ go gɛt `(UPS)`.
Di risk factor dɛm wae dɛn dɔn no naw na:
- Fɔ bi man: Man dɛn kin gɛt dis sik pas uman dɛn, ɛn di risk kin rili bɔku pan wayt man dɛn.
- Ɔva 50 ia: De pɔrsin wae gɛt dis sik kin bɔku wae pɔrsin de ol.
- Sɔm kayn mɛrɛsin: Fɔ ɛgzampul, pipul dɛn we gɛt sik dɛn lɛk nyurofibromatosis (wan sik we kin mek tumbu fɔm na di nervous system) ɔ Paget’s disease of bone (na sik we kin mek dɛn bon gro fayn fayn wan) kin gɛt mɔ risk fɔ gɛt (UPS).
- Sɔm tin dɛn we kin apin we pɔsin gɛt jɛnɛtiks:Pipul wae gɛt rare jenɛtik kɔndishɔn lɛk Li-Fraumeni syndrome kin gɛt bɔrku risk fɔ gɛt difrɛn kayn kansa, inklud (UPS).
- If yu gɛt sɔm kemikal dɛn: If yu de yuz sɔm kemikal dɛn fɔ lɔng tɛm, lɛk asɛnik ɔ vaynil klorayd, dat kin mek yu gɛt prɔblɛm bak.
- Fɔs rayt tritmɛnt to di say we di sik afɛkt: If yu dɔn gɛt redyushɔn tɛrapi to wan eria fɔ ɔda sik, smɔl risk de fɔ mek yu gɛt sarkoma (UPS) na da eria de leta.
- Di wok we yu de du fɔ gɛt raytin: If yu fɔ gɛt raytin na sɔm wok dɛn, dat kin bi bak di prɔblɛm.
E fayn fɔ no se bɔrku pipul dɛm wae gɛt UPS nɔr kin gɛt ɛni wan pan dɛn tin ya wae kin mek pɔrsin gɛt dis sik . So if yu si sɔntin we tan lɛk wan ɔnusual lump na yu bɔdi, nɔ ignore am bay we yu tink se, "A nɔ gɛt ɛni wan pan dɛn risk factor ya."
Aw dɔktɔ dɛn kin no `(UPS)`?
We yu si dɔktɔ wit wan lump lɛk dis, i go aks yu fɔs bɔt yu wɛlbɔdi, if ɛnibɔdi na yu famili dɔn gɛt sik lɛk kansa (family history), etc. Dɔn i go aks yu bɔt yu simptom dɛm. Aw lɔng dis lump dɔn de de? Yu tink se i de big mɔ ɛn mɔ? Yu tink se i de mek pɔsin fil pen? Apat frɔm dat, i go du dɛn tɛst ya:
1. Fyzikal ɛgzam: Di dɔktɔ go chɛk usay di tumbu de, in saiz, ɛn aw i kin fil we dɛn tɔch am (i at ɔ i saf).
2. Imej tɛst: Dɛn tɛst ya kin ɛp fɔ si aw di tumbu tan lɛk insay ɛn aw fa i dɔn skata. Bɔku tɛm, dɛn kin du wan ɔ mɔ tɛst dɛn lɛk X-ray, ɔltra saund skan, ɛn/ɔ MRI skan .
3. Bayopsi: Dis na di tɛst we impɔtant pas ɔl fɔ no di sik klia wan . Dis min se dɛn kin tek smɔl pat pan di tisu frɔm di tumbu (sɔntɛm dɛn kin yuz smɔl tin we tan lɛk nidul) ɛn mek pɔsin we de stɔdi bɔt sik dɛn (dɔktɔ we spɛshal fɔ no if pɔsin gɛt sik) chɛk am ɔnda maykroskɔp. Na da tɛm de nɔmɔ wi go se fɔ tru if na UPS ɔ ɔda kɔndishɔn.
Wetin na di tritmɛnt dɛm fɔ `(UPS)`?
Di tritmɛnt fɔ UPS dipen pan tin dɛn lɛk di sayz fɔ di tɔŋ ɛn if di kansa dɔn skata. Di men tritmɛnt fɔ di UPS we kin bigin na di ɔpreshɔn fɔ pul di tumbu . Bɔku tɛm dɛn kin du dis wit redyushɔn tɛrapi . Bɔt sɔntɛnde, dɛn kin nid fɔ gɛt ɔda tritmɛnt dɛn fɔ kansa.
Ɔpreshɔn
Di men gol fɔ ɔpreshɔn fɔ UPS na fɔ pul di kansa tɔŋ kpatakpata.. di dכkta dεm de tray fכ pul nכto di kεnsar nכmכ, bכt dεn kin tray fכ pul sכm hεlty tisu dεm we de rawnd am (dεn kכl dis "margin") . Jɔs lɛk we wi pul gras na gadin, wi nɔ jɔs de pul di plant, bɔt wi de pul wan smɔl layt we de rawnd am. Dɔn ivin smɔl pat pan di gras rut nɔ de lɛf. Semweso, we dɔktɔ dɛn pul dis kansa, dɛn kin pul am wit smɔl wɛlbɔdi tisu we de rawnd am. Na da tɛm de nɔmɔ wi go mek shɔ se dɛn pul ɔl di kansa sɛl dɛn we nɔ gɛt ɛni wan we lɛf. If kansa sɛl dɛn de na di ed pat pan di tɔŋ we dɛn pul, dat min se sɔntɛm mɔ kansa sɛl dɛn go lɛf na di bɔdi.
If di tumbu de na yu an ɔ yu leg, yu dɔktɔ go tray fɔ pul di kansa ɛn kip di wok we i ebul fɔ du na da an ɔ leg de. Bɔt insay sɔm bad bad kes dɛn, i kin nid fɔ kɔt in an . So, i impɔtant fɔ tɔk to yu ɔnkɔlɔjis fɔ disayd us tritmɛnt opshɔn go bɛtɛ fɔ yu sityueshɔn.
Ɔda Tritmɛnt dɛn fɔ Kansa
Di wan dɛn we de mɛn kansa kin yuz ɔda tritmɛnt dɛn bak bifo ɔ afta dɛn du di ɔpreshɔn. Pan ɔl we bɔku tɛm dɛn tritmɛnt ya nɔ kin mek di tumbu smɔl, dɛn kin ɛp fɔ mek i sef fɔ mek dɛn du di ɔpreshɔn fɔ pul di tumbu, ɔ fɔ kil ɛni kansa sɛl we kin lɛf afta dɛn dɔn du di ɔpreshɔn.
Dɛn ɔda tritmɛnt ya na:
- Kimotɛrapi: Fɔ gi mɛrɛsin dɛn we de kil kansa sɛl dɛn.
- Immunotherapy: I de mek di bɔdi in yon imyun sistɛm fɔ fɛt di kansa sɛl dɛn.
- Radieshɔn tɛrapi: Fɔ pwɛl di kansa sɛl dɛn we yu de yuz ay ɛnaji rayt.
Yu tritmɛnt plan na fɔ yu nɔmɔ. I kin difrɛn frɔm ɔda pɔsin in yon. So tɔk to yu dɔktɔ we de mɛn kansa bɔt di tin dɛn we yu go ebul fɔ du. Bɔku tɛm na wan tim we gɛt bɔku tin dɛn go trit yu . Dis tim kin gɛt dɔktɔ we de du ɔpreshɔn, dɔktɔ we de mɛn kansa we gɛt raytin, ɛn dɔktɔ we de mɛn kansa. Pan ɔl we ɛni spɛshal pɔsin gɛt difrɛn wok fɔ du, dɛn ɔl de wok togɛda fɔ trit yu. Dɛn go ɛp yu fɔ disayd wetin bɛtɛ fɔ yu sityueshɔn.
Ustɛm a fɔ go to dɔktɔ?
If yu notis wan lump ɔ gro ɛnisay na yu bɔdi we de gro sloslo , mɔ if i gɛt sɔm sayn dɛn lɛk pen, swel, ɔ we yu nɔ ebul fɔ muv yu an fayn fayn wan , yu fɔ go to dɔktɔ wantɛm wantɛm .
If yu dɔn ɔlrɛdi no se yu gɛt `(UPS)`, yuIf yu gɛt nyu sik, ɔ if yu sik de wɔs, tɛl yu dɔktɔ we de mɛn kansa wantɛm wantɛm .
Us kayn tin pɔsin we gɛt `(UPS)` kin ɛkspɛkt?
Di layf we pɔsin kin liv kin difrɛn frɔm wan pɔsin to ɔda pɔsin. I dipen pan di saiz fɔ di sarkoma ɛn di stej we di sik de . in jεnarכl, di fayv ia sכvayv rεt fכ hεy-grεd (UPS) na bכt 60% . Dis min se lɛk 60% pan di pipul dɛm wae dɛn dɔn no se gɛt dis sik stil de alayv afta fayv ia. di 10 ia rεt we de liv na bכt 48% .
Bɔt mɛmba se dɛn kayn we ya we pipul dɛn kin liv na jɔs jɔnaral ɛstimat . Dɛn nɔr kin tɛl yu ustɛm yu go liv ɔr us tritmɛnt go woke fayn fɔ yu. Fɔ no mɔ bɔt aw pipul dɛn kin liv ɛn aw dɛn kin afɛkt yu, i bɛtɛ fɔ tɔk to yu ɔnkɔlɔji tim.
Yu tink se `(UPS)` kin wɛl kɔmplit wan?
(UPS) kin wɛl ɔl, mɔ if dɛn no se i gɛt am kwik . Ivin pan kes dɛm wae de sik dɔn skata, tritmɛnt de wae kin ɛp fɔ mek yu gɛt bɛtɛ layf ɛn fɔ mek yu liv lɔng. Jɔs lɛk ɛni kayn kansa, fɔ no ɛn trit (UPS) kwik kwik wan na di bɛst we fɔ mek yu gɛt sakrifays .
Tin dɛn we wi fɔ tink bɔt
We dɛn no se yu gɛt kansa, i kin afɛkt ɔltin na yu layf. If na kansa wae nɔr kin bɔrku lɛk Undifferentiated Pleomorphic Sarcoma (UPS), yu kin fil lɛk yu wan ɛn lɛk se nɔbɔdi nɔ ɔndastand yu. Sɔntɛnde lɛk dis, i kin fayn fɔ jɔyn sɔpɔt grup usay ɔda pipul dɛn de we de go tru di sem ɛkspiriɛns lɛk yu . We yu tɔk to dɛn, dat go ɛp yu fɔ ɔndastand aw yu de fil ɛn kɔntrol dɛn.
Dɔn bak, yu mɛdikal tim de ɛp yu ɔltɛm . Dɛn kin tɔk to yu bɔt yu tritmɛnt opshɔn dɛm, sɔpɔt yu, ɛn gi yu di infɔmeshɔn ɛn tin dɛm wae yu nid fɔ disayd fɔ gɛt wɛl bɔdi. Nɔ fred fɔ aks dɛn ɛni kwɛstyɔn we yu gɛt . Mɛmba ɔltɛm se nɔto yu wangren de.
` Undifferentiated Pleomorphic Sarcoma, UPS, sarkoma, sɔft tisu kansa, kansa, tumor, kansa simptom, kansa tritmɛnt











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