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Lɛ wi tɔk bɔt Wilson’s Disease, we na wan sik we kɔpa kin gɛda na di bɔdi.

Lɛ wi tɔk bɔt Wilson’s Disease, we na wan sik we kɔpa kin gɛda na di bɔdi.

Kɔpa, we na di minral kɔpa, impɔtant fɔ mek wi ɔl wok fayn fayn wan pan smɔl smɔl tin dɛn. Bɔt imajin wetin go apin if dis impɔtant kɔpa gɛda na di bɔdi pas di wan we dɛn nid? Na da tɛm de wan sik we nɔ kin apin so ɔltɛm bɔt we kin rili siriɔs we dɛn kɔl Wilson Disease kin apin. Nɔ fred fɔ yɛri dis. Dɛn kin ebul fɔ mɛn am fayn fayn wan bay we dɛn tɛl yu bɔt am fayn fayn wan ɛn fɛn di rayt tritmɛnt. Tide, wi go tɔk bɔt dis simpul wan, insay langwej we yu go ɔndastand.

Wetin rili na di sik we Wilsin gɛt?

Fɔ tɔk am simpul wan, di sik we Wilsin gɛt na sik we pɔsin kin gɛt frɔm in jɛnɛtiks . I de pas frɔm wan jɛnɛreshɔn to ɔda jɛnɛreshɔn. Di liva na di men ɔgan na wi bɔdi we de filta kɔpa we de kam insay wi bɔdi. I tan lɛk wata filta. bכt pan pכsin we gεt Wilson in sik, difεkt de na wan jin (di `ATP7B` jin) we riliyt to dis kכpa filta prכsεs.

Dis kin mek di liva nɔ ebul fɔ du in wok fayn fayn wan. Dis kin mek di kɔpa we pasmak kin bigin fɔ gɛda na di men pat dɛn lɛk di liva, di bren, ɛn di yay instead fɔ pul am kɔmɔt na di bɔdi. As tɛm de go, dis kɔpa we kin gɛda kin pwɛl dɛn ɔgan dɛn ya ɛn mek dɛn gɛt difrɛn sayn dɛn.

di imכtant tin na dat, biכs dis na jεnεtik sik, fכ mek di sik kam, di pikin fכ gεt dis jin we nכ de wok fayn frכm di mama εn di papa. If na wan mama ɔ papa nɔmɔ i gɛt am, di sayn dɛn nɔ go sho, bɔt da pɔsin de kin gɛt di sik. Dis min se dɛn kin pas dis jin to dɛn pikin dɛn.

Wetin na di sayn dɛm fɔ dis sik?

De sayn dɛm fɔ Wilson in sik nɔr kin apin kwik kwik wan. Bikɔs kɔpa kin tek sɔm tɛm fɔ gɛda na di bɔdi, di sayn dɛn kin bigin fɔ sho afta sɔm tɛm. Dɔn bak, di sayn dɛn kin difrɛn difrɛn wan bay di ɔgan we di kɔpa de insay mɔ. Lɛ wi si wetin na dɛn men sayn ya.

Ɔgan/sistim we dɛn afɛkt Di sayn dɛn we pɔsin kin si
Simptom dɛm we gɛt fɔ du wit di liva
Liva

  • Taya ɛn wik we yu nɔ ebul fɔ ɛksplen
  • I nɔ kin want fɔ it ɛn i nɔ kin gɛt bɔku bɔku bɔdi
  • Nɔs ɛn vɔmit
  • Skin we de it
  • Di skin ɛn yay we de yɔlɔ (Jaundice) .
  • Bɛlɛ de pen ɛn blo
  • Mɔsul dɛn we kin kramp
  • Spayda angiomas (rɛd blɔd vesel dɛn we tan lɛk spayda wɛb na di skin) .

Nyurolɔjik simptom dɛm we gɛt fɔ du wit di bren ɛn di nervɔs sistɛm
Bren

  • I nɔ izi fɔ tɔk ɔ fɔ tɔk smɔl smɔl
  • I nɔ izi fɔ swɛla ɛn drɔl
  • Di an ɛn fut dɛn we de shek shek ɔ we yu nɔ de kɔntrol
  • Chenj na di we aw yu de waka (Improper walking) .
  • Pɔsin kin chenj, i kin vɛks
  • Prɔblɛm fɔ mɛmba ɛn si tin
  • Pwɛl hat ɛn Wɔri
  • Nɔ ebul slip

Di simptom dɛm we de na di yay
Yay

Dis na wan rili patikyula sayn. Wan gold-brawn ring de apia rawnd di blak yay. Dɔktɔ dɛn kɔl dis Kayser-Fleischer ring . Dis na di men sayn we de sho se kɔpa de insay di yay. Sɔm pipul dɛn kin gɛt sanflawa katarakt bak, we tan lɛk sanflawa.

Ɔda tin dɛn we de apin

Apat frɔm di men sayn dɛm we wi bin dɔn tɔk bɔt, sɔm ɔda prɔblɛm dɛn kin apin bikɔs di kɔpa de bɔku na di bɔdi.

  • Kidni ston dɛn
  • Menstrual saykl we nɔ de ɔltɛm na uman dɛn
  • Lɔw bon dɛnsiti ɛn at at sik
  • Blu diskɔlɔreshɔn na di nel dɛn

Udat dɛn kin gɛt dis sik?

Bikɔs dis na sik we pɔsin kin gɛt frɔm in jɛnɛtiks, di men tin we kin mek i gɛt dis sik na in famili istri .

If pɔrsin na yu famili, mɔr yu mama ɛn papa, yu brɔda, ɔr sista, gɛt Wilson in sik, yu de pan denja fɔ gɛt dis sik ɔr bi pɔrsin wae gɛt dis sik.

Bɔrku tɛm, di sik kin bigin fɔ sho bitwin 5 ɛn 40 ia. Bɔt dɛn dɔn ripɔt se di sik kin apin we dɛn yɔŋ pasmak, lɛk pikin we ol 9 mɔnt ɛn big pɔsin we ol 70 ia.

If pɔsin na yu famili gɛt dis sik, di bɛst tin fɔ du na fɔ go to yu dɔktɔ ɛn tɔk bɔt am ɛn nɔ shem. If nid de, dɛn kin du jenɛtik tɛst fɔ no if pɔsin gɛt di sik.

Aw dɛn kin trit am?

Pan ɔl we fɔ yɛri bɔt Wilson in sik kin mek yu fred, di gud nyus na dat, fayn tritmɛnt dɛn de fɔ am . Di tritmɛnt gɛt tu men gol dɛn.

1. Fɔ pul di kɔpa we pasmak we dɔn ɔlrɛdi gɛda na di bɔdi:

Fɔ dis, dɔktɔ dɛn kin gi yu wan spɛshal kayn mɛrɛsin. dεn kכl dεn tin ya `chelating agents`. Dɛn mɛrɛsin ya de wok bay we dɛn de atak di ɛkstra kɔpa patikyula dɛn na di bɔdi ɛn pul dɛn kɔmɔt na di bɔdi tru di urine. We dɛn kɔntinyu fɔ du dis tritmɛnt, dɛn kin kɔntrol di kɔpa lɛvɛl na di bɔdi. Bɔt we yu de tek dɛn mɛrɛsin ya, di wund dɛn kin te fɔ wɛl. So, if yu go du ɔpreshɔn, yu fɔ tɛl yu dɔktɔ bɔt am bifo tɛm.

2. Fכ mek di kכpa we de kכmכt frכm it nכ go insay di bכdi:

Dɛn kin gi yu zink sɔpɔtmɛnt fɔ dis. zink de ridyus di absכpshכn fכ kכpa na di dijestiv sistεm. Sɔmtɛm, dɔktɔ kin bigin dis zink tritmɛnt ivin pan pipul dɛm wae dɛn dɔn no se gɛt dis sik bɔt nɔr dɔn gɛt dis sik yet.

I rili impɔtant fɔ tek dis tritmɛnt fɔ di res ɔf yu layf , lɛk aw yu dɔktɔ se, ɛn yu nɔ go mis wan de. Yu dɔktɔ kin advays yu bak fɔ stɔp fɔ it tin dɛn we gɛt bɔku kɔpa (e.g. shelfish, liva, chɔklɛt, nɛt).

Mɛsej we dɛn kin kɛr go na os

  • Wilson in sik na wan sik wae nɔr kin bɔrku pan jɛnɛtiks wae kin kam wae kɔpa kin gɛda na di bɔdi.
  • Dis kin afɛkt di liva, di bren, ɛn di yay mɔ.
  • Di men sayn dɛm kin bi jaundice wae nɔr kin ɛksplen, pɔrsin kin chenj, ɛn wan golden-brawn ring rawnd di blak yay (Kayser-Fleischer ring).
  • If ɛnibɔdi na yu famili gɛt dis sik, go to yu dɔktɔ kwik kwik wan fɔ advays, ilɛksɛf nɔ gɛt ɛni sayn.
  • If yu no am kwik ɛn trit yu fɔ ɔl yu layf, dat kin ɛp yu fɔ liv wɛl, nɔrmal layf. Nɔ ɛva stɔp di tritmɛnt if yu nɔ gɛt dɔktɔ advays.

Wilson in sik, Wilson in sik Sinhala, kɔpa we de bɔku, liva sik, Kayser-Fleischer ring, jenɛtik sik
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Lɛ wi tɔk bɔt Wilson’s Disease, we na wan sik we kɔpa kin gɛda na di bɔdi.

Lɛ wi tɔk bɔt Wilson’s Disease, we na wan sik we kɔpa kin gɛda na di bɔdi.

Kɔpa, we na di minral kɔpa, impɔtant fɔ mek wi ɔl wok fayn fayn wan pan smɔl smɔl tin dɛn. Bɔt imajin wetin go apin if dis impɔtant kɔpa gɛda na di bɔdi pas di wan we dɛn nid? Na da tɛm de wan sik we nɔ kin apin so ɔltɛm bɔt we kin rili siriɔs we dɛn kɔl Wilson Disease kin apin. Nɔ fred fɔ yɛri dis. Dɛn kin ebul fɔ mɛn am fayn fayn wan bay we dɛn tɛl yu bɔt am fayn fayn wan ɛn fɛn di rayt tritmɛnt. Tide, wi go tɔk bɔt dis simpul wan, insay langwej we yu go ɔndastand.

Wetin rili na di sik we Wilsin gɛt?

Fɔ tɔk am simpul wan, di sik we Wilsin gɛt na sik we pɔsin kin gɛt frɔm in jɛnɛtiks . I de pas frɔm wan jɛnɛreshɔn to ɔda jɛnɛreshɔn. Di liva na di men ɔgan na wi bɔdi we de filta kɔpa we de kam insay wi bɔdi. I tan lɛk wata filta. bכt pan pכsin we gεt Wilson in sik, difεkt de na wan jin (di `ATP7B` jin) we riliyt to dis kכpa filta prכsεs.

Dis kin mek di liva nɔ ebul fɔ du in wok fayn fayn wan. Dis kin mek di kɔpa we pasmak kin bigin fɔ gɛda na di men pat dɛn lɛk di liva, di bren, ɛn di yay instead fɔ pul am kɔmɔt na di bɔdi. As tɛm de go, dis kɔpa we kin gɛda kin pwɛl dɛn ɔgan dɛn ya ɛn mek dɛn gɛt difrɛn sayn dɛn.

di imכtant tin na dat, biכs dis na jεnεtik sik, fכ mek di sik kam, di pikin fכ gεt dis jin we nכ de wok fayn frכm di mama εn di papa. If na wan mama ɔ papa nɔmɔ i gɛt am, di sayn dɛn nɔ go sho, bɔt da pɔsin de kin gɛt di sik. Dis min se dɛn kin pas dis jin to dɛn pikin dɛn.

Wetin na di sayn dɛm fɔ dis sik?

De sayn dɛm fɔ Wilson in sik nɔr kin apin kwik kwik wan. Bikɔs kɔpa kin tek sɔm tɛm fɔ gɛda na di bɔdi, di sayn dɛn kin bigin fɔ sho afta sɔm tɛm. Dɔn bak, di sayn dɛn kin difrɛn difrɛn wan bay di ɔgan we di kɔpa de insay mɔ. Lɛ wi si wetin na dɛn men sayn ya.

Ɔgan/sistim we dɛn afɛkt Di sayn dɛn we pɔsin kin si
Simptom dɛm we gɛt fɔ du wit di liva
Liva

  • Taya ɛn wik we yu nɔ ebul fɔ ɛksplen
  • I nɔ kin want fɔ it ɛn i nɔ kin gɛt bɔku bɔku bɔdi
  • Nɔs ɛn vɔmit
  • Skin we de it
  • Di skin ɛn yay we de yɔlɔ (Jaundice) .
  • Bɛlɛ de pen ɛn blo
  • Mɔsul dɛn we kin kramp
  • Spayda angiomas (rɛd blɔd vesel dɛn we tan lɛk spayda wɛb na di skin) .

Nyurolɔjik simptom dɛm we gɛt fɔ du wit di bren ɛn di nervɔs sistɛm
Bren

  • I nɔ izi fɔ tɔk ɔ fɔ tɔk smɔl smɔl
  • I nɔ izi fɔ swɛla ɛn drɔl
  • Di an ɛn fut dɛn we de shek shek ɔ we yu nɔ de kɔntrol
  • Chenj na di we aw yu de waka (Improper walking) .
  • Pɔsin kin chenj, i kin vɛks
  • Prɔblɛm fɔ mɛmba ɛn si tin
  • Pwɛl hat ɛn Wɔri
  • Nɔ ebul slip

Di simptom dɛm we de na di yay
Yay

Dis na wan rili patikyula sayn. Wan gold-brawn ring de apia rawnd di blak yay. Dɔktɔ dɛn kɔl dis Kayser-Fleischer ring . Dis na di men sayn we de sho se kɔpa de insay di yay. Sɔm pipul dɛn kin gɛt sanflawa katarakt bak, we tan lɛk sanflawa.

Ɔda tin dɛn we de apin

Apat frɔm di men sayn dɛm we wi bin dɔn tɔk bɔt, sɔm ɔda prɔblɛm dɛn kin apin bikɔs di kɔpa de bɔku na di bɔdi.

  • Kidni ston dɛn
  • Menstrual saykl we nɔ de ɔltɛm na uman dɛn
  • Lɔw bon dɛnsiti ɛn at at sik
  • Blu diskɔlɔreshɔn na di nel dɛn

Udat dɛn kin gɛt dis sik?

Bikɔs dis na sik we pɔsin kin gɛt frɔm in jɛnɛtiks, di men tin we kin mek i gɛt dis sik na in famili istri .

If pɔrsin na yu famili, mɔr yu mama ɛn papa, yu brɔda, ɔr sista, gɛt Wilson in sik, yu de pan denja fɔ gɛt dis sik ɔr bi pɔrsin wae gɛt dis sik.

Bɔrku tɛm, di sik kin bigin fɔ sho bitwin 5 ɛn 40 ia. Bɔt dɛn dɔn ripɔt se di sik kin apin we dɛn yɔŋ pasmak, lɛk pikin we ol 9 mɔnt ɛn big pɔsin we ol 70 ia.

If pɔsin na yu famili gɛt dis sik, di bɛst tin fɔ du na fɔ go to yu dɔktɔ ɛn tɔk bɔt am ɛn nɔ shem. If nid de, dɛn kin du jenɛtik tɛst fɔ no if pɔsin gɛt di sik.

Aw dɛn kin trit am?

Pan ɔl we fɔ yɛri bɔt Wilson in sik kin mek yu fred, di gud nyus na dat, fayn tritmɛnt dɛn de fɔ am . Di tritmɛnt gɛt tu men gol dɛn.

1. Fɔ pul di kɔpa we pasmak we dɔn ɔlrɛdi gɛda na di bɔdi:

Fɔ dis, dɔktɔ dɛn kin gi yu wan spɛshal kayn mɛrɛsin. dεn kכl dεn tin ya `chelating agents`. Dɛn mɛrɛsin ya de wok bay we dɛn de atak di ɛkstra kɔpa patikyula dɛn na di bɔdi ɛn pul dɛn kɔmɔt na di bɔdi tru di urine. We dɛn kɔntinyu fɔ du dis tritmɛnt, dɛn kin kɔntrol di kɔpa lɛvɛl na di bɔdi. Bɔt we yu de tek dɛn mɛrɛsin ya, di wund dɛn kin te fɔ wɛl. So, if yu go du ɔpreshɔn, yu fɔ tɛl yu dɔktɔ bɔt am bifo tɛm.

2. Fכ mek di kכpa we de kכmכt frכm it nכ go insay di bכdi:

Dɛn kin gi yu zink sɔpɔtmɛnt fɔ dis. zink de ridyus di absכpshכn fכ kכpa na di dijestiv sistεm. Sɔmtɛm, dɔktɔ kin bigin dis zink tritmɛnt ivin pan pipul dɛm wae dɛn dɔn no se gɛt dis sik bɔt nɔr dɔn gɛt dis sik yet.

I rili impɔtant fɔ tek dis tritmɛnt fɔ di res ɔf yu layf , lɛk aw yu dɔktɔ se, ɛn yu nɔ go mis wan de. Yu dɔktɔ kin advays yu bak fɔ stɔp fɔ it tin dɛn we gɛt bɔku kɔpa (e.g. shelfish, liva, chɔklɛt, nɛt).

Mɛsej we dɛn kin kɛr go na os

  • Wilson in sik na wan sik wae nɔr kin bɔrku pan jɛnɛtiks wae kin kam wae kɔpa kin gɛda na di bɔdi.
  • Dis kin afɛkt di liva, di bren, ɛn di yay mɔ.
  • Di men sayn dɛm kin bi jaundice wae nɔr kin ɛksplen, pɔrsin kin chenj, ɛn wan golden-brawn ring rawnd di blak yay (Kayser-Fleischer ring).
  • If ɛnibɔdi na yu famili gɛt dis sik, go to yu dɔktɔ kwik kwik wan fɔ advays, ilɛksɛf nɔ gɛt ɛni sayn.
  • If yu no am kwik ɛn trit yu fɔ ɔl yu layf, dat kin ɛp yu fɔ liv wɛl, nɔrmal layf. Nɔ ɛva stɔp di tritmɛnt if yu nɔ gɛt dɔktɔ advays.

Wilson in sik, Wilson in sik Sinhala, kɔpa we de bɔku, liva sik, Kayser-Fleischer ring, jenɛtik sik
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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