Wali otidde ng’akaana ko akatono kafuuse bbululu mu bwangu? Oba afuna obuzibu mu kussa ng’ayonsa, ng’akaaba oba ng’akyuka? Kya bulijjo maama oba taata yenna okutya ng’alaba ebintu nga bino. Leero twogera ku
Tetralogy of Fallot , embeera y’omutima ey’obuzaale eyinza okuleeta obubonero nga buno. Wadde erinnya lino liyinza okuwulikika nga lizibu katono, ka tulinnyonnyole mu ngeri ennyangu.
Tetralogy ya Fallot kye ki ddala?
Mu ngeri ennyangu, Tetralogy of Fallot ye kugatta ebizibu by’omutima bina ebibeerawo ng’azaalibwa. Era eyitibwa embeera y’omutima ey’obuzaale. Kizibu ekibaawo ng’omutima gukula ng’omwana akula mu lubuto. Kino kireetera omusaayi ogulimu omukka gwa oxygen (omusaayi omumyufu) okutabula n’omusaayi ogutaliimu oxygen (omusaayi gwa bbululu). Olwo omusaayi guno ogutabuliddwa omutima ne gusindikibwa mu mubiri. N’ekyavaamu, ebitundu by’omubiri mu mubiri tebifuna mukka gwa oxygen gumala. Mu busawo, embeera eno tugiyita
hypoxemia .
Omubiri bwe gubulwa omukka gwa oxygen okumala ebbanga eddene, olususu lw’omwana, emimwa n’enjala bifuna langi ya bbululu. Kino kiyitibwa cyanosis , oba ‘okufuuka bbululu’.
Kino okusobola okukitegeera obulungi, ka tulabe engeri omutima omulamu gye gukolamu.
Engeri omutima omulamu gye gukolamu
Kuba akafaananyi ng’omutima gwaffe gulinga ennyumba ey’ebisenge bina. Ku mwaliiro ogwa waggulu kuliko ebisenge bibiri (atria) n’ebisenge bibiri ebinene ku mwaliiro ogwa wansi (ventricles). Wakati w’ebisenge bino waliwo vvaalu, ng’enzigi. Oludda olwa ddyo ne kkono olw’omutima lwawulwamu bbugwe (septum). 1.
Oludda olwa ddyo: Omusaayi gw’omubiri ogutaliimu mukka gwa oxygen, ogwa bbululu guyingira mu kisenge kya ddyo nga guyita mu misuwa egy’okungulu n’omusuwa ogwa wansi. 2. Okuva awo, omusaayi guyita mu vvaalu (tricuspid valve) ne guyingira mu kisenge kya ddyo. 3. Okuva mu ventricle eya ddyo, omusaayi guno ogwa bbululu guyitira mu valve endala (pulmonic valve) ne guyingira mu musuwa omukulu (pulmonary artery) ogugenda mu mawuggwe. 4.
Munda mu mawuggwe: Omusaayi guno gufuna omukka omupya, ne gufuuka omusaayi omumyufu omulongoofu. 5.
Oludda olwa kkono: Omusaayi guno omumyufu ogulimu omukka gwa oxygen gudda mu kitundu kya kkono eky’omutima. 6. Okuva awo, kiyita mu vvaalu (mitral valve) ne kiyingira mu kisenge kya kkono. 7. N’ekisembayo, omusaayi guno omumyufu omulongoofu okuva mu kisenge kya kkono guyisibwa mu musuwa ogusinga obunene mu mubiri (aorta) okutuuka ku mubiri gwonna. Eno y’engeri ebitundu byaffe gye bifunamu omukka gwa oxygen gwe byetaaga okusobola okuwangaala.
Ebikyamu ebina ebibeerawo mu Tetralogy of Fallot (The "Tetralogy") .
Mu mutima gw’omwana alina obulwadde bwa Tetralogy of Fallot, waliwo obulema buna obukulu obukyusa enkola eya bulijjo gye twogeddeko.
| Obulema ku Mutima | Mu ngeri ennyangu... |
|---|
| Obuzibu mu kitundu ky’omubiri ekiyitibwa Ventricular Septal Defect (VSD) . | Ekinnya mu bbugwe (septum) wakati w’ebisenge ebibiri ebya wansi (ebisenge) eby’omutima. Kino kisobozesa omusaayi ogwa bbululu ogutaliimu oxygen omutono ku ludda olwa ddyo okutabula n’omusaayi omumyufu ogulimu oxygen omungi ku ludda olwa kkono. |
| Okusannyalala kw’amawuggwe (PS) . | Okufunda kw’ekisenge ky’amawuggwe oba omusuwa gw’amawuggwe ogutwala omusaayi mu mawuggwe. Kino kikendeeza ku musaayi ogugenda mu mawuggwe. Diguli ya bbululu etera okusalibwawo okusinziira ku bunene bw’okufunda kuno. |
| Okusukkulumye ku Aorta | Omusuwa omukulu (aorta) ogutwala omusaayi mu mubiri gwonna gusangibwa wakati w’ennyindo zombi, okusinga okutwala omusuwa ogwa kkono gwokka nga bwe kiri ekya bulijjo. N’olwekyo omusaayi ogutabuddwamu oguyita mu kinnya kya VSD guyingira butereevu mu musuwa guno ne gugenda mu mubiri. |
| Obulwadde bwa Right Ventricular Hypertrophy | Olw’okuba ekkubo erigenda mu mawuggwe lifunda (Pulmonary Stenosis), omusuwa ogwa ddyo gulina okukola ennyo okukuba omusaayi. Ng’ebinywa bwe bikula ng’okola dduyiro, kino kigonza ekisenge ky’omusuwa ogwa ddyo. |
Kiki ekivaako embeera eno?
Ekituufu ekivuddeko kino tekinnamanyika. Buba bulema obubeerawo ng’ebitundu by’omutima bitondeddwa nga bukyali ng’omwana akula mu lubuto. Si musango gwo, era si kintu kye wakola ng’oli lubuto. Kale towulira musango ku nsonga eyo.
Omwana wo naye alina obubonero buno?
Abaana
abasinga abalina obulwadde bwa Tetralogy of Fallot balaga obubonero mu mwaka ogusooka mu bulamu bwabwe.
- Okubeera kwa bbululu (Cyanosis): .Kano ke kabonero akakulu. Emimwa gy’omwana, olulimi, olususu n’emisumaali bifuna langi ya bbululu oba eya kakobe.
- "Tet Spells / Hypercyanosis": Kino kintu kikulu nnyo. Omwana bw’akaaba, bw’anywa amata, bw’agezaako okugenda mu kaabuyonjo oba ng’azuukuka ku makya, ayinza okufuuka langi ya bbululu enzito mu bwangu, okukaluubirirwa okussa, n’okutabuka nnyo. Oluusi bayinza n’okubulwa amagezi. Embeera eno esobola okumala eddakiika ntono okutuuka ku ssaawa eziwerako.
- Okukaluubirirwa okussa : Omwana akoowa mangu n’agwa mu tulo oluvannyuma lw’okudduka n’okuzannya.
- Okufukamira: Omwana omuto bw’aba akooye okuzannya, ajja kutuula mangu ng’amaviivi gasimbuddwa okutuuka mu kifuba (okufukamira). Kino mu butamanya kyongera ku muwendo gw’omusaayi ogugenda mu mawuggwe gaabwe, ne kibanguyira okussa .
- Okulemererwa okukula: Omwana okugejja , okukula, n’okukula kuyinza okulwawo okusinga abaana abalala.
Ddi lw’osaanidde okunoonya amagezi g’omusawo?
Tosubwa ddwaaliro lya mwana wo buli mwezi. Omusawo asobola okuzuula embeera zino ng’akebera omwana wo.
Bw’oba olina obubonero buno wammanga, laba omusawo mu bwangu.- Singa olususu n’emimwa gy’omwana bifuuka bbululu.
- Bwoba olina obuzibu mu kussa .
- Bw’oba okooye ng’oyonsa oba ng’okaaba.
- Bw’owulira ng’okukula kwo kukendeera.
Singa wabaawo embeera ez’amangu zino wammanga, twala mangu omuntu oyo mu ddwaaliro erikuli okumpi mu kitongole ky’abalwadde ab’amangu (ETU):- Tet Okuloga
- Kizibu nnyo okussa.
- Okukonziba
- Okuzirika
- Obukoowu oba obunafu obuyitiridde
Obulwadde buno buzuulibwa butya? (Okukebera n’okuzuula obulwadde)
Omusawo ajja kukebera omwana, awulirize omutima bw’akuba, era bwe wabaawo okubuusabuusa kwonna akusindikire okukeberebwa okuwerako.
- X-ray y’ekifuba: Eno etunuulira enkula y’omutima. Mu Tetralogy of Fallot, omutima guyinza okulabika nga "guli mu ngeri ya boot" kubanga ventricle eya ddyo egaziwa.
- Electrocardiogram ( ECG ): Ekigezo ekitaliimu bulumi ekipima amasannyalaze g’omutima.
- Okukebera omutima (Echo): .Kino kye kigezo ekisinga obukulu era ekituufu. Kiringa sikaani. Kisobola okulaba obulungi buli kimu ekiri mu mutima, gamba ng’ebisenge, vvaalu, ebituli ( VSD ), n’okufunda (PS).
- Cardiac Catheterization: Mu mbeera ezimu, okukebera kuno kukolebwa nga tebannalongoosebwa okupima puleesa y’omutima n’omukka gwa oxygen, n’okutunuulira obulungi ensengekera y’emisuwa. Mu kukebera kuno, akatundu akatono kayisibwa mu musuwa mu kisambi okutuuka ku mutima.
Obujjanjabi bwe buruwa?
Obujjanjabi bwokka obw'olubeerera eri Tetralogy of Fallot kwe
kulongoosa .
Singa ofuna "Tet Spell" okola ki?
Singa omwana wo afuuka bbululu nnyo mu bwangu, kikulu nnyo okubeera
omukkakkamu . 1. Teeka omwana ku mugongo gwe,
ng’amaviivi gasimbuddwa okutuuka mu kifuba (knee-to-chest position) . 2. Omwana mutwale mu ddwaaliro mu bwangu. Mu ddwaaliro, omwana agenda kuweebwa omukka gwa oxygen n'eddagala nga propranolol okufuga "tet spells".
Okuloongoosa
Ekiseera ky’okulongoosebwa kisinziira ku buzibu bw’obubonero bw’omwana. Okulongoosa kutera kukolebwa mu myaka ebiri egisooka egy’obulamu.
- Okulongoosa okukkakkanya obulumi (Blalock-Taussig shunt): Abalongo abamu batono nnyo oba banafu era bayinza obutasobola kugumira kulongoosebwa mu bujjuvu. Mu mbeera ng’ezo, akakwate akatono akalinga ttanka kakolebwa wakati w’omusuwa mu mubiri n’omusuwa mu mawuggwe okwongera ku muwendo gw’omusaayi ogugenda mu mawuggwe. Kino kiyinza okuyamba omwana okukula katono n’amaanyi.
- Okulongoosa mu bujjuvu: Mu kino, ekituli mu mutima (VSD) kiggalwa n’akatundu, era ekkubo erifunda erigenda mu mawuggwe (PS) ne ligaziwa. Oluvannyuma lw’okulongoosebwa kuno, omusaayi mu mutima gudda mu mbeera eya bulijjo.
Olw’okukulaakulana kwa tekinologiya w’ebyobujjanjabi ennaku zino, okulongoosa kuno kugenda bulungi nnyo.
Oluvannyuma lw'okulongoosebwa...
Oluvannyuma lw’okulongoosebwa obulungi, abaana abasinga basobola okubeera mu bulamu obwa bulijjo nga tebalina bubonero bwonna oba obuzibu bwonna. Basobola okugenda ku ssomero, okuzannya, okukola mu biseera eby’omu maaso, n’okufumbiriganwa. Kyokka ne bwe baba bamaze okulongoosebwa, kyetaagisa
okugoberera omusawo buli kiseera obulamu bwabwe bwonna. Oluusi, enkyukakyuka mu nnyimba z’omutima (arrhythmias) ziyinza okubaawo, n’olwekyo kikulu okwekebejjebwa buli kiseera.
Obubaka Obutwala Awaka
- Tetralogy of Fallot kwe kugatta obulema buna obw’omutima obuzaalibwa. Guno si musango gwo.
- Akabonero akasinga omwana okufuuka bbululu (cyanosis), ekiyinza okweyongera naddala ng’akaaba oba ng’anyigirizibwa.
- Omwana bw’afuuka bbululu nnyo mu bwangu (Tet Spell), tosattira, amaviivi galeete mu kifuba ogatwale mu ddwaaliro mu bwangu.
- Obulwadde buno busobola bulungi okuzuulibwa ng’okozesa enkola ya Echocardiogram.
- Okulongoosa bwe bujjanjabi obw’olubeerera. Leero, okulongoosa kuno kugenda bulungi nnyo.
- Oluvannyuma lw’okulongoosebwa, omwana asobola okubeera mu bulamu obwa bulijjo, obulungi, naye kyetaagisa okugoberera amagezi g’abasawo n’okukeberebwa obulamu bwe bwonna.
tetralogy of fallot, obulwadde bw’omutima, abaana, blue baby, cyanosis, tet spells, obulema mu kuzaalibwa, obulema bw’omutima obuzaalibwa, ekituli mu mutima, VSD
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