I chau a, i chau fo em? A nih loh leh thil tenawm ber ber atang pawhin natna khirh tak tak i nei em? I taksa pum puiah hliam i hmu em? Chûng thilte chu thil pangngaiah kan ngai mai thei a, mahse a châng chuan kan taksa chhungril takah harsatna a awm tih chhinchhiahna a ni thei bawk. Chumi awmzia chu kan taksa thisen siamna factory ber, ruhro (bone marrow) hian chawlh a nei em tih enfiah a hun tawh tihna a ni.
Aplastic anemia hi eng nge ni tak tak?
A awlsam zawngin sawi ila, aplastic anemia hi thisen lama natna awm lo tak, mahse na tak a ni. Thil thleng chu kan ruh chhunga spongy part, bone marrow , an tih chuan thisen cell thar a siam tawh lo. Kan taksa thisen siamna factory lian ber chu rang takin nawrh huaihawt ang maiin han ngaihtuah teh.
Kan thisenah hian cell chi thum a awm a, chungte chu:
- Thisen sen (red blood cells): Hengte hi taksa pum puia oxygen phurtu an ni.
- White blood cells: Hengte hi natna leh hri kai dotu kan sipaite an ni.
- Platelets: Hengte hi hliam a awm chuan thisen chhuah titawptu an ni.
A chang chuan aplastic anemia-ah hian heng thisen cell chi thum zinga pakhat chauh a lo piang chhuak thin. Mahse a tam zawkah chuan chi pathumte hi an siam chhuah tlem vek a ni. Hetiang dinhmun hi zawi zawiin emaw, rang takin emaw a lo awm thei a ni. Thisen cell zat a tlahniam nasa hle a nih chuan nunna atana hlauhawm tak a ni thei.
He natna hi kum eng pawhah lo awm thei mahse, thalai kum 20 hnuai lam leh kum 60 chunglam zingah a tam ber.
Eng thilin nge hetiang dinhmun hi a thlen?
Aplastic anemia hian chhan hrang hrang a nei thei. Doctor ten eng chi nge a nih leh engtiang chiahin nge a nasat tih an rel ang.
Aplastic Anemia rochun a ni
Hei hi i pianpui genetic defect thenkhat avanga lo awm a ni. Heng genes te hian i ruhro hian thisen cell a siam tling thei lo. Entirnan, Fanconi anemia leh Dyskeratosis congenita ang chi natna te hi he thil nen hian a inzawm tlat a ni.
A hnu lama a chhan (Acquired Aplastic Anemia) .
Hei hi a tam ber chi a ni. Heta thil thleng hi kan taksa hriselna (immune system) hian kan ruhro (bone marrow cell) te hi a rawn bei sual a ni. A chhan dang pawh a awm:
- Virus thenkhat chu `HIV` emaw `(Epstein-Barr)` emaw ang chi te hi an ni.
- Damdawi thenkhat, a bik takin antibiotics thenkhat.
- Chemical tha lo tak tak nena inzawmna.
- Cancer natna tan radiation emaw chemotherapy emaw hmanga enkawl a ni.
- Autoimmune disorder dangte pawh a awm bawk.
A chhan hmuh theih loh (Idiopathic Aplastic Anemia) .
A châng chuan, doctor-te chuan he natna hi a chhan chiang tak an hmu thei lo. Heng case te hi hetiang hian an sawi thin.
"Aplastic crisis" tih hi a danglam hle. Thisen sen siam chhuahna tihtawp nghal mai a ni. Mahse kar tlemte chhungin a reh tlangpui. Aplastic anemia hi a rei zawk a ni.
Eng symptoms nge i hriat?
I symptoms chu eng thisen cell chi nge tlakchham tih ah a innghat ang. Mahse, cell chi thumte hi a tlakchham fo avangin heng natna lan chhuah dan hi a inzawm khawm tih i hmu mai thei.
| Thisen cell chi hrang hrang a tlahniam | Symptoms awm thei te |
|---|---|
| Thisen sen (red blood cells) a tlahniam |
|
| Thisen var (white blood cells) tlahniam |
|
| Platelet tlahniam |
|
Engtin nge hei hi i hmuh theih, Doctor?
Hetiang symptoms i neih chuan i doctor chuan test eng emaw zat a ti ang a, chu chuan i natna hmuhchhuah chu a nemnghet ang.
- Complete Blood Count (FBC): Hei hian i thisena cell chi hrang hrang awm zat a teh a ni.
- Peripheral Blood Smear hmanga tihfai: 1.1.Hetah hian i thisen sample chu microscope hmangin an enfiah a, cell pianzia leh lian tham lo awm leh awm loh an enfiah thin.
- Bone Marrow Aspiration emaw Biopsy: Hei hi a natna hriat chian nan test pawimawh ber leh chiang ber a ni. Anesthesia hnuaiah hian hip ruh emaw ruh remchang dang emaw atang hian ruhro sample tlemte tak tak lak a ni. Hei hi eng emaw chen chu test harsa tak ni mah se, dik taka natna hriat chian a pawimawh hle.
Hei hi eng enkawlna nge ni?
Enkawl dan chu natna thlentu, a nasat dan leh i kum ang chi thil hrang hrangah a innghat a ni.
- A chhan enkawl dan: A châng chuan, he natna thlentu hi damdawi emaw, chemical emaw a nih chuan, tihtawp chuan natna chu a ti ṭha thei a ni.
- En reng la, nghah rawh: Natna hi a na lutuk lo a nih chuan i doctor chuan damdawi engmah a pe lo mai thei a, i thisen zat enfiah fo chungin i dinhmun a enfiah thei bawk.
- Ruihhlo hmanga enkawl dan:
- Immunosuppressants: Heng damdawi te hian i immune system in i ruhro a beih loh nan a pui thin.
- Bone Marrow Stimulants: Heng damdawi te hian bone marrow hian thisen cell tam zawk siam turin a pui thin.
- Thisen pek: Thisen sen emaw, platelet emaw a tlakchham tawh tam zawk nan pawn lam atanga thisen pek a ngai a ni. Hei hi damdawi a ni lo a, mahse a natna lan chhuah dan control nan a pui a ni.
- Stem Cell Transplant: Hei hi Bone Marrow Transplant tia hriat a ni bawk. Hei hian ruhro natna nei chu mi hrisel (a tam zawkah chuan a chhungte hnai tak) atanga stem cell hrisel tak tak hmanga thlak a huam a ni. Hei hian natna chu a tidam vek thei a ni. Hei hi enkawlna hlawhtling tak a ni a, a bik takin damlo naupang tan chuan a hlawhtling hle.
Enkawlna tinreng hian a thatna leh a hlauhawmna a nei vek a, chuvangin i doctor nen inenkawlna tha ber chungchang sawiho a tha ber.
Hetiang dinhmun hi engtin nge i nunpui?
Aplastic anemia i neih chuan i hriselna i ngaihtuah bik a ngai a ni.
- Infection laka invenna: Kut sil fo thin ang che. Damlo leh mipui tamna hmun a\angin a theih ang angin inthiarfihlim rawh.
- Hliam pumpelh tur: Thisen chhuah a hlauhawm avangin infiamna leh hliam thlen thei thil tih loh tur.
- Chawlh hahdamna tha tak nei rawh: I chau tih i hriat hunah chawlh hahdamna tha tak nei rawh.
- Ei leh in inthlau tak: Chaw tha tak tak ei thin ang che.
- Damdawi lam thurawn zawm rawh:Damdawi doctor-in a pek chu a hun takah ei thin ang che. Tin, thil danglam bik, thlawhna i thlawh hmain doctor rawn hmasa phawt ang che.
Take-Home Thuchah a ni
- Aplastic anemia hi thil awm lo mahse na tak a ni a, ruhro hian thisen cell a siam chhuak tawh lo.
- Sudden extreme fatigue, infection awm fo, leh i taksaa random bruises ang chi symptoms te chu ngaihthah suh.
- Tunah chuan hei hi enkawlna tha tak tak a awm ta. Chuvangin natna hi hriat hmasak a, enkawl tan a pawimawh hle.
- I natna lan chhuah dan te, hlauhthawnna te, leh enkawlna kawng hrang hrang te chu i doctor hnenah inhawng tak leh rinawm takin sawi rawh. Damdawi lam kaihhruaina dik tak nen chuan he natna hi hlawhtling taka enkawl theih a ni.











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