Doctor-in i naupang tê chu a thinlungah thawm tê tê a nei tih a hrilh che khan i hlau hle a ni ngei ang, ‘thinlung murmur’ a ni. A nih loh leh, kum 40 i tling tawh a, exercise tlemte pawh i la thawk chhuak thei lo va, i la chau reng em? Chung thil pahnih chhan chu thinlunga khur te tak te a ni mai thei. Damdawi lam hawi chuan hei hi ‘Atrial Septal Defect’ emaw ASD emaw kan ti a. He hming i hriat hian hlau suh. Hei hi pianpui thinlung natna (congenital heart condition) a awm fo thin. Vawiin hian awlsam tak leh friendly takin i sawi vek ang u.
A awlsam zawngin, he thinlunga khur (ASD) hi eng nge ni?
Awle, hei hi hrethiam tur chuan kan thinlung hi pindan pali awmna in angin ngaihtuah ila. He in hian a chung lamah pindan pahnih a nei a, a hnuai lamah pindan pahnih a nei bawk. Damdawi lamah chuan heng pindan pahnih hi a chung lam chu atria tiin kan ko thin. Chu chu dinglam atrium leh veilam atrium tihna a ni. Heng upper chamber pahnih inkarah hian bang a awm a. He wall hi atrial septum kan ti a .
A tlangpuiin taksa thisen oxygen tlachham, thianghlim lo chu dinglam atrium-ah a lut a, lungah a kal a, a thianghlim (oxygenated) a, veilam atrium-ah a kir leh a ni. He thisen oxygen tamna, thianghlim tak hi taksa pum puiah a pump chhuak ta a ni.
Tunah chuan han ngaihtuah teh, a chung lam chamber pahnih inthenna tur bang (septum)-ah hian khur te tak te awm ta se eng nge thleng ang? Tichuan, veilam chamber atanga oxygen tamna, thisen tha tak tak thenkhat chu he khur atang hian dinglam chamber chhungah a luang lut ang. Tichuan, he thisen tha tak hi dinglam atanga thisen bawlhhlawh nen a inhmeh ang. Chuvângin, thisen ṭûl lo tak chu a dinglamah a pung khâwm ang a, chu thisen tam zâwk chu lungah pump kir leh tûrin thinlung dinglam chuan a thawkrim lehzual a ngai ang. Chu chu ASD chu a ni.
Pawimawh: Mi thenkhat chuan ASD hi Patent Foramen Ovale (PFO) tih natna nen an inzawm tir thin. An pahnih hi a inang lo va, dinhmun hrang hrang pahnih a ni.
ASD chi hrang hrang lian ber ber a awm em?
Ni e, atrial fibrillation hi chi li a awm a, chu chu heart wall-a khawiah nge a khur awmna a zirin a ni. Hei hi hriat a pawimawh a, enkawl dan tur chu a chi hrang hrangah a innghat fo thin.
| ASD chi hrang hrang | Hrilhfiahna |
|---|---|
| Secundum ASD a ni | Hei hi a tam ber chi a ni . ASD vei mi sawm zinga pariat chuan hetiang chi hi an nei a ni. Chu khur chu atria inkar bang lai takah a awm a. |
| Primum ASD a ni | He khur hi bang hnuai lam a awm a ni. Hetiang chi naute thenkhat hian heart valve-ah emaw, lower chamber (ventricles) inkar wall-ah emaw chhiatna dang an nei thei bawk. |
| Sinus Venosus ah hian a awm a | He khur hi a tlangpuiin bang chunglam emaw, a hnung lamah emaw a awm thin. Hetiang chi hi a chang chuan thinlunga thisen phurtu vein lian ber berte chhiatna nen a inzawm thei bawk. |
| Coronary Sinus chu a inchung lo | Hei hi a rarest type a ni . Thinlung leh veilam atrium nena inzawm vein pawl pakhat inkara wall awm lo emaw, a kim lo emaw a nih chuan a thleng thin. |
Hetiang natna lan chhuah dan hi engte nge ni?
Mak tak maiin ASD hi pianpui natna ni mahse, mi tam tak chuan kum tam tak hnuah, kum chanve vel thleng pawhin an nei lo. Chu khur chu a te lutuk (millimeter 5 aia tlem) a nih chuan thinlung emaw, lung emaw-ah nghawng lian tham a nei lo thei a, chuvangin a lan chhuah dan a awm lo thei bawk.
Naupang tê tête natna lan chhuah dan
Vawi tam tak chu naupang têin ASD a vei tih chhinchhiahna hmasa ber chu doctor-in stethoscope a enfiah laiin a hriat thin thinlung ri (heart murmur) danglam tak a ni. Chu chu chhinchhiahna langsar ber a ni.
Hei bakah hian naupang thenkhat chuan natna lan chhuahna te pawh an nei thei bawk:
- Kum nena inmil taka taksa rihna tihtlem leh than chak lohna.
- Thluak lam natna (khawsik, pneumonia ang chi) awm fo thin.
- Inkhelh laiin chau nghal vat.
- Thâwk harsa.
- Heart rhythm irregularities (arrhythmias) - mahse hei hi naupangteah chuan a tlem deuh.
Puitlingah a natna lan chhuah dan
Naupan laia hriat loh khur lian tak i neih chuan kum 40 vel atang khan symptoms a lo lang tan thei a, hei hi a chhan chu thinlung leh lung dinglam hian kum tam tak chhung hna a thawk nasa zawk a, a chau tawh bawk.
Puitlingte chuan natna lan chhuahna an nei thei a, chungte chu:
- Chhan awm lova hah lutuk.
- Thâwk harsa, hla vak lo kal lai emaw, stairs chhoh lai emaw ang chi.
- Heart rate dik lo (palpitations) hriatna.
- Lung natna (tachycardia) chak tak.
- Ke, ke ruh leh kut zungtang (edema) a awm.
- A chang chuan hmui leh vun hi a sen (cyanosis) a lo awm thin.
Heng symptoms te hi i neih chuan doctor rawn nghal tur a ni. Hengte hi ASD enkawl loh chhinchhiahna a ni thei a, thinlung natna dang chhinchhiahna pawh a ni thei bawk. I rilru a na a nih chuan hospital emergency department (ETU) hnai ber pan nghal tur a ni.
Engvangin nge hetiang dinhmun hi a lo awm?
Hei hi a chhan dik tak erawh hriat a la ni lo. Amaherawhchu, heng piansualna tam zawk hi chu nausen pum chhunga naute lo seilian laia genetic changes lo awm vang a ni. NKX2.5/CSX, GATA4, leh TBX5 ang chi genes inthlak danglamna hi ASD nen a inzawm tih hmuhchhuah a ni.
Tin, a chang chuan ASD vei naute hian thinlung lama harsatna dang emaw, genetic condition dang, Down syndrome ang chi emaw an nei thei bawk.
Naupai laiin risk tipungtu thil
Nu naupai hian natna engemaw zat a neih chuan naute hian pianpui thinlung natna a vei theihna a sang deuh thei a ni.
- Nu hian nau a pai hmain zunthlum a nei a.
- Naupai laiin flu ang chi virus infection lo awm.
- Zu leh zuk leh hmuam hman.
- Doctor thurawn tel lova damdawi thenkhat hman.
- Cocaine ang chi ruihhlo hman.
Enkawl loh chuan eng harsatna nge thleng thei?
Hole te tak te chuan chhiatna a thlen tam lo ang. Amaherawhchu, khur lian tak chu rei tak enkawl loha dah a nih chuan hriselna lama harsatna lian tak a thlen thei a ni. Hei hi a chhan chu thinlung dinglam leh lungte hian hna an thawk nasa zawk reng a, chu chuan a tichhia a ni.
- Right heart enlargement: Hetianga a kal zel chuan heart failure a thlen thei a ni.
- Heart rhythm disorders (Arrhythmia): Kum 40 chunglam ASD vei zinga a chanve vel chuan heart rhythm disorder (atrial fibrillation ang chi) an nei thin.
- Stroke: A chang chuan thinlunga thisen zam te tak te lo awm te hian he khur atang hian thluak chhungah a lut thei a, chu chuan stroke a thlen thin.
- Pulmonary Hypertension: Pulmonary Hypertension: Lung lama thisen phurtu thisen kalna kawng hrang hrangah thisen sang a sang. Hei hi dinhmun hlauhawm tak a ni.
- Eisenmenger Syndrome natna vei te hi:ASD a awm a, pulmonary hypertension na tak a awm chuan complication na tak a ni.
Doctor-te hian engtin nge hei hi an hmuh?
I natna lan chhuah dan an zawt ang a, taksa enfiahna an nei ang a, chutah chuan i thinlung hnathawh leh insiam dan enfiah turin test eng emaw zat an nei ang.
| Fiahna | Chuta tang chuan eng nge i zir? |
|---|---|
| ECG (Electrocardiogram) hmanga tih a ni. | Thinlung electrical activity chu record a ni. Hei hian thinlung thawk mumal lo emaw, thinlung dinglam a lian em tih emaw clues a pe thei a ni. |
| Chest X-ray neih a ni | Thinlung dinglamah chamber te chu a lian em tih leh lung a nghawng em tih i enfiah thei ang. |
| Echocardiogram (Echocardiogram - TTE) tih hi a tha hle. | Hei hi test pawimawh ber leh pawimawh ber a ni . Heart scan ang mai a ni. Chu khur lian leh te, a awmna hmun te, thisen kal dan te, thinlunga nghawng a neih dan te chu chiang takin a lang thei a ni. |
| Trans-esophageal Echo (TEE) a awm a, a chhuahna tur hmun leh a hmanna tur hmun a awm lo. | Ultrasound test bik, camera te tak te chu larynx kaltlanga pass a ni. Hei hian hole chungchang chipchiar zawka hriat theih nan a pui a ni. |
A then phei chuan cardiac CT emaw MRI scan emaw pawh a ngai thei bawk.
Hei hi eng enkawlna nge ni?
ASD chhinchhiahna thenkhat control nan damdawi pek theih ni mahse, a khur chu a khar thei ngai lo. A khur hi khar dan kawng hnih a awm a, chungte chu operation emaw non-surgical (percutaneous repair) hmanga khur khar emaw a ni.
- ASD tenau te:Khur te tak te, a bik takin naupangte tan chuan a mah chauhin a khar mai thei. A nih loh chuan, leh harsatna an thlen loh chuan doctor chuan "watchful waiting" tih a rawt ang a, chu chu check fo mai loh chu engmah tih loh tur tihna a ni.
- ASD lian tak tak: A khur a lian a nih chuan a lan chhuah loh pawhin khar a tha ber. Hei hian nakin lawka harsatna lian tham lo thleng thei tur a veng thei a ni. A tlangpuiin thinlung dinglam a lian a nih chuan, emaw, a khur atanga thisen tam tak a luang chhuak a nih chuan enkawl a tha ngei ang.
Enkawl dan tur
1. Percutaneous Device Closure: Hei hi tuna hman tlanglawn ber a ni. Kea vein lian tak kaltlangin tube te tak te (catheter) dahin, thinlung lam pan a kaihruai a, umbrella ang chi hmanrua te tak te (device) dahin a khur chu khar a ni. Hei hian incision lian tak a ngai lo. Damdawi ina awm chhung hi ni khat emaw ni hnih emaw chauh a ni. Hetiang method hi ASD chi hrang hrang tan hman theih a ni lo.
2. Open-Heart Surgery: He surgery hi a chunga kan sawi ang hian khur khar theih loh emaw, heart defect dang nena inzawm khur emaw tan tih a ni. Hetah hian rilru chu hawn a, thinlunga khur chu stitches emaw patch emaw hmangin an khar a ni. Tunah chuan hei hi surgery him leh hlawhtling tak a ni ta.
Inenkawl zawhah i doctor chuan thla 6 vel chhung lung natna laka inven nan thisen tithianghlimtu leh antibiotics ei turin a hrilh ang che.
ASD nen hian nun hi eng ang nge ni?
Nangmah emaw i fain emaw ASD an vei tih an hriat chuan hlauhthawn hi thil pangngai a ni. Mahse thu lawmawm tak chu tunlai damdawi lam science hmasawn tak hmang hian he natna hi hlawhtling taka enkawl theih a ni a, mite chu hrisel takin, nun pangngai takin an nung thei a ni .
Naupang khur khar tawh chuan a dam hnuah naupang dang ang bawkin a khel thei ang a, a tlan thei ang a, infiamna a khel thei bawk ang. Puitling an nih pawhin enkawl hnuah pawh an thil tih dan pangngai chu an chhunzawm thei a ni.
A pawimawh ber chu doctor thupek dik taka zawm a, a hun taka clinic-a checkup turin kal hi a ni. A bik takin, hetiang congenital heart disease specialist enkawlna hnuaia awm hi i hriselna atan a pawimawh hle.
Take-Home Thuchah a ni
- Atrial Septal Defect (ASD) hi lungphun chunglam pahnih inthenna bang chhunga khur awm a ni. A tlangpuiin, pianpui atanga lo chhuak a ni.
- Mi tam tak, a bik takin a khur a te a nih chuan kum tam tak chhung chu natna lanchhuahna engmah an nei lo.
- Naupangah chuan thinlung ri (murmur) pangngai lo a hriat theih a, puitlingah chuan hah lutuk leh thawk harsa lutuk hi a lan chhuahna ber a ni thei.
- Enkawl loh chuan khur lian tak takte hian hun kal zelah thinlung leh lung a tichhe thei a ni.
- He natna hi tunlai enkawlna hmasawn tak tak (non-surgical emaw surgical emaw) hmang hian a dam kim thei a ni.
- Enkawlna dik tak a awm chuan naupang leh puitlingte chu nun famkim, hrisel, active tak tak an neih theih lohna tur engmah a awm lo. I doctor ring la, a thurawn zawm rawh.











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