Budd-Chiari Syndrome, natna khirh tak, liver chhunga thisen kalna kawngte a inkharkhip thin chungchang hi i zir dawn teh ang.

Kan taksa peng pawimawh ber pakhat chu thin (liver) hi a ni. Factory lian tak ang bawkin liver hian thisen kalna kawng lian tak a nei a, chu chuan thisen atanga bawlhhlawh paih chhuak a ni. Ngaihtuah teh, chûng thisen kalna kawng khat emaw, a aia tam emaw chu a inkhar emaw, a tlêm emaw a nih chuan eng nge thleng ang? Damdawi lamah chuan hei hi thil awm lo mahse na tak a ni a, chu chu liver atanga thisen chhuahna thisen kalna kawng (veins) a inkharkhip vang a ni . Hei hi hriat chian a pawimawh hle. A awlsam zawngin sawi ila.

A awlsam zawngin, Budd-Chiari Syndrome hi eng nge ni?

Hei hi hriatthiam dan tha ber chu kan in chhunga tui luang chhuak (drain) a inkharkhip a nih chuan eng nge thleng tih ngaihtuah hi a ni. Pipe khar chu tuiin a khat ang bawkin, hepatic veins a inkhar chuan thisen chu liver chhungah a inkhawm tan thin. Hei hi thisen zam vang te, vein chhunga a hring vang te, pawn lam atanga pressure vang te pawh a ni thei.

Hetianga thisen a pungkhawm chuan thin (liver) a lo hring a, a lian ta hle a ni. Chu mai ni lovin, he pressure avang hian spleen pawh a lian thei bawk. Hetiang dinhmun hi a awm chhunzawm zel chuan side effect na tak dang engemaw zat a awm thei bawk.

• Portal Hypertension: Liver (`portal vein`)-a thisen phurtu main vein-a pressure tam lutuk.
• Varices: He pressure sang tak avang hian chaw kawng leh pum ang hmuna thisen kalna kawngte chu a lian a, a puak darh thei a, thisen a chhuak thei bawk.
• Ascites: Tui ang tuiin pum a luah khat a, a hring chhuak thin. Hei hi "ascites" kan ti a.
• Cirrhosis: Hun rei tak chhung liver a tichhia a, chu chuan liver cell a thih phah a, liver a hliam a awm bawk. Hei hi dinhmun khirh tak, tihdanglam theih loh a ni.

He natna chi hrang hrang a awm em?

Ni e, a natna lan chhuah chak dan leh a nasat dan a zirin chi hrang hrangah then theih a ni. Tin, a chhan bulpui (underlying cause) atanga thlirin chi hnih a awm bawk.

A chhan a zirin chi hnih a awm a, chungte chu:

1. Primary Budd-Chiari Syndrome: Hetiang a nih chuan buaina chu thisen kalna chhung ngeiah a awm a. Hei hi thisen zam (thrombus) vang emaw, vein chhunga a hring vang emaw a ni thei.

2. Secondary Budd-Chiari Syndrome: Hetah hian harsatna hi thisen kalna pawn lam atanga lo chhuak a ni. Entirnan, liver bula cancer emaw cancer nei lo emaw tumor a awm chuan thisen kalna kawng a tikhawlo thei a ni.

Hei hi eng symptoms nge ni?

He natna lan chhuah dan hi mi hrang hrangah a inang lo thei. Natna chi hrang hrang a zirin an danglam bawk. Mahse, a lan chhuah dan tlangpui tlemte hmuh theih a awm.

Engvangin nge Budd-Chiari Syndrome hi a lo awm? A chhante chu engte nge ni?

Vawi tam tak chu hei hi damdawi lam dinhmun avanga taksain thisen zam a siam duhna a tipung a ni.

• Thisen natna (Myeloproliferative neoplasms - MPNs): Hengte hi thisen cancer chi hrang hrang hmuh tur awm lo tak a ni. Anni hian taksain thisen cell a siam tam lutuk a, thisen zam a tipung a ni.
• Hypercoagulable disorders: Genetic cause emaw natna dang emaw avanga thisen a inzawm rang lutuk. Entirnan, `Protein C` emaw `S` tlakchhamna, `Antiphospholipid antibody syndrome` ang chi dinhmun.
• Liver emaw kidney tumor: Cancer emaw benign tumor emaw hian pawn lam atanga thisen kalna kawng a tikhawlo thei a.
• Naupai: Hmeichhia hi an pianphungah chuan naupai laiin thisen zam a tam zawk.
• Birth control pills: Birth control pill chi thenkhat hman hian thisen zam a tipung thei bawk.
• Natna dang: `Sickle cell disease` leh `Inflammatory bowel disease (IBD)` ang chi natna te pawhin hei hi a thlen thei a ni.

Mahse, a châng chuan a chhan dik tak hmuh theih lohna a awm . Chu chu `idiopathic` kan ti a.

Engtin nge doctor hian hei hi a hmuh theih?

Doctor i hmuh chuan i natna lan chhuah dan chu ngun takin a ngaithla ang che a, a enfiah ang che a, chutah chuan i natna hriat chian nan test eng emaw zat a ti ang.

1. Thisen test: Hengte hian liver enzyme level check-na leh thisen zam awm theihna a awm leh awm loh hriat theih nan a pui thin.

2. Imaging test hrang hrang: 1.1.

• Doppler Ultrasound Scan: Hei hi scan hmasa ber, awlsam ber leh pawimawh ber a ni. Liver thisen kalna kawng hrang hranga thisen kal dan en nan sound wave a hmang a. Hei hian blockage a awm leh awm loh hriatna tha tak a pe thei a ni.
• CT Scan emaw MRI Scan: Heng scan chi hrang hrang hian thin leh a chhehvel taksa peng hrang hrangte thlalak chiang zawkin a la thei a ni. A châng chuan thisen kalna kawngte hmuh theih nân taksaah tui bik (`contrast material`) inject theih a ni.
• Venography (venogram): He test hi scan dang a chiang lo a nih chuan tih a ni. He test-ah hian thisen kalna kawng khatah tui bik dahin, thisen kal dan enfiah nan X-ray image lak a ni.

3. Liver Biopsy: Liver-ah chhiatna engzat nge a awm tih chiang taka hriat theih nan leh cirrhosis a lo awm leh awm loh hriat chian nan, thisen peng te tak te tak te chu needle te tak te hmangin la in microscope hmangin an enfiah thin.

Hei hi eng enkawlna nge ni?

Enkawlna kawngah hian tum lian tak pahnih a awm a. Pakhat chu thisen kalna kawng khar chu hawn leh emaw, thisen kalna tur kawng dang siam emaw a ni. A dang chu a chhan bulpui enkawlna a ni.

Damdawi hmanga enkawl

A tirah chuan thisen zam chu a tithianghlim a, thisen zam thar a lo awm loh nan damdawi anticoagulants (blood thinners ) te pek thin a ni. Entirnan, damdawi chi hrang hrang heparin emaw warfarin emaw.

Surgery ni lo enkawlna bik

Damdawi chauh hian a natna hi a thunun theih loh chuan specialist doctor-te’n enkawlna kawng hrang hrang an nei a ni.

• Transjugular Intrahepatic Portosystemic Shunt (TIPS): Hei hi a buaithlak deuh a ni. A awlsam zawngin, liver chhungah "bypass" a siam a ni. High-pressure portal vein leh hepatic vein inkarah hian tube te tak te (stent) dah a ni a, chu chuan liver atanga thisen a chhuah tir thin. Hei hian thisen chu a inkharkhip loh nan kawng thar a siam a ni.
• Percutaneous Transluminal Angioplasty: Hei hian thisen kalna kawng khar emaw, a zim emaw chu balloon hmanga inflate a ni. A châng chuan mesh ang chi tube te tak te (`stent`) an dah a, chu chu a vessel chu a zim leh tawh loh nan a ni.

Liver Transplant a ni

Enkawlna dang zawng zawng a hlawhchham chuan, emaw, liver a hlawhchham vek (liver failure) emaw, cirrhosis a lo vei emaw a nih chuan, a hnuhnung ber chu liver transplant hrisel hi a ni.

He natna hian hmalam hun eng nge ni ang?

Prognosis hi thil engemaw zat ah a innghat a ni. Natna hi engtiang chiahin nge hriat a nih hma, a chhiat nasat zia leh a enkawl danah engtiang chiahin nge a chhân lêt tih te hi a pawimawh vek a ni.

Enkawl loh chuan damlo thisen kalna kawngkhar khar vek tawh chu kum thum vel chhungin liver failure vangin a thi thei a ni. Mahse, enkawl dan dik tak, a bik takin liver transplant a nih chuan dam rei tak i dam thei tlangpui. Chuvangin, hemi chungchanga hriat tur tha ber chu i doctor hnen atangin a ni. I dinhmun azirin chiang takin a hrilhfiah ang che.