I dam em? Vawiin hian mit natna hriat tlem, mahse pawimawh tak mai kan sawi dawn a ni. A chang chuan kan mit hian kan hriat lohvin kan hmuh dan a thlak danglam thei. Target board-a target ang maia lang pattern i hre tawh em? Chu chu he Bull's Eye Maculopathy'' an tih dinhmunah hian a thleng thin. A hming hi a mak deuhin a ri a ni lawm ni? Mahse, lungngai suh, chipchiar tak leh awlsam takin sawi ila.
Bull's Eye Maculopathy'' hi eng nge ni? A awlsam zawngin sawi ila...
Bull’s Eye Maculopathy hi thil awm lo tak a ni a, retina hmun pawimawh ber macula -a cell te chu a chak lo zauh zauh a, a dik zawka sawi chuan a chhe vek bawk.
Ngaihtuah teh, i mit chu camera ang a nih chuan retina chu camera hnung lama film emaw sensor emaw ang a ni. Thlalak kan hmuhte chu chutah chuan record a ni. Retina lai takah hian hmun te tak te, mahse pawimawh tak tak a awm a, chu chuan thil chiang tak leh chiang takin min hmu thei a ni. Chu chu macula an tih chu a ni. He macula hian lehkhabu kan chhiar lai te, mi hmel kan en lai te, a nih loh leh thread te tak te kan bun lai te ang chi thil chipchiar tak takte chiang taka hmuh theih turin min pui a ni.
Chuvangin, Bull's Eye Maculopathy'' ah hian he macula'' chhunga cell te a chhiat chuan doctor in mit chhung lam a enfiah chuan chu macula'' ah chuan ring rawng danglam tak tak pattern an hmu thin. A hming hi a chhan chu archery target (bull’s eye pattern)-a ring ang a nih vang a ni. Hetiang dinhmun hian mitdelna a thlen thei a ni.
He natna hi rochun theih a ni (i.e., i nu leh pate hnen atangin genes hmanga kai theih a ni). Doctor-te chuan he rochun chi hi Bull's Eye Maculopathy'' hi Benign Concentric Annular Macular Dystrophy (BCAMD)'' an ti \hin. Mit natna dang avang emaw, damdawi thenkhat hun rei tak hman avanga side effect vang emaw pawh a ni thei bawk .
Mit lama harsatna eng pawh hi a hlauhawm thei hle. Mahse i doctor chuan a chhan zawng turin a pui thei che a, chu natna i hmachhawn theihna tura i mamawh enkawlna leh puihna a pe thei bawk che a ni.
Bull’s Eye Maculopathy hian mit hmuhnaah eng nghawng nge a neih theih?
Bull’s Eye Maculopathy hi thil hmuh theihna tura min puitu cell te tihchhiat vang a ni. Chuvangin, hei hian i central vision chu degree hrang hrangin a nghawng thei a ni.
- Mi ṭhenkhat chuan thil chipchiar ṭha tak takte chiang taka hmuh harsa an ti mai thei.
- I rawng i thliar hrang thei lo mai thei a, a nih loh leh i rawng hmuhna a tlahniam thei bawk.
- Zanah mit hmuh a tlahniam thei.
- As central vision weakens , lehkhabu chhiar te, lirthei khalh te, leh thil awm dan dik tak hmuh te chu a harsa thei hle.
- He natna hian mit pakhat chauh emaw, mit pahnih emaw a nghawng thei a ni.
Mahse a tam zawkah chuan Bull’s Eye Maculopathy vei te hian an peripheral vision - chu chu an mit kil atanga an hmuh theih danah harsatna lian tham an nei lo. Mahse, hei hi a tlangpuiin a zual zel avangin, hun kal zelah mit a chhe zual thei a ni .
Tute nge Bull's Eye Maculopathy'' vei theihna chance sang zawk?
Risk factor chu natna vei theihna tipungtu thil a ni. Bull's Eye Maculopathy hi risk factor engemaw zat a awm a:
- Chhungkaw zinga mi pakhatin Bull's Eye Maculopathy'' (a hereditary history) a neih chuan .
- Mit natna dang macular degeneration te neih .
- Genetic conditions thenkhat , entirnan, Batten natna emaw Stargardt natna emaw.
- Damdawi thenkhat hun rei tak hman, a bik takin autoimmune diseases (autoimmune diseases, a awlsam zawnga sawi chuan, i taksa ngeia immune system-in nangmah ngeiin i cell hrisel tak takte a beih dan a ni).
Hetiang dinhmun hi engtiang chiahin nge a awm?
Bull’s Eye Maculopathy hi a takah chuan a awm lo hle. Entirnan, United States-ah pawh hian mi tlemte chauhvin he natna hi an vei a ni. Chuvangin, i mit hmuh danah inthlak danglamna i hmuh chuan hlauthawng suh.
Bull's Eye Maculopathy'' hi engte nge ni?
Hetiang thil a thlen theih chhan hi chhan hrang hrang a awm a:
1. Genetics chungchang: 1.1.
Bull’s Eye Maculopathy, BCAMD tia hriat bawk hi autosomal dominant condition a ni. A awlsam zawngin, nu leh pa zinga pakhatin natna atana mutated gene an neih chuan an fain natna hi a rochun theihna chance 50% a awm a ni. Heng genes te hi kan DNA peng hrang hrang, kan taksaa information dahkhawmtu an ni.
2. Natna dang: 1.1.
Mit natna dang, cone-rod dystrophy emaw retinitis pigmentosa emaw pawhin Bull’s Eye Maculopathy a thlen thei bawk. Tin, kan sawi tawh ang khan Batten natna emaw Stargardt natna emaw ang chi genetic disease nei te pawhin he natna hi an vei theihna a hlauhawm hle bawk.
3. Toxicity a awm thei: 1.1.
Thil thenkhat, a bik takin damdawi thenkhat hian i mit hmuhna lairil (macula)-a cell te chu a tichhe thei a ni. Entirnan, hun rei tak chhunga damdawi, chloroquine emaw hydroxychloroquine emaw, rheumatoid arthritis emaw lupus emaw ang chi natna enkawlna atana hman chuan Bull’s Eye Maculopathy a thlen thei a ni.
Tin, thisen pek fo ngai te hian hemochromatosis (iron overload) tih natna an nei thei bawk. Hei hian i macula a tichhe thei bawk.
Engtin nge damdawi (Hydroxychloroquine) hian (Bull's Eye Maculopathy) a thlen?
Hetiang thil hi engtin nge a awm tih chiang takin mithiamte chuan an la hre lo. Mahse zirchianna chuan he damdawi hian i retina-a cell-te chu a binding thei a, chu cell-te hnathawh dan a nghawng thei tih a tarlang. Hei hi damdawi dose sang tak rei tak i ei hian a thleng fo thin. Chuvangin doctor-te chuan heng damdawi ei thinte hi mit enfiah fo thin turin an rawt a ni.
Bull's Eye Maculopathy'' natna lan chhuah dan chu engte nge ni?
Hetiang dinhmun hian mit hmuhna a nghawng ber a ni. A lan chhuah dan chu:
- Vision blur emaw foggy emaw a awm.
- I field of vision-a hmun dum emaw, thlalak dum emaw hmuh.
- Rangkachak hriat harsa emaw, rawng mitdelna (complete color blindness) emaw.
- Mit hmaa thread inphah (eye floater) ang chi thil hmuh emaw, êng eng mawi tak tak hmuh emaw.
- Mit a hniam hle .
Heng symptoms pakhat emaw pahnih emaw i neih vang mai mai hian Bull’s Eye Maculopathy i vei tih ngaihtuah suh. Hengte hi mit natna dang chhinchhiahna a ni thei bawk. Chuvangin damdawi lam thurawn lak a pawimawh hle.
Engtin nge Bull's Eye Maculopathy'' hi mit chhungah a lang?
Hei hi darthlalang atanga i hriat theih thil a ni lo. Ophthalmologist chuan i macula leh retina chu ophthalmoscope an tih hmanraw bik hmangin i nei leh neih loh a enfiah ang.
A tlangpuiin he "bull's eye" pattern hi a laiah round, dum angin a lang a, a chhehvelah hian ring eng emaw zat a awm a ni. Dark center hian retina pangngai a entir a ni. A chhehvel ring te chu a pangngai lo hle. Heng ring te hi light orange, pink, purple emaw a ni thei. Heng rawng hrang hrangte hi mit hmuhna lairil (macula) a chhiat emaw, a chhe emaw avanga lo awm a ni.
Engtin nge Bull’s Eye Maculopathy hi hmuhchhuah a nih?
I doctor chuan Bull’s Eye Maculopathy i vei em tih hriat nan mit test vawi tam tak a nei thei ang. Chung zinga ṭhenkhat chu:
- Visual acuity test: Hei hi i hmuh theih dan tur test a ni. Standardized letter chart (Snellen chart'') emaw, letter size hrang hrang nei monitor emaw chhiar turin an ti ang che. I mit chu mit pahnih leh mit pakhat a hrana khar chungin test a ni ang.
- Visual field test: 1.1.Hei hian i central vision leh peripheral vision a check ang. Mitdel i neih leh neih loh pawh a hrilh thei bawk. Line grid en turin an ti che a, a nih loh leh i hma leh a sir lam i hmuh theih dan tur en turin light on emaw, i kut kha sawn emaw i ti thei bawk.
- Color vision test: Dot rawng hrang hranga siam thlalak, a laiah number awm (color plate test) i entir ang. Number i hmuh theih loh chuan color blindness i nei thei. Tin, anomaloscope an tih hmanrua hmangin êng i hriat dan leh rawng engte chu i hmu thei bawk.
- Ophthalmoscopy: Hei hian mittui tlakna (emp drops) hmanga mitmeng (pipils) tihzauh a ni. Tichuan, ophthalmoscope hmangin i mit (cornea), lens, retina, macula, optic nerve leh a chhehvel thisen kalna kawngte chu enfiah a ni. He test hi fundoscopy an ti bawk.
- Optical coherence tomography (OCT) test: Hei hi natna nei lo test a ni. Light wave hmangin i mit hmuhna lairil a i retina layer, a bik takin macula layer hrang hrangte chu chipchiar tak tak, three-dimensional (3D) (3D) thlalak a la a ni. He test hian macula-a chhiatna leh degeneration te chu test dang aiin a hmain leh chiang zawkin a hmu thei a ni.
- Fundus autofluorescence imaging (FAF) test: Hei hi imaging technique thar a ni. Blue light hmangin i retina chhunga pigmented cells te chu a enfiah thin. Cell thenkhat chuan he êng hi a dang aiin an absorb emaw, an reflect danglam emaw a ni. Hei hian doctor chu retina-ah chhiatna emaw, chhiatna emaw a awm leh awm loh a hriat theih nan a pui a ni.
Bull’s Eye Maculopathy hi a dam vek thei ang em?
Lungchhiatthlak takin Bull's Eye Maculopathy'' hi damdawi kimchang hmuh a la ni lo.
Bull’s Eye Maculopathy hi engtin nge enkawl a nih?
Tunah hian Bull's Eye Maculopathy avanga mit hloh tawh siam\hat thei tur damdawi a awm lo. Mahse, he natna hi damdawi emaw taksaa iron tam lutuk (poisoning) avanga lo awm a nih chuan damdawi tihtawp emaw, iron level control emaw hian natna a zual zel loh nan a veng thei a, a thunun thei bawk.
A tam zawkah chuan enkawlna tum ber chu damlote chu mit hmuh lohna leh rawng mitdelna ang chi natna nena nunpui hi a ni. I doctor chuan a hnuaia mi hi a rawn rawt thei ang:
- Assistive technology: Entîr nân, video magnifier, projector, a nih loh leh screen reader.
- Glasses emaw contact lens emaw hman tur a ni.
- Low vision rehabilitation emaw occupational therapy: Hengte hian nitin hna thawh tur hrang hrang, mitdelna neia tih dan tur leh hmanraw hrang hrang a zirtir che a ni.
- Vision aids: Kut hmanga magnifier, telescope, emaw light-filtering lens ang chi thil.
Bull's Eye Maculopathy'' vei tan chuan eng nge a hmalam hun?
Bull’s Eye Maculopathy avanga mit hloh hi a awm reng thin a, hun kal zelah a kal zel thei bawk . Mahse, kan sawi tawh ang khan, macular chhiatna hi thil tha lo avanga lo awm a nih chuan, chu thil tha lo chu pumpelh chuan a natna a zual zel loh nan a pui thei a ni.
Bull's Eye Maculopathy'' hi ven theih dan a awm em?
Dik tak chuan Bull's Eye Maculopathy'' lo awm tur venna tur kawng bik a awm lo.
Mahse, damdawi thenkhat (e.g., hydroxychloroquine) hian he natna thlen theihna a keng tel avangin, chutiang damdawi chu hun rei tak ei a nih chuan, doctor thurawn angin mit enfiah fo hian chhiatna eng pawh hriat hmasak a pui thei a, natna a zual zel loh nan a pui thei bawk.
Bull's Eye Maculopathy'' chungchangah hian ka doctor hnenah eng zawhna nge ka zawh tur?
Bull's Eye Maculopathy'' i neih chuan i doctor hnenah zawhna thenkhat zawt la, hetiang hi:
- "Doctor, tuna ka ei mek hi he natna tizual thei tur damdawi a awm em?"
- "Ka mit hmuhna tichak thei tur nutritional supplement a awm em?"
- "He mitdelna nen hian engtin nge ka nitin nunah ka hnathawh theih ang? Chutianga tanpuina ka hmuh theih dan tur thenkhat chu engte nge ni?"
- "Engtin nge ka tan chuan lirthei khalh hi a la him em tih ka hriat theih ang?"
- "He ka mit hloh hi a awm reng dawn em ni?"
- "Engtiang chiahin nge ka mit a chhe zual ang?"
Bull’s Eye Maculopathy hi natna awm lo tak a ni. I mit hmuh danah inthlak danglamna i hmuh chuan he natna avanga lo awm a nih a rinawm loh. Mahse, mit hmuhna lama harsatna awm reng reng chu ngaihthah suh. I mit hmuhna hloh chu hlauhawm leh lungngaihna thlen thei mah se, hmachhawn dan tur a awm. I doctor chuan vision aids, support services, leh treatment i mamawh te hnenah a refer thei che a ni.
I mit hmuh danah inthlak danglamna, mit a fiah lo emaw, natna lan chhuah thar dang emaw i hmuh chuan doctor pan nghal rawh. I mit hmuh lohna chhan chu eng pawh ni se, enkawl hmasak chuan mitdelna chu a tikhawtlai thei a, a titawp thei a, a tidanglam thei bawk.
Hriat reng tur pawimawh ber berte (Take-Home Message) .
Okay, chuvangin vawiin a kan sawi tawh thenkhat, pawimawh i tih mai theihte kha han khaikhawm ila:
- Bull's Eye Maculopathy hi mit natna hmuh tur awm lo tak a ni a, mit chhunga mit hmuhna hmun (macula) a chhiat avangin "bull's eye" ang chi a awm thin.
- Hei hian central vision a tichak lo thei a ni. Hei hian lehkhabu chhiar leh hmel hriatna ang chi thilte a nghawng thei a ni.
- Hei hi thlahtute, natna dangte, leh damdawi ṭhenkhat hun rei tak hman avânga lo awm thei a ni .
- He natna hi damdawi chiang tak a la awm lo. Mahse, symptoms enkawl dan tur leh nun awlsam zawka siam theihna tur kawng a awm.
- I mit hmuh danah danglamna i hmu a nih chuan mit doctor pan vat a pawimawh. Hriat chian leh enkawl vat chuan natna a zual zel loh nan a pui thei a ni.
I mit enkawl hi i mawhphurhna a ni. Mit hrisel hi nunah eng ropui tak a ni.




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