I naute piang thar vun leh hmui chu a sen deuhin a lang em? Thâwk lakah harsatna a nei deuh niin a lang em? A nih loh leh bawnghnute a in hian a thawmhnaw a chhuak nasa em? Hengte hi thil thleng mai mai anga ngaih suh. A châng chuan hengte hi i naute pianpui thinlung natna chhinchhiahna a ni thei bawk. Vawiin hian thinlung natna hmuh tur awm lo tak kan sawi dawn a, chu chu nang pawhin nu leh pa angin i hriat chian ngei ngei tur a ni. Chu chu Double Outlet Right Ventricle, a tawi zawngin DORV a ni.
A awlsam zawngin, Double Outlet Right Ventricle (DORV) hi eng nge ni?
Hei hi hrethiam tur chuan thinlung hrisel hnathawh dan hi han ngaihtuah hmasa ila. Kan thinlung hi in te tak te, pindan pali nei ang mai a ni. A chung lam pindan pahnih leh a hnuai lam pindan pahnih a awm bawk. A hnuaia room lian leh chak tak pahnih hi ventricles an ti a. Pakhat chu dinglam (Right Ventricle) ah a awm a, pakhat chu veilam (Left Ventricle) ah a awm bawk.
Hei hi a thleng tlangpui chu a ni:
- Oxygen tlachham, "bawlhhlawh" thisen lung-a phurtu thisen kalna bulpui ber, pulmonary artery chu right ventricle -ah a intan a ni.
- Thisen kalna kawng lian ber, aorta chu veilam ventricle atanga intan a ni a, thisen "thianghlim", lung atanga oxygen pek chhuah chu taksa pum puiah a phur a ni.
A felfai hle a ni lawm ni? Room tinah tube lian tak pakhat.
Tunah chuan DORV chungchangah chuan he thupek hi tihbuai a ni ta. DORV vei nauteah chuan kan sawi tak thisen kalna kawng lian ber pahnih, Pulmonary Artery leh Aorta te hi Right Ventricle nen an inzawm kim emaw, a then emaw an inzawm vek a ni. Tichuan, Left Ventricle hi thisen kalna bulpui engmah nen a inzawm lo emaw, a then tlemte chauh a inzawm emaw a ni.
A awlsam zawngin, taksa pum puia oxygenated thisen phurtu aorta leh lung-a deoxygenated thisen phurtu pulmonary artery te hi hmun khat, right ventricle atanga lo chhuak an ni. Hei hi pianpui thinlung natna a ni.
Hei hian zawhna pahnih a siam a:
1. Oxygen tamna thisen thianghlim, taksa peng dang pan tura kal ngai chu oxygen tlachham, thisen thianghlim lo nen a inpawlh a.
2. A mamawh aia tam lungah thisen pump lut a ni. Hei hian thinlung leh lungah pawh harsatna nasa tak a siam a ni. Hun kal zelah heng taksa peng hrang hrangte hi a chhe thei hle.
DORV chungchangah hian eng harsatna dang nge hmuh theih?
DORV vei naute hian nau piangah harsatna dang an tawk fo thin. Chung zinga ṭhenkhat chu:
- Ciliary dysfunction: Naute thawkna kawng nalh tak tak, sam ang chi te hnathawh danah harsatna a awm.
- Heterotaxy a awm dan: 1.1.Naute taksa peng hrang hrangte chu a rilru leh a pum chhunga awmte chu an awmna pangngai ni lo hmun dangah an dah a ni.
- Intestinal malrotation: Naute intestines a inthlak danglam dan pangngai lo.
- Pulmonary stenosis: Ventricle dinglam leh pulmonary artery inkar valve a tawi emaw a tawi emaw.
- Ventricular hypoplasia: Thinlung chamber pakhat emaw pahnih emaw chu a tlangpui aia te zawk a ni.
DORV chi hrang hrang a awm em? Engtin nge hengte hi an thliar hrang theih ang?
Ni e, DORV hi chi hrang hrang a awm. He classification hi thil pawimawh tak pakhatin a hril a ni. Chu chu DORV vei naute zawng zawng deuhthaw hian thinlung chamber pahnih inkar bangah khur an nei vek bawk (Ventricular Septal Defect - VSD). He khur hian chamber pahnih inkarah thisen a kal leh chhuak thei lo.
Doctor-te chuan DORV hi VSD, a nih loh leh hole awmna hmun a zirin an classified a.
| DORV Type a ni | Hrilhfiahna awlsam tak |
|---|---|
| DORV chu subaortic VSD nei a ni | Thinlung khur (VSD) hi aorta hnuaiah a awm a. |
| DORV hi subpulmonary VSD (Taussig-Bing) nei a ni. | Thinlung khur hi pulmonary artery hnuaiah a awm a. Hei hi Taussig-Bing condition an ti bawk. |
| DORV chu double committed VSD nei a ni | He hole hi thisen kalna kawng lian pahnih (Aorta leh Pulmonary Artery) hnuaiah a awm a. |
| DORV chu noncommitted (remote) VSD nei a ni | Chu khur chu heng thisen kalna kawng lian pahnih atanga hla takah, inzawmna nei lo hmunah a awm a ni. |
Hei hi eng chi nge tih chiang taka hriat hi enkawlna ruahmanna atan a pawimawh hle.
Nu leh pa, heng symptoms te hi fimkhur rawh u!
DORV natna lan chhuah dan hi pian hnu ni engemaw zat emaw, kar hmasa emaw chhungin a lang tlangpui. Hengte hi i fimkhur hle tur a ni.
| Symptom a ni | Hei hian eng nge a awmzia? |
|---|---|
| Blueness (Cyanosis) tih hi a ni. | Naute vun, hmui emaw, kut zungtang emaw chu a sen emaw, a sen emaw a lo ni thei. Hei hi thisenah oxygen tlakchham vang a ni. |
| Thâwk harsa | Thâwk chak tak, rang taka thawk (tachypnea) emaw thawk harsa tih hriatna. |
| Ei/in harsatna | Bawnghnute in duh lo va, tlem tal in pawh nise, rei vak lo hnuah i chawlhsan mai ang. Hei hian taksa rihna a ti tlem thei bawk. |
| Thinlung Murmur | Doctor-in stethoscope hmanga thinlung a endik hian a lungphun bâkah thawm danglam tak a hre ṭhin. |
| Lung natna chak tak (Tachycardia) . | Heart rate hi minute khatah beat 100 aia chak zawk. |
| Thaw hah lutuk | Naute chu a thawmhnaw a thawk nasa hle a, a bik takin hnute a pek hian a thawk a hah hle. |
| Mutthilh lohna danglam tak | Naute chu a muhil reng a, nunna nei lo a ni. |
Eng thilin nge he dinhmun hi a thlen? Eng harsatna nge thleng thei?
Dik tak chuan zirchiangtute chuan DORV hi a chhan chiang tak an la hmu lo. Mahse, he natna vei naute zinga 50% vel chuan an chromosome, kan genetic information (DNA) hmun thenkhatah hian danglamna chi khat an nei tih hmuhchhuah a ni.
Mahse hei hi hre reng ang che. Hei hi i sualna a ni lo, i sualna a ni lo. Chuvangin ngaihtuah ngai suh la, nangmah leh nangmah mawhpuh rawh.
DORV hi uluk taka enkawl a nih loh chuan hun kal zelah harsatna a awm thei a ni.
- Thinlung thawk mumal lo (Arrhythmias) .
- Heart valve chungchangah harsatna a awm
- Lung lam chak lohna
- Pulmonary hypertension a awm bawk
- Thinlung chhungril lam natna (Endocarditis) .
Doctor-te hian engtin nge DORV status hi an hriat theih?
A châng chuan, he thinlung natna chi hi naute pian hma pawhin, i naupai lai scan lai pawhin hriat theih a ni. Chumi atana hman tur special scan chu ``Fetal Echocardiogram'' an ti a.
Chutiang chu a theih loh chuan doctor-te chuan a hmaa kan sawi tawh symptoms te kha naute pian hnua a lo lan hunah chauh hei hi an ringhlel ang. Tichuan naute chu an enfiah ang.
- Naute vun chu a sen deuh tawh em tih enfiah thin ang che.
- Thinlung chu stethoscope hmangin ngaihthlak a ni a, ri dik lo (murmurs) a awm leh awm loh enfiah a ni.
- Pulse Oximetry hi naute thisena oxygen awm zat tehna a ni a, naute kut zungtang emaw beng emaw-ah clip ang chi thil te tak te dahin, naute thisenah oxygen awm zat tehna a ni. Hei hi test awlsam tak a ni a, naute a ti na lo.
Heng test hmasa berte hnuah hian test eng emaw zat tih belh lehin a natna hmuhchhuah a ni thei bawk.
- Noninvasive imaging test: CT scan, MRI scan, leh X-ray naute taksa pawn lama tih a ni.
- Electrocardiogram (ECG or EKG): Natna nei lo test, thinlung electric hnathawh dan tehna a ni.
- Echocardiogram (echo): Hei hi thinlung scan ang a ni. Sound wave hmangin thinlung chungchâng zawng zawng, a pianzia te, a hnathawh dân te, leh a thisen kalna kawngte inzawm dân te pawh chiang takin a hmu thei a ni.
- Cardiac catheterization: Hetah hian naute kawchhung emaw, a kut emaw chhunga thisen kalna kaltlangin thinlungah tube (catheter) te tak te tak te dahin, chu chuan thinlung pressure, oxygen level leh structure chungchangah information dik tak a hmu thei a ni.
Lungngai suh, hei hi enkawl dan tur a awm! - Surgery chungchang i zir ang u
DORV vei naute zawng zawng deuhthaw chu an dam kum khatnaah open-heart surgery an mamawh ang. Hei hi i tan chuan hlauhawm takin a ri mai thei. Chu chu thil pangngai a ni. Mahse, tunlai damdawi lam thiamna hmang hian heng surgery te hi hlawhtling takin tih theih a ni tih hre reng ang che.
I doctor leh cardiac surgeon te chuan surgery chungchanga thutlukna an siam hunah thil engemaw zat an ngaihtuah ang.
- Naute DORV type chu eng nge ni?
- Naute thinlungah emaw, taksa peng dangah emaw harsatna dang a awm leh awm loh.
- Naute hriselna zawng zawng.
Surgery chi hrang hrang tih tlangpui a awm a.
- Intraventricular repair: Hetiang tihnaah hian surgeon chuan VSD, a nih loh leh thinlung chhunga khur kaltlangin tunnel a siam a, chu chu patch bik hmangin a siam a ni. He tunnel hian left ventricle atanga aorta thlenga thisen kalna tur kawng a siam a ni.
- Biventricular repair emaw arterial switch: Naute ventricle pahnih a dinhmun a tha a, DORV chu subpulmonary VSD (Taussig-Bing) type a nih chuan surgeon chuan aorta chu la chhuakin left ventricle nen a thlunzawm thei a ni.
- Univentricular repair (Fontan operation): DORV hi a buaithlak hle a nih chuan surgeon chuan he surgery hi a rawt thei ang. Hei hian taksa hnuai lam atanga oxygen tlachham thisen direct-a lung lam pan a huam a ni. Hei hi surgery buaithlak tak a ni a, stage engemaw zat a awm a ni.
Lung surgery eng pawhah hian hlauhawmna a awm. Chung zingah chuan thisen chhuah, thisen zam, natna hrik, leh anesthesia lama harsatna te a tel. Mahse doctor-te chuan heng hlauhawmnate hi tih tlem tumin theihtawp an chhuah thin.
Surgery hnuah nun chu eng ang nge ni ang?
Surgery zawhah naute chu kar khat emaw a aia rei emaw damdawi inah a awm a ngai dawn a ni. Operation chi hrang hrang leh naute dinhmun a zirin hun rei zawng chu a inang lo ang.
A pawimawh ber chu operation hnuah DORV vei naute tam zawk hi puitling nun hrisel, pangngai takin an nung thei a ni.
Mahse thil pakhat hriat reng tur chu DORV surgery nei tawh chu a dam chhung zawng cardiologist enkawlna hnuaiah a awm reng tur a ni. Hun ruat anga check-up neih a, a tul anga test neih a pawimawh hle.
Mi thenkhat chuan operation an neih hnu kum tam takah pawh heartbeat mumal lo emaw heart problem emaw an nei thei a, chuvangin i hriselna enkawl reng a pawimawh.
Doctor hmuh hun tur leh ETU pan hun tur
Operation hnuah pawh i fa chu ngun takin en reng ang che. A hnuaia symptoms te hi a lo lang a nih chuan doctor hnenah hriattir nghal tur a ni.
- Lungphung pangngai lo, rang tak emaw, na tak tak emaw i hriat chuan.
- I rilru a na emaw, thawk harsatna emaw i neih chuan (hengte hi heart attack chhinchhiahna a ni thei).
A hnuaia thil thlengah hian nausen chu damdawi in hnai ber Emergency Treatment Unit (ETU)-ah tlai lovin hruai thin tur a ni.
I fain thawk harsatna nasa tak a neih a,/ emaw an kut zungtang, hmui, emaw vun emaw a sen tih hriat theih a nih chuan ETU-ah kal nghal rawh!
Doctor zawh tur zawhna pawimawh
I naute hian DORV a vei tih i hriat chuan zawhna tam tak neih hi thil pangngai a ni. Nangmah ah engmah dah suh. I doctor hnenah engkim zawt la, hrilhfiah rawh. Zawhna i zawh theih ṭhenkhat chu hetiang hi a ni.
1. Ka fa hian eng DORV nge a neih?
2. Eng ang surgery nge neih i duh?
3. Engtikah nge surgery hi tih tur?
4. Surgery neih hian eng hlauhawmna nge a neih?
5. Surgery neih loh hian eng hlauhawmna nge a neih?
6. He operation hnuah hian ka fa hian operation tam zawk a mamawh dawn em?
7. Ka fa hian a dam chhungin damdawi a ei a ngai dawn em ni?
Hetiang zawhna zawta engkim i hriat chian hunah chuan hlauhna awm lovin thutlukna dik tak i siam thei tawh ang.
Take-Home Thuchah a ni
- Double Outlet Right Ventricle (DORV) hi pianpui thinlung natna khirh tak, mahse enkawl theih a ni.
- Hetiang dinhmun hi a chhan dik tak hriat a nih loh avangin, hei hi nu leh pa i nih angin i sualna a ni tih ngaihtuah ngai suh.
- A hmaa hriatchhuah leh a hun taka zai hian naupangte chu hrisel, dam rei theihna hun remchang a pe a ni.
- Operation hnuah chuan i dam chhung zawng cardiologist enkawlna hnuaia awm a ngai a ni.
- Emergency warning signs, thawk harsatna nasa tak leh vun sen hring ang chi te chu fimkhur reng ang che. Chutiang a nih chuan naupang chu Emergency Treatment Unit (ETU)-ah hruai nghal tur a ni.
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