He cancer hmuh tur awm lo DSRCT an tih hi i hre tawh em? (Desmoplastic Small Round Cell Tumor) A chipchiar zawkin sawi ila!

Vawiin hian cancer chi khat, a buaithlak deuh leh hmuh tur awm lo tak chungchang kan sawi dawn a ni. Chu chu Desmoplastic Small Round Cell Tumor, a nih loh leh Doctor-te’n an tih angin DSRCT an ti a. He hming hi i la hre ngai lo mai thei, a chhan chu mi tlemte chauh vei natna a nih vang a ni. Mahse chutiang dinhmun hriat reng chu keimahni leh kan hmangaihte tan chuan a pawimawh hle thei a ni.

Chuti a nih chuan he DSRCT hi eng nge ni?

A awlsam zawngin, DSRCT hi cancer natna lian tham tak tak thlentu natna a ni . Hei hi soft tissue sarcoma category ah a tel a ni . Chumi awmzia chu heng tumor te hi kan taksa peng nem tak, ruh nei lo, taksa ruh, thau leh nerve-ah te a awm thei tihna a ni. Mahse, DSRCT-ah chuan heng tumor te hi kan pum chhung (peritoneum) khuh tu membrane-ah an lo thang lian ber a ni. Ngaihtuah teh, hei hi kan pum chhunga taksa peng hrang hrang, thin leh intestines ang chi te humhimtu, membrane te tak te a ni. Chuvangin hetah hian chu cancer cell te chu an inthen chak hle a, tumor an siam tan thin.

He natna hi tu chungah pawh lo awm thei mah se, tlangval kum 20 leh 30 inkarah hmuh tur a tam ber a, chu chu mak a ti lo em ni? Hei hi enkawlna a awm a, a châng chuan a lan chhuah dân chu a bo a, natna chu test-ah hmuh theih a ni a, chu chu remission-ah a ni . Mahse, thil lungchhiatthlak tak chu hetianga tihtlem tawh natna hi a lo lang leh a, chu chu a lo lang leh mai thei tihna a ni .

He natna hi DSRCT an tih hi engtiang chiahin nge a tlem?

I ngaihtuah phak lo khawp mai. Kum 1989-a zirchiangtute’n he natna hi an hmuhchhuah hmasak ber aṭang khan khawvel puma mi maktaduai khat zinga 1 velin he natna hi an hmuchhuak tawh a ni. Chumi awmzia chu, Sri Lanka rama mihring awm zat nena khaikhin chuan kum engemaw zat chhungin vawi khat pawh mi hmuh a harsa tihna a ni. Chutiang khawpa rare chu a ni.

DSRCT natna lan chhuah dante chu engte nge ni?

A tam zawkah chuan pum chhunga tumor lo thang lian te hian a lian lutuk a, pum chhunga hmun a luah a, chaw ei dan a nghawng hma loh chuan symptom lian tham a nei lo. Mahse, a lan chhuah dan tlangpui tlemte hmuh theih a awm a:

• Pum natna: Pum natna awm reng, a chang chuan a zual zel.
• Constipation: Bowel movement mumal neih harsat.
• Diarrhea: Luak chhuak.
• Distended belly: Pum chu a lianin a hring chhuak niin a lang.
• Nausea leh vomiting: Chaw ei duh lohna a awm a, chu chu nausea leh vomiting nen a inzawm a ni.
• Sawifiah loha taksa rihna tihtlem: Ei leh in lama khapna bik awm lovin a taksa rihna tlahniam nghal.

Tunah chuan en teh, heng thil, chaw ei kham, ril\am, leh rilru hahna te hi kan vei tlangpui natna tenauah te pawh kan hmu thei a ni lawm ni? Chuvangin heng symptoms te hi i neih vang mai maia natna khirh tak hlauh hi thil tha a ni lo.Mahse, heng symptoms te hi ni rei lo te aia rei emaw, a na zual emaw a nih chuan Doctor rawn pan hi a finthlak hle ang.

Engvangin nge he DSRCT hi a lo awm? Eng nge a chhan?

Zirchiangtute chuan DSRCT hi kan cell-a chromosome inthlak danglam vang a ni tih an hmuchhuak a. He inthlak danglamna hian gene danglam tak EWS-WT1 tih a siam a ni. He gene hian cancer cell te chu a ti thang lian thin a ni. Mahse, heng chromosome te hi engvangin nge hetiang hian an inthlak danglam tih erawh hriat chian a la ni lo. Chu chu heng natna hrang hranga thil buaithlak ber chu a ni.

Engtin nge doctor-te hian he DSRCT natna hi an hriat chhuah?

Chu chu hriat chian nân doctor-te chuan test engemaw zât an hmang khâwm a, thutlukna an siam a ni:

• Taksa enfiahna: A hmasa berin doctor chuan i pum chu a hre ang a, eng emaw i hriat theih leh theih loh a en ang a, chu chu lumps ang chi hi a ni.
• Imaging test: Chung zingah chuan CT scan , MRI scan , leh ultrasound test te pawh a tel. Chûngte chuan peritoneum-ah tumor a awm leh awm loh, a lian zia leh hmun dangah a darh leh darh loh hriat theih nân a ṭanpui thei a ni.
• Genetic tests: Heng test te hian a hmaa kan sawi tawh EWS-WT1 genetic mutation hi a awm leh awm loh finfiah nan a pui thin. Hei hi DSRCT a nih leh nih loh dik taka hriat theihna chu a ni.

DSRCT enkawl dan tur chu engte nge ni?

Doctor-te chuan DSRCT enkawlna atan hian kawng hrang hrang an hmang a. A bulpui berte chu:

• Surgery: Cancer tumor tam thei ang ber surgery hmanga lakchhuah.
• HIPEC (Hyperthermic Intraperitoneal Chemotherapy): Hei hi a specialized deuh deuh a ni. Tumor chu surgery hmanga lakchhuah a nih hnuah, chemotherapy damdawi lum tak tak chu pum chhungah an inject a, cancer cell la awm zawng zawng chu an tichhe vek a ni.
• Chemotherapy: Damdawi chak tak, cancer cell tihchhiatna atana taksa tana pek thin a ni.
• Radiation therapy: Cancer cell tihchhiat nan high-energy rays hman a ni.

Heng enkawlnate hian natna hi remission -ah a dah thei a, chu chu symptoms a awm lo tihna a ni a, test engmahin natna hi a hmu thei lo tihna a ni. Mahse, he remission hi a rei lo fo thin. Natna hi a lo lang leh thei a, chuvangin enkawlna thar emaw, enkawl dan hrang hrang emaw tan a ngai mai thei.

Pawimawh: Eng enkawlna pawh dawng ila, i medical team atanga palliative careChumi chungchang chu zawt ngei ang che. Hei hi natna avanga taksa natna leh rilru hahna tihziaawmna tur leh he natna hi a tha thei ang bera nunpui theihna tura i mamawh damdawi lam, khawtlang leh rilru lam tanpuina pekna tur a ni. Hei hi cancer tidam thei damdawi a ni lo va, mahse i nunphung chu nasa takin a tichangtlung thei a ni.

Enkawlna hian side effect a nei em?

Ni e, operation te, chemotherapy te, leh radiation therapy te hian side effect a nei vek thei a ni. DSRCT tumor lakchhuahna atana operation i neih hnuah chuan general anesthesia emaw thisen chhuah emaw avanga thil tha lo (side effects) i nei thei a ni. Radiation therapy leh chemotherapy hmanga side effect awm tlangpui chu:

• Kawthalo
• Chau
• Nausea leh luak chhuak

Heng side effects te hi mi zawng zawng tan a awm dan inang vek lo, mi thenkhat chuan an tawng tlem thei a, thenkhat chuan an tawng tam zawk thei bawk. Hemi chungchang hi i doctor chuan a hriattir ang che.

DSRCT-ah hian damlo prognosis chu eng nge ni?

Hei hi sawi harsa ber a ni a, mi zawng zawngin an hriat duh ber a ni. Prognosis hi doctor ten enkawl hnua i beisei theih an tih hi a ni. He thutlukna hi cancer awmna hmun, a darh tawh leh tawh loh, operation neih laiin engzat nge lak chhuah tih te a zirin an siam thin.

DSRCT hi cancer hmuh tur awm lo tak a nih avangin zirchianna a tlem em em a ni. Chuvangin doctor tan chuan eng nge i beisei theih ang tih leh eng chen nge i dam theih ang tih chiang taka sawi a harsa hle. Hei hi thinlung ti na tak a ni.

Tuna data atanga a lan dan chuan DSRCT natna hmuhchhuah hnua kum nga chhunga dam rei zat chu 15% leh 38% inkar a ni . Chumi awmzia chu mi zawng zawng an dam leh vek dawn lo tihna a ni. Mahse, zirchianna pakhatah chuan metastatic DSRCT vei zinga za zela tlemte chu enkawlna hmangin an dam vek tih hmuhchhuah a ni. Tin, cancer a darh hmaa enkawl zinga 60% vel chu kum nga hnuah an dam tawh bawk. Chuvangin, a hmaa hriatchhuah a, enkawlna tan thuai a pawimawhzia chu i hmu thei a ni lawm ni?

Hetiang dinhmun hi engtin nge ka in enkawl ang?

DSRCT hi cancer hmuh tur awm lo leh na tak a ni. Enkawlna hnu thla emaw kum tam tak emaw hnuah a lo let leh thei a ni. Cancer lo kir leh hlauhna nena nun chu thil awlsam a ni lo. Mahse, he zinkawngah hian i tanpui thei tur thil tlemte a awm a:

• I dinhmun hrethiam rawh: DSRCT hi a tlem avângin, a chungchânga thu dik leh hunbi neia hmuh chu a harsa thei hle. Chuvangin, i medical team-te chu eng nge an beisei tih zawt hreh ngai suh. Nang leh i dinhmun hi an hre chiang ber.
• Clinical trial-a tel chungchang zawt rawh:Researcher-te chuan DSRCT enkawl dan thar an test mek a ni. Clinical trial ah i tel thei em tih doctor zawt rawh .
• Cancer damchhuak hi ngaihtuah teh: I natna hmuhchhuah ni atang khan i dam chhung zawngin indotu leh damchhuak i ni tawh a. I medical team hnenah cancer vei leh tawhte tana programme bik chungchang zawt rawh.
• Ṭanpuina dawng rawh: I medical team-te hnenah cancer natna hlauhawm tak nei te tanpuitu pawl chungchang zawt rawh. Nangmah ang bawka thil tawn tawh, emaw, thil tawn ang chi nei tawhte nena hun hman leh inbiakna neih hian DSRCT hmanga nunpui avanga mahni chauhna thenkhat tihziaawmna a pui thei a ni.

Engtikah nge ka doctor ka hmuh leh ang?

DSRCT hi a lo lang leh thei fo thin. Chuvangin, i doctor chuan thla thum atanga thla ruk danah imaging test (CT scan ang chi) hmangin i pum chhunga lining emaw hmun dangah emaw tumor thar a awm leh awm loh enfiah turin a rawt thei ang. Heng follow-up checkup te hi tlawh loh a pawimawh hle.

Doctor hnenah eng zawhna nge ka zawh ang?

Hetiang hunah hian zawhna tam tak i nei mai thei. Vawikhatah engkim hriatthiam a har khawp mai. Hlauthawng suh, heng zawng zawng hi tlem tlem in zir rawh. A bul tanna atana zawhna i zawh theih thenkhat chu hetiang hi a ni:

• Engtin nge ka natna lan chhuah dan hi he DSRCT an tih natna avanga lo awm a ni tih chiang taka ka hriat theih ang?
• Hei hi enkawlna hmangin a dam kim thei ang em?
• Eng enkawlna nge i rawt?
• Chutiang enkawlnate chuan eng side effect nge a neih?
• Clinical trial-a tel hi ka ngaihtuah tur em ni?

DSRCT i vei tih hmuhchhuah a nih chuan nun tidanglam thei thil a ni thei. Emotion-in a hneh hle tih i inhria mai thei. A hnua thil thleng tur te, enkawl dan tur te, leh i hmalam hun tur te chu i ngaihtuah hle mai thei. Khawvela mi za zela tlemte chauh vei natna chungchanga hriat tur hmuh chu a lungchhiatthlak thei bawk.

I medical team hian heng rilru put hmang zawng zawng hi an hrethiam vek a ni. I chunga thil thleng leh a hnua thil thleng thei tur hriatthiam nan i mamawh ang zat hun an pe ang che. Anmahni biak leh zawhna i neih apiang zawt hlau suh.

Take-Home Thuchah hnuhnung ber

Hetiang dinhmun DSRCT an tih hi i hriat hian i rilru a hah lutuk hi thil pangngai a ni. Mahse, heng thute hi hre reng ang che:

• DSRCT hi cancer hmuh tur awm lo leh na tak a ni. Chu chu hriat hmasak a pawimawh.
• Symptoms te chu fimkhur rawh. I pum na reng reng, i pum puar, emaw, i taksa rihna tlahniam emaw i neih chuan doctor rawn la.
• Hriat hmasak leh enkawl vat a pawimawh. Hei hian natna kal dan chu eng emaw chen a thlak danglam thei a ni.
• Nangmah chauh i ni lo.Medical team, chhungkua leh support group te chu i tanpui turin an awm reng a ni.
• Palliative care hi ngaihtuah ngei ang. Hei hian i nunphung nasa takin a tichangtlung thei a ni.
• Zawhna zawh hreh suh. I doctor hnen atangin engkim chiang takin i hre vek tur a ni.

He thu hian he natna hlauhawm tak hi hriatthiamna engemaw chen i neih theih nan a puih ngei kan beisei. Eng harsatna pawh hmachhawn tur chuan awareness hi chakna lian ber a ni tih hre reng ang che.

` DSRCT, Desmoplastic Small Round Cell Tumor, Cancer, Pum Cancer, Cancer Rare, Cancer Symptoms, Cancer Enkawlna, Peritoneum Cancer