I taksa peng pakhat, i kawr, i kut, i ke emaw, i mitmeng emaw pawh ni se, a rawn inher nghal vat a, a rawn inher chhuak a, a nih loh leh hmun engemaw takah a tang mai mai ang tih i inhriat ngai em? Hei hi thil nuam lo tak, a chang chuan hrehawm tak a ni thei bawk. Hetianga taksa ruhte hi thunun theih loha an che hi thil pangngai a ni lo. Vawiin hian neurological condition dystonia tih kan sawi a, chu chuan heng symptoms te hi a thlen a, mahse khawtlang nunah chuan sawi a hlawh lo hle.
Dystonia hi eng nge ni tak tak?
A awlsam zawngin sawi ila, dystonia hi thluak lam natna a ni a, chu chuan chetna a tichhe thei a ni. Kan taksa peng hrang hrangte inzawmkhawm leh tih hahdam dan hi thluak atanga signal lo chhuak hian a thunun a ni. Mahse, dystonia-ah chuan thluak thuk tak, chetna thununtu basal ganglia-a nerve cell-te inbiakpawhna lamah harsatna a awm a. Chumi avang chuan taksa pengte hian signal dik lo an dawng a, thunun theih lohvin an inzawm khawm thin. Hei hian taksa peng hrang hrang a tikehsawm a, a tizau a, hmun khatah a tang a ni.
Hetiang dinhmun hian taksa peng pakhat emaw, taksa peng pakhat emaw, taksa pum pui emaw a nghawng thei a ni. Mi thenkhat chuan condition pahnih dystonia leh dyskinesia te hi an ti buai hle. Dyskinesia hi dystonia chi khat a ni bawk a, chu chu duh loh zawnga, taksa peng hrang hrang (muscle contraction) avanga chetna (jerking movement) pawl a ni.
Dystonia natna lan chhuah dan chu engte nge ni?
A symptom ber chu control theih loh muscle contraction a ni. Chungte chu a na lo hle atanga na tak thlengin a awm thei. Heng symptoms te hi hun kal zelah a na zual tlangpui.
A tir lama hmuh theih symptoms tlanglawn thenkhat chu hetiang hi a ni:
- Kal laiin ke pakhatin a hrual ang maia hriat.
- Kephah hnuai lam a hrual fo thin.
- Thunun theih lohvin a kawr chu a sir khatah hrual emaw, a hrual emaw.
- Thunun theih loh khawpin a mit a chhing.
- Thusawi harsa.
- Thuziak i tan hnuah i kutziak a buai emaw, i kut a na tan emaw a ni.
- Taksa peng hrang hrang a nghing.
Heng symptoms te hi stress emaw hah emaw lai hian a lo lang thei a, a na zual thei bawk. Heng damlote hian taksa ruh (muscle contraction) reng reng avang hian natna leh hahna an nei bawk.
He natna hi a lo awm kum a zirin a natna lan chhuah dan hi a inang lo.
- Naupan lai chuan:A lan chhuah dan hi kut emaw ke emaw atanga tan a ni tlangpui a, mahse hun kal zelah taksa pumpuiah a darh thei a ni.
- Tleirawl puitlingah: A lan chhuah dan hi taksa chunglam (e.g., kawng, kut) atanga tan a ni tlangpui. Symptoms chu a darh zauh zauh a.
Dystonia hi engte nge ni?
Dystonia tam zawk hian chhan chiang tak an nei lo a, mahse doctor-te chuan he natna hi chi thum-ah an ṭhen a ni.
1. Genetic Dystonia natna (Genetic Dystonia) a awm thin
Hei hi nu leh pa hnen atanga kan rochun genes-a chhiatna awm vang a ni. Dystonia nena inzawm gene engemawzat hmuhchhuah a ni tawh bawk. Entirnan, DYT1, DYT5, leh DYT6 ang chi gene-a mutations hian he natna hi a thlen thei a ni. Heng chi thenkhat hi naupan lai atanga tan a ni thei a, rualbanlohna nasa tak pawh a thlen thei bawk.
2. Dystonia (Dystonia) a neih tawh
Hei hi secondary dystonia an ti bawk. Thluak peng pakhat basal ganglia tihchhiat avanga lo awm a ni. He chhiatna hi thil hrang hrang atanga lo awm thei a ni:
- Brain Trauma a ni
- Thai
- Thluak natna (brain tumor) a awm
- Pian tirh emaw, hun dang emawa thluaka oxygen tlakchhamna
- Thluak natna a awm
- Carbon monoxide emaw, lead ang chi metal rit tak tak emaw ei avanga poisoning awm. (Poisoning i rinhlelh chuan Colombo National Hospital-a National Poisons Information Center-ah zawh nghal rawh.)
- Damdawi thenkhat (Tardive Dystonia) avanga thil thleng. Chungte chu hun eng emaw chen atan a ni tlangpui.
3. Idiopathic Dystonia natna a awm thei
Idiopathic tih thumal hi "a chhan hmuh tur a awm lo" tihna a ni. Dystonia vei tam tak chuan chhan hriat lohvin he natna hi an nei thin.
Dystonia chi hrang hrangte chu engte nge ni?
Dystonia hi taksa peng hrang hrang a nghawng dan azirin chi hrang hrangah then theih a ni. He classification hi hriatthiamna hian i dinhmun hi a hrethiam zawk ang.
| Dystonia chi hrang hrang | Hrilhfiahna |
|---|---|
| Cervical Dystonia a awm thin | Hei hi a tam ber chi a ni. Torticollis tia koh bawk a ni a, kawr ruhte a nghawng a, lu chu a sir khatah a hruai a, a tikehsawm a, hmalam emaw hnunglam emaw a tilt a ni. |
| Blepharospasm a ni | Mit vel muscle te a nghawng a ni. Thunun theih loh mitmeng atanga tan a ni a, a chang chuan mit chu nghet takin a inkhar reng thei bawk. Hmuh tha viau mah se, mit a khap tlat a, mi mitdel ang maiin a lang. |
| Laryngeal Dystonia a awm thin | Thusawi puitu i rilru chhunga vocal cords ruh (muscles) te a nghawng a ni. I aw chu a chak lo thei a, a bengchheng thei a, a nih loh leh thawm ri a nei thei a, chu chuan mi dangte hriatthiam a ti harsa thei a ni. |
| Oromandibular Dystonia natna a ni | Kan hmui, hmui leh lei ruhte a nghawng a, tawng leh ei harsat phah a ni. |
| Hnathawh tur bik Dystonia | Hei hi hna bik (specific repetitive task) neih lai chauh a thleng thin. Entirnan, writer’s cramp, ziak lai chauha lo awm, emaw, musical instrument tumtute’n an tawn hrehawmna emaw te hi a ni. |
Dystonia hi eng enkawlna nge ni?
Dystonia hi damdawi a la awm lo. Mahse, natna lan chhuah dan control thei tur leh nun awlsam zawka siam thei tur enkawlna tha tak tak engemaw zat a awm. I doctor chuan i tana enkawlna tha ber tur a ruat ang.
Damdawi chi hrang hrang
Damdawi chi hrang hrang a awm a, chu chuan thluaka signal dik lo thawn chhuah a tihtlem avangin taksa ruh inzawmna (muscle contraction) control-na a pui a ni.
- Dopamine system tichhe thei damdawi: `Levodopa` ang chi damdawi.
- Anti-cholinergic damdawi: `Trihexyphenidyl` ang chi damdawi.
- GABA regulating drugs: Damdawi `Baclofen`, `Clonazepam` ang chi te.
- Botulinum Toxin Injection hmanga tihdam theih a ni.Hei hi thil tam takah chuan enkawlna tha ber pakhat a ni. `Botox` tia hriat a ni. Hei hian he damdawi hi a natna taksa peng (muscle)-ah direct-a inject a ngai a ni. Hei hian hun engemaw chen chu ruh chu a tichak lo va, duh loh zawnga inzawmkhawmna chu a titawp bawk. He injection hi doctor thiam takin thla 3 danah vawi khat vel pek tur a ni.
Inzai
Damdawi hmanga thunun theih loh natna khirh tak takah chuan zai hi ngaihtuah a ni.
- Deep Brain Stimulation (DBS): Hei hi thluak natna hmunah electrode dahin, a rilru vun hnuaia battery nen inzawm tir a ni. He electrode atanga electrical pulse fiah lo tak tak chhuak hian thluaka signal pangngai lo te chu a control a, taksa ruh inzawmna a ti tlem bawk.
Therapies dangte pawh a awm
- Physical Therapy: Taksa tichak turin a pui a, stretching exercise a ti a, range of motion a ti sang bawk.
- Occupational Therapy: Nitin hna hrang hrang, incheina leh ei leh in awlsam zawka i tih theih nan a pui thin.
- Speech Therapy: Aw lama harsatna nei te chu awlsam zawka tawng turin a pui thin.
In lama i tih theih thilte
Damdawi lam enkawlna bakah hian natna lan chhuahna tihziaawmna turin nangmah ngeiin i tih theih tur thil engemaw zat a awm bawk.
- Muscle naah compress lum emaw cold emaw hmangin hnawih thin ang che.
- Stress tihziaawm rawh. Thâwk thûk taka exercise leh meditation ang chi thilte hian a ṭanpui thei a ni.
- "Sensory tricks" an tih hi han ti ve teh. Mi thenkhat chuan an taksa peng emaw, an bula hmun emaw chu zawi zawiin an khawih a, chu chu rei lo te chhung atan an inher emaw, an inhnek emaw chu an titawp thei a ni.
- Diet chungchangah chuan ei leh in pakhatin dystonia a nghawng tih finfiahna a awm lo. Mahse, caffeine hi a tichaktu a ni a, mi thenkhatah chuan symptoms a tipung thei a ni. Chuvângin, tea leh coffee ang chi thilte tihtlem chu i ngaihtuah mai thei. Mahse, ei leh in lama inthlak danglamna lian tham i tih hmain i doctor nen inbiakna neih hmasak phawt ang che.
Take-Home Thuchah a ni
- Dystonia hi neurological condition a ni a, thluak signals a malfunction vangin muscle te chu control theih lohvin an inzawm khawm thin.
- Hetiang dinhmun hi genetics vang emaw, thluak chhiatna vang emaw, chhan awm lo pawhin a awm thei a ni.
- Simptoms, kawng khar, duh loh vanga mit khar, leh ziak laiin kut natna te hi a lan chhuahna bulpui ber a ni.
- Damdawi, Botox injection, DBS surgery, leh physical therapy te ang chi enkawlna te hian natna lanchhuahna te chu tha takin a control thei a ni.
- Nangmah emaw i hriat miin emaw heng symptoms te hi i neih chuan a tha ber chu neurologist pan a, a diagnosis dik tak leh enkawl dan tur ruahmanna siam hi a ni.











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