I mit chu a sen vek tawh em? Liver-a inthlak danglamna tlemte pawh a ni thei: Gilbert’s Syndrome chungchang hi i zir dawn nia!

I mit var , leh a chang chuan i vun chu a sen deuh tih i hmu tawh em? A nih loh leh doctor-in i thisen test-naah bilirubin level a sang deuh tih a hrilh che em? I lungngai viau mai thei. Mahse, lungngai suh, a chhan chu a tam zawkah chuan chutiang chuan a pawi lo. Vawiin hian chutiang chiah chu kan sawi dawn a, chu chu Gilbert’s Syndrome an ti a ni.

`Gilbert-a Syndrome` hi eng nge ni?

A awlsam zawngin sawi ila, `Gilbert's Syndrome` hi genetic condition a ni a, kan thin hian `bilirubin` an tih thil pakhat chu a process tha thei lo. Ngaihtuah teh, kan taksaa thisen sen hlui (red blood cells) te hi a chhe vek hian thil sen (yellow substance) `bilirubin` an tih chu a lo chhuak thin. Hei hi bawlhhlawh a ni. Mi hrisel thin chuan he `bilirubin` hi a la a, a thlak danglam a, taksa atangin a paih chhuak thin.

Mahse Gilbert’s Syndrome vei teah chuan liver hian bilirubin tihchhiat pui thei enzyme chi khat a siam chhuak tlem hle. A dik tak chuan chu enzyme siamnaah chuan tlakchhamna tlem a awm a ni. Chuti a nih chuan eng nge thleng ang? Chu bilirubin chu taksaah a pungkhawm thin. Hetiang hian thisenah bilirubin level a san chuan damdawi lam chuan hyperbilirubinemia kan ti thin.

Chuti a nih chuan, he `Bilirubin` hi eng nge ni?

Bilirubin hi a hmaa kan sawi tawh ang khan kan thisen sen hlui te a chhiat chuan a rawng sen (yellow pigment) a ni a. Kan bile-ah a awm. Bile hi liver atanga tui lo chhuak a ni a, kan ei tur thau awmte chu a tithianghlim thei a ni. I hriat angin liver hi kan digestive system-ah hian organ pawimawh tak a ni. Thisen atanga toxins a filter a, thau a digest a, energy atana mamawh glucose chu glycogen angin a dahkhawm bawk.

Gilbert’s Syndrome hi engtiang chiahin nge a hluar?

Hei hi a takah chuan i ngaihtuah angin a tlem lo. United States ang ramah chuan mipui 3% leh 7% inkar velin he natna hi an vei nia chhut a ni. Tin, hmeichhia aiin mipa hian `Gilbert's Syndrome` an vei tam zawk bawk. Kum eng pawh ni se, hnam eng pawh a nghawng thei a ni.

Tuin nge `Gilbert's Syndrome` vei thei? Eng thilin nge a thlen?

Gilbert’s Syndrome hi thlahtute atanga lo chhuak a ni. Chumi awmzia chu nu leh pa a\angin fate hnenah a inthlunzawm tihna a ni. Kan mizia zawng zawng (entir nan, vun rawng , sam rawng, san zawng) ang bawkin, gene-in a hril a ni. Chutiang bawkin Gilbert’s Syndrome vei te pawhin UGT1A1 an tih gene bik pakhatah hian inthlak danglamna, a nih loh leh mutation an rochun thin.

A dik tak chuan `UGT1A1` gene hrisel tak hian a chunga kan sawi tak `bilirubin` chu tichhiain taksa atanga paih chhuaktu liver enzymes a siam chhuak thin. Mahse, `UGT1A1` gene-a mutation nei miah chuan he enzyme mamawh zat 30% chauh a siam chhuak thin. Chuvang chuan `bilirubin` chu bile nen a inzawm tha lo va, taksa a chhuahsan ta a ni. Chuvangin, chu extra `bilirubin` chu thisenah a pung khawm ta a ni.

`Gilbert's Syndrome` natna lan chhuah dan chu engte nge ni?

Mak tak maiin Gilbert’s Syndrome vei mi pathum zinga pakhat vel chuan symptom an nei lo. Thil dang thisen test an neih hunah chauh an dinhmun hi an hrechhuak ta a ni.

Mahse, natna lan chhuahna nei tak takte zingah chuan a lan chhuah tam ber chu jaundice, a nih loh leh jaundice hi a ni. Hei hi thisenah bilirubin level sang lutuk vang a ni. Jaundice hian i vun leh i mit var te chu a ti sen thei a ni. Mahse, he yellowing hian a tichhe lo hauh lo tih hre reng ang che.

A châng chuan, jaundice emaw Gilbert’s Syndrome vei te pawhin hetiang chi hi an nei thei bawk:

• Zun rawng dum emaw, leilung rawng emaw bawlhhlawh.
• Thil pakhata ngaihtuahna seng harsa.
• Luak chhuak tih hriatna .
• Digestive system lama harsatna: Entirnan, pum na, riltam, luak chhuak.
• Chau lutuk (chau) tih hriat.
• Flu -like symptoms, khawsik leh khawsik te.
• Chaw chu a thlum lo.

Eng thil nge Gilbert’s Syndrome symptoms tizual?

A hnuaia thilte hian Gilbert’s Syndrome vei thisenah bilirubin level a tisang thei a, jaundice a thlen thei a ni :

• Dehydration: Tui i in tam loh chuan. Hei hi kan ram khaw lum lai hian a thleng tam thei hle.
• Chaw nghei emaw chaw ei loh emaw: Chawhmeh ei loh emaw, chawhmeh ei tlai emaw ang chi thil.
• Natna emaw, hri kai emaw: Khawsik emaw, natna dang emaw pawhin bilirubin level a tisang thei a ni.
• Menstruation : Hmeichhia tan pawh heng symptoms te hi thlasik laiin a langsar zawk thei bawk.
• Thawhrim lutuk: I thawhrim reng hian inkhelh la, exercise la, hna rit tak tak i thawk bawk.
• Stress: Exam hnaih leh hnathawh mawhphurhna a san chhoh zel avanga pressure lo awm hian nghawng a nei bawk.

Ngaihtuah teh, tlangval naupang pakhat Nimal-a a awm a. `Gilbert's Syndrome` a vei tih a hre lo. Ni khat chu a thiante nen cricket an khel a, a thawmhnaw a thawk nasa hle a, tui a in tlem hle bawk. A tuk zingah chuan a nu chuan Nimal mitmeng chu a sen deuh tih a hmuchhuak a. Doctor hnena a hmuhtir chauh hian `Gilbert's Syndrome` a vei tih a hre ta a, ni khata hah lutuk leh tui tlakchham vangin a bilirubin level a sang tih a hre bawk.

Engtin nge Gilbert’s Syndrome hi an hriat theih?

Gilbert’s Syndrome hi genetic condition a ni a, chu chu pian tirh atangin a awm tihna a ni. Mahse thisen test-naah bilirubin level sang tak a awm hma chuan hriat lohvin a awm fo thin. Kum naupan lai, kum sawmhnih hnuai lam emaw, kum sawmhnih tir lam emaw, thil dang atana thisen test an tih hian hmuhchhuah a ni tlangpui.

Thisen test bakah hian hetiang test hi i nei thei bawk:

• Liver function test: Hengte hian i liver hnathawh that dan leh i bilirubin level engzat nge a nih tih an enfiah thin.
• Genetic test: Hei hian `Gilbert's Syndrome` thlentu `UGT1A1` gene mutation a awm leh awm loh dik takin a hriat theih.

Gilbert’s Syndrome natna avanga harsatna awm thei te chu engte nge ni?

Hetah hian a pawimawh ber chu: Gilbert’s Syndrome hi natna khirh tak a ni. Hun rei tak chhung harsatna leh hriselna lama harsatna lian tham a thlen lo. Chuvangin ngaihtuahawm tur a awm lo.

Gilbert’s Syndrome hi enkawlna tur a awm em? Engtin nge enkawl a nih?

Mit sen, emaw jaundice neih hi rilru lam hriselna ngaihtuahawm deuh a ni thei. "Aw, ka mit chu a sen a, tu pawhin engtin nge an ngaihtuah ang?" Mahse, jaundice emaw Gilbert’s Syndrome emaw hian enkawlna bik a mamawh lo.

Hei hi kan vun rawng ang a ni. Ṭhenkhat chu an fair hle a, ṭhenkhat chu an pale hle. Natna a ni lo. Chutiang chu a ni.

Gilbert-a Syndrome hi a veng thei ang em?

Gilbert’s Syndrome hi thlahtute atanga lo chhuak a nih avangin ven dan tur a awm lo.

Gilbert’s Syndrome vei tan chuan eng prognosis nge a awm?

Hei pawh hi chanchin lawmawm tak a ni. `Gilbert's Syndrome` vei te hi harsatna nei lovin dam rei tak, hrisel takin an nung thei a ni. Hetiang dinhmun avang hian hun rei tak chhung hriselna lama harsatna an nei lo.

Gilbert’s Syndrome chungchangah hian engtikah nge doctor i hmuh ang?

Hei hian a tlangpuiin enkawlna bik a mamawh lo nain, hetiang symptoms i neih chhunzawm zel chuan doctor pan a tha ang:

• Chaw ei lama harsatna awm reng (e.g., pum na, ril\am).
• Zun dum emaw, leilung hring hring emaw .
• Khawsik leh khawsik.
• Vun emaw mit emaw a sen reng emaw, a sen fo emaw (jaundice) .

Gilbert’s Syndrome chungchangah hian ka doctor hnenah eng zawhna nge ka zawh ang?

Gilbert’s Syndrome i vei tih i hriat chuan zawhna tam tak neih hi thil pangngai a ni. I doctor hnenah hetiang thil hi i zawt mai thei:

• Engvangin nge `Gilbert's Syndrome` ka neih?
• Hemi atan hian enkawlna ka mamawh em?
• Jaundice laka inven nan eng nge ka tih theih ang?
• Jaundice hi eng chen nge a awm?
• Ka chhungkaw member dangte hian Gilbert’s Syndrome an vei em tih hriat nan genetic test ka nei tur em ni?
• Complication chungchangah hian ka ngaihtuah tur em ni? (Hei hi low-risk procedure a ni tih kan hria a, mahse hriat a tha hle.)

A tawp berah chuan hriat reng tur tlemte (Take-Home Message) .

Gilbert’s Syndrome hi a na lo hle a, enkawl ngai lo a ni. Mit leh vun a sen fo hian a ti thinrim deuh thei a, mahse jaundice hian hriselna atan harsatna a thlen lo. He vun leh mit sen hring hi a bo tlangpui a . Gilbert’s Syndrome nena inzawm jaundice vei theihna tihtlem dan tur i doctor chuan a hrilh thei che a ni. Chuvangin, ngaihtuah lutuk suh. Nun hlim takin awm rawh!

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