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I fate hian an mitmengah hetiang danglamna hi a nei em? (Congenital Glaucoma) chungchang hi i zir dawn teh ang!

I fate hian an mitmengah hetiang danglamna hi a nei em? (Congenital Glaucoma) chungchang hi i zir dawn teh ang!

Kan fate mit kan en hian a chang chuan thil mak emaw, danglam emaw kan hmuchhuak thin a ni lawm ni? Nausen thenkhat mit chu a lian deuhin a lang a, a nih loh leh mittui a tla fo thin a, a êng en chu an duh lo. Chûngte chu a châng chuan thil awlsam tak leh thil pangngai tak a ni thei bawk. Mahse, chutih rual chuan, a chang chuan ngaihven tlem ngai thil pakhat chhinchhiahna an ni thei bawk. Vawiin hian mit natna, hetiang naupang te te, a bik takin an pian lai emaw, an pian tirh lamah emaw a lo awm thei a, mahse a hmaa hriat chian a nih chuan a thunun tha thei a, naupang mit hmuhna pawh a venghim thei tih kan sawi dawn a ni. Hei hi congenital glaucoma an ti a .

Congenital glaucoma chu eng nge ni?

A awlsam zawngin sawi ila, congenital glaucoma hi pian tirh emaw, naupan lai emaw (kum 2-3 chhunga) genetic factor thenkhat avanga awm thin a ni. Tunah chuan, "Glaucoma chu eng nge ni?" Glaucoma hi mit natna eng pawh, mit chhunga min puitu nerve lian ber, mit nerve tichhe thei tih hming tlanglawn tak a ni. He chhiatna hian zawi zawiin mit a tichhe thei a ni.

Naupang pianpui glaucoma vei te hian an mit chhungah pressure sang tak an nei a, chu chu ocular hypertension an ti a ni. Kan mit hian tui bik a siam chhuak a , chu chu aqueous humor tih a ni . He tui hi mit hriselna atana pawimawh tak a ni. A tlangpuiin he tui hi mit atang hian a lo chhuak a, a chhuak tha hle. Mahse, naupang pianpui glaucoma neiah chuan he tui hi a chhuak tha lo. Chumi hnuah chuan he tui hi mit chhungah a lo awm khawm a, mit chhunga pressure chu a pung zauh zauh a ni. Hetianga pressure sang hian a hmaa ka sawi tawh optic nerve chu a compress tir thin. Hun kal zelah hei hian mit pianzia pawh a tidanglam thei a ni. I fa mit chu a lian zawk tih i hmu mai thei a, a nih loh leh iris (mit chhunga rawng nei tak tak - iris) chu a thim a, a rawng a danglam thei bawk.

Hei hi enkawl theih natna a ni. Mahse, enkawl loh chuan mit a chhe zauh zauh thei a, mitdelna hial a thlen thei a ni. Chuvangin heng symptoms te hi hriat chian a, a rang thei ang bera enkawl tan a pawimawh hle. Chumi hnuah chauh chuan chhiatna chu a tlem thei ang bera, naupang mit hmuhna chu a theih ang anga venhim theih a ni ang.

He natna lan chhuah dan engte nge ni? Engtin nge kan hriat chian?

He natna lanchhuahna lian ber berte bakah hian chhinchhiahna dang a awm bawk.

A lan chhuah dan tlangpui pathum a awm a, chungte chu:

Heng mizia pathumte hi doctor ten an ngaihven ber a ni.

  • Mit mittui tla fo (Epiphora): A dik tak chuan naupang tap lo pawhin mit atang hian mittui a luang chhuak ang maiin a lang.
  • Photophobia: Naupang chuan pawn lama a chhuah dawnin êng êng tak, mit khap emaw, hmai hawi emaw chu a en duh lo mai thei.
  • Blepharospasm: Mitmeng chu a na hle ang tih a ni a, a nih loh leh mit khap tlat tum ang maiin a lang.

I hmuh theih chhinchhiahna dang:

  • Buphthalmos: Naute mit chu naute dang aiin a lianin a bulh zawkin a lang . Nu leh pa thenkhat chuan, "Naute mit chu bawng mit lian tak ang mai a ni," an ti.
  • Mitmeng blue appearance: Mit chhunga a var (sclera) chu a hnuaia membrane kaltlangin a lang thei a, chu chuan blue angin a lang thei a ni.
  • Cornea var emaw, chhum ang maia lang: Mit dum (cornea) chunga membrane chiang tak chu chhum a lo ni a, glass-a fog ang maiin a lang.

Heng thilte hi i fate mit hmuh dan inthlak danglamna angin i hmu thei bawk:

  • Astigmatism: Naupangin thil a hmu chiang lo mai thei.
  • Myopia: Thil hnai tak takte chu chiang taka hmuh theih, mahse thil hla tak takte chu chiang taka hmuh theih loh dinhmun a ni.
  • Anisometropia: Mit pakhata mit hmuh dan chu a dang nen a danglam avangin naupang chuan mit hmu tha zawk chauh hman a tum mai thei.

Mit enfiahnaah i doctor-in a hmuh theih dangte chu:

  • Corneal Edema: Mit hma lama awm transparent part chu a lo hring chhuak a.
  • Corneal abrasions: Pressure nasa lutuk vangin cornea hi a inzawm khawm a, a chungah hian scratch te tak te a awm thei bawk.
  • Mit (corneal scarring): Hun rei tak a chhiat chuan mit (cornea)-ah hliam awm reng thei a ni.

Heng symptoms te hi mit pahnih ah hmuh tur a awm tlangpui a, mahse a chang chuan mit pakhatah chauh a lang thei.

Engvangin nge hetiang (Congenital Glaucoma) hi a lo awm? Eng nge a chhan?

Congenital glaucoma hi naupang mit thanna lama chhiatna atanga tan a ni. Defect awm tam ber chu mit chhunga aqueous humor, trabecular meshwork drain tu tissue lo piang chhuak defect hi a ni. Sink chhunga khur ang maiin han ngaihtuah teh. Chu khur chu siam ṭhat a nih loh chuan tui chu a luang chhuak ṭha lo ang. Hei hi he mi pawh hi a ni. Trabecular meshwork hi a lo thang tha lo a, mit chhunga tui awm chu a chhuak tha lo hle. Tichuan chu tui chu mit chhungah a pung khawm a, mit chhunga pressure a ti sang hle. Hetiang pressure sang hian optic nerve a tichhe a ni. Tin, he pressure hian mit hmalam (cornea), mit hmalam chu a ti lian thei a, a tizau thei a, a hrual (streak) a, a hliam pawh a siam thei bawk.

Hetiang kalphung hi zawi zawiin a kal zel a ni. Chu chu natna a zual zel tihna a ni. Engtiang chiahin nge a na zual zel tih chu naupang mit a chhiatna awm dan te, tui awm zat leh mit chhunga pressure awm zat ah a innghat a ni.

Nausen ṭhenkhat chuan an pian tirh atangin heng chhinchhiahnate hi an nei tih hi han ngaihtuah teh. Chu chu an pum chhunga an la awm laiin an dinhmun a lo thang chho zel tihna a ni (Fetal Development). Naupang dangte tan chuan natna lan chhuah dan chu a hnu deuhah a lang thei a, thla engemaw zat emaw, kum khat emaw, kum hnih emaw pawh a ni thei. Hei hi a chhan chu piansualna hi a nasat loh vang a ni a, symptoms a lan theih nan hun rei tak a ngai thin.

Congenital Glaucoma chi hrang hrang a awm em?

Ni e, doctor-te hian he natna hi an classified dan kawng hrang hrang a awm.

Natna lan chhuah tirh kum a zirin classification:

  • Neonatal type: Nausen pian tirh emaw, nau piang thla hmasa chhung emaw hian natna lan chhuah dan a lang thin.
  • Infantile type: Nausen pian tirh atanga kum hnih atanga kum thum chhungin natna lanchhuahna a lang thin.

Natna thlentu chhiatna awm dan azirin classification:

  • Primary type: Hetiang chi ah hian glaucoma hi mit chhunga chhiatna langsar dang awm lovin a awm chauh a ni. Researcher te chuan gene mutations engemawzat an hmuchhuak a, hei hian he primary congenital glaucoma chi hi a thlen thei a ni.
  • Secondary / Developmental type: Hetah hian glaucoma hi mit chhunga chhiatna dangte nen, genetic disease dang hriat chhuah zinga mi angin a lo awm a ni.

Secondary Congenital Glaucoma thlen thei genetic condition thenkhat:

  • Aniridia: Mit (iris) rawng nei chu a bo vek emaw, a then emaw a bo vek.
  • Axenfeld-Rieger syndrome: Mit, ha leh navel nena inzawm harsatna hrang hrang thlentu natna a ni.
  • Sturge-Weber syndrome: Thluak leh mit lama harsatna thlen thei natna a ni a, chubakah hmaiah hmun sen lian tak (port-wine stain) a awm bawk.

Engtin nge he natna hi dik taka hriat theih a nih?

Mit lam doctor-te chuan a bik takin naupang tê mitmenga a hmaa kan sawi tawh ang chi natna lan chhuahna bulpui berte an hmuh chuan congenital glaucoma an ringhlel a ni. Chu rinhlelhna chu nemnghet turin naupang chu anesthetized (anesthesia hnuaiah) a ni a, mit enfiahna kimchang tak neih a ni. Lungngai suh, naupangin anesthesia avang hian natna engmah a hre lovang a, doctor-te tan pawh mit dik taka enfiah a awlsam zawk.

He test-ah hian, .

  • Tonometry hian mit chhunga pressure a teh thin .
  • Gonioscopy hmangin mit atanga drainage angle enfiah thin a ni .

Tin, test dang pawh tih theih a ni a, chungte chu:

  • Optical Coherence Tomography (OCT): Hei hian mit nerve chu chipchiar zawkin a hmu thei a ni.
  • Genetic Testing: Natna thlen thei genetic mutations a awm leh awm loh enfiah thin ang che.

Hei hi eng enkawl dan nge ni ang?

Naupang tam tak, congenital glaucoma vei tan chuan mit atanga tui chhuak thei lo tur chhiatna chu siamthat tur a ni.Mit zai a ngai a ni. He natna enkawlna bulpui leh hlawk ber chu surgery a ni. Tin, operation tih hma chuan result a tha zawk bawk. Damdawi pawhin hmun a chang tlem hle. Doctor chuan operation hma emaw, operation hnu emawa hman tur damdawi a pe thei a ni. A tlem hle a, damdawi chauh hi enkawlna atan a tawk.

Inzai

Heng surgery te hian an tum ber chu naupang mit chhunga pressure sang (Itraocular Pressure) tihziaawm hi a ni. Hei hian mit nerve leh mit peng dangte chhiatna a ti tlem ang. Tin, chhiatna dang a veng bawk ang. Naupangin enkawlna a tan thuai dan azirin, chhiatna lo thleng tawh ṭhenkhat chu a lo let leh thei hial a ni. Lungngai suh, naupang chu mit surgery laiin anesthesia hnuaiah a awm dawn a, chuvang chuan engmah a hre lo ang.

Naupang kum leh dinhmun a zirin surgeon chuan a hnuaia surgery dan zinga pakhat a thlang ang:

  • Goniotomy: Hei hi trabecular meshwork, fluid filter tu tissue-ah drainage angle-ah incision te tak te siam a ni. Surgeon-te chuan gonioscope an tih hmanrua hmangin an ti thin.
  • Trabeculotomy: A châng chuan, mit (cornea) kal tlanga tui a luang chhuahna angle chiang taka hmuh theih loh chuan, surgeon-te chuan mit var (sclera) kal tlangin, he tissue-ah hian electrocautery device trabeculotome an tih hmangin incision an siam ang.
  • Trabeculectomy: A chunga kan sawi tak surgery te hian hna a thawk lo a nih chuan surgeon chuan mit var (sclera) chu a paltlang ang a, trabecular meshwork atanga a tlem ber chu a la chhuak ang a, tui chhuahna tur kawng thar a siam ang.
  • Glaucoma Drainage Device: A chang chuan surgeon chuan naupang mit chhungah tube ang chi device te tak te (Tube Shunt) a dah ang. He tube hian mit chhunga tui awmkhawm chu mit chunga membrane te tak te (conjunctiva) hnuaia disc te tak teah a khawlkhawm thei a, chu chu taksaah a chhuah tir a ni.

Damdawi chi hrang hrang

Damdawi hian naupang tê têteah side effect a neih theih avangin doctor-te chuan uluk takin an pe a. I doctor chuan i mit chhunga pressure tihhniam nan emaw, operation hmaa i mit (cornea) chiang zawk nan emaw damdawi a pe thei che a ni. Hei hian i surgery result a ti tha thei a ni. Operation lai leh operation hnua harsatna awm lo turin damdawi an pe thei bawk.

A hnuaia damdawi te hi hman theih a ni:

  • Beta-blockers te pawh a awm
  • Diuretics (mit chhunga tui awm zat tihtlem) .
  • Prostaglandins te hi a awm a
  • Alpha-adrenergic agonists te hi a awm a
  • Antibiotics (infection venna) 1.1.
  • Corticosteroids (swelling tihziaawmna) .
  • Mitomycin (operation hnua hliam tihziaawmna tur) .

Enkawl hnuah eng dinhmun nge awm ang? (Prognosis) tih a ni.

Congenital glaucoma surgery hian mit chhunga pressure tihziaawmna leh naupang mitdelna tichhe thei process tihtawp nan a hlawhtling tlangpui. Naupang enkawlna dawng hma, chu chu chhiatna nasa tak a thlen hmaa an lo puitlin chuan mit hmuhna pangngai tak neiin an lo seilian thei a ni. Mahse, a châng chuan a chhiatna chu a let leh vek lo thei a ni. Tin, naupang thenkhat chuan enkawlna dang, glasses te pawh an mamawh thei bawk. A pawimawh ber chu i fa chu i doctor-in a tih angin checkup-na atan hruai chhunzawm zel hi a ni.

He natna laka inven dan tur a awm em?

Dik tak chuan, pianpui glaucoma hi chhungkaw hrang hrangah kal thei mah se, random takin a thleng fo thin. Genetic testing hian genetic mutation i neih leh neih loh leh i fate hnena a kai theih dan tur a hriattir thei che a ni. Amaherawhchu, kan genes te hi kan fate hnena a inthlunzawm tur chu kan dang thei lo. Mahse, naupangin he genetic disease hi a neih theihna chance a awm chuan kan inpeih thei a ni. Entîr nân, natna lan chhuah dân kan hre chiang thei a, hma kan la thuai thei bawk.

I fa hian pianpui natna a nei tih i hriat chuan a rang thei ang bera enkawl ngai a ni tih i hriat chuan rilru hah lutuk hi thil pangngai a ni. Khawthlang lamah chuan i fa enkawl dan tur chungchangah thu tlûkna i siam vat a ngai a, khawthlang lamah chuan nangmah ngeiin hlauhna leh lungkhamnate i thunun a ngai bawk. Naupang te tak te zai tura tirh leh damdawi pek hi thil harsa tak a ni tak zet a ni. Mahse, i medical team-ah rinna nei rawh. He hun harsa tak hi a tawp thuai dawn a, i fa chu damna kawngah a kal tawh dawn a ni.

A tawp berah chuan take-home message:

I fa mitmengah thil danglam emaw, danglamna emaw i hmuh chuan – mit lian, mittui tla fo, pawn chhuah duh lohna te hi – ngaihthah suh. Thil awlsam tak a ni thei a, mahse congenital glaucoma ang chi natna chhinchhiahna a ni thei bawk.

  • A hmaa hriatchhuah leh enkawl vat hi thil pawimawh ber a ni a, chutiang chuan naupang mit hmuhna chu a theih ang anga humhalh a nih theih nan.
  • He natna hi surgery hmanga enkawlna hlawhtling tak a awm a.
  • Doctor-in a rawt angin i fa chu medical checkup-ah hruai chhunzawm zel ang che.
  • Thil ngaihtuah leh rinhlelhna i neih chuan doctor nen inbia ang che.

I enkawlna leh hmalak vat hi i fa hmalam hun thlirna atana chakna lian ber a ni tih hre reng ang che.


` Glaucoma, Congenital Glaucoma, Mit Natna, Naupang Mit Natna, Mit Pressure, Mit Nerve, Mit Nerve

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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I fate hian an mitmengah hetiang danglamna hi a nei em? (Congenital Glaucoma) chungchang hi i zir dawn teh ang!
Surgery neih a niJuly 5, 2026

I fate hian an mitmengah hetiang danglamna hi a nei em? (Congenital Glaucoma) chungchang hi i zir dawn teh ang!

Kan fate mit kan en hian a chang chuan thil mak emaw, danglam emaw kan hmuchhuak thin a ni lawm ni? Nausen thenkhat mit chu a lian deuhin a lang a, a nih loh leh mittui a tla fo thin a, a êng en chu an duh lo. Chûngte chu a châng chuan thil awlsam tak leh thil pangngai tak a ni thei bawk. Mahse, chutih rual chuan, a chang chuan ngaihven tlem ngai thil pakhat chhinchhiahna an ni thei bawk. Vawiin hian mit natna, hetiang naupang te te, a bik takin an pian lai emaw, an pian tirh lamah emaw a lo awm thei a, mahse a hmaa hriat chian a nih chuan a thunun tha thei a, naupang mit hmuhna pawh a venghim thei tih kan sawi dawn a ni. Hei hi congenital glaucoma an ti a .

Congenital glaucoma chu eng nge ni?

A awlsam zawngin sawi ila, congenital glaucoma hi pian tirh emaw, naupan lai emaw (kum 2-3 chhunga) genetic factor thenkhat avanga awm thin a ni. Tunah chuan, "Glaucoma chu eng nge ni?" Glaucoma hi mit natna eng pawh, mit chhunga min puitu nerve lian ber, mit nerve tichhe thei tih hming tlanglawn tak a ni. He chhiatna hian zawi zawiin mit a tichhe thei a ni.

Naupang pianpui glaucoma vei te hian an mit chhungah pressure sang tak an nei a, chu chu ocular hypertension an ti a ni. Kan mit hian tui bik a siam chhuak a , chu chu aqueous humor tih a ni . He tui hi mit hriselna atana pawimawh tak a ni. A tlangpuiin he tui hi mit atang hian a lo chhuak a, a chhuak tha hle. Mahse, naupang pianpui glaucoma neiah chuan he tui hi a chhuak tha lo. Chumi hnuah chuan he tui hi mit chhungah a lo awm khawm a, mit chhunga pressure chu a pung zauh zauh a ni. Hetianga pressure sang hian a hmaa ka sawi tawh optic nerve chu a compress tir thin. Hun kal zelah hei hian mit pianzia pawh a tidanglam thei a ni. I fa mit chu a lian zawk tih i hmu mai thei a, a nih loh leh iris (mit chhunga rawng nei tak tak - iris) chu a thim a, a rawng a danglam thei bawk.

Hei hi enkawl theih natna a ni. Mahse, enkawl loh chuan mit a chhe zauh zauh thei a, mitdelna hial a thlen thei a ni. Chuvangin heng symptoms te hi hriat chian a, a rang thei ang bera enkawl tan a pawimawh hle. Chumi hnuah chauh chuan chhiatna chu a tlem thei ang bera, naupang mit hmuhna chu a theih ang anga venhim theih a ni ang.

He natna lan chhuah dan engte nge ni? Engtin nge kan hriat chian?

He natna lanchhuahna lian ber berte bakah hian chhinchhiahna dang a awm bawk.

A lan chhuah dan tlangpui pathum a awm a, chungte chu:

Heng mizia pathumte hi doctor ten an ngaihven ber a ni.

  • Mit mittui tla fo (Epiphora): A dik tak chuan naupang tap lo pawhin mit atang hian mittui a luang chhuak ang maiin a lang.
  • Photophobia: Naupang chuan pawn lama a chhuah dawnin êng êng tak, mit khap emaw, hmai hawi emaw chu a en duh lo mai thei.
  • Blepharospasm: Mitmeng chu a na hle ang tih a ni a, a nih loh leh mit khap tlat tum ang maiin a lang.

I hmuh theih chhinchhiahna dang:

  • Buphthalmos: Naute mit chu naute dang aiin a lianin a bulh zawkin a lang . Nu leh pa thenkhat chuan, "Naute mit chu bawng mit lian tak ang mai a ni," an ti.
  • Mitmeng blue appearance: Mit chhunga a var (sclera) chu a hnuaia membrane kaltlangin a lang thei a, chu chuan blue angin a lang thei a ni.
  • Cornea var emaw, chhum ang maia lang: Mit dum (cornea) chunga membrane chiang tak chu chhum a lo ni a, glass-a fog ang maiin a lang.

Heng thilte hi i fate mit hmuh dan inthlak danglamna angin i hmu thei bawk:

  • Astigmatism: Naupangin thil a hmu chiang lo mai thei.
  • Myopia: Thil hnai tak takte chu chiang taka hmuh theih, mahse thil hla tak takte chu chiang taka hmuh theih loh dinhmun a ni.
  • Anisometropia: Mit pakhata mit hmuh dan chu a dang nen a danglam avangin naupang chuan mit hmu tha zawk chauh hman a tum mai thei.

Mit enfiahnaah i doctor-in a hmuh theih dangte chu:

  • Corneal Edema: Mit hma lama awm transparent part chu a lo hring chhuak a.
  • Corneal abrasions: Pressure nasa lutuk vangin cornea hi a inzawm khawm a, a chungah hian scratch te tak te a awm thei bawk.
  • Mit (corneal scarring): Hun rei tak a chhiat chuan mit (cornea)-ah hliam awm reng thei a ni.

Heng symptoms te hi mit pahnih ah hmuh tur a awm tlangpui a, mahse a chang chuan mit pakhatah chauh a lang thei.

Engvangin nge hetiang (Congenital Glaucoma) hi a lo awm? Eng nge a chhan?

Congenital glaucoma hi naupang mit thanna lama chhiatna atanga tan a ni. Defect awm tam ber chu mit chhunga aqueous humor, trabecular meshwork drain tu tissue lo piang chhuak defect hi a ni. Sink chhunga khur ang maiin han ngaihtuah teh. Chu khur chu siam ṭhat a nih loh chuan tui chu a luang chhuak ṭha lo ang. Hei hi he mi pawh hi a ni. Trabecular meshwork hi a lo thang tha lo a, mit chhunga tui awm chu a chhuak tha lo hle. Tichuan chu tui chu mit chhungah a pung khawm a, mit chhunga pressure a ti sang hle. Hetiang pressure sang hian optic nerve a tichhe a ni. Tin, he pressure hian mit hmalam (cornea), mit hmalam chu a ti lian thei a, a tizau thei a, a hrual (streak) a, a hliam pawh a siam thei bawk.

Hetiang kalphung hi zawi zawiin a kal zel a ni. Chu chu natna a zual zel tihna a ni. Engtiang chiahin nge a na zual zel tih chu naupang mit a chhiatna awm dan te, tui awm zat leh mit chhunga pressure awm zat ah a innghat a ni.

Nausen ṭhenkhat chuan an pian tirh atangin heng chhinchhiahnate hi an nei tih hi han ngaihtuah teh. Chu chu an pum chhunga an la awm laiin an dinhmun a lo thang chho zel tihna a ni (Fetal Development). Naupang dangte tan chuan natna lan chhuah dan chu a hnu deuhah a lang thei a, thla engemaw zat emaw, kum khat emaw, kum hnih emaw pawh a ni thei. Hei hi a chhan chu piansualna hi a nasat loh vang a ni a, symptoms a lan theih nan hun rei tak a ngai thin.

Congenital Glaucoma chi hrang hrang a awm em?

Ni e, doctor-te hian he natna hi an classified dan kawng hrang hrang a awm.

Natna lan chhuah tirh kum a zirin classification:

  • Neonatal type: Nausen pian tirh emaw, nau piang thla hmasa chhung emaw hian natna lan chhuah dan a lang thin.
  • Infantile type: Nausen pian tirh atanga kum hnih atanga kum thum chhungin natna lanchhuahna a lang thin.

Natna thlentu chhiatna awm dan azirin classification:

  • Primary type: Hetiang chi ah hian glaucoma hi mit chhunga chhiatna langsar dang awm lovin a awm chauh a ni. Researcher te chuan gene mutations engemawzat an hmuchhuak a, hei hian he primary congenital glaucoma chi hi a thlen thei a ni.
  • Secondary / Developmental type: Hetah hian glaucoma hi mit chhunga chhiatna dangte nen, genetic disease dang hriat chhuah zinga mi angin a lo awm a ni.

Secondary Congenital Glaucoma thlen thei genetic condition thenkhat:

  • Aniridia: Mit (iris) rawng nei chu a bo vek emaw, a then emaw a bo vek.
  • Axenfeld-Rieger syndrome: Mit, ha leh navel nena inzawm harsatna hrang hrang thlentu natna a ni.
  • Sturge-Weber syndrome: Thluak leh mit lama harsatna thlen thei natna a ni a, chubakah hmaiah hmun sen lian tak (port-wine stain) a awm bawk.

Engtin nge he natna hi dik taka hriat theih a nih?

Mit lam doctor-te chuan a bik takin naupang tê mitmenga a hmaa kan sawi tawh ang chi natna lan chhuahna bulpui berte an hmuh chuan congenital glaucoma an ringhlel a ni. Chu rinhlelhna chu nemnghet turin naupang chu anesthetized (anesthesia hnuaiah) a ni a, mit enfiahna kimchang tak neih a ni. Lungngai suh, naupangin anesthesia avang hian natna engmah a hre lovang a, doctor-te tan pawh mit dik taka enfiah a awlsam zawk.

He test-ah hian, .

  • Tonometry hian mit chhunga pressure a teh thin .
  • Gonioscopy hmangin mit atanga drainage angle enfiah thin a ni .

Tin, test dang pawh tih theih a ni a, chungte chu:

  • Optical Coherence Tomography (OCT): Hei hian mit nerve chu chipchiar zawkin a hmu thei a ni.
  • Genetic Testing: Natna thlen thei genetic mutations a awm leh awm loh enfiah thin ang che.

Hei hi eng enkawl dan nge ni ang?

Naupang tam tak, congenital glaucoma vei tan chuan mit atanga tui chhuak thei lo tur chhiatna chu siamthat tur a ni.Mit zai a ngai a ni. He natna enkawlna bulpui leh hlawk ber chu surgery a ni. Tin, operation tih hma chuan result a tha zawk bawk. Damdawi pawhin hmun a chang tlem hle. Doctor chuan operation hma emaw, operation hnu emawa hman tur damdawi a pe thei a ni. A tlem hle a, damdawi chauh hi enkawlna atan a tawk.

Inzai

Heng surgery te hian an tum ber chu naupang mit chhunga pressure sang (Itraocular Pressure) tihziaawm hi a ni. Hei hian mit nerve leh mit peng dangte chhiatna a ti tlem ang. Tin, chhiatna dang a veng bawk ang. Naupangin enkawlna a tan thuai dan azirin, chhiatna lo thleng tawh ṭhenkhat chu a lo let leh thei hial a ni. Lungngai suh, naupang chu mit surgery laiin anesthesia hnuaiah a awm dawn a, chuvang chuan engmah a hre lo ang.

Naupang kum leh dinhmun a zirin surgeon chuan a hnuaia surgery dan zinga pakhat a thlang ang:

  • Goniotomy: Hei hi trabecular meshwork, fluid filter tu tissue-ah drainage angle-ah incision te tak te siam a ni. Surgeon-te chuan gonioscope an tih hmanrua hmangin an ti thin.
  • Trabeculotomy: A châng chuan, mit (cornea) kal tlanga tui a luang chhuahna angle chiang taka hmuh theih loh chuan, surgeon-te chuan mit var (sclera) kal tlangin, he tissue-ah hian electrocautery device trabeculotome an tih hmangin incision an siam ang.
  • Trabeculectomy: A chunga kan sawi tak surgery te hian hna a thawk lo a nih chuan surgeon chuan mit var (sclera) chu a paltlang ang a, trabecular meshwork atanga a tlem ber chu a la chhuak ang a, tui chhuahna tur kawng thar a siam ang.
  • Glaucoma Drainage Device: A chang chuan surgeon chuan naupang mit chhungah tube ang chi device te tak te (Tube Shunt) a dah ang. He tube hian mit chhunga tui awmkhawm chu mit chunga membrane te tak te (conjunctiva) hnuaia disc te tak teah a khawlkhawm thei a, chu chu taksaah a chhuah tir a ni.

Damdawi chi hrang hrang

Damdawi hian naupang tê têteah side effect a neih theih avangin doctor-te chuan uluk takin an pe a. I doctor chuan i mit chhunga pressure tihhniam nan emaw, operation hmaa i mit (cornea) chiang zawk nan emaw damdawi a pe thei che a ni. Hei hian i surgery result a ti tha thei a ni. Operation lai leh operation hnua harsatna awm lo turin damdawi an pe thei bawk.

A hnuaia damdawi te hi hman theih a ni:

  • Beta-blockers te pawh a awm
  • Diuretics (mit chhunga tui awm zat tihtlem) .
  • Prostaglandins te hi a awm a
  • Alpha-adrenergic agonists te hi a awm a
  • Antibiotics (infection venna) 1.1.
  • Corticosteroids (swelling tihziaawmna) .
  • Mitomycin (operation hnua hliam tihziaawmna tur) .

Enkawl hnuah eng dinhmun nge awm ang? (Prognosis) tih a ni.

Congenital glaucoma surgery hian mit chhunga pressure tihziaawmna leh naupang mitdelna tichhe thei process tihtawp nan a hlawhtling tlangpui. Naupang enkawlna dawng hma, chu chu chhiatna nasa tak a thlen hmaa an lo puitlin chuan mit hmuhna pangngai tak neiin an lo seilian thei a ni. Mahse, a châng chuan a chhiatna chu a let leh vek lo thei a ni. Tin, naupang thenkhat chuan enkawlna dang, glasses te pawh an mamawh thei bawk. A pawimawh ber chu i fa chu i doctor-in a tih angin checkup-na atan hruai chhunzawm zel hi a ni.

He natna laka inven dan tur a awm em?

Dik tak chuan, pianpui glaucoma hi chhungkaw hrang hrangah kal thei mah se, random takin a thleng fo thin. Genetic testing hian genetic mutation i neih leh neih loh leh i fate hnena a kai theih dan tur a hriattir thei che a ni. Amaherawhchu, kan genes te hi kan fate hnena a inthlunzawm tur chu kan dang thei lo. Mahse, naupangin he genetic disease hi a neih theihna chance a awm chuan kan inpeih thei a ni. Entîr nân, natna lan chhuah dân kan hre chiang thei a, hma kan la thuai thei bawk.

I fa hian pianpui natna a nei tih i hriat chuan a rang thei ang bera enkawl ngai a ni tih i hriat chuan rilru hah lutuk hi thil pangngai a ni. Khawthlang lamah chuan i fa enkawl dan tur chungchangah thu tlûkna i siam vat a ngai a, khawthlang lamah chuan nangmah ngeiin hlauhna leh lungkhamnate i thunun a ngai bawk. Naupang te tak te zai tura tirh leh damdawi pek hi thil harsa tak a ni tak zet a ni. Mahse, i medical team-ah rinna nei rawh. He hun harsa tak hi a tawp thuai dawn a, i fa chu damna kawngah a kal tawh dawn a ni.

A tawp berah chuan take-home message:

I fa mitmengah thil danglam emaw, danglamna emaw i hmuh chuan – mit lian, mittui tla fo, pawn chhuah duh lohna te hi – ngaihthah suh. Thil awlsam tak a ni thei a, mahse congenital glaucoma ang chi natna chhinchhiahna a ni thei bawk.

  • A hmaa hriatchhuah leh enkawl vat hi thil pawimawh ber a ni a, chutiang chuan naupang mit hmuhna chu a theih ang anga humhalh a nih theih nan.
  • He natna hi surgery hmanga enkawlna hlawhtling tak a awm a.
  • Doctor-in a rawt angin i fa chu medical checkup-ah hruai chhunzawm zel ang che.
  • Thil ngaihtuah leh rinhlelhna i neih chuan doctor nen inbia ang che.

I enkawlna leh hmalak vat hi i fa hmalam hun thlirna atana chakna lian ber a ni tih hre reng ang che.


` Glaucoma, Congenital Glaucoma, Mit Natna, Naupang Mit Natna, Mit Pressure, Mit Nerve, Mit Nerve

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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