A chang chuan thisen report kan en hian a chhungah hian tawngkam hriat loh tak tak kan hmu thin a ni lawm ni? Doctor-in hetiang thu a sawi hian hriat duhna tlem kan nei a, kan hlauthawng deuh pawh a ni mai thei. Chutiang hming pakhat chu ‘Heinz Bodies’ tih a ni. Chuvangin vawiinah hian hei hi eng nge a nih tak tak, natna a ni em, natna lanchhuahna a ni em tih hi han sawi ila. Hei hi chiang taka i hriatthiam chuan i hlauhthawnna chu a bo vek ang.
A awlsam zawngin, heng Heinz Bodies te hi engte nge ni?
A awlsam zawngin Heinz Bodies hi natna a ni lo. I thisen sen (red blood cells) a chhiatzia tilangtu mai an ni. Car chhunga dent kan hmuh hian khawi emaw laiah a tla tih kan hriat ang bawkin, hei pawh hi chutiang bawk chu a ni.
Hengte hi kan thisen sen (red blood cells)-a speck te tak te te an ni. Doctor (a bik takin pathologist) te chuan dye bik an hman a, microscope hmanga an en chauhvin an hmu thei a ni. Heng specks te hi a takah chuan protein pakhat hemoglobin an tih, a chhiat tawh atanga siam a ni. Chuvangin, thisen test-a hengte hi hmuh chhuah chuan thisen sen (red blood cells)-ah hian thil dik lo a awm tihna a ni. Anemia ang chi natna chhinchhiahna a ni thei bawk.
Hengte hi engtin nge an lo pian chhuah tih hi i hrethiam ang u?
Hei hi hrethiam tur chuan kan thisen sen (red blood cells) chungchang tlem kan hriat hmasak a ngai a ni.
Thisen sen (red blood cells) hi kan taksa pum puia oxygen phurtu delivery service angin han ngaihtuah teh. He delivery vehicle chhunga bungrua hi hemoglobin a ni. He hemoglobin hian oxygen a la khawm a, lung atanga taksa peng zawng zawngah a phur a ni. He hemoglobin hi kan thisen rawng sen petu a ni.
A tlangpuiin kan taksaa cell pakhat hian nucleus a nei a. Mahse, thisen sen puitling chuan nucleus a nei lo. Chuvangin hemoglobin molecule maktaduai tam tak a pai thei a ni.
Eng emaw chhan vanga heng hemoglobins te hi a chhiat chuan (oxidative damage) , an thawk tha lo. An inzawm khawm a, an inzawm khawm bawk. Chu hemoglobin piece clumped, chhia chu Heinz Bodies kan ti a. Chutiang a nih chuan thisen sen (red blood cells) te hian oxygen an phur tha thei lo. Tin, an chhe tan a, a tlangpui aia rang zawkin an boral bawk. Damdawi lamah chuan he thisen sen rang taka tihchhiat hi hemolysis an ti a.
Heinz Bodies a awm chuan eng symptom nge a awm theih?
He natna lan chhuah dan hi Heinz Bodies atanga lo chhuak tak tak a ni lo va, a chhan bulpui (underlying condition) avanga lo awm a ni a, chu chu red blood cell count (anemia) a ni. I thisen zam (red blood cell count) a tlem hle a nih chuan symptoms i nei lo mai thei. A tam zawkah chuan heng symptoms te hi i taksain oxygen a hmuh tlem vang a ni.
| Symptom a ni | Hrilhfiahna awlsam tak |
|---|---|
| Chau | Engmah ti lo pawhin chau lutuk tih hriat. |
| Luak chhuak thei | Luak chhuak leh balance hloh tih hriatna. |
| Vun dum (pale skin) a ni | Thisen tlakchham vangin vun leh hmui a dum. |
| Lung natna chak tak (Tachycardia) . | Thinlung thawk chak tak, i rilru a na ang maia hriat. |
| Thâwk harsa (Dyspnea) . | Thâwk hahna, thawhrimna tlemte pawh ni se, rilru hah. |
| Jaundice a awm | Vun sen leh mit var. |
| Splenomegaly a ni | Thisen sen (red blood cells) chhia te paih chhuaktu, spleen tihzauh. |
Engtin nge hengte hi i hmuh chhuah?
Doctor te chuan heng Heinz Bodies te hi peripheral blood smear an tih test hmangin an hmuchhuak thin . Hei hian i kut zungtang atanga thisen tlemte la chhuakin glass slide-ah hnawih a, dye bik dah a, microscope hmanga enfiah a huam a ni.
Mak tak mai chu heng Heinz Bodies nei thisen sen te hi a chang chuan mi pakhatin cell thenkhat a seh ang maiin an lang thin. Hengte hi "bite cells" kan ti a.
Hetiang hian a thawk a ni: Thisen sen chhia chhia te chu kan ril a paltlang chuan kan ril chu filter angin a thawk thin. Heinz Bodies chhia te chu a "chew" vek a ni. Thisen sen la awmte chu mi pakhatin a ei tawh chaw chi khat ang mai a ni.
Heinz Bodies hmuh theihna damdawi lam dinhmun lian ber berte chu engte nge ni?
Tunah chuan Heinz Bodies hi natna chhinchhiahna a ni tih kan hre ta. Chuvangin, an hmuh theihna tur condition lian ber ber thenkhat chu hetiang hi a ni.
| Damdawi lam dinhmun | Hrilhfiahna awlsam tak |
|---|---|
| Hemolytic Anemia avanga thisen tlakchhamna (Hemolytic Anemia). | Anemia hi thisen sen (red blood cells) siam chhuah aiin a rang zawka a chhe leh tihchhiat vang a ni. |
| G6PD tlakchhamna | Hei hi genetic (inherited) condition a ni. Enzyme G6PD tlakchhamna hian thisen sen (red blood cells) a tihchhiat theihna a tipung a ni. |
| Alpha-thalassemia natna a ni | Hei hi genetic disease a ni bawk. Hetiang a nih chuan taksain hemoglobin hrisel a siam chhuak thei lo. |
| Spleen a lian zawk | Thisen sen (red blood cells) chhia tam tak paih chhuah nan hian spleen hian nasa zawkin hna a thawk a ngai a, chu chuan a ti lian a ni. |
Engvangin nge heng Heinz Bodies te hi an lo awm? A chhante chu engte nge ni?
Hemoglobin tichhe thei chhan lian tak tak engemaw zat a awm.
- Damdawi leh chemical thenkhat nena inzawmna: Entirnan, zun kawng (UTI) damdawi thenkhat leh phar damdawi.
- Mineral tlakchhamna: Mineral pakhat, a bik takin selenium taksaa tlakchhamna.
- G6PD tlakchhamna nei tan ei tur bik: G6PD tlakchhamna nei chuan fava beans ang chi ei a ei chuan an thisen sen (red blood cells) a chhiat thei a, Heinz Bodies a lo awm thei bawk.
Enkawlna leh invenna
Hei hi mi tam takin harsatna an neih a ni. Heinz Bodies hi enkawlna bik a awm lo. A chhan chu natna ni lo, natna lanchhuahna a nih vang a ni. A pawimawh ber chu a chhan bulpui (underlying condition) zawng chhuakin enkawl hi a ni. I doctor chuan test tul tak tak a ti ang a, a chhan dik tak chu a zawng chhuak ang a, a enkawlna tur dik tak a pe ang.
A veng thei ang em? Ni e, ṭhenkhatah chuan a ti thei.
Entirnan, G6PD tlakchhamna i nei tih i hriat chuan fava bean ei loh vek tur a ni. Tin, natna dang damdawi i ei dawnin G6PD tlakchhamna i nei tih doctor hriattir a pawimawh hle bawk. Chutiang chuan i doctor chuan a tichhe lo tur damdawi a pe thei che a ni.
Take-Home Thuchah a ni
- Heinz Bodies hi natna a ni lo, i thisen sen (red blood cells) a chhiatzia tilangtu mai a ni.
- Chungte chu thisen tla (Peripheral Blood Smear)-a test bik (special test) hmanga hriat theih a ni.
- Hengte hi genetic condition, G6PD tlakchhamna, thalassemia, damdawi thenkhat emaw avanga lo awm thei a ni.
- Heinz Bodies hi enkawlna bik a awm lo. Enkawlna chu anmahni thlentu dinhmun hnuaia awm (underlying condition) lam hawi a ni.
- I thisen report-ah hetiang hming hi i nei a nih chuan lungngai suh, i doctor hmu nghal la , sawipui rawh. I mamawh thurawn zawng zawng a pe ang che.











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