Kum 50 i tlin hnuah pawh i kut leh ke chakna a tlahniam zauh zauh niin i hria em? Cup dik taka vawn, kawr button button, i kal laiin i tlu nasa zawk mai thei? Heng thilte hi tar chakna pangngai anga ngaih fo mah ila, a chang chuan he thil hnung lamah hian Inclusion Body Myositis (IBM) tih natna a awm thei bawk. Vawiin hian he thu hi awlsam takin, in hriatthiam theih angin kan sawi dawn a ni.
A awlsam zawngin, Inclusion Body Myositis (IBM) hi eng nge ni?
Inclusion Body Myositis (IBM) hi i taksa ruhte a tichak lo zauh zauh thin a ni . A pawimawh ber chu a hrehawm lo tih hi a ni. A tam zawkah chuan kum 50 an tlin hnuah symptoms hi a intan thin a, cell phone-a battery chu zawi zawiin a chhuak a, zawi zawiin chakna a hloh ang maiin ngaihtuah rawh.
He natna hi kum tam tak chhungin zawi zawiin a zual zel a. Nunna atana hlauhawm tak a ni lo va, a that lo vang che tihna a ni. Amaherawhchu, hun kal zelah nitin hna thawh a harsat phah thei a ni. A châng chuan taksa peng khat chu a dang aiin a nghawng nasa zawk thei bawk. He natna vei zinga a chanve vel pawhin hun kal zelah ei harsa an ti thei bawk .
Hei hi damdawi chiang tak la awm lo mah se, physical therapy hian i taksa chakna chu a rei thei ang bera vawng reng turin a pui thei che a ni.
Hetiang natna lan chhuahna berte chu engte nge ni?
IBM-ah hian taksa chak lohna hi vawi khatah a thleng vek lo. Zawi zawiin a thleng thin a, hun kal zelah a thleng thin. Mi thenkhat chuan an keah an hre hmasa mai thei. Mi dangte chuan an kut, kutphah, a nih loh leh kut zungtangah an hre mai thei. Mi thenkhat chuan hna nalh tak tak, kawr button vuah emaw, pen hmanga ziah emaw ang chi hna thawh harsa an ti tan thin. Mi dangte chu kea kal laiin an tlu fo tan bawk.
Natna a zual zel chuan hetiang thil hi i tawng mai thei. Hei hi chiang taka hrethiam turin table- ah han en ila.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Kut, ke, ke, leh hip-a chak lohna | Chair atanga tho leh stairs lawn te, thil rit phurh te chu a harsa ta hle. I thil lakkhawmte chu leiah a tla thla thin. |
| Chaw ei harsa leh kawng chak lohna | Chaw ei lai hian a tlakbuak ang maiin a lang. I lu chu dinglam taka vawn reng chu a harsa a, i lu chu hmalam pan ang maiin. |
| Muscle Atrophy a ni | Muscle chak lote chu a lianin a te zawk thin. Chumi awmzia chu kut leh ke ruh te chu a bo vek niin a lang. |
| Natna tlem (Myalgia) . | Natna nasa tak awm lo mah se, mi ṭhenkhat chuan an taksa ruh (muscles)-ah natna tlemte an nei thei a, chu chu an hriat reng reng a ni. |
Engvangin nge hetiang natna hi a lo awm? Eng nge a chhan?
Dik tak chuan doctor-te chuan IBM hi a chhan chiang tak an la hmu lo . Chutiang natna chu ``idiopathic`` kan ti a.
Mahse hemi chungchanga zirchianna hian thil engemaw zat a hmuchhuak a:
- Inflammation: Myositis chi dang ang bawkin, he myositis hian hun rei tak chhunga taksa peng hrang hrang inflammation, a nih loh leh inflammation, a huam tel bawk. Hei hian taksa ruhte a tichak lo hle. Mahse he inflammation hi engvangin nge a awm tih erawh hriat a la ni lo. Autoimmune disease a ni thei ang tih rinhlelh a ni a, chutah chuan kan taksa chakna (immune system) ngeiin kan taksa ngei pawh a bei a ni.
- Inclusion Bodies: Hetah hian natna hming a puanna a ni. Muscle cell chhungah hian protein clump pangngai lo, "inclusion body" an tih chu a lo awm a. Kan cell chhunga bawlhhlawh tul lo tak tak a lo awm khawm ang mai a ni. Heng protein clump te hian cell te hnathawh dan pangngai a tibuai niin an ngai.
Engtin nge doctor hian hei hi a hriat chian?
Hetiang symptoms i sawi hian i doctor-in a tih hmasak ber tur chu zawhna tha tak zawt chein i taksa ruhte a enfiah ang, a chhan chu IBM ang chi natna dang nei, polymyositis leh myasthenia gravis te hi a awm a ni.
Chuvangin, doctor chuan a bik takin thil a ngaihven hle a, chungte chu:
- Eng muscle nge chak lo?
- Taksa kil khat a nghawng nasa zawk em?
- I taksa ruhte chu a chhe tawh tih i hmu em?
- Kum engzat nge a nih atanga a lan chhuah tan?
Chumi hnuah chuan hetiang test hi eng emaw zat tih a ni thei a, chu chuan natna dang a awm loh nan leh a natna hmuhchhuah chu a nemnghet thei a ni.
| Fiahna | Hemiah hian eng nge i hmuh? |
|---|---|
| Creatine kinase (CK) hmanga enfiah a ni | Hei hi thisen test a ni a, thisenah enzyme pakhat, taksa ruh a chhiat huna a awm zat tehna a ni. |
| Thisen test dang | Viral infection emaw autoimmune natna dang emaw a awm leh awm loh enfiah thin ang che. |
| Electromyogram (EMG) hmanga tih a ni. | Muscle-a electrical activity awm zat chu teh a ni. |
| Nerve kalpui dan zirchianna (NCS) 1.1. | Muscle control tu nerve kal tlanga electrical signal kal chak dan a teh a ni. |
| Test chiang ber: Muscle Biopsy | |
| Hei hi IBM nemnghehna kawng tha ber leh chiang ber a ni. Heta i tih tur chu a natna vei taksa peng te tak te tak te chu anesthesia hmangin la la, microscope hmangin i enfiah ang. Tichuan, a hmaa kan sawi tawh protein clump (inclusion body) pangngai lo tak takte chu chu cell chhungah chuan a awm em tih chiang takin i hmu thei ang. | |
Hei hi eng enkawlna nge ni?
Hei hi rinawmna kan mamawhna hmun a ni. IBM damdawi hi a la awm lo. Inflammatory condition dang atana hman thin corticosteroids emaw immunosuppressant damdawi te hian he natna tan hian hna a thawk tha lo hle.
Mahse, chu chuan kan tih theih a awm lo tihna erawh a ni lo. He natna hi enkawl dan tur leh nun awlsam thei ang bera siam turin kan tih theih tam tak a awm a.
- Physical Therapy: Hei hi a pawimawh hle. Exercise leh technique dik tak chuan i taksa chakna chu a rei thei ang bera vawng reng turin a pui ang che.
- Occupational Therapy: I natnain nitin hna, inchei emaw, ei emaw ang chi tih a tiharsa hunah chuan, chutiang hna awlsam zawka siam thei tur hmanraw dang leh hmanraw dang zirtir i ni ang.
- Speech-Language Pathology: I ei harsat chuan speech therapist chuan him taka ei theih dan tur a hrilh thei che a ni.
Hun a kal zel a, mi ṭhenkhat chuan wheelchair ang chi ṭanpuitu hmanrua an mamawh mai thei.
Hetiang dinhmun hi ka nunpui theih nan eng nge ka tih theih ang?
IBM hi natna zual zel a ni. Chuvângin, i hmaa inthlâk danglamna lo thleng tûrte chu insiamrem tûrin hun tam tak i nei a ni. Taksa leh rilru hrisel taka awm theihna turin hun rei tak chhung ruahmanna siam a tha ber.
I tih theih ṭhenkhat chu hetiang hi a ni:
- I exercise program chhunzawm zel rawh: Physics therapist emaw, in lama exercise emaw pawh ni se, tih dan anga tih chhunzawm zel chuan i taksa ruh chakna chu a vawng reng thei a ni.
- Nun hrisel tak nei rawh: Ei leh in inthlau tak ei la, mut tam la, lungkhamna tihziaawm la, i hmangaih tak takte nen inlaichinna tha tak nei rawh. Chûng zawng zawng chuan chakna a pe ang che.
- Support Group-ah tel ve rawh: Nangmah ang bawka thil tawn tawhte nena inbiakna neih hian rilru lam hahdamna nasa tak leh thurawn tangkai tak tak a pe thei a ni.
- In leh hnathawhna hmunah inthlak danglamna siam rawh: Khawvelah hian nitin hnathawh awlsam zawka siam thei tur gadget leh method tam tak a awm a. Anmahni chu chhui chhuak rawh.
- Doctor hmu fo rawh: I doctor nen inbiak reng rawh. Symptom thar i neih chuan ei harsat ang chi i neih chuan hriattir nghal rawh.
- Clinical trial chungchangah fimkhur rawh: Researcher te chuan IBM damdawi thar an test reng a. Chûng fiahna zînga pakhatah chuan tel theihna hun remchâng i nei mai thei.
Inclusion Body Myositis hi natna a ni a, dam chhung kum hnihnaah a lo lang nghal thei a, a chhan hriat chian loh a ni. Tuman beisei ang thil a ni lo. Mahse, zinkawng thui tak a nih avangin, i hmaa inthlak danglamna tur ruahmanna siam turin hun tam tak i nei a ni. Thil \ha ngaihtuah a, i hriselna zawng zawng vawng reng tura i beih hian kum tam tak chhung chu hlim takin i nung thei ang.
Take-Home Thuchah a ni
- Inclusion Body Myositis (IBM) hi kan upat deuh deuh chuan taksa ruh a tichak lo zauh zauh thin. Nunna atana hlauhawm a ni lo.
- Hei hi damdawi chiang tak awm lo mah se, taksa chakna leh taksa chakna vawng reng hi a pawimawh hle.
- Natna nena nunpui hian nitin hna thawh dan thar zir a, a awlsam zawk nan assistive devices hmangin i nunphung i tichangtlung thei a ni.
- Symptom thar i neih chuan, ei harsat ang chi i neih chuan doctor hnenah hriattir nghal rawh.
- Thiltih \ha leh enkawlna \ha tak nen chuan he dinhmun hi i nung \ha thei ang.











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh