I fate khawsik chu ni nga aia rei a reh lo em ni? An taksa pum puiah hian hmun sen a awm em? An mit a sen a, an hmui a chhe vek em? Hetiang hunah hian nu leh pa angin engtiang chiahin nge kan hlauh? Khawsik pangngai emaw, khawsik emaw chauh nia i ngaih pawhin, a chang chuan thil pawi zawk a ni thei. Vawiin hian naupang tê tête tuar thei, natna hriat chian leh enkawl vat ngai, natna hlauhawm tak kan sawi dawn a ni. Chu chu Kawasaki Disease a ni.
Kawasaki Natna hi eng nge ni?
A awlsam zawngin sawi ila, Kawasaki natna hi kan taksa chhunga thisen kalna (blood vessels) te chu a lo hring chhuak a, chu chu a hring chhuak a, a sen vek tihna a ni. Damdawi lamah chuan hei hi vasculitis tiin kan sawi thin. Kan taksa pum puia thisen kalna kawngte hi tui phurtu pipe angin ngaihtuah rawh. Heng pipe te hi a chhung atanga a inflamed a nih chuan eng nge thleng ang? Thisen kal a tikhawlo a, chu pipe-te bang pawh a chak lo thei bawk.
He natna hian taksa chhunga thisen kalna kawng eng pawh a nghawng thei a, mahse doctor kan nih angin thinlunga thisen pe chhuaktu coronary arteries hi kan ngaihtuah ber a ni. A chhan chu thinlung hi kan taksa engine a nih vang a ni. Chu engine-a thisen pe chhuaktu vessel lian ber berte chu coronary arteries an ti a. Chungte chu a lo hring emaw, a chak lo emaw a nih chuan thinlung hnathawhna chu nasa takin a tichhe thei a ni.
He natna hi naupang thla 6 leh kum 5 inkar ah a tam ber a . Amaherawhchu, a tha ber chu a hun takah natna hi hriatchhuah a nih a, enkawl dan mumal tak tan a nih chuan naupang tam zawk chu thla hnih vel chhungin an dam kim vek ang. Chuvang chuan hlauhthawn loh leh natna lan chhuah dan fimkhur a pawimawh.
He natna hi engtiang chiahin nge a hluar?
Kawasaki natna hi a tlem hle. United States leh Canada ang ramah chuan naupang kum 5 hnuai lam 100,000 zinga 10 atanga 20 inkar a vei a, mahse Asia ram Japan leh Korea ang ramah chuan he zat hi a tam deuh hlek a ni. A pawimawh ber chu ram changkang zawka naupangte zingah Kawasaki natna hi acquired heart disease thlentu lian ber a ni ta a ni.
He natna lan chhuah dan engte nge ni? Engtin nge kan hriat chian?
Nu leh pa i nih angin he thil hi i fimkhur hle tur a ni. A chhan chu heng symptoms te hi viral flu tlanglawn tak nen hian a inang deuh thei a ni. Mahse heng symptoms te hi a lo inzawm khawm chuan a bik takin i ngaihven tur a ni.
A chhinchhiahna pawimawh ber chu khawsik sang tak, ni 5 emaw a aia rei emaw a awm hi a ni. He khawsik hi damdawi pangngai, paracetamol ang chi hmanga tihziaawm vek a ni lo mai thei.
Hetiang hian thil pawimawh dangte chu hriatreng a awlsam zawk nan i en ang u.
| Symptom a ni | Thuziak (i hmuh dan) . |
|---|---|
| Ni 5 aia rei khawsik a awm | Hei hi a symptom ber leh langsar ber a ni. Khawsik hi 101°F (38.3°C) aia sang a ni thei. |
| Mit a sen vek | Mit var chu pink emaw sen emaw a lo ni a, mahse mit atang chuan mucus leh pus a chhuak lo. |
| Kawng, hmui leh leiah inthlak danglamna | A hmui chu a sen hring dup a, a chhe a, a vawt bawk. Lei chu strawberry-red a lo ni a, bump te te (Strawberry tongue) a nei thei bawk. A ril pawh a sen thei bawk. |
| Kut leh kea inthlak danglamna | Naupang kutphah leh kephah chu a sen a, a hring bawk. Hetianga a hring hian naupang tan kal a ti harsa thei a, kut hmanga thil chelh a harsa thei bawk. |
| Vun a hring chhuak | A rilru, pum leh a kekawrteah hian vun sen (red rashes) a lang fo thin. Chungte chu measles nen a inang thei. |
| Kawngkhar chhunga lymph nodes a lo hring chhuak | Kawr sir khatah lymph node (nodule) a hring a, a tlangpuiin centimetre 1.5 aia lian a ni. |
| Vun peeling | Natna a lo chhuah atanga kar 2-3 hnuah kut zungtang leh ke ruh atanga vun a lo chhuak tan thin. |
| Hahdam lohna lutuk | Naupang chu a hma aia nasain a tap a, a hrisel lo niin a lang. |
Naupang thenkhat chuan heng symptoms hi vawi khatah an lantir vek lo. Symptom tlemte chauh a lan chuan incomplete Kawasaki disease kan ti a ni. Mahse, i fa chu khawsik ruala heng symptoms pakhat emaw pahnih emaw nei mahse doctor hnena hruai nghal a pawimawh hle.
Engvangin nge he natna hi a lo awm? Hri kai theih a ni em?
Dik tak chuan doctor-te chuan Kawasaki natna thlen chhan chiang tak an la hmu lo a, mahse theory engemaw zat a awm.
- Infection avanga chhanna: Zirchiangtu thenkhat chuan virus emaw bacteria emaw taksaa a luh chuan kan immune system hian a overreacted nasa lutuk a, thisen kalna kawng a tichhia niin an ngai.
- Environment factors: He natna hi kum khat chhunga hun engemaw chen, a bik takin thlasik tawp lam leh thlasik tir lamah a awm tam zawk.
- Genetic predisposition: Naupang genes thenkhat kengte hian he natna hi an vei duh zawk mai thei niin an ngai.
A pawimawh ber chu Kawasaki natna hi a kai theih loh hi a ni. Chumi awmzia chu i fain he natna hi a vei a nih chuan in lamah emaw, sikulah emaw naupang dangte hnena theh darh tur ngaihtuah buai a ngai lo tihna a ni.
Tute nge risk sang zawk?
- Naupang hmeichhia aiin naupang mipa hi an hlauhawmna a sang deuh hlek a ni.
- Naupang kum 5 hnuai lam.
- Asian emaw Pacific Islander hnam chhuak naupangte tan.
Eng harsatna nge Kawasaki natna hlauhawma siam thei?
Hei hi kan ngaihven ber tur a ni. Enkawl loh emaw, enkawl tlai emaw a nih chuan harsatna awm thei, a bik takin thinlung nena inzawmte chu a hlauhawm thei hle.
- Coronary artery aneurysms: Hei hi harsatna lian ber leh hlauhawm ber a ni. Aneurysm chu thisen kalna kawng (blood vessel wall)-a bulge, inflammation avanga chak lo tak a ni. Chungte chu a bulging thei a, a chang chuan a rupture thei bawk.
- Heart attack: Aneurysm chhungah thisen zam a lo awm a, heart-a thisen kal tur a tikhawlo a nih chuan heart attack a awm thei.
- Myocarditis: Thinlung ruh natna (inflammation) a awm.
- Heart valve harsatna: Heart valve te hi a chhe thei a, a inhawng leh khar tha lo thei bawk.
- Heart failure: Thinlung hian taksa pum puia thisen tling tawk a pump thei lo.
Heng harsatna chungchang hriat hian a ti hlauhawm thei che a ni. Mahse hre reng ang che, heng harsatna tam zawk hi chu natna lan chhuah tirh atanga ni 10 chhunga enkawl tan a nih chuan ven theih a ni. Chuvang chuan khawsik leh a chunga kan sawi tak symptoms i neih chuan rei lovah Doctor pan rawh kan ti a ni.
Engtin nge doctor hian he natna hi a hriat chian tak tak?
Kawasaki natna finfiah theihna tur thisen test leh scan pakhat mah a awm lo. Doctor chuan naupang natna lan chhuah dan uluk taka enfiahin diagnosis a siam thin. Hei hi clinical diagnosis kan ti a .
Doctor chuan Kawasaki natna chu a enfiah ang a, ni engzat nge a khawsik a awm tih a en a, eng symptom dang nge a awm tih a en a, a natna dang (e.g. measles, scarlet fever) a awm loh nan a enfiah ang.
Natna hi stage thum a ni
Kawasaki natna hi a tlangpuiin stage thum kaltlangin a kal zel a.
1. Stage 1 - Acute: Hei hi a hmasa ber kar hnih vel a ni. Hemi hun chhung hian natna lan chhuah dan ber, khawsik, vun, mit sen, leh kaa inthlak danglamna te hi a awm vek a ni. Hetih lai hian naupang chu a rilru a hahdam lo hle thin.
2. Stage 2 - Subacute: Kar hnih atanga kar li chhung a daih. Hetih lai hian khawsik chu a reh tawh. Mahse, pum na, ril\am, leh ruh na ang chi symptoms a awm thei. A pawimawh ber chu he hun chhung hian kut zungtang leh ke ruh vun hi a lo hring tan thin. Hetih lai hian coronary artery aneurysm vei theihna a sang ber a ni.
3. Stage 3 - Convalescent: Hei hi thla khat emaw thla hnih emaw chhung a daih thei. Symptom zawng zawng chu zawi zawiin a bo vek. Mahse, naupang chu a chau deuhin a hria. Thisen kalna kawng chhia a dam theih nan hun a duh a ni.
Eng test nge tih thin?
Natna hi finfiah theih a ni lo a nih pawhin doctor chuan a natna a nasat dan hriat chian nan leh natna dang a awm loh nan test eng emaw zat a ti thei a ni.
- Thisen test: CRP leh ESR ang chi thil zawng la, chu chuan taksaa inflammation level a tarlang a ni.
- Urinalysis tih a ni
- Echocardiogram: Hei hi test pawimawh ber a ni. Hei hi ultrasound scan a ni. Thinlung hnathawh dan te, valve dinhmun te, a bik takin coronary arteries a chhiat leh aneurysm a lo awm leh awm loh chiang takin a hmu thei a ni.
- Electrocardiogram (EKG): Hei hian thinlung electrical activity (rhythm) en turin a pui a ni.
Engtin nge enkawl a nih?
Kawasaki natna nia rinhlelh a nih veleh naupang chu damdawi inah dah a ni. Damdawi inah enkawl tan a ni. Enkawlna atana thil tum lian pali a awm a, chungte chu:
1. Taksa chhunga khawsik leh inflammation tihziaawmna.
2. Thisen kalna kawng, a bik takin coronary arteries tihchhiat ven emaw tihtlem emaw.
3. Lung lam harsatna laka invenna.
4. Thisen zam tur venna.
Enkawl dan tlangpui pahnih hman a ni a, chungte chu:
- Intravenous Immunoglobulin (IVIG): Hei hi a enkawlna ber a ni. A awlsam zawngin sawi ila, mi hrisel tak tak atanga lak chhuah antibodies awmna thil a ni. Naupang hnenah saline angin thisenah (IV) pek a ni. Taksa overactive immune response control-na leh thisen kalna kawng chhiatna tihziaawmna hmangin hna a thawk a ni. Ni 10 chhunga he enkawlna hi pek hian thinlung lama harsatna awm theihna chu 25% atanga 5% aia tlem loah a tihniam thei a ni.
- Aspirin: Viral fever nei naupangte hi aspirin kan pe tlangpui lo. Mahse, Kawasaki natnaah chuan aspirin hi a tir lamah chuan khawsik leh inflammation tihziaawm nan a tam zawkin pek thin a ni a, chumi hnuah kar engemaw zat thisen zam loh nan a tlem zawkin pek thin a ni.
Heng enkawlna bakah hian naupang chu tui tlakchhamna tur venna atan saline ang chi thil te pek a ni bawk a, natna leh hliam nana damdawi pek a ni bawk.
Damdawi in atanga i haw hnuah eng nge thleng?
Naupang khawsik chu a bo vek tawh a, oral fluid leh damdawi a ei thei tawh chuan damdawi in atangin a haw thei tawh ang. Mahse a haw hnuah hna a la tawp lo. Naupang chu uluk taka enkawl a ngai a ni.
I pediatrician leh cardiologist te nen follow-up visit neih chhunzawm zel a ngai ang.
- In lamah i haw ang a, kar khat emaw kar hnih emaw hnuah echocardiogram i nei ang a, kar 4-6 hnuah i thinlung dinhmun i en leh ang.
- Coronary arteries-ah chhiatna a awm a nih chuan hun rei tak chhung chu doctor enkawlna hnuaiah i awm a ngai dawn a, i dam chhung zawng pawh a hun hunah test neih a ngai mai thei bawk.
Kawasaki natna hi tihdam theih vek a ni em?
Naupang tam zawk chu an dam chhuak vek. A natna lan chhuah dan hi kar 4-6 vel a awm thei. Naupang chu thla hnih vel chhung chu chau leh hahdam lo takin a inhria thei. A tlem hle (2-3%) velin natna hi a lo lang leh thei.
Enkawl zawhah chuan thisen kalna kawng chhiatna 50% vel chu kum khat emaw kum hnih emaw chhungin a dam leh ang. Amaherawhchu, a chhiatna chu a nasat em em a, chu chu aneurysm ang chi a nih chuan dam chhung zawng harsatna a ni thei.
Nu leh pa angin eng nge i tih theih?
Naupang damloh laia i rilru hahna leh lungngaihna hi kan hrethiam. Mahse i chakna hi i fa chakna ber a ni.
- Doctor thupek dik takin zawm rawh: I damdawi ei tur chu a tih ang chiah chiah ei rawh. Follow-up appointment engmah lo nei tawh suh.
- Vaccine pek chungchangah fimkhur rawh:Aspirin i ei lai hian i fa chu chickenpox leh influenza ang chi virus natna laka venhim a pawimawh hle. Aspirin leh virus thenkhat hian natna hlauhawm tak, mahse hlauhawm tak Reye’s syndrome an tih chu a thlen thei a ni. Chuvangin i fate vaccine pek dan tur chu a hun taka hman a nih leh nih loh enfiah turin i doctor nen inbia ang che.
- Virus nung vaccine chungchangah fimkhur rawh: Virus nung vaccine, measles-mumps-rubella (MMR) leh chickenpox (varicella) te hi IVIG enkawl a nih atanga thla 11 chhung pek loh tur a ni. Hei hi a chhan chu IVIG hmanga enkawlna hian taksain heng vaccine-te laka antibody tha tak a siam theih loh phah thei a ni.
- Thiltih tihtlem: I fa thinlung a nghawng a nih chuan i doctor chuan infiamna hahthlak tak tak leh tlan chakna chu rei lo te chhung tihtlem turin a fuih thei che a ni. Heng thupekte hi uluk takin zawm rawh.
- I fa chu thlamuan rawh: I fa chu damdawi ina a awm laiin, a duh ber infiamna emaw, lehkhabu emaw pe la. I aw leh i fawh hian he hun harsa tak karah hian i fa tan thlamuanna nasa tak a thlen ang.
Take-Home Thuchah a ni
- I fa hian ni 5 aia rei khawsik a neih a, mit sen, hmui chhe, vun hring, leh ke ruh hring te ang chi natna a awm chuan khawsik pangngai maiah ngai suh la , doctor lam pan nghal rawh.
- Kawasaki natna hi a kai thei lo . A tul lovah hlau suh.
- Natna hi a hmaa hriatchhuah a, a lan chhuah tirh atanga ni 10 chhunga enkawl tan chuan thinlung chhiatna nasa tak tam tak chu a veng thei a ni.
- Enkawlna an neih zawh hnuah pawh naupang dam rei theihna atan doctor-in a tih ang anga a thupek leh test te zawm a pawimawh hle.
- He natna hi a tlem hle nachungin, enkawlna nen chuan naupang tam zawk chu an dam kim vek tih hre reng ang che , positive leh chak takin an awm reng thin.











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