I thinlung veilam ventricle chungchang hengte hi i hria em? (Left Ventricular Non-Compaction - LVNC) Kan sawi dun ang u!

Vawiin hian thinlung dinhmun buaithlak deuh, mahse pawimawh tak tak ni thei tur chungchang kan sawi dawn a ni. He thu hi i la hre ngai lo mai thei. Doctor ten an tih angin Left Ventricular Non-Compaction (LVNC) an ti a. A hming hi thil lian tak angin a lang thei a, mahse lungngai suh, awlsam takin i vawng ang u.

Chuti a nih chuan left ventricular noncongestive heart failure (LVNC) hi eng nge ni?

A awlsam zawngin sawi ila, hei hi kan thinlung veilam sir hnuai lam, Left Ventricle a lo thanglian tha lo a nih chuan a lo awm thin a ni. Ngaihtuah teh, a tlangpuiin he kan thinlung veilam ventricle hi sa chak tak, hmin tak a ni. Kan taksa pum puia thisen pump chhuaktu ber a ni. Mahse he `(LVNC)` nei mi pakhatah chuan veilam ventricle chu sponge ang mai a ni a, a thuk deuh a, net ang maiin a inrem bawk. Tlâng lam a nei a, chhangphut chhungril ang mai a ni.

Hei hi congenital heart condition anga ngaih a ni tlangpui. Chumi awmzia chu i pian tirh atangin i thinlungah he dinhmun hi i nei thei tihna a ni . Enkawl that loh chuan he ``(LVNC)`` hian thinlung lama harsatna lian tak, chu chu thinlung natna a thlen thei a ni.

He LVNC dinhmun hian engtin nge thinlung hnathawh a nghawng?

Tunah en teh, kan thinlung veilam ventricle hian hna pawimawh tak a nei a. Hei hi a ni, oxygen tamna thisen chu lung atanga taksa pum puiah a pump chhuak thin. Tui motor ang maiin. Mahse, he `(LVNC)` dinhmun hi a lo awm chuan, sponge ang maia veilam ventricle chu a contract tha thei lo va, a relax tha thei lo bawk. Chu chu thisen kha khauh leh hmalam pan tir, a nih loh leh thisen a khat turin chawlh hahdam leh harsa a ti tihna a ni. Chuvangin, a rah chhuah chu taksa pum puia thisen pump chhuahna hnathawh chu a thleng dik lo a ni . Hei vang hian harsatna chi hrang hrang a lo chhuak tan a ni.

Hetiang dinhmun hi engtiang chiahin nge LVNC tia koh a nih?

Hei hi a takah chuan thil awm lo tak a ni. Damdawi lama mithiamte sawi dan chuan kum tin mi maktaduai khat zinga mi sawm leh pahnih vel chauhvin he natna hi an vei tih hmuhchhuah a ni. Mahse, a number tak tak chu a tam zawk hle mai thei . A chhan chu mi thenkhatin symptom an lantir loh vang a ni. Tichuan Doctor hnenah an kal lo va, chuvangin diagnosis an dawng lo.

LVNC natna lan chhuah dante chu engte nge ni?

Hei hi a pawimawh ber a ni. Mi thenkhat chuan symptom an nei lo mai thei . Mahse, mi dangte chuan thinlung lama harsatna lian tak tak an nei thei a ni. Entirnan, cardiac death rang tak a awm thei. LVNC vei hmun thuma ṭhena hmun hnih vel chu heart failure vei theihna an nei a ni .

Okay, chuvangin `(LVNC)` vei hian eng ang symptom nge a lantir theih tih hi han en ila:

A lan chhuah dan tlangpui :

• Thisen zam a lo awm thei. Hengte hi a hlauhawm hle a, a chhan chu heng clots te hi thluak emaw lung emaw thlenga an kal chuan harsatna lian tak a ni thei a ni.
• Khumah mut laiin thawk harsa i nei thei.
• Fainting a awm .
• Heart palpitations - Hei hi rilru chhunga drum ri ang maiin a awm thei a, thinlung a na hle bawk.
• Exercise theih lohna, thawhrimna tlemte pawh nise thawk hah (Dyspnea) .
• Thinlung ri mumal lo (Arrhythmia) .
• Ke ruh hring (Lymphedema) - a bik takin ke ruhroah.
• Thâwk lak tawi / Dyspnea - Thawhrimna tlemte pawh nise thawk harsa ang maia inhriatna.

Engvangin nge he LVNC condition hi a lo awm? A chhante chu engte nge ni?

A tam zawkah chuan he `(LVNC)` dinhmun hi i pian hmaa lo awm thin genetic change (Gene mutation) vang a ni. Hei hi thil buaithlak tak a ni. He genetic change hi random takin a thleng thei a, chhan awm lovin a thleng thei a, i nu leh pate hnen atanga rochun a ni thei bawk. Chumi awmzia chu chhungkuaa kal thei thil a ni thei tihna a ni. Ngaihtuah teh, chhungkaw thenkhatah chuan hetiang thinlung natna hi an tam hle.

Tin, hmeichhia za zela tlemte chauhvin naupai laiin a vawi khat nan chhan hriat lohvin LVNC an vei thei bawk. Doctor-te chuan naupai laiin heart muscle-a extra strain a awm vang pawh a ni thei niin an ngai. Hmeichhe thenkhat tan chuan nau an pai hnuah heng symptoms te hi a bo thin. Mahse midang tan chuan LVNC hian hun rei tak chhung nghawng a nei thei a ni.

Engtin nge doctor-te hian he LVNC natna hi an hriat theih?

Doctor chuan he ``(LVNC)`` natna hi i neih leh neih loh chiang taka hriat theih nan test engemaw zat a ti ang. Eng nge an nih hi han thlir ila:

• Echocardiogram: Hei hian i thinlungin thisen a pump that dan te, valve-te hnathawh that dan te, valve-a harsatna a awm leh awm loh te a en a ni. Thinlung ultrasound scan ang mai a ni. Hei hi left ventricle spongy nature i hmuh hmasak berna hmun a ni.
• Electrocardiogram (ECG): Hei hian i thinlung electrical activity a teh a. I thinlung rhythm-a harsatna awm apiang a hmuchhuak thei.
• Special imaging test: Heng zingah hian cardiac CT scan leh magnetic resonance imaging (MRI) te a tel. Chûngte chuan thinlung insiam dân, thinlung siam dân leh a bang thukzia te chu a târ lang thei a ni. LVNC-ah chuan heng scan-ah hian sponge ang maia lang chu chiang takin a lang.
• Coronary angiogram: Hei hian thinlunga thisen petu coronary arteries kal tlanga thisen a kal dan te, blockage a awm leh awm loh te a enfiah thin. A châng chuan thinlung natna dang hriat loh nân he test hi a ngai thei bawk.

He LVNC natna hi eng enkawlna nge ni?

LVNC enkawl dan hi i natna lan chhuah dan azirin a inang lo. Mi zawng zawng hi a inang vek lo. Entirnan, heart failure i neih chuan i doctor chuan damdawi a pe thei a, chungte chu:

• Angiotensin tidanglam thei enzyme inhibitor (ACE inhibitor): Entirnan, benazepril (Lotensin®) emaw lisinopril (Prinivil®, Zestril®) emaw sacubitril-valsartan (Entresto®) (angiotensin-neprilysin inhibitor) emaw a ni thei. Hengte hian i thisen kalna kawng (veins leh arteries) te chu a ti hahdam a, a hawng a, chu chuan thisen a kal awlsam phah a ni. Hei hian thinlunga hnathawh tur a tihtlem phah a ni.
• Beta-blockers: Entirnan, metoprolol (Lopressor®, Toprol XL®) emaw atenolol (Tenormin®) emaw a ni thei. Hengte hian hormone thenkhat (e.g. adrenaline) a block a, thisen sang a tihhniam bakah heart rate a control bawk.
• Digoxin (Digoxin®, Lanoxin®): Hei hian i heart rate a control a, i heart pumping strength tlem a ti sang a, thisen kal dan a ti tha bawk.
• Diuretics emaw "water pills": Hengte hian taksain zun hmanga chi leh tui tam lutuk a chhuah tir avangin hna a thawk a ni. Hei hian swelling a ti tlem a, thinlunga hnathawh tur a ti tlem bawk.

A châng chuan, lungphu chawl nghal mai theihna a awm chuan, doctor chuan thinlung vun hnuaiah Implantable Cardioverter Defibrillator (ICD) an tih hmanrua dah a rawt thei a ni. Hei hi battery hmanga hman theih thil te tak te a ni. Thinlung chhunga rhythm chak tak, nunna atana hlauhawm tak a hmuchhuak a, thinlungah electric shock a pe a, chu chuan rhythm pangngai a siam leh ta a ni. A nasat em avangin enkawlna dang a hlawhtlin loh chuan thinlung thlak a ngai mai thei.

He LVNC condition hi a dam kim thei ang em? A let leh thei ang em?

Aw ni lo. Tunah hian LVNC hi damdawi a la awm lo . Chu chu tihdanglam theih a ni lo tihna a ni. Mahse, lungngai suh. Enkawlna hian i nunphung a ti tha thei a , thinlung natna avanga harsatna awm thei te pawh a ti tlem thei bawk . Tin, ka sawi tawh ang khan, a na ber berah chuan thinlung thlak a ngai mai thei bawk.

He LVNC dinhmun hi engtin nge kan pumpelh ang?

LVNC ven dan tur a awm lo. Hei hi a chhan chu genetic factors avanga lo awm a nih fo vang a ni. Mahse, chu natna thlentu gene mutation i neih chuan, emaw, i nei thei nia i ngaih chuan (entir nan, i chhungkuaa mi pakhatin he natna hi a neih chuan), genetic testing hi a \angkai hle thei a ni.Genetic counselor chuan i test result chu nang leh i chhungte hnenah a hrilhfiah ang che. LVNC neih awmzia leh i fate hnena i thlen theihna tur risk chu eng nge ni tih hriatthiamna an pe ang che.

He LVNC natna nen hian damdawi lam harsatna dang a awm em?

Awle. A châng chuan he `(LVNC)` an tih hi genetic condition dang (syndromes)-a tel ve anga ngaih theih a ni bawk. Hengte hi a buaithlak deuh a, mahse doctor-te pawhin `(LVNC)` an hmuhchhuah hian heng dinhmunte hi an ngaihtuah bawk. Entirna tlemte chu hetiang hi a ni:

• Barth natna a ni
• Noonan syndrome a ni
• Roifman natna a ni
• Toriello Carey natna a ni

LVNC nei mi pakhat hmalam hun chu eng nge ni? A dam rei zawng chu eng nge ni?

LVNC vei tan chuan outlook a inang lo thei. Mi tin a inang lo. Enkawlna tha tak nen chuan symptoms te chu control theih a ni , mi thenkhat chuan dam rei zawng pangngai an hmang thin.

LVNC hi thihna thlen thei a ni a, mahse chutiang chu a ni ngai lo . LVNC vei tam zawk hi chu natna vangin an thi lo. A pawimawh ber chu cardiologist hmuh fo a test neih hi a ni . I thinlung hriselna enkawl dan tur leh harsatna i neih theihna tur a tihtlem theih nan a pui thei che a ni.

Kei emaw ka fa emaw hian LVNC kan nei a nih chuan eng zawhna nge doctor hnenah ka zawh ang?

Nangmah emaw i fain (LVNC) i neih chuan, emaw, ngaihtuahna i neih chuan, i doctor hnenah hetiang zawhna hi zawh a tha ang:

• Ka/ka fa LVNC dinhmun hi eng nge ni thei ber? (i.e. genetic nge thil dang)
• LVNC hi genetic test neih i rawt em? Chutiang a nih chuan, chhûngkaw member dangte tân a pawimawh ang em?
• LVNC hriat theih nan kei/ka fa hian eng test nge ka neih a ngai? An hnen atangin eng nge ka beisei theih ang?
• LVNC enkawl dan tur chu engte nge ni? Kei/ka fa tan eng enkawlna nge tha ber? Heng enkawlnate hian side effect a nei em?
• Ka fa emaw kei emaw hian cardiac arrest nghal kan neih chuan eng symptoms nge a neih? Engtin nge ka tih nghâl ang?

Heng zawhnate hian i doctor nen sawihoin i dinhmun hriatthiamna tha zawk i neih theih nan a pui ang che.

Chuti a nih chuan, he thawnthu atang hian eng thil nge kan hriat reng tur pawimawh ber?

Left ventricular non-functioning heart (LVNC) hi thinlung natna hmuh tur awm lo, pianpui atanga lo piang a ni fo thin. Hei hi thinlung veilam ventricle a lo thang tha lo a nih chuan a ni. Muscle hrual, chak tak ni lovin, a thuk a, a spongy ta zawk a ni. Hei hian thinlungin thisen a pump tha lo a ti thin.

`(LVNC)` i neih chuan, .A pawimawh ber chu cardiologist pan fo a, an thurawn zawm hi a ni. Hei hi damdawi awm lo mahse, i doctor-in a pek che hian harsatna i neih theihna a ti tlem thei a, i nunphung a ti tha thei bawk. Hlauthawng lo va enkawlna dik tak neih a pawimawh . Nangmah chauh i ni lo tih hre reng la, doctor-te pawh tanpui turin an awm reng a ni.

` Lung natna, left ventricle, LVNC, Lung natna lan chhuah dan, thinlung tha lo, genetic natna, lung natna enkawl