Moms and Dads, in fate lu chu kum inang naute dang aiin a lian deuh tih in hre tawh mai thei. A nih loh leh clinic-a doctor chuan lu vel a teh a, chutiang chuan a sawi em? Hei hi damdawi lam chuan ``Macrocephaly'' kan tih chu a ni. Mahse, he hming i hriat hian hlau suh, a tha em? A chhan chu lu lian zawng zawng hi natna a ni vek lo. Hemi chungchang hi chipchiar takin sawi ila.
Macrocephaly chu eng nge ni?
A awlsam zawngin, `(Macrocephaly)` tih awmzia chu ``lu lian tak'' tihna a ni.I naute hian ``(Macrocephaly)`` a neih chuan a lu vel chu a kum leh a mipa leh hmeichhia naute dangte aiin a lian zawk tihna a ni. A dik tak chuan doctor-te sawi dan chuan naute lu vel (lu lian ber vel tehna) chu chutiang kum naupang 100 zinga 97 aia lian a ni tihna a ni (doctor-te hman chart-a ``97th percentile``). Chumi awmzia chu a kum leh mipa naupang 97% aiin a lu a lian zawk tihna a ni.
Mahse, he thu i hriat hian hlauthawng suh. `(Macrocephaly)` hi a chang chuan enkawl ngai natna chhinchhiahna a ni thei. Amaherawhchu, i naute lu a lian chhan pawh hi i chhungkuaa thil kal zel a ni thei bawk. Enkawl ngai lo natna hlauhawm lo tak a ni. Hei hi `(Benign Familial Macrocephaly)` kan ti a ni.
Hetiang dinhmun hi engtiang chiahin nge a awm?
``Macrocephaly'' an tih hian United States-a mipui 2% leh 5% inkar a nghawng niin an sawi. Hetiang dinhmun hi kan ramah pawh hmuh tur a awm. Chuvang chuan he thu hi kan hriat chuan mak a ti lo.
Macrocephaly natna lan chhuah dan chu engte nge ni?
Tunah chuan `(Macrocephaly)` hmanga symptoms hmuh theihte chu engte nge ni tih i lo en ang u. Mahse, naute zawng zawng hian heng symptom zawng zawng hi an neih vek a ngai lo tih hre reng ang che. Naute thenkhat chuan symptoms an nei lo tak tak thei a, lu lian tak mai an nei mai thei.
- Lu thang chak: I lu chu beisei aia chak zawka thang a nih chuan hriat reng tur a ni.
- Lu vun chunga veins hmuh theih: A chang chuan, lu vun hnuaiah hian veins chiang takin a lang thei.
- Developmental Delays: Naute chu kum engemaw zat a tih tur thil tih a tlai a nih chuan (entir nan: nuihzatthlak, kawr tihchak, inher, thut, kal, etc.), chu chu ``Developmental Delays'' an nei tihna a ni.
- Mit hnuai lam hawi: Naute mit chu hmalam hawi lovin hnuai lam hawi reng a nih chuan (hei hi ``Setting-Sun Eye Phenomenon'' an ti bawk).
- Luruh ruh inkar hmun (fontanels) inkar a khauh emaw, a bulh emaw): Naute lu ruh chhunga hmun nem (fontanels kan ti a, doctor-te chuan ``fontanels'' an ti) chu ruh a inzawm kim loh avangin a khauh emaw, a bulh emaw a nih chuan.
- Ei duhna: Naute hian ei leh in a duh loh chuan, emaw, ei leh in duhna a neih tlem chuan.
- Thil dang nena lo awm dun: A chang chuan `(Epilepsy)` (seizures/ convulsionsHe ``(Macrocephaly)`` hi ``(Autism)`` ang chi condition nen pawh hmuh theih a ni.
Ngaihtuah teh, i naute hian ``Benign Familial Macrocephaly'' (chhungkaw chhunga lu lian tak, harsatna nei lo, chhungkuaa tlan chhuak tihna) a neih chuan, lu lian danglam tak tih loh chu chhinchhiahna dang i hmu lo fo ang.
Macrocephaly hi engte nge ni?
Awle, tunah chuan he `(Macrocephaly)` hi engvangin nge a lo awm tih hi han en ila, a chhante chu engte nge ni. Hei hi a chhan chu benign atanga severe thlengin a awm thei.
I naute hian ``Benign Familial Macrocephaly'' a neih chuan a lu chu a tlangpui aia lian zawk a ni tihna mai a ni. He lu lian tak hi thlahtu a ni a, chhungkaw zinga mi dang nen a lian leh te pawh a inang thei bawk. Hei hi ngaihtuahawm tur a ni lo.
Mahse, ``Macrocephaly'' thlentu dang, a chang chuan hlauhawm tak tak pawh a awm. Chung zinga ṭhenkhat chu pianpui a ni thei a, ṭhenkhat erawh chu hun kal zelah a lo awm thei thung. Chung zingah chuan:
- Megalencephaly: Thluak lian lo tak.
- Hydrocephalus: Hei hi thluak hual veltu cerebrospinal fluid (CSF) tam lutuk a awm hian a ni. He tui tam lutuk hian thluak chu luruh chhungah a nawr lut a, thluak chu pressure a siam a ni.
- Thluaka thisen chhuak: A chang chuan thluaka thisen kalna kawng dik lo (`Arteriovenous Malformation` ang chi) vang a ni thei.
- Cranial Hyperostosis: Luru ruh a thim lutuk.
- Thluak natna (brain tumor) a awm.
- Hematomas: Hengte hi thisen zam (blood clots) a ni. Lu hliam emaw, tlu emaw, naute tihnghing emaw ang chi thil vang pawh a ni thei.
- Thluak natna: Entirnan, meningitis, encephalitis, emaw thluaka abscess emaw.
- Genetic disorders: Entirnan, genetic conditions `(Achondroplasia)` (a thang chak lohna tur natna), `(Fragile X Syndrome)`, `(Neurofibromatosis Type 1)`, `(PTEN Hamartoma Tumor Syndrome)` (`(Cowden Syndrome)` tia koh bawk), `(Gorlin Syndrome)` leh `(Greig Cephalopolysyndactyly Syndrome natna a ni)`.
- Increased Intracranial Pressure: Eng thil vang pawha luruh chhunga pressure sang .
Engtin nge (Macrocephaly) hi kan hriat theih ang?
Tunah chuan doctor-te’n macrocephaly an hmuhchhuah dan te, a chhan hriat dan tur te i en ang u.
Pian hma
I doctor hian i naupai lai hian ultrasound scan hmangin i naute hian macrocephaly a nei em tih a hre thei a, a bik takin second trimester tawp lam emaw third trimester tir lamah emaw a ni.
Pian hnuah
Naute a pian hnuah, a tlangpuiin clinic tinah kum nga vel chhung chu doctor chuan naute lu vel chu a teh thin. Tichuan, chu tehna chu chutiang kum leh sex-a naute dangte thanna chart pangngai nen khaikhin a ni. Nu, pa leh pi leh pute lu lian leh te pawh ngaihtuah tel a ni.
Macrocephaly hmuhchhuah a nih chuan a dawt leh tur chu a chhan zawn a ni. Chumi atan chuan Doctor chuan test hrang hrang a ti ang.
Neurologic Exam neih a ni
He test chhung hian doctor chuan a hnuaia mi ang hian a ti ang:
- Naute hmasawnna chanchin leh tuna a dinhmun hriat tumin zawhna an zawt ang che emaw, test tenau te an ti ang che.
- Naute hian lu-ah hliam emaw, thluak emaw, nervous system emaw a tichhe tawh em tih zawt rawh.
- Naupai lai khan natna hrik i neih leh neih loh an zawt ang a, naute pian hnua meningitis ang chi natna i neih leh neih loh an zawt ang. Chungte chuan hydrocephalus (thluak chunga tui awmkhawm) a thlen thei a ni.
- Naute chu a luak chhuak em tih zawt la, a hma aia nasa zawkin a thinrim em tih emaw, lu na (i.e., nungchang thlak danglam emaw, thlamuan theih loha tap) a lantir em tih zawt rawh. Hengte hi thluak chhunga pressure sang zawk chhinchhiahna a ni thei.
- Naute hian seizures a nei tawh em tih zawt rawh.
Taksa lam Exam
He test neih chhung hian lu vel tehna bakah hian doctor chuan a hnuaia mite hi a en bawk ang:
- Fontanels: Hei hi naute lu chunglama hmun nem tak tak , fontanels an tih chu a ni. Hengte hi luruh ruhte chu a la inzawm kim lohna hmunte a ni. Hei hian naute a pian huna a lu chu awlsam taka a chhuah theihna tur a ni. Lu hnung lama fontanel hi thla 2-3 chhungin a khar tlangpui. Lu hmalam fontanel hi thla 9 leh 18 inkarah a khar thin. He fontanel hi a lian a, a bulging a, a khauh a nih chuan intracranial pressure (ICP) tihpunna chhinchhiahna a ni thei.
- Lu chhunga thisen zam lian tak tak: Hei hi thluak chhunga thisen kalna kawng hrang hranga thisen volume sang zawk chhinchhiahna a ni.
- `Setting-Sun Eye Phenomenon`: Naute mit chu hnuai lam hawiin a awm reng a, hmalam hawi nghal mai ai chuan. Hei hi thluak chhunga pressure sang zawk chhinchhiahna a ni bawk.
- Taksa tihpun loh: Ei duh loh vanga taksa rihna tihpun loh, ``Failure to Thrive'' kan tih hi a chang chuan thluak lama harsatna nen a inzawm thei bawk.
Imaging Test te pawh a awm
Hei hian a hnuaia mite hi a huam thei ang:
- `(Ultrasound Scan)` (Ultrasound Scan): Hei hi doctor-in a tih theih hmasak ber a ni. A chhan chu a him (non-radioactive), a rang, tih a awlsam, naute mut tir a ngai lo. Naute hmalam fossa (a bik takin lu hma lama awm) chu khar loh chuan he scan hian thluaka thil tam tak a en thei a ni.
- `(Computed Tomography - CT Scan)` (CT Scan): He scan hian thluak tissue inthlak danglamna a zawng thei a. Mahse, radiation a hman avangin doctor chuan `(Ultrasound)`-in thu dik a pek loh chuan emaw, naute mut tir theih loh emaw chauhvin hetiang hi a rawt a ni.
- Magnetic Resonance Imaging (MRI) scan: Hei hi MRI tih dan bik, rang tak a ni. Naute chu sedated a ngai lo. Thluak chhunga tui tam lutuk chu a hmuchhuak thei a ni.
Macrocephaly natna avanga harsatna awm thei te chu engte nge ni?
Tin, ``(Macrocephaly)`` natna nena inzawm harsatna awm thei te pawh kan hriat a ngai bawk. Hengte hi mi zawng zawngin kan tawng vek dawn lo a, mahse hriat chian a tha.
- Brainstem compression: Lu lian vangin thluak chhungril lamah hmun a nei tlem a nih chuan thluak chu a compress thei a ni.
- Hydrocephalus (thluak chunga tui): Enkawl vat loh chuan hei hi nunna atana hlauhawm a ni thei.
- Seizures leh epilepsy natna te.
- Hmasawnna lama tihkhawtlai.
- Thluak hnathawh dan pangngai lo.
Macrocephaly hi engtin nge enkawl a nih?
Awle, chuti a nih chuan he `(Macrocephaly)` hi engtin nge i enkawl? A pawimawh ber chu a enkawlna chu a chhan bulpuiah a innghat a ni.
(Benign Familial Macrocephaly) leh (Nausen laia Subarachnoid Space tihzauh - BESSI) te a ni.
I naute hian neurological symptoms a nei lo va, a hmasawnna tur milestone a hlen chhuak tha a, chhungkaw history-ah lu lian tak a nei a nih chuan he lu lian tak hi thlahtute atanga lo chhuak a nih a rinawm. Chutiang a nih chuan , enkawlna a ngai lo. `(BESSI)` pawh hi harsatna nei lo dinhmun a ni. Hemiah hian thluak hmun thenkhatah `(Cerebrospinal Fluid)` (cerebral spinal fluid) tlem a awm a, mahse a pawi lo a, enkawl loh chuan hun kal zelah a reh mai ang.
Genetic atanga lo chhuak (Macrocephaly) .
Heng hunah hian enkawl chhunzawm zel a ngai mai thei. Hei hian taksa lam enkawlna, hnathawhna lama enkawlna, thusawi leh tawng hmanga enkawlna, leh nungchang lama enkawlna te a huam thei a ni.
Thluak a hring emaw, thluaka thisen chhuak emaw
Chutiang a nih chuan tui tam lutuk lakchhuah emaw, thisen chhuah tihtawp emaw nan operation neih a ngai mai thei.
Thluak natna (brain tumor) a awm
Enkawlna kawng hrang hrangah chuan operation, chemotherapy, radiation therapy, leh steroid te a tel.
Macrocephaly hi a veng thei ang em?
Macrocephaly hi lu lian tak sawina atana hman thin thumal mai a ni. A thumal ngei pawh hian a pawi tihna a ni lo. I chhungte hian lu lian tak tak neia hriat an nih chuan lu lian tak neih hi thil pangngai tak, hrisel tak a ni thei. I naute doctor chuan macrocephaly hi damdawi lam thil a awm leh awm loh a rel ang.
Macrocephaly venna tur hian engmah tih theih a awm lo tak zet a ni. Mahse, a thlentu dinhmun tam tak control theihna tur enkawlna a awm.
Ka naute hian Macrocephaly a vei a nih chuan eng nge thleng ang?
I naute hian `(Macrocephaly)` a neih chuan eng nge thleng ang?
I naute lu hi a lian a, mahse a danglamna chu a pangngai (developmental milestones, neurological tests) a nih chuan ``macrocephaly'' hi a hlauhawm lo tlangpui a, a rah chhuah pawh a tha hle. Enkawl a ngai lo. Hei hi i naute chu ``benign familial macrocephaly'' a vei tih hmuhchhuah a nih chuan a ni tlangpui.
Mahse, macrocephaly awm chhan bulpui a awm a nih chuan beisei tur chu a chhan bik a innghat ang. I naute enkawl dan tur chu a tan bik a ni ang.
Engtikah nge Doctor ka hmuh ang?
Hei hi a pawimawh hle. I naute zingah heng symptoms zinga pakhat tal i hmuh chuan doctor pan nghal rawh.
- Naute lu chunga hmai ( soft spot) a bulh chuan.
- Chaw ei duhna i neih loh chuan.
- I luak fo chuan.
- Mit chetna pangngai lo a awm chuan.
- A tlangpui aia mut hahdam zawka i hriat chuan.
- A hma aia i thinrim a, thlamuan harsa i tih chuan.
Heng symptoms te hian naute dinhmun a danglam thei tih a tilang a, chuvangin doctor chuan a chhui chiang ang a, enkawl a tul leh tul loh a rel ang. Hlauthawng suh, damdawi lam thurawn zawng nghal rawh.
Naupang tête lu chu engtiang chiahin nge a lian?
Nausen laia naute lu a sei lian zia hi han thlir ila. Hengte hi hlutna pangngai mai mai a ni em? Hemi atan hian doctor-te chuan growth chart an pawm a ni. Naute lu chu a thang pangngai em tih dik taka hretu an ni. Clinic chuan heng tehnate hi a la ang a, a hrilhfiah ang che.
(Macrocephaly) leh (Megalencephaly) hi eng nge an danglamna?
Heng thumal pahnih hi eng emaw chen a inang viau a, mahse a danglamna tlem a awm.
`(Macrocephaly)` tih hi thumal zau tak a ni. ‘Lu lian danglam tak’ tihna mai a ni. `(Megalencephaly)` hi `(Macrocephaly)` thlentu pakhat a ni thei.
``Megalencephaly'' tih hi a chiang zawk. ‘Thinlung lian lo tak’ tihna a ni. ' .
“Nausen laia benign extra-axial collections” tih hi eng nge ni?
Hei hi `(Benign External Hydrocephalus)` an ti bawk. Chumi awmzia chu naute thluak leh luruh inkarah tui tlemte a awm khawm tihna a ni. Hei hi nausen lu lian tak takah chuan a tam hle. Enkawl a ngai lo tlangpui. I doctor chuan i naute chu uluk takin a enkawl ang. A tam zawkah chuan naute an lo upat deuh deuh chuan he natna hi a bo vek a ni.
A tawp berah chuan thil hriat reng tur
Okay, chuvangin kan sawi tawh atang hian thil pawimawh tak tak i hriat reng tur thenkhat han thlir ila.
Macrocephaly tih awmzia chu i naute lu chu a tlangpui aia lian a ni tihna a ni. Hei hi pian tirh atangin hriat theih a ni fo.
A pawimawh ber chu lu lian zawng zawng hi natna a ni vek lo. I chhungkuaa mi dangte pawhin lu lian tak tak an nei a, chhinchhiahna dang a awm loh chuan hei hi a pawi lo thei a ni.
Mahse, ``Macrocephaly'' hi a chang chuan natna khirh tak chhinchhiahna a ni thei.
Chuvangin, i naute doctor chuan taksa leh thluak lam uluk takin a enfiah ang a, a tul chuan a lu chu imaging test (scan) a ti ang.
Chu test result a\angin doctor chuan a chhan chu a hre chhuak ang a, enkawlna tur ruahmanna \ha tak a siam ang.
I naute chungchangah ngaihtuahna i neih chuan, a bik takin kan sawi tawh warning signs i hmuh chuan doctor pan ngei ngei tur a ni. A pawimawh ber chu hlauthawng ni lovin, damdawi lam thurawn mumal tak lak a ni. I naute hrisel taka dam leh theihna tura duhsakna hlan!
👩🏽 ⚕️ Zawhna dang (FAQ)
💬 Macrocephaly hi sakeibaknei lu nei natna a ni em?
Layman tawngkam chuan naute lu chu an kum rualpui naupang dang 98% (the 98th Percentile) aiin a lian zawk a nih chuan hei hi damdawi lam thumal hman a ni. Hei hi natna a ni ngai lo va, chhungkaw member (genetically) chuan lu lian tak nei se, naute lu pawh a lian ang (Benign familial macrocephaly) hi dinhmun hrisel tak a ni.
💬 Chuti a nih chuan engtikah nge lu lian tak neih i hlauh ang?
Lu chu zawi zawiin a lo thang chak zawk a nih chuan, naute chu a luak fo a nih chuan, mit chu ni tlak a nih chuan, leh lu chhunga thisen kalna (veins) hmuh theih a nih chuan, hydrocephalus an tih chu hlauhawm tak a ni ngei ang.
💬 Hei hi scan a ngai em?
Doctor chuan thla tin lu circumference a teh a, a pangngai lo taka a pung tih a hmuh chuan ultrasound scan emaw MRI scan emaw hmangin thluak chhunga pressure awm leh awm loh an enfiah ngei ang. Harsatna a awm chuan tube (shunt) dahin tui chu lakchhuah theih a ni.
` Lu lian, macrocephaly, naute lu, thluak thanlenna, hydrocephalus, genetic diseases, neurological diseases











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