Neuromyelitis optica , emaw, a tawi zawnga kan sawi NMO emaw tih hi i hre tawh em? A ni lo mai thei. A chhan chu khawvela natna tlanglawn tak a nih loh vang a ni. Mahse kan mit leh ruhro (spinal cord) direct-a nghawng thei natna khirh tak a ni. Chuvangin, hemi chungchang hi hriat a pawimawh hle. Vawiin hian i hriatthiam theih tur awlsam takin kan sawi dawn a ni.
A awlsam zawngin NMO chu eng nge ni?
NMO hian hming dang eng emaw zat a nei bawk. Thenkhatin Neuromyelitis Optica Spectrum Disorder (NMOSD) an ti a, thenkhat chuan Devic’s Disease an ti bawk. Hei hi thil mak tak mai a ni. Kan taksa invenna system, immune system hian tihsualin kan cell hrisel tak takte chu a rawn bei tan ta a ni. Keimahni sipai ngeiin mahni ram an bei ang mai a ni. He attack hian kan central nervous system hmun hnih a target ber a, chungte chu mit atanga thluak thlenga information phurtu optic nerve leh ruhro hnuai lam pan thin spinal cord te an ni.
He natna hi kawng lian pahnih a awm thei a:
1. Monophasic NMO: Hemiah hian ni emaw kar emaw chhungin symptoms a lo lang nghal a, attack vawi khatah a reh ta a ni.
2. Relapsing NMO: Hei hi a tam ber chi a ni. Hetah hian symptoms a lo lang a, hun engemaw chen a reh bawk. Mahse, chutah chuan thla tam tak emaw, kum tam tak emaw hnuah pawh beihna dang a thleng thei a ni. Attack apiangin symptoms a na zual thei.
A chi khatna hian hmeichhia leh mipa a nghawng thei a, mahse chi hnihna, a nih loh leh NMO relapsing hi mipa aiin hmeichhiaah a tam zawk. Naupang tê tê a nghawng thei bawk.
NMO natna lanchhuahna chu engte nge ni?
NMO symptoms hi chi hnih ah then a ni. Heng zinga pakhat tal i neih chuan a rang thei ang bera Doctor pan a pawimawh hle.
| Damdawi lam dinhmun | Hrilhfiahna leh a lan chhuah dan |
|---|---|
| Mit lam natna (Optic neuritis) a awm | Hei hi mit chhunga optic nerve a inflamed lai a ni. I mit chhungah natna nasa tak i nei nghal mai thei . Hei hi mit hmuh lohna (blurred vision) pawhin a zui thei a, a chang chuan mit hmuhna hloh vek pawh a awm thei bawk. Mit pakhat a nghawng tlangpui a, a chang chuan mit pahnih a nghawng thei bawk. |
| Transverse myelitis a awm bawk | Hei hi ruhro chhunga ruhro (spinal cord) a lo hring chhuah lai a ni. Hei hian kut leh keah natna, chak lohna, rilru hahna, paralysis emaw a thlen thei a ni. I bladder leh bowels control i hloh thei bawk. Chu bakah, natna lan chhuah dan, luak chhuak, luak chhuak, hiccups awm reng, kawng khauh, leh lu na te pawh a awm thei bawk. |
Naupang tête hian NMO an vei chuan an nungchang tihdanglam, hriatna ṭha lo, seizure, coma ang chi natna lan chhuahna na tak tak an nei thei a ni.
NMO hi MS (Multiple Sclerosis) nen a inang em?
Ni lo, hei hi mi tam tak buaina hmun a ni. MS hi Multiple Sclerosis tihna a ni a, natna dang, nervous system tichhe thei, immune system hnathawh avanga lo awm a ni. Tun hma chuan doctor-te chuan NMO hi MS chi khat niin an ngai a. Mahse tunah chuan zirchianna chuan heng natna pahnih hi a danglam vek tawh tih hmuhchhuah a ni.
Chutiang inthlak danglamna thenkhat chu hetiang hi a ni :
| Thlentu | NMO (Neuromyelitis Optica) tih hi a awm a. | MS (Multiple Sclerosis) natna hi a awm thei lo. |
|---|---|---|
| Natna lo chhuah chak dan | Symptoms hi a tlangpuiin a rang hle a, a na hle bawk. | Symptoms hi a tlangpuiin a lo lang zawi zawk a, hun rei zawkah a lo lang thin. |
| Thisen test a ni | NMO hriat theihna tur thisen test (antibody test) bik a awm a. | Hetiang thisen test bik hi MS hriat theihna tur a awm lo. |
| MRI scan hmanga thluak a scan | Natna bul tan tirh lamah chuan thluak MRI scan hi a pangngai angin a lang thei. | MS-ah chuan thluak MRI scan-ah hian inthlak danglamna hmuh tur a awm tlangpui. |
| Thil dang pawh a awm | Symptoms, luak chhuak, luak chhuak, leh hiccups te hi a awm fo thin. | Heng symptoms te hi MS ah hian hmuh tur a awm lo. |
Eng thilin nge NMO hi a thlen?
Dik tak chuan doctor-te chuan NMO awm chhan dik tak hi an la hre lo. Thla khat atanga thlah dangah a kal zel tih finfiahna a awm lo. Mahse thil pakhat chu a chiang. NMO vei tam tak chuan autoimmune diseases dang an nei , a nih loh leh an chhungte pawhin an nei ve tho. A awlsam zawngin kan taksa defense system, immune system-in kan cell hrisel tak takte a rawn beih sualna dinhmun a ni. Diabetes (Type 1 Diabetes), rheumatoid arthritis, psoriasis, leh vitiligo te hi chutiang natna entir tlemte chauh an ni.
Engtin nge natna hi hriat chhuah a nih?
I natna lan chhuah dan a zawh hnuah i doctor chuan a enfiah ang che. Hei hian i ngaihtuahna thiamna, i mit hmuhna, i thusawi, i taksa chakna leh i reflexes te test a huam ang.
Chu bakah, heng test te hi tih theih a ni bawk:
- Thisen test: NMO vei zinga 70% aia tam chuan an thisenah protein bik, antibody an tih chu an nei a. Hei hi thisen test hmanga hriat theih a ni.
- Spinal fluid test: A chang chuan ruh atanga tui lak a, test a ngai mai thei.
- MRI scan: MRI ( magnetic resonance imaging) hmanga enfiah a ni.) tih hi magnet lian tak leh computer hmanga i taksa chhungril thlalak chiang tak tak lakna a ni. Hei hian i ruhro (spinal cord) a hring em tih hriat nan a pui thei a ni.
- Mit enfiah: Mit lam doctor hnenah refer i ni thei a, ani chuan mit nerve a chhiat leh chhiat loh enfiah nan OCT (Optical Coherence Tomography) ang chi test bik a ti ang.
NMO enkawlna tur engte nge ni?
Hei hi a pawimawh ber a ni. NMO damdawi a la awm lo. Mahse enkawlna tha tak tak a awm a, chu chuan symptoms control thei tur leh nakin lawka attack lo awm tur venna kawngah a pui thei a ni.
- Anti-seizure drugs: Tun hnaia NMO atana phalna thar eng emaw zat a awm. Eculizumab (Soliris), inebilizumab-cdon (Uplizna), leh satralizumab-mwge (Enspryng) te hi heng damdawi thenkhat te hi an ni. Heng damdawi te hian kan cell hrisel tak takte beitu antibodies te chu target-in hna an thawk thei lo. Chu bâkah, i doctor chuan taksa chakna tichhe thei damdawi dang a pe thei bawk.
- Steroids: Steroid damdawi hi taksaa inflammation tihziaawm nan pek thin a ni. Chungte chu vein (IV) hmanga pek a ni tlangpui.
- Plasma exchange: Plasmapheresis an ti bawk a, hei hi thisen tithianghlimtu ang a ni. Machine bik chuan i thisen atanga plasma chu a then a, chu chuan antibody tha lo tak tak a nei a, chu chu a paih chhuak thin. Tichuan, a thlaktu tur dah belh a ni a, thisen thianghlim chu i taksaah dah leh a ni.
Take-Home Thuchah a ni
- NMO hi autoimmune natna hmuh tur awm lo mahse na tak a ni a, kan mit leh ruhro a nghawng a ni.
- Mit na nghal mai, mit na lo, i ke ruh chak lo emaw, hrual emaw ang chi symptoms i neih chuan tihkhawtlai lohvin doctor rawn la.
- NMO hi MS (Multiple Sclerosis) nen chuan natna danglam tak a ni. Thisen test bik chuan an pahnih hi a thliar hrang thei a ni.
- Dam kim theih ni lo mah se, tunlai hian a natna lan chhuah dan thunun tur leh nakin lawka beihna laka invenna tur damdawi tha tak tak a awm a.
- Hemi chungchangah hian nangmah emaw, i hriat miin emaw rinhlelhna emaw zawhna emaw i neih chuan i doctor nen zalen takin inbia ang che.











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