Thu i sawi lai hian a chang chuan thu dik tak zawn kawngah harsatna i nei em? A nih loh leh mi pakhat thusawi hrethiam turin hun engemaw chen i hmang em? Hun kal zelah heng thilte hi a chhe zual zel niin a lang em? Hei hi kum upat deuh deuha thil thleng mai a ni lo. He dinhmun, kan sawi tur, ‘Primary Progressive Aphasia’ (PPA) tih hi i hriat a pawimawh mai thei.
Primary Progressive Aphasia (PPA) hi eng nge ni?
A awlsam zawngin sawi ila, Primary Progressive Aphasia (PPA) hi kan thluak ṭawng nena inzawm thilte tihchhiat avânga thu ziak thiamna leh hriatthiamna a tlahniam zauh zauh ṭhinna dinhmun a ni. ‘Aphasia’ tih hi thluak chhiat avanga tawng hman thiamna hloh hi a ni.
Tunah chuan he natna ‘aphasia’ an tih hi neurodegenerative disease (thluak natna) a lo awm a, hun kal zelah a zual zauh zauh a nih chuan doctor-te chuan ‘primary progressive aphasia’ an ti a ni. A tirah chuan, i ngaihtuahna sawi chhuah nân thumal dik tak hmuh chu i harsat phah mai thei. Hun a lo kal zêl a, he dinhmun hi a zual zêl a, i ziak thiamna te, ṭawng thiamna te, a nih loh leh ṭawng hriat thiamna te chu i hloh vek thei a ni.
Vawi tam tak chu PPA awm chhan bulpui ber chu thluak natna zual zel, Alzheimer natna emaw, frontotemporal dementia emaw ang chi a ni. Heng natnateah hian kan thluak peng hrang hrang, thusawi thununtu leh thumal leh a awmzia hrethiam tura min puitu te chu zawi zawiin a chak lo chho zel a.
PPA chi hrang hrangte chu engte nge ni?
Tunah chuan PPA chi hrang hrang hi eng nge ni tih i lo en ang u. Specialist doctor-te chuan hei hi chi thum-ah an ṭhen a:
- Logopenic progressive aphasia: Hetiang chi ah hian thumal dik tak hmuh harsa i ti thei. Mi dangte thusawi hriatthiam harsa i ti thei bawk. Entirnan, eng emaw sawi duh mah la, thumal dik tak i hmu thei lo ang maiin i inhria. A châng chuan, thumal a buaithlâk thei bawk.
- Progressive non-fluent aphasia: Hei hi grammar dik lo emaw, tawng thiam leh thiam taka sawi harsatna emaw a ni. Thusawi chu a rilru a buai hle thei a, thumal siam a harsa thei a, sentence a tawi hle thei a, thusawi chu thawhrimna nasa tak angin a lang thei bawk.
- Semantic dementia: Hetiang chiah hian miten thil pakhat an hmuh chuan a hming hriat reng harsa an ti hle. Thumal pakhat zel awmzia hriatthiam harsa an ti thei bawk. Entirnan, miin ‘cup’ a tih hian eng nge a nih leh eng nge a tih tih an hrethiam lo mai thei. Amaherawhchu, grammatically dik takin an tawng thei a, mahse a thumal awmziaah chuan an bo vek a ni.
Hetiang dinhmun hian tute nge a nghawng nasa ber?
Tu pawhin PPA an nei thei. Mahse, mi thenkhat chuan an vei theihna chance a sang zawk. Chung zingah chuan:
- Chhungkaw zinga tu emaw chuan PPA a lo nei tawh a nih chuan (Family history of PPA) chu chu eng emaw chen chu rochun theih a ni tihna a ni.
- Mi thenkhat chu an piang a, genetic changes (entir nan, GRN gene-a gene mutations) . Mahse, hei hi mi zawng zawng tan chuan a awm lo.
- Zirna thenkhatah chuan he risk hi zirlai harsatna nei tan pawh a sang deuh tih hmuhchhuah a ni , mahse hemi chungchangah hian zirchianna dang neih mek a ni.
PPA natna lan chhuah dante chu engte nge ni?
PPA symptoms hi kum 50 leh 70 inkarah a lang tan tlangpui a, a tir lamah chuan thusawi harsatna tenau tak angin a intan thei. Mahse hun kal zelah ngaihtuahna leh thutlukna dik siamnaah nghawng a nei thei a ni.
PPA natna lan chhuah dan ber chu:
- Thil pakhat tana thumal dik tak hmuh harsat . A châng chuan "Chu... chu, chu chu eng nge..." tih ang chi thumal chu a aiah hman theih a ni.
- Thusawi laiin chawlhsan fo, thumal inkar hmun zau zawk .
- Grammatical dik lo awm fo thin . Entirnan, verb hman dik loh.
- Thusawi slow tak tak .
- Midang thusawi hriatthiam harsa , a bik takin sentence buaithlak tak takte.
- Hun a kal zel a, tawng hman thiamna chu a bo vek a ni .
PPA siam chhuahna atana thil pawimawh ber berte chu engte nge ni?
PPA thlentu ber chu kan thluaka ṭawng thununtu hmun hrang hrang – a bik takin thluak veilam lama awmte chak lohna leh tihtlem (atrophy) zauh zauh hi a ni. Chutianga thluak tissue a lo tlem chuan kan inbiakpawhna chu direct-in a nghawng a ni.
A châng chuan, he thluak chhiatna chi hi kan pian tirh aṭangin gene mutation avângin a inṭan thei a ni . A châng dangah chuan chhan hriat lohvin a thleng thei bawk.
Mi tam tak tan chuan doctor-te chuan a risk factor chiang tak an hmu thei lo. Tunah hian environment leh genetic factors inzawmkhawm hian PPA a thlen thei niin an ngai. Gene mutation nei lo mah la, i chhungkuaa mi tu emaw chuan he natna hi a nei thei a ni.
Engtin nge PPA ka neih leh neih loh ka hriat theih ang?
I doctor chuan i symptoms a zirin PPA i nei tih a ringhlel mai thei. A hmasain, i doctor chuan i thusawi lama harsatna i neih ṭan dan te, hun kal zelah a zual zel em tih te, leh harsatna dang i neihte chu zawhna tam tak a zawt ang che . I medical history leh family history te pawh a en ang a, PPA vei theihna chance a sang zawk em tih a en bawk ang.
He diagnosis hi nemnghet tur chuan hetiang test hi i neih a ngai ang:
- Specialized cognitive tests: Hengte hian i hriatrengna, tawng thiamna leh ngaihvenna ang chi thilte a test thin.
- Brain scan: Entirnan, MRI emaw CT scan emaw tih theih a ni. Heng scan te hian thluak hmun eng emaw zat a tihtlem emaw, thluak dinhmun dang emaw a enfiah thei a ni.
- A châng chuan thisen test ang chi thilte chu damdawi lam thil dang tih loh nan tih theih a ni.
PPA enkawl dan tur chu engte nge ni?
Tunah hian PPA damdawi a la awm lo a, he natna hi a zual zel tur ven dan tur a awm lo bawk. Mahse, enkawlna thenkhat chuan natna zual zel tur a tikhawlo thei a, i nunphung a ti tha thei bawk.
PPA vei te hian enkawlna an dawng thei a, chungte chu:
- Speech therapy leh cognitive therapy ah te tel ve thin . Hei hian i tawng leh ngaihtuahna thiamna chu a rei thei ang bera vawng reng turin a pui thei che a ni. Exercise ang maiin ngaihtuah la, he therapy hian i thluak chu chutiang thiamna hmang turin a zirtir a ni. Speech therapist chuan thumal zawn dan leh sentence dahkhawm dan hrang hrang a zirtir ang che.
- Inbiakpawhna kawng thar zir , sign language te, thlalak hman te, a nih loh leh inbiakpawhna hmanrua bik hman te.
- SSRIs (Selective Serotonin Reuptake Inhibitors) ang chi damdawi te hi PPA nena lo awm thei nungchang inthlak danglamna, lungkhamna, emaw lungngaihna te enkawl nan hman theih a ni. Hengte hi damdawi lam thurawn hnuaiah chauh lak tur a ni.
- PPA awm chhan bulpui ber chu Alzheimer’s disease a nih chuan, chutiang atana phalna nei damdawi ei hi a tha. Heng damdawi te hian PPA hi a tidam kim lo nain, a natna lan chhuah dan thenkhat chu a thunun thei a ni.
PPA vei theihna hi a tlahniam thei ang em?
PPA hi genetics in a nghawng bawk avangin 100% surefire way a awm lo . Mahse, nunphung ṭhenkhat tihdanglamna chuan dementia , hriatrengna hlohna thlentu natna vei theihna a ti tlem thei a ni. Heng thilte hian PPA hi indirect takin a nghawng thei bawk:
- I kum, i mipa leh hmeichhia leh i taksa chi hrang hrang nena inmil tur taksa rihna hrisel tak neih .
- Lu natna nasa tak laka invenna. Hei hian lirtheia chuang laiin seatbelt vuah, tlu laka invenna, etc. Infiamna khelh hunah pawh invenna helmet vuah a pawimawh bawk.
- Thei, thlai, whole grains, lean protein, leh thau hrisel tak tak a pai a niEi leh in inthlau tak ei.
- Exercise neih fo thin ang che. Aerobic exercise leh strength training te pawh telh vek tur a ni . Ni khatah minute 30 tal kea kal pawh a tha.
- Nitin zu in tur khap tlat ang che. Mipa tan ni khatah vawi hnih aia tlem in tur a ni a , hmeichhia tan ni khatah vawi khat aia tlem in tur a ni .
- Khawtlang inzawmna nghet tak neih reng . Thiante leh chhungte nena inbiakna leh hlim taka awm hi thluak hriselna atan pawh a pawimawh hle.
- I thisen sang leh cholesterol level chu hrisel range chhungah dah la, i thinlung hriselna pawh uluk takin enkawl rawh. Diabetes ang chi natna i neih chuan uluk takin control la.
- Meizial zuk bânsan, i zuk chuan i thluak leh i taksa pum pui tan a \angkai hle.
PPA vei hian eng ang hmalam hun nge a beisei theih ang?
PPA hi hun kal zelah a na zual zel a ni . PPA vei tam tak chuan kum tam tak chhung chu an tawng thiamna an hloh vek a, chu chuan midangte nena inbiak theihna a tikhawtlai a ni.
Medical record-ah chuan he natna vei tam zawk hi natna an hmuhchhuah hmasak ber atanga kum 3 atanga kum 12 chhung vel an dam tih a tarlang. He hun chhung hi mi hrang hrangah a inang lo thei. Hun a kal zel a, mi tam tak chuan ni tin hna, incheina, ei leh in, leh inbual ang chite thawk tûrin mi dangte ṭanpuina an mamawh ang. Chuvangin chutiang mi tan chuan chhungte thlawpna leh hmangaihna hi a pawimawh hle a ni.
I doctor zawh tur zawhna pawimawh
Nangmah emaw, i hnaih ber emaw hian PPA a vei nia i rinhlelh a nih chuan, emaw, he natna hi i vei tih hmuhchhuah a nih chuan, i doctor hnenah hetiang zawhna hi zawh a tha ang:
- PPA natna lan chhuah hmasak berte chu engte nge ni? Heng symptoms te hi ka nei em?
- PPA hriat theihna atan eng test nge hman thin ? Chu test atang chuan eng nge i hmuh beisei?
- PPA natna zual zel tur tikhawtlai thei tur enkawlna a awm em? Eng enkawlna nge ka tan a tha?
- PPA ka neih chhung hian ka nunphung tihsan nan eng nge ka tih theih ang?
- Hetiang dinhmun hmachhawn tur hian kei leh ka chhungte tanpuina kan hmuh theihna hmun a awm em?
Kan sawi tawh atanga i hriat reng tur pawimawh ber berte chu hetiang hi a ni! (In lama hruai tur thuchah)
Primary progressive aphasia (PPA) hi tawng thiamna a bo zauh zauh thin a ni. It is a symptom of an underlying neurodegenerative disease , natna chuan thluak cell te chu a tichhe zauh zauh thin.
Mi thenkhat chuan PPA hi Alzheimer natna ang deuh niin an ngai.A symptom hmasa ber pawh a ni thei. Mi dangte tan chuan frontotemporal dementia an tih natna nen a inzawm a ni.
A chhan dik tak chu hriat chian ni lo mah se, boruak leh thlahtute inzawmkhawm avânga lo awm a ni fo .
PPA tihdanglam theih dan awm lo mah se, enkawlna hian a theih ang anga rei tak inbiakpawhna thiamna vawng reng turin a pui thei a ni. Hei hi Speech therapy leh cognitive therapy te hian a pui thei a ni.
Heng symptoms te hi i neih chuan hlau suh . A pawimawh ber chu a rang thei ang bera damdawi lam thurawn lak hi a ni. I doctor nen i tana enkawlna tha ber leh thurawn tha ber tur chu zalen takin sawipui rawh. Engmah ngaihtuah buai suh, information dik tak lak leh damdawi lam thurawn lak hi hetiang dinhmunah hian tih tur tha ber a ni.
` Primary progressive aphasia, PPA, tawng thiam lohna, tawng lama harsatna, thluak natna, thluak lam natna, Alzheimer’s, dementia











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