I vun a thim a, a khauh chho zel em? Scleroderma chungchang hi i zir dawn teh ang!

A chang chuan i vun hi a hma aia tlem a thim leh tight deuhin i hria em? A nih loh leh i ruh natna emaw, zing lama i natna emaw i nei em? Chûngte chu kan ngaihven vak lo mai thei thilte a ni. Mahse, Scleroderma tih hming pu natna hlauhawm tak chhinchhiahna an ni thei bawk. Vawiin hian he thu hi chipchiar deuhin sawi ila, kan sawi dawn em ni?

Scleroderma chu eng nge ni?

A awlsam zawngin sawi ila, Scleroderma hi thil awm lo tak a ni a, i taksa chhunga tissue te chu a tlangpui aia thim leh khauh zawka awm thin a ni. A tam zawkah chuan vun a nghawng thin. Mahse a chang chuan, he natna hian taksa chhunga tissue dang eng pawh a nghawng thei a ni.

Hei hi a takah chuan autoimmune disorder a ni . Tunah chuan ‘autoimmune disorder’ tih hi eng nge ni tih i ngaihtuah mai thei. Kan taksa hian natna laka min vengtu sipai ang chi system a nei a, chu chu immune system an ti a. Mahse hetiang dinhmunah hian chu system chu a kal sual a, ram dang hrik do ai chuan kan cell tha tak takte chu a rawn bei tan ta zawk a ni. Tu nge keimahni ta leh tute nge hmelma tih kan hre thei lo ang mai a ni. Doctor-te pawhin hetiang thil hi a thlen chhan chiang takin an la hre thei lo.

Scleroderma i vei chuan i immune system chuan i taksa cell-te chu collagen tih protein siam tam lutuk turin signal a pe a ni. Kan taksa hian collagen a mamawh tak zet a ni. Kan taksa peng hrang hrangte thlawptu connective tissue chak leh hrisel tak siamtu a ni. Mahse a lo pung tam lutuk chuan vun leh tissue dangte chu a tlangpui aiin a thim zawk a, a fibrous zawk bawk.

Scleroderma hi natna khirh tak a ni a . Chumi awmzia chu heng symptoms te nen hian rei tak i nunpui a ngai mai thei a, i dam chhung zawng pawh a ni mai thei. Tin, i chhungril taksa peng hrang hrang tissue a nghawng chuan nunna atana hlauhawm harsatna a thlen thei bawk. Heart attack nei anga i inhriat emaw, thawk harsa i tih emaw, ei harsa i tih chuan 911 (or i awmna hmuna emergency number) call nghal la, damdawi in emergency room-ah kal nghal rawh.

I ruhkawr, a bik takin i kut zungtang leh ke ruh vel a na emaw, a khauh emaw i neih chuan doctor pan ngei ngei tur a ni.

Scleroderma chi hrang hrangte chu engte nge ni?

Doctor-te chuan scleroderma hi chi hnih ah an then a:

1. Localized Scleroderma: ‘Localized’ tih hian hmun khata inkhung hran tihna a ni. Hetiang chi hian taksa peng pakhat (a tlangpuiin vun) chauh a nghawng a ni. Vun thickened, waxy patch emaw streak emaw a siam thin. A tha ber chu localized scleroderma hi a chang chuan a mah chauhin a reh thei a ni . Tin, taksa peng dangah pawh a darh tlangpui lo.

2. 2. A rilru a hah lutuk chuan a rilru a buai em em a.Systemic Sclerosis: Hetiang chi hian vun bakah taksa peng dang a nghawng thei bawk. I thawkna system (thâwk leh rim hriatna atana ṭanpuitu taksa peng) leh i chaw ei (kan ei tur chu chakna lama chantirtu taksa peng) te a nghawng thei a ni. Scleroderma hian i thawk chhuah theihna emaw, ei tur tha tak tak i lakluh theihna emaw a nghawng chuan harsatna lian tak i nei thei a ni. Thihna thlen thei hial a ni. Systemic Sclerosis hian subtype pathum a nei bawk – diffuse, limited, leh sine sclerosis.

Diffuse Sclerosis natna a ni

‘Diffuse’ tih awmzia chu ‘widespread’ tihna a ni. Hetiang dinhmunah hian diffuse sclerosis hi taksa hmun zau takah a lo awm nghal a ni. Entir nan:

• Awm
• Pum chhunga awm
• Thighs a ni
• Arms a ni
• Ke te
• Hmai

Tin, vawi khatah taksa peng engemaw zat a nghawng thei bawk. Chumi awmzia chu:

• Chaw ei dan (Digestive system - GI tract) 1.1.
• Kidney a ni
• Thinlung
• Chuap

A rilru a buai em em a, a rilru a hah em em bawk a.

Doctor te chuan Limited Scleroderma hi CREST syndrome tiin an sawi fo thin . CREST-a letter tin hian a vanga symptom pakhat a entir a ni:

• C - Calcinosis: Vun chhunga calcium awm tam lutuk. Vunah hian hnah dum te te angin a lang thei.
• R - Raynaud’s syndrome: Kut zungtang leh ke ruh rawng danglam leh hring. Khua a vawt chuan an dum, a sen, a sen emaw a ni thei.
• E - Esophageal dysfunction: Chaw ei harsa leh acid reflux.
• S - Sclerodactyly: Kut zungtang vun a tight a, kut zungtang ben leh tihdik a harsa.
• T - Telangiectasias: Vunah hmun te te, sen emaw, rawng danglam emaw a awm. Chungte chu rulhut (spider web) ang maiin a lang thei.

Sine Sclerosis natna a ni

Sine Sclerosis-ah chuan a hmaa kan sawi tawh ang khan Limited Sclerosis symptoms hi a awm a, mahse vun erawh a nghawng lo . Chu chu CREST syndrome-a tarlan symptom thenkhat i nei thei a, mahse vun thickening hmuh tur a awm lo tihna a ni.

Scleroderma hi engtiang chiahin nge a awm?

Scleroderma hi natna hmuh tur awm lo tak a ni.Mithiamte chuan United States-ah hian mi maktaduai khatah 250 velin scleroderma chi thum hi an vei vek niin an chhut. Heng zinga mi 100,000 velin systemic sclerosis an vei a ni.

Scleroderma natna lan chhuah dan chu engte nge ni?

Scleroderma vei thenkhat chuan a tir lamah chuan symptom an nei lo mai thei. Mahse, mi tam tak tan chuan a lan chhuahna ber chu vunah thickened, waxy patches emaw streaks emaw lo lang hi a ni. Chu bakah, natna lan chhuah dan tlangpui dang engemaw zat a awm bawk:

• Joint natna
• Stiffness , a bik takin zing thawh veleh
• Chauhna (chau lutuk tih hriat reng reng) .
• Sawifiah loha taksa rihna tlahniam

Symptom dang i tawn (leh a nghawngna hmun che) chu scleroderma i neih chi hrang hrangah a innghat a ni.

Localized Scleroderma natna lan chhuah dan

Localized scleroderma vei te hian vun thickening chauh an nei tlangpui . He thickening hi hmun khatah a awm thei a, patch-ah pawh a awm thei bawk. A hnuaia vun hmunte hi a nghawng thei a ni:

• Awm
• Abdomen (pui chhung vel) .
• Kut leh ke (I kut leh ke) .
• Kut leh kut zungtang
• Ke leh ke ruh

Mahse, localized scleroderma, internal organs tichhe thei hi a awm lo hle .

Systemic Sclerosis natna lan chhuah dan

Systemic sclerosis hian symptom hrang hrang a thlen thei a. Hei hian vun a ti thim bawk a, mahse a tlangpuiin hmun zau tak leh hmun zau takah a awm thin. A bik takin hmai leh kut ah. Vun thim tak hi kut zungtang leh ke ruh atanga intan a, taksa pum puiah a darh thei a ni. Raynaud’s syndrome i neih chuan, a natna hmuna kut zungtang leh ke ruhte chu khaw lum (a tlangpuiin var, sen, emaw, purplish-blue rawng) i neih chuan a rawng a danglam thei a ni.

Systemic sclerosis hian i taksa peng dang leh tissue dangte pawh a ti lang thei bawk. Entir nan:

• Muscles: A bik takin kut leh ke (i taksa peng tawp)-ah a hring leh a hring.
• Joints: A khauh, a hring, leh a che thei lo.
• Lungs: Khuh leh thawk harsa (dyspnea).
• Digestive tract: Dysphagia, thinlung na, puak, chaw ei kham, leh ril\am.
• Thinlung:Lungphung pangngai lo (arrhythmia), thinlung chhehvela tui awm (pericardial effusion), leh thinlung ruh (fibrosis) a thim (fibrosis).
• Kidney: Kidney failure (hei hi nunna atana hlauhawm tak a ni thei).
• Genitals: Mipaah ​​Erectile Dysfunction (ED) a awm a, hmeichhiaah vaginal dryness a awm bawk.

Eng thilin nge Scleroderma hi a thlen?

Dik tak chuan doctor-te chuan scleroderma awm chhan dik tak hi an la hre lo .

Zirna thenkhatah chuan chhungkaw zingah eng emaw chen a kal thei tih hmuhchhuah a ni (nu leh pa atanga fate hnena kai theih tihna a ni), mahse a tlem em avangin genetic disorder a nihzia chiang taka finfiahna tur evidence a awm lo

Scleroderma natna thlen thei thilte

Tu pawhin scleroderma an vei thei a, mahse pawl thenkhatah chuan an hlauhawm zawk:

• Hmeichhia hian mipa aiin a let li velin he natna hi an vei tam zawk a ni.
• Kum 30 leh 50 inkar ah a awm tlangpui a, Scleroderma hi kum 30 hnuai lam ah a awm tlem hle.
• Mihring dumte hian scleroderma an vei tam zawk. Tin, natna hi an vei hma deuh duh bawk a, lung tichhe thei symptom an nei tam zawk a, vun symptom na tak tak an nei bawk.

Scleroderma natna avanga harsatna awm thei te chu engte nge ni?

Scleroderma vei te hian natna dang pahnih: Raynaud’s syndrome leh Sjögren’s syndrome te an vei theihna chance a sang zawk a ni.

Raynaud’s syndrome hian i kut zungtang leh ke ruh (i digit)-a thisen kalna kawng te te a nghawng a ni. Hetiang natna vei te hian symptoms episode (a then chuan ‘attacks’ an ti) an nei thin. Hei hi i kut zungtang chhunga thisen kalna kawngte chu a inzawm tlat thut a, a nghet lutuk a ni. Hei hian kut zungtang natna vei vun chu a ti hring thei a, i vun rawng pianpui aiin a ti eng thei bawk. A châng chuan, a sen hring pawh a lang thei bawk.

Sjögren’s syndrome hian i taksa gland thenkhatah tui a siam tlem phah thin – a tam zawkah chuan i ka chhunga salivary glands leh i mittui tlakna glands te hi a siam chhuak thin. Sjögren’s syndrome vei thenkhat chuan taksa ruh leh ruh natna an nei bawk.

Scleroderma chi thenkhat chuan harsatna lian tak a thlen thei . Chung zinga ṭhenkhat chu:

• Kidney tha lo a awm
• Pulmonary hypertension (thinlung atanga lung thlenga thisen phurtu thisen kalna kawng hrang hranga thisen sang) .
• Pulmonary fibrosis (lung tissue-a hliam awm) .
• Cardiovascular disease (i thinlung leh thisen kalna kawng tichhe thei harsatna) .
• Congestive heart failure, thinlung natna a ni
• Immunodeficiency a awm thei
• Gastrointestinal diseases (taksain ei tur a process dan leh nutrients a lakluh dan tichhe thei dinhmun) .
• Ngawt

Heng harsatna thenkhat hi chu thihna thlen thei a ni . Symptom thar emaw, danglam zel emaw i hmuh chuan a rang thei ang bera Doctor pan rawh. Heart attack chhinchhiahna, thawk harsa emaw, ei harsa emaw i neih nia i hriat chuan 911 (or i awmna hmuna emergency number) call nghal la, a nih loh leh damdawi in emergency room-ah kal rawh.

Engtin nge Scleroderma hi an hriat theih?

Doctor chuan taksa enfiahna leh test dang engemaw zat hmangin scleroderma a vei tih a hmuchhuak a.

Rheumatologist , doctor, immune system natna enkawlna lama tui tak pawh i hmuh a ngai mai thei. A enfiah ang che a, i symptoms te a zawt ang che. I natna lan chhuah dan te, engtik atanga a lo intan tirh te, eng thil pawhin a ti na zual ang tih te chu i doctor hnenah i hrilh tur a ni.

Tin, chutiang bawka chhinchhiahna thlentu natna dang i neih loh nan test eng emaw zat i neih a ngai bawk ang.

Doctor-te hian Scleroderma hi eng test nge an hman?

Scleroderma hmuhchhuah hi ‘differential diagnosis’ an tih danah a tel tlangpui. Chumi awmzia chu i doctor chuan natna dang a paih chhuak mai thei a, scleroderma i vei tih a hriat hmain i natna lan chhuah chhan hriat tumin test engemaw zat a nei mai thei tihna a ni. Test i neih theih thenkhat chu hetiang hi a ni:

• Thisen test a, i immune system hnathawh dan enfiah thin.
• Pulmonary function test hmangin i lung emaw thawkna lam emaw a nghawng em tih enfiah thin.
• Biopsy chu vun natna vei emaw, tissue dang emaw sample tlemte lak a, laboratory-a test a ni.
• Digestive (GI) symptoms i neih chuan endoscopy chu i rilru emaw, i pum emaw hnuai lam, camera te tak te, tube sei leh te tak tea dah hmanga enfiah a ni.

Hei bakah hian i taksa chhungril thlalak lak nan imaging test eng emaw zat i neih a ngai dawn bawk. Chung zingah chuan:

• Electrocardiogram (ECG) hmanga tih a ni.
• Echocardiogram (Echocardiogram - Echo) tih hi a awm lo.
• A rilru X-ray a ni
• CT scan (Computed Tomography - CT scan) hmanga tihchhuah a ni.

Scleroderma hi engtin nge enkawl a nih?

There is no cure for scleroderma , mahse i doctor chuan i natna lan chhuah dan control thei tur leh i nitin nunah nghawng a neih tlem theihna tur enkawlna hrang hrang zawng turin a pui thei che a ni.

I mamawh enkawlna chi chu i natna lan chhuahna hmun leh a nasat danah a innghat a ni. Scleroderma enkawlna hman tlanglawn thenkhat chu hetiang hi a ni:

• Vun enkawl dan: I vun a vawt loh nan cream leh moisturizer i hman a ngai dawn a ni.
• Immunosuppressants: Heng damdawi te hian i immune system hian cell leh tissue hrisel tak tak a tihchhiat loh nan a titawp thin.
• Symptoms bik control nan damdawi: Entirnan, i thisen sang control nan te, thawk hahdam nan te, kidney failure control nan te, emaw digestive symptoms tihziaawmna tur damdawi i ei a ngai mai thei.
• Physical therapy: Physical therapist chuan i taksa chezia a titha thei che a ni.
• Phototherapy: Hei hian vun natna enkawlna atan ultraviolet (UV) light eng tak, focused tak hman a ni. Hei hian vun thicked enkawl nan a pui thei a ni.
• Stem cell transplant: Mi thenkhat, symptom na tak nei te chuan stem cell transplant an mamawh mai thei. Hei hian thisen cell chhia te chu donor cell hrisel tak tak hmanga thlak a huam a ni.

Scleroderma ka vei a nih chuan eng nge ka beisei ang?

Scleroderma leh a symptoms te hi i dam chhung zawng enkawl i beisei tur a ni . Damdawi nghet tak awm lo mah se, mi tam tak chuan an natna lan chhuah danin an nitin nunah nghawng a neih tlem thei ang bera enkawlna leh nunphung tihdanglamna an hmu a ni.

Hun rei tak natna nena nun chu a châng chuan a lungchhiatthlâk hle thei a ni. I doctor hnenah support group emaw, zirna lama hun remchang emaw zawt la, chu chuan i stress leh rilru hriselna i enkawl theih nan a pui ang che.

Scleroderma hi ven theih a ni em?

A chhan dik tak hriat a nih loh avangin scleroderma .

Engtin nge ka in enkawl ang? (Mahni inenkawlna) .

I enkawlna pangngai bakah hian i nitin nunphung tihdanglamna engemaw zat siamin natna lan chhuahna thenkhat chu i thunun thei mai thei bawk. Chung zinga ṭhenkhat chu:

• I duh ang ei leh in hrisel leh exercise plan zawm.
• I dam loh laia taksa tihchakna nasa tak pumpelh .
• I vun hi i chhehvel nena inmil taka incheiin, pawn lama i chhuah dawnin sunscreen quality tha tak hmang la, venghim rawh.
• Ha tihfai leh checkup neih fo turin dentist (dental care provider) tlawh thin ang che.

Engtikah nge ka doctor ka hmuh ang?

Scleroderma hian symptom hrang hrang a thlen thei a, chuvangin a tir lamah chuan hriat harsa a ti fo thin. Natna thar emaw, symptom dang emaw i neih chuan, a bik takin a na zual a nih chuan doctor pan rawh. I natna lan chhuah dan hi thil dang avanga lo awm ni mahse, i doctor chuan a chhan chu a hrechhuak thei a, a thunun theih nan enkawl dan tur a rawt thei bawk.

I scleroderma enkawlna hian a thawk tha lo niin a lang a, emaw, i natna lan chhuah dan a danglam emaw, a na zual emaw a nih chuan – a bik takin i thawk emaw, i ei theihna emaw a nghawng a nih chuan – i doctor nen inbia ang che.

Engtikah nge Emergency Treatment Unit (ETU) ah ka kal ang ?

Heart attack symptoms , i rilru natna, thawk harsa, emaw, i ei thei lo anga i hriat chuan 911 (or i awmna hmuna emergency number) call nghal la, a nih loh leh damdawi in emergency department-ah kal rawh.

Doctor hnenah eng zawhna nge ka zawh ang?

Doctor i hmuh hunah heng zawhnate hi zawh theihnghilh suh:

• Scleroderma emaw natna dang emaw ka nei em?
• Eng ang Scleroderma nge ka neih?
• Eng ang enkawlna nge ka mamawh?
• Eng harsatna nge ka hriat bik tur?

Scleroderma vei dam rei zawng chu engzat nge ni ang?

Scleroderma vei tam zawk chuan nunna atana hlauhawm harsatna an nei lo .

Mahse, systemic sclerosis, internal organs tichhe thei i neih chuan harsatna lian tham i neih theihna a sang zawk. I doctor chuan i beisei tur leh thihna thlen thei harsatna i neih theihna a sang zawk em tih a hrilh ang che.

Scleroderma hi natna khirh tak a ni em?

Natna khirh tak dang ang bawkin scleroderma hi natna langsar tak, na tak a ni.. Hei hi a chhan chu i dam chhung zawngin natna lan chhuah dan chu i hmachhawn a ngai mai thei a ni. Mahse, chu chuan Scleroderma hian i nun a thunun dawn tihna erawh a ni lo. Mi tinin kan tawnhriat a inang lo. I hlauhthawnna te, rinhlelhna te, leh ngaihtuahna te chu i doctor nen sawiho rawh.

Scleroderma hi nunpui tur chuan a lungchhiatthlak hle thei. Doctor-te’n a chhan an hriat chian loh avangin leh enkawlna pakhat chauh a awm loh avangin, i natna lan chhuahna (symptoms) control tha thei tur damdawi hmuh nan hun engemaw chen a ngai thei. I doctor chuan i kalna apiangah a pui ang che.

I gut feeling ring la, ‘dik lo’ nia i hriat chu ring rawh. Symptoms inthlak danglamna tlemte pawh hi doctor-in a enfiah ngai harsatna chhinchhiahna a ni thei. Zawhna zawh hreh suh la, i natna lan chhuah dan emaw, i enkawl dan emaw chungchangah i ngaihdan sawi chhuak rawh.

Natna khirh tak nena nun hi a hahthlak hle thei. I natna lan chhuah dan enkawlna atana i thawhrimna avangin zahna leh hriatpuina engemaw chen pe turin hun hmang rawh.

Thil pawimawh thenkhat i hriat reng tur (Take-Home Message) .

Okay, tunah chuan Scleroderma chungchang hi kan sawi tam tawh hle. Thutawp atan chuan i hriat reng tur pawimawh ber berte chu hetiang hi a ni:

• Scleroderma hi natna hlauhawm tak, autoimmune disease a ni a, taksain collagen a siam tam lutuk a, vun leh a chang chuan chhungril lam taksa peng hrang hrang a ti thim thin.
• Hei hi chi hnih a awm a, chungte chu localized leh systemic te an ni. Systemic type hi a hlauhawm deuh a, a chhan chu internal organs te pawh a nghawng thei a ni.
• Symptoms a inang lo. A bulpui ber chu vun thicking, ruh natna, hahna, leh Raynaud’s syndrome te hi a ni.
• Damdawi nghet awm lo mah se, natna lan chhuah dan thunun theihna tur enkawlna tha tak tak a awm. I doctor nen inbia la, i tana tha tur enkawlna ruahmanna siam rawh.
• A hmaa hriatchhuah leh enkawl hi a pawimawh hle. Chuvangin heng symptoms te hi i neih chuan doctor thurawn la ngei ngei tur a ni.
• Hei hi hun rei tak chhunga awm a nih avangin rilru lama chak taka awm reng a pawimawh. A tul chuan support group-te hnen atangin tanpuina zawng rawh.

Lungngai suh, nangmah chauh i ni lo. Hriatna dik leh damdawi lam thurawn i neih chuan he natna hi hlawhtling takin i nung thei ang.

` Scleroderma, Scleroderma, Vun thim, Immune natna, Collagen, Raynaud’s syndrome, Systemic sclerosis, Vun natna