I fate chu a rawn sen nghal vat a, i hlau ngai em? A nih loh leh nau hnute a pek lai te, a tap lai te, a inher lai te hian thawk a harsat em? Nu leh pa tu pawhin hetiang thil an hmuh hian hlauhthawn hi thil pangngai tak a ni. Vawiin hian
Tetralogy of Fallot , congenital heart condition, hetiang symptoms thlen thei chungchang kan sawi dawn a ni. A hming hi a buaithlak deuhin a lang thei a, mahse awlsam takin han sawifiah ila.
Tetralogy of Fallot hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Tetralogy of Fallot hi nau piang laia thinlung natna pali awmte inzawmkhawm a ni. Congenital heart condition an ti bawk. Nausen pum chhunga a lo seilian laia thinlung lo thanglian chhoh laia harsatna lo awm thin a ni. Hei hian oxygen tamna thisen (red blood) chu oxygen tlakchhamna thisen (blue blood) nen a inhmeh tir thin. He thisen inzawmkhawm hi thinlung hian taksaah a pump lut leh thin. Chuvang chuan taksa peng hrang hrangte hian oxygen an dawng tlem hle. Damdawi lamah chuan he dinhmun hi
hypoxemia kan ti a.
Taksain oxygen a tlakchham rei chuan naute vun, hmui leh kut zungtangte hian rawng dum a nei a. Hei hi cyanosis , a nih loh leh ‘turning blue’ an ti a.
Hei hi hrethiam zawk tur chuan thinlung hrisel hnathawh dan hi han thlir ila.
Thinlung hrisel tak hnathawh dan
Kan thinlung hi pindan pali nei in ang mai niin han ngaihtuah teh. Chhawng chunglam (atria)-ah hian chamber pahnih a awm a, a hnuai lam (ventricles)-ah chuan chamber lian pahnih a awm bawk. Heng chamber inkarah hian kawngkhar ang maia valve a awm a. Thinlung dinglam leh veilam chu bang (septum) hmanga inthen a ni. 1.
Right side: Taksa oxygen tlachham, blue blood chu superior vena cava leh inferior vena cava kaltlangin right atrium ah a lut a. 2. Chuta tang chuan thisen chu valve (tricuspid valve) kal tlangin ventricle dinglam ah a lut a. 3. Ventricle dinglam atang hian he thisen dum hi valve dang (pulmonic valve) kaltlangin main vein (pulmonary artery) ah a pump lut a, chu chu lung lam pan a ni. 4.
Lung chhung: He thisen hi oxygen thar a ni a, thisen sen thianghlim a lo ni ta a ni. 5.
Left side: He oxygen tamna thisen sen hi thinlung veilam atrium-ah a kir leh thin. 6. Chuta tang chuan valve (mitral valve) kal tlangin veilam ventricle ah a lut a. 7. A tawp berah chuan he veilam ventricle atanga thisen sen thianghlim tak hi taksa thisen kalna lian ber (aorta) kaltlangin taksa pum puiah pump chhuah a ni. Hei hi kan taksa peng hrang hrangte hian dam khawchhuahna atana an mamawh oxygen an hmuh dan a ni.
Tetralogy of Fallot-a chhiatna pali lo awmte (The "Tetralogy") .
Tetralogy of Fallot vei naute thinlungah hian kan sawi tawh angin thil kalphung pangngai tidanglamtu chhiatna lian tak pali a awm a.
| Lung lam chhiatna | A awlsam zawngin... |
|---|
| Ventricular Septal Defect (VSD) a awm a, a chhuahna tur hmun leh a hmanna tur a awm lo. | Thinlung hnuai lam (chamber) pahnih inkar bang (septum) chhunga khur awm. Hei hian dinglam a oxygen hniam nei blue blood chu veilam a oxygen tamna red blood nen a inhmeh tir thei a ni. |
| Pulmonary Stenosis (PS) natna a awm thei. | Pulmonic valve emaw, lung chhunga thisen phurtu pulmonary artery emaw a tawi. Hei hian lung chhunga thisen kal zat a ti tlem a ni. Blueness degree hi he narrowing zau zawng hian a hril fo thin. |
| Aorta chungah a awm | Taksa pum puia thisen phurtu main artery (aorta) chu ventricle pahnih inkarah a awm a, a pangngai angin left ventricle chauh ni lovin. Chuvangin VSD hole kaltlanga thisen inzawm chu he artery-ah hian direct-in a lut a, taksaah a kal a ni. |
| Ventricular dinglam (Ventricular Hypertrophy) a awm a | Lung lam panna kawng chu a tawi (Pulmonary Stenosis) avangin thisen pump turin right ventricle hian nasa zawkin hna a thawk a ngai a ni. Exercise i tih hian muscle tissue a lian ang bawkin hei hian right ventricle wall a ti thim a ni. |
Eng thilin nge he dinhmun hi a thlen?
Hei hi a chhan dik tak erawh hriat a la ni lo. Nausen pum chhunga naute lo thanglian chhoh tirh lamah thinlung peng hrang hrang an lo insiam laia lo awm thin defect a ni. I sualna a ni lo va, naupai laia i thil tih pawh a ni lo. Chuvangin chutiang thil chu inthiam lo takin inhria suh.
I naute pawhin heng symptoms te hi a nei ve em?
Tetralogy of Fallot vei naupang
tam zawk chuan an dam kum khatnaah symptom an nei thin.
- A rilru a buai em em a, a rilru a hah em em bawk a. 1. Blueness (Cyanosis):Hei hi a symptom ber a ni. Naute hmui, lei, vun leh nail te hian bluish emaw purplish emaw rawng an nei a.
- "Tet Spells / Hypercyanosis": Hei hi thil pawimawh tak a ni. Nausen a tap a, bawnghnute a in a, inthiarna kal a tum emaw, zing a harh emaw hian rang takin rawng dum thuk tak an lo chang thei a, thawk harsa an ti a, an rilru a hah hle thei bawk. A châng chuan hriatna pawh an hloh thei bawk. Hetiang dinhmun hi minute tlemte atanga darkar engemaw zat thleng a awm thei.
- Thâwk harsa : Naute chu rang takin a chau a, a tlan kual a, a inkhelh hnuah a muhil ta a ni.
- Squatting: Naupang tê tê chu inkhelh avanga a chau chuan an khup chu an rilru thlenga hrual chungin an thu nghal mai ang (squatting). Hei hian hriat lohvin an lungah thisen kal a tipung a, thawk pawh a ti awlsam hle .
- Growth failure: Naute rihna sang , thanlen leh thanlenna chu naupang dangte aiin a slow zawk thei.
Engtikah nge damdawi lam thurawn i lak ang?
I naute thla tin clinic neih thin kha lo tlawh ve suh. Doctor chuan i naute a enfiah hian heng dinhmunte hi a hmu thei a ni.
A hnuaia symptoms te hi i neih chuan doctor pan nghal tur a ni.- Naute vun leh hmui a rawn sen chuan.
- Thâwk harsa i neih chuan .
- Nau hnute i pek lai emaw, i tap lai emaw i chau a nih chuan.
- I thanlenna a tlahniam nia i hriat chuan.
A hnuaia emergency a awm chuan damdawi in hnai ber Emergency Department (ETU)-ah hruai nghal tur a ni:- Tet Spell a ni
- Thâwk lak a har hle mai.
- Seizures a awm thin
- Fainting a ni
- Chauh lutuk emaw, chak lohna emaw
Engtin nge natna hi hriat chhuah a nih? (Test leh Diagnosis) 1.1.
I doctor chuan naute chu a enfiah ang a, thinlung thawk a ngaithla ang a, rinhlelhna a awm chuan test eng emaw zat nei turin a refer ang che.
- Chest X-ray: Hei hian thinlung pianzia a en a. Tetralogy of Fallot-ah chuan thinlung hi "boot-shaped" angin a lang thei a, a chhan chu right ventricle a lian vang a ni.
- Electrocardiogram ( ECG ): Thinlung electric hnathawh dan tehna, natna nei lo test a ni.
- Echocardiogram (Echo) tih a ni a: 1.1.Hei hi test pawimawh leh dik ber a ni. Scan ang mai a ni. Thinlung chhunga thil awm zawng zawng chiang takin a hmu thei a, chu chu chamber, valve, hole ( VSD ), leh narrowing (PS) te hi a ni.
- Cardiac Catheterization: A then phei chuan he test hi operation hmain heart pressure leh oxygen level tehna atan tih a ni a, thisen kalna kawng (veins) awm dan pawh ngun taka enfiah a ni bawk. He test-ah hian tube te tak te chu groin chhunga vein pakhat kaltlangin thinlungah an kal a.
Enkawlnate chu engte nge ni?
Tetralogy of Fallot enkawlna awmchhun chu
surgery a ni .
"Tet Spell" i hmuh chuan engtin nge i tih ang?
I naute chu a rawn sen nghal vat a nih chuan, i rilru a
hahdam a pawimawh hle . 1. Naute chu a hnungzang chungah dah la,
khup chu a rilruah (knee-to-chest position) . 2. Naute chu damdawi inah hruai nghal rawh. Hospital-ah chuan naute chu oxygen leh "tet spells" control nan propranolol ang chi damdawi pek a ni ang.
Inzai
Surgery hun tur hi naute symptoms nasat danah a innghat a ni. Surgery hi kum hnih hmasa berah tih a ni tlangpui.
- Palliative Surgery (Blalock-Taussig shunt): Naute thenkhat chu an te hle emaw, an chak lo hle emaw a, surgery kimchang an tuar thei lo mai thei. Chutiang hunah chuan taksaa thisen kalna kawng leh lung chhunga thisen kalna (artery) inkarah hian tube ang maia te tak te inzawmkhawmna siam a ni a, chu chuan lung chhunga thisen kal zat a tipung a ni. Hei hian naute chu tlem a lianin a chak zawk theih nan a pui thei a ni.
- Total Corrective Surgery: Hetah hian thinlung chhunga khur (VSD) chu patch hmangin an khar a, chu chu lung (PS) panna kawng zau tak chu a zau zawk a ni. He operation hnu hian thinlunga thisen kal dan chu a pangngaiin a awm leh thin.
Tunlai damdawi lam thiamna a lo thang chho zel a, he surgery hi a hlawhtling hle a ni.
Operation hnuah...
Surgery hlawhtling tak an neih hnuah naupang tam zawk chuan symptom leh limitation nei lovin nun pangngaiin an hmang thei a ni. Sikul an kal thei a, an inkhel thei a, nakin lawkah hna an thawk thei a, nupui pasal an nei thei bawk. Mahse, operation an neih hnuah pawh an dam chhung zawngin
doctor nen enkawl zui reng a pawimawh hle. A chang chuan heart rhythm inthlak danglamna (arrhythmias) a awm thei a, chuvangin check-up neih fo a pawimawh.
Take-Home Thuchah a ni
- Tetralogy of Fallot hi pianpui heart defect pali inzawmkhawm a ni. Hei hi i sualna a ni lo.
- A lan chhuah dan ber chu naute a rawn sen (cyanosis) a ni a, a bik takin tap emaw, a rilru hah emaw hian a na zual thei.
- Naute chu a rawn sen nghal vat (Tet Spell) chuan hlauthawng suh, khup chu a rilruah hruai la, damdawi inah hruai nghal rawh.
- He natna hi Echocardiogram hmangin awlsam takin hriat theih a ni.
- Surgery hi a enkawlna nghet tak a ni. Tunah chuan heng surgery te hi an hlawhtling hle a ni.
- Surgery hnuah naupang chu nun pangngai, hrisel takin a nung thei a, mahse damdawi lam thurawn zawm a, dam chhung zawng test neih a pawimawh hle.
tetralogy of fallot, thinlung natna, naupang enkawlna, blue baby, cyanosis, tet spells, piansualna, pianpui thinlung natna, thinlunga khur, VSD
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