Nangmah emaw, i hriat miin emaw cystic fibrosis an neih chuan i doctor chuan he damdawi Tezacaftor an tih hi a lo pe tawh mai thei; Ivacaftor a ni. He damdawi brand name chu Symdeko a ni. Hei hi eng emaw chen chu specialized, tunlai damdawi a nih avangin a chungchang chiang taka hriat leh hman dik a pawimawh hle. Chuvangin vawiinah hian he damdawi chungchang te, a hnathawh dan te, ei dan tur te, fimkhur tur zawng zawng te hi han sawi mai ila.
Tezacaftor chu eng nge ni; Ivacaftor a ni em?
A awlsam zawngin sawi ila, hei hi natna Cystic Fibrosis (CF) tih enkawlna atana hman thin pill a ni. Mahse, CF vei zawng zawng tan pek a ni lo. He damdawi hian an genes-a mutations engemaw zat nei tan chauh a thawk a ni. I doctor chuan he damdawi hi i tan a tha em tih hriat nan a tul angin test a ti ang. CF vanga i taksaa protein awmte chungchanga harsatna awm chu siamthat nan a pui thin. I doctor pawhin chhan dang vangin a pe thei bawk. Chuvangin zawhna i neih chuan doctor zawt la.
He damdawi hi i ei tan hmaa i doctor hnena i hrilh tur thilte
I doctor-in he damdawi a pek hma hian i hriselna chanchin kimchang a hriat a ngai dawn a ni. Chuvangin, a hnuaia dinhmunte hi i neih chuan i doctor hnenah hrilh ngei ang che .
- Kidney natna i neih chuan.
- Liver natna i neih chuan.
- Tun hmaa thil tel Tezacaftor, Ivacaftor emaw, damdawi dang, ei tur emaw, preservative dang emaw avanga allergy danglam tak i neih tawh chuan.
- Naupai i nih chuan, emaw naupai thuai i beisei a nih chuan.
- Nu hnute pe lai i nih chuan.
He thu hi thup lova doctor hnena hrilh hi nangmah himna atan a pawimawh hle.
Engtin chiah nge he damdawi hi ka hman ang?
He damdawi hi a hlawk ber tur chuan a pek ang chiah chiah i ei a ngai a ni.
- Chaw thau nen ei: He damdawi hi chaw thau nen ei fo tur a ni . Entirnan, artui, cheese, peanut butter, avocado, etc. te hian taksain damdawi a hip tha zawk ang.
- Tablet chu a pumin ei rawh: Tablet chu tichhia suh, tikehsawm suh, ei suh . Tui glass khat nen a pumin ei rawh.
- Grapefruit Juice nen ei loh tur: Hei hi a pawimawh hle. He damdawi hi i ei lai hian grape emaw grapefruit tui emaw ei leh in loh vek tur a ni .Damdawi thatna a tibuai thei a ni.
- A hun takah ei rawh: I damdawi chu i doctor-in a pek hunah, hun remchang takah ei rawh. Ni khatah vawi khat a nih chuan nitin hun khata ei tum ang che.
- Doctor thurawn tel lova i damdawi ei kha bansan suh: Doctor zawt hmasa lovin i damdawi ei kha titawp suh, i rilru a hahdam vang emaw, chhan dang vang emaw pawh nise.
He damdawi hi naupangte hnena i pek chuan...
He damdawi hi a chang chuan naupang kum 6 chunglam tan a tha hle. Mahse, hei hi i pediatrician-in thutlukna a siam tur a ni. A thupekte chu dik takin zawm rawh.
Damdawi i ei tam lutuk (overdose) a nih chuan engtin nge i tih ang?
Overdose i ei nia i rinhlelh chuan hlauthawng suh la, Colombo National Hospital-a National Poisons Information Center chu call nghal rawh. A nih loh leh, a theih chuan , a rang thei ang bera damdawi in hnai ber Emergency Treatment Unit (ETU)-ah kal rawh .
Damdawi dose khat ka ei loh chuan engtin nge ni ang?
Dose i ei theihnghilh chuan i hriatreng veleh ei nghal rawh. Mahse i dose leh tur thleng darkar 6 aia rei lo a nih chuan missed dose kha skip rawh. Dose dang chu a hun ruatah ei mai rawh. Dose theihnghilh tawh chu siam that nan vawi khatah vawi hnih ei ngai suh.
He damdawi nena inzawm thei damdawi dang (Drug Interactions) .
He damdawi hian damdawi dang thenkhat nen a inzawm thei bawk. Chuvangin, i damdawi ei zawng zawng (vitamin, herbal damdawi, leh supplement te pawh tiamin) i doctor hnenah hrilh hmasak a pawimawh hle. A hnuaia table hian hei hi a sawifiah belh leh a ni.
| Ruihhlo chi hrang hrang | Thuziak / Entirna |
|---|---|
| Hengte hi ei khawm vek loh tur. | |
| Damdawi thenkhat fit atan pek thin | Carbamazepine, Phenobarbital, Phenytoin te a awm bawk |
| Tuberculosis natna damdawi | Rifampin, Rifabutin tih a ni |
| Herb pakhat a ni | Mithianghlim Johana Wort |
| A in tur a ni | Grapefruit tui tak a ni |
| Chungte chuan buaina a thlen thei bawk (damdawi lam thurawn hnuaiah chauh hman) . | |
| Antibiotics thenkhat | A rilru a buai em em a, a rilru a hah em em bawk a |
| Antifungals a ni | Fluconazole, Itraconazole, Ketoconazole, Posaconazole, Voriconazole te a ni |
| Transplant hnua damdawi pek thin | Cyclosporine, Everolimus, Sirolimus, Tacrolimus te a awm bawk |
| Lung natna damdawi a ni | Digoxin a ni |
Damdawi ei laiin side effect awm thei
Damdawi dang ang bawkin he damdawi hian mi thenkhatah side effect a nei thei a ni. Ṭhenkhat chu a serious a, a then chu a common.
| Side effect chi hrang hrang | Natna |
|---|---|
| Side effect na tak tak, doctor hnena hriattir nghal tur | |
| Allergic Reaction awm thei te | Vun vun rawng, hnim hring, hmai, hmui emaw lei emaw a hring, thawk harsa. |
| Vision a danglam thin | Mit hmuh fiah lo, mit var (cataracts) inthlak danglam. |
| Liver Injury natna lan chhuah dan | Zun dum dum emaw, sen emaw, mit emaw vun sen (jaundice), ei duh lohna, luak chhuak, pum dinglam chunglam na, bawlhhlawh sen hring, hahna danglam tak. |
| Common side effects te chu a awm reng chuan doctor hnenah hriattir tur a ni | |
| Lu na | Lu na tlangpui. |
| Luak chhuak thei | Lung a na hle tih a hriat. Driving kha pumpelh rawh. |
| Luhai | Luak chhuak ang maia hriatna. |
| Sinus lama harsatna a awm | Hnar hrual, mucus. |
He list-a tarlan loh symptom dang danglam tak i neih chuan i doctor hnenah pawh hrilh bawk ang che.
Take-Home Thuchah a ni
- Tezacaftor-a chuan; Ivacaftor (Symdeko) hi Cystic Fibrosis natna vei genetic condition thenkhat tan damdawi bik a ni.
- He damdawi hi chaw thau tak nen ei fo tur a ni .
- He damdawi hi i ei lai hian grapefruit tui in vek loh tur a ni.
- Damdawi dang i ei zawng zawng chu i doctor hnenah hrilh rawh.
- Liver chhiatna chhinchhiahna i hmuh chuan, mit hmuhna danglam emaw, vun sen emaw , doctor thurawn zawng nghal rawh.
- He damdawi hi i tan chauh a ni. Midang hnenah share ngai suh.
- I doctor hnenah harsatna i neih chuan zawt hreh suh.











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