I lu a na nghal a, i rilru a na a, i mit a sen a, i muhil dawn ang maiin i inhria em? A chang chuan hei hi thinlung rhythm hlauhawm tak chhinchhiahna a ni thei bawk. Vawiin hian chutiang dinhmun hmuh tur awm lo mahse hlauhawm tak pakhat kan sawi dawn a ni. Torsades de Pointes (French tawng, "torsades de pointes" tia lam tur) tih a ni. A hming hi a mak deuhin a lang thei a, mahse a awmzia leh a tih theih dan hriat a pawimawh.
A awlsam zawngin Torsades de Pointes chu eng nge ni?
Hei hi heart rhythm chak tak, pangngai lo leh hlauhawm tak a ni a, i thinlung hnuai lam chamber pahnih (ventricles) atanga intan a ni. A dik tak chuan hei hi heart rate chak tak (Ventricular Tachycardia) chi khat bik a ni. A tlangpuiin mi hrisel chuan minute khatah 60 leh 100 inkar vel a ni. Mahse, hetiang dinhmun hi a lo awm chuan heart rate chu minute khatah beat 150 atanga 300 thlengin a sang thei a ni .
Hei hi a hlauhawm hle a ni , a chhan chu vaukhânna awm lovin cardiac death nghal mai theihna a awm a ni .
I EKG (electrocardiogram) i en chuan hetiang dinhmunah hian doctor-te hmuh thin pattern bik a awm a. Wave pattern a ni a, a hnung leh a inher chhuak a, coil ang mai a ni. French tawng "Torsades de Pointes" tih awmzia chu "point hrang hrang tihdanglam" tihna a ni. A hming hi EKG twisted nature atanga lak a ni.
Hetiang dinhmun hi thinlung electrical activity-a harsatna dang nen a lo awm tlangpui. QT interval rei tak an ti a. A awlsam zawngin sawi ila, QT interval hi i thinlung hnuai lam chamber vawi khat a beat a, a hnua a beat leh tur atana inbuatsaih hun a ni. He hun hi a tlangpuiin a rei (QT rei) a nih chuan extra beat a awm thei a, Torsades de Pointes a thlen thei a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
Heta thil hlauhawm tak chu he natna vei zinga a chanve chiah hian symptoms an nei lo . Symptoms nei ve thote chuan a hnuaia mi hi an tawng thei a ni. Hengte hi i fimkhur hle tur a ni.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Luak chhuak thei | Thinlung hian thisen a pump tha tawk lo a, chu chuan thluaka thisen a tihtlem phah a ni. |
| Palpitations a awm | I thinlung chu a na rang emaw, a thawk mumal lo emaw tih i hre tan thin. |
| Lung hring (lightheadedness) a awm | Ka hriatna hloh dawn ang maiin ka inhria. |
| Fainting a ni | Thluaka thisen kalna hun eng emaw chen a tihbuai vang a ni thei. |
| Lung natna (Cardiac arrest) a awm | Hei hi dinhmun hlauhawm tak a ni. Thinlung chu a reh nghal vat a. |
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Hei hi a chhan lian ber pahnih a awm a.
1. Congenital causes: Mi thenkhat chu pianpui atanga lo piang an ni a, `Long QT Syndrome` an tih. Chumi awmzia chu an chhungkuaah hetiang dinhmun hi an nei tihna a ni. Heng mite hi Torsades de Pointes vei theihna chance a sang zawk a ni.
2. A hnu lama a chhan: Hei hi a tam ber a ni. Damdawi thenkhat hman leh taksaa electrolyte level tlahniam hian `QT interval` hi a ti rei thei a ni. Hei hian Torsades de Pointes vei theihna a tipung a ni.
Damdawi hlauhawmna tipungtu:
- Heart rhythm control thei damdawi thenkhat (Antiarrhythmics) .
- Antibiotics thenkhat
- Luak chhuak damdawi thenkhat (Antimetics) .
- Antifungals a ni
- Antipsychotics hi rilru lam natna thenkhat enkawlna atana hman thin damdawi a ni.
- Cancer damdawi thenkhat
Pawimawh: Hetiang damdawi chi hrang hrang i ei a nih chuan hlauthawng suh. Hetiang dinhmun hi mi zawng zawngin an tawng vek dawn lo. Mahse hemi chungchang hi doctor nen inbiakna neih a pawimawh hle a, a hlauhawmna pawh hriat chian a pawimawh hle.
Hei hi eng risk factors nge awm?
Mi thenkhat chuan he natna hi an nei tam zawk. Heng risk factors te hi:
- `Long QT Syndrome` tih natna nei.
- Lung natna dang neih.
- Hmeichhia nih (hmeichhia hi an hlauhawm zawk) .
- Kum 65 chunglam a nih vang a ni.
- Thyroid a thawk tha lo.
- Stroke a vei tawh avangin.
- Diuretics hman dan.
- Lung natna (Bradycardia) a ti hniam.
- Taksaah hian calcium, magnesium, potassium a tlem.
- Luak chhuak lutuk emaw, luak chhuak emaw.
Risk hi tihziaawm theih a ni em?
Ni e, i ti thei ngei ang. Thil engemaw zat tih theih a awm a:
- I chhungkuaa mi pakhatin `Long QT Syndrome` a neih chuan i test ngei ngei tur a ni. I neih chuan exercise program i tan hmain cardiologist hmu hmasa phawt ang che.
- Damdawi i ei danah fimkhur rawh: `QT interval` ti rei thei damdawi i ei a nih chuan, chu ai chuan damdawi dang i ei theih leh theih loh zawt la. Damdawi thar i tan dawnin i doctor hnenah tuna i damdawi ei mek ah harsatna a thlen loh nan hrilh rawh.
- Ei leh in chungchang ngaihtuah rawh: I doctor-in a rawt chuan i calcium, magnesium leh potassium level tipung rawh.
- I damdawi ei tur chu a hun takah ei rawh: Hetiang natna hi a lo awm leh tawh loh nan i doctor-in a tih ang chiah khan damdawi hi hmang ang che.
- Tui in tam: Taksaah tui leh chi level dik tak vawng reng ang che.
- I heart rate hre rawh: Lungphung pangngai chu eng nge ni tih leh a teh dan tur zir rawh.
- Heart monitor pek i nih chuan: I doctor-in in lama bun tur heart monitor a pe che a nih chuan bun ngei ngei tur a ni.
Engtin nge diagnosis hi siam a nih?
Hei hi hriat theih dan ber chu `EKG` (Electrocardiogram) test hmanga enfiah a ni. Doctor-te chuan `EKG`-a `twisted` pattern danglam tak leh `QT interval` rei tak hmuh theih chu enin an hre thei a ni.
Tin, heng test te hi tih theih a ni bawk:
- Thisen test: Taksa chhunga electrolytes awm zat, magnesium leh potassium awm zat enfiah thin ang che.
- Echocardiogram: Thinlung insiam dan leh hnathawh dan enfiahna scan a ni.
- Heart Monitor: Ni eng emaw zat bun a, thinlung thawk dan enfiah chhunzawm zel tur hmanrua a ni.
Engtin nge enkawl a nih?
Enkawlna chu a natna chhan a zirin a ni. Congenital Long QT Syndrome vei chuan ruihhlo vanga natna vei aiin hun rei zawk enkawl a ngai dawn a ni.
| Enkawlna chi hrang hrang | Hrilhfiahna |
|---|---|
| Damdawi chi hrang hrang | |
| Buaina thlentu damdawi tihtawp | A hmasa ber chu doctor-in he thil thlentu nia a hriat damdawi chu a chawlhsan mai tur a ni. |
| Magnesium leh/ emaw potassium te a ni | Taksa chhunga heng salt level hi a hniam chuan a pangngaia a awm leh theih nan thisenah pek thin a ni. |
| Beta-blockers te pawh a awm | Heart rate control nan leh `Long QT Syndrome' nei te tan pek a ni. |
| Thiltih dan leh hmanraw dang (Procedures) . | |
| Pacemaker a ni | Heart rate hniam tak tak nei tan chuan a rhythm dik taka a awm theih nan device te tak te dah a ni. |
| ICD (Cardioverter Defibrillator dah theih) hmanga siam a ni. | Hei hi taksaa dah luh a ni bawk. Heart rhythm hlauhawm tak a hriat chuan electrical shock a pe nghal a, chu chuan heart chu a normal leh ta a ni. |
| Electric hmanga Cardioversion/Defibrillation hmanga tihdam theih a ni | Emergency-ah chuan heart rhythm pangngai siam leh turin rilruah electric shock thlen. |
Engtikah nge Doctor ka hmuh ang?
Pulse chak tak, rilru na, luak chhuak, mit sen, hriatna hloh ang chi symptoms i neih chuan damdawi in Emergency Department (ETU) ah kal nghal rawh. Hei hi emergency a ni.
Torsades de Pointes vangin damdawi inah i awm a ngai a nih chuan kar hnih hnuah follow-up nei turin i haw ngei ngei tur a ni. Hei hi thihna hlauhawm tak a nih avangin, cardiologist enkawlna hnuaia awm reng a pawimawh hle.
I doctor hnenah heng zawhnate hi i zawt thei ang:
- Long QT Syndrome nei ka piang nge, damdawi avanga lo awm?
- Ka chhungkaw mi dangte pawhin he natna hi a lo awm theihna chance engzat nge awm?
- Hetiang hlauhawmna thlentu ai hian damdawi dang ka ei theih a awm em?
Enkawlna hmang hian he natna hi control theih a ni a, nun tha tak i hmang thei bawk. Mahse, enkawl loh chuan thihna a thlen thei a ni. Chuvangin doctor thupek dik tak zawm a, ni ruat saah clinic-ah kal a pawimawh hle.
Take-Home Thuchah a ni
- Torsades de Pointes hi thinlung rhythm chak tak, nunna atana hlauhawm tak a ni.
- Hei hi genetic condition (`Long QT Syndrome`) vang emaw, damdawi thenkhat leh taksaa chi tlakchham vang emaw a ni thei.
- I rilru natna, luak chhuak, hriatna hloh emaw ang chi symptoms i neih chuan emergency a ni. ETU (Emergency Treatment Unit) ah kal nghal rawh.
- I damdawi ei kha titawp ngai suh la, i doctor thurawn tel lo chuan a dose pawh thlak ngai suh.
- Hetiang dinhmun hi hriatchhuah a nih chuan cardiologist hnuaia enkawl leh enkawl zui zel a pawimawh hle.











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