A châng chuan chhan awm lovin i chau leh chau lutuk tih i inhria em? Chaw ei chak lohna emaw , taksa rihna tlahniam emaw , luak chhuak emaw i nei em ? I vun, a bik takin i elbows leh knees , a rawn sen deuh tih pawh i hmu tawh mai thei. Heng thilte hi ngaihthah mai mai suh. I taksa chhunga thil pawimawh tak thleng chhinchhiahna an ni thei. Vawiin hian chutiang dinhmun pakhat, Addison’s Disease , kan sawi dawn a ni.
A awlsam zawngin Addison-a Natna hi eng nge ni?
Kan taksa hi company lian tak angin han ngaihtuah teh. He company hian “chemical messenger ” pawl a nei a, hna hrang hrangte chu a kal tluang taka kalpui theih nan thuchah an inthleng thin. Heng hormone te hi kan ti a .
Kan kal chungah hian lukhum te tak te pahnih ang maiin gland te tak te pahnih a awm a. Hengte hi adrenal glands kan tih te hi an ni . Heng gland te hian kan nun atana pawimawh hormone pawimawh pahnih an siam chhuak thin. Anni chu cortisol leh aldosterone te an ni .
Addison natna hi eng emaw chhan vanga adrenal glands te a chhiat avangin heng hormone mamawh zat an siam chhuak thei lo. Hei hi thil awm lo tak a ni. Mahse hei hi hriat chian a pawimawh hle.
Hormone pahnih hian eng hna nge an thawh?
- Cortisol: Hei hi kan taksa "stress manager" ang mai a ni. He hormone hian taksa chu natna, hlauhawm leh lungkhamna hmachhawn turin a buatsaih a ni. Thisen sang, thisen sugar level leh protein, carbohydrates leh thau hman dan tur a control bawk.
- Aldosterone: He hormone hi kan taksa "salt and water regulator" a ni. Kan kal (kidney) te hian taksaa chi (sodium) leh potassium level inthlauhna nei turin a pui thin. Kan thisen sang pawh a control bawk.
Heng hormone te hi a hniam chuan taksa pum hnathawh a tibuai a ni. Chutiang chu Addison natnaah chuan a thleng thin.
Addison natna lan chhuah dan chu engte nge ni?
Addison natna lanchhuahna chu zawi zawiin, zawi zawiin a lo lang chhuak thin. Chuvangin natna anga hriat theih nan a chang chuan hun rei tak a la ngai thei. Heng symptoms te hi natna tlanglawn dangte nen a inang a, chuvangin hriatthiam loh theih a ni.
I hmuh tur feature lian ber berte chu a hnuaia table hi en la.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Chronic fatigue leh muscle chak lohna | Nilengin chau leh nunna nei lo anga inhriatna, eng ang pawhin chawlh hahdam mah la. |
| Vun a rawn sen/a dum (Hyperpigmentation) . | Elbows, khup, knuckles, hmui, leh gums ang chi hmuna vun a dum. Scar hlui pawh a dum thei. |
| Chaw ei chakna hloh leh taksa rihna tlahniam | Chaw ei duh lohna leh a hnu lama taksa rihna tlahniam. |
| Thisen sang hniam (Hypotension) . | I luak chhuak a, a bik takin thut atanga i ding chuan thisen sang hniam vang pawh a ni thei. I hriatna pawh i hloh mai thei. |
| Chi ei duhna lutuk | Taksa chi (salt level) a tlahniam chuan chaw chi leh pickles ang chi ei duhna a awm reng a ni. |
| Thil dang pawh a awm | Hmeichhiaah chuan luak chhuak, luak chhuak, pum na, pum na, thisen sugar hniam (hypoglycemia), rilru hahdam lo, leh thlasik hun mumal lo. |
Addison natna hi engte nge ni?
Addison natna thlentu ber chu autoimmune natna a ni.A awlsam zawngin, hei hi kan taksa ngeia immune system-in a kal a, kan adrenal glands-te a rawn beih a, a tihchhiat hun a ni. Hei hi Addison-a damlo 70% awm chhan a ni.
Chu bâkah, chhan dang pawh a awm thei bawk.
- Infection: Hun rei tak infection tuberculosis leh HIV te hian adrenal glands a tichhe thei a ni.
- Cancer: Hmun danga cancer cell lo awm tawhte chu adrenal glands-ah an darh a.
- Internal bleeding: Adrenal glands chhunga thisen chhuak.
- Genetic causes: Genetic condition thenkhat avang hian he natna hi vei theihna a awm bawk.
- Surgery: Adrenal glands lakchhuahna tur surgery i neih tawh chuan.
Engtin nge hei hi i hmuh theih, Doctor?
Heng symptoms te hi i neih chuan a rang thei ang bera chhungkaw doctor pan thin ang che. A enfiah ang che a, a tul chuan specialist hnenah a refer ang che.
Thisen test eng emaw zat hi natna hriat chian nan hman a ni ber.
1. Basic blood test: Hei hian i thisen sodium (salt) level a hniam em tih emaw, i potassium level a sang em tih emaw a enfiah ang.
2. ACTH Stimulation Test: Hei hi test pawimawh ber a ni. Hemiah hian i thluak atanga chhuak hormone ACTH an tih tlem te te chu injection angin pek a ni. Mi hrisel takah chuan he injection hian adrenal glands-ah hormone cortisol tam tak a siam chhuak thin. Mahse, Addison natna veiah chuan glands te hian hetiang hian an chhang lo. Thisen sample lak a, he cortisol level hi teh a, natna hi finfiah a ni.
Chu bâkah, CT scan hmangin adrenal gland-a natna hrik, cancer, a nih loh leh thisen chhuak a awm leh awm loh enfiah theih a ni bawk.
A hlauhawm ber chu: Addisonian Crisis
Hei hi Addison natna hlauhawm ber leh rang ber a ni. Symptoms hi a lo lang zauh zauh thin a, chuvangin mi thenkhat chuan he natna hi an nei tih pawh an hre lo. Hetih lai hian taksain harsatna nasa tak a tawk a, natna dang emaw, zai emaw, accident emaw a nih chuan a natna lan chhuah dan chu a na hle thut thei a ni. Hei hi Addisonian crisis an ti a .
Hei hi medical emergency a ni a, enkawl loh chuan thihna a thlen thei a ni.
Addisonian crisis a lan chhuah dan:
- Hnung lam, pum emaw, ke emaw a na nghal vat a, nasa takin a na.
- Luak chhuak nasa tak leh riltam, chu chuan tui tlakchhamna a thlen thin.
- Thisen sang lutuk avanga shock awm.
- Thil hriatna hloh.
- Khawsik leh chak lohna nasa tak.
Heng symptoms te hi a lo lang a nih chuan, .Damlo chu damdawi in hnai ber Emergency Treatment Unit (ETU)-ah hruai nghal tur a ni.
Enkawlna leh nun pangngai
Addison natna chungchang hi i hriat chuan i hlau mai thei a, mahse thu lawmawm tak chu a enkawlna tha tak tak a awm tih hi a ni.
He natna hi taksaa hormone chi hnih bo vang a ni. Chuvangin enkawlna chu chu hormone te chu pawn lam atanga pill angin pek hi a ni.
- Hydrocortisone: Steroid pill a ni a, hormone cortisol thlaktu a ni.
- Fludrocortisone: Hormone aldosterone thlaktu pill a ni.
He damdawi hi nitin ei tur a ni a, doctor-in a pek ang chiah chiah a ni.
A pawimawh ber chu damdawi dose khat pawh skip ngai lo tur a ni. Dose khat pawh hloh chu a hlauhawm thei hle.
Infection i neih emaw, khawsik i neih emaw, operation i neih emaw chuan i doctor chuan Addisonian crisis i neih loh nan he damdawi hi rei lo te chhung atan a tipung ang.
Enkawlna dik tak a neih chuan Addison natna vei chu nun pangngai tak, hrisel takin a nung thei a ni .
Take-Home Thuchah a ni
- Addison natna hi adrenal glands-in hormone cortisol leh aldosterone a siam chhuah tlem vang a ni.
- A lan chhuah dan ber chu chau reng reng, taksa rihna tlahniam, thisen sang hniam leh vun a thim thin te hi a ni.
- Heng symptoms te hi i neih chuan hlauthawng suh la, doctor pan nghal rawh.
- Hei hi dam chhung zawnga dinhmun ni mahse, nitin damdawi ei hian nun pangngai tak i hmang thei a ni.
- Addison natna i vei chuan i dinhmun tarlanna card emaw bracelet emaw ha fo ang che. Emergency-ah chuan nunna chhanhimtu a ni thei.
- Addisonian crisis hi emergency a ni a, enkawl vat a ngai a ni. A lan chhuah dan hriat a pawimawh.
Addison’s Disease, hormone, adrenal glands, cortisol, aldosterone, hah reng, vun dum, adrenal glands, adrenal insufficiency, thisen sang hniam











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