I naute piang thar hian a pian hnu ni hnih emaw ni thum emaw chhung chu a poop lo em ni? A nih loh leh an pum chu a hring mai a, khawih a harsa mai em ni? Nu thar emaw, pa thar emaw chuan hetiang thil an hmuh hian tlem a hlauhthawn hi thil pangngai tak a ni. A tam zawkah chuan hengte hi thil pawi tak a ni lo. Mahse, a tlem berah chuan heng symptoms te hi Hirschsprung’s Disease , tunlaia kan sawi mek natna avanga lo awm thei a ni. Chuvangin, hlau lovin he thu hi chipchiar takin sawi ila.
A awlsam zawngin, Hirschsprung natna hi eng nge ni?
Hirschsprung’s Disease hi a awm lo hle a, pianpui atanga lo piang a ni a, naute chu a colon hmun hnuhnung bera nerve cells awm lovin a piang a , chu chuan stool chhuah tir turin a pui a ni.
Kan intestine hi tube angin han ngaihtuah teh. Kan ei tur chu a hmin a, bawlhhlawh, bawlhhlawh an tih chu he tube hnuaiah hian a kal thla thin. He zinkawng hi intestine wall-a nerve cells te hian an pui thin. Heng cell te hian intestines chhunga muscle te hnenah signal an thawn a, chu chuan a ti contract a, a ti relax a, feces chu hmalam pan turin a nawr a ni.
Hirschsprung natna vei naute hian a intestine lian tawp lamah heng nerve cells te hi a nei lo. Chuvangin, stool a rawn luh chuan a kal tlang thei lo va, a tang ta a ni. Car traffic-a a tlakbuak ang maiin. Hei hian bawlhhlawh a tipung a, intestine-ah blockage lian tak a siam a ni. Hei hian naute chu chaw ei kham nasa tak, intestinal obstruction, leh a châng chuan natna hlauhawm tak tak a thlen thei a ni .
A tlangpuiin naute hrisel chuan a pian tirh atanga darkar 24-48 chhungin an ril a chhuah hmasak ber thin. He bawlhhlawh hmasa ber hi ‘meconium’ an ti a. A tlangpuiin thil dum, thuk tak a ni. Amaherawhchu Hirschsprung natna vei nausen chuan he riltam chi hi a nei thei lo.
Hetiang dinhmun a lo awm chhan bik chu eng nge ni?
Doctor-te chuan naute ṭhenkhatin he natna hi an vei chhan chiang takin an la hre lo a, mahse mi tam tak chuan genes nena inzawm niin an ngai a ni .
A awlsam zawngin, nausen pum chhunga a lo seilian tirh kar tlemte chhung hian naute chaw ei kawng zawng zawngah, ka atanga a hnute thlengin, nerve cells te chu a lo thang lian thin. Mahse Hirschsprung natna vei nauteah chuan he nerve cell thanna hi a intestine lian tawp lamah a tawp nghal a ni.
Hei hi kan taksa DNA-a inthlak danglamna (mutations) thenkhat vang pawh a ni thei a, chu chu instruction book ang mai a ni. A châng chuan heng genetic changes te hi nu leh pa atanga fate rochun theih a ni. Tin, naupang pianpui natna dang, Down syndrome, leh thinlung natna thenkhat nei te chu Hirschsprung natna vei theihna chance a sang deuh hlek bawk.
Engtin nge heng symptoms te hi kan hriat theih?
A tam zawkah chuan heng symptoms te hi dam chhung kar 6 chhungin a lang a, a bik takin darkar 48 hmasa berah a lang thin. Mahse, naupang thenkhatah chuan natna lan chhuah nan kum engemaw zat a la ngai thei.
A hnuaia mizia te hi i hriat chian a ngai a ni.
| Mihring ziarang | Hrilhfiahna |
|---|---|
| Efecate lo | Nausen piang thar chhinchhiahna ber pakhat chu nau piang atanga darkar 48 hnuah pawh ril a nei lo tih hi a ni. Naute hi tlem a upa zawk a nih chuan chronic constipation an nei thei a, chu chu rei tak a daih a, damdawi ei pawh a chhang lo thei bawk. |
| Pum a hring chhuak | Naute pum chu a pum chhunga ek leh boruak a tang avangin a hring leh a khauh angin a lang thei. |
| Luak chhuak | Naute chu a luak chhuak thei. A chang chuan he vomit hi green emaw brown emaw angin a lang thei. Hei hian intestines-a blockage vangin bile a rawn sang tihna a ni thei. |
| Thisen chhuak riltam | Hei hi symptom hlauhawm tak a ni . Nunna atana hlauhawm intestinal infection enterocolitis tih a lo awm tih a tilang a ni. Khawsik, riltam na tak, pum na te pawh a awm thei bawk. |
| Stunted growth a ni | Naupang chu a upa deuh tawh a, natna a vei tih hmuhchhuah a nih loh chuan chaw ei tam leh ei leh in tha lo chuan a than chak lo thei a, a chau reng bawk. |
A pawimawh ber chu i naute hian heng symptoms te hi a neih chuan, a bik takin naute piang thar hian pooping a nei lo a nih chuan ngaihthah suh. I naute hi doctor hnena hruai nghal a pawimawh.
Engtin nge doctor hian he natna hi dik taka a hriat theih ang?
I fa chu doctor hnena i hruai chuan i fa chu a enfiah ang a, i natna lan chhuah dan a zawt ang che a, chutah chuan a natna hriat chian nan test eng emaw zat neih a rawt ang.
- Abdominal X-ray: Hei hi bowel obstruction emaw bloat emaw enfiah nan hman theih a ni .
- Contrast Enema: Hetah hian naute rectum chhungah tui dum bik (dye an tih chu barium an tih) an kalpui a, X-ray thlalak hrang hrang an la thin. He tui hian intestine chhung lam chu chiang takin a hmu thei a ni. Nerve cell nei lo chu a hring tlangpuiin a lang a, a chunga stool-a khat chu a lian zawkin a hring zawkin a lang thung. Hei hian natna chungchang ngaihtuahna tha tak a pe thei a ni.
- Rectal Biopsy: Hei hi 100% a natna finfiahna test a ni. Hemiah hian doctor chuan naupang rectum chhung lam bang atanga tissue te tak te (tissue sample) a la a, microscope hmangin a enfiah thin. Chu tissue piece-ah chuan nerve cell a awm leh awm loh en chuan natna chu dik takin a hriat theih a ni.
- Anorectal Manometry: He test hi naupang kum upa zawkte tih thin a ni tlangpui. Balloon ang chi thil te tak te chu rectum chhungah dahin, chu chu inflate-in, rectum chhunga muscle te chu a thawk tha em tih enfiah a ni.
Hei hi eng enkawlna nge ni?
Hirschsprung’s Disease hi damdawi hmanga tihdam theih a ni lo. A enkawlna awmchhun leh nghet ber chu operation a ni . Ngaihtuah buai suh, tunah hian he surgery hi hlawhtling takin an ti mek a ni.
Surgery neih chhung hian doctor chuan colon chhunga nerve cell awm lohna hmun chu a la chhuak a, colon hrisel tak, nerve khata khat chu rectum nen direct-in a thlunzawm a ni. He surgery hi "pull-through procedure" an ti a.
A châng chuan naupang dinhmun a zirin he main surgery hma hian hun eng emaw chen atan "ostomy" surgery neih a ni thei bawk. Hei hian intestine hrisel tak thenkhat chu pum vun chung lamah a lo kal theih nan opening (stoma) siam a huam a ni. Tichuan, he opening-ah hian ostomy bag an dah a, chu chuan stool an la khawm thin. Naupang chu a dam tlem a, main surgery atan a inpeih tawh chuan he opening hi khar a ni a, pull-through surgery tih a ni.
Operation hnuah eng complication nge awm thei?
Naupang tam zawk chuan operation hnuah an rilru a na thei a, nun hrisel tak an hmang zui thei bawk. Mahse, naupang thenkhat chuan operation an neih hnuah pawh harsatna engemaw zat an la nei thei tho. Hei hi hriat chian a pawimawh hle.
Hirschsprung nena inzawm enterocolitis a awm
Hei hi complication hlauhawm ber a ni . Operation hma emaw, operation hnuah emaw a awm thei. Intestines natna na tak a ni.
I fain operation hnua symptoms a neih chuan khawsik, pum na, luak chhuak, luak chhuak na tak, ek chhunga thisen chhuak te hi emergency a ni. I fa chu damdawi in Emergency Department (ETU) ah hruai nghal rawh.
Fecal incontinence a awm thei
Naupang thenkhat chuan operation an neih hnuah an riltam control harsa an ti thei. Chumi awmzia chu an hriat loh pawhin stool an pass mai thei tihna a ni. Hei hi surgery-in rectum ruh a nghawng vang a ni thei. Hun leh exercise thenkhat (pelvic physical therapy) hmang hian he natna hi nasa takin control theih a ni.
Constipation leh blockage te a awm
Naupang thenkhat chuan operation hnuah constipation an nei thei. Hei hi surgery hmun a tawi vang emaw, thil dang vang emaw pawh a ni thei. Chutiang hunah chuan i doctor chuan a tul angin a enkawl ang.
Hetiang dinhmun hi surgery hmanga enkawl ni mah se, naupang dinhmun enfiah chhunzawm zel a pawimawh. I fate ril leh ei leh in chungchang doctor nen inbia fo ang che.
Take-Home Thuchah a ni
- Hirschsprung’s Disease hi piansualna hmuh tur awm lo tak a ni a, intestine-a nerve cell awm loh avangin ek chhuah theih lohna a thlen thin.
- Nausen piang tharin darkar 48 chhunga a ril a chhuah loh, a pum a hring, leh green/brown vomit a lan chhuah dan ber chu: Hengte hi i hmuh chuan doctor pan nghal tur a ni.
- He natna hi biopsy hmanga finfiah a ni.
- Enkawlna chu surgery a ni. Hlawhtling taka zai hnuah naupang tam zawk chuan nun pangngai an hmang thei a ni.
- Operation hnua khawsik, pum na, thisen chhuak riltam ang chi symptoms i neih chuan damdawi in Emergency Department (ETU)-ah i kal nghal tur a ni a, hei hi enterocolitis an tih natna hlauhawm tak chhinchhiahna a nih theih avangin.
- Hei hi dam chhung zawnga enkawl ngai dinhmun a ni. Chuvang chuan Doctor thupek zawm a, i fa chu hunbi neia enfiah tir a pawimawh hle.
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