Kua whakaaro kē koe mō te mate pukupuku korokoro ? Tērā pea kua whakaaro kē koe. I tēnei rā ka kōrero tātou mō tētahi momo mate pukupuku e puta ana i roto i te korokoro, engari he iti ake te kōrero. Ko te ingoa o tēnei ko te Mate Pukupuku Hypopharyngeal. He māmā noa iho, ka puta i te wāhanga o raro o tō tātou korokoro, arā, i te wāhanga o raro o te korokoro (`(Pharynx)`), i muri tonu i te pouaka reo (`(Larynx)`). Me titiro tātou ki tēnei me ētahi atu taipitopito, e tika ana?
He pēhea te noa o tēnei mate pukupuku?
Ina hoki, ehara tēnei mate pukupuku hypopharyngeal i te mea noa. Whakaarohia, ahakoa i roto i tētahi whenua pēnei i a Amerika, e 2000 ki te 4000 noa iho ngā tāngata e kitea ana tēnei mate i ia tau. Engari ki te whakatauritea ki tētahi mea pēnei i te mate pukupuku pūkahukahu , he tino iti taua tau. Hei tauira, i te tau 2023 anake, e kiia ana neke atu i te rua rau mano ngā tāngata i kitea he mate pukupuku pūkahukahu i Amerika. Nō reira, ko te tikanga he onge tēnei, arā, kāore e kitea pinepinetia.
He aha ngā tohu o te mate pukupuku hypopharyngeal?
Ko tētahi raruraru i konei, kāore pea tēnei mate pukupuku e whakaatu i ngā tohu i ngā wāhanga tōmua . I ētahi wā, kua horapa te mate pukupuku (kua horapa) i te wā e puta mai ai ngā tohu. Heoi, ko ngā tohu e puta mai ana ko:
- He korokoro mamae , he āhua rānei kei te mau tetahi mea i roto i te korokoro.
- Te reo pāorooro .
- Te uaua ki te horomi i te kai .
- Te mamae o te taringa .
- Ngā kōpuku lymph pupuhi i te kaki .
- Te poto o te manawa , te mea rānei e mau ana i roto i te korokoro, kāore he take e kitea ana.
- Te tino ngenge (‘ Fatigue’ ).
- Ngā huringa reo .
- Te uaua ki te manawa , te haruru rānei i te wā e manawa ana (`(Stridor)`).
- Te maremare toto .
- Te hiroki noa iho , kāore he take.
Ko te mea nui, kaua e wehi kei pāngia koe e tēnei mate pukupuku nā te mea kei a koe ēnei tohu. Nā te mea ka kitea anō hoki ēnei tohu i roto i ētahi atu mate iti. Heoi, ki te roa atu i te rua wiki te roa o tētahi o ēnei tohu, he mea whakaaro nui kia toro atu ki te tākuta me te rapu tohutohu.
He aha te take e whanake ai te mate pukupuku hypopharyngeal?
Ki te kī ngāwari, ka puta tēnei mate pukupuku i roto i ngā pūtau e whakarārangi ana i tō hypopharynx (te wāhanga o tō korokoro e whakarārangi ana i tō korokoro). Ka huri ēnei pūtau, ka noho hei mate pukupuku, ka wehea, ka hanga he pukupuku. Kāore e taea e ngā tohunga te kī tika he aha tēnei e puta ai. Heoi, kei reira ētahi āhuatanga mōrearea e whakanui ake ana i tō tupono ki te whakawhanake i tēnei mate pukupuku. Ko ēnei:
- Te kai hikareti: Koinei te tino take mōrearea mō te mate pukupuku korokoro, tae atu ki te mate pukupuku hypopharyngeal. Kei roto i tēnei ko ngā hikareti, ngā hikā, te kai paipa, te whakamahi hikareti hiko (`(hikareti hiko)`), te tupeka ngaungau, te kapia ngaungau, me te tupeka ngaungau.
- Te inu nui me te inu auau: Ko te inu nui me te inu auau ko te inu i te neke atu i te rua wae waipiro ia rā mō ngā tāne, ā, neke atu i te kotahi wae waipiro ia rā mō ngā wāhine.
- Mate HPV: He mate tuku iho (STI) te Human Papillomavirus (HPV). Ka taea te horapa mā te moe ā-waha ki tētahi kua pangia e te huaketo.
He aha ngā raruraru ka puta mai i tēnei āhuatanga?
Ka taea e te mate pukupuku hypopharyngeal te horapa ki ngā kōpū lymph i te kaki i ōna wāhanga tōmua. Koia te mea nui kia kōrero koe ki te tākuta mēnā ka kite koe i tētahi puku i tō kaki. Ki te kore e rongoatia, ka taea e tēnei mate pukupuku te horapa ki ngā wāhi e whai ake nei:
- Tō korokoro (`(Esophagus)`).
- Ētahi atu wāhanga o te korokoro.
- Te repe tairoiti (`(Tairoiti)`).
- Te pūhā (te pūhā o te korokoro).
- Wheua Hyoid (`(Wheua Hyoid)`).
- Te arai o te kōhao o te uma.
- Te kiko e karapoti ana i te taha whakarunga o te tuaiwi.
- Te uaua carotid (`(Te uaua carotid)`).
Me pēhea te tautuhi i tēnei mate pukupuku?
Ina kite koe i tētahi tākuta, ka pātai atu ia ki a koe mō ō tohumate, te roa o te wā e pāngia ana koe e ēnei tohumate, me te mea kei te kai tupeka koe, kei te inu waipiro rānei, nā te mea ka piki ake te tūponotanga o te pāngia e tēnei mate pukupuku.
Kātahi ka tirohia koe e te tākuta. Ka pāngia tō kaki e ia kia kite ai mēnā kei te pupuhi ō pona lymph, ā, ka tirohia anō hoki tō korokoro.
I runga i ō tohumate, ka tukuna pea koe e tō tākuta ki tētahi tohunga taringa, ihu, me te korokoro (he tohunga ENT, he tohunga Otolaryngologist rānei). He tohunga ia ki te tātaritanga me te rongoā i ngā mate o te mahunga me te kaki. Ka taea e ia te tono whakamātautau pēnei i:
- Endoscopy: I tēnei whakamātautau, ka whakaurua e te tākuta he ngongo roa, angiangi (endoscope) ki roto i tō korokoro hei tirotiro i te wāhanga o raro o tō korokoro. Tērā pea ka mahia he whakamātautau e kīia nei ko te laryngoscopy hei tirotiro i te pouaka reo (larynx).
- Whakamātautau koiora (`(Biopsy)`):Tērā pea ka tonoa e te tākuta he wero ngira pai (FNA) hei tango i tētahi tauira kiko. Kātahi ka tirohia tēnei tauira kiko i raro i te karuārai e te tohunga mate pukupuku hei tirotiro mō ngā pūtau matepukupuku.
- Ngā whakamātautau whakaahua: Mena ka whakaūtia e te koiora he mate pukupuku hypopharyngeal tōu, ka tukuna koe e tō tohunga ENT ki tētahi tohunga pukupuku. Tērā pea ka tonoa e ia he whakamātautau whakaahua hei tirotiro mēnā kua horapa te mate pukupuku mai i te pito o raro o te korokoro ki ētahi atu wāhanga o te tinana. Tērā pea kei roto i ēnei he matawai CT (Computed Tomography), he matawai MRI (Magnetic Resonance Imaging), he matawai PET rānei (Positron Emission Tomography).
Me ako anō hoki tātou mō te whakatauranga me te taumata o te mate pukupuku.
Ko te whakatau i te āhua o te mate pukupuku he huarahi mā ngā tākuta pukupuku ki te kōrero taipitopito mō te mate pukupuku. Hei tauira, kei hea te pukupuku, mēnā kua horapa, ā, mēnā kua horapa, kei hea, mēnā rānei kua horapa te mate pukupuku ki ētahi atu wāhanga o te tinana.
Ko ngā wāhanga o te mate pukupuku hypopharyngeal mai i te Wāhanga I – ina noho te mate pukupuku ki te pito o raro o te korokoro, ā, kāore anō kia horapa – ki te Wāhanga IV. Ko te Wāhanga IV ko te wā kua horapa te mate pukupuku ki ētahi atu wāhanga o te korokoro me te waha, te tuara o te ihu (nasopharynx), te turanga o te angaanga, me te arai o te kōhao o te uma.
Ka whakarōpūtia hoki te mate pukupuku hypopharyngeal mā te taumata. Mā te taumata o te mate pukupuku ka taea e ngā tākuta pukupuku te matapae i te tere o te horapa o te mate pukupuku. Kei roto i ēnei taumata te GX (he iti te tūponotanga o te horapa o te mate pukupuku) ki te G3 (he tino tūponotanga ka horapa te mate pukupuku).
He aha ngā maimoatanga mō tēnei?
Ko te maimoatanga tino noa ko te pokanga hei tango i te pukupuku me te rongoā irahiko hei patu i ngā pūtau matepukupuku e toe ana. Tērā pea ka whakakotahihia e tō tākuta matepukupuku te pokanga me te rongoā matū, te rongoā ārai mate rānei.
Anei ētahi kōwhiringa pokanga mō te mate pukupuku hypopharyngeal:
- Te tango i te korokoro katoa, te tango hapa rānei: Ka tangohia e tēnei pokanga te katoa, te wāhanga rānei o tō korokoro. Tērā pea ka uru atu ki tēnei he pokanga e kiia nei ko te tango i te pouaka reo (larynx). Nā te mea ka āwhina tō korokoro i a koe ki te manawa, ka hangaia he stoma, he whakatuwheratanga rānei, i muri i te pokanga kia taea ai te whakauru i tētahi ngongo tango i te korokoro. Ka manawa koe mā roto i tēnei ngongo i muri i te pokanga.
- Te tango i te korokoro (`(Te tango i te korokoro)`):Mena ka tangohia tō laryngectomy, ka hangaia pea e tō taote pokanga he kōhao iti (tracheoesophageal puncture – TEP) i waenganui i tō pūwero (trachea) me tō esophagus (oesophagus). Koinei te wāhi e whakauruhia ai he prosthesis reo (laryngectomy speaker device).
- Te tapahi kaki: Ka taea e te taote pokanga te mahi i tenei hei tango i nga pona lymph e pa ana ki te kaki.
- Pokanga karetao whakawhiti-waha (TORS): Mā tēnei pokanga ka taea e ngā taote pokanga te tango i ngā pukupuku matepukupuku i ngā wāhi uaua ki te tae atu, pērā i te pito o raro o te korokoro.
- Pokanga hanga hou: Whai muri i te pokanga hei tango i te katoa, i te wāhanga rānei o te korokoro, o te pouaka reo rānei, me mahi pea te pokanga hanga hou hei whakaora i ngā mahi pēnei i te kai, te manawa, me te kaha ki te whakamahi i tētahi taputapu reo.
Ka pāngia pea tō kaha ki te kōrero, ki te kai, me te manawa e te pokanga mō te matepukupuku korokoro. I mua i te pokanga, pātai atu ki tō taote pokanga me pēhea te pānga o te maimoatanga ki a koe. Hei tauira, ka taea e koe te mahi tahi me tētahi tohunga reo-kōrero (Speech-language pathologist) ki te ako i ngā huarahi hei whakahaere i ngā uauatanga kōrero, horomi rānei ka puta mai i te pokanga.
He ara hei ārai i tēnei mate pukupuku?
Ahakoa kāore e taea te ārai katoa, kei reira ētahi mea ka taea e koe te mahi hei whakaiti i tō tupono ki te whakawhanake i te mate pukupuku hypopharyngeal:
- Te whakamutu rawa i te whakamahi tupeka me te karo i te auahi tuarua.
- Te whakamutu i te inu waipiro, te whakawhāiti rānei i te nui o te waipiro e inuhia ana e koe.
- Tiakina koe i te mate HPV mā te werohanga i te huaketo HPV me te mahi i te moe haumaru.
He aha taku e tumanako atu ai mēnā kei a au tēnei āhuatanga?
Ka taea e te mate pukupuku hypopharyngeal te hoki mai (ka hoki anō) i muri i te maimoatanga. Ka piki ake hoki te mōrearea o te whakawhanake i tētahi momo mate pukupuku hou i ētahi atu wāhi o te tinana. Ka kiia tēnei e ngā tākuta he "mate pukupuku tuarua".
Nō reira, me whakarite koe i ngā wā tirotiro ā-tinana hei āwhina i tō rōpū tiaki matepukupuku ki te aroturuki i tō hauora whānui me te tirotiro i ngā tohu o te hokinga mai, te horapa (metastatic) o te matepukupuku hypopharyngeal, te matepukupuku tuarua rānei. Tērā pea ka uru atu ki tēnei tirotiro ā-tinana ngā whakamātautau whakaahua me ngā whakamātautau tinana. Tērā pea ka whakaritea ēnei wā tirotiro penei:
- Ia rua marama mō te tau tuatahi i muri i te maimoatanga.
- Ia whā marama i te tau tuarua .
- Ia ono marama i te tau tuatoru .
- Kotahi te wā i te tau i te tau tuawhā me te tau tuarima .
- I ētahi wā, ka tūtohu pea tō tīma maimoatanga matepukupuku kia whakahaerehia he tirotiro ā-muri mō te wā katoa .
He aha ngā reiti oranga?
Ina whakaarohia ngā reiti oranga, he mea nui kia mahara he whakatau tata noa iho ēnei i runga i ngā wheako o ētahi atu kua pāngia e te mate pukupuku hypopharyngeal. He rerekē rawa ēnei reiti i runga i te mea kei te wāhi kotahi te mate pukupuku i tīmata ai, kua horapa ki ngā kiko tata me ngā kōpū lymph ('ā-rohe'), kua horapa rānei ki ētahi atu wāhanga o te tinana ('tawhiti').
Waihoki, ka rerekē pea ēnei reiti i runga i tō hauora whānui me ētahi atu āhuatanga. Pātai atu ki tō tākuta matepukupuku kia whakamārama mai me pēhea te pānga o ēnei reiti oranga ki tō āhuatanga. E mōhio ana ia ki a koe me tō hauora whānui, nō reira ko ia te puna mōhiohio pai rawa atu.
Ka taea te whakaora katoa i tēnei?
I ētahi wā, ka taea te rongoā i te mate pukupuku hypopharyngeal mā te pokanga me ētahi atu maimoatanga. Tērā pea ka puta tēnei mena he iti iho i te 2 henimita te rahi o te pukupuku, ā, kāore anō kia horapa. Heoi, heoi anō, he maha ngā tāngata e pāngia ana e tēnei mate pukupuku ka kitea i te wā kua tae ki ngā wāhanga tino kino o te mate.
Me pēhea taku tiaki i ahau anō?
Mena kua pokangahia tō korokoro, me ako koe i ngā huarahi hou mō te manawa me te kōrero. He huringa nui tēnei hei whakahaere. Nō reira, kaua e mangere ki te tono āwhina ki tō tākuta reo-ā-waha. Tērā pea he whakaaro ā rātou mō ngā rōpū tautoko mō te hunga e ora ana i te pokanga korokoro.
Anei ētahi atu huarahi hei tiaki i a koe anō:
- Whakaarohia te oranga o te mate pukupuku. Ka hoki mai pea te mate pukupuku hypopharyngeal, ka puta mai rānei he mate pukupuku tuarua. Tērā pea ka āwangawanga koe mō te heke mai. He maha ngā kaupapa whakaora mate pukupuku e tautoko ana i te hauora hinengaro.
- Me karo tonu i te kai tupeka me te whakawhāiti i te inu waipiro.
- Kai pai. Ka pāngia pea tō kaha ki te kai me te inu e te pokanga korokoro. Whakawhitiwhiti kōrero ki tētahi tohunga kai (tohunga kai) mō ngā mahere kai me ngā taunakitanga. Pātai atu ki tō kaiwhakaora reo me te reo mō ngā huarahi hei whakahaere i ngā raruraru ka whakararuraru i te kai pai.
Āhea ahau me kite i te tākuta?
Kei tō āhua me tō maimoatanga te mea nui. Pātai atu ki tō rōpū tiaki matepukupuku he aha ngā tohumate, ngā raruraru rānei ka pā mai ki a koe, me te wā me whakapā atu koe ki a rātou.
He aha ngā pātai me pātai atu ki te tākuta mate pukupuku?
Ina kite koe i tō tākuta, he mea tino nui kia pātai koe i ēnei pātai:
- He aha te wāhanga o taku matepukupuku?
- He aha ngā kōwhiringa maimoatanga e taunaki ana koe?
- Mena ka pokangahia ahau, he aha ngā kaupapa tautoko e wātea ana hei āwhina i ahau ki te whakatau i ngā huringa ka puta mai?
- He aha te pānga o te maimoatanga ki te kounga o tōku oranga?
- He whakamātautau haumanu kei reira e tika ana kia uru atu ahau?
Ngā mea hei maumahara hei whakarāpopototanga
He mate morearea te mate pukupuku hypopharyngeal. Engari, he maha ngā wā ka kitea i muri i te horapa o te mate pukupuku. I tēnei wā, me mahi pea koe i tētahi pokanga nui, kātahi ka huri i te āhua noho, ā, me noho koe i raro i te tirotiro a te rata mō te toenga o tō oranga.
Ki te pāngia koe e tēnei mate pukupuku, ka harikoa koe i te mōhio kei te whakapau kaha te katoa o tō rōpū tiaki mate pukupuku ki te āwhina i a koe. Ka āwhina rātou i a koe ki te mārama ki tō tātaritanga me ngā kōwhiringa maimoatanga. Ka tautoko hoki rātou i a koe i a koe e ako ana ki te noho me ngā huringa ka puta mai i te maimoatanga mate pukupuku. Kaua e mangere ki te tono āwhina mai i a rātou. He mea pai tonu te rapu tohutohu hauora mēnā he mamae tō korokoro, he uaua ki te horomi, he rerekē rānei tō reo e roa ana mō te neke atu i te rua wiki.











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