Kei a koe anō ēnei tohu rerekē? Me ako tātou mō te Mate a Behçet i roto i ngā kupu māmā noa iho!

Kua rongo kē koe i te mate a Behçet? Tērā pea he ahua rerekē te ingoa. Engari he mate uaua engari ka taea te whakahaere, ā, ka pā ki ngā wāhanga rerekē o ō tātou tinana. Nō reira, me kōrero taipitopito tātou mō tēnei i tēnei rā, he tino māmā noa iho, pērā i te kōrero ki tētahi hoa.

He aha te mate a Behçet?

Ki te kī ngāwari, ko te mate a Behçet he mumura mau tonu o ngā oko toto i roto i ō tātou tinana. Ka karangatia hoki e ngā tākuta ko te "vasculitis." He āhuatanga tēnei e pupuhi ai, e whero ai, e mamae ai hoki ngā oko toto. Ka pā pea ki ngā oko toto nui (ngā uaua) me ngā oko toto iti (ngā uaua). I ētahi wā ka kiia tēnei mate ko te "mate Silk Road" nā te mea he mea noa i ngā rohe o te Silk Road i roto i te hītori.

Ko wai te mea ka nui ake te tūponotanga ka pāngia e tēnei mate?

Ka pāngia te tangata katoa o te ao e te mate a Behçet. Heoi, he nui ake te kitea i ētahi whenua. Hei tauira, he nui ake te kitea i te raki o Turkey, i ngā whenua huri noa i te Moana Mediterranean, i te Middle East me te East Asia. He iti ake te kitea i ngā whenua pēnei i te United States. I te nuinga o te wā ka tīmata ngā tohu i waenga i te 20 me te 30 tau. Heoi, ka taea te puta i ngā tau katoa. Ahakoa i whakaarohia i te tīmatanga ka pā ōrite ki ngā tāne me ngā wāhine, e whakaatu ana ētahi rangahau he paku nui ake te tūponotanga o ngā tāne ki te pāngia e tēnei mate .

He aha ngā tohu o tēnei mate? He aha ō tātou kare ā-roto?

Koinei te mea tino nui. Ka rerekē pea ngā tohu o te mate a Behçet i ia tangata, i ia tangata. Ko te tikanga, kāore pea ō tohu e rite ki ō tētahi atu. Engari, he iti noa ngā tohu matua e kitea whānuitia ana.

Ngā mate waha

Koinei te tohu tuatahi e kitea ana e te tini tāngata . He rite ki ngā mate pukupuku e pā ana ki roto i ō tātou waha, engari he nui ake, he auau ake, he mamae ake hoki . Tērā pea ka pāngia ētahi tāngata e ēnei mate pukupuku waha i mua i te putanga mai o ētahi atu tohu. Ka puta pea ki ngā ngutu, ki te arero, ki roto hoki i ngā paparinga.

Whakaarohia, ka pāngia tonutia koe e ngā mate pukupuku waha, ka tino mamae, kāore e taea e koe te kai, te inu rānei, ā, ahakoa i muri i te tango rongoā, ka hoki mai anō i muri i ētahi rā. He āhua pērā tēnā.

Ngā mate o te ira tangata

Pērā i ngā mate waha, ka puta anō hoki ngā mate taihemahema. Ka mamae anō hoki ēnei. Ka puta anō hoki ki te kiriuhi i roto i ngā tāne, me te kiriuhi i roto i ngā wāhine. Heoi, kāore i te tino kitea pērā i ngā mate waha.

Mumura o te kanohi

He tohu kino anō hoki te mumura o ngā kanohi mō tēnei mate. Ka puta te whero, te mamae, te pōuri o te tirohanga, te aro ki te mārama, me te wai o ngā kanohi . Ki te kore e rongoatia tika, ka taea te ngaro katoa o te tirohanga.Tērā pea. E ai ki ngā pūrongo he tino noa tēnei momo whara kanohi i ngā whenua pēnei i te Middle East me Hapani.

Ngā raruraru kiri

He maha hoki ngā raruraru kiri. I ētahi wā, ka puta mai ngā pupuhi rite ki te pītiti me ngā pona whero (erythema nodosum). He mamae ēnei pupuhi ki te pā atu. I ētahi wā, ka puta mai ngā mate kiri. Ko ētahi o ēnei he papaku noa iho, ko ētahi he hohonu. Ko tētahi atu āhuatanga rerekē ko te mea ki te rakurakuhia, ki te werohia rānei te kiri, ka whero te wāhi, ā, ka puta mai he pupuhi iti i roto i ētahi rā . E kiia ana tēnei e ngā tākuta he "whakamātautau pathergy pai".

Mamae hononga

He mea noa hoki te mamae o ngā hononga i waenga i ēnei tūroro. Ka pāngia ngā pona waewae, ngā turi, ngā tuke, me ngā hope . Tērā pea ka pupuhi, ka whero, ka mamae hoki ngā hononga ina pā atu. Heoi, he iti noa te kino tuturu ki ngā hononga.

Te mumura o te uaua

Ka taea e te mumura i roto i ngā oko toto te whakapūpū i te toto, te aukati , te aukati katoa rānei i ngā oko toto. Ka pā tēnei ki ngā uaua papatahi, e tata ana ki te kiri, me ngā uaua hohonu, e hohonu ana i roto i te tinana. I ētahi wā, ka pāngia te uaua nui rawa atu o tō tātou tinana, te vena cava, ka arahi pea ki ngā raruraru hauora nui. Ko te mumura te take o ēnei raruraru oko toto, ehara i te mea he hapa i roto i te pūnaha toto.

Te whai wāhi o te roro

I ētahi wā ka pāngia hoki te roro e tēnei mate. Ina koa ko ngā kiriuhi e kapi ana i te roro (meninges). Kātahi ka kitea ngā tohu pēnei i te kirika, te ānini nui, te kaki pakari, me te uaua ki te whakarite i te nekehanga i te wā e hikoi ana . I ētahi wā , ka pāngia hoki te roro e te whiu . Koinei te wā ka aukatihia, ka pakaru rānei te uaua toto i roto i te roro.

Ngā āhuatanga o te ara gastrointestinal (GI)

Tērā pea ka puta ngā raruraru i roto i te pūnaha nakunaku, arā, i roto i ngā whekau. Tērā pea ka kite koe i ngā mea pēnei i te mamae o te puku me te toto i roto i te tūtae . Nā te mea he patunga kei roto i te waha me te wāhi taihemahema, me ngā patunga kei roto i ngā whekau. He paku morearea ēnei patunga i roto i ngā whekau, nā te mea ka taea e rātou te whakaheke toto mai i ngā whekau, te pakaru rānei.

Ngā pānga ki ētahi atu okana

Ahakoa he tino onge, ka pā anō hoki te mate ki ētahi atu okana, pērā i ngā pukahukahu, ngā whatukuhu, me ngā uaua toto nui (aorta).

He aha te take e puta ai te mate a Behçet? He aha te take?

Kāore anō kia mōhiotia te tino pūtake o tēnei mate . Kei te rangahau tonu ngā kaipūtaiao. Ko tētahi ariā he "mate pūnaha ārai mate" pea. Ki te kī ngāwari, ko tōna tikanga ko tō tātou ake pūnaha ārai mate, te pūnaha e tiaki ana i a tātou i te mate, ka whakaeke hē i ō tātou ake pūtau hauora.. Ko tēnei whakaeke te take o ngā āhuatanga mumura kua whakahuatia ake nei. Ko ētahi tohu ira, pērā i te `(HLA-B5)` me te `(HLA-B51), ka kitea i roto i ētahi tāngata whai mate nei. Heoi, ehara i te katoa he tohu ira ēnei ka pāngia e te mate a Behçet. Nō reira, kāore e taea te kī ko ngā ira anake te take. E whakapono ana hoki ngā kairangahau i roto i ngā tāngata he mate ira te take, he whakaaro kei te puta mai tēnei mate i te mate (huakita, huaketo rānei) . Ko te tikanga ka pāngia pea e ngā āhuatanga ira me te taiao.

Ko wai kei te nui ake te mōrearea ki te whakawhanake i tēnei mate?

He nui ake te mōrearea o ētahi tāngata ki te pāngia e tēnei mate i ētahi atu:

• Ngā tāngata e noho ana i ngā rohe e kitea whānuitia ana tēnei mate (hei tauira, Turkey, Middle East).
• Ngā tāngata i waenga i te 20 me te 40 tau te pakeke .
• Ngā tāngata whai ira motuhake (HLA-B5, HLA-B51 rānei)
• Ngā tāne (he nui ake te mōrearea o ngā tāne ki te pangia e tēnei mate i ngā wāhine).

Me pēhea te tautuhi tika i tēnei mate? (Tautuhinga)

Kāore he whakamātautau taiwhanga kotahi hei tautuhi i te mate a Behçet. Ka tautuhia te mate e ngā tākuta i runga i ō tohumate. Ko tā rātou e rapu ana ko:

• Te hokinga mai o ngā mate pukupuku waha i ngā wā maha (neke atu i te toru ngā wā i te tau).
• Hei tāpiritanga, me rua pea o ngā āhuatanga e whai ake nei :
• Ngā whara ki te rohe ira tangata.
• Te mumura o ngā kanohi.
• Ngā raruraru kiri.
• He whakamātautau pathergy pai - Ko te tikanga ka puta he ponana whero, he rite ki te mirumiru i roto i ētahi rā i muri i te werohanga, te werohanga rānei o te kiri. Mā tēnei ka kitea te pai o te mahi a te pūnaha ārai mate.

Hei tātaritanga tika i tēnei mate, me whakakore te mate kē atu e puta ai ngā mate waha e rite ana ki te mate a Behçet . Hei tauira, ko te `(systemic lupus)`, ko te `(Crohn's disease)` (he mate mumura o ngā whekau), me ētahi atu momo `(vasculitis)`. Tērā pea ka tonoa e tō tākuta he whakamātautau toto hei āwhina i te whakakore i ēnei atu mate.

He mate tuku iho tēnei?

Kāore he taunakitanga mārama e whakaatu ana he mate tuku iho te mate a Behçet . Ko te nuinga o ngā take ka puta noa mai, kāore he hītori whānau. Ahakoa he iti noa te ōrau o ngā take kua pūrongohia i roto i ētahi mema o te whānau kotahi, kāore he tauira tuku iho mārama.

He aha ngā maimoatanga mō tēnei? (Maimoatanga)

Kāore anō kia kitea he rongoā mō tēnei mate . Heoi anō, he maha ngā rongoā hei āwhina i te whakahaere i ngā tohu:

• Ngā corticosteroids (hei tauira, prednisone): Koinei ngā maimoatanga matua. Ka whakaitihia e ēnei rongoā te mumura me te kaha rawa o te pūnaha ārai mate.
• Colchicine (Colcrys®): Ka āwhina tēnei i ngā mate waha, ngā mate tākihi, me te mamae hononga i ētahi wā.
• Ko etahi atu raau taero immunosuppressant : Ko nga tauira ko te methotrexate (Trexall®, Rasuvo®), azathioprine (Imuran®, Azasan®), cyclophosphamide (Cytoxan®, Neosar®), me te cyclosporine (Gengraf®, Neoral®, Sandimmune®). I roto i nga keehi kino ake, ka whakamahia ano hoki nga anti-TNF (Tumor Necrosis Factor) koiora penei i te infliximab (Remicade®), etanercept (Enbrel®), me te tocilizumab (Actemra®).

He mea nui: Ka taea e ēnei rongoā ārai mate te whakaiti i te kaha o tō tinana ki te whawhai ki te mate, ka piki ake ai tō tūponotanga ki te whakawhanake i ētahi atu mate.

• Apremilast (Otezla®) : He papa rongoā tēnei. Kua whakaaetia hei rongoā i ngā mate waha o te hunga whai mate a Behçet.

I runga i te kaha o tō mate, ka ngana pea tō tākuta ki te whakahaere i ngā tohumate me ngā mea pēnei i ngā pata kanohi, ngā horoi waha, me ngā hinu kiri i mua i te whakamahinga o ēnei rongoā.

He aha te momo tumanako ka taea e koe te whai i a koe e ora tahi ana me tēnei mate?

He mate mau tonu te mate Behçet. Ko te tikanga, ahakoa te maimoatanga, ka ngaro pea, ka puta anō i ētahi wā. Nā tēnei he uaua ki te kī tika i te angitu o te maimoatanga. He maha ngā tūroro ka pāngia e ēnei tohu i ētahi wā puta noa i ō rātou oranga. Heoi, ka taea e te nuinga o te tangata te noho noa, te ora tonu .

Me pēhea te angitu o te ārai i tēnei mate?

He maha ngā huarahi hei āwhina i te wā e noho tahi ana me tēnei mate:

• Te taurite i waenga i te okiokinga me te mahi : Mā te mahi whakakori tinana auau ka pai te ahua o tō tinana, ka whakaiti i te mamae o ngā hononga me ētahi atu wāhi raruraru. Waihoki, he pai te whai wā ki te okioki ina kaha ngā tohu mō tō hauora hinengaro, ā, ka taea hoki te whakaiti i te pānga o ngā tohu.
• Ngā wheako me te hapori tiritahi : Ko te tikanga o tēnei ko te kimi me te kōrero ki ētahi atu tāngata he rite tonu te āhua o te mate. He uaua pea tēnei nā te mea he onge te āhua. Engari ka taea e tō tākuta te āwhina i a koe ki te kimi i ngā tāngata kua rite ngā wheako.

Ka taea e tēnei mate te whakamate?

Ko te ōrau mate mai i tēnei mate he tata ki te 5%.Ko ngā tino take o te mate ko te pakaru o te puku, te whiu, me te pakaru o ngā aneurysms. Ahakoa kāore te mate a Behçet e whakamate tika, ka taea e ia te whakaputa i ngā momo raruraru hauora me ngā āhuatanga hauora puta noa i te tinana, he maha o ēnei he mamae. Heoi, ka taea te whakahaere angitu i te mate me te noho i te oranga noa . Ina koa mēnā ka whakakorikori tinana koe i ia wā, ka okioki, ka kōrero ki ētahi atu e pāngia ana e te taua āhuatanga.

Hei whakamutunga, kia maumahara ki ēnei mea!

He mate uaua, he mate whakararuraru hoki te mate a Behçet. Engari kia maumahara:

• He mate tēnei e taea te whakahaere .
• Ki te puta mai ēnei tohu, rapua tonutia he tohutohu hauora .
• Ka taea e koe te ngana ki te noho i te oranga noa mā te maimoatanga tika me ngā huringa momo noho.
• Kaua e mamae ko koe anake, hono atu ki ngā rōpū tautoko, ki ētahi atu tūroro rānei .

Ko tāku tumanako ka whai hua ēnei kōrero ki a koe. Kia ora tonu!