Kua pāngia koe e te mamae puku nui, te whakapairuaki, me te mimi pouri kāore i te whakamāramatia? I ētahi wā ko te take o tēnei he mate onge kāore anō kia rangona e tātou. Nā te mea he onge rawa, he tokomaha te hunga kāore e mōhio ana. I tēnei rā ka kōrero tātou mō tētahi o aua mate, ko te Acute Hepatic Porphyria (AHP). Kaua e manukanuka, ka kōrerohia e tātou tēnei i roto i te huarahi māmā noa iho, i roto i te huarahi e mārama ai te katoa.
He aha te Acute Hepatic Porphyria (AHP)?
Ko te Acute Hepatic Porphyria, arā, ko te AHP, he mate e puta mai ana i te nui rawa o te kohikohinga o ngā porphyrin, he momo matū e hangaia ana i roto i te tinana, i roto i te ate me ētahi atu wāhanga o te tinana. Ehara tēnei i te mate kotahi, engari he rōpū mate. Ina kohikohia ngā porphyrin i tēnei ara, ka pā ki te pūnaha io, ā, ka puta he maha atu ngā tohu whakararuraru.
Ahakoa kāore anō kia kitea he rongoā mō tēnei mate, mā te maimoatanga tika ka āwhina i a koe ki te whakahaere i ngā tohu me te whakapai ake i tō oranga.
He aha i puta ai tēnei mate? Kia tirohia tata atu tātou.
Hei mārama tika ki tēnei, me mōhio tātou ki tētahi mea tino nui i roto i ō tātou tinana. Ko te ingoa o tēnā ko te ' Heme ' .
He wāhanga nui te heme o te pūmua hemoglobin i roto i ō tātou toto whero. E mōhio ana koe, ko te hemoglobin te mea e kohi ana i te hāora mai i ngā pukahukahu, ā, e tohatoha ana puta noa i te tinana. Nō reira, he mea nui tēnei heme mō te mahi a ngā wāhi pēnei i te ate, ngā uaua, me te hinu wheua.
Inaianei, tirohia, ina hangaia e tō tātou tinana tēnei 'heme', e 8 ngā momo whākōkī hei āwhina i te whakahaere tika i taua tukanga. He rite ki te 8 ngā momo mea kakara e hiahiatia ana hei hanga i tētahi rihi. Mēnā he ngoikoretanga, he ngoikore rānei tētahi o ēnei whākōkī e 8, ka mutu te tukanga hanga 'heme' i waenganui. Ko te mea ka tupu ko ngā 'porphyrins' i kōrerohia e tātou i mua ake nei, arā, ngā kai e whakamahia ana hei hanga 'heme', ka tīmata ki te kohikohi i roto i te tinana .
I roto i te AHP, ka kohia te nuinga o tēnei matū e kiia nei ko te ' porphyrin ' ki roto i te ate . Ko ngā pānga o tēnei kohi ka puta hei tohu.
| Ngā tohu e kitea whānuitia ana | He kōrero anō mō tēnei |
|---|---|
| Mamae nui o te puku | Koinei te tohu matua, te tohu kino rawa atu hoki. Tērā pea ka pāngia koe e te mamae puku nui, kāore i te mārama te take. |
| Whakapairuaki me te ruaki | Ka puta pea tēnei āhuatanga me te mamae nui o te puku. |
| Mimi pouri | Ka huri pea te tae o te mimi hei parauri pouri, hei whero rānei. |
| Te aro o te kiri | I ētahi momo porphyria, ka tino pāngia te kiri e te hihi o te rā. |
| Ngā raruraru o te pūnaha io | Tērā pea ka puta ngā āhuatanga kino pērā i te ngoikore o te tinana, te mamae, te ngoikore o te uaua me te haurangi. |
Ko te "whakaekenga" o te AHP ka tīmata i te mamae nui o te puku. Ka roa pea tēnei mō ngā rā. I roto i ēnei āhuatanga , me haere ki te hōhipera . Ko te tikanga o tēnei ko te haere ki te Tari Whawhati Tata (ETU).
Ko wai ka pāngia e tēnei mate? Ko wai kei te mōrearea?
He maha ngā wā, he mate tuku iho tēnei. Arā, ka riro i a koe ngā ira e puta ai tēnei mate i ō mātua.
Engari ko te mea nui i konei , ehara i te mea ko te hunga katoa kei a rātou te ira e puta ai te mate ka pāngia e ngā tohu . Ko te nuinga o te hunga whai ira AHP ka taea te noho hauora puta noa i ō rātou oranga me te kore he tohu.
He rite tēnei ki te raiona e moe ana. Ahakoa kei reira te ira, ki te kore he mea hei whakaoho i a ia, hei "whakaara" rānei i a ia, ka taea e ia te noho tonu me te kore he raruraru.
Nā, he aha ngā mea e whakaoho ana i tēnei mate?
He wāhanga tino nui tēnei. Mena kei a koe, kei tētahi atu rānei e mōhio ana koe, he mea nui kia mōhio koe ki ēnei mea.
| Whakaoho | Ngā kōrero nui |
|---|---|
| Ētahi rongoā | Ko ētahi rongoā whakamamae mamae, rongoā whakangāwari, rongoā barbiturates, rongoā whakangāwari, me ngā pire ārai whānau ka raru pea. Mena kei te whakapae koe kua pāngia koe e te AHP, kaua e tango i tētahi rongoā me te kore kōrero ki te tākuta. |
| Te inu waipiro me te momi hikareti | Ka ngāwari noa iho te whakaoho i te mate nā te mea ka nui te pēhanga ki te ate. |
| Te kai tino tika, te nohopuku rānei | He tino kino ki ēnei tūroro te whakawhāiti i te kai, te kore rānei e kai i ngā kai hei whakaiti i tō rātou taumaha. He tino take nui tēnei o te korenga e whiwhi i ngā kaora e hiahiatia ana e te tinana. |
| Te ahotea hinengaro me te ahotea tinana | Ka taea hoki e ngā āhuatanga pēnei i te ahotea nui, te pokanga, me ngā mate pāwera te whakaoho i te mate. |
Me aha ahau?
Mena kei te pāngia koe e tētahi o ngā tohu kua whakahuatia i roto i tēnei tuhinga, inā koa te mamae puku kino, kāore i te mārama, i ia wā , kaua e whakaaro he mea noa. Tirohia he tākuta whai tohu tonu.
Ka tirohia koe e te tākuta, ā, ki te tika, ka tonoa he whakamātautau mimi, toto, me ngā whakamātautau ira hei whakatau mēnā kei a koe te mate.
He mea tino nui te kai taurite mō te tangata e pāngia ana e te AHP. Mēnā e tika ana, ka tukuna pea koe e tō tākuta ki tētahi tohunga kai.
Karere Tangohia ki te Kāinga
- Ko te Acute Hepatic Porphyria (AHP) he mate onge, he mate tuku iho e puta mai ana i te kohi o te matū e kiia nei ko te porphyrin i roto i te ate.
- Ko te tino take o tēnei he korenga o te whākōkī e hiahiatia ana i roto i te tukanga hanga 'heme'.
- Ko te tohu matua ko te mamae o te puku e kore e taea te manawanui. Ka pā mai hoki ngā raruraru ki te pūnaha io.
- Ahakoa kei a koe te ira e puta ai te mate, ki te karohia e koe ngā mea e puta ai te mate, tērā pea kāore koe e kite i ngā tohu.
- Ko ētahi rongoā, te waipiro, te momi hikareti, te kai tōtika, me te ahotea ngā mea matua e whakaoho ana i te mate.
- Ki te mea kei a koe tētahi o ēnei tohu, ki te whakaaro rānei koe kei a koe te AHP, me kōrero koe ki te tākuta. Kaua rawa e haere ki waho ki te tiki rongoā māu ake.
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