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He mate pukupuku repeure anō tōu? Me ako tātou mō tēnei.

He mate pukupuku repeure anō tōu? Me ako tātou mō tēnei.

Kua rongo pea koe i ngā kupu 'Adrenal Cancer', he mea hou rānei tēnei ki a koe. Heoi, he mea noa te mataku me te hiahia ki te mōhio ina rongo koe i tēnei ingoa. Kaua e manukanuka, ka kōrerohia e mātou tēnei mea kia māmā noa iho, kia mārama ai koe. Nā te mea, he mea tino nui te mōhio tika ki ngā mea pēnei.

He aha tonu te matepukupuku repeure?

Hei whakarāpopototanga, e rua ā tātou whatukuhu i roto i te tinana, tika? I runga ake i aua whatukuhu e rua, e rua ngā repe, he rite ki ngā taupoki iti e rua. Koinei ngā mea e kiia nei e tātou ko ngā repe adrenal . Ahakoa he iti te rahi, he mahi tino nui tā rātou i roto i tō tātou tinana. Arā, ka whakaputahia e rātou ngā momo homoni e tika ana mō te mahi a tō tātou tinana. He maha ngā mea e whakahaeretia ana e ēnei homoni i roto i tō tātou tinana, hei tauira, te pākia o te tinana me te toto toto tiketike.

He aha te mate pukupuku? Ka wehea, ka tipu, ā, ka mate ngā pūtau o roto i tō tātou tinana. He tukanga noa tēnā. Engari i ētahi wā, ka puta he huringa, he whakarerekētanga rānei, i roto i ngā pūtau o ēnei repe adrenal, ā, ka tīmata aua pūtau te wehe tere me te kore e taea te whakahaere. Ka huihui ēnei pūtau e tipu rerekē ana hei hanga i tētahi pukupuku . Ki te kino tēnei pukupuku, koinā te mea e kiia nei e tātou ko te 'mate pukupuku adrenal'. Ka taea e tēnei mate pukupuku te whanake i roto i te repe adrenal kotahi anake, ka taea rānei te whanake i roto i ngā repe e rua.

He momo matepukupuku repeure kei reira?

Ae, he maha ngā momo matua o te mate pukupuku repe adrenal, i runga i te wāhi e puta ai. Me titiro tātou ki ēnei momo:

1. Te Matepukupuku Adrenocortical (ACC): Koinei te momo matepukupuku adrenal tino noa. Ka puta i te paparanga o waho o te repe adrenal, e kiia nei ko te cortex . Ka whakaputahia e tēnei cortex ngā homoni steroid e whakahaere ana i ngā mea pēnei i te pākia o te tinana, te toto toto tiketike, te āhua o te tinana, me te tipu o te makawe.

2. Neuroblastoma: Ka whanake tēnei momo matepukupuku i roto i ngā pūtau io. Nō reira, ka taea e rātou te whanake i roto i ngā wāhanga rerekē o te tinana. Heoi, tata ki te hautoru o ēnei ka whanake i roto i te wāhanga o roto o te repe adrenal, e kiia nei ko te medulla . Ka whakaputahia e te medulla ngā matū e kiia nei ko te epinephrine me te norepinephrine. Ka āwhina ēnei ki te whakahaere i te pūnaha io sympathetic, e whakahaere ana i ngā mea pēnei i te werawera, te tere o te ngakau, me te toto toto. Ko tēnei momo matepukupuku te mea tino noa i roto i ngā pēpi me ngā tamariki kei raro iho i te 10 tau te pakeke.

3. Pheochromocytoma: Ka tīmata tēnei mate pukupuku i waenganui o te medulla, i roto i ngā pūtau e whakaputa ana i te adrenaline. He homoni te adrenaline e āwhina ana ki te whakahaere i te toto toto me te tere o te ngakau.

He pēhea te noa o tēnei mate pukupuku repeure?

He tino onge te mate pukupuku o te repe adrenal. Hei tauira, i roto i tētahi whenua pērā i te Hononga o Amerika, e rua rau noa iho ngā tāngata e kitea ana tēnei mate i ia tau. Nō reira kaua e mataku rawa i te rongonga mō tēnei mate.

He aha ngā tohu pea o te mate pukupuku repe adrenal?

He mea tino nui tēnei. Kāore te mate pukupuku adrenal e pā ki te katoa i te huarahi kotahi. Tērā pea ka pāngia ētahi tāngata e te mamae i te tipu o te pukupuku me te pēhi i ngā whekau tata. Mō ētahi atu, ka puta pea i te pukupuku ngā tohu maha nā ngā homoni e whakaputaina ana e ia.

Anei ētahi o ngā tohu e kitea whānuitia ana:

  • Mamae puku
  • Mamae tuara
  • Te ahua o te kī i roto i tō puku
  • Ngā uaua e māuiui ana, e mamae ana
  • Te ngoikore o te tinana
  • Ngā mamae o te upoko

Tērā anō hoki ētahi tohu motuhake i puta mai i ngā huringa homoni. Hei tauira:

  • Te tupu o ngā huruhuru kāore e hiahiatia ana i te mata, i te tinana rānei (hirsutism)
  • Te tīmatanga ohorere o te mate huka , te taumata huka toto tiketike rānei
  • toto toto tiketike
  • Ngā taumata pāhare pāporo iti i roto i te toto (hypokalemia)
  • Te whakahekenga taumaha kāore i te whakamāramahia
  • Te pikinga taumaha kāore i te whakamāramahia
  • Te tere o te manawa (Te tere o te manawa)
  • Ngā ū kua whakanuia (i roto i ngā wāhine me ngā tāne)
  • Te whakanui rerekē o ngā ira tangata (ure i roto i ngā tama, clitoris rānei i roto i ngā kōtiro) i roto i ngā tamariki
  • Te iti o te hiahia
  • Te manukanuka auau
  • Ngā whakaekenga mataku

He mea nui, i ētahi wā kāore he tohu o ngā pukupuku repe adrenal, ā, i ētahi wā ka kitea noa iho i te wā o te matawai mō tētahi atu take.

Ngā Tohu o te Matepukupuku Adrenal Metastatic

Mena ka horapa te mate pukupuku ki tua atu i ngā repe adrenal, arā, ki ētahi atu wāhanga o te tinana (metastatic), ka kaha ake pea ngā tohu. Ko ngā tohu o te mate pukupuku wāhanga 4 ko:

  • Whakapairuaki me te ruaki
  • Pupuhi
  • Ngenge
  • Kirika
  • Pōhēhētanga
  • Te ngaronga o te hiahia kai

He aha ngā take o te matepukupuku repeure?

Ina hoki, kāore anō kia mōhiotia e ngā tākuta te tino take o te mate pukupuku repe adrenal i te nuinga o ngā wā. E mōhio ana tātou ka taea e ngā huringa (ngā whakarerekētanga) o te DNA i roto i ō tātou pūtau te meinga kia rerekē te whanonga o ngā pūtau, kia noho hei mate pukupuku. Engari ko te mea kāore i te mārama ko te take i puta ai ēnei huringa DNA.

Ka riro i ētahi tāngata tētahi whakarerekētanga ira mai i ō rātou mātua, ā, ka piki ake te tūponotanga ki te pāngia e ēnei mate pukupuku. I ētahi atu wā, ka taea hoki e te pānga ki ngā matū whakaputa mate pukupuku te take. Heoi, i roto i te nuinga o ngā wā, te āhua nei ka puta ēnei whakarerekētanga DNA me te kore he take e kitea ana.

He aha ngā āhuatanga mōrearea mō te mate pukupuku repe adrenal?

Ko te tūponotanga mōrearea he mea e whakanui ake ai i te tūponotanga o te pāngia e te mate. Ehara i te mea ka tino pāngia koe e te mate. Engari ka taea e ia te kī atu kei te nui ake tō tūponotanga.

Ko ētahi o ngā āhuatanga mōrearea taiao ka pā ki te mate pukupuku repe adrenal ko:

  • Te momi hikareti
  • Te pānga ki ētahi matū, hei tauira, te asbestos me te radon .
  • I mua i te whiwhinga i te rongoā irahiko ki te puku (kei hea ngā repe adrenal).

Ahakoa te nuinga o ngā pukupuku adrenal ka puta mai i waho o te tinana, tata ki te 15% o te hunga e pāngia ana e ngā pukupuku adrenal he mate ira . He mea tino noa tēnei i roto i ngā tamariki. Ko ētahi o ngā mate ira ka pā pea ki te mate pukupuku repe adrenal ko:

  • Te mate Beckwith-Wiedemann
  • Te mate o Von Hippel-Lindau
  • Te mate Li-Fraumeni
  • Te polyposis adenomatous whānau (FAP)
  • Neurofibromatosis momo 1
  • Ngā neoplasia endocrine maha (MEN)
  • Te matatini o Carney
  • Te mate Lynch

He ahua uaua tēnei, kāore? Ki te mea he ruarua āu mō tēnei momo āhuatanga, he pai ake te kōrero ki te tākuta.

Me pēhea koe e mōhio ai mēnā he mate pukupuku repe tāu?

Tērā pea ka whakapae tō tākuta kei te mate pukupuku koe i te repe adrenal i runga i ō tohu (hei tauira, te tupu rerekē o te makawe, te huringa ohorere o te taumaha). Engari i ētahi wā, ka kitea noa iho ēnei pukupuku i te wā o te matawai CT (matawai tomography rorohiko) te matawai MRI rānei (whakaahua aukume) i mahia mō tētahi atu take.

Ina haere koe ki te tākuta, ka mahia e ia ēnei mea:

  • Whakahaerehia he whakamātautau tinana.
  • Ka arotakehia tō hītori hauora.
  • Kei te pātai atu ahau mō ō tohumate.
  • Ka tirohia e rātou mēnā he take mōrearea kei a koe mō te mate pukupuku repe adrenal.
  • Pātai atu mō tō hītori whānau mō te mate pukupuku.

He aha ngā whakamātautau hei āwhina i te tautuhi i te mate pukupuku repe?

I muri i te whakamātautau tinana, ka whakahaerehia pea e te tākuta ētahi atu whakamātautau, hei whakaū i te mate, hei whakakore rānei i ētahi atu mate hauora. Kei roto i ēnei whakamātautau:

  • Ngā whakamātautau toto:Ka taea te whakamahi i ēnei hei tirotiro i ngā taumata homoni me ētahi atu tohu.
  • Tātaritanga mimi: Ka taea te whakamātautau i te mimi mō ngā homoni me ētahi atu matū.
  • Ngā whakamātautau whakaahua: Mā ngā whakamātautau pēnei i ngā karapa CT, ngā karapa MRI, me ngā karapa PET ka taea te whakaatu mārama i te rahi, te wāhi, me te horapa o te pukupuku. I ētahi wā ka taea te mahi i te koiora , arā, te tango i tētahi wāhanga iti o te pukupuku hei whakamātautau, engari kāore i te mahia tonutia tēnei i roto i te matepukupuku repeure.

Te whakatau i te mate pukupuku adrenal

Ka whakamahia e ngā tākuta he pūnaha whakatauranga mate pukupuku hei tātaritanga i te mate pukupuku repe tākihi. Kei roto i tēnei ko te rahi o te puku, tōna wāhi, me te mea kua horapa (metastasized) ki ētahi atu wāhanga o te tinana.

Ki te kī māmā noa, ka nui ake te horapa o te mate pukupuku:

  • Wāhanga 1: E 5 henimita te rahi o te pukupuku, iti iho rānei, ā, kāore anō kia horapa ki tua atu i te repe adrenal.
  • Wāhanga 2: He nui ake te pukupuku i te 5 henimita, engari kāore anō kia horapa ki tua atu i te repe adrenal.
  • Wāhanga 3: Kei roto i te repe adrenal te mate pukupuku, ā, kua horapa ki ngā kiko e karapoti ana, ki ngā kōpū lymph tata rānei.
  • Wāhanga 4: Kei roto i te repe adrenal te mate pukupuku, ā, kua horapa ki ngā whekau tawhiti pērā i ngā pukahukahu me te ate.

He uaua pea ēnei wāhanga. Mena he pātai motuhake āu mō tō mate, he pai ake te kōrero ki tō tākuta.

Ka taea te rongoā i te mate pukupuku repeure?

He raruraru tēnei mō te tini o te tangata. Mena kei te repe adrenal anake te mate pukupuku, ā, kāore anō kia horapa ki ētahi atu wāhanga o te tinana, tera pea ka ora. Ko te tango pokanga o te repe (adrenalectomy) te maimoatanga matua mō tēnei wā.

Heoi, ki te horapa te mate pukupuku ki tua atu i te repe adrenal, ka iti ake te tūponotanga o te ora katoa. Heoi anō, ka taea e te maimoatanga te whakahaere i te tipu o te pukupuku me te whakapai ake i te kounga o tō oranga.

Me pēhea te rongoā i te mate pukupuku repe adrenal?

Ko te maimoatanga mō te matepukupuku repe adrenal e whakawhirinaki ana ki te rahi o te pukupuku, tōna wāhi, me te mea kua horapa atu ki tua atu i te repe adrenal. He maha ngā maimoatanga ka taea:

  • Pokanga:

Mena kei roto noa te puku i te repe adrenal, kua horapa rānei ki ngā kiko tata, ki ngā kōpū lymph rānei, tera pea ka tūtohu tō tākuta kia pokangahia. Ka tangohia e te taote pokanga te repe adrenal katoa (adrenalectomy) me ngā wāhanga mate tata katoa.

Mena kei roto i te repe adrenal kotahi anake te mate pukupuku, ka mahi noa te repe kē atu. I te nuinga o te wā, kāore he mahi kē atu e hiahiatia ana. Heoi, ki te tangohia ngā repe adrenal e rua, me tango rongoā koe hei whakakapi i ngā homoni i hangaia e aua repe mō te toenga o tō oranga.

I ētahi wā, ka tūtohutia te chemotherapy , te radiation therapy rānei i muri i te pokanga hei whakangaro i ngā pūtau matepukupuku e toe ana, hei whakaiti hoki i te tūponotanga o te hokinga mai o te matepukupuku.

Ahakoa kua horapa te mate pukupuku, tera tonu ētahi wā ka tūtohutia kia pokangahia hei tango i te nuinga o te pukupuku. Ka kiia tēnei ko te 'pokanga tango i te pukupuku' .

  • Te rongoā irahiko:

Ko te tikanga o tēnei ko te whakamahi i ngā hihi X-ray kaha-teitei hei whakangaro i ngā pūtau matepukupuku. He iti noa te whakamahinga o te rongoā irahiko hei rongoā tuatahi mō te matepukupuku repeure. Ka taea te whakamahi hei whakaiti i te tūponotanga o te hokinga mai o te matepukupuku i muri i te pokanga. Ka taea hoki te whakamahi hei whakaiti i ngā tohu i te wāhi kua horapa te matepukupuku. Ka taea e ngā tākuta te hoatu rongoā irahiko me te chemotherapy, me ētahi atu rongoā rānei.

  • Te rongoā matū:

Ko te chemotherapy te whakamahinga o ngā rongoā hei patu i ngā pūtau matepukupuku. Ka taea te hoatu i ēnei rongoā hei pire, hei werohanga rānei mā roto i te uaua. He maha ngā wā ka whakamahia te chemotherapy hei rongoā i te matepukupuku repeure kua horapa ki ētahi atu wāhanga o te tinana. Ka taea hoki te whakamahi hei patu i ngā pūtau matepukupuku e toe ana i muri i te pokanga.

He rongoā chemotherapy te Mitotane e whakamahia whānuitia ana hei rongoā i te mate pukupuku o te repe adrenal.

  • Ētahi atu rongoā:

Ka whakamahia hoki e ngā tākuta ētahi atu rongoā hei rongoā i ngā pukupuku repe adrenal. Ka taea e ētahi rongoā, pērā i te metyrapone, te whakaiti i te hanga o ngā homoni steroid adrenal. Ko ētahi atu rongoā, pērā i te spironolactone me te mifepristone, ka ārai i ngā pānga o ngā homoni i hangaia e te pukupuku.

Ahakoa ka taea e ēnei rongoā te whakaora i ō tohumate, kāore e whakaiti, e whakangaro rānei i ngā pūtau matepukupuku.

Ko wai e rongoā ana i te mate pukupuku repeure?

Mena he mate pukupuku repe tāu, tera pea he maha ngā tohunga kei roto i tō rōpū hauora, tae atu ki:

  • Ngā tohunga mate pukupuku - e pā ana ki te pokanga, te irahiko, me ngā maimoatanga rongoā.
  • Ngā endocrinologists - mō ngā raruraru e pā ana ki ngā homoni.

Ka tere te horapa o te mate pukupuku repe?

Ka rerekē tēnei i runga i te momo pukupuku kei a koe:

  • Ko te adrenocortical carcinoma, te momo tino noa, ka tere te tipu me te horapa.
  • Ka puhoi te tipu o ētahi momo neuroblastoma , ko ētahi ia ka tere te tipu.
  • Ka puhoi te tipu o te nuinga o ngā pheochromocytomas matepukupuku.

Kāore te mate pukupuku adrenal e pā ki te katoa i te huarahi kotahi. Mena he pātai āu mō te tere o te tipu o tō pukupuku, he pai ake te kōrero ki tō tākuta.

He pēhea te kino o te mate pukupuku repe adrenal?

I te nuinga o te wā, he uaua ki te rongoā te mate pukupuku repe adrenal. Ko te āhua o te mate pukupuku e whakawhirinaki ana ki te wāhi o te puku, tōna rahi, me te horapa rānei ki ētahi atu wāhanga o te tinana.

Ka taea e koe te ora i te pukupuku adrenal? Ngā Auau Ora o te Matepukupuku Adrenal

Ae, ka taea te ora i te mate pukupuku repeure. Heoi, he maha ngā āhuatanga e pā ana ki tēnei.

Mō ngā reiti oranga, ko te reiti oranga mō te mate pukupuku repe adrenal i roto i ngā tau e rima i te tīmatanga kei waenganui i te 50% me te 60% . Ko te tikanga tēnei tae atu ki te 60% o te hunga whai mate kei te ora tonu i roto i ngā tau e rima i muri i te tātaritanga. Heoi, ina horapa te mate pukupuku ki ētahi atu wāhanga o te tinana, ka heke tēnei reiti oranga mō ngā tau e rima ki te 10% ki te 20%.

Engari kia maumahara ki tēnei: ​​He tatauranga noa iho ngā reiti ora. Kāore e whakaatu tika ana i te roa o tō oranga, i te angitu rānei o tētahi maimoatanga mōu. Kōrero ki tō tākuta kia mōhio ai koe me pēhea te pānga o ēnei tatauranga ki tō āhuatanga.

Ka taea te ārai i te mate pukupuku repe adrenal?

Kāore anō kia kitea he huarahi hei ārai i te mate pukupuku o te repe adrenal, engari mā te karo i ngā āhuatanga mōrearea taiao, pērā i te momi hikareti, ka āwhina i te whakaiti i tō mōrearea whānui ki tētahi taumata.

Āhea ahau me toro atu ki te tākuta?

Kāore i te ngāwari te kite i ngā tohu o te matepukupuku repe adrenal. Heoi, me toro atu ki te tākuta mēnā ka pāngia koe e tētahi o ēnei e whai ake nei:

  • Mamae puku
  • Te mate huka ohorere
  • Te whakahekenga taumaha, te pikinga taumaha rānei kāore i te whakamāramatia
  • Te tupu nui o te makawe
  • Ngā huringa ki ō ira tangata

Mena kua pāngia tētahi mema o te whānau tata (matua, teina rānei) e te mate pukupuku repeure, he mea pai hoki kia kōrero koe ki tētahi tākuta mō tō mōrearea.

He aha ngā pātai me pātai atu e au ki taku tākuta?

Mena kua tāpaetia koe, tō whanaunga rānei, kei te mate pukupuku repe adrenal koe, he mea pai pea kia pātai atu koe ki a koe anō i ēnei pātai:

  • Kei hea te pukupuku? (Kei hea te pukupuku?)
  • He aha te rahi o te pukupuku?
  • Kua horapa te mate pukupuku ki waho o taku repe adrenal?
  • Me nui ake ngā whakamātautau e hiahiatia ana e au?
  • He aha aku kōwhiringa maimoatanga?
  • Ka taea e au te mahi, te haere rānei ki te kura i te wā e rongoatia ana?
  • Āhea ahau ka tīmata ai te maimoatanga?
  • He aha taku e taea ai hei whakamama i aku tohumate?
  • He aha ngā tūponotanga ka hoki mai anō te mate pukupuku repe?

He mea noa te maha o ngā kare ā-roto e pāngia ana e te mate pukupuku repeure. Kei reira tō tākuta hei āwhina i a koe. Haunga te kōrero mō ngā kōwhiringa maimoatanga, ka taea hoki e ia te kōrero ki a koe mō ngā puna kōrero me te tautoko. Tērā pea ka taea e koe te kōrero ki ētahi atu e pāngia ana e ngā wheako ōrite mā roto i ngā rōpū tautoko, i tō rohe, i te ipurangi rānei. He tino āwhina ēnei mō tō oranga hinengaro, kare ā-roto, me tō oranga wairua i tēnei wā uaua.

Karere Tangohia ki te Kāinga

Āe, me whakarapopoto tātou i ētahi o ngā kōrero tino nui o ngā mea kua kōrerohia e tātou.

  • He mate onge te matepukupuku adrenal.
  • He rerekē ngā tohu, ā, i ētahi wā, kāore pea he tohu. Ki te kite koe i tētahi mea rerekē, rapua he tohutohu hauora.
  • Kāore i te mārama tonu te take, engari tera pea he pānga o ngā āhuatanga ira me te taiao.
  • He maha ngā kōwhiringa maimoatanga, kei runga i te wāhanga me te āhua o te mate pukupuku.
  • Mā te kitenga wawe ka nui ake te tūponotanga o te whakaoranga.
  • Mena he pātai āu, he pātai rānei tā tētahi e mōhio ana koe mō tēnei, kaua e wehi ki te kōrero ki te tākuta. He mea tino nui ngā mōhiohio tika me te tautoko.

Kia maumahara, kāore koe i te mokemoke. Kua whanake haere te pūtaiao hauora, ā, he tokomaha ngā tāngata ka taea te āwhina i a koe.


Matepukupuku adrenal , repe adrenal, homoni, tohumate pukupuku, maimoatanga pukupuku, whatukuhu, wāhanga pukupuku

Frequently Asked Questions (FAQ)

He aha ngā whakamātautau hei āwhina i te tautuhi i te mate pukupuku repe?

I muri i te whakamātautau tinana, ka whakahaerehia pea e te tākuta ētahi atu whakamātautau, hei whakaū i te mate, hei whakakore rānei i ētahi atu mate hauora. Kei roto i ēnei whakamātautau:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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He mate pukupuku repeure anō tōu? Me ako tātou mō tēnei.

He mate pukupuku repeure anō tōu? Me ako tātou mō tēnei.

Kua rongo pea koe i ngā kupu 'Adrenal Cancer', he mea hou rānei tēnei ki a koe. Heoi, he mea noa te mataku me te hiahia ki te mōhio ina rongo koe i tēnei ingoa. Kaua e manukanuka, ka kōrerohia e mātou tēnei mea kia māmā noa iho, kia mārama ai koe. Nā te mea, he mea tino nui te mōhio tika ki ngā mea pēnei.

He aha tonu te matepukupuku repeure?

Hei whakarāpopototanga, e rua ā tātou whatukuhu i roto i te tinana, tika? I runga ake i aua whatukuhu e rua, e rua ngā repe, he rite ki ngā taupoki iti e rua. Koinei ngā mea e kiia nei e tātou ko ngā repe adrenal . Ahakoa he iti te rahi, he mahi tino nui tā rātou i roto i tō tātou tinana. Arā, ka whakaputahia e rātou ngā momo homoni e tika ana mō te mahi a tō tātou tinana. He maha ngā mea e whakahaeretia ana e ēnei homoni i roto i tō tātou tinana, hei tauira, te pākia o te tinana me te toto toto tiketike.

He aha te mate pukupuku? Ka wehea, ka tipu, ā, ka mate ngā pūtau o roto i tō tātou tinana. He tukanga noa tēnā. Engari i ētahi wā, ka puta he huringa, he whakarerekētanga rānei, i roto i ngā pūtau o ēnei repe adrenal, ā, ka tīmata aua pūtau te wehe tere me te kore e taea te whakahaere. Ka huihui ēnei pūtau e tipu rerekē ana hei hanga i tētahi pukupuku . Ki te kino tēnei pukupuku, koinā te mea e kiia nei e tātou ko te 'mate pukupuku adrenal'. Ka taea e tēnei mate pukupuku te whanake i roto i te repe adrenal kotahi anake, ka taea rānei te whanake i roto i ngā repe e rua.

He momo matepukupuku repeure kei reira?

Ae, he maha ngā momo matua o te mate pukupuku repe adrenal, i runga i te wāhi e puta ai. Me titiro tātou ki ēnei momo:

1. Te Matepukupuku Adrenocortical (ACC): Koinei te momo matepukupuku adrenal tino noa. Ka puta i te paparanga o waho o te repe adrenal, e kiia nei ko te cortex . Ka whakaputahia e tēnei cortex ngā homoni steroid e whakahaere ana i ngā mea pēnei i te pākia o te tinana, te toto toto tiketike, te āhua o te tinana, me te tipu o te makawe.

2. Neuroblastoma: Ka whanake tēnei momo matepukupuku i roto i ngā pūtau io. Nō reira, ka taea e rātou te whanake i roto i ngā wāhanga rerekē o te tinana. Heoi, tata ki te hautoru o ēnei ka whanake i roto i te wāhanga o roto o te repe adrenal, e kiia nei ko te medulla . Ka whakaputahia e te medulla ngā matū e kiia nei ko te epinephrine me te norepinephrine. Ka āwhina ēnei ki te whakahaere i te pūnaha io sympathetic, e whakahaere ana i ngā mea pēnei i te werawera, te tere o te ngakau, me te toto toto. Ko tēnei momo matepukupuku te mea tino noa i roto i ngā pēpi me ngā tamariki kei raro iho i te 10 tau te pakeke.

3. Pheochromocytoma: Ka tīmata tēnei mate pukupuku i waenganui o te medulla, i roto i ngā pūtau e whakaputa ana i te adrenaline. He homoni te adrenaline e āwhina ana ki te whakahaere i te toto toto me te tere o te ngakau.

He pēhea te noa o tēnei mate pukupuku repeure?

He tino onge te mate pukupuku o te repe adrenal. Hei tauira, i roto i tētahi whenua pērā i te Hononga o Amerika, e rua rau noa iho ngā tāngata e kitea ana tēnei mate i ia tau. Nō reira kaua e mataku rawa i te rongonga mō tēnei mate.

He aha ngā tohu pea o te mate pukupuku repe adrenal?

He mea tino nui tēnei. Kāore te mate pukupuku adrenal e pā ki te katoa i te huarahi kotahi. Tērā pea ka pāngia ētahi tāngata e te mamae i te tipu o te pukupuku me te pēhi i ngā whekau tata. Mō ētahi atu, ka puta pea i te pukupuku ngā tohu maha nā ngā homoni e whakaputaina ana e ia.

Anei ētahi o ngā tohu e kitea whānuitia ana:

  • Mamae puku
  • Mamae tuara
  • Te ahua o te kī i roto i tō puku
  • Ngā uaua e māuiui ana, e mamae ana
  • Te ngoikore o te tinana
  • Ngā mamae o te upoko

Tērā anō hoki ētahi tohu motuhake i puta mai i ngā huringa homoni. Hei tauira:

  • Te tupu o ngā huruhuru kāore e hiahiatia ana i te mata, i te tinana rānei (hirsutism)
  • Te tīmatanga ohorere o te mate huka , te taumata huka toto tiketike rānei
  • toto toto tiketike
  • Ngā taumata pāhare pāporo iti i roto i te toto (hypokalemia)
  • Te whakahekenga taumaha kāore i te whakamāramahia
  • Te pikinga taumaha kāore i te whakamāramahia
  • Te tere o te manawa (Te tere o te manawa)
  • Ngā ū kua whakanuia (i roto i ngā wāhine me ngā tāne)
  • Te whakanui rerekē o ngā ira tangata (ure i roto i ngā tama, clitoris rānei i roto i ngā kōtiro) i roto i ngā tamariki
  • Te iti o te hiahia
  • Te manukanuka auau
  • Ngā whakaekenga mataku

He mea nui, i ētahi wā kāore he tohu o ngā pukupuku repe adrenal, ā, i ētahi wā ka kitea noa iho i te wā o te matawai mō tētahi atu take.

Ngā Tohu o te Matepukupuku Adrenal Metastatic

Mena ka horapa te mate pukupuku ki tua atu i ngā repe adrenal, arā, ki ētahi atu wāhanga o te tinana (metastatic), ka kaha ake pea ngā tohu. Ko ngā tohu o te mate pukupuku wāhanga 4 ko:

  • Whakapairuaki me te ruaki
  • Pupuhi
  • Ngenge
  • Kirika
  • Pōhēhētanga
  • Te ngaronga o te hiahia kai

He aha ngā take o te matepukupuku repeure?

Ina hoki, kāore anō kia mōhiotia e ngā tākuta te tino take o te mate pukupuku repe adrenal i te nuinga o ngā wā. E mōhio ana tātou ka taea e ngā huringa (ngā whakarerekētanga) o te DNA i roto i ō tātou pūtau te meinga kia rerekē te whanonga o ngā pūtau, kia noho hei mate pukupuku. Engari ko te mea kāore i te mārama ko te take i puta ai ēnei huringa DNA.

Ka riro i ētahi tāngata tētahi whakarerekētanga ira mai i ō rātou mātua, ā, ka piki ake te tūponotanga ki te pāngia e ēnei mate pukupuku. I ētahi atu wā, ka taea hoki e te pānga ki ngā matū whakaputa mate pukupuku te take. Heoi, i roto i te nuinga o ngā wā, te āhua nei ka puta ēnei whakarerekētanga DNA me te kore he take e kitea ana.

He aha ngā āhuatanga mōrearea mō te mate pukupuku repe adrenal?

Ko te tūponotanga mōrearea he mea e whakanui ake ai i te tūponotanga o te pāngia e te mate. Ehara i te mea ka tino pāngia koe e te mate. Engari ka taea e ia te kī atu kei te nui ake tō tūponotanga.

Ko ētahi o ngā āhuatanga mōrearea taiao ka pā ki te mate pukupuku repe adrenal ko:

  • Te momi hikareti
  • Te pānga ki ētahi matū, hei tauira, te asbestos me te radon .
  • I mua i te whiwhinga i te rongoā irahiko ki te puku (kei hea ngā repe adrenal).

Ahakoa te nuinga o ngā pukupuku adrenal ka puta mai i waho o te tinana, tata ki te 15% o te hunga e pāngia ana e ngā pukupuku adrenal he mate ira . He mea tino noa tēnei i roto i ngā tamariki. Ko ētahi o ngā mate ira ka pā pea ki te mate pukupuku repe adrenal ko:

  • Te mate Beckwith-Wiedemann
  • Te mate o Von Hippel-Lindau
  • Te mate Li-Fraumeni
  • Te polyposis adenomatous whānau (FAP)
  • Neurofibromatosis momo 1
  • Ngā neoplasia endocrine maha (MEN)
  • Te matatini o Carney
  • Te mate Lynch

He ahua uaua tēnei, kāore? Ki te mea he ruarua āu mō tēnei momo āhuatanga, he pai ake te kōrero ki te tākuta.

Me pēhea koe e mōhio ai mēnā he mate pukupuku repe tāu?

Tērā pea ka whakapae tō tākuta kei te mate pukupuku koe i te repe adrenal i runga i ō tohu (hei tauira, te tupu rerekē o te makawe, te huringa ohorere o te taumaha). Engari i ētahi wā, ka kitea noa iho ēnei pukupuku i te wā o te matawai CT (matawai tomography rorohiko) te matawai MRI rānei (whakaahua aukume) i mahia mō tētahi atu take.

Ina haere koe ki te tākuta, ka mahia e ia ēnei mea:

  • Whakahaerehia he whakamātautau tinana.
  • Ka arotakehia tō hītori hauora.
  • Kei te pātai atu ahau mō ō tohumate.
  • Ka tirohia e rātou mēnā he take mōrearea kei a koe mō te mate pukupuku repe adrenal.
  • Pātai atu mō tō hītori whānau mō te mate pukupuku.

He aha ngā whakamātautau hei āwhina i te tautuhi i te mate pukupuku repe?

I muri i te whakamātautau tinana, ka whakahaerehia pea e te tākuta ētahi atu whakamātautau, hei whakaū i te mate, hei whakakore rānei i ētahi atu mate hauora. Kei roto i ēnei whakamātautau:

  • Ngā whakamātautau toto:Ka taea te whakamahi i ēnei hei tirotiro i ngā taumata homoni me ētahi atu tohu.
  • Tātaritanga mimi: Ka taea te whakamātautau i te mimi mō ngā homoni me ētahi atu matū.
  • Ngā whakamātautau whakaahua: Mā ngā whakamātautau pēnei i ngā karapa CT, ngā karapa MRI, me ngā karapa PET ka taea te whakaatu mārama i te rahi, te wāhi, me te horapa o te pukupuku. I ētahi wā ka taea te mahi i te koiora , arā, te tango i tētahi wāhanga iti o te pukupuku hei whakamātautau, engari kāore i te mahia tonutia tēnei i roto i te matepukupuku repeure.

Te whakatau i te mate pukupuku adrenal

Ka whakamahia e ngā tākuta he pūnaha whakatauranga mate pukupuku hei tātaritanga i te mate pukupuku repe tākihi. Kei roto i tēnei ko te rahi o te puku, tōna wāhi, me te mea kua horapa (metastasized) ki ētahi atu wāhanga o te tinana.

Ki te kī māmā noa, ka nui ake te horapa o te mate pukupuku:

  • Wāhanga 1: E 5 henimita te rahi o te pukupuku, iti iho rānei, ā, kāore anō kia horapa ki tua atu i te repe adrenal.
  • Wāhanga 2: He nui ake te pukupuku i te 5 henimita, engari kāore anō kia horapa ki tua atu i te repe adrenal.
  • Wāhanga 3: Kei roto i te repe adrenal te mate pukupuku, ā, kua horapa ki ngā kiko e karapoti ana, ki ngā kōpū lymph tata rānei.
  • Wāhanga 4: Kei roto i te repe adrenal te mate pukupuku, ā, kua horapa ki ngā whekau tawhiti pērā i ngā pukahukahu me te ate.

He uaua pea ēnei wāhanga. Mena he pātai motuhake āu mō tō mate, he pai ake te kōrero ki tō tākuta.

Ka taea te rongoā i te mate pukupuku repeure?

He raruraru tēnei mō te tini o te tangata. Mena kei te repe adrenal anake te mate pukupuku, ā, kāore anō kia horapa ki ētahi atu wāhanga o te tinana, tera pea ka ora. Ko te tango pokanga o te repe (adrenalectomy) te maimoatanga matua mō tēnei wā.

Heoi, ki te horapa te mate pukupuku ki tua atu i te repe adrenal, ka iti ake te tūponotanga o te ora katoa. Heoi anō, ka taea e te maimoatanga te whakahaere i te tipu o te pukupuku me te whakapai ake i te kounga o tō oranga.

Me pēhea te rongoā i te mate pukupuku repe adrenal?

Ko te maimoatanga mō te matepukupuku repe adrenal e whakawhirinaki ana ki te rahi o te pukupuku, tōna wāhi, me te mea kua horapa atu ki tua atu i te repe adrenal. He maha ngā maimoatanga ka taea:

  • Pokanga:

Mena kei roto noa te puku i te repe adrenal, kua horapa rānei ki ngā kiko tata, ki ngā kōpū lymph rānei, tera pea ka tūtohu tō tākuta kia pokangahia. Ka tangohia e te taote pokanga te repe adrenal katoa (adrenalectomy) me ngā wāhanga mate tata katoa.

Mena kei roto i te repe adrenal kotahi anake te mate pukupuku, ka mahi noa te repe kē atu. I te nuinga o te wā, kāore he mahi kē atu e hiahiatia ana. Heoi, ki te tangohia ngā repe adrenal e rua, me tango rongoā koe hei whakakapi i ngā homoni i hangaia e aua repe mō te toenga o tō oranga.

I ētahi wā, ka tūtohutia te chemotherapy , te radiation therapy rānei i muri i te pokanga hei whakangaro i ngā pūtau matepukupuku e toe ana, hei whakaiti hoki i te tūponotanga o te hokinga mai o te matepukupuku.

Ahakoa kua horapa te mate pukupuku, tera tonu ētahi wā ka tūtohutia kia pokangahia hei tango i te nuinga o te pukupuku. Ka kiia tēnei ko te 'pokanga tango i te pukupuku' .

  • Te rongoā irahiko:

Ko te tikanga o tēnei ko te whakamahi i ngā hihi X-ray kaha-teitei hei whakangaro i ngā pūtau matepukupuku. He iti noa te whakamahinga o te rongoā irahiko hei rongoā tuatahi mō te matepukupuku repeure. Ka taea te whakamahi hei whakaiti i te tūponotanga o te hokinga mai o te matepukupuku i muri i te pokanga. Ka taea hoki te whakamahi hei whakaiti i ngā tohu i te wāhi kua horapa te matepukupuku. Ka taea e ngā tākuta te hoatu rongoā irahiko me te chemotherapy, me ētahi atu rongoā rānei.

  • Te rongoā matū:

Ko te chemotherapy te whakamahinga o ngā rongoā hei patu i ngā pūtau matepukupuku. Ka taea te hoatu i ēnei rongoā hei pire, hei werohanga rānei mā roto i te uaua. He maha ngā wā ka whakamahia te chemotherapy hei rongoā i te matepukupuku repeure kua horapa ki ētahi atu wāhanga o te tinana. Ka taea hoki te whakamahi hei patu i ngā pūtau matepukupuku e toe ana i muri i te pokanga.

He rongoā chemotherapy te Mitotane e whakamahia whānuitia ana hei rongoā i te mate pukupuku o te repe adrenal.

  • Ētahi atu rongoā:

Ka whakamahia hoki e ngā tākuta ētahi atu rongoā hei rongoā i ngā pukupuku repe adrenal. Ka taea e ētahi rongoā, pērā i te metyrapone, te whakaiti i te hanga o ngā homoni steroid adrenal. Ko ētahi atu rongoā, pērā i te spironolactone me te mifepristone, ka ārai i ngā pānga o ngā homoni i hangaia e te pukupuku.

Ahakoa ka taea e ēnei rongoā te whakaora i ō tohumate, kāore e whakaiti, e whakangaro rānei i ngā pūtau matepukupuku.

Ko wai e rongoā ana i te mate pukupuku repeure?

Mena he mate pukupuku repe tāu, tera pea he maha ngā tohunga kei roto i tō rōpū hauora, tae atu ki:

  • Ngā tohunga mate pukupuku - e pā ana ki te pokanga, te irahiko, me ngā maimoatanga rongoā.
  • Ngā endocrinologists - mō ngā raruraru e pā ana ki ngā homoni.

Ka tere te horapa o te mate pukupuku repe?

Ka rerekē tēnei i runga i te momo pukupuku kei a koe:

  • Ko te adrenocortical carcinoma, te momo tino noa, ka tere te tipu me te horapa.
  • Ka puhoi te tipu o ētahi momo neuroblastoma , ko ētahi ia ka tere te tipu.
  • Ka puhoi te tipu o te nuinga o ngā pheochromocytomas matepukupuku.

Kāore te mate pukupuku adrenal e pā ki te katoa i te huarahi kotahi. Mena he pātai āu mō te tere o te tipu o tō pukupuku, he pai ake te kōrero ki tō tākuta.

He pēhea te kino o te mate pukupuku repe adrenal?

I te nuinga o te wā, he uaua ki te rongoā te mate pukupuku repe adrenal. Ko te āhua o te mate pukupuku e whakawhirinaki ana ki te wāhi o te puku, tōna rahi, me te horapa rānei ki ētahi atu wāhanga o te tinana.

Ka taea e koe te ora i te pukupuku adrenal? Ngā Auau Ora o te Matepukupuku Adrenal

Ae, ka taea te ora i te mate pukupuku repeure. Heoi, he maha ngā āhuatanga e pā ana ki tēnei.

Mō ngā reiti oranga, ko te reiti oranga mō te mate pukupuku repe adrenal i roto i ngā tau e rima i te tīmatanga kei waenganui i te 50% me te 60% . Ko te tikanga tēnei tae atu ki te 60% o te hunga whai mate kei te ora tonu i roto i ngā tau e rima i muri i te tātaritanga. Heoi, ina horapa te mate pukupuku ki ētahi atu wāhanga o te tinana, ka heke tēnei reiti oranga mō ngā tau e rima ki te 10% ki te 20%.

Engari kia maumahara ki tēnei: ​​He tatauranga noa iho ngā reiti ora. Kāore e whakaatu tika ana i te roa o tō oranga, i te angitu rānei o tētahi maimoatanga mōu. Kōrero ki tō tākuta kia mōhio ai koe me pēhea te pānga o ēnei tatauranga ki tō āhuatanga.

Ka taea te ārai i te mate pukupuku repe adrenal?

Kāore anō kia kitea he huarahi hei ārai i te mate pukupuku o te repe adrenal, engari mā te karo i ngā āhuatanga mōrearea taiao, pērā i te momi hikareti, ka āwhina i te whakaiti i tō mōrearea whānui ki tētahi taumata.

Āhea ahau me toro atu ki te tākuta?

Kāore i te ngāwari te kite i ngā tohu o te matepukupuku repe adrenal. Heoi, me toro atu ki te tākuta mēnā ka pāngia koe e tētahi o ēnei e whai ake nei:

  • Mamae puku
  • Te mate huka ohorere
  • Te whakahekenga taumaha, te pikinga taumaha rānei kāore i te whakamāramatia
  • Te tupu nui o te makawe
  • Ngā huringa ki ō ira tangata

Mena kua pāngia tētahi mema o te whānau tata (matua, teina rānei) e te mate pukupuku repeure, he mea pai hoki kia kōrero koe ki tētahi tākuta mō tō mōrearea.

He aha ngā pātai me pātai atu e au ki taku tākuta?

Mena kua tāpaetia koe, tō whanaunga rānei, kei te mate pukupuku repe adrenal koe, he mea pai pea kia pātai atu koe ki a koe anō i ēnei pātai:

  • Kei hea te pukupuku? (Kei hea te pukupuku?)
  • He aha te rahi o te pukupuku?
  • Kua horapa te mate pukupuku ki waho o taku repe adrenal?
  • Me nui ake ngā whakamātautau e hiahiatia ana e au?
  • He aha aku kōwhiringa maimoatanga?
  • Ka taea e au te mahi, te haere rānei ki te kura i te wā e rongoatia ana?
  • Āhea ahau ka tīmata ai te maimoatanga?
  • He aha taku e taea ai hei whakamama i aku tohumate?
  • He aha ngā tūponotanga ka hoki mai anō te mate pukupuku repe?

He mea noa te maha o ngā kare ā-roto e pāngia ana e te mate pukupuku repeure. Kei reira tō tākuta hei āwhina i a koe. Haunga te kōrero mō ngā kōwhiringa maimoatanga, ka taea hoki e ia te kōrero ki a koe mō ngā puna kōrero me te tautoko. Tērā pea ka taea e koe te kōrero ki ētahi atu e pāngia ana e ngā wheako ōrite mā roto i ngā rōpū tautoko, i tō rohe, i te ipurangi rānei. He tino āwhina ēnei mō tō oranga hinengaro, kare ā-roto, me tō oranga wairua i tēnei wā uaua.

Karere Tangohia ki te Kāinga

Āe, me whakarapopoto tātou i ētahi o ngā kōrero tino nui o ngā mea kua kōrerohia e tātou.

  • He mate onge te matepukupuku adrenal.
  • He rerekē ngā tohu, ā, i ētahi wā, kāore pea he tohu. Ki te kite koe i tētahi mea rerekē, rapua he tohutohu hauora.
  • Kāore i te mārama tonu te take, engari tera pea he pānga o ngā āhuatanga ira me te taiao.
  • He maha ngā kōwhiringa maimoatanga, kei runga i te wāhanga me te āhua o te mate pukupuku.
  • Mā te kitenga wawe ka nui ake te tūponotanga o te whakaoranga.
  • Mena he pātai āu, he pātai rānei tā tētahi e mōhio ana koe mō tēnei, kaua e wehi ki te kōrero ki te tākuta. He mea tino nui ngā mōhiohio tika me te tautoko.

Kia maumahara, kāore koe i te mokemoke. Kua whanake haere te pūtaiao hauora, ā, he tokomaha ngā tāngata ka taea te āwhina i a koe.


Matepukupuku adrenal , repe adrenal, homoni, tohumate pukupuku, maimoatanga pukupuku, whatukuhu, wāhanga pukupuku

Frequently Asked Questions (FAQ)

He aha ngā whakamātautau hei āwhina i te tautuhi i te mate pukupuku repe?

I muri i te whakamātautau tinana, ka whakahaerehia pea e te tākuta ētahi atu whakamātautau, hei whakaū i te mate, hei whakakore rānei i ētahi atu mate hauora. Kei roto i ēnei whakamātautau:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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